{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,27]],"date-time":"2026-10-27T20:17:00Z","timestamp":1793132220155,"version":"4.5.0"},"reference-count":128,"publisher":"Springer Science and Business Media LLC","issue":"1","license":[{"start":{"date-parts":[[2012,10,28]],"date-time":"2012-10-28T00:00:00Z","timestamp":1351382400000},"content-version":"tdm","delay-in-days":0,"URL":"http:\/\/www.springer.com\/tdm"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["J Muscle Res Cell Motil"],"published-print":{"date-parts":[[2013,2]]},"DOI":"10.1007\/s10974-012-9330-9","type":"journal-article","created":{"date-parts":[[2012,10,29]],"date-time":"2012-10-29T14:39:15Z","timestamp":1351521555000},"page":"1-13","source":"Crossref","is-referenced-by-count":89,"title":["Contribution of oxidative stress to pathology in diaphragm and limb muscles with Duchenne muscular dystrophy"],"prefix":"10.1007","volume":"34","author":[{"given":"Jong-Hee","family":"Kim","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Hyo-Bum","family":"Kwak","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"LaDora V.","family":"Thompson","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"John M.","family":"Lawler","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2012,10,28]]},"reference":[{"issue":"3","key":"9330_CR1","first-page":"94","volume":"28","author":"E Abdel-Salam","year":"2009","unstructured":"Abdel-Salam E, Abdel-Meguid I, Korraa SS (2009) Markers of degeneration and regeneration in Duchenne muscular dystrophy. Acta Myol 28(3):94\u2013100","journal-title":"Acta Myol"},{"issue":"4","key":"9330_CR2","doi-asserted-by":"crossref","first-page":"889","DOI":"10.1172\/JCI30556","volume":"117","author":"S Acharyya","year":"2007","unstructured":"Acharyya S, Villalta SA, Bakkar N, Bupha-Intr T, Janssen PM, Carathers M, Li ZW, Beg AA, Ghosh S, Sahenk Z, Weinstein M, Gardner KL, Rafael-Fortney JA, Karin M, Tidball JG, Baldwin AS, Guttridge DC (2007) Interplay of IKK\/NF-kappaB signaling in macrophages and myofibers promotes muscle degeneration in Duchenne muscular dystrophy. J Clin Invest 117(4):889\u2013901","journal-title":"J Clin Invest"},{"issue":"4","key":"9330_CR3","doi-asserted-by":"crossref","first-page":"959","DOI":"10.1016\/S0735-1097(98)00626-3","volume":"33","author":"V Adams","year":"1999","unstructured":"Adams V, Jiang H, Yu J, Mobius-Winkler S, Fiehn E, Linke A, Weigl C, Schuler G, Hambrecht R (1999) Apoptosis in skeletal myocytes of patients with chronic heart failure is associated with exercise intolerance. J Am Coll Cardiol 33(4):959\u2013965","journal-title":"J Am Coll Cardiol"},{"issue":"6","key":"9330_CR4","doi-asserted-by":"crossref","first-page":"1385","DOI":"10.1083\/jcb.150.6.1385","volume":"150","author":"ME Adams","year":"2000","unstructured":"Adams ME, Kramarcy N, Krall SP, Rossi SG, Rotundo RL, Sealock R, Froehner SC (2000) Absence of alpha-syntrophin leads to structurally aberrant neuromuscular synapses deficient in utrophin. J Cell Biol 150(6):1385\u20131398","journal-title":"J Cell Biol"},{"issue":"2","key":"9330_CR5","doi-asserted-by":"crossref","first-page":"83","DOI":"10.1139\/Y09-058","volume":"88","author":"DG Allen","year":"2010","unstructured":"Allen DG, Gervasio OL, Yeung EW, Whitehead NP (2010) Calcium and the damage pathways in muscular dystrophy. Can J Physiol Pharmacol 88(2):83\u201391","journal-title":"Can J Physiol Pharmacol"},{"issue":"3","key":"9330_CR6","doi-asserted-by":"crossref","first-page":"956","DOI":"10.1152\/japplphysiol.00538.2006","volume":"102","author":"S Arbogast","year":"2007","unstructured":"Arbogast S, Smith J, Matuszczak Y, Hardin BJ, Moylan JS, Smith JD, Ware J, Kennedy AR, Reid MB (2007) Bowman-Birk inhibitor concentrate prevents atrophy, weakness, and oxidative stress in soleus muscle of hindlimb-unloaded mice. J Appl Physiol 102(3):956\u2013964","journal-title":"J Appl Physiol"},{"issue":"6","key":"9330_CR7","doi-asserted-by":"crossref","first-page":"744","DOI":"10.4187\/respcare.00831","volume":"56","author":"JR Bach","year":"2011","unstructured":"Bach JR, Martinez D (2011) Duchenne muscular dystrophy: continuous noninvasive ventilatory support prolongs survival. Respir Care 56(6):744\u2013750","journal-title":"Respir Care"},{"issue":"1","key":"9330_CR8","doi-asserted-by":"crossref","first-page":"106","DOI":"10.1002\/(SICI)1097-4598(200001)23:1<106::AID-MUS14>3.0.CO;2-D","volume":"23","author":"MA Badalamente","year":"2000","unstructured":"Badalamente MA, Stracher A (2000) Delay of muscle degeneration and necrosis in mdx mice by calpain inhibition. Muscle Nerve 23(1):106\u2013111","journal-title":"Muscle Nerve"},{"issue":"3","key":"9330_CR9","doi-asserted-by":"crossref","first-page":"187","DOI":"10.1016\/0306-9877(89)90193-X","volume":"29","author":"MS Baker","year":"1989","unstructured":"Baker MS, Austin L (1989) The pathological damage in Duchenne muscular dystrophy may be due to increased intracellular oxy-radical generation caused by the absence of dystrophin and subsequent alterations in Ca2\u00a0+\u00a0metabolism. Med Hypotheses 29(3):187\u2013193","journal-title":"Med Hypotheses"},{"key":"9330_CR129","unstructured":"Berneske GM, Butson AR, Gauld EN, Levy D (1960) Clinical trial of high dosage vitamin E in human muscular dystrophy. Can Med Assoc J 82:418\u2013421"},{"issue":"24","key":"9330_CR10","doi-asserted-by":"crossref","first-page":"1289","DOI":"10.1056\/NEJM196512092732401","volume":"273","author":"HJ Binder","year":"1965","unstructured":"Binder HJ, Herting DC, Hurst V, Finch SC, Spiro HM (1965) Tocopherol deficiency in man. N Engl J Med 273(24):1289\u20131297","journal-title":"N Engl J Med"},{"issue":"6","key":"9330_CR11","doi-asserted-by":"crossref","first-page":"751","DOI":"10.1016\/S0006-2952(98)00055-0","volume":"56","author":"L Bornman","year":"1998","unstructured":"Bornman L, Rossouw H, Gericke GS, Polla BS (1998) Effects of iron deprivation on the pathology and stress protein expression in murine X-linked muscular dystrophy. Biochem Pharmacol 56(6):751\u2013757","journal-title":"Biochem Pharmacol"},{"issue":"5","key":"9330_CR12","doi-asserted-by":"crossref","first-page":"743","DOI":"10.1016\/0092-8674(95)90471-9","volume":"82","author":"JE Brenman","year":"1995","unstructured":"Brenman JE, Chao DS, Xia H, Aldape K, Bredt DS (1995) Nitric oxide synthase complexed with dystrophin and absent from skeletal muscle sarcolemma in Duchenne muscular dystrophy. Cell 82(5):743\u2013752","journal-title":"Cell"},{"issue":"5","key":"9330_CR13","doi-asserted-by":"crossref","first-page":"757","DOI":"10.1016\/S0092-8674(00)81053-3","volume":"84","author":"JE Brenman","year":"1996","unstructured":"Brenman JE, Chao DS, Gee SH, McGee AW, Craven SE, Santillano DR, Wu Z, Huang F, Xia H, Peters