{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,28]],"date-time":"2026-08-28T14:40:41Z","timestamp":1787928041692,"version":"build-2784847793"},"reference-count":90,"publisher":"Springer Science and Business Media LLC","issue":"2","license":[{"start":{"date-parts":[[2021,2,1]],"date-time":"2021-02-01T00:00:00Z","timestamp":1612137600000},"content-version":"tdm","delay-in-days":0,"URL":"http:\/\/www.springer.com\/tdm"},{"start":{"date-parts":[[2021,2,1]],"date-time":"2021-02-01T00:00:00Z","timestamp":1612137600000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/www.springer.com\/tdm"}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["Curr Allergy Asthma Rep"],"published-print":{"date-parts":[[2021,2]]},"DOI":"10.1007\/s11882-021-00991-3","type":"journal-article","created":{"date-parts":[[2021,2,10]],"date-time":"2021-02-10T04:33:27Z","timestamp":1612931607000},"update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":42,"title":["Distinguishing Blau Syndrome from Systemic Sarcoidosis"],"prefix":"10.1007","volume":"21","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-0417-963X","authenticated-orcid":false,"given":"Katherine P.","family":"Kaufman","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mara L.","family":"Becker","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2021,2,9]]},"reference":[{"issue":"5","key":"991_CR1","doi-asserted-by":"publisher","first-page":"689","DOI":"10.1016\/S0022-3476(85)80394-2","volume":"107","author":"EB Blau","year":"1985","unstructured":"\u2022 Blau EB. Familial granulomatous arthritis, iritis, and rash. J Pediatr. 1985;107(5):689\u201393. https:\/\/doi.org\/10.1016\/S0022-3476(85)80394-2. First published description of familial granulomatous disease, later named Blau syndrome.","journal-title":"J Pediatr"},{"issue":"5","key":"991_CR2","first-page":"1097","volume":"59","author":"G Tromp","year":"1996","unstructured":"Tromp G, Kuivaniemi H, Raphael S, Ala-Kokko L, Christiano A, Considine E, et al. Genetic linkage of familial granulomatous inflammatory arthritis, skin rash, and uveitis to chromosome 16. Am J Hum Genet. 1996;59(5):1097\u2013107.","journal-title":"Am J Hum Genet"},{"issue":"1","key":"991_CR3","doi-asserted-by":"publisher","first-page":"19","DOI":"10.1038\/ng720","volume":"29","author":"C Miceli-Richard","year":"2001","unstructured":"Miceli-Richard C, Lesage S, Rybojad M, Prieur AM, Manouvrier-Hanu S, H\u00e4fner R, et al. CARD15 mutations in Blau syndrome. Nat Genet. 2001;29(1):19\u201320. https:\/\/doi.org\/10.1038\/ng720.","journal-title":"Nat Genet"},{"issue":"11","key":"991_CR4","doi-asserted-by":"publisher","first-page":"3805","DOI":"10.1002\/art.22966","volume":"56","author":"JI Ar\u00f3stegui","year":"2007","unstructured":"Ar\u00f3stegui JI, Arnal C, Merino R, Modesto C, Antonia Carballo M, Moreno P, et al. NOD2 gene-associated pediatric granulomatous arthritis: clinical diversity, novel and recurrent mutations, and evidence of clinical improvement with interleukin-1 blockade in a Spanish cohort. Arthritis Rheum. 2007;56(11):3805\u201313. https:\/\/doi.org\/10.1002\/art.22966.","journal-title":"Arthritis Rheum"},{"issue":"6","key":"991_CR5","doi-asserted-by":"publisher","first-page":"1797","DOI":"10.1002\/art.24533","volume":"60","author":"CD Ros\u00e9","year":"2009","unstructured":"Ros\u00e9 CD, Ar\u00f3stegui JI, Martin TM, Espada G, Scalzi L, Yag\u00fce J, et al. NOD2-associated pediatric granulomatous arthritis (PGA): an expanding phenotype. A study of an international registry and a national cohort. Arthritis Rheum. 2009;60(6):1797\u2013803.","journal-title":"Arthritis Rheum"},{"key":"991_CR6","doi-asserted-by":"publisher","first-page":"2153","DOI":"10.1056\/NEJMra071714","volume":"357","author":"MC Iannuzzi","year":"2007","unstructured":"Iannuzzi MC, Rybicki BA, Teirstein AS. Sarcoidosis. N Engl J Med. 2007;357:2153\u201365. https:\/\/doi.org\/10.1056\/NEJMra071714.","journal-title":"N Engl J Med"},{"issue":"10","key":"991_CR7","doi-asserted-by":"publisher","first-page":"981","DOI":"10.1080\/17476348.2019.1655401","volume":"13","author":"D Bennett","year":"2019","unstructured":"Bennett D, Bargagli E, Refini RM, Rottoli P. New concepts in the pathogenesis of sarcoidosis. Expert Rev Respir Med. 2019;13(10):981\u201391. https:\/\/doi.org\/10.1080\/17476348.2019.1655401.","journal-title":"Expert Rev Respir Med"},{"key":"991_CR8","doi-asserted-by":"publisher","first-page":"1885","DOI":"10.1164\/rccm2104046","volume":"164","author":"RP Baughman","year":"2001","unstructured":"Baughman RP, Teirstein AS, Judson MA, et al. Clinical characteristics of patients in a case control study of Sarcoidosis. Am J Respir Crit Care Med. 2001;164:1885\u20139. https:\/\/doi.org\/10.1164\/rccm2104046.","journal-title":"Am J Respir Crit Care Med"},{"issue":"1","key":"991_CR9","doi-asserted-by":"publisher","first-page":"144","DOI":"10.1378\/chest.10-0413","volume":"139","author":"YC Cozier","year":"2011","unstructured":"Cozier YC, Berman JS, Palmer JR, Boggs DA, Serlin DM, Rosenberg L. Sarcoidosis in black women in the United States: data from the Black Women\u2019s Health Study. Chest. 2011;139(1):144\u201350. https:\/\/doi.org\/10.1378\/chest.10-0413.","journal-title":"Chest."