{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,23]],"date-time":"2026-10-23T06:01:18Z","timestamp":1792735278544,"version":"4.5.0"},"reference-count":75,"publisher":"Springer Science and Business Media LLC","issue":"2","license":[{"start":{"date-parts":[[2021,1,6]],"date-time":"2021-01-06T00:00:00Z","timestamp":1609891200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.springer.com\/tdm"},{"start":{"date-parts":[[2021,1,6]],"date-time":"2021-01-06T00:00:00Z","timestamp":1609891200000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/www.springer.com\/tdm"}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["Clinic Rev Allerg Immunol"],"published-print":{"date-parts":[[2021,4]]},"DOI":"10.1007\/s12016-020-08822-5","type":"journal-article","created":{"date-parts":[[2021,1,6]],"date-time":"2021-01-06T04:04:14Z","timestamp":1609905854000},"page":"293-304","update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":200,"title":["Interstitial Lung Disease in Anti-MDA5 Positive Dermatomyositis"],"prefix":"10.1007","volume":"60","author":[{"given":"Wanlong","family":"Wu","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Li","family":"Guo","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Yakai","family":"Fu","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Kaiwen","family":"Wang","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Danting","family":"Zhang","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Wenwen","family":"Xu","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Zhiwei","family":"Chen","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Shuang","family":"Ye","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2021,1,6]]},"reference":[{"issue":"5","key":"8822_CR1","doi-asserted-by":"publisher","first-page":"1571","DOI":"10.1002\/art.21023","volume":"52","author":"S Sato","year":"2005","unstructured":"Sato S, Hirakata M, Kuwana M, Suwa A, Inada S, Mimori T, Nishikawa T, Oddis CV, Ikeda Y (2005) Autoantibodies to a 140-kd polypeptide, CADM-140, in Japanese patients with clinically amyopathic dermatomyositis. Arthritis Rheum 52(5):1571\u20131576. https:\/\/doi.org\/10.1002\/art.21023","journal-title":"Arthritis Rheum"},{"issue":"7","key":"8822_CR2","doi-asserted-by":"publisher","first-page":"2193","DOI":"10.1002\/art.24621","volume":"60","author":"S Sato","year":"2009","unstructured":"Sato S, Hoshino K, Satoh T, Fujita T, Kawakami Y, Fujita T, Kuwana M (2009) RNA helicase encoded by melanoma differentiation-associated gene 5 is a major autoantigen in patients with clinically amyopathic dermatomyositis association with rapidly progressive interstitial lung disease. Arthritis Rheum 60(7):2193\u20132200. https:\/\/doi.org\/10.1002\/art.24621","journal-title":"Arthritis Rheum"},{"issue":"4","key":"8822_CR3","doi-asserted-by":"publisher","first-page":"626","DOI":"10.1067\/mjd.2002.120621","volume":"46","author":"RD Sontheimer","year":"2002","unstructured":"Sontheimer RD (2002) Would a new name hasten the acceptance of amyopathic dermatomyositis (dermatomyositis sine myositis) as a distinctive subset within the idiopathic inflammatory dermatomyopathies spectrum of clinical illness? J Am Acad