MF, Froehner SC, Bredt DS (1996) Interaction of nitric oxide synthase with the postsynaptic density protein PSD-95 and alpha1-syntrophin mediated by PDZ domains. Cell 84(5):757\u2013767","journal-title":"Cell"},{"issue":"8","key":"9330_CR14","doi-asserted-by":"crossref","first-page":"1753","DOI":"10.1002\/j.1460-2075.1996.tb00524.x","volume":"15","author":"M Buck","year":"1996","unstructured":"Buck M, Chojkier M (1996) Muscle wasting and dedifferentiation induced by oxidative stress in a murine model of cachexia is prevented by inhibitors of nitric oxide synthesis and antioxidants. EMBO J 15(8):1753\u20131765","journal-title":"EMBO J"},{"issue":"4","key":"9330_CR15","doi-asserted-by":"crossref","first-page":"749","DOI":"10.1093\/ajcn\/75.4.749","volume":"75","author":"TM Buetler","year":"2002","unstructured":"Buetler TM, Renard M, Offord EA, Schneider H, Ruegg UT (2002) Green tea extract decreases muscle necrosis in mdx mice and protects against reactive oxygen species. Am J Clin Nutr 75(4):749\u2013753","journal-title":"Am J Clin Nutr"},{"issue":"5","key":"9330_CR16","doi-asserted-by":"crossref","first-page":"1789","DOI":"10.1016\/S0002-9440(10)65050-X","volume":"156","author":"B Cai","year":"2000","unstructured":"Cai B, Spencer MJ, Nakamura G, Tseng-Ong L, Tidball JG (2000) Eosinophilia of dystrophin-deficient muscle is promoted by perforin-mediated cytotoxicity by T cell effectors. Am J Pathol 156(5):1789\u20131796","journal-title":"Am J Pathol"},{"issue":"3","key":"9330_CR17","doi-asserted-by":"crossref","first-page":"719","DOI":"10.1016\/j.nbd.2005.05.003","volume":"20","author":"CG Carlson","year":"2005","unstructured":"Carlson CG, Samadi A, Siegel A (2005) Chronic treatment with agents that stabilize cytosolic IkappaB-alpha enhances survival and improves resting membrane potential in MDX muscle fibers subjected to chronic passive stretch. Neurobiol Dis 20(3):719\u2013730","journal-title":"Neurobiol Dis"},{"issue":"5","key":"9330_CR18","doi-asserted-by":"crossref","first-page":"455","DOI":"10.1097\/00002060-200009000-00009","volume":"79","author":"GT Carter","year":"2000","unstructured":"Carter GT, McDonald CM (2000) Preserving function in Duchenne dystrophy with long-term pulse prednisone therapy. Am J Phys Med Rehabil 79(5):455\u2013458","journal-title":"Am J Phys Med Rehabil"},{"issue":"9","key":"9330_CR19","doi-asserted-by":"crossref","first-page":"2195","DOI":"10.1096\/fj.06-7353com","volume":"21","author":"JS Chamberlain","year":"2007","unstructured":"Chamberlain JS, Metzger J, Reyes M, Townsend D, Faulkner JA (2007) Dystrophin-deficient mdx mice display a reduced life span and are susceptible to spontaneous rhabdomyosarcoma. FASEB J 21(9):2195\u20132204","journal-title":"FASEB J"},{"issue":"17","key":"9330_CR20","doi-asserted-by":"crossref","first-page":"9142","DOI":"10.1073\/pnas.93.17.9142","volume":"93","author":"WJ Chang","year":"1996","unstructured":"Chang WJ, Iannaccone ST, Lau KS, Masters BS, McCabe TJ, McMillan K, Padre RC, Spencer MJ, Tidball JG, Stull JT (1996) Neuronal nitric oxide synthase and dystrophin-deficient muscular dystrophy. Proc Natl Acad Sci U S A 93(17):9142\u20139147","journal-title":"Proc Natl Acad Sci U S A"},{"issue":"2","key":"9330_CR21","doi-asserted-by":"crossref","first-page":"784","DOI":"10.1046\/j.1471-4159.1998.71020784.x","volume":"71","author":"DS Chao","year":"1998","unstructured":"Chao DS, Silvagno F, Bredt DS (1998) Muscular dystrophy in mdx mice despite lack of neuronal nitric oxide synthase. J Neurochem 71(2):784\u2013789","journal-title":"J Neurochem"},{"issue":"1","key":"9330_CR22","doi-asserted-by":"crossref","first-page":"89","DOI":"10.1007\/s12031-007-9005-y","volume":"34","author":"M Chen","year":"2008","unstructured":"Chen M, Cheng C, Yan M, Niu S, Gao S, Shi S, Liu H, Qin Y, Shen A (2008) Involvement of CAPON and nitric oxide synthases in rat muscle regeneration after peripheral nerve injury. J Mol Neurosci 34(1):89\u2013100","journal-title":"J Mol Neurosci"},{"issue":"11","key":"9330_CR23","doi-asserted-by":"crossref","first-page":"1572","DOI":"10.1053\/apmr.2002.35109","volume":"83","author":"MK Childers","year":"2002","unstructured":"Childers MK, Okamura CS, Bogan DJ, Bogan JR, Petroski GF, McDonald K, Kornegay JN (2002) Eccentric contraction injury in dystrophic canine muscle. Arch Phys Med Rehabil 83(11):1572\u20131578","journal-title":"Arch Phys Med Rehabil"},{"issue":"5","key":"9330_CR24","doi-asserted-by":"crossref","first-page":"823","DOI":"10.1093\/hmg\/7.5.823","volume":"7","author":"RH Crosbie","year":"1998","unstructured":"Crosbie RH, Straub V, Yun HY, Lee JC, Rafael JA, Chamberlain JS, Dawson VL, Dawson TM, Campbell KP (1998) mdx muscle pathology is independent of nNOS perturbation. Hum Mol Genet 7(5):823\u2013829","journal-title":"Hum Mol Genet"},{"issue":"10","key":"9330_CR25","doi-asserted-by":"crossref","first-page":"1871","DOI":"10.1006\/jmcc.2001.1453","volume":"33","author":"L Dalla Libera","year":"2001","unstructured":"Dalla Libera L, Sabbadini R, Renken C, Ravara B, Sandri M, Betto R, Angelini A, Vescovo G (2001) Apoptosis in the skeletal muscle of rats with heart failure is associated with increased serum levels of TNF-alpha and sphingosine. J Mol Cell Cardiol 33(10):1871\u20131878","journal-title":"J Mol Cell Cardiol"},{"issue":"17","key":"9330_CR26","doi-asserted-by":"crossref","first-page":"1309","DOI":"10.1212\/WNL.0b013e3182518302","volume":"78","author":"L Pasquale De","year":"2012","unstructured":"De Pasquale L, D\u2019Amico A, Verardo M, Petrini S, Bertini E, De Benedetti F (2012) Increased muscle expression of interleukin-17 in Duchenne muscular dystrophy. Neurology 78(17):1309\u20131314","journal-title":"Neurology"},{"issue":"45","key":"9330_CR27","doi-asserted-by":"crossref","first-page":"32486","DOI":"10.1074\/jbc.274.45.32486","volume":"274","author":"MH Disatnik","year":"1999","unstructured":"Disatnik MH, Rando TA (1999) Integrin-mediated muscle cell spreading. The role of protein kinase c in outside-in and inside-out signaling and evidence of integrin cross-talk. J Biol Chem 274(45):32486\u201332492","journal-title":"J Biol Chem"},{"issue":"1","key":"9330_CR28","doi-asserted-by":"crossref","first-page":"77","DOI":"10.1016\/S0022-510X(98)00258-5","volume":"161","author":"MH Disatnik","year":"1998","unstructured":"Disatnik MH, Dhawan J, Yu Y, Beal MF, Whirl MM, Franco AA, Rando TA (1998) Evidence of oxidative stress in mdx mouse muscle: studies of the pre-necrotic state. J Neurol Sci 161(1):77\u201384","journal-title":"J Neurol Sci"},{"issue":"5","key":"9330_CR29","doi-asserted-by":"crossref","first-page":"784","DOI":"10.1002\/(SICI)1097-4598(200005)23:5<784::AID-MUS17>3.0.CO;2-Y","volume":"23","author":"MH Disatnik","year":"2000","unstructured":"Disatnik