},{"key":"991_CR10","first-page":"119","volume":"29","author":"MA Judson","year":"2012","unstructured":"Judson MA, Boan AD, Lackland DT. The clinical course of sarcoidosis: presentation, diagnosis, and treatment in a large white and black cohort in the United States. Sarcoidosis Vasc Diffus Lung Dis. 2012;29:119\u201327.","journal-title":"Sarcoidosis Vasc Diffus Lung Dis"},{"issue":"1","key":"991_CR11","doi-asserted-by":"publisher","first-page":"16","DOI":"10.4081\/reumatismo.2017.965","volume":"69","author":"P Ungprasert","year":"2017","unstructured":"Ungprasert P, Crowson CS, Matteson EL. Epidemiology and clinical characteristics of sarcoidosis: an update from a population-based cohort study from Olmsted County, Minnesota. Reumatismo. 2017;69(1):16\u201322. https:\/\/doi.org\/10.4081\/reumatismo.2017.965.","journal-title":"Reumatismo"},{"issue":"3","key":"991_CR12","doi-asserted-by":"publisher","first-page":"358","DOI":"10.1016\/j.mayocpiqo.2019.04.006","volume":"3","author":"P Ungprasert","year":"2019","unstructured":"\u2022 Ungprasert P, Ryu JH, Matteson EL. Clinical manifestations, diagnosis, and treatment of sarcoidosis. Mayo Clin Proc Innov Qual Outcomes. 2019;3(3):358\u201375. https:\/\/doi.org\/10.1016\/j.mayocpiqo.2019.04.006. A thorough and updated review about sarcoidosis.","journal-title":"Mayo Clin Proc Innov Qual Outcomes"},{"key":"991_CR13","doi-asserted-by":"publisher","first-page":"1","DOI":"10.1186\/1546-0096-6-16","volume":"6","author":"AK Shetty","year":"2008","unstructured":"Shetty AK, Gedalia A. Childhood sarcoidosis: a rare but fascinating disorder. Pediatr Rheumatol. 2008;6:1\u201310. https:\/\/doi.org\/10.1186\/1546-0096-6-16.","journal-title":"Pediatr Rheumatol"},{"issue":"1","key":"991_CR14","doi-asserted-by":"publisher","first-page":"95","DOI":"10.1586\/eci.11.84","volume":"8","author":"RP Baughman","year":"2012","unstructured":"Baughman RP, Nunes H. Therapy for sarcoidosis: evidence-based recommendations. Expert Rev Clin Immunol. 2012;8(1):95\u2013103. https:\/\/doi.org\/10.1586\/eci.11.84.","journal-title":"Expert Rev Clin Immunol"},{"key":"991_CR15","doi-asserted-by":"publisher","first-page":"158","DOI":"10.1016\/j.ajo.2017.08.017","volume":"187","author":"IL Sarens","year":"2018","unstructured":"Sarens IL, Casteels I, Anton J, Bader-Meunier B, Brissaud P, Ch\u00e9deville G, et al. Blau syndrome\u2013associated uveitis: preliminary results from an international prospective interventional case series. Am J Ophthalmol. 2018;187:158\u201366. https:\/\/doi.org\/10.1016\/j.ajo.2017.08.017.","journal-title":"Am J Ophthalmol"},{"issue":"6","key":"991_CR16","doi-asserted-by":"publisher","first-page":"1093","DOI":"10.1016\/j.semarthrit.2018.10.005","volume":"48","author":"BL Adler","year":"2019","unstructured":"Adler BL, Wang CJ, Bui TL, Schilperoort HM, Armstrong AW. Anti-tumor necrosis factor agents in sarcoidosis: a systematic review of efficacy and safety. Semin Arthritis Rheum. 2019;48(6):1093\u2013104. https:\/\/doi.org\/10.1016\/j.semarthrit.2018.10.005.","journal-title":"Semin Arthritis Rheum"},{"key":"991_CR17","doi-asserted-by":"publisher","first-page":"1492","DOI":"10.1136\/annrheumdis-2020-217320","volume":"79","author":"T Matsuda","year":"2020","unstructured":"\u2022 Matsuda T, Kambe N, Ueki Y, et al. Clinical characteristics and treatment of 50 cases of Blau syndrome in Japan confirmed by genetic analysis of the NOD2 mutation. Ann Rheum Dis. 2020;79:1492\u20139. https:\/\/doi.org\/10.1136\/annrheumdis-2020-217320. A recent study describing a large cohort of Blau syndrome patients.","journal-title":"Ann Rheum Dis"},{"issue":"4","key":"991_CR18","doi-asserted-by":"publisher","first-page":"1","DOI":"10.3390\/diagnostics9040160","volume":"9","author":"B Chiu","year":"2019","unstructured":"Chiu B, Chan J, Das S, Alshamma Z, Sergi C. Pediatric sarcoidosis: a review with emphasis on early onset and high-risk sarcoidosis and diagnostic challenges. Diagnostics. 2019;9(4):1\u201313. https:\/\/doi.org\/10.3390\/diagnostics9040160.","journal-title":"Diagnostics."},{"issue":"8","key":"991_CR19","doi-asserted-by":"publisher","first-page":"1244","DOI":"10.1513\/AnnalsATS.201511-760OC","volume":"13","author":"RP Baughman","year":"2016","unstructured":"Baughman RP, Field S, Costabel U, Crystal RG, Culver DA, Drent M, et al. Sarcoidosis in America: analysis based on health care use. Ann Am Thorac Soc. 2016;13(8):1244\u201352. https:\/\/doi.org\/10.1513\/AnnalsATS.201511-760OC.","journal-title":"Ann Am Thorac Soc"},{"issue":"1","key":"991_CR20","doi-asserted-by":"publisher","first-page":"1","DOI":"10.1186\/1546-0096-12-333r5","volume":"12","author":"CH Wouters","year":"2014","unstructured":"\u2022 Wouters CH, Maes A, Foley KP, Bertin J, Rose CD. Blau Syndrome, the prototypic auto-inflammatory granulomatous disease. Pediatr Rheumatol. 2014;12(1):1\u20139. https:\/\/doi.org\/10.1186\/1546-0096-12-333r5. Excellent review about Blau syndrome, addressing presentation, genetics, histology.","journal-title":"Pediatr Rheumatol"},{"issue":"6","key":"991_CR21","doi-asserted-by":"publisher","first-page":"1008","DOI":"10.1093\/rheumatology\/keu437","volume":"54","author":"CD Ros\u00e9","year":"2015","unstructured":"\u2022\u2022 Ros\u00e9 CD, Pans S, Casteels I, et al. Blau syndrome: cross-sectional data from a multicentre study of clinical, radiological and functional outcomes. Rheumatol (United Kingdom). 