{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,26]],"date-time":"2026-09-26T10:48:47Z","timestamp":1790419727139,"version":"4.1.0"},"reference-count":25,"publisher":"Springer Science and Business Media LLC","issue":"1","license":[{"start":{"date-parts":[[2017,10,28]],"date-time":"2017-10-28T00:00:00Z","timestamp":1509148800000},"content-version":"unspecified","delay-in-days":0,"URL":"http:\/\/www.springer.com\/tdm"}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["J Clin Immunol"],"published-print":{"date-parts":[[2018,1]]},"DOI":"10.1007\/s10875-017-0456-9","type":"journal-article","created":{"date-parts":[[2017,10,28]],"date-time":"2017-10-28T03:21:10Z","timestamp":1509160870000},"page":"28-34","update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":100,"title":["Autoimmune Cytopenias and Associated Conditions in CVID: a Report From the USIDNET Registry"],"prefix":"10.1007","volume":"38","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-9668-5619","authenticated-orcid":false,"given":"Elizabeth J.","family":"Feuille","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Niloofar","family":"Anooshiravani","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Kathleen E.","family":"Sullivan","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ramsay L.","family":"Fuleihan","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Charlotte","family":"Cunningham-Rundles","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2017,10,28]]},"reference":[{"key":"456_CR1","doi-asserted-by":"crossref","first-page":"38","DOI":"10.1016\/j.jaip.2015.07.025","volume":"4","author":"FA Bonilla","year":"2016","unstructured":"Bonilla FA, Barlan I, Chapel H, Costa-Carvalho BT, Cunningham-Rundles C, de la Morena MT, et al. International Consensus Document (ICON): common variable immunodeficiency disorders. J Allergy Clin Immunol Pract. 2016;4:38\u201359.","journal-title":"J Allergy Clin Immunol Pract"},{"key":"456_CR2","doi-asserted-by":"crossref","first-page":"696","DOI":"10.1007\/s10875-015-0201-1","volume":"35","author":"C Picard","year":"2015","unstructured":"Picard C, Al-Herz W, Bousfiha A, Casanova JL, Chatila T, Conley ME, et al. Primary immunodeficiency diseases: an update on the classification from the International Union of Immunological Societies Expert Committee for primary immunodeficiency 2015. J Clin Immunol. 2015;35:696\u2013726.","journal-title":"J Clin Immunol"},{"key":"456_CR3","doi-asserted-by":"crossref","first-page":"277","DOI":"10.1182\/blood-2007-11-124545","volume":"112","author":"H Chapel","year":"2008","unstructured":"Chapel H, Lucas M, Lee M, Bjorkander J, Webster D, Grimbacher B, et al. Common variable immunodeficiency disorders: division into distinct clinical phenotypes. Blood. 2008;112:277\u201386.","journal-title":"Blood"},{"key":"456_CR4","doi-asserted-by":"crossref","first-page":"1650","DOI":"10.1182\/blood-2011-09-377945","volume":"119","author":"ES Resnick","year":"2012","unstructured":"Resnick ES, Moshier EL, Godbold JH, Cunningham-Rundles C. Morbidity and mortality in common variable immune deficiency over 4 decades. Blood. 2012;119:1650\u20137.","journal-title":"Blood"},{"key":"456_CR5","doi-asserted-by":"crossref","first-page":"203","DOI":"10.1111\/cei.12178","volume":"174","author":"R Ameratunga","year":"2013","unstructured":"Ameratunga R, Woon ST, Gillis D, Koopmans W, Steele R. New diagnostic criteria for common variable immune deficiency (CVID), which may assist with decisions to treat with intravenous or subcutaneous immunoglobulin. Clin Exp Immunol. 2013;174:203\u201311.","journal-title":"Clin Exp Immunol"},{"key":"456_CR6","doi-asserted-by":"crossref","first-page":"116","DOI":"10.1016\/j.jaci.2013.12.1077","volume":"134","author":"B Gathmann","year":"2014","unstructured":"Gathmann B, Mahlaoui N, Ceredih L, Gerard E, Oksenhendler K, Warnatz I, et al. European Society for Immunodeficiencies Registry Working. Clinical picture and treatment of 2212 patients with common variable immunodeficiency. J Allergy Clin Immunol. 