{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,6,26]],"date-time":"2026-06-26T14:20:36Z","timestamp":1782483636226,"version":"3.54.5"},"reference-count":49,"publisher":"Springer Science and Business Media LLC","issue":"2","license":[{"start":{"date-parts":[[2017,11,27]],"date-time":"2017-11-27T00:00:00Z","timestamp":1511740800000},"content-version":"unspecified","delay-in-days":0,"URL":"http:\/\/www.springer.com\/tdm"}],"funder":[{"name":"Intercept"},{"name":"Fondazione epatocentro Ticino"},{"name":"Swiss Association for the Study of the Liver"},{"DOI":"10.13039\/501100006484","name":"Vifor Pharma","doi-asserted-by":"publisher","id":[{"id":"10.13039\/501100006484","id-type":"DOI","asserted-by":"publisher"}]}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["Clinic Rev Allerg Immunol"],"published-print":{"date-parts":[[2018,4]]},"DOI":"10.1007\/s12016-017-8656-x","type":"journal-article","created":{"date-parts":[[2017,11,26]],"date-time":"2017-11-26T23:32:51Z","timestamp":1511739171000},"page":"295-306","update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":17,"title":["Geoepidemiology of Primary Biliary Cholangitis: Lessons from Switzerland"],"prefix":"10.1007","volume":"54","author":[{"ORCID":"https:\/\/orcid.org\/0000-0001-5004-5029","authenticated-orcid":false,"given":"Benedetta","family":"Terziroli Beretta-Piccoli","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Guido","family":"Stirnimann","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Andreas","family":"Cerny","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"David","family":"Semela","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Roxane","family":"Hessler","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Beat","family":"Helbling","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Felix","family":"Stickel","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Carolina","family":"Kalid-de Bakker","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Florian","family":"Bihl","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Emiliano","family":"Giostra","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Magdalena","family":"Filipowicz Sinnreich","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Carl","family":"Oneta","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Adriana","family":"Baserga","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Pietro","family":"Invernizzi","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Marco","family":"Carbone","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Joachim","family":"Mertens","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2017,11,27]]},"reference":[{"key":"8656_CR1","doi-asserted-by":"publisher","unstructured":"European Association for the Study of the Liver (2017) EASL Clinical Practice Guidelines: The diagnosis and management of patients with primary biliary cholangitis. J Hepatol 67:145\u2013172. \nhttps:\/\/doi.org\/10.1016\/j.jhep.2017.03.022","DOI":"10.1016\/j.jhep.2017.03.022"},{"issue":"1","key":"8656_CR2","doi-asserted-by":"publisher","first-page":"105","DOI":"10.1159\/000282073","volume":"28","author":"C Selmi","year":"2010","unstructured":"Selmi C, Gershwin ME (2010) The etiology mystery in primary biliary cirrhosis. Dig Dis Basel Switz 28(1):105\u2013115. \nhttps:\/\/doi.org\/10.1159\/000282073","journal-title":"Dig Dis Basel