2015;54(6):1008\u201316. https:\/\/doi.org\/10.1093\/rheumatology\/keu437. Recent, multicenter study addressing presentation and outcomes.","journal-title":"Rheumatol (United Kingdom)"},{"key":"991_CR22","doi-asserted-by":"publisher","first-page":"S421","DOI":"10.1513\/AnnalsATS.201707-564OT","volume":"14","author":"AK Gerke","year":"2017","unstructured":"Gerke AK, Judson MA, Cozier YC, Culver DA, Koth LL. Disease burden and variability in sarcoidosis. Ann Am Thorac Soc. 2017;14:S421\u20138. https:\/\/doi.org\/10.1513\/AnnalsATS.201707-564OT.","journal-title":"Ann Am Thorac Soc"},{"issue":"10","key":"991_CR23","doi-asserted-by":"publisher","first-page":"3337","DOI":"10.1002\/art.22122","volume":"54","author":"CD Ros\u00e9","year":"2006","unstructured":"Ros\u00e9 CD, Wouters CH, Meiorin S, Doyle TM, Davey MP, Rosenbaum JT, et al. Pediatric granulomatous arthritis: an international registry. Arthritis Rheum. 2006;54(10):3337\u201344. https:\/\/doi.org\/10.1002\/art.22122.","journal-title":"Arthritis Rheum"},{"key":"991_CR24","doi-asserted-by":"publisher","first-page":"1","DOI":"10.1155\/2018\/6292308","volume":"2018","author":"M Imayoshi","year":"2018","unstructured":"Imayoshi M, Ogata Y, Yamamoto S. A case of sporadic Blau syndrome with an uncommon clinical course. Case Rep Rheumatol. 2018;2018:1\u20135. https:\/\/doi.org\/10.1155\/2018\/6292308.","journal-title":"Case Rep Rheumatol"},{"issue":"1","key":"991_CR25","doi-asserted-by":"publisher","first-page":"70","DOI":"10.3928\/23258160-20171215-12","volume":"49","author":"H Nascimento","year":"2018","unstructured":"Nascimento H, Sousa JM, Fern\u00e1ndez DG, Salom\u00e3o GHA, Sato EH, Muccioli C, et al. Blau-Jabs syndrome in a tertiary ophthalmologic center. Ophthalmic Surg Lasers Imaging Retin. 2018;49(1):70\u20135. https:\/\/doi.org\/10.3928\/23258160-20171215-12.","journal-title":"Ophthalmic Surg Lasers Imaging Retin"},{"issue":"7","key":"991_CR26","doi-asserted-by":"publisher","first-page":"1879","DOI":"10.1007\/s10067-015-2870-9","volume":"35","author":"A Gedalia","year":"2016","unstructured":"Gedalia A, Khan TA, Shetty AK, Dimitriades VR, Espinoza LR. Childhood sarcoidosis: Louisiana experience. Clin Rheumatol. 2016;35(7):1879\u201384. https:\/\/doi.org\/10.1007\/s10067-015-2870-9.","journal-title":"Clin Rheumatol"},{"issue":"3","key":"991_CR27","doi-asserted-by":"publisher","first-page":"1195","DOI":"10.1182\/blood-2004-07-2972","volume":"105","author":"N Kanazawa","year":"2005","unstructured":"Kanazawa N, Okafuji I, Kambe N, Nishikomori R, Nakata-Hizume M, Nagai S, et al. Early-onset sarcoidosis and CARD15 mutations with constitutive nuclear factor-\u03baB activation: common genetic etiology with Blau syndrome. Blood. 2005;105(3):1195\u20137. https:\/\/doi.org\/10.1182\/blood-2004-07-2972.","journal-title":"Blood."},{"issue":"6","key":"991_CR28","doi-asserted-by":"publisher","first-page":"1804","DOI":"10.1002\/art.24532","volume":"60","author":"FT Saulsbury","year":"2009","unstructured":"Saulsbury FT, Wouters CH, Martin TM, Austin CR, Doyle TM, Goodwin KA, et al. Incomplete penetrance of the NOD2 E383K substitution among members of a pediatric granulomatous arthritis pedigree. Arthritis Rheum. 2009;60(6):1804\u20136. https:\/\/doi.org\/10.1002\/art.24532.","journal-title":"Arthritis Rheum"},{"issue":"6","key":"991_CR29","doi-asserted-by":"publisher","first-page":"e385","DOI":"10.1111\/pde.12908","volume":"33","author":"J Harada","year":"2016","unstructured":"Harada J, Nakajima T, Kanazawa N. A case of Blau syndrome with NOD2 E383K mutation. Pediatr Dermatol. 2016;33(6):e385\u20137. https:\/\/doi.org\/10.1111\/pde.12908.","journal-title":"Pediatr Dermatol"},{"issue":"4","key":"991_CR30","doi-asserted-by":"publisher","first-page":"1076","DOI":"10.1016\/j.jaci.2012.02.004","volume":"129","author":"CEI Janssen","year":"2012","unstructured":"Janssen CEI, Rose CD, De Hertogh G, et al. Morphologic and immunohistochemical characterization of granulomas in the nucleotide oligomerization domain 2-related disorders Blau syndrome and Crohn disease. J Allergy Clin Immunol. 2012;129(4):1076\u201384. https:\/\/doi.org\/10.1016\/j.jaci.2012.02.004.","journal-title":"J Allergy Clin Immunol"},{"issue":"May","key":"991_CR31","doi-asserted-by":"publisher","first-page":"1","DOI":"10.1038\/ncomms11813","volume":"7","author":"S Maekawa","year":"2016","unstructured":"Maekawa S, Ohto U, Shibata T, Miyake K, Shimizu T. Crystal structure of NOD2 and its implications in human disease. Nat Commun. 2016;7(May):1\u201311. https:\/\/doi.org\/10.1038\/ncomms11813.","journal-title":"Nat Commun"},{"key":"991_CR32","doi-asserted-by":"publisher","DOI":"10.1016\/bs.apcsb.2019.11.005","volume-title":"Computational model to analyze and characterize the functional mutations of NOD2 protein causing inflammatory disorder \u2013 Blau Syndrome","author":"D Thirumal Kumar","year":"2020","unstructured":"Thirumal Kumar D, Udhaya Kumar S, Nishaat Laeeque AS, et al. Computational model to analyze and characterize the functional mutations of NOD2 protein causing inflammatory disorder \u2013 Blau Syndrome, vol. 120. Amsterdam: Elsevier Ltd; 2020. https:\/\/doi.org\/10.1016\/bs.apcsb.2019.11.005."