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Participants included 55 families and their children (ages 5 to 18 years) and teachers. Measures included a MSUD Family Survey, the Behavior Assessment System for Children (BASC) and the Pediatric Quality of Life Inventory (PedsQL). Parents reported via the MSUD Family Survey that the greatest sources of stress were financial and emotional. Many parents reported difficulty interacting with the medical staff and with schools. On the BASC, half of the children fell within the average range in psychosocial adjustment, although there were elevations in scales measuring attention, hyperactivity, and learning problems. On the PedsQL, the mean quality of life scores were closer to children with cancer than to a healthy sample. Despite the emotional and financial burden, parents reported that MSUD has also had a positive influence on their lives, leading to a world\u2010view that is more compassionate and caring.<\/jats:p>","DOI":"10.1007\/s10897-007-9114-3","type":"journal-article","created":{"date-parts":[[2007,8,16]],"date-time":"2007-08-16T12:59:48Z","timestamp":1187269188000},"page":"799-809","source":"Crossref","is-referenced-by-count":28,"title":["Psychosocial Issues in Families Affected by Maple Syrup Urine Disease"],"prefix":"10.1002","volume":"16","author":[{"given":"Wendy","family":"Packman","sequence":"first","affiliation":[{"name":"Pacific Graduate School of Psychology 935 E. Meadow Drive Palo Alto CA 94303 USA"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Shelly L.","family":"Henderson","sequence":"additional","affiliation":[{"name":"Pacific Graduate School of Psychology 935 E. 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