MH, Chamberlain JS, Rando TA (2000) Dystrophin mutations predict cellular susceptibility to oxidative stress. Muscle Nerve 23(5):784\u2013792","journal-title":"Muscle Nerve"},{"issue":"2","key":"9330_CR30","doi-asserted-by":"crossref","first-page":"C616","DOI":"10.1152\/ajpcell.00425.2005","volume":"290","author":"OM Dorchies","year":"2006","unstructured":"Dorchies OM, Wagner S, Vuadens O, Waldhauser K, Buetler TM, Kucera P, Ruegg UT (2006) Green tea extract and its major polyphenol (-)-epigallocatechin gallate improve muscle function in a mouse model for Duchenne muscular dystrophy. Am J Physiol Cell Physiol 290(2):C616\u2013C625","journal-title":"Am J Physiol Cell Physiol"},{"issue":"10","key":"9330_CR31","doi-asserted-by":"crossref","first-page":"1105","DOI":"10.1002\/mus.880151008","volume":"15","author":"EE Dupont-Versteegden","year":"1992","unstructured":"Dupont-Versteegden EE, McCarter RJ (1992) Differential expression of muscular dystrophy in diaphragm versus hindlimb muscles of mdx mice. Muscle Nerve 15(10):1105\u20131110","journal-title":"Muscle Nerve"},{"issue":"3","key":"9330_CR32","doi-asserted-by":"crossref","first-page":"298","DOI":"10.1002\/mus.20579","volume":"34","author":"WJ Durham","year":"2006","unstructured":"Durham WJ, Arbogast S, Gerken E, Li YP, Reid MB (2006) Progressive nuclear factor-kappaB activation resistant to inhibition by contraction and curcumin in mdx mice. Muscle Nerve 34(3):298\u2013303","journal-title":"Muscle Nerve"},{"issue":"2","key":"9330_CR33","doi-asserted-by":"crossref","first-page":"168","DOI":"10.1007\/s11910-001-0013-y","volume":"1","author":"DM Escolar","year":"2001","unstructured":"Escolar DM, Scacheri CG (2001) Pharmacologic and genetic therapy for childhood muscular dystrophies. Curr Neurol Neurosci Rep 1(2):168\u2013174","journal-title":"Curr Neurol Neurosci Rep"},{"issue":"6","key":"9330_CR34","doi-asserted-by":"crossref","first-page":"705","DOI":"10.1096\/fj.05-4661fje","volume":"20","author":"K Fecchi","year":"2006","unstructured":"Fecchi K, Volonte D, Hezel MP, Schmeck K, Galbiati F (2006) Spatial and temporal regulation of GLUT4 translocation by flotillin-1 and caveolin-3 in skeletal muscle cells. FASEB J 20(6):705\u2013707","journal-title":"FASEB J"},{"issue":"11","key":"9330_CR35","doi-asserted-by":"crossref","first-page":"1164","DOI":"10.1002\/mus.880111110","volume":"11","author":"GM Fenichel","year":"1988","unstructured":"Fenichel GM, Brooke MH, Griggs RC, Mendell JR, Miller JP, Moxley RT 3rd, Park JH, Provine MA, Florence J, Kaiser KK et al (1988) Clinical investigation in Duchenne muscular dystrophy: penicillamine and vitamin E. Muscle Nerve 11(11):1164\u20131168","journal-title":"Muscle Nerve"},{"issue":"6","key":"9330_CR36","doi-asserted-by":"crossref","first-page":"1349","DOI":"10.1089\/ars.2008.2378","volume":"11","author":"AB Fisher","year":"2009","unstructured":"Fisher AB (2009) Redox signaling across cell membranes. Antioxid Redox Signal 11(6):1349\u20131356","journal-title":"Antioxid Redox Signal"},{"issue":"10","key":"9330_CR37","doi-asserted-by":"crossref","first-page":"435","DOI":"10.1016\/S1471-4914(01)02105-0","volume":"7","author":"F Galbiati","year":"2001","unstructured":"Galbiati F, Razani B, Lisanti MP (2001) Caveolae and caveolin-3 in muscular dystrophy. Trends Mol Med 7(10):435\u2013441","journal-title":"Trends Mol Med"},{"issue":"Pt 13","key":"9330_CR38","doi-asserted-by":"crossref","first-page":"2246","DOI":"10.1242\/jcs.032003","volume":"121","author":"OL Gervasio","year":"2008","unstructured":"Gervasio OL, Whitehead NP, Yeung EW, Phillips WD, Allen DG (2008) TRPC1 binds to caveolin-3 and is regulated by Src kinase - role in Duchenne muscular dystrophy. J Cell Sci 121(Pt 13):2246\u20132255","journal-title":"J Cell Sci"},{"issue":"4","key":"9330_CR39","doi-asserted-by":"crossref","first-page":"215","DOI":"10.1038\/12034","volume":"1","author":"RM Grady","year":"1999","unstructured":"Grady RM, Grange RW, Lau KS, Maimone MM, Nichol MC, Stull JT, Sanes JR (1999) Role for alpha-dystrobrevin in the pathogenesis of dystrophin-dependent muscular dystrophies. Nat Cell Biol 1(4):215\u2013220","journal-title":"Nat Cell Biol"},{"issue":"6","key":"9330_CR40","doi-asserted-by":"crossref","first-page":"676","DOI":"10.1096\/fj.03-1024com","volume":"18","author":"MD Grounds","year":"2004","unstructured":"Grounds MD, Torrisi J (2004) Anti-TNFalpha (Remicade) therapy protects dystrophic skeletal muscle from necrosis. FASEB J 18(6):676\u2013682","journal-title":"FASEB J"},{"issue":"3","key":"9330_CR41","doi-asserted-by":"crossref","first-page":"428","DOI":"10.1002\/1097-4598(200103)24:3<428::AID-MUS1018>3.0.CO;2-E","volume":"24","author":"JV Hartel","year":"2001","unstructured":"Hartel JV, Granchelli JA, Hudecki MS, Pollina CM, Gosselin LE (2001) Impact of prednisone on TGF-beta1 and collagen in diaphragm muscle from mdx mice. Muscle Nerve 24(3):428\u2013432","journal-title":"Muscle Nerve"},{"issue":"5","key":"9330_CR42","doi-asserted-by":"crossref","first-page":"260","DOI":"10.1055\/s-2007-979768","volume":"26","author":"E Hauser","year":"1995","unstructured":"Hauser E, Hoger H, Bittner R, Widhalm K, Herkner K, Lubec G (1995) Oxyradical damage and mitochondrial enzyme activities in the mdx mouse. Neuropediatrics 26(5):260\u2013262","journal-title":"Neuropediatrics"},{"issue":"1","key":"9330_CR43","doi-asserted-by":"crossref","first-page":"357","DOI":"10.1097\/00001756-199612200-00070","volume":"8","author":"JW Haycock","year":"1996","unstructured":"Haycock JW, MacNeil S, Jones P, Harris JB, Mantle D (1996) Oxidative damage to muscle protein in Duchenne muscular dystrophy. NeuroReport 8(1):357\u2013361","journal-title":"NeuroReport"},{"key":"9330_CR44","doi-asserted-by":"crossref","unstructured":"Hess DR (2012) The growing role of noninvasive ventilation in patients requiring prolonged mechanical ventilation. Respir Care 57 (6):900\u2013918; discussion 918\u2013920","DOI":"10.4187\/respcare.01692"},{"issue":"6","key":"9330_CR45","doi-asserted-by":"crossref","first-page":"1509","DOI":"10.2353\/ajpath.2008.071009","volume":"172","author":"K Hnia","year":"2008","unstructured":"Hnia K, Gayraud J, Hugon G, Ramonatxo M, De La Porte S, Matecki S, Mornet D (2008) l-arginine decreases inflammation and modulates the nuclear factor-kappaB\/matrix metalloproteinase cascade in mdx muscle fibers. Am J Pathol 172(6):1509\u20131519","journal-title":"Am J Pathol"},{"issue":"9\u201310","key":"9330_CR46","doi-asserted-by":"crossref","first-page":"591","DOI":"10.1016\/j.nmd.2006.06.011","volume":"16","author":"S Hodgetts","year":"2006","unstructured":"Hodgetts S, Radley H, Davies M, Grounds MD (2006) Reduced necrosis of dystrophic muscle by depletion of host neutrophils, or blocking TNFalpha