{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,1,10]],"date-time":"2026-01-10T09:27:18Z","timestamp":1768037238988,"version":"3.49.0"},"reference-count":35,"publisher":"Springer Science and Business Media LLC","issue":"2","license":[{"start":{"date-parts":[[2010,1,1]],"date-time":"2010-01-01T00:00:00Z","timestamp":1262304000000},"content-version":"tdm","delay-in-days":0,"URL":"http:\/\/www.springer.com\/tdm"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["J Thromb Thrombolysis"],"published-print":{"date-parts":[[2010,8]]},"DOI":"10.1007\/s11239-009-0435-y","type":"journal-article","created":{"date-parts":[[2009,12,31]],"date-time":"2009-12-31T05:32:55Z","timestamp":1262237575000},"page":"172-178","source":"Crossref","is-referenced-by-count":49,"title":["Associated prothrombotic conditions are probably responsible for the occurrence of thrombosis in almost all patients with congenital FVII deficiency. Critical review of the literature"],"prefix":"10.1007","volume":"30","author":[{"given":"A.","family":"Girolami","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"F.","family":"Tezza","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"R.","family":"Scandellari","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"S.","family":"Vettore","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"B.","family":"Girolami","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"297","published-online":{"date-parts":[[2010,1,1]]},"reference":[{"key":"435_CR1","doi-asserted-by":"crossref","first-page":"120","DOI":"10.1159\/000093642","volume":"116","author":"A Girolami","year":"2006","unstructured":"Girolami A, Ruzzon E, Fabris F et al (2006) Myocardial infarction and other arterial occlusions in hemophilia A patients. A cardiological evaluation of all 42 cases reported in the literature. Acta Haematol 116:120\u2013125","journal-title":"Acta Haematol"},{"key":"435_CR2","doi-asserted-by":"crossref","first-page":"279","DOI":"10.1007\/s11239-006-6556-7","volume":"2","author":"A Girolami","year":"2006","unstructured":"Girolami A, Scandellari R, Zanon E et al (2006) Non-catheter associated venous thrombosis in hemophilia A and B. A critical review of all reported cases. J Thromb Thrombolysis 2:279\u2013284","journal-title":"J Thromb Thrombolysis"},{"key":"435_CR3","doi-asserted-by":"crossref","first-page":"298","DOI":"10.1160\/TH04-03-0148","volume":"92","author":"M Franchini","year":"2004","unstructured":"Franchini M (2004) Thrombotic complications in patients with hereditary bleeding disorders. Thromb Haemost 92:298\u2013304","journal-title":"Thromb Haemost"},{"key":"435_CR4","doi-asserted-by":"crossref","first-page":"248","DOI":"10.1097\/00005792-198307000-00004","volume":"62","author":"LT Goodnough","year":"1983","unstructured":"Goodnough LT, Saito H, Ratnoff OD (1983) Thrombosis or myocardial infarction in congenital clotting factor abnormalities and chronic thrombocytopenias: a report of 21 patients and a review of 50 previously reported cases. Medicine (Baltim) 62:248\u2013255","journal-title":"Medicine (Baltim)"},{"key":"435_CR5","doi-asserted-by":"crossref","first-page":"175","DOI":"10.1007\/s11239-006-5732-0","volume":"21","author":"A Girolami","year":"2006","unstructured":"Girolami A, Tezza F, Scapin M et al (2006) Arterial and venous thrombosis in patients with von Willebrand\u2019s disease: a critical review of the literature. J Thromb Thrombolysis 21:175\u2013178","journal-title":"J Thromb Thrombolysis"},{"key":"435_CR6","doi-asserted-by":"crossref","first-page":"43","DOI":"10.1007\/s11239-005-2227-3","volume":"20","author":"A Girolami","year":"2005","unstructured":"Girolami A, Randi ML, Ruzzon E et al (2005) Myocardial infarction, other arterial thrombosis and invasive coronary procedures, in hemaophilia