{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,10]],"date-time":"2026-10-10T06:17:15Z","timestamp":1791613035895,"version":"4.3.4"},"reference-count":25,"publisher":"Springer Science and Business Media LLC","issue":"6","license":[{"start":{"date-parts":[[2024,4,18]],"date-time":"2024-04-18T00:00:00Z","timestamp":1713398400000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0"},{"start":{"date-parts":[[2024,4,18]],"date-time":"2024-04-18T00:00:00Z","timestamp":1713398400000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0"}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["Int J Cardiovasc Imaging"],"abstract":"<jats:title>Abstract<\/jats:title>\n                  <jats:p>Scimitar Syndrome is part of a complex spectrum of congenital cardiovascular anomalies related to anomalous pulmonary venous return. Depending on the extent of involvement, treatment can be either expectant or surgical. Prognosis and survival have been controversial, with some results supporting early surgical management. This research aims to disclose the outcomes and describe the management, clinical and imaging characteristics of patients diagnosed with Scimitar Syndrome treated in a tertiary referral healthcare center. Longitudinal descriptive observational study. The study included all patients diagnosed with scimitar syndrome in our institution between January\/2011 and December\/2022. A description of the sociodemographic and clinical characteristics, diagnostic tools used, treatment features, and patient outcomes is provided. Eleven patients were included, with a mean age at diagnosis of five years (CI 0\u201317), six of which were female (54.55%). Nine (81.82%) patients had evidence of a scimitar vein on the chest radiograph, six (54.55%) cardiac dextroposition, six (54.55%) pulmonary hypoplasia, five (45.45%) right pulmonary artery hypoplasia, and three (27.27%) had aortopulmonary collaterals. Four (36.36%) patients had horseshoe lungs, and four (36.36%) had bronchopulmonary sequestration. In the associations, two (18.18%) patients were found to have an atrial septal defect, three (27.27%) ventricular septal defect, and one (9%) had Tetralogy of Fallot. Pulmonary hypertension was demonstrated in two (18.18%) patients. Seven (63.64%) required surgical management to correct the scimitar vein, and two patients died due to unrelated complications. Scimitar syndrome presents diagnostic and treatment challenges, necessitating a multidisciplinary approach for timely care. Chest radiography and CT scans are primary diagnostic tools, with surgical intervention often warranted alongside other heart defects or significant hemodynamic repercussions. Medical management is effective for mild to moderate cases. Long-term patient outcomes remain uncertain due to study limitations, but improved life expectancy is anticipated with ongoing care.<\/jats:p>","DOI":"10.1007\/s10554-024-03102-1","type":"journal-article","created":{"date-parts":[[2024,4,18]],"date-time":"2024-04-18T01:01:56Z","timestamp":1713402116000},"page":"1319-1328","update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":7,"title":["Clinical characteristics, imaging findings, management, and outcomes of patients with scimitar syndrome at a tertiary referral healthcare center in Colombia"],"prefix":"10.1007","volume":"40","author":[{"given":"Ana M.","family":"Aristizabal","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Carlos A.","family":"Guzm\u00e1n-Serrano","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Nancy Vanessa","family":"Mondol-Villamil","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Lina Maria","family":"Bola\u00f1os-Vallejo","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Valentina","family":"Mejia-Qui\u00f1ones","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Maria