function with Etanercept in mdx mice. Neuromuscul Disord 16(9\u201310):591\u2013602","journal-title":"Neuromuscul Disord"},{"issue":"2","key":"9330_CR47","doi-asserted-by":"crossref","first-page":"131","DOI":"10.1023\/A:1020256316659","volume":"23","author":"S Hoshino","year":"2002","unstructured":"Hoshino S, Ohkoshi N, Ishii A, Shoji S (2002) The expression of alpha-dystrobrevin and dystrophin during skeletal muscle regeneration. J Muscle Res Cell Motil 23(2):131\u2013138","journal-title":"J Muscle Res Cell Motil"},{"issue":"8","key":"9330_CR48","doi-asserted-by":"crossref","first-page":"2539","DOI":"10.1096\/fj.09-129833","volume":"23","author":"P Huang","year":"2009","unstructured":"Huang P, Zhao XS, Fields M, Ransohoff RM, Zhou L (2009) Imatinib attenuates skeletal muscle dystrophy in mdx mice. FASEB J 23(8):2539\u20132548","journal-title":"FASEB J"},{"issue":"1","key":"9330_CR49","doi-asserted-by":"crossref","first-page":"47","DOI":"10.1016\/j.nmd.2010.09.006","volume":"21","author":"Y Ishikawa","year":"2011","unstructured":"Ishikawa Y, Miura T, Aoyagi T, Ogata H, Hamada S, Minami R (2011) Duchenne muscular dystrophy: survival by cardio-respiratory interventions. Neuromuscul Disord 21(1):47\u201351","journal-title":"Neuromuscul Disord"},{"issue":"6","key":"9330_CR50","doi-asserted-by":"crossref","first-page":"456","DOI":"10.1016\/S0960-8966(03)00066-X","volume":"13","author":"KJ Jones","year":"2003","unstructured":"Jones KJ, Compton AG, Yang N, Mills MA, Peters MF, Mowat D, Kunkel LM, Froehner SC, North KN (2003) Deficiency of the syntrophins and alpha-dystrobrevin in patients with inherited myopathy. Neuromuscul Disord 13(6):456\u2013467","journal-title":"Neuromuscul Disord"},{"issue":"1","key":"9330_CR51","doi-asserted-by":"crossref","first-page":"145","DOI":"10.1016\/j.freeradbiomed.2007.04.003","volume":"43","author":"JJ Kaczor","year":"2007","unstructured":"Kaczor JJ, Hall JE, Payne E, Tarnopolsky MA (2007) Low intensity training decreases markers of oxidative stress in skeletal muscle of mdx mice. Free Radic Biol Med 43(1):145\u2013154","journal-title":"Free Radic Biol Med"},{"issue":"4","key":"9330_CR52","doi-asserted-by":"crossref","first-page":"2193","DOI":"10.1074\/jbc.274.4.2193","volume":"274","author":"S Kameya","year":"1999","unstructured":"Kameya S, Miyagoe Y, Nonaka I, Ikemoto T, Endo M, Hanaoka K, Nabeshima Y, Takeda S (1999) Alpha1-syntrophin gene disruption results in the absence of neuronal-type nitric-oxide synthase at the sarcolemma but does not induce muscle degeneration. J Biol Chem 274(4):2193\u20132200","journal-title":"J Biol Chem"},{"issue":"6\u20137","key":"9330_CR53","doi-asserted-by":"crossref","first-page":"517","DOI":"10.1016\/S0960-8966(01)00215-2","volume":"11","author":"HJ Kaminski","year":"2001","unstructured":"Kaminski HJ, Andrade FH (2001) Nitric oxide: biologic effects on muscle and role in muscle diseases. Neuromuscul Disord 11(6\u20137):517\u2013524","journal-title":"Neuromuscul Disord"},{"issue":"9","key":"9330_CR54","doi-asserted-by":"crossref","first-page":"1597","DOI":"10.1016\/j.freeradbiomed.2012.01.015","volume":"52","author":"J-H Kim","year":"2012","unstructured":"Kim J-H, Lawler JM (2012) Amplification of proinflammatory phenotype, damage, and weakness by oxidative stress in the diaphragm muscle of mdx mice. Free Radic Biol Med 52(9):1597\u20131606","journal-title":"Free Radic Biol Med"},{"issue":"959","key":"9330_CR55","first-page":"8","volume":"22","author":"J-H Kim","year":"2008","unstructured":"Kim J-H, Kwak HB, Lawler JM (2008) NAD(P)H oxidase inhibition upregulates anti-apoptotic BAG-4 protein expression in the mdx diaphragm. FASEB J 22(959):8","journal-title":"FASEB J"},{"issue":"5","key":"9330_CR56","doi-asserted-by":"crossref","first-page":"1476","DOI":"10.1152\/japplphysiol.00708.2007","volume":"104","author":"DJ Kosek","year":"2008","unstructured":"Kosek DJ, Bamman MM (2008) Modulation of the dystrophin-associated protein complex in response to resistance training in young and older men. J Appl Physiol 104(5):1476\u20131484","journal-title":"J Appl Physiol"},{"issue":"3","key":"9330_CR57","doi-asserted-by":"crossref","first-page":"386","DOI":"10.1096\/fj.02-0542com","volume":"17","author":"A Kumar","year":"2003","unstructured":"Kumar A, Boriek AM (2003) Mechanical stress activates the nuclear factor-kappaB pathway in skeletal muscle fibers: a possible role in Duchenne muscular dystrophy. FASEB J 17(3):386\u2013396","journal-title":"FASEB J"},{"issue":"7","key":"9330_CR58","doi-asserted-by":"crossref","first-page":"434","DOI":"10.1007\/s00109-004-0555-y","volume":"82","author":"A Kumar","year":"2004","unstructured":"Kumar A, Takada Y, Boriek AM, Aggarwal BB (2004) Nuclear factor-kappaB: its role in health and disease. J Mol Med 82(7):434\u2013448","journal-title":"J Mol Med"},{"issue":"3","key":"9330_CR59","doi-asserted-by":"crossref","first-page":"624","DOI":"10.1172\/JCI36612","volume":"119","author":"Y Lai","year":"2009","unstructured":"Lai Y, Thomas GD, Yue Y, Yang HT, Li D, Long C, Judge L, Bostick B, Chamberlain JS, Terjung RL, Duan D (2009) Dystrophins carrying spectrin-like repeats 16 and 17 anchor nNOS to the sarcolemma and enhance exercise performance in a mouse model of muscular dystrophy. J Clin Invest 119(3):624\u2013635","journal-title":"J Clin Invest"},{"issue":"1","key":"9330_CR60","doi-asserted-by":"crossref","first-page":"9","DOI":"10.1016\/S0891-5849(03)00186-2","volume":"35","author":"JM Lawler","year":"2003","unstructured":"Lawler JM, Song W, Demaree SR (2003) Hindlimb unloading increases oxidative stress and disrupts antioxidant capacity in skeletal muscle. Free Radic Biol Med 35(1):9\u201316","journal-title":"Free Radic Biol Med"},{"key":"9330_CR61","doi-asserted-by":"crossref","unstructured":"Lawler JM, Hord JM, Yang Lee, Kumar Joshi, and Jong-Hee Kim (2011) Redox regulation of caveolin-3 and MMP-9 in the diaphragm of mdx mice. FASEB J LB:519","DOI":"10.1096\/fasebj.25.1_supplement.lb519"},{"issue":"14","key":"9330_CR62","doi-asserted-by":"crossref","first-page":"2584","DOI":"10.1093\/hmg\/ddp191","volume":"18","author":"H Li","year":"2009","unstructured":"Li H, Mittal A, Makonchuk DY, Bhatnagar S, Kumar A (2009) Matrix metalloproteinase-9 inhibition ameliorates pathogenesis and improves skeletal muscle regeneration in muscular dystrophy. Hum Mol Genet 18(14):2584\u20132598","journal-title":"Hum Mol Genet"},{"issue":"4","key":"9330_CR63","doi-asserted-by":"crossref","first-page":"456","DOI":"10.1002\/mus.20139","volume":"30","author":"JH Lim","year":"2004","unstructured":"Lim JH, Kim DY, Bang MS (2004) Effects of exercise and steroid on skeletal muscle apoptosis in the mdx mouse. Muscle Nerve 30(4):456\u2013462","journal-title":"Muscle