Switz"},{"issue":"10003","key":"8656_CR3","doi-asserted-by":"publisher","first-page":"1565","DOI":"10.1016\/S0140-6736(15)00154-3","volume":"386","author":"EJ Carey","year":"2015","unstructured":"Carey EJ, Ali AH, Lindor KD (2015) Primary biliary cirrhosis. Lancet Lond Engl 386(10003):1565\u20131575. \nhttps:\/\/doi.org\/10.1016\/S0140-6736(15)00154-3","journal-title":"Lancet Lond Engl"},{"key":"8656_CR4","doi-asserted-by":"publisher","first-page":"1338","DOI":"10.1053\/j.gastro.2014.08.029","volume":"147","author":"WJ Lammers","year":"2014","unstructured":"Lammers WJ, van Buuren HR, Hirschfield GM et al (2014) Levels of alkaline phosphatase and bilirubin are surrogate end points of outcomes of patients with primary biliary cirrhosis: an international follow-up study. Gastroenterology 147:1338\u20131349.e5; quiz e15. \nhttps:\/\/doi.org\/10.1053\/j.gastro.2014.08.029","journal-title":"Gastroenterology"},{"issue":"7","key":"8656_CR5","doi-asserted-by":"publisher","first-page":"1804","DOI":"10.1053\/j.gastro.2015.07.061","volume":"149","author":"WJ Lammers","year":"2015","unstructured":"Lammers WJ, Hirschfield GM, Corpechot C, Nevens F, Lindor KD, Janssen HL, Floreani A, Ponsioen CY, Mayo MJ, Invernizzi P, Battezzati PM, Par\u00e9s A, Burroughs AK, Mason AL, Kowdley KV, Kumagi T, Harms MH, Trivedi PJ, Poupon R, Cheung A, Lleo A, Caballeria L, Hansen BE, van Buuren HR, Global PBC Study Group (2015) Development and validation of a scoring system to predict outcomes of patients with primary biliary cirrhosis receiving ursodeoxycholic acid therapy. Gastroenterology 149(7):1804\u20131812.e4. \nhttps:\/\/doi.org\/10.1053\/j.gastro.2015.07.061","journal-title":"Gastroenterology"},{"issue":"3","key":"8656_CR6","doi-asserted-by":"publisher","first-page":"930","DOI":"10.1002\/hep.28017","volume":"63","author":"M Carbone","year":"2016","unstructured":"Carbone M, Sharp SJ, Flack S, Paximadas D, Spiess K, Adgey C, Griffiths L, Lim R, Trembling P, Williamson K, Wareham NJ, Aldersley M, Bathgate A, Burroughs AK, Heneghan MA, Neuberger JM, Thorburn D, Hirschfield GM, Cordell HJ, Alexander GJ, Jones DEJ, Sandford RN, Mells GF, and the members of the UK-PBC Consortium (2016) The UK-PBC risk scores: derivation and validation of a scoring system for long-term prediction of end-stage liver disease in primary biliary cholangitis. Hepatol Baltim Md 63(3):930\u2013950. \nhttps:\/\/doi.org\/10.1002\/hep.28017","journal-title":"Hepatol Baltim Md"},{"issue":"1","key":"8656_CR7","doi-asserted-by":"publisher","first-page":"291","DOI":"10.1002\/hep.22906","volume":"50","author":"KD Lindor","year":"2009","unstructured":"Lindor KD, Gershwin ME, Poupon R, Kaplan M, Bergasa NV, Heathcote EJ, American Association for Study of Liver Diseases (2009) Primary biliary cirrhosis. Hepatol Baltim Md 50(1):291\u2013308. \nhttps:\/\/doi.org\/10.1002\/hep.22906","journal-title":"Hepatol Baltim Md"},{"issue":"3","key":"8656_CR8","doi-asserted-by":"publisher","first-page":"659","DOI":"10.1002\/hep.21583","volume":"45","author":"S Oertelt","year":"2007","unstructured":"Oertelt S, Rieger R, Selmi C, Invernizzi P, Ansari AA, Coppel RL, Podda M, Leung PSC, Gershwin ME (2007) A sensitive bead assay for antimitochondrial antibodies: chipping away at AMA-negative primary biliary cirrhosis. Hepatol Baltim Md 45(3):659\u2013665. \nhttps:\/\/doi.org\/10.1002\/hep.21583","journal-title":"Hepatol Baltim