},{"issue":"8","key":"991_CR33","doi-asserted-by":"publisher","first-page":"1","DOI":"10.1371\/journal.pone.0043907","volume":"7","author":"I Adrianto","year":"2012","unstructured":"Adrianto I, Lin CP, Hale JJ, Levin AM, Datta I, Parker R, et al. Genome-wide association study of African and European Americans implicates multiple shared and ethnic specific loci in sarcoidosis susceptibility. PLoS One. 2012;7(8):1\u201310. https:\/\/doi.org\/10.1371\/journal.pone.0043907.","journal-title":"PLoS One"},{"issue":"2","key":"991_CR34","doi-asserted-by":"publisher","first-page":"206","DOI":"10.1165\/rcmb.2014-0227OC","volume":"53","author":"AAM Levin","year":"2015","unstructured":"Levin AAM, Adrianto I, Datta I, et al. Association of HLA-DRB1 with sarcoidosis susceptibility and progression in African Americans. Am J Respir Cell Mol Biol. 2015;53(2):206\u201316. https:\/\/doi.org\/10.1165\/rcmb.2014-0227OC.","journal-title":"Am J Respir Cell Mol Biol"},{"issue":"5","key":"991_CR35","doi-asserted-by":"publisher","first-page":"777","DOI":"10.1093\/rheumatology\/kex317","volume":"57","author":"K Bechman","year":"2018","unstructured":"Bechman K, Christidis D, Walsh S, Birring SS, Galloway J. A review of the musculoskeletal manifestations of sarcoidosis. Rheumatology (Oxford). 2018;57(5):777\u201383. https:\/\/doi.org\/10.1093\/rheumatology\/kex317.","journal-title":"Rheumatology (Oxford)"},{"issue":"4","key":"991_CR36","doi-asserted-by":"publisher","first-page":"888","DOI":"10.1183\/09031936.00033812","volume":"41","author":"S Hofmann","year":"2013","unstructured":"Hofmann S, Fischer A, Nothnagel M, Jacobs G, Schmid B, Wittig M, et al. Genome-wide association analysis reveals 12q13.3-q14.1 as new risk locus for sarcoidosis. Eur Respir J. 2013;41(4):888\u2013900. https:\/\/doi.org\/10.1183\/09031936.00033812.","journal-title":"Eur Respir J"},{"issue":"1","key":"991_CR37","doi-asserted-by":"publisher","first-page":"259","DOI":"10.1007\/s11033-013-2859-x","volume":"41","author":"GG Song","year":"2014","unstructured":"Song GG, Kim JH, Lee YH. Associations between TNF-\u03b1 -308 A\/G and lymphotoxin-\u03b1 +252 A\/G polymorphisms and susceptibility to sarcoidosis: a meta-analysis. Mol Biol Rep. 2014;41(1):259\u201367. https:\/\/doi.org\/10.1007\/s11033-013-2859-x.","journal-title":"Mol Biol Rep"},{"key":"991_CR38","doi-asserted-by":"publisher","first-page":"1133","DOI":"10.1007\/978-90-481-8566-5_5","volume-title":"Role of NOD2 pathway genes in sarcoidosis cases with clinical characteristics of Blau Syndrome","author":"GA Bello","year":"2015","unstructured":"Bello GA, Dumancas GG, Levin AM, Iannuzzi MC, Rybicki BA, Montgomery C. Role of NOD2 pathway genes in sarcoidosis cases with clinical characteristics of Blau Syndrome; 2015. p. 1133\u20135. https:\/\/doi.org\/10.1007\/978-90-481-8566-5_5."},{"issue":"4","key":"991_CR39","doi-asserted-by":"publisher","first-page":"1","DOI":"10.1371\/journal.pone.0122639","volume":"10","author":"Y Lin","year":"2015","unstructured":"Lin Y, Wei J, Fan L, Cheng D. BTNL2 gene polymorphism and sarcoidosis susceptibility:a meta-analysis. PLoS One. 2015;10(4):1\u201310. https:\/\/doi.org\/10.1371\/journal.pone.0122639.","journal-title":"PLoS One"},{"issue":"1","key":"991_CR40","doi-asserted-by":"publisher","first-page":"219","DOI":"10.1177\/1470320313489059","volume":"16","author":"GG Song","year":"2015","unstructured":"Song GG, Kim JH, Lee YH. Associations between the angiotensin-converting enzyme insertion\/deletion polymorphism and susceptibility to sarcoidosis: a meta-analysis. JRAAS - J Renin-Angiotensin-Aldosterone Syst. 2015;16(1):219\u201326. https:\/\/doi.org\/10.1177\/1470320313489059.","journal-title":"JRAAS - J Renin-Angiotensin-Aldosterone Syst"},{"key":"991_CR41","doi-asserted-by":"publisher","first-page":"39","DOI":"10.1016\/j.ajoc.2016.05.005","volume":"3","author":"S Davoudi","year":"2016","unstructured":"Davoudi S, Navarro-Gomez D, Shen L, Ung C, Ren A, Sullivan L, et al. NOD2 genetic variants and sarcoidosis-associated uveitis. Am J Ophthalmol Case Reports. 2016;3:39\u201342. https:\/\/doi.org\/10.1016\/j.ajoc.2016.05.005.","journal-title":"Am J Ophthalmol Case Reports"},{"issue":"1","key":"991_CR42","doi-asserted-by":"publisher","first-page":"36","DOI":"10.1007\/s12016-015-8479-6","volume":"49","author":"G Rossi","year":"2015","unstructured":"Rossi G, Cavazza A, Colby TV. Pathology of Sarcoidosis. Clin Rev Allergy Immunol. 2015;49(1):36\u201344. https:\/\/doi.org\/10.1007\/s12016-015-8479-6.","journal-title":"Clin Rev Allergy Immunol"},{"issue":"2","key":"991_CR43","doi-asserted-by":"publisher","first-page":"340","DOI":"10.1111\/jdv.15963","volume":"34","author":"J Poline","year":"2020","unstructured":"\u2022\u2022 Poline J, Fogel O, Pajot C, et al. Early-onset granulomatous arthritis, uveitis and skin rash: characterization of skin involvement in Blau syndrome. J Eur Acad Dermatol Venereol. 2020;34(2):340\u20138. https:\/\/doi.org\/10.1111\/jdv.15963. Excellent review of the cutaneous manifestations of Blau syndrome.","journal-title":"J Eur Acad Dermatol Venereol"},{"issue":"1","key":"991_CR44","doi-asserted-by":"publisher","first-page":"339","DOI":"10.1016\/j.jaci.2017.04.013","volume":"141","author":"S Takada","year":"2018","unstructured":"Takada S, Kambe N, Kawasaki Y, et al. Pluripotent stem cell models of Blau syndrome reveal an IFN-\u03b3\u2013dependent inflammatory response in macrophages. J Allergy Clin Immunol. 