Nerve"},{"issue":"8","key":"9330_CR64","doi-asserted-by":"crossref","first-page":"557","DOI":"10.1111\/j.1440-1681.2004.04026.x","volume":"31","author":"GS Lynch","year":"2004","unstructured":"Lynch GS (2004) Role of contraction-induced injury in the mechanisms of muscle damage in muscular dystrophy. Clin Exp Pharmacol Physiol 31(8):557\u2013561","journal-title":"Clin Exp Pharmacol Physiol"},{"issue":"6 Pt 1","key":"9330_CR65","doi-asserted-by":"crossref","first-page":"C2063","DOI":"10.1152\/ajpcell.1997.272.6.C2063","volume":"272","author":"GS Lynch","year":"1997","unstructured":"Lynch GS, Rafael JA, Hinkle RT, Cole NM, Chamberlain JS, Faulkner JA (1997) Contractile properties of diaphragm muscle segments from old mdx and old transgenic mdx mice. Am J Physiol 272(6 Pt 1):C2063\u2013C2068","journal-title":"Am J Physiol"},{"issue":"Pt 2","key":"9330_CR66","doi-asserted-by":"crossref","first-page":"591","DOI":"10.1111\/j.1469-7793.2001.00591.x","volume":"535","author":"GS Lynch","year":"2001","unstructured":"Lynch GS, Hinkle RT, Chamberlain JS, Brooks SV, Faulkner JA (2001) Force and power output of fast and slow skeletal muscles from mdx mice 6\u201328\u00a0months old. J Physiol 535(Pt 2):591\u2013600","journal-title":"J Physiol"},{"issue":"1","key":"9330_CR67","doi-asserted-by":"crossref","first-page":"2","DOI":"10.1002\/mus.880170103","volume":"17","author":"K Matsumura","year":"1994","unstructured":"Matsumura K, Campbell KP (1994) Dystrophin-glycoprotein complex: its role in the molecular pathogenesis of muscular dystrophies. Muscle Nerve 17(1):2\u201315","journal-title":"Muscle Nerve"},{"issue":"2","key":"9330_CR68","doi-asserted-by":"crossref","first-page":"150","DOI":"10.1164\/rccm.200601-142OC","volume":"175","author":"JM McClung","year":"2007","unstructured":"McClung JM, Kavazis AN, DeRuisseau KC, Falk DJ, Deering MA, Lee Y, Sugiura T, Powers SK (2007) Caspase-3 regulation of diaphragm myonuclear domain during mechanical ventilation-induced atrophy. Am J Respir Crit Care Med 175(2):150\u2013159","journal-title":"Am J Respir Crit Care Med"},{"issue":"988","key":"9330_CR69","doi-asserted-by":"crossref","first-page":"1143","DOI":"10.1126\/science.172.3988.1143","volume":"172","author":"JR Mendell","year":"1971","unstructured":"Mendell JR, Engel WK, Derrer EC (1971) Duchenne muscular dystrophy: functional ischemia reproduces its characteristic lesions. Science 172(988):1143\u20131145","journal-title":"Science"},{"issue":"15","key":"9330_CR70","doi-asserted-by":"crossref","first-page":"1429","DOI":"10.1056\/NEJMoa1000228","volume":"363","author":"JR Mendell","year":"2010","unstructured":"Mendell JR, Campbell K, Rodino-Klapac L, Sahenk Z, Shilling C, Lewis S, Bowles D, Gray S, Li C, Galloway G, Malik V, Coley B, Clark KR, Li J, Xiao X, Samulski J, McPhee SW, Samulski RJ, Walker CM (2010) Dystrophin immunity in Duchenne\u2019s muscular dystrophy. N Engl J Med 363(15):1429\u20131437","journal-title":"N Engl J Med"},{"issue":"3","key":"9330_CR71","doi-asserted-by":"crossref","first-page":"918","DOI":"10.2353\/ajpath.2006.050673","volume":"168","author":"S Messina","year":"2006","unstructured":"Messina S, Altavilla D, Aguennouz M, Seminara P, Minutoli L, Monici MC, Bitto A, Mazzeo A, Marini H, Squadrito F, Vita G (2006a) Lipid peroxidation inhibition blunts nuclear factor-kappaB activation, reduces skeletal muscle degeneration, and enhances muscle function in mdx mice. Am J Pathol 168(3):918\u2013926","journal-title":"Am J Pathol"},{"issue":"1","key":"9330_CR72","doi-asserted-by":"crossref","first-page":"234","DOI":"10.1016\/j.expneurol.2005.11.021","volume":"198","author":"S Messina","year":"2006","unstructured":"Messina S, Bitto A, Aguennouz M, Minutoli L, Monici MC, Altavilla D, Squadrito F, Vita G (2006b) Nuclear factor kappa-B blockade reduces skeletal muscle degeneration and enhances muscle function in Mdx mice. Exp Neurol 198(1):234\u2013241","journal-title":"Exp Neurol"},{"issue":"2","key":"9330_CR73","doi-asserted-by":"crossref","first-page":"349","DOI":"10.1016\/j.expneurol.2009.09.015","volume":"220","author":"S Messina","year":"2009","unstructured":"Messina S, Bitto A, Aguennouz M, Mazzeo A, Migliorato A, Polito F, Irrera N, Altavilla D, Vita GL, Russo M, Naro A, De Pasquale MG, Rizzuto E, Musaro A, Squadrito F, Vita G (2009) Flavocoxid counteracts muscle necrosis and improves functional properties in mdx mice: a comparison study with methylprednisolone. Exp Neurol 220(2):349\u2013358","journal-title":"Exp Neurol"},{"issue":"1","key":"9330_CR74","first-page":"16","volume":"30","author":"S Messina","year":"2011","unstructured":"Messina S, Vita GL, Aguennouz M, Sframeli M, Romeo S, Rodolico C, Vita G (2011) Activation of NF-kappaB pathway in Duchenne muscular dystrophy: relation to age. Acta Myol 30(1):16\u201323","journal-title":"Acta Myol"},{"issue":"3","key":"9330_CR75","doi-asserted-by":"crossref","first-page":"164","DOI":"10.1002\/jemt.1167","volume":"55","author":"Y Miyagoe-Suzuki","year":"2001","unstructured":"Miyagoe-Suzuki Y, Takeda SI (2001) Association of neuronal nitric oxide synthase (nNOS) with alpha1-syntrophin at the sarcolemma. Microsc Res Tech 55(3):164\u2013170","journal-title":"Microsc Res Tech"},{"issue":"6","key":"9330_CR76","doi-asserted-by":"crossref","first-page":"993","DOI":"10.1212\/01.WNL.0000049913.27181.51","volume":"60","author":"MC Monici","year":"2003","unstructured":"Monici MC, Aguennouz M, Mazzeo A, Messina C, Vita G (2003) Activation of nuclear factor-kappaB in inflammatory myopathies and Duchenne muscular dystrophy. Neurology 60(6):993\u2013997","journal-title":"Neurology"},{"issue":"6","key":"9330_CR77","doi-asserted-by":"crossref","first-page":"881","DOI":"10.1038\/labinvest.3780092","volume":"80","author":"J Morrison","year":"2000","unstructured":"Morrison J, Lu QL, Pastoret C, Partridge T, Bou-Gharios G (2000) T-cell-dependent fibrosis in the mdx dystrophic mouse. Lab Invest 80(6):881\u2013891","journal-title":"Lab Invest"},{"issue":"5","key":"9330_CR78","doi-asserted-by":"crossref","first-page":"489","DOI":"10.1023\/B:HIJO.0000045947.83628.a7","volume":"35","author":"Y Nakae","year":"2004","unstructured":"Nakae Y, Stoward PJ, Kashiyama T, Shono M, Akagi A, Matsuzaki T, Nonaka I (2004) Early onset of lipofuscin accumulation in dystrophin-deficient skeletal muscles of DMD patients and mdx mice. J Mol Histol 35(5):489\u2013499","journal-title":"J Mol Histol"},{"issue":"4","key":"9330_CR79","doi-asserted-by":"crossref","first-page":"489","DOI":"10.1007\/s00418-008-0390-2","volume":"129","author":"Y Nakae","year":"2008","unstructured":"Nakae Y, Hirasaka K, Goto J, Nikawa T, Shono M, Yoshida M, Stoward PJ (2008) Subcutaneous injection, from birth, of epigallocatechin-3-gallate, a component of green tea, limits the onset of muscular