Md"},{"issue":"4","key":"8656_CR9","doi-asserted-by":"publisher","first-page":"275","DOI":"10.1002\/hep4.1044","volume":"1","author":"A Tanaka","year":"2017","unstructured":"Tanaka A, Leung PSC, Young HA, Gershwin ME (2017) Toward solving the etiological mystery of primary biliary cholangitis. Hepatol Commun 1(4):275\u2013287. \nhttps:\/\/doi.org\/10.1002\/hep4.1044","journal-title":"Hepatol Commun"},{"issue":"03","key":"8656_CR10","doi-asserted-by":"publisher","first-page":"334","DOI":"10.1055\/s-0034-1383732","volume":"34","author":"M Nakamura","year":"2014","unstructured":"Nakamura M (2014) Clinical significance of autoantibodies in primary biliary cirrhosis. Semin Liver Dis 34(03):334\u2013340. \nhttps:\/\/doi.org\/10.1055\/s-0034-1383732","journal-title":"Semin Liver Dis"},{"issue":"3","key":"8656_CR11","doi-asserted-by":"publisher","first-page":"366","DOI":"10.1016\/S0168-8278(00)00040-4","volume":"34","author":"P Invernizzi","year":"2001","unstructured":"Invernizzi P, Podda M, Battezzati PM, Crosignani A, Zuin M, Hitchman E, Maggioni M, Meroni PL, Penner E, Wesierska-Gadek J (2001) Autoantibodies against nuclear pore complexes are associated with more active and severe liver disease in primary biliary cirrhosis. J Hepatol 34(3):366\u2013372. \nhttps:\/\/doi.org\/10.1016\/S0168-8278(00)00040-4","journal-title":"J Hepatol"},{"issue":"1","key":"8656_CR12","doi-asserted-by":"publisher","first-page":"118","DOI":"10.1002\/hep.21472","volume":"45","author":"M Nakamura","year":"2007","unstructured":"Nakamura M, Kondo H, Mori T, Komori A, Matsuyama M, Ito M, Takii Y, Koyabu M, Yokoyama T, Migita K, Daikoku M, Abiru S, Yatsuhashi H, Takezaki E, Masaki N, Sugi K, Honda K, Adachi H, Nishi H, Watanabe Y, Nakamura Y, Shimada M, Komatsu T, Saito A, Saoshiro T, Harada H, Sodeyama T, Hayashi S, Masumoto A, Sando T, Yamamoto T, Sakai H, Kobayashi M, Muro T, Koga M, Shums Z, Norman GL, Ishibashi H (2007) Anti-gp210 and anti-centromere antibodies are different risk factors for the progression of primary biliary cirrhosis. Hepatol Baltim Md 45(1):118\u2013127. \nhttps:\/\/doi.org\/10.1002\/hep.21472","journal-title":"Hepatol Baltim Md"},{"issue":"5","key":"8656_CR13","doi-asserted-by":"publisher","first-page":"1135","DOI":"10.1002\/hep.21172","volume":"43","author":"J Wesierska-Gadek","year":"2006","unstructured":"Wesierska-Gadek J, Penner E, Battezzati PM, Selmi C, Zuin M, Hitchman E, Worman HJ, Gershwin ME, Podda M, Invernizzi P (2006) Correlation of initial autoantibody profile and clinical outcome in primary biliary cirrhosis. Hepatol Baltim Md 43(5):1135\u20131144. \nhttps:\/\/doi.org\/10.1002\/hep.21172","journal-title":"Hepatol Baltim Md"},{"issue":"03","key":"8656_CR14","doi-asserted-by":"publisher","first-page":"318","DOI":"10.1055\/s-0034-1383730","volume":"34","author":"L Griffiths","year":"2014","unstructured":"Griffiths L, Dyson JK, Jones DEJ (2014) The new epidemiology of primary biliary cirrhosis. Semin Liver Dis 34(03):318\u2013328. \nhttps:\/\/doi.org\/10.1055\/s-0034-1383730","journal-title":"Semin Liver Dis"},{"issue":"6","key":"8656_CR15","doi-asserted-by":"publisher","first-page":"1083","DOI":"10.1053\/jhep.2001.29760","volume":"34","author":"MI Prince","year":"2001","unstructured":"Prince MI, Chetwynd A, Diggle P, Jarner M, Metcalf JV, James OF (2001) The geographical distribution of primary biliary cirrhosis in a well-defined cohort. Hepatol Baltim Md 