{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,4]],"date-time":"2026-10-04T20:23:22Z","timestamp":1791145402963,"version":"4.1.0"},"reference-count":13,"publisher":"Springer Science and Business Media LLC","issue":"5","license":[{"start":{"date-parts":[[2005,9,1]],"date-time":"2005-09-01T00:00:00Z","timestamp":1125532800000},"content-version":"tdm","delay-in-days":0,"URL":"http:\/\/www.springer.com\/tdm"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["J Clin Immunol"],"published-print":{"date-parts":[[2005,9]]},"DOI":"10.1007\/s10875-005-5637-2","type":"journal-article","created":{"date-parts":[[2005,9,13]],"date-time":"2005-09-13T02:10:43Z","timestamp":1126577443000},"page":"496-502","source":"Crossref","is-referenced-by-count":92,"title":["Mutational Analysis of Human BAFF Receptor TNFRSF13C (BAFF-R) in Patients with Common Variable Immunodeficiency"],"prefix":"10.1007","volume":"25","author":[{"given":"Claretta Gioia","family":"Losi","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Antonietta","family":"Silini","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Claudia","family":"Fiorini","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Annarosa","family":"Soresina","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Antonella","family":"Meini","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Simona","family":"Ferrari","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Luigi D.","family":"Notarangelo","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Vassilios","family":"Lougaris","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Alessandro","family":"Plebani","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","reference":[{"key":"5637_CR1","doi-asserted-by":"crossref","first-page":"34","DOI":"10.1006\/clim.2001.5197","volume":"103","author":"K Agematsu","year":"2002","unstructured":"Agematsu K, Futatani T, Hokibara S, Kobayashi N, Takamoto M, Tsukada S, Suzuki H, Koyasu S, Miyawaki T, Sugane K, Komiyama A, Ochs HD: Absence of memory B cells in patient with common variable immunodeficiency. Clin Immunol 103:34\u201342, 2002","journal-title":"Clin Immunol"},{"key":"5637_CR2","doi-asserted-by":"crossref","first-page":"261","DOI":"10.1038\/ni902","volume":"4","author":"B Grimbacher","year":"2003","unstructured":"Grimbacher B, Hutloff A, Schlesier M, Glocker E, Warnatz K, Dr\u00e4ger R, Eibel H, Fischer B, Sch\u00e4ffer A, Mages HW, Kroczek RA, Peter HH: Homozygous loss of ICOS is associated with adult-onset common variable immunodeficiency. Nat Immunol 4:261\u2013268, 2003","journal-title":"Nat Immunol"},{"key":"5637_CR3","doi-asserted-by":"crossref","first-page":"289","DOI":"10.1016\/S1074-7613(01)00183-2","volume":"15","author":"JA Gross","year":"2001","unstructured":"Gross JA, Dillon SR, Mudri S, Johnston J, Littau A, Roque R, Rixon M, Schou O, Foley KP, Haugen H, McMillens S, Waggie K, Schrechhise RV, Shoemaker K, Vu T, Moore M, Grossman A, Clegg CH: TACI-Ig neutralized molecules critical for B cell development and autoimmune disease. Impaired B cell maturation in mice lacking BLyS. Immunity 15:289\u2013302, 2001","journal-title":"Immunity"},{"key":"5637_CR4","doi-asserted-by":"crossref","first-page":"2111","DOI":"10.1126\/science.1061964","volume":"293","author":"B Schiemann","year":"2001","unstructured":"Schiemann B, Gommerman JL, Vora K, Cachero TG, Shulga-Morskaya S, Dobles D, Frew E, and Scott ML: An essential role for BAFF in the normal development of B cells trough a BCMA-independent pathway. Science 293:2111\u20132114, 2001","journal-title":"Science"},{"issue":"11","key":"5637_CR5","doi-asserted-by":"crossref","first-page":"1697","DOI":"10.1084\/jem.190.11.1697","volume":"190","author":"F Mackay","year":"1999","unstructured":"Mackay F, Woodcock SA, Lawton P, Ambrose C, Baetscher M, Schneider P, Tschopp J, Browning JL: Mice transgenic for BAFF develop lymphocytic disorders along with autoimmune manifestations. J. Exp. Med. 190(11):1697\u20131710, 1999","journal-title":"J. Exp. Med."