dystrophy in mdx mice: a quantitative histological, immunohistochemical and electrophysiological study. Histochem Cell Biol 129(4):489\u2013501","journal-title":"Histochem Cell Biol"},{"issue":"Pt 3","key":"9330_CR80","doi-asserted-by":"crossref","first-page":"833","DOI":"10.1113\/jphysiol.2003.051912","volume":"553","author":"HX Nguyen","year":"2003","unstructured":"Nguyen HX, Tidball JG (2003) Null mutation of gp91phox reduces muscle membrane lysis during muscle inflammation in mice. J Physiol 553(Pt 3):833\u2013841","journal-title":"J Physiol"},{"issue":"4","key":"9330_CR81","doi-asserted-by":"crossref","first-page":"531","DOI":"10.1016\/S1016-8478(23)17614-X","volume":"25","author":"Y Pan","year":"2008","unstructured":"Pan Y, Chen C, Shen Y, Zhu CH, Wang G, Wang XC, Chen HQ, Zhu MS (2008) Curcumin alleviates dystrophic muscle pathology in mdx mice. Mol Cells 25(4):531\u2013537","journal-title":"Mol Cells"},{"issue":"5","key":"9330_CR82","doi-asserted-by":"crossref","first-page":"353","DOI":"10.1111\/j.1365-2990.1991.tb00735.x","volume":"17","author":"T Partridge","year":"1991","unstructured":"Partridge T (1991) Animal models of muscular dystrophy\u2013what can they teach us? Neuropathol Appl Neurobiol 17(5):353\u2013363","journal-title":"Neuropathol Appl Neurobiol"},{"issue":"10","key":"9330_CR83","doi-asserted-by":"crossref","first-page":"1147","DOI":"10.1002\/mus.880181011","volume":"18","author":"C Pastoret","year":"1995","unstructured":"Pastoret C, Sebille A (1995) Age-related differences in regeneration of dystrophic (mdx) and normal muscle in the mouse. Muscle Nerve 18(10):1147\u20131154","journal-title":"Muscle Nerve"},{"issue":"1","key":"9330_CR84","doi-asserted-by":"crossref","first-page":"81","DOI":"10.1083\/jcb.138.1.81","volume":"138","author":"MF Peters","year":"1997","unstructured":"Peters MF, Adams ME, Froehner SC (1997) Differential association of syntrophin pairs with the dystrophin complex. J Cell Biol 138(1):81\u201393","journal-title":"J Cell Biol"},{"issue":"5","key":"9330_CR85","doi-asserted-by":"crossref","first-page":"375","DOI":"10.1080\/08830180802302389","volume":"27","author":"JM Peterson","year":"2008","unstructured":"Peterson JM, Guttridge DC (2008) Skeletal muscle diseases, inflammation, and NF-kappaB signaling: insights and opportunities for therapeutic intervention. Int Rev Immunol 27(5):375\u2013387","journal-title":"Int Rev Immunol"},{"issue":"3","key":"9330_CR86","doi-asserted-by":"crossref","first-page":"263","DOI":"10.1093\/hmg\/11.3.263","volume":"11","author":"JD Porter","year":"2002","unstructured":"Porter JD, Khanna S, Kaminski HJ, Rao JS, Merriam AP, Richmonds CR, Leahy P, Li J, Guo W, Andrade FH (2002) A chronic inflammatory response dominates the skeletal muscle molecular signature in dystrophin-deficient mdx mice. Hum Mol Genet 11(3):263\u2013272","journal-title":"Hum Mol Genet"},{"issue":"6","key":"9330_CR87","doi-asserted-by":"crossref","first-page":"2389","DOI":"10.1152\/japplphysiol.01202.2006","volume":"102","author":"SK Powers","year":"2007","unstructured":"Powers SK, Kavazis AN, McClung JM (2007) Oxidative stress and disuse muscle atrophy. J Appl Physiol 102(6):2389\u20132397","journal-title":"J Appl Physiol"},{"issue":"6\u20137","key":"9330_CR88","doi-asserted-by":"crossref","first-page":"379","DOI":"10.1016\/S0960-8966(97)00096-5","volume":"7","author":"RJ Ragusa","year":"1997","unstructured":"Ragusa RJ, Chow CK, Porter JD (1997) Oxidative stress as a potential pathogenic mechanism in an animal model of Duchenne muscular dystrophy. Neuromuscul Disord 7(6\u20137):379\u2013386","journal-title":"Neuromuscul Disord"},{"issue":"12","key":"9330_CR89","doi-asserted-by":"crossref","first-page":"1575","DOI":"10.1002\/mus.1192","volume":"24","author":"TA Rando","year":"2001","unstructured":"Rando TA (2001a) The dystrophin-glycoprotein complex, cellular signaling, and the regulation of cell survival in the muscular dystrophies. Muscle Nerve 24(12):1575\u20131594","journal-title":"Muscle Nerve"},{"issue":"4","key":"9330_CR90","doi-asserted-by":"crossref","first-page":"223","DOI":"10.1002\/jemt.1172","volume":"55","author":"TA Rando","year":"2001","unstructured":"Rando TA (2001b) Role of nitric oxide in the pathogenesis of muscular dystrophies: a \u201ctwo hit\u201d hypothesis of the cause of muscle necrosis. Microsc Res Tech 55(4):223\u2013235","journal-title":"Microsc Res Tech"},{"issue":"11 Suppl","key":"9330_CR91","doi-asserted-by":"crossref","first-page":"S175","DOI":"10.1097\/00002060-200211001-00018","volume":"81","author":"TA Rando","year":"2002","unstructured":"Rando TA (2002) Oxidative stress and the pathogenesis of muscular dystrophies. Am J Phys Med Rehabil 81(11 Suppl):S175\u2013S186","journal-title":"Am J Phys Med Rehabil"},{"issue":"1","key":"9330_CR92","doi-asserted-by":"crossref","first-page":"14","DOI":"10.1016\/S0960-8966(97)00124-7","volume":"8","author":"TA Rando","year":"1998","unstructured":"Rando TA, Disatnik MH, Yu Y, Franco A (1998) Muscle cells from mdx mice have an increased susceptibility to oxidative stress. Neuromuscul Disord 8(1):14\u201321","journal-title":"Neuromuscul Disord"},{"issue":"9","key":"9330_CR93","doi-asserted-by":"crossref","first-page":"1217","DOI":"10.1016\/S0891-5849(03)00141-2","volume":"34","author":"MC Rodriguez","year":"2003","unstructured":"Rodriguez MC, Tarnopolsky MA (2003) Patients with dystrophinopathy show evidence of increased oxidative stress. Free Radic Biol Med 34(9):1217\u20131220","journal-title":"Free Radic Biol Med"},{"issue":"5","key":"9330_CR94","doi-asserted-by":"crossref","first-page":"266","DOI":"10.1001\/archneur.1979.00500410044005","volume":"36","author":"RI Roelofs","year":"1979","unstructured":"Roelofs RI, de Arango GS, Law PK, Kinsman D, Buchanan DC, Park JH (1979) Treatment of Duchenne\u2019s muscular dystrophy with penicillamine. Results of a double-blind trial. Arch Neurol 36(5):266\u2013268","journal-title":"Arch Neurol"},{"issue":"12","key":"9330_CR95","doi-asserted-by":"crossref","first-page":"1373","DOI":"10.1016\/S1357-2725(99)00063-1","volume":"31","author":"M Sandri","year":"1999","unstructured":"Sandri M, Carraro U (1999) Apoptosis of skeletal muscles during development and disease. Int J Biochem Cell Biol 31(12):1373\u20131390","journal-title":"Int J Biochem Cell Biol"},{"issue":"2","key":"9330_CR96","doi-asserted-by":"crossref","first-page":"194","DOI":"10.1113\/expphysiol.2010.054379","volume":"96","author":"JT Selsby","year":"2011","unstructured":"Selsby JT (2011) Increased catalase expression improves muscle function in mdx mice. Exp Physiol 96(2):194\u2013202","journal-title":"Exp Physiol"},{"issue":"17","key":"9330_CR97","doi-asserted-by":"crossref","first-page":"1873","DOI":"10.1093\/hmg\/ddh204","volume":"13","author":"T