2014;134:116\u201326.","journal-title":"J Allergy Clin Immunol"},{"key":"456_CR7","doi-asserted-by":"crossref","first-page":"45","DOI":"10.1111\/cei.12661","volume":"182","author":"K Marschall","year":"2015","unstructured":"Marschall K, Hoernes M, Bitzenhofer-Gruber M, Jandus P, Duppenthaler A, Wuillemin WA, et al. The Swiss National Registry for primary immunodeficiencies: report on the first 6 years\u2019 activity from 2008 to 2014. Clin Exp Immunol. 2015;182:45\u201350.","journal-title":"Clin Exp Immunol"},{"key":"456_CR8","doi-asserted-by":"crossref","first-page":"25","DOI":"10.1016\/j.jaut.2010.10.002","volume":"36","author":"J Boileau","year":"2011","unstructured":"Boileau J, Mouillot G, Gerard L, Carmagnat M, Rabian C, Oksenhendler E, et al. Autoimmunity in common variable immunodeficiency: correlation with lymphocyte phenotype in the French DEFI study. J Autoimmun. 2011;36:25\u201332.","journal-title":"J Autoimmun"},{"key":"456_CR9","doi-asserted-by":"crossref","first-page":"57","DOI":"10.1016\/j.jaut.2005.04.006","volume":"25","author":"J Wang","year":"2005","unstructured":"Wang J, Cunningham-Rundles C. Treatment and outcome of autoimmune hematologic disease in common variable immunodeficiency (CVID). J Autoimmun. 2005;25:57\u201362.","journal-title":"J Autoimmun"},{"key":"456_CR10","doi-asserted-by":"crossref","first-page":"254","DOI":"10.1097\/01.md.0000133624.65946.40","volume":"83","author":"M Michel","year":"2004","unstructured":"Michel M, Chanet V, Galicier L, Ruivard M, Levy Y, Hermine O, et al. Autoimmune thrombocytopenic purpura and common variable immunodeficiency: analysis of 21 cases and review of the literature. Medicine (Baltimore). 2004;83:254\u201363.","journal-title":"Medicine (Baltimore)"},{"key":"456_CR11","doi-asserted-by":"crossref","first-page":"941","DOI":"10.1016\/j.jaip.2015.07.004","volume":"3","author":"PJ Maglione","year":"2015","unstructured":"Maglione PJ, Overbey JR, Cunningham-Rundles C. Progression of common variable immunodeficiency interstitial lung disease accompanies distinct pulmonary and laboratory findings. J Allergy Clin Immunol Pract. 2015;3:941\u201350.","journal-title":"J Allergy Clin Immunol Pract"},{"key":"456_CR12","doi-asserted-by":"crossref","first-page":"1042","DOI":"10.1513\/AnnalsATS.201511-728OC","volume":"13","author":"A Mannina","year":"2016","unstructured":"Mannina A, Chung JH, Swigris JJ, Solomon JJ, Huie TJ, Yunt ZX, et al. Clinical predictors of a diagnosis of common variable immunodeficiency-related granulomatous-lymphocytic interstitial lung disease. Ann Am Thorac Soc. 2016;13:1042\u20139.","journal-title":"Ann Am Thorac Soc"},{"key":"456_CR13","doi-asserted-by":"crossref","first-page":"331","DOI":"10.1111\/j.1365-2249.2008.03711.x","volume":"153","author":"C Ward","year":"2008","unstructured":"Ward C, Lucas M, Piris J, Collier J, Chapel H. Abnormal liver function in common variable immunodeficiency disorders due to nodular regenerative hyperplasia. Clin Exp Immunol. 2008;153:331\u20137.","journal-title":"Clin Exp Immunol"},{"key":"456_CR14","doi-asserted-by":"crossref","first-page":"848","DOI":"10.1002\/ajh.23262","volume":"87","author":"DR Terrell","year":"2012","unstructured":"Terrell DR, Beebe LA, Neas BR, Vesely SK, Segal JB, George JN. Prevalence of primary immune thrombocytopenia in Oklahoma. Am J Hematol. 2012;87:848\u201352.","journal-title":"Am J Hematol"},{"key":"456_CR15","doi-asserted-by":"crossref","first-page":"1","DOI":"10.1016\/j.jaut.2007.05.002","volume":"29","author":"WW Eaton","year":"2007","unstructured":"Eaton WW, Rose NR, Kalaydjian A, Pedersen MG, Mortensen PB. Epidemiology of autoimmune diseases in Denmark. J Autoimmun. 2007;29:1\u20139.","journal-title":"J Autoimmun"},{"key":"456_CR16","doi-asserted-by":"crossref","unstructured":"Aladjidi N, Jutand MA, Beaubois C, Fernandes H, Jeanpetit J, Coureau G, Gilleron V, Kostrzewa A, Lauroua P, Jeanne M, Thiebaut R, Leblanc T, Leverger G, Perel Y. Reliable assessment of the incidence of childhood autoimmune hemolytic anemia. Pediatr Blood Cancer. 2017.","DOI":"10.1002\/pbc.26683"},{"key":"456_CR17","doi-asserted-by":"crossref","first-page":"431","DOI":"10.1136\/jcp.45.5.431","volume":"45","author":"EG Lyall","year":"1992","unstructured":"Lyall EG, Lucas GF, Eden OB. Autoimmune neutropenia of infancy. J Clin Pathol. 