},{"key":"5637_CR6","first-page":"18","volume":"27","author":"JL Bodmer","year":"2002","unstructured":"Bodmer JL, Shneider P, Tschopp J: The molecular architecture of the TNF superfamily. TIBS 27:18\u201326, 2002","journal-title":"TIBS"},{"key":"5637_CR7","doi-asserted-by":"crossref","first-page":"2108","DOI":"10.1126\/science.1061965","volume":"293","author":"JS Thompson","year":"2001","unstructured":"Thompson JS, Bixler SA, Quian F, Vora K, Scott ML, Cachero TG, Heisson C, Schneider P, Sizing ID, Mullen C, Strauch K, Zafari M, Benjamin CD, Tschopp J, Browning JL, Ambrose C: BAFF-R, a newly identified TNF receptor that specifically interacts with BAFF. Science 293:2108\u20132111, 2001","journal-title":"Science"},{"key":"5637_CR8","doi-asserted-by":"crossref","first-page":"1547","DOI":"10.1016\/S0960-9822(01)00481-X","volume":"11","author":"M Yan","year":"2001","unstructured":"Yan M, Brady JR, Chan B, Lee WP, Hsu B, Harless S, Cancro M, Grewal IS, Dixit VM: Identification of a novel receptor for B lymphocyte stimulator that is mutated in a mouse strain with severe B cell deficiency. Curr Biol 11:1547\u20131552, 2001","journal-title":"Curr Biol"},{"key":"5637_CR9","doi-asserted-by":"crossref","first-page":"2245","DOI":"10.4049\/jimmunol.173.4.2245","volume":"173","author":"S Sasaki","year":"2004","unstructured":"Sasaki S, Casola S, Kutok JL, Rajewsky K, Schmidt-Supprian M: TNF family member B cell- activating factor (BAFF) receptor-depending and -independing roles for BAFF in B cell physiology. J Immunol 173:2245\u20132252, 2004","journal-title":"J Immunol"},{"key":"5637_CR10","doi-asserted-by":"crossref","first-page":"762","DOI":"10.4049\/jimmunol.172.2.762","volume":"172","author":"L Gorelik","year":"2004","unstructured":"Gorelik L, Cutler AH, Thill G, Miklasz D, Shea DE, Ambrose C, Bixler SA, Su L, Scott ML, Kalled SL: Cutting Edge: BAFF regulated CD21\/35 and CD23 expression independent of its B cell survival function. J Immunol 172:762\u2013766, 2004","journal-title":"J Immunol"},{"key":"5637_CR11","doi-asserted-by":"crossref","first-page":"2331","DOI":"10.4049\/jimmunol.173.4.2331","volume":"173","author":"S Shulga-Morskaya","year":"2004","unstructured":"Shulga-Morskaya S, Dobles M, Walsh ME, Ng LG, MacKay F, Rao SP, Kalled SL, Scott ML: B cell-activating factor belonging to the TNF family acts through separate receptors to support B cell survival and T cell-independent antibody formation. J Immunol 173:2331\u20132341, 2004","journal-title":"J Immunol"},{"key":"5637_CR12","doi-asserted-by":"crossref","first-page":"807","DOI":"10.4049\/jimmunol.173.2.807","volume":"173","author":"LG Ng","year":"2004","unstructured":"Ng LG, Sutherland AP, Newton R, Qian F, Cachero TG, Scott ML, Thompson JS, Wheway J, Chtanova T, Groom J, Sutton IJ, Xin C, Tangye SG, Kalled SL, Mackay F, Mackay CR: B cell-activating factor belonging to the TNF family (BAFF)-R is the principal BAFF receptor facilitating BAFF costimulation of circulating T and B cells. J Immunol 173:807\u2013817, 2004","journal-title":"J Immunol"},{"key":"5637_CR13","doi-asserted-by":"crossref","first-page":"35","DOI":"10.1084\/jem.20032000","volume":"201","author":"C Castigli","year":"2005","unstructured":"Castigli C, Wilson SA, Scott S, Dedeoglu F, Xu S, Lam KP, Bram RJ, Jabara H, Geha RS: TACI and BAFF-R mediate isotype switching in B cells. J Exp Med 201:35\u201339, 2005","journal-title":"J Exp Med"}],"container-title":["Journal of Clinical Immunology"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1007\/s10875-005-5637-2.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/link.springer.com\/article\/10.1007\/s10875-005-5637-2\/fulltext.html","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1007\/s10875-005-5637-2","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2019,5,31]],"date-time":"2019-05-31T00:09:57Z","timestamp":1559261397000},"score":1,"resource":{"primary":{"URL":"http:\/\/link.springer.com\/10.1007\/s10875-005-5637-2"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2005,9]]},"references-count":13,"journal-issue":{"issue":"5","published-print":{"date-parts":[[2005,9]]}},"alternative-id":["5637"],"URL":"https:\/\/doi.org\/10.1007\/s10875-005-5637-2","relation":{},"ISSN":["0271-9142","1573-2592"],"issn-type":[{"value":"0271-9142","type":"print"},{"value":"1573-2592","type":"electronic"}],"subject":[],"published":{"date-parts":[[2005,9]]}}}