B: a critical evaluation of reported cases. J Thromb Thrombolysis 20:43\u201346","journal-title":"J Thromb Thrombolysis"},{"key":"435_CR7","doi-asserted-by":"crossref","first-page":"345","DOI":"10.1111\/j.1365-2516.2006.01299.x","volume":"12","author":"A Girolami","year":"2006","unstructured":"Girolami A, Ruzzon E, Tezza F et al (2006) Arterial and venous thrombosis in rare congenital bleeding disorders: a critical review. Haemophilia 12:345\u2013351","journal-title":"Haemophilia"},{"key":"435_CR8","doi-asserted-by":"crossref","first-page":"944","DOI":"10.1097\/00007611-198007000-00037","volume":"73","author":"DL Solanki","year":"1980","unstructured":"Solanki DL, Corn M (1980) Thromboembolism in patient with hereditary deficiency of coagulation factors. South Med J 73:944\u2013946","journal-title":"South Med J"},{"key":"435_CR9","doi-asserted-by":"crossref","first-page":"172","DOI":"10.1016\/0002-9343(64)90003-8","volume":"37","author":"CA Hall","year":"1964","unstructured":"Hall CA, Rapaport SI, Ames SB, Degroot JA (1964) A clinical and family study of hereditary proconvertin (factor VII) deficiency. Am J Med 37:172\u2013181","journal-title":"Am J Med"},{"key":"435_CR10","doi-asserted-by":"crossref","first-page":"245","DOI":"10.1055\/s-0038-1653533","volume":"21","author":"R Heikinheimo","year":"1969","unstructured":"Heikinheimo R, Reinikainen M (1969) Congenital factor VII deficiency. Two cases in children of cousins. Thromb Diath Haemorrh 21:245\u2013248","journal-title":"Thromb Diath Haemorrh"},{"key":"435_CR11","doi-asserted-by":"crossref","first-page":"325","DOI":"10.1111\/j.0954-6820.1962.tb04194.x","volume":"171","author":"HC Godal","year":"1962","unstructured":"Godal HC, Madsen K, Meyer RN (1962) Thrombo-embolism in patients with total proconvertin (factor VII) deficency. A report on two cases. Acta Med Scand 171:325\u2013327","journal-title":"Acta Med Scand"},{"key":"435_CR12","doi-asserted-by":"crossref","first-page":"196","DOI":"10.1007\/s007010050085","volume":"140","author":"HS Kang","year":"1998","unstructured":"Kang HS, Kim DG, Yoon BW (1998) Superior sagittal sinus thrombosis with homocystinuria and deficiency of antithrombin III and factor VII: case report. Acta Neurochir (Wien) 140:196\u2013198","journal-title":"Acta Neurochir (Wien)"},{"key":"435_CR13","doi-asserted-by":"crossref","first-page":"1006","DOI":"10.1016\/S0140-6736(85)90548-3","volume":"2","author":"JJ Lefrere","year":"1985","unstructured":"Lefrere JJ, Chaunu MP, Canard J et al (1985) Congenital factor VII deficiency and cerebrovascular stroke. Lancet 2:1006\u20131007","journal-title":"Lancet"},{"key":"435_CR14","doi-asserted-by":"crossref","first-page":"208","DOI":"10.1016\/j.pediatrneurol.2004.08.008","volume":"32","author":"K Lietz","year":"2005","unstructured":"Lietz K, Kuehling SE, Parkhurst JB (2005) Hemorrhagic stroke in a child with protein S and factor VII deficiencies. Pediatr Neurol 32:208\u2013210","journal-title":"Pediatr Neurol"},{"key":"435_CR15","first-page":"771","volume":"91","author":"K Nakagawa","year":"1990","unstructured":"Nakagawa K, Furusawa A, Momono S et al (1990) Gastrectomy for a patient with congenital factor VII deficiency: a case report. Nippon Geka Gakkai Zasshi 91:771\u2013773","journal-title":"Nippon Geka Gakkai Zasshi"},{"key":"435_CR16","doi-asserted-by":"crossref","first-page":"2153","DOI":"10.1046\/j.1538-7836.2003.00395.x","volume":"1","author":"G Mariani","year":"2003","unstructured":"Mariani G, Herrmann FH, Schulman S et al (2003) International Factor VII Deficiency Study Group. Thrombosis in inherited factor VII deficiency. J Thromb Haemost 1:2153\u20132158","journal-title":"J Thromb Haemost"},{"key":"435_CR17","doi-asserted-by":"crossref","first-page":"564","DOI":"10.1111\/j.1365-2516.2007.01647.x","volume":"14","author":"S