2018;141(1):339\u2013349.e11. https:\/\/doi.org\/10.1016\/j.jaci.2017.04.013.","journal-title":"J Allergy Clin Immunol"},{"issue":"1","key":"991_CR45","doi-asserted-by":"publisher","first-page":"127692","DOI":"10.4061\/2010\/127692","volume":"1","author":"CT Dow","year":"2010","unstructured":"Dow CT, Ellingson JLE. Detection of Mycobacterium avium ss. paratuberculosis in Blau syndrome tissues. Autoimmune Dis. 2010;1(1):127692. https:\/\/doi.org\/10.4061\/2010\/127692.","journal-title":"Autoimmune Dis"},{"issue":"3","key":"991_CR46","doi-asserted-by":"publisher","first-page":"257","DOI":"10.1007\/s00296-006-0250-0","volume":"27","author":"T-H Kim","year":"2007","unstructured":"Kim T-H, Payne U, Zhang X, Iwanaga Y, Davey MP, Rosenbaum JT, et al. Altered host:pathogen interactions conferred by the Blau syndrome mutation of NOD2. Rheumatol Int. 2007;27(3):257\u201362. https:\/\/doi.org\/10.1007\/s00296-006-0250-0.","journal-title":"Rheumatol Int"},{"issue":"1","key":"991_CR47","doi-asserted-by":"publisher","first-page":"1","DOI":"10.1186\/s12890-016-0332-z","volume":"16","author":"T Esteves","year":"2016","unstructured":"Esteves T, Aparicio G, Garcia-Patos V. Is there any association between Sarcoidosis and infectious agents?: a systematic review and meta-analysis. BMC Pulm Med. 2016;16(1):1\u201313. https:\/\/doi.org\/10.1186\/s12890-016-0332-z.","journal-title":"BMC Pulm Med"},{"issue":"8","key":"991_CR48","doi-asserted-by":"publisher","first-page":"1","DOI":"10.1371\/journal.pone.0154716","volume":"11","author":"C Fang","year":"2016","unstructured":"Fang C, Huang H, Xu Z. Immunological evidence for the role of mycobacteria in sarcoidosis: a meta-analysis. PLoS One. 2016;11(8):1\u201314. https:\/\/doi.org\/10.1371\/journal.pone.0154716.","journal-title":"PLoS One"},{"issue":"9","key":"991_CR49","doi-asserted-by":"publisher","first-page":"794","DOI":"10.1016\/j.bbadis.2006.07.006","volume":"1762","author":"T Tanabe","year":"2006","unstructured":"Tanabe T, Ishige I, Suzuki Y, Aita Y, Furukawa A, Ishige Y, et al. Sarcoidosis and NOD1 variation with impaired recognition of intracellular Propionibacterium acnes. Biochim Biophys Acta Mol basis Dis. 2006;1762(9):794\u2013801. https:\/\/doi.org\/10.1016\/j.bbadis.2006.07.006.","journal-title":"Biochim Biophys Acta Mol basis Dis"},{"issue":"4","key":"991_CR50","doi-asserted-by":"publisher","first-page":"1292","DOI":"10.1002\/art.22509","volume":"56","author":"ML Becker","year":"2007","unstructured":"Becker ML, Martin TM, Doyle TM, Ros\u00e9 CD. Interstitial pneumonitis in Blau syndrome with documented mutation in CARD15. Arthritis Rheum. 2007;56(4):1292\u20134. https:\/\/doi.org\/10.1002\/art.22509.","journal-title":"Arthritis Rheum"},{"key":"991_CR51","doi-asserted-by":"publisher","first-page":"1","DOI":"10.1155\/2014\/216056","volume":"2014","author":"K Chauhan","year":"2014","unstructured":"Chauhan K, Michet C. A case of Blau syndrome. Case Rep Rheumatol. 2014;2014:1\u20133. https:\/\/doi.org\/10.1155\/2014\/216056.","journal-title":"Case Rep Rheumatol"},{"issue":"5","key":"991_CR52","doi-asserted-by":"publisher","first-page":"1179","DOI":"10.1093\/rheumatology\/kez484","volume":"59","author":"JC Ellis","year":"2020","unstructured":"Ellis JC, Faber BG, Uri IF, Emerson JS. Early onset sarcoidosis (Blau syndrome): erosive and often misdiagnosed. Rheumatol (United Kingdom). 2020;59(5):1179\u201380. https:\/\/doi.org\/10.1093\/rheumatology\/kez484.","journal-title":"Rheumatol (United Kingdom)"},{"issue":"3","key":"991_CR53","doi-asserted-by":"publisher","first-page":"602","DOI":"10.1093\/rheumatology\/kez312","volume":"59","author":"S Jha","year":"2020","unstructured":"Jha S, Mittal S, Kumar RR, Dhooria A, Rawat A, Dhir V. An unusual cause of deforming erosive arthritis in an adult. Rheumatol (United Kingdom). 2020;59(3):602. https:\/\/doi.org\/10.1093\/rheumatology\/kez312.","journal-title":"Rheumatol (United Kingdom)"},{"issue":"June","key":"991_CR54","doi-asserted-by":"publisher","first-page":"257","DOI":"10.1016\/j.jpeds.2020.01.057","volume":"221","author":"J Poline","year":"2020","unstructured":"Poline J, Bourrat E, Meinzer U. Camptodactlyly in pediatric practice: Blau syndrome. J Pediatr. 2020;221(June):257\u20139. https:\/\/doi.org\/10.1016\/j.jpeds.2020.01.057.","journal-title":"J Pediatr"},{"key":"991_CR55","doi-asserted-by":"publisher","first-page":"499","DOI":"10.1136\/ard.61.6.499","volume":"61","author":"H Visser","year":"2002","unstructured":"Visser H, Vos K, Zanelli E, Verduyn W, Schreuder GM, Speyer I, et al. Sarcoid arthritis: clinical characteristics, diagnostic aspects, and risk factors. Ann Rheum Dis. 2002;61:499\u2013504. https:\/\/doi.org\/10.1136\/ard.61.6.499.","journal-title":"Ann Rheum Dis"},{"issue":"10","key":"991_CR56","doi-asserted-by":"publisher","first-page":"1799","DOI":"10.1111\/jdv.13760.Epidemiology","volume":"30","author":"P Ungprasert","year":"2016","unstructured":"Ungprasert P, Wetter DA, Crowson CS, Matteson EL. Epidemiology of cutaneous sarcoidosis, 1976-2013: a population based study from Olmsted County, Minnesota. J Eur Acad Dermatol Venereol. 2016;30(10):1799\u2013804. https:\/\/doi.org\/10.1111\/jdv.13760.Epidemiology.","journal-title":"J Eur Acad Dermatol Venereol"},{"key":"991_CR57","doi-asserted-by":"publisher","first-page":"1","DOI":"10.1007\/s00296-019-04316-6","volume":"0123456789","author":"AK Jindal","year":"2019","unstructured":"Jindal AK, Pilania RK, Suri D, Gupta A, Gattorno M, Ceccherini I, et al. A young female with early onset arthritis, uveitis, hepatic, and renal granulomas: a clinical tryst with Blau syndrome over 20 years and case-based review. Rheumatol Int. 2019;0123456789:1\u20139. https:\/\/doi.org\/10.1007\/s00296-019-04316-6.","journal-title":"Rheumatol Int"},{"key":"991_CR58","doi-asserted-by":"publisher","first-page":"1","DOI":"10.3899\/jrheum.190768","volume":"48","author":"MA Turk","year":"2020","unstructured":"Turk MA, Hayworth JL, Nevskaya T, Pope JE. Ocular manifestations in rheumatoid arthritis, connective tissue disease, and vasculitis: a systematic review and meta-analysis. J Rheumatol. 