Dermatol 46(4):626\u2013636. https:\/\/doi.org\/10.1067\/mjd.2002.120621","journal-title":"J Am Acad Dermatol"},{"issue":"1","key":"8822_CR4","doi-asserted-by":"publisher","first-page":"70","DOI":"10.1016\/j.nmd.2019.10.005","volume":"30","author":"Mammen AL, Allenbach Y, Stenzel W, Benveniste O, Group EtWS","year":"2020","unstructured":"Mammen AL, Allenbach Y, Stenzel W, Benveniste O, Group EtWS (2020) 239th ENMC International Workshop: Classification of dermatomyositis, Amsterdam, the Netherlands, 14\u201316 December 2018. Neuromuscul Disord 30(1):70\u201392. https:\/\/doi.org\/10.1016\/j.nmd.2019.10.005","journal-title":"Neuromuscul Disord"},{"key":"8822_CR5","doi-asserted-by":"publisher","DOI":"10.1016\/j.chest.2020.04.057","author":"X Lian","year":"2020","unstructured":"Lian X, Zou J, Guo Q, Chen S, Lu L, Wang R, Zhou M, Fu Q, Ye Y, Bao C (2020) Mortality risk prediction in amyopathic dermatomyositis associated with interstitial lung disease: the FLAIR model. Chest. https:\/\/doi.org\/10.1016\/j.chest.2020.04.057","journal-title":"Chest"},{"issue":"12","key":"8822_CR6","doi-asserted-by":"publisher","first-page":"1955","DOI":"10.1136\/annrheumdis-2017-211468","volume":"76","author":"Lundberg IE, Tjarnlund A, Bottai M, Werth VP, Pilkington C, Visser M, Alfredsson L, Amato AA, Barohn RJ, Liang MH, Singh JA, Aggarwal R, Arnardottir S, Chinoy H, Cooper RG, Danko K, Dimachkie MM, Feldman BM, Torre IG, Gordon P, Hayashi T, Katz JD, Kohsaka H, Lachenbruch PA, Lang BA, Li Y, Oddis CV, Olesinska M, Reed AM, Rutkowska-Sak L, Sanner H, Selva-O'Callaghan A, Song YW, Vencovsky J, Ytterberg SR, Miller FW, Rider LG, International Myositis Classification Criteria Project consortium TEr, The Juvenile Dermatomyositis Cohort Biomarker S, Repository","year":"2017","unstructured":"Lundberg IE, Tjarnlund A, Bottai M, Werth VP, Pilkington C, Visser M, Alfredsson L, Amato AA, Barohn RJ, Liang MH, Singh JA, Aggarwal R, Arnardottir S, Chinoy H, Cooper RG, Danko K, Dimachkie MM, Feldman BM, Torre IG, Gordon P, Hayashi T, Katz JD, Kohsaka H, Lachenbruch PA, Lang BA, Li Y, Oddis CV, Olesinska M, Reed AM, Rutkowska-Sak L, Sanner H, Selva-O\u2019Callaghan A, Song YW, Vencovsky J, Ytterberg SR, Miller FW, Rider LG, International Myositis Classification Criteria Project consortium TEr, The Juvenile Dermatomyositis Cohort Biomarker S, Repository (2017) 2017 European League Against Rheumatism\/American College of Rheumatology classification criteria for adult and juvenile idiopathic inflammatory myopathies and their major subgroups. Ann Rheum Dis 76(12):1955\u20131964. https:\/\/doi.org\/10.1136\/annrheumdis-2017-211468","journal-title":"Ann Rheum Dis"},{"key":"8822_CR7","doi-asserted-by":"publisher","first-page":"1","DOI":"10.1016\/j.jim.2016.02.017","volume":"433","author":"I Cavazzana","year":"2016","unstructured":"Cavazzana I, Fredi M, Ceribelli A, Mordenti C, Ferrari F, Carabellese N, Tincani A, Satoh M, Franceschini F (2016) Testing for myositis specific autoantibodies: comparison between line blot and immunoprecipitation assays in 57 myositis sera. J Immunol Methods 433:1\u20135. https:\/\/doi.org\/10.1016\/j.jim.2016.02.017","journal-title":"J Immunol