Alejandra","family":"Recio-G\u00f3mez","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Enrique Carlos","family":"Garc\u00eda-Pretelt","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mauricio","family":"Mej\u00eda-Gonz\u00e1lez","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Walter Mosquera","family":"Alvarez","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jaiber Alberto","family":"Guti\u00e9rrez-Gil","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2024,4,18]]},"reference":[{"key":"3102_CR1","doi-asserted-by":"publisher","unstructured":"Dennehy W, Neverman EM (2021) Scimitar syndrome, Journal of Osteopathic Medicine, vol. 121, no. 9, pp. 771\u2013772, Jul. https:\/\/doi.org\/10.1515\/jom-2021-0142","DOI":"10.1515\/jom-2021-0142"},{"key":"3102_CR2","doi-asserted-by":"publisher","unstructured":"Gudjonsson U, Brown JW (2006) Scimitar Syndrome, Seminars in Thoracic and Cardiovascular Surgery: Pediatric Cardiac Surgery Annual, vol. 9, no. 1, pp. 56\u201362, Jan. https:\/\/doi.org\/10.1053\/j.pcsu.2006.02.011","DOI":"10.1053\/j.pcsu.2006.02.011"},{"key":"3102_CR3","doi-asserted-by":"publisher","unstructured":"Vida VL, Guariento A (Mar. 2020) A sword threatening the heart: the scimitar syndrome. JTCVS Techniques 1:75\u201380. https:\/\/doi.org\/10.1016\/j.xjtc.2020.01.017","DOI":"10.1016\/j.xjtc.2020.01.017"},{"key":"3102_CR4","doi-asserted-by":"publisher","unstructured":"Chowdhury UK et al (2021) Oct., Surgical management of the scimitar syndrome, Journal of Cardiac Surgery, vol. 36, no. 10, pp. 3770\u20133795, https:\/\/doi.org\/10.1111\/jocs.15857","DOI":"10.1111\/jocs.15857"},{"issue":"2","key":"3102_CR5","doi-asserted-by":"publisher","first-page":"275","DOI":"10.1016\/j.jpeds.2012.07.066","volume":"162","author":"A Chemin","year":"2013","unstructured":"Chemin A, Bonnet D, Le Bourgeois M, Levy M, Delacourt C (2013) Respiratory outcome in children with Scimitar Syndrome. J Pediatr 162(2):275\u2013279 .e1, Feb. https:\/\/doi.org\/10.1016\/j.jpeds.2012.07.066","journal-title":"J Pediatr"},{"key":"3102_CR6","doi-asserted-by":"publisher","unstructured":"Jarroumi-Sellak I, Arenas-Gordillo M, Garc\u00eda-S\u00e1nchez M\u00c1, Luque-Romero LG (2020) S\u00edndrome de la cimitarra en la edad adulta, Atenci\u00f3n Primaria, vol. 52, no. 10, pp. 789\u2013791, Dec. https:\/\/doi.org\/10.1016\/j.aprim.2020.02.010","DOI":"10.1016\/j.aprim.2020.02.010"},{"key":"3102_CR7","doi-asserted-by":"publisher","unstructured":"Vida VL et al (2010) Sep., Scimitar Syndrome: A European Congenital Heart Surgeons Association (ECHSA) Multicentric Study, Circulation, vol. 122, no. 12, pp. 1159\u20131166, https:\/\/doi.org\/10.1161\/CIRCULATIONAHA.109.926204","DOI":"10.1161\/CIRCULATIONAHA.109.926204"},{"key":"3102_CR8","doi-asserted-by":"publisher","unstructured":"Katekaru-Tokeshi DI, Pati\u00f1o-Bahena EJ, Garc\u00eda-Montes JA, Jim\u00e9nez-Santos M (2020) Tetralogy of Fallot with Scimitar Syndrome, Radiology: Cardiothoracic Imaging, vol. 2, no. 5, p. e200253, Oct. https:\/\/doi.org\/10.1148\/ryct.2020200253","DOI":"10.1148\/ryct.2020200253"},{"key":"3102_CR9","unstructured":"Diaz-Frias J, Widrich J Scimitar Syndrome, in StatPearls, Treasure Island (FL): StatPearls Publishing, 2023. 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Due to the retrospective nature of the protocol, it was approved without the need for informed consent.","order":3,"name":"Ethics","group":{"name":"EthicsHeading","label":"Ethical approval"}},{"value":"The authors have no relevant financial or non-financial interests to disclose. No use of any AI or large language model were used during the writing, processing or editing of the present manuscript.","order":4,"name":"Ethics","group":{"name":"EthicsHeading","label":"Conflict of interest"}}]}}