2020;48:1\u201325. https:\/\/doi.org\/10.3899\/jrheum.190768.","journal-title":"J Rheumatol"},{"issue":"5","key":"991_CR59","doi-asserted-by":"publisher","first-page":"801","DOI":"10.1016\/0002-9343(85)90286-4","volume":"78","author":"DA Jabs","year":"1985","unstructured":"Jabs DA, Houk JL, Bias WB, Arnett FC. Familial granulomatous synovitis, uveitis, and cranial neuropathies. Am J Med. 1985;78(5):801\u20134. https:\/\/doi.org\/10.1016\/0002-9343(85)90286-4.","journal-title":"Am J Med"},{"issue":"S1","key":"991_CR60","doi-asserted-by":"publisher","first-page":"1","DOI":"10.1186\/1546-0096-9-s1-p36","volume":"9","author":"R Khubchandani","year":"2011","unstructured":"Khubchandani R, Hasija R, Touitou I, Khemani C. Aortoarteritis and cardiomyopathy in a child with Blau syndrome. Pediatr Rheumatol. 2011;9(S1):1\u20132. https:\/\/doi.org\/10.1186\/1546-0096-9-s1-p36.","journal-title":"Pediatr Rheumatol"},{"issue":"9","key":"991_CR61","doi-asserted-by":"publisher","first-page":"1888","DOI":"10.3899\/jrheum.120156","volume":"39","author":"RP Khubchandani","year":"2012","unstructured":"Khubchandani RP, Hasija R, Touitou I, Khemani C, Wouters CH, Rose CD. Blau arteritis resembling Takayasu disease with a novel NOD2 mutation. J Rheumatol. 2012;39(9):1888\u201392. https:\/\/doi.org\/10.3899\/jrheum.120156.","journal-title":"J Rheumatol"},{"issue":"11","key":"991_CR62","doi-asserted-by":"publisher","first-page":"2071","DOI":"10.1002\/jbmr.3532","volume":"33","author":"MP Whyte","year":"2018","unstructured":"Whyte MP, Lim E, McAlister WH, et al. Unique variant of NOD2 pediatric granulomatous arthritis with severe 1,25-dihydroxyvitamin D-mediated hypercalcemia and generalized osteosclerosis. J Bone Miner Res. 2018;33(11):2071\u201380. https:\/\/doi.org\/10.1002\/jbmr.3532.","journal-title":"J Bone Miner Res"},{"issue":"8","key":"991_CR63","doi-asserted-by":"publisher","first-page":"871","DOI":"10.1080\/080352598750013662","volume":"87","author":"N Milman","year":"1998","unstructured":"Milman N, Hoffmann AL, Byg KE. Sarcoidosis in children. Epidemiology in Danes, clinical features, diagnosis, treatment and prognosis. Acta Paediatr. 1998;87(8):871\u20138. https:\/\/doi.org\/10.1080\/080352598750013662.","journal-title":"Acta Paediatr"},{"key":"991_CR64","doi-asserted-by":"publisher","first-page":"2504","DOI":"10.1186\/1546-0096-12-33","volume":"34","author":"AE Nia","year":"2007","unstructured":"Nia AE, Nabavi M, Nasab MM, Kashef S. Central nervous system involvement in Blau syndrome: a new feature of the syndrome? J Rheumatol. 2007;34:2504\u20135. https:\/\/doi.org\/10.1186\/1546-0096-12-33.","journal-title":"J Rheumatol"},{"issue":"11","key":"991_CR65","doi-asserted-by":"publisher","first-page":"850","DOI":"10.1136\/ard.59.11.850","volume":"59","author":"V Weiler","year":"2000","unstructured":"Weiler V, Redtenbacher S, Bancher C, Fischer MB, Smolen JS. Concurrence of sarcoidosis and aortitis: case report and review of the literature. Ann Rheum Dis. 2000;59(11):850\u20133. https:\/\/doi.org\/10.1136\/ard.59.11.850.","journal-title":"Ann Rheum Dis"},{"issue":"23","key":"991_CR66","doi-asserted-by":"publisher","first-page":"2915","DOI":"10.2169\/internalmedicine.50.5298","volume":"50","author":"K Izumikawa","year":"2011","unstructured":"Izumikawa K, Motoi N, Takaya H, Miyamoto A, Eishi Y, Yoshimura K, et al. A case of concurrent sarcoidosis, aortitis syndrome and Crohn\u2019s disease. Intern Med. 2011;50(23):2915\u20137. https:\/\/doi.org\/10.2169\/internalmedicine.50.5298.","journal-title":"Intern Med"},{"issue":"6","key":"991_CR67","doi-asserted-by":"publisher","first-page":"851","DOI":"10.4103\/0366-6999.152694","volume":"128","author":"Y Liu","year":"2015","unstructured":"Liu Y, Li S, Cao J, Wang YX, Bi YL, Xu ZJ, et al. Concurrence of sarcoidosis and Takayasu aortitis. Chin Med J. 2015;128(6):851\u20132. https:\/\/doi.org\/10.4103\/0366-6999.152694.","journal-title":"Chin Med J"},{"issue":"4","key":"991_CR68","doi-asserted-by":"publisher","first-page":"311","DOI":"10.36141\/svdld.v36i4.8667","volume":"36","author":"BK Saha","year":"2019","unstructured":"Saha BK, Burns SL, Foulke LA, Judson MA. Coexistent Takayasu arteritis and sarcoidosis: a case report and review of the literature. Sarcoidosis Vasc Diffus Lung Dis. 2019;36(4):311\u20137. https:\/\/doi.org\/10.36141\/svdld.v36i4.8667.","journal-title":"Sarcoidosis Vasc Diffus Lung Dis"},{"issue":"6","key":"991_CR69","doi-asserted-by":"publisher","first-page":"937","DOI":"10.1016\/S0022-3476(05)80347-6","volume":"121","author":"JJ Nocton","year":"1992","unstructured":"Nocton JJ, Stork JE, Jacobs G, Newman AJ. Sarcoidosis associated with nephrocalcinosis in young children. J Pediatr. 1992;121(6):937\u201340. https:\/\/doi.org\/10.1016\/S0022-3476(05)80347-6.","journal-title":"J Pediatr"},{"issue":"1","key":"991_CR70","doi-asserted-by":"publisher","first-page":"68","DOI":"10.1016\/s0022-3476(81)80959-6","volume":"99","author":"GE Rodriguez","year":"1981","unstructured":"Rodriguez GE, Shin BC, Abernathy RS, Kendig ELJ. Serum angiotensin-converting enzyme activity in normal children and in those with sarcoidosis. J Pediatr. 