1992;45:431\u20134.","journal-title":"J Clin Pathol"},{"key":"456_CR18","doi-asserted-by":"crossref","unstructured":"Fischer A, Provot J, Jais JP, Alcais A, Mahlaoui N, C.F.P.I.D.s.g. members of the, autoimmune and inflammatory manifestations occur frequently in patients with primary immunodeficiencies. J Allergy Clin Immunol. 2017.","DOI":"10.1016\/j.jaci.2016.12.978"},{"key":"456_CR19","doi-asserted-by":"crossref","first-page":"198","DOI":"10.1016\/j.clim.2009.05.001","volume":"133","author":"O Ardeniz","year":"2009","unstructured":"Ardeniz O, Cunningham-Rundles C. Granulomatous disease in common variable immunodeficiency. Clin Immunol. 2009;133:198\u2013207.","journal-title":"Clin Immunol"},{"key":"456_CR20","doi-asserted-by":"crossref","first-page":"370","DOI":"10.1007\/s11882-005-0008-x","volume":"5","author":"Y Morimoto","year":"2005","unstructured":"Morimoto Y, Routes JM. Granulomatous disease in common variable immunodeficiency. Curr Allergy Asthma Rep. 2005;5:370\u20135.","journal-title":"Curr Allergy Asthma Rep"},{"key":"456_CR21","doi-asserted-by":"crossref","first-page":"452","DOI":"10.1016\/j.anai.2014.04.024","volume":"113","author":"PJ Maglione","year":"2014","unstructured":"Maglione PJ, Overbey JR, Radigan L, Bagiella E, Cunningham-Rundles C. Pulmonary radiologic findings in common variable immunodeficiency: clinical and immunological correlations. Ann Allergy Asthma Immunol. 2014;113:452\u20139.","journal-title":"Ann Allergy Asthma Immunol"},{"key":"456_CR22","doi-asserted-by":"crossref","first-page":"4190","DOI":"10.1182\/blood-2010-08-302984","volume":"117","author":"C Neunert","year":"2011","unstructured":"Neunert C, Lim W, Crowther M, Cohen A, Solberg L Jr, Crowther MA. The American Society of Hematology 2011 evidence-based practice guideline for immune thrombocytopenia. Blood. 2011;117:4190\u2013207.","journal-title":"Blood"},{"key":"456_CR23","doi-asserted-by":"crossref","first-page":"168","DOI":"10.1182\/blood-2009-06-225565","volume":"115","author":"D Provan","year":"2010","unstructured":"Provan D, Stasi R, Newland AC, Blanchette VS, Bolton-Maggs P, Bussel JB, et al. International consensus report on the investigation and management of primary immune thrombocytopenia. Blood. 2010;115:168\u201386.","journal-title":"Blood"},{"key":"456_CR24","doi-asserted-by":"crossref","first-page":"462","DOI":"10.1046\/j.1525-1438.2002.00053.x","volume":"42","author":"G Lucas","year":"2002","unstructured":"Lucas G, Rogers S, de Haas M, Porcelijn L, Bux J. Report on the fourth international granulocyte immunology workshop: progress toward quality assessment. Transfusion. 2002;42:462\u20138.","journal-title":"Transfusion"},{"key":"456_CR25","doi-asserted-by":"crossref","first-page":"929","DOI":"10.1016\/S0031-3955(02)00030-5","volume":"49","author":"W Kyono","year":"2002","unstructured":"Kyono W, Coates TD. A practical approach to neutrophil disorders. Pediatr Clin N Am. 2002;49:929\u201371. viii","journal-title":"Pediatr Clin N Am"}],"container-title":["Journal of Clinical Immunology"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/link.springer.com\/article\/10.1007\/s10875-017-0456-9\/fulltext.html","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1007\/s10875-017-0456-9.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1007\/s10875-017-0456-9.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2022,8,5]],"date-time":"2022-08-05T15:38:44Z","timestamp":1659713924000},"score":1,"resource":{"primary":{"URL":"http:\/\/link.springer.com\/10.1007\/s10875-017-0456-9"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2017,10,28]]},"references-count":25,"journal-issue":{"issue":"1","published-print":{"date-parts":[[2018,1]]}},"alternative-id":["456"],"URL":"https:\/\/doi.org\/10.1007\/s10875-017-0456-9","relation":{},"ISSN":["0271-9142","1573-2592"],"issn-type":[{"value":"0271-9142","type":"print"},{"value":"1573-2592","type":"electronic"}],"subject":[],"published":{"date-parts":[[2017,10,28]]}}}