Shiao","year":"2004","unstructured":"Shiao T, Fond A, Deng B, Wehling-Henricks M, Adams ME, Froehner SC, Tidball JG (2004) Defects in neuromuscular junction structure in dystrophic muscle are corrected by expression of a NOS transgene in dystrophin-deficient muscles, but not in muscles lacking alpha- and beta1-syntrophins. Hum Mol Genet 13(17):1873\u20131884","journal-title":"Hum Mol Genet"},{"issue":"2","key":"9330_CR98","doi-asserted-by":"crossref","first-page":"192","DOI":"10.1002\/1097-4598(200102)24:2<192::AID-MUS40>3.0.CO;2-S","volume":"24","author":"RQ Skrabek","year":"2001","unstructured":"Skrabek RQ, Anderson JE (2001) Metabolic shifts and myocyte hypertrophy in deflazacort treatment of mdx mouse cardiomyopathy. Muscle Nerve 24(2):192\u2013202","journal-title":"Muscle Nerve"},{"issue":"6\u20137","key":"9330_CR99","doi-asserted-by":"crossref","first-page":"556","DOI":"10.1016\/S0960-8966(01)00198-5","volume":"11","author":"MJ Spencer","year":"2001","unstructured":"Spencer MJ, Tidball JG (2001) Do immune cells promote the pathology of dystrophin-deficient myopathies? Neuromuscul Disord 11(6\u20137):556\u2013564","journal-title":"Neuromuscul Disord"},{"issue":"11","key":"9330_CR100","doi-asserted-by":"crossref","first-page":"2745","DOI":"10.1172\/JCI119464","volume":"99","author":"MJ Spencer","year":"1997","unstructured":"Spencer MJ, Walsh CM, Dorshkind KA, Rodriguez EM, Tidball JG (1997) Myonuclear apoptosis in dystrophic mdx muscle occurs by perforin-mediated cytotoxicity. J Clin Invest 99(11):2745\u20132751","journal-title":"J Clin Invest"},{"issue":"8","key":"9330_CR101","doi-asserted-by":"crossref","first-page":"612","DOI":"10.1016\/S0960-8966(00)00160-7","volume":"10","author":"MJ Spencer","year":"2000","unstructured":"Spencer MJ, Marino MW, Winckler WM (2000) Altered pathological progression of diaphragm and quadriceps muscle in TNF-deficient, dystrophin-deficient mice. Neuromuscul Disord 10(8):612\u2013619","journal-title":"Neuromuscul Disord"},{"issue":"2","key":"9330_CR102","doi-asserted-by":"crossref","first-page":"235","DOI":"10.1006\/clim.2000.4966","volume":"98","author":"MJ Spencer","year":"2001","unstructured":"Spencer MJ, Montecino-Rodriguez E, Dorshkind K, Tidball JG (2001) Helper (CD4(+)) and cytotoxic (CD8(+)) T cells promote the pathology of dystrophin-deficient muscle. Clin Immunol 98(2):235\u2013243","journal-title":"Clin Immunol"},{"issue":"5","key":"9330_CR103","doi-asserted-by":"crossref","first-page":"371","DOI":"10.1016\/j.nmd.2008.03.008","volume":"18","author":"CF Spurney","year":"2008","unstructured":"Spurney CF, Knoblach S, Pistilli EE, Nagaraju K, Martin GR, Hoffman EP (2008) Dystrophin-deficient cardiomyopathy in mouse: expression of Nox4 and Lox are associated with fibrosis and altered functional parameters in the heart. Neuromuscul Disord 18(5):371\u2013381","journal-title":"Neuromuscul Disord"},{"issue":"6335","key":"9330_CR104","doi-asserted-by":"crossref","first-page":"536","DOI":"10.1038\/352536a0","volume":"352","author":"HH Stedman","year":"1991","unstructured":"Stedman HH, Sweeney HL, Shrager JB, Maguire HC, Panettieri RA, Petrof B, Narusawa M, Leferovich JM, Sladky JT, Kelly AM (1991) The mdx mouse diaphragm reproduces the degenerative changes of Duchenne muscular dystrophy. Nature 352(6335):536\u2013539","journal-title":"Nature"},{"issue":"6","key":"9330_CR105","doi-asserted-by":"crossref","first-page":"342","DOI":"10.1001\/archneur.1982.00510180020004","volume":"39","author":"LZ Stern","year":"1982","unstructured":"Stern LZ, Ringel SP, Ziter FA, Menander-Huber KB, Ionasescu V, Pellegrino RJ, Snyder RD (1982) Drug trial of superoxide dismutase in Duchenne\u2019s muscular dystrophy. Arch Neurol 39(6):342\u2013346","journal-title":"Arch Neurol"},{"issue":"Pt 3","key":"9330_CR106","doi-asserted-by":"crossref","first-page":"457","DOI":"10.1111\/j.1469-7793.2000.t01-3-00457.x","volume":"522","author":"ED Stevens","year":"2000","unstructured":"Stevens ED, Faulkner JA (2000) The capacity of mdx mouse diaphragm muscle to do oscillatory work. J Physiol 522(Pt 3):457\u2013466","journal-title":"J Physiol"},{"issue":"3","key":"9330_CR107","doi-asserted-by":"crossref","first-page":"173","DOI":"10.1093\/hmg\/10.3.173","volume":"10","author":"Y Sunada","year":"2001","unstructured":"Sunada Y, Ohi H, Hase A, Hosono T, Arata S, Higuchi S, Matsumura K, Shimizu T (2001) Transgenic mice expressing mutant caveolin-3 show severe myopathy associated with increased nNOS activity. Hum Mol Genet 10(3):173\u2013178","journal-title":"Hum Mol Genet"},{"issue":"2","key":"9330_CR108","doi-asserted-by":"crossref","first-page":"138","DOI":"10.5435\/00124635-200203000-00009","volume":"10","author":"M Sussman","year":"2002","unstructured":"Sussman M (2002) Duchenne muscular dystrophy. J Am Acad Orthop Surg 10(2):138\u2013151","journal-title":"J Am Acad Orthop Surg"},{"issue":"4","key":"9330_CR109","doi-asserted-by":"crossref","first-page":"312","DOI":"10.1016\/j.ymgme.2004.06.006","volume":"82","author":"JG Tidball","year":"2004","unstructured":"Tidball JG, Wehling-Henricks M (2004) Expression of a NOS transgene in dystrophin-deficient muscle reduces muscle membrane damage without increasing the expression of membrane-associated cytoskeletal proteins. Mol Genet Metab 82(4):312\u2013320","journal-title":"Mol Genet Metab"},{"issue":"4","key":"9330_CR110","doi-asserted-by":"crossref","first-page":"1677","DOI":"10.1152\/japplphysiol.01145.2006","volume":"102","author":"JG Tidball","year":"2007","unstructured":"Tidball JG, Wehling-Henricks M (2007) The role of free radicals in the pathophysiology of muscular dystrophy. J Appl Physiol 102(4):1677\u20131686","journal-title":"J Appl Physiol"},{"key":"9330_CR111","doi-asserted-by":"crossref","unstructured":"Tkatchenko AV, Le Cam G, L\u00e9ger JJ, Dechesne CA (2000) Large-scale analysis of differential gene expression in the hindlimb muscles and diaphragm of mdx mouse. Biochim Biophys Acta 1500 (1):17\u201330","DOI":"10.1016\/S0925-4439(99)00084-8"},{"issue":"6","key":"9330_CR112","doi-asserted-by":"crossref","first-page":"1289","DOI":"10.1089\/ars.2008.2333","volume":"11","author":"M Ushio-Fukai","year":"2009","unstructured":"Ushio-Fukai M (2009) Compartmentalization of redox signaling through NADPH oxidase-derived ROS. Antioxid Redox Signal 11(6):1289\u20131299","journal-title":"Antioxid Redox Signal"},{"issue":"2","key":"9330_CR113","doi-asserted-by":"crossref","first-page":"109","DOI":"10.1111\/j.1474-9726.2006.00198.x","volume":"5","author":"A Vasilaki","year":"2006","unstructured":"Vasilaki A, Mansouri A, Remmen H, van der Meulen JH, Larkin L, Richardson AG, McArdle A, Faulkner JA, Jackson MJ (2006) Free radical generation by skeletal muscle of adult and old mice: effect of contractile activity. Aging Cell 5(2):109\u2013117","journal-title":"Aging Cell"},{"issue":"45","key":"9330_CR114","doi-asserted-by":"crossref","first-page":"28187","DOI":"10.1074\/jbc.272.45.28187","volume":"272","author":"VJ Venema","year":"1997","unstructured":"Venema VJ, Ju H, Zou R, Venema RC (1997) Interaction of neuronal nitric-oxide synthase with caveolin-3 in skeletal muscle. Identification of a novel caveolin scaffolding\/inhibitory domain. J Biol Chem 272(45):28187\u201328190","journal-title":"J Biol Chem"},{"issue":"5","key":"9330_CR115","doi-asserted-by":"crossref","first-page":"455","DOI":"10.1007\/s004010050733","volume":"94","author":"Y Wakayama","year":"1997","unstructured":"Wakayama Y, Inoue M, Murahashi M, Shibuya S, Jimi T, Kojima H, Oniki H (1997) Ultrastructural localization of alpha 1-syntrophin and neuronal nitric oxide synthase in normal skeletal myofiber, and their relation to each other and to dystrophin. Acta Neuropathol 94(5):455\u2013464","journal-title":"Acta Neuropathol"},{"issue":"2","key":"9330_CR116","doi-asserted-by":"crossref","first-page":"169","DOI":"10.1093\/brain\/77.2.169","volume":"77","author":"JN Walton","year":"1954","unstructured":"Walton JN, Nattrass FJ (1954) On the classification, natural history and treatment of the myopathies. Brain 77(2):169\u2013231","journal-title":"Brain"},{"key":"9330_CR117","doi-asserted-by":"crossref","first-page":"477","DOI":"10.1113\/jphysiol.1993.sp019646","volume":"464","author":"GL Warren","year":"1993","unstructured":"Warren GL, Hayes DA, Lowe DA, Prior BM, Armstrong RB (1993) Materials fatigue initiates eccentric contraction-induced injury in rat soleus muscle. J Physiol 464:477\u2013489","journal-title":"J Physiol"},{"issue":"1","key":"9330_CR118","doi-asserted-by":"crossref","first-page":"123","DOI":"10.1083\/jcb.200105110","volume":"155","author":"M Wehling","year":"2001","unstructured":"Wehling M, Spencer MJ, Tidball JG (2001) A nitric oxide synthase transgene ameliorates muscular dystrophy in mdx mice. J Cell Biol 155(1):123\u2013131","journal-title":"J Cell Biol"},{"issue":"15","key":"9330_CR119","doi-asserted-by":"crossref","first-page":"2280","DOI":"10.1093\/hmg\/ddn129","volume":"17","author":"M Wehling-Henricks","year":"2008","unstructured":"Wehling-Henricks M, Sokolow S, Lee JJ, Myung KH, Villalta SA, Tidball JG (2008) Major basic protein-1 promotes fibrosis of dystrophic muscle and attenuates the cellular immune response in muscular dystrophy. Hum Mol Genet 17(15):2280\u20132292","journal-title":"Hum Mol Genet"},{"issue":"12","key":"9330_CR120","doi-asserted-by":"crossref","first-page":"845","DOI":"10.1016\/j.nmd.2006.07.024","volume":"16","author":"NP Whitehead","year":"2006","unstructured":"Whitehead NP, Streamer M, Lusambili LI, Sachs F, Allen DG (2006) Streptomycin reduces stretch-induced membrane permeability in muscles from mdx mice. Neuromuscul Disord 16(12):845\u2013854","journal-title":"Neuromuscul Disord"},{"issue":"7","key":"9330_CR121","doi-asserted-by":"crossref","first-page":"2003","DOI":"10.1113\/jphysiol.2007.148338","volume":"586","author":"NP Whitehead","year":"2008","unstructured":"Whitehead NP, Pham C, Gervasio OL, Allen DG (2008) N-Acetylcysteine ameliorates skeletal muscle pathophysiology in mdx mice. J Physiol 586(7):2003\u20132014","journal-title":"J Physiol"},{"issue":"12","key":"9330_CR122","doi-asserted-by":"crossref","first-page":"e15354","DOI":"10.1371\/journal.pone.0015354","volume":"5","author":"NP Whitehead","year":"2010","unstructured":"Whitehead NP, Yeung EW, Froehner SC, Allen DG (2010) Skeletal muscle NADPH oxidase is increased and triggers stretch-induced damage in the mdx mouse. PLoS ONE 5(12):e15354","journal-title":"PLoS ONE"},{"issue":"3","key":"9330_CR123","doi-asserted-by":"crossref","first-page":"H1969","DOI":"10.1152\/ajpheart.00489.2007","volume":"293","author":"IA Williams","year":"2007","unstructured":"Williams IA, Allen DG (2007) The role of reactive oxygen species in the hearts of dystrophin-deficient mdx mice. Am J Physiol Heart Circ Physiol 293(3):H1969\u2013H1977","journal-title":"Am J Physiol Heart Circ Physiol"},{"issue":"6","key":"9330_CR124","doi-asserted-by":"crossref","first-page":"831","DOI":"10.1093\/hmg\/6.6.831","volume":"6","author":"RA Williamson","year":"1997","unstructured":"Williamson RA, Henry MD, Daniels KJ, Hrstka RF, Lee JC, Sunada Y, Ibraghimov-Beskrovnaya O, Campbell KP (1997) Dystroglycan is essential for early embryonic development: disruption of Reichert\u2019s membrane in Dag1-null mice. Hum Mol Genet 6(6):831\u2013841","journal-title":"Hum Mol Genet"},{"issue":"3","key":"9330_CR125","doi-asserted-by":"crossref","first-page":"236","DOI":"10.4103\/0028-3886.43441","volume":"56","author":"EM Yiu","year":"2008","unstructured":"Yiu EM, Kornberg AJ (2008) Duchenne muscular dystrophy. Neurol India 56(3):236\u2013247","journal-title":"Neurol India"},{"issue":"7","key":"9330_CR126","doi-asserted-by":"crossref","first-page":"1033","DOI":"10.1093\/hmg\/9.7.1033","volume":"9","author":"M Yoshida","year":"2000","unstructured":"Yoshida M, Hama H, Ishikawa-Sakurai M, Imamura M, Mizuno Y, Araishi K, Wakabayashi-Takai E, Noguchi S, Sasaoka T, Ozawa E (2000) Biochemical evidence for association of dystrobrevin with the sarcoglycan-sarcospan complex as a basis for understanding sarcoglycanopathy. Hum Mol Genet 9(7):1033\u20131040","journal-title":"Hum Mol Genet"},{"issue":"8","key":"9330_CR127","doi-asserted-by":"crossref","first-page":"771","DOI":"10.1097\/NEN.0b013e3181e9a34b","volume":"69","author":"L Zhou","year":"2010","unstructured":"Zhou L, Lu H (2010) Targeting fibrosis in Duchenne muscular dystrophy. J Neuropathol Exp Neurol 69(8):771\u2013776","journal-title":"J Neuropathol Exp Neurol"}],"container-title":["Journal of Muscle Research and Cell Motility"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1007\/s10974-012-9330-9.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/link.springer.com\/article\/10.1007\/s10974-012-9330-9\/fulltext.html","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1007\/s10974-012-9330-9","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2024,4,30]],"date-time":"2024-04-30T21:06:53Z","timestamp":1714511213000},"score":1,"resource":{"primary":{"URL":"http:\/\/link.springer.com\/10.1007\/s10974-012-9330-9"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2012,10,28]]},"references-count":128,"journal-issue":{"issue":"1","published-print":{"date-parts":[[2013,2]]}},"alternative-id":["9330"],"URL":"https:\/\/doi.org\/10.1007\/s10974-012-9330-9","relation":{},"ISSN":["0142-4319","1573-2657"],"issn-type":[{"value":"0142-4319","type":"print"},{"value":"1573-2657","type":"electronic"}],"subject":[],"published":{"date-parts":[[2012,10,28]]}}}