1981;99(1):68\u201372. https:\/\/doi.org\/10.1016\/s0022-3476(81)80959-6.","journal-title":"J Pediatr"},{"issue":"2","key":"991_CR71","doi-asserted-by":"publisher","first-page":"344","DOI":"10.1093\/clinchem\/36.2\/344","volume":"36","author":"B B\u00e9n\u00e9teau-Burnat","year":"1990","unstructured":"B\u00e9n\u00e9teau-Burnat B, Baudin B, Morgant G, Baumann FC, Giboudeau J. Serum angiotensin-converting enzyme in healthy and sarcoidotic children: comparison with the reference interval for adults. Clin Chem. 1990;36(2):344\u20136. https:\/\/doi.org\/10.1093\/clinchem\/36.2\/344.","journal-title":"Clin Chem"},{"key":"991_CR72","doi-asserted-by":"publisher","first-page":"82","DOI":"10.1016\/j.ajo.2018.07.010","volume":"194","author":"RL Niederer","year":"2018","unstructured":"Niederer RL, Al-Janabi A, Lightman SL, Tomkins-Netzer O. Serum angiotensin-converting enzyme has a high negative predictive value in the investigation for systemic sarcoidosis. Am J Ophthalmol. 2018;194:82\u20137. https:\/\/doi.org\/10.1016\/j.ajo.2018.07.010.","journal-title":"Am J Ophthalmol"},{"issue":"1","key":"991_CR73","doi-asserted-by":"publisher","first-page":"91","DOI":"10.1016\/j.physbeh.2017.03.040","volume":"195","author":"P Ungprasert","year":"2016","unstructured":"Ungprasert P, Carmona EM, Crowson CS, Matteson EL. Diagnostic utility of angiotensin converting enzyme in sarcoidosis: a population-based study. Lung. 2016;195(1):91\u20135. https:\/\/doi.org\/10.1016\/j.physbeh.2017.03.040.","journal-title":"Lung."},{"issue":"10","key":"991_CR74","doi-asserted-by":"publisher","first-page":"1","DOI":"10.1371\/journal.pone.0223897","volume":"14","author":"LEM Eurelings","year":"2019","unstructured":"Eurelings LEM, Miedema JR, Dalm VASH, van Daele PLA, van Hagen PM, van Laar JAM, et al. Sensitivity and specificity of serum soluble interleukin-2 receptor for diagnosing sarcoidosis in a population of patients suspected of sarcoidosis. PLoS One. 2019;14(10):1\u201315. https:\/\/doi.org\/10.1371\/journal.pone.0223897.","journal-title":"PLoS One"},{"issue":"2","key":"991_CR75","doi-asserted-by":"publisher","first-page":"513","DOI":"10.1002\/art.37776","volume":"65","author":"G Simonini","year":"2013","unstructured":"Simonini G, Xu Z, Caputo R, de Libero C, Pagnini I, Pascual V, et al. Clinical and transcriptional response to the long-acting interleukin-1 blocker canakinumab in Blau syndrome-related uveitis. Arthritis Rheum. 2013;65(2):513\u20138.","journal-title":"Arthritis Rheum"},{"issue":"1","key":"991_CR76","doi-asserted-by":"publisher","first-page":"129","DOI":"10.1007\/s10792-015-0135-x","volume":"36","author":"M Achille","year":"2016","unstructured":"Achille M, Ilaria P, Teresa G, Roberto C, Ilir A, Piergiorgio N, et al. Successful treatment with adalimumab for severe multifocal choroiditis and panuveitis in presumed (early-onset) ocular sarcoidosis. Int Ophthalmol. 2016;36(1):129\u201335. https:\/\/doi.org\/10.1007\/s10792-015-0135-x.","journal-title":"Int Ophthalmol"},{"issue":"1","key":"991_CR77","doi-asserted-by":"publisher","first-page":"126","DOI":"10.2340\/00015555-2485","volume":"97","author":"KB Arvesen","year":"2017","unstructured":"Arvesen KB, Herlin T, Larsen DA, Koppelhus U, Ramsing M, Skytte AB, et al. Diagnosis and treatment of blau syndrome\/early-onset sarcoidosis, an autoinflammatory granulomatous disease, in an infant. Acta Derm Venereol. 2017;97(1):126\u20137. https:\/\/doi.org\/10.2340\/00015555-2485.","journal-title":"Acta Derm Venereol"},{"issue":"4","key":"991_CR78","doi-asserted-by":"publisher","first-page":"536","DOI":"10.3899\/jrheum.160672","volume":"44","author":"T Nagakura","year":"2017","unstructured":"Nagakura T, Wakiguchi H, Kubota T, Yamatou T, Yamasaki Y, Nonaka Y, et al. Tumor necrosis factor inhibitors provide longterm clinical benefits in pediatric and young adult patients with Blau syndrome. J Rheumatol. 2017;44(4):536\u20138.","journal-title":"J Rheumatol"},{"issue":"10","key":"991_CR79","doi-asserted-by":"publisher","first-page":"1066","DOI":"10.1001\/jamadermatol.2017.2172","volume":"153","author":"S Thareja","year":"2017","unstructured":"Thareja S, Kollmann K, Ardalan K, Klein-Gitelman MS, Paller AS, Arkin LM. Oral macrolides for the dermatologic manifestations of Blau syndrome. JAMA Dermatol. 2017;153(10):1066\u20137. https:\/\/doi.org\/10.1001\/jamadermatol.2017.2172.","journal-title":"JAMA Dermatol"},{"issue":"5","key":"991_CR80","doi-asserted-by":"publisher","first-page":"727","DOI":"10.1016\/j.semarthrit.2017.09.010","volume":"47","author":"L Lu","year":"2018","unstructured":"Lu L, Shen M, Jiang D, Li Y, Zheng X, Li Y, et al. Blau syndrome with good reponses to tocilizumab: a case report and focused literature review. Semin Arthritis Rheum. 2018;47(5):727\u201331. https:\/\/doi.org\/10.1016\/j.semarthrit.2017.09.010.","journal-title":"Semin Arthritis Rheum"},{"issue":"10","key":"991_CR81","doi-asserted-by":"publisher","first-page":"1483","DOI":"10.4103\/ijo.IJO_629_18","volume":"66","author":"AU Naik","year":"2018","unstructured":"Naik AU, Annamalai R, Biswas J. Uveitis in sporadic Blau syndrome: long-term follow-up of a refractory case treated successfully with adalimumab. Indian J Ophthalmol. 2018;66(10):1483\u20135. https:\/\/doi.org\/10.4103\/ijo.IJO_629_18.","journal-title":"Indian J Ophthalmol"},{"issue":"7","key":"991_CR82","doi-asserted-by":"publisher","first-page":"811","DOI":"10.1111\/ced.14016","volume":"44","author":"GWM Millington","year":"2019","unstructured":"Millington GWM, Dobson J, Holden S, Waters G, Puvanachandra N, Close R, et al. Sporadic Blau syndrome treated with adalimumab. Clin Exp Dermatol. 