Methods"},{"issue":"4","key":"8822_CR8","doi-asserted-by":"publisher","first-page":"e0154285","DOI":"10.1371\/journal.pone.0154285","volume":"11","author":"S Sato","year":"2016","unstructured":"Sato S, Murakami A, Kuwajima A, Takehara K, Mimori T, Kawakami A, Mishima M, Suda T, Seishima M, Fujimoto M, Kuwana M (2016) Clinical utility of an enzyme-linked immunosorbent assay for detecting anti-melanoma differentiation-associated gene 5 autoantibodies. PLoS ONE 11(4):e0154285. https:\/\/doi.org\/10.1371\/journal.pone.0154285","journal-title":"PLoS ONE"},{"key":"8822_CR9","doi-asserted-by":"publisher","first-page":"48","DOI":"10.1016\/j.jaut.2019.04.001","volume":"101","author":"Z Betteridge","year":"2019","unstructured":"Betteridge Z, Tansley S, Shaddick G, Chinoy H, Cooper RG, New RP, Lilleker JB, Vencovsky J, Chazarain L, Danko K, Nagy-Vincze M, Bodoki L, Dastmalchi M, Ekholm L, Lundberg IE, McHugh N, contributors UK, (2019) Frequency, mutual exclusivity and clinical associations of myositis autoantibodies in a combined European cohort of idiopathic inflammatory myopathy patients. J Autoimmun 101:48\u201355. https:\/\/doi.org\/10.1016\/j.jaut.2019.04.001","journal-title":"J Autoimmun"},{"issue":"8","key":"8822_CR10","doi-asserted-by":"publisher","first-page":"1307","DOI":"10.1002\/acr.21992","volume":"65","author":"JC Hall","year":"2013","unstructured":"Hall JC, Casciola-Rosen L, Samedy L-A, Werner J, Owoyemi K, Danoff SK, Christopher-Stine L (2013) Anti-melanoma differentiation-associated protein 5-associated dermatomyositis: expanding the clinical spectrum. Arthritis Care & Research 65(8):1307\u20131315. https:\/\/doi.org\/10.1002\/acr.21992","journal-title":"Arthritis Care & Research"},{"issue":"5","key":"8822_CR11","doi-asserted-by":"publisher","first-page":"689","DOI":"10.1002\/acr.22728","volume":"68","author":"S Moghadam-Kia","year":"2016","unstructured":"Moghadam-Kia S, Oddis CV, Sato S, Kuwana M, Aggarwal R (2016) Anti-melanoma differentiation-associated gene 5 is associated with rapidly progressive lung disease and poor survival in US patients with amyopathic and myopathic dermatomyositis. Arthritis Care & Research 68(5):689\u2013694. https:\/\/doi.org\/10.1002\/acr.22728","journal-title":"Arthritis Care & Research"},{"issue":"5","key":"8822_CR12","doi-asserted-by":"publisher","first-page":"511","DOI":"10.1684\/ejd.2019.3634","volume":"29","author":"S-i Motegi","year":"2019","unstructured":"Motegi S-i, Sekiguchi A, Toki S, Kishi C, Endo Y, Yasuda M, Ikeuchi H, Sakairi T, Hara K, Yamaguchi K, Maeno T, Hiromura K, Ishikawa O (2019) Clinical features and poor prognostic factors of anti-melanoma differentiation-associated gene 5 antibody-positive dermatomyositis with rapid progressive interstitial lung disease. European Journal of Dermatology 29(5):511\u2013517. https:\/\/doi.org\/10.1684\/ejd.2019.3634","journal-title":"European Journal of Dermatology"},{"issue":"6","key":"8822_CR13","doi-asserted-by":"publisher","first-page":"788","DOI":"10.1164\/rccm.2009-040GL","volume":"183","author":"G Raghu","year":"2011","unstructured":"Raghu G, Collard HR, Egan JJ, Martinez FJ, Behr J, Brown KK, Colby TV, Cordier JF, Flaherty KR, Lasky