Marty","year":"2008","unstructured":"Marty S, Barro C, Chatelain B et al (2008) The paradoxical association between inherited factor VII deficiency and venous thrombosis. Haemophilia 14:564\u2013570","journal-title":"Haemophilia"},{"key":"435_CR18","doi-asserted-by":"crossref","first-page":"108","DOI":"10.1002\/(SICI)1098-1004(1996)8:2<108::AID-HUMU2>3.0.CO;2-7","volume":"8","author":"F Bernardi","year":"1996","unstructured":"Bernardi F, Castaman G, Pinotti M et al (1996) Mutation pattern in clinically asymptomatic coagulation factor VII deficiency. Hum Mutat 8:108\u2013115","journal-title":"Hum Mutat"},{"key":"435_CR19","doi-asserted-by":"crossref","first-page":"402","DOI":"10.1160\/TH08-09-0572","volume":"101","author":"E Arellano-Rodrigo","year":"2009","unstructured":"Arellano-Rodrigo E, Gironella M, Nicolau I, Vila M (2009) Clinical management of thrombosis in inherited factor VII deficiency: a description of two cases. Thromb Haemost 101:402\u2013404","journal-title":"Thromb Haemost"},{"key":"435_CR20","first-page":"248","volume":"64","author":"WL Cooke","year":"1968","unstructured":"Cooke WL (1968) Acute myocardial infarction with decreased factor VII. W Va Med J 64:248\u2013249","journal-title":"W Va Med J"},{"key":"435_CR21","first-page":"41","volume":"43","author":"MF Ben Dridi","year":"1986","unstructured":"Ben Dridi MF, Karoui S, Kastally R et al (1986) L\u2019homocystinuria. Forme avec thrombose vasculaire et deficit en facteur VII (Homocystinuria. A type with vascular thrombosis and factor VII deficiency). Arch Fr Pediatr 43:41\u201344","journal-title":"Arch Fr Pediatr"},{"key":"435_CR22","doi-asserted-by":"crossref","first-page":"739","DOI":"10.1111\/j.1365-2141.1995.tb05378.x","volume":"91","author":"M Escoffre","year":"1995","unstructured":"Escoffre M, Zini JM, Schliamser L, Mazoyer E, Soria C, Tobelem G, Dupuy E (1995) Severe arterial thrombosis in a congenitally factor VII deficient patient. Br J Haematol 91:739\u2013741","journal-title":"Br J Haematol"},{"key":"435_CR23","doi-asserted-by":"crossref","first-page":"141","DOI":"10.1056\/NEJM197301182880309","volume":"288","author":"ME Gershwin","year":"1973","unstructured":"Gershwin ME, Gude JK (1973) Deep vein thrombosis and pulmonary embolism in congenital factor VII deficiency. N Engl J Med 288:141\u2013142","journal-title":"N Engl J Med"},{"key":"435_CR24","first-page":"387","volume":"91","author":"A Girolami","year":"1978","unstructured":"Girolami A, Fabris F, Dal Bo Zanon R et al (1978) Factor VII Padua: a congenital coagulation disorder due to an abnormal factor VII with a peculiar activation pattern. J Lab Clin Med 91:387\u2013395","journal-title":"J Lab Clin Med"},{"key":"435_CR25","doi-asserted-by":"crossref","first-page":"60","DOI":"10.1159\/000206513","volume":"71","author":"T Shifter","year":"1984","unstructured":"Shifter T, Machtey I, Creter D (1984) Thromboembolism in congenital factor VII deficiency. Acta Haematol 71:60\u201362","journal-title":"Acta Haematol"},{"key":"435_CR26","first-page":"679","volume":"86","author":"A Sabharwal","year":"1992","unstructured":"Sabharwal A, Kuppusiwamy M, Foster D et al (1992) Factor VII deficiency (FVII Richmond mutant R304A) associated with thrombosis. Circulation 86:679 (abstract)","journal-title":"Circulation"},{"key":"435_CR27","doi-asserted-by":"crossref","first-page":"619","DOI":"10.1055\/s-0038-1646470","volume":"66","author":"S Schulman","year":"1991","unstructured":"Schulman S, Johnsson H, Lindmarker P (1991) Thrombotic complications after substitution with a FVII concentrate. Thromb Haemost 66:619","journal-title":"Thromb Haemost"},{"key":"435_CR28","doi-asserted-by":"crossref","first-page":"79","DOI":"10.1002\/ajh.2830100112","volume":"10","author":"MV