2019;44(7):811\u20133. https:\/\/doi.org\/10.1111\/ced.14016.","journal-title":"Clin Exp Dermatol"},{"issue":"2","key":"991_CR83","doi-asserted-by":"publisher","first-page":"611","DOI":"10.1002\/art.24222","volume":"60","author":"TM Martin","year":"2009","unstructured":"Martin TM, Zhang Z, Kurz P, Ros\u00e9 CD, Chen H, Lu H, et al. The NOD2 defect in Blau syndrome does not result in excess interleukin-1 activity. Arthritis Rheum. 2009;60(2):611\u20138. https:\/\/doi.org\/10.1002\/art.24222.","journal-title":"Arthritis Rheum"},{"issue":"2","key":"991_CR84","doi-asserted-by":"publisher","first-page":"286","DOI":"10.1002\/acr.22792","volume":"69","author":"T Reese","year":"2017","unstructured":"Reese T, Villegas L, Wood J, Gotte A. A 21-month-old male with refusal to walk, rash, and weight loss. Arthritis Care Res. 2017;69(2):286\u201393. https:\/\/doi.org\/10.1002\/acr.22792.","journal-title":"Arthritis Care Res"},{"issue":"3","key":"991_CR85","doi-asserted-by":"publisher","first-page":"e180","DOI":"10.1111\/pde.13475","volume":"35","author":"J Toral-L\u00f3pez","year":"2018","unstructured":"Toral-L\u00f3pez J, Gonz\u00e1lez-Huerta LM, Mart\u00edn-del Campo M, Messina-Baas O, Cuevas-Covarrubias SA. Familial Blau syndrome without uveitis caused by a novel mutation in the nucleotide-binding oligomerization domain-containing protein 2 gene with good response to infliximab. Pediatr Dermatol. 2018;35(3):e180\u20133. https:\/\/doi.org\/10.1111\/pde.13475.","journal-title":"Pediatr Dermatol"},{"issue":"1","key":"991_CR86","doi-asserted-by":"publisher","first-page":"111","DOI":"10.5606\/ArchRheumatol.2020.7060","volume":"35","author":"A Pa\u00e7 Kisaarslan","year":"2020","unstructured":"Pa\u00e7 Kisaarslan A, S\u00f6zeri B, \u015eahin N, et al. Blau syndrome and early-onset sarcoidosis: a six case series and review of the literature. Arch Rheumatol. 2020;35(1):111\u201327. https:\/\/doi.org\/10.5606\/ArchRheumatol.2020.7060.","journal-title":"Arch Rheumatol"},{"issue":"AUG","key":"991_CR87","doi-asserted-by":"publisher","first-page":"1","DOI":"10.3389\/fimmu.2019.01947","volume":"10","author":"S Mezouar","year":"2019","unstructured":"Mezouar S, Diarra I, Roudier J, Desnues B, Mege JL. Tumor necrosis factor-alpha antagonist interferes with the formation of granulomatous multinucleated giant cells: New insights into Mycobacterium tuberculosis infection. Front Immunol. 2019;10(AUG):1\u201314. https:\/\/doi.org\/10.3389\/fimmu.2019.01947.","journal-title":"Front Immunol"},{"issue":"1","key":"991_CR88","first-page":"56","volume":"28","author":"RP Baughman","year":"2011","unstructured":"Baughman RP, Nagai S, Balter M, et al. Defining the clinical outcome status (COS) in sarcoidosis: results of WASOG Task Force. Sarcoidosis Vasc Diffus Lung Dis. 2011;28(1):56\u201364.","journal-title":"Sarcoidosis Vasc Diffus Lung Dis"},{"issue":"2","key":"991_CR89","doi-asserted-by":"publisher","first-page":"65","DOI":"10.1097\/00005792-199903000-00001","volume":"78","author":"CJ Johns","year":"1999","unstructured":"Johns CJ, Michele TM. The clinical management of sarcoidosis. A 50-year experience at the Johns Hopkins Hospital. Medicine (Baltimore). 1999;78(2):65\u2013111. https:\/\/doi.org\/10.1097\/00005792-199903000-00001.","journal-title":"Medicine (Baltimore)"},{"issue":"1","key":"991_CR90","doi-asserted-by":"publisher","first-page":"79","DOI":"10.1007\/s12016-015-8492-9","volume":"49","author":"RP Baughman","year":"2015","unstructured":"Baughman RP, Lower EE. Treatment of Sarcoidosis. Clin Rev Allergy Immunol. 2015;49(1):79\u201392. https:\/\/doi.org\/10.1007\/s12016-015-8492-9.","journal-title":"Clin Rev Allergy Immunol"}],"container-title":["Current Allergy and Asthma Reports"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1007\/s11882-021-00991-3.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/link.springer.com\/article\/10.1007\/s11882-021-00991-3\/fulltext.html","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1007\/s11882-021-00991-3.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2021,3,2]],"date-time":"2021-03-02T22:13:50Z","timestamp":1614723230000},"score":1,"resource":{"primary":{"URL":"http:\/\/link.springer.com\/10.1007\/s11882-021-00991-3"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2021,2]]},"references-count":90,"journal-issue":{"issue":"2","published-print":{"date-parts":[[2021,2]]}},"alternative-id":["991"],"URL":"https:\/\/doi.org\/10.1007\/s11882-021-00991-3","relation":{},"ISSN":["1529-7322","1534-6315"],"issn-type":[{"value":"1529-7322","type":"print"},{"value":"1534-6315","type":"electronic"}],"subject":[],"published":{"date-parts":[[2021,2]]},"assertion":[{"value":"18 January 2021","order":1,"name":"accepted","label":"Accepted","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"9 February 2021","order":2,"name":"first_online","label":"First Online","group":{"name":"ArticleHistory","label":"Article History"}},{"order":1,"name":"Ethics","group":{"name":"EthicsHeading","label":"Compliance with Ethical Standards"}},{"value":"The authors declare no conflicts of interest relevant to this manuscript.","order":2,"name":"Ethics","group":{"name":"EthicsHeading","label":"Conflict of Interest"}},{"value":"This article does not contain any studies with human or animal subjects performed by any of the authors.","order":3,"name":"Ethics","group":{"name":"EthicsHeading","label":"Human and Animal Rights and Informed Consent"}}],"article-number":"10"}}