JA, Lynch DA, Ryu JH, Swigris JJ, Wells AU, Ancochea J, Bouros D, Carvalho C, Costabel U, Ebina M, Hansell DM, Johkoh T, Kim DS, King TE Jr, Kondoh Y, Myers J, Muller NL, Nicholson AG, Richeldi L, Selman M, Dudden RF, Griss BS, Protzko SL, Schunemann HJ, Fibrosis AEJACoIP, (2011) An official ATS\/ERS\/JRS\/ALAT statement: idiopathic pulmonary fibrosis: evidence-based guidelines for diagnosis and management. Am J Respir Crit Care Med 183(6):788\u2013824. https:\/\/doi.org\/10.1164\/rccm.2009-040GL","journal-title":"Am J Respir Crit Care Med"},{"key":"8822_CR14","doi-asserted-by":"publisher","first-page":"1","DOI":"10.1016\/j.rmed.2018.05.010","volume":"140","author":"K Yamaguchi","year":"2018","unstructured":"Yamaguchi K, Yamaguchi A, Kashiwagi C, Sawada Y, Taguchi K, Umetsu K, Oshima K, Uchida M, Suzuki M, Kono S, Takemura M, Masubuchi H, Kitahara S, Hara K, Maeno T, Motegi S-i, Muro Y, Sakairi T, Hisada T, Kurabayashi M (2018) Differential clinical features of patients with clinically amyopathic dermatomyositis who have circulating anti-MDA5 autoantibodies with or without myositis-associated autoantibodies. Respir Med 140:1\u20135. https:\/\/doi.org\/10.1016\/j.rmed.2018.05.010","journal-title":"Respir Med"},{"issue":"6","key":"8822_CR15","doi-asserted-by":"publisher","first-page":"1655","DOI":"10.1007\/s10067-019-04457-w","volume":"38","author":"L Jiang","year":"2019","unstructured":"Jiang L, Wang Y, Peng Q, Shu X, Wang G, Wu X (2019) Serum YKL-40 level is associated with severity of interstitial lung disease and poor prognosis in dermatomyositis with anti-MDA5 antibody. Clin Rheumatol 38(6):1655\u20131663. https:\/\/doi.org\/10.1007\/s10067-019-04457-w","journal-title":"Clin Rheumatol"},{"issue":"11","key":"8822_CR16","doi-asserted-by":"publisher","first-page":"1971","DOI":"10.1007\/s00296-019-04398-2","volume":"39","author":"K Huang","year":"2019","unstructured":"Huang K, Vinik O, Shojania K, Yeung J, Shupak R, Nimmo M, Avina-Zubieta JA (2019) Clinical spectrum and therapeutics in Canadian patients with anti-melanoma differentiation-associated gene 5 (MDA5)-positive dermatomyositis: a case-based review. Rheumatol Int 39(11):1971\u20131981. https:\/\/doi.org\/10.1007\/s00296-019-04398-2","journal-title":"Rheumatol Int"},{"issue":"7","key":"8822_CR17","doi-asserted-by":"publisher","first-page":"1278","DOI":"10.1093\/rheumatology\/ker518","volume":"51","author":"T Koga","year":"2012","unstructured":"Koga T, Fujikawa K, Horai Y, Okada A, Kawashiri S-y, Iwamoto N, Suzuki T, Nakashima Y, Tamai M, Arima K, Yamasaki S, Nakamura H, Origuchi T, Hamaguchi Y, Fujimoto M, Ishimatsu Y, Mukae H, Kuwana M, Kohno S, Eguchi K, Aoyagi K, Kawakami A (2012) The diagnostic utility of anti-melanoma differentiation-associated gene 5 antibody testing for predicting the prognosis of Japanese patients with DM. Rheumatology 51(7):1278\u20131284. https:\/\/doi.org\/10.1093\/rheumatology\/ker518","journal-title":"Rheumatology"},{"issue":"1","key":"8822_CR18","doi-asserted-by":"publisher","first-page":"75","DOI":"10.1016\/j.tim.2018.08.007","volume":"27","author":"AG Dias Junior","year":"2019","unstructured":"Dias Junior AG, Sampaio NG, Rehwinkel J (2019) A balancing act: MDA5 in antiviral immunity and autoinflammation. Trends Microbiol 27(1):75\u201385. https:\/\/doi.org\/10.1016\/j.tim.2018.08.007","journal-title":"Trends Microbiol"},{"key":"8822_CR19","doi-asserted-by":"publisher","unstructured":"Muro Y, Sugiura K, Hoshino K, Akiyama M, Tamakoshi K (2011) Epidemiologic study of clinically amyopathic dermatomyositis and anti-melanoma differentiation-associated gene 5 antibodies in central Japan. Arthritis Research & Therapy 13 (6).