34(6):1083\u20131088. \nhttps:\/\/doi.org\/10.1053\/jhep.2001.29760","journal-title":"Hepatol Baltim Md"},{"issue":"3","key":"8656_CR16","doi-asserted-by":"publisher","first-page":"525","DOI":"10.1002\/hep.21076","volume":"43","author":"A Ala","year":"2006","unstructured":"Ala A, Stanca CM, Bu-Ghanim M, Ahmado I, Branch AD, Schiano TD, Odin JA, Bach N (2006) Increased prevalence of primary biliary cirrhosis near superfund toxic waste sites. Hepatol Baltim Md 43(3):525\u2013531. \nhttps:\/\/doi.org\/10.1002\/hep.21076","journal-title":"Hepatol Baltim Md"},{"issue":"6243","key":"8656_CR17","doi-asserted-by":"publisher","first-page":"772","DOI":"10.1136\/bmj.281.6243.772","volume":"281","author":"DR Triger","year":"1980","unstructured":"Triger DR (1980) Primary biliary cirrhosis: an epidemiological study. Br Med J 281(6243):772\u2013775. \nhttps:\/\/doi.org\/10.1136\/bmj.281.6243.772","journal-title":"Br Med J"},{"key":"8656_CR18","doi-asserted-by":"publisher","first-page":"560","DOI":"10.1053\/j.gastro.2012.12.005","volume":"144","author":"M Carbone","year":"2013","unstructured":"Carbone M, Mells GF, Pells G et al (2013) Sex and age are determinants of the clinical phenotype of primary biliary cirrhosis and response to ursodeoxycholic acid. Gastroenterology 144:560\u2013569. \nhttps:\/\/doi.org\/10.1053\/j.gastro.2012.12.005","journal-title":"Gastroenterology"},{"issue":"Suppl 2","key":"8656_CR19","doi-asserted-by":"publisher","first-page":"94","DOI":"10.1159\/000440754","volume":"33","author":"H Zhang","year":"2015","unstructured":"Zhang H, Carbone M, Lleo A, Invernizzi P (2015) Geoepidemiology, genetic and environmental risk factors for PBC. Dig Dis Basel Switz 33(Suppl 2):94\u2013101. \nhttps:\/\/doi.org\/10.1159\/000440754","journal-title":"Dig Dis Basel Switz"},{"issue":"5","key":"8656_CR20","doi-asserted-by":"publisher","first-page":"1181","DOI":"10.1016\/j.jhep.2011.10.025","volume":"56","author":"K Boonstra","year":"2012","unstructured":"Boonstra K, Beuers U, Ponsioen CY (2012) Epidemiology of primary sclerosing cholangitis and primary biliary cirrhosis: a systematic review. J Hepatol 56(5):1181\u20131188. \nhttps:\/\/doi.org\/10.1016\/j.jhep.2011.10.025","journal-title":"J Hepatol"},{"issue":"7","key":"8656_CR21","doi-asserted-by":"publisher","first-page":"e200","DOI":"10.1111\/liv.12479","volume":"34","author":"M Koulentaki","year":"2014","unstructured":"Koulentaki M, Mantaka A, Sifaki-Pistolla D, Thalassinos E, Tzanakis N, Kouroumalis E (2014) Geoepidemiology and space-time analysis of primary biliary cirrhosis in Crete, Greece. Liver Int Off J Int Assoc Study Liver 34(7):e200\u2013e207. \nhttps:\/\/doi.org\/10.1111\/liv.12479","journal-title":"Liver Int Off J Int Assoc Study Liver"},{"issue":"4","key":"8656_CR22","doi-asserted-by":"publisher","first-page":"830","DOI":"10.1093\/ije\/26.4.830","volume":"26","author":"JV Metcalf","year":"1997","unstructured":"Metcalf JV, Bhopal RS, Gray J et al (1997) Incidence and prevalence of primary biliary cirrhosis in the city of Newcastle upon Tyne, England. Int J Epidemiol 26(4):830\u2013836. \nhttps:\/\/doi.org\/10.1093\/ije\/26.4.830","journal-title":"Int J Epidemiol"},{"issue":"1","key":"8656_CR23","doi-asserted-by":"publisher","first-page":"152","DOI":"10.1002\/hep.28859","volume":"65","author":"G Dahlqvist","year":"2017","unstructured":"Dahlqvist G, Gaouar F, Carrat F, Meurisse S, Chazouill\u00e8res O, Poupon R, Johanet C, Corpechot C, the French