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There is currently a lack of consensus on when to order <jats:italic>APC<\/jats:italic> (<jats:italic>adenomatous polyposis coli<\/jats:italic>) gene testing or implement surveillance for hepatoblastoma. An online questionnaire was completed by 62 genetic counselors to capture their current practices regarding these questions. Extracolonic findings associated with FAP that were most likely to prompt <jats:italic>APC<\/jats:italic> testing in an otherwise asymptomatic 10 year\u2010old child with a negative family history were multiple desmoid tumors, congenital hypertrophy of the retinal pigment epithelium (CHRPE), jaw osteomas, and hepatoblastoma. For hepatoblastoma screening, the majority did recommend this in children less than age five years with known <jats:italic>APC<\/jats:italic> mutations. An interval of every 3\u20136 months was most commonly suggested; however, responses extended to screening on a less than annual basis. These results highlight the need for further investigation into why some genetic counselors do not recommend <jats:italic>APC<\/jats:italic> testing in young at\u2010risk children and what factors influence views about the ideal age and indication for <jats:italic>APC<\/jats:italic> testing. Studies of these issues would help to define the best clinical practice model for genetic testing and hepatoblastoma screening in pediatric patients with FAP.<\/jats:p>","DOI":"10.1007\/s10897-016-0030-2","type":"journal-article","created":{"date-parts":[[2016,12,3]],"date-time":"2016-12-03T02:39:23Z","timestamp":1480732763000},"page":"586-593","update-policy":"http:\/\/dx.doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":6,"title":["Genetic Counselor Practices Involving Pediatric Patients with FAP: an Investigation of their Self\u2010Reported Strategies for Genetic Testing and Hepatoblastoma Screening"],"prefix":"10.1002","volume":"26","author":[{"given":"Caitlin E.","family":"Lawson","sequence":"first","affiliation":[{"name":"Children's Mercy Hospital\/University of Missouri\u2010Kansas City School of Medicine Kansas City MO USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Thomas M.","family":"Attard","sequence":"additional","affiliation":[{"name":"Children's Mercy Hospital\/University of Missouri\u2010Kansas City School of Medicine Kansas City MO USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Hongying","family":"Dai","sequence":"additional","affiliation":[{"name":"Children's Mercy Hospital\/University of Missouri\u2010Kansas City School of Medicine Kansas City MO USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Seth","family":"Septer","sequence":"additional","affiliation":[{"name":"Children's Hospital Colorado Aurora CO USA"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[2016,12,3]]},"reference":[{"key":"e_1_2_10_2_1","doi-asserted-by":"publisher","DOI":"10.1002\/pbc.20698"},{"key":"e_1_2_10_3_1","doi-asserted-by":"publisher","DOI":"10.1002\/ajmg.a.30585"},{"key":"e_1_2_10_4_1","doi-asserted-by":"publisher","DOI":"10.1002\/1097-0215(20010320)95:2<102::AID-IJC1018>3.0.CO;2-8"},{"key":"e_1_2_10_5_1","doi-asserted-by":"publisher","DOI":"10.1002\/humu.1380030206"},{"key":"e_1_2_10_6_1","doi-asserted-by":"publisher","DOI":"10.1542\/peds.2010-3743"},{"key":"e_1_2_10_7_1","doi-asserted-by":"publisher","DOI":"10.1002\/(SICI)1096-911X(199903)32:3<196::AID-MPO6>3.0.CO;2-9"},{"key":"e_1_2_10_8_1","doi-asserted-by":"publisher","DOI":"10.1067\/S0022-3476(03)00306-8"},{"issue":"4","key":"e_1_2_10_9_1","first-page":"345","article-title":"Attitudes toward colon cancer gene testing: factors predicting test uptake","volume":"8","author":"Codori A. 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