Ragni","year":"1981","unstructured":"Ragni MV, Lewis JH, Spero JA, Hasiba U (1981) Factor VII deficicency. Am J Hematol 10:79\u201388","journal-title":"Am J Hematol"},{"key":"435_CR29","doi-asserted-by":"crossref","first-page":"757","DOI":"10.1046\/j.1365-2516.1998.00181.x","volume":"4","author":"LL Worth","year":"1998","unstructured":"Worth LL, Hoots WK (1998) Development of a subdural vein thrombosis following aggressive factor VII replacement for postnatal intracranial haemorrhage in a homozygous factor VII-deficient infant. Haemophilia 4:757\u2013761","journal-title":"Haemophilia"},{"key":"435_CR30","doi-asserted-by":"crossref","first-page":"46","DOI":"10.1182\/blood.V54.1.46.46","volume":"54","author":"A Girolami","year":"1979","unstructured":"Girolami A, Cattarozzi G, Dal Bo Zanon R, Toffanin F (1979) Factor VII Padua 2: another factor VII abnormality with defective ox brain thromboplastin activation and a complex hereditary pattern. Blood 54:46\u201353","journal-title":"Blood"},{"key":"435_CR31","doi-asserted-by":"crossref","first-page":"1284","DOI":"10.1182\/blood.V66.6.1284.1284","volume":"66","author":"DA Triplett","year":"1985","unstructured":"Triplett DA, Brandt JT, Batard MA et al (1985) Hereditary factor VII deficiency: heterogeneity defined by combined functional and immunochemical analysis. Blood 66:1284\u20131287","journal-title":"Blood"},{"issue":"Suppl","key":"435_CR32","doi-asserted-by":"crossref","first-page":"S241","DOI":"10.1097\/00003246-200205001-00012","volume":"30","author":"SN Doshi","year":"2002","unstructured":"Doshi SN, Marmur JD (2002) Evolving role of tissue factor and its pathway inhibitor. Crit Care Med 30(Suppl):S241\u2013S250","journal-title":"Crit Care Med"},{"key":"435_CR33","doi-asserted-by":"crossref","first-page":"884","DOI":"10.1111\/j.1538-7836.2004.00720.x","volume":"2","author":"A Piccioli","year":"2004","unstructured":"Piccioli A, Lensing AW, Prins MH, SOMIT Investigators Group et al (2004) Extensive screening for occult malignant disease in idiopathic venous thromboembolism: a prospective randomized clinical trial. J Thromb Haemost 2:884\u2013889","journal-title":"J Thromb Haemost"},{"key":"435_CR34","doi-asserted-by":"crossref","first-page":"260","DOI":"10.1056\/NEJM196810032791407","volume":"279","author":"OD Ratnoff","year":"1968","unstructured":"Ratnoff OD, Busse RJ, Sheen RP (1968) The demise of Mr. Hageman. N Engl J Med 279:260\u2013261","journal-title":"N Engl J Med"},{"key":"435_CR35","doi-asserted-by":"crossref","unstructured":"Girolami A, Candeo N, Vettore S et\u00a0al (2009) The clinical significance of the lack of arterial or venous thrombosis in patients with congenital prothrombin or FX deficiency. J Thromb Thrombolysis. doi: 10.1007\/s11239-009-0342-2","DOI":"10.1007\/s11239-009-0342-2"}],"container-title":["Journal of Thrombosis and Thrombolysis"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1007\/s11239-009-0435-y.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/link.springer.com\/article\/10.1007\/s11239-009-0435-y\/fulltext.html","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1007\/s11239-009-0435-y","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2020,5,26]],"date-time":"2020-05-26T10:38:36Z","timestamp":1590489516000},"score":1,"resource":{"primary":{"URL":"http:\/\/link.springer.com\/10.1007\/s11239-009-0435-y"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2010,1,1]]},"references-count":35,"journal-issue":{"issue":"2","published-print":{"date-parts":[[2010,8]]}},"alternative-id":["435"],"URL":"https:\/\/doi.org\/10.1007\/s11239-009-0435-y","relation":{},"ISSN":["0929-5305","1573-742X"],"issn-type":[{"value":"0929-5305","type":"print"},{"value":"1573-742X","type":"electronic"}],"subject":[],"published":{"date-parts":[[2010,1,1]]}}}