network of Immunology Laboratories (2017) Large-scale characterization study of patients with antimitochondrial antibodies but nonestablished primary biliary cholangitis. Hepatol Baltim Md 65(1):152\u2013163. \nhttps:\/\/doi.org\/10.1002\/hep.28859","journal-title":"Hepatol Baltim Md"},{"key":"8656_CR24","doi-asserted-by":"publisher","unstructured":"Selmi C, Mackay IR, Gershwin ME (2014) Chapter 62\u2014primary biliary cirrhosis. In: Autoimmune Dis. Fifth Ed. Academic Press, Boston, pp 909\u2013924, \nhttps:\/\/doi.org\/10.1016\/B978-0-12-384929-8.00062-9","DOI":"10.1016\/B978-0-12-384929-8.00062-9"},{"issue":"2-3","key":"8656_CR25","doi-asserted-by":"publisher","first-page":"192","DOI":"10.1007\/s12016-014-8427-x","volume":"48","author":"A Floreani","year":"2015","unstructured":"Floreani A, Franceschet I, Cazzagon N, Spinazz\u00e8 A, Buja A, Furlan P, Baldo V, Gershwin ME (2015) Extrahepatic autoimmune conditions associated with primary biliary cirrhosis. Clin Rev Allergy Immunol 48(2-3):192\u2013197. \nhttps:\/\/doi.org\/10.1007\/s12016-014-8427-x","journal-title":"Clin Rev Allergy Immunol"},{"issue":"10","key":"8656_CR26","doi-asserted-by":"publisher","first-page":"1175","DOI":"10.1097\/MEG.0000000000000424","volume":"27","author":"P Muratori","year":"2015","unstructured":"Muratori P, Fabbri A, Lalanne C, Lenzi M, Muratori L (2015) Autoimmune liver disease and concomitant extrahepatic autoimmune disease. Eur J Gastroenterol Hepatol 27(10):1175\u20131179. \nhttps:\/\/doi.org\/10.1097\/MEG.0000000000000424","journal-title":"Eur J Gastroenterol Hepatol"},{"issue":"5","key":"8656_CR27","doi-asserted-by":"publisher","first-page":"1194","DOI":"10.1002\/hep.20907","volume":"42","author":"ME Gershwin","year":"2005","unstructured":"Gershwin ME, Selmi C, Worman HJ, Gold EB, Watnik M, Utts J, Lindor KD, Kaplan MM, Vierling JM, USA PBC Epidemiology Group (2005) Risk factors and comorbidities in primary biliary cirrhosis: a controlled interview-based study of 1032 patients. Hepatol Baltim Md 42(5):1194\u20131202. \nhttps:\/\/doi.org\/10.1002\/hep.20907","journal-title":"Hepatol Baltim Md"},{"issue":"03","key":"8656_CR28","doi-asserted-by":"publisher","first-page":"298","DOI":"10.1055\/s-2005-916321","volume":"25","author":"P Invernizzi","year":"2005","unstructured":"Invernizzi P, Selmi C, Ranftler C, Podda M, Wesierska-Gadek J (2005) Antinuclear antibodies in primary biliary cirrhosis. Semin Liver Dis 25(03):298\u2013310. \nhttps:\/\/doi.org\/10.1055\/s-2005-916321","journal-title":"Semin Liver Dis"},{"issue":"6","key":"8656_CR29","doi-asserted-by":"publisher","first-page":"e31","DOI":"10.1111\/liv.12434","volume":"34","author":"K Boonstra","year":"2014","unstructured":"Boonstra K, Kunst AE, Stadhouders PH, Tuynman HA, Poen AC, van Nieuwkerk KMJ, Witteman EM, Hamann D, Witteman BJ, Beuers U, Ponsioen CY, the Epi PSC PBC study group (2014) Rising incidence and prevalence of primary biliary cirrhosis: a large population-based study. Liver Int Off J Int Assoc Study Liver 34(6):e31\u2013e38. \nhttps:\/\/doi.org\/10.1111\/liv.12434","journal-title":"Liver Int Off J Int Assoc Study Liver"},{"issue":"3","key":"8656_CR30","doi-asserted-by":"publisher","first-page":"871","DOI":"10.1002\/hep.22428","volume":"48","author":"C Corpechot","year":"2008","unstructured":"Corpechot C, Abenavoli L, Rabahi N, Chr\u00e9tien Y, Andr\u00e9ani T, Johanet C, Chazouill\u00e8res O, Poupon R (2008) Biochemical response to ursodeoxycholic acid and long-term prognosis in primary biliary cirrhosis. Hepatol Baltim Md 48(3):871\u2013877. \nhttps:\/\/doi.org\/10.1002\/hep.22428","journal-title":"Hepatol Baltim Md"},{"issue":"6","key":"8656_CR31","doi-asserted-by":"publisher","first-page":"1361","DOI":"10.1016\/j.jhep.2011.02.031","volume":"55","author":"C Corpechot","year":"2011","unstructured":"Corpechot C, Chazouill\u00e8res O, Poupon R (2011) Early primary biliary cirrhosis: biochemical response to treatment and prediction of long-term outcome. J Hepatol 55(6):1361\u20131367. \nhttps:\/\/doi.org\/10.1016\/j.jhep.2011.02.031","journal-title":"J Hepatol"},{"issue":"10","key":"8656_CR32","doi-asserted-by":"publisher","first-page":"2186","DOI":"10.1038\/ajg.2010.216","volume":"105","author":"T Kumagi","year":"2010","unstructured":"Kumagi T, Guindi M, Fischer SE, Arenovich T, Abdalian R, Coltescu C, Heathcote EJ, Hirschfield GM (2010) Baseline ductopenia and treatment response predict long-term histological progression in primary biliary cirrhosis. Am J Gastroenterol 105(10):2186\u20132194. \nhttps:\/\/doi.org\/10.1038\/ajg.2010.216","journal-title":"Am J Gastroenterol"},{"issue":"8","key":"8656_CR33","doi-asserted-by":"publisher","DOI":"10.1038\/ctg.2017.43","volume":"8","author":"K-S Cheung","year":"2017","unstructured":"Cheung K-S, Seto W-K, Fung J, Lai CL, Yuen MF (2017) Epidemiology and natural history of primary biliary cholangitis in the Chinese: a territory-based study in Hong Kong between 2000 and 2015. Clin Transl Gastroenterol 8(8):e116. \nhttps:\/\/doi.org\/10.1038\/ctg.2017.43","journal-title":"Clin Transl Gastroenterol"},{"issue":"1-2","key":"8656_CR34","doi-asserted-by":"publisher","first-page":"13","DOI":"10.3121\/cmr.2017.1351","volume":"15","author":"R Kanth","year":"2017","unstructured":"Kanth R, Shrestha RB, Rai I, Van Wormer JJ, Roy PK (2017) Incidence of primary biliary cholangitis in a rural midwestern population. Clin Med Res 15(1-2):13\u201318. \nhttps:\/\/doi.org\/10.3121\/cmr.2017.1351","journal-title":"Clin Med Res"},{"key":"8656_CR35","doi-asserted-by":"publisher","unstructured":"Lleo A, Jepsen P, Morenghi E, Carbone M, Moroni L, Battezzati PM, Podda M, Mackay IR, Gershwin ME, Invernizzi P (2016) Evolving trends in female to male incidence and male mortality of primary biliary cholangitis. Sci Rep 6(1). \nhttps:\/\/doi.org\/10.1038\/srep25906","DOI":"10.1038\/srep25906"},{"issue":"1","key":"8656_CR36","doi-asserted-by":"publisher","first-page":"154","DOI":"10.1111\/apt.13448","volume":"43","author":"K-A Kim","year":"2016","unstructured":"Kim K-A, Ki M, Choi HY, Kim BH, Jang ES, Jeong SH (2016) Population-based epidemiology of primary biliary cirrhosis in South Korea. Aliment Pharmacol Ther 43(1):154\u2013162. \nhttps:\/\/doi.org\/10.1111\/apt.13448","journal-title":"Aliment Pharmacol Ther"},{"issue":"4","key":"8656_CR37","doi-asserted-by":"publisher","first-page":"492","DOI":"10.1093\/aje\/kwt308","volume":"179","author":"RJQ McNally","year":"2014","unstructured":"McNally RJQ, James PW, Ducker S, Norman PD, James OFW (2014) No rise in incidence but geographical heterogeneity in the occurrence of primary biliary cirrhosis in North East England. Am J Epidemiol 179(4):492\u2013498. \nhttps:\/\/doi.org\/10.1093\/aje\/kwt308","journal-title":"Am J Epidemiol"},{"issue":"8","key":"8656_CR38","doi-asserted-by":"publisher","first-page":"e193","DOI":"10.1016\/j.ejim.2012.09.004","volume":"23","author":"J-S Delgado","year":"2012","unstructured":"Delgado J-S, Vodonos A, Delgado B, Jotkowitz A, Rosenthal A, Fich A, Novack V (2012) Primary biliary cirrhosis in Southern Israel: a 20 year follow up study. Eur J Intern Med 23(8):e193\u2013e198. \nhttps:\/\/doi.org\/10.1016\/j.ejim.2012.09.004","journal-title":"Eur J Intern Med"},{"issue":"7","key":"8656_CR39","doi-asserted-by":"publisher","first-page":"824","DOI":"10.1097\/MEG.0b013e328353753d","volume":"24","author":"TR Baldursdottir","year":"2012","unstructured":"Baldursdottir TR, Bergmann OM, Jonasson JG, Ludviksson BR, Axelsson TA, Bj\u00f6rnsson ES (2012) The epidemiology and natural history of primary biliary cirrhosis: a nationwide population-based study. Eur J Gastroenterol Hepatol 24(7):824\u2013830. \nhttps:\/\/doi.org\/10.1097\/MEG.0b013e328353753d","journal-title":"Eur J Gastroenterol Hepatol"},{"issue":"4","key":"8656_CR40","doi-asserted-by":"publisher","first-page":"796","DOI":"10.1007\/s12072-011-9329-0","volume":"6","author":"JH Ngu","year":"2012","unstructured":"Ngu JH, Gearry RB, Wright AJ, Stedman CAM (2012) Low incidence and prevalence of primary biliary cirrhosis in Canterbury, New Zealand: a population-based study. Hepatol Int 6(4):796\u2013800. \nhttps:\/\/doi.org\/10.1007\/s12072-011-9329-0","journal-title":"Hepatol Int"},{"issue":"6","key":"8656_CR41","first-page":"622","volume":"9","author":"VH Chong","year":"2010","unstructured":"Chong VH, Telisinghe PU, Jalihal A (2010) Primary biliary cirrhosis in Brunei Darussalam. Hepatobiliary Pancreat Dis Int HBPD INT 9(6):622\u2013628","journal-title":"Hepatobiliary Pancreat Dis Int HBPD INT"},{"issue":"4","key":"8656_CR42","doi-asserted-by":"publisher","first-page":"599","DOI":"10.1111\/j.1440-1746.2007.05058.x","volume":"23","author":"R-K Wong","year":"2008","unstructured":"Wong R-K, Lim S-G, Wee A, Chan YH, Aung MO, Wai CT (2008) Primary biliary cirrhosis in Singapore: evaluation of demography, prognostic factors and natural course in a multi-ethnic population. J Gastroenterol Hepatol 23(4):599\u2013605. \nhttps:\/\/doi.org\/10.1111\/j.1440-1746.2007.05058.x","journal-title":"J Gastroenterol Hepatol"},{"issue":"6","key":"8656_CR43","doi-asserted-by":"publisher","first-page":"909","DOI":"10.1007\/s12072-016-9767-9","volume":"10","author":"A Tanaka","year":"2016","unstructured":"Tanaka A, Ma X, Yokosuka O, Weltman M, You H, Amarapurkar DN, Kim YJ, Abbas Z, Payawal DA, Chang ML, Efe C, Ozaslan E, Abe M, Mitchell-Thain R, Zeniya M, Han KH, Vierling JM, Takikawa H (2016) Autoimmune liver diseases in the Asia-Pacific region: proceedings of APASL symposium on AIH and PBC 2016. Hepatol Int 10(6):909\u2013915. \nhttps:\/\/doi.org\/10.1007\/s12072-016-9767-9","journal-title":"Hepatol Int"},{"issue":"1","key":"8656_CR44","doi-asserted-by":"publisher","DOI":"10.1186\/1471-230X-10-100","volume":"10","author":"H Liu","year":"2010","unstructured":"Liu H, Liu Y, Wang L, Xu D, Lin B, Zhong R, Gong S, Podda M, Invernizzi P (2010) Prevalence of primary biliary cirrhosis in adults referring hospital for annual health check-up in Southern China. BMC Gastroenterol 10(1):100. \nhttps:\/\/doi.org\/10.1186\/1471-230X-10-100","journal-title":"BMC Gastroenterol"},{"issue":"6","key":"8656_CR45","doi-asserted-by":"publisher","first-page":"1884","DOI":"10.1002\/hep.23210","volume":"50","author":"RP Myers","year":"2009","unstructured":"Myers RP, Shaheen AAM, Fong A, Burak KW, Wan A, Swain MG, Hilsden RJ, Sutherland L, Quan H (2009) Epidemiology and natural history of primary biliary cirrhosis in a Canadian health region: a population-based study. Hepatol Baltim Md 50(6):1884\u20131892. \nhttps:\/\/doi.org\/10.1002\/hep.23210","journal-title":"Hepatol Baltim Md"},{"issue":"15-16","key":"8656_CR46","doi-asserted-by":"publisher","first-page":"1211","DOI":"10.1016\/j.cca.2012.03.020","volume":"413","author":"MG Mytilinaiou","year":"2012","unstructured":"Mytilinaiou MG, Meyer W, Scheper T, Rigopoulou EI, Probst C, Koutsoumpas AL, Abeles D, Burroughs AK, Komorowski L, Vergani D, Bogdanos DP (2012) Diagnostic and clinical utility of antibodies against the nuclear body promyelocytic leukaemia and Sp100 antigens in patients with primary biliary cirrhosis. Clin Chim Acta Int J Clin Chem 413(15-16):1211\u20131216. \nhttps:\/\/doi.org\/10.1016\/j.cca.2012.03.020","journal-title":"Clin Chim Acta Int J Clin Chem"},{"issue":"2","key":"8656_CR47","doi-asserted-by":"publisher","first-page":"360","DOI":"10.1002\/hep.510280210","volume":"28","author":"AJ Czaja","year":"1998","unstructured":"Czaja AJ (1998) Frequency and nature of the variant syndromes of autoimmune liver disease. Hepatol Baltim Md 28(2):360\u2013365. \nhttps:\/\/doi.org\/10.1002\/hep.510280210","journal-title":"Hepatol Baltim Md"},{"issue":"2","key":"8656_CR48","doi-asserted-by":"publisher","first-page":"296","DOI":"10.1002\/hep.510280203","volume":"28","author":"O Chazouill\u00e8res","year":"1998","unstructured":"Chazouill\u00e8res O, Wendum D, Serfaty L, Montembault S, Rosmorduc O, Poupon R (1998) Primary biliary cirrhosis-autoimmune hepatitis overlap syndrome: clinical features and response to therapy. Hepatol Baltim Md 28(2):296\u2013301. \nhttps:\/\/doi.org\/10.1002\/hep.510280203","journal-title":"Hepatol Baltim Md"},{"issue":"10","key":"8656_CR49","doi-asserted-by":"publisher","first-page":"1681","DOI":"10.1111\/j.1440-1746.2010.06384.x","volume":"25","author":"JH Ngu","year":"2010","unstructured":"Ngu JH, Bechly K, Chapman BA, Burt MJ, Barclay ML, Gearry RB, Stedman CAM (2010) Population-based epidemiology study of autoimmune hepatitis: a disease of older women? J Gastroenterol Hepatol 25(10):1681\u20131686. \nhttps:\/\/doi.org\/10.1111\/j.1440-1746.2010.06384.x","journal-title":"J Gastroenterol Hepatol"}],"container-title":["Clinical Reviews in Allergy &amp; Immunology"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/link.springer.com\/article\/10.1007\/s12016-017-8656-x\/fulltext.html","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1007\/s12016-017-8656-x.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1007\/s12016-017-8656-x.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2018,8,23]],"date-time":"2018-08-23T08:12:20Z","timestamp":1535011940000},"score":1,"resource":{"primary":{"URL":"http:\/\/link.springer.com\/10.1007\/s12016-017-8656-x"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2017,11,27]]},"references-count":49,"journal-issue":{"issue":"2","published-print":{"date-parts":[[2018,4]]}},"alternative-id":["8656"],"URL":"https:\/\/doi.org\/10.1007\/s12016-017-8656-x","relation":{},"ISSN":["1080-0549","1559-0267"],"issn-type":[{"value":"1080-0549","type":"print"},{"value":"1559-0267","type":"electronic"}],"subject":[],"published":{"date-parts":[[2017,11,27]]}}}