\u00a0https:\/\/doi.org\/10.1186\/ar3547","DOI":"10.1186\/ar3547"},{"key":"8822_CR20","doi-asserted-by":"publisher","unstructured":"Nishina N, Sato S, Masui K, Gono T, Kuwana M (2020) Seasonal and residential clustering at disease onset of anti-MDA5-associated interstitial lung disease. RMD Open 6 (2). https:\/\/doi.org\/10.1136\/rmdopen-2020-001202","DOI":"10.1136\/rmdopen-2020-001202"},{"issue":"10","key":"8822_CR21","first-page":"S822","volume":"64","author":"T Gono","year":"2012","unstructured":"Gono T, Kawaguchi Y, Kuwana M, Sugiura T, Furuya T, Takagi K, Ichida H, Katsumata Y, Hanaoka M, Okamoto Y, Ota Y, Kataoka S, Yamanaka H (2012) HLA-DRB1*0101\/*0405 is associated with susceptibility to anti-MDA5 antibody-positive dermatomyositis in the Japanese population. Arthritis Rheum 64(10):S822\u2013S822","journal-title":"Arthritis Rheum"},{"issue":"7","key":"8822_CR22","doi-asserted-by":"publisher","first-page":"996","DOI":"10.1136\/annrheumdis-2019-215046","volume":"78","author":"S Rothwell","year":"2019","unstructured":"Rothwell S, Chinoy H, Lamb JA, Miller FW, Rider LG, Wedderburn LR, McHugh NJ, Mammen AL, Betteridge ZE, Tansley SL, Bowes J, Vencovsky J, Deakin CT, Danko K, Vidya L, Selva-O\u2019Callaghan A, Pachman LM, Reed AM, Molberg O, Benveniste O, Mathiesen PR, Radstake T, Doria A, de Bleecker J, Lee AT, Hanna MG, Machado PM, Ollier WE, Gregersen PK, Padyukov L, O\u2019Hanlon TP, Cooper RG, Lundberg IE, Myositis Genetics C (2019) Focused HLA analysis in Caucasians with myositis identifies significant associations with autoantibody subgroups. Ann Rheum Dis 78(7):996\u20131002. https:\/\/doi.org\/10.1136\/annrheumdis-2019-215046","journal-title":"Ann Rheum Dis"},{"issue":"4","key":"8822_CR23","doi-asserted-by":"publisher","first-page":"602","DOI":"10.1136\/annrheumdis-2017-212149","volume":"77","author":"Y Kochi","year":"2018","unstructured":"Kochi Y, Kamatani Y, Kondo Y, Suzuki A, Kawakami E, Hiwa R, Momozawa Y, Fujimoto M, Jinnin M, Tanaka Y, Kanda T, Cooper RG, Chinoy H, Rothwell S, Lamb JA, Vencovsky J, Mann H, Ohmura K, Myouzen K, Ishigaki K, Nakashima R, Hosono Y, Tsuboi H, Kawasumi H, Iwasaki Y, Kajiyama H, Horita T, Ogawa-Momohara M, Takamura A, Tsunoda S, Shimizu J, Fujio K, Amano H, Mimori A, Kawakami A, Umehara H, Takeuchi T, Sano H, Muro Y, Atsumi T, Mimura T, Kawaguchi Y, Mimori T, Takahashi A, Kubo M, Kohsaka H, Sumida T, Yamamoto K (2018) Splicing variant of WDFY4 augments MDA5 signalling and the risk of clinically amyopathic dermatomyositis. Ann Rheum Dis 77(4):602\u2013611. https:\/\/doi.org\/10.1136\/annrheumdis-2017-212149","journal-title":"Ann Rheum Dis"},{"issue":"6","key":"8822_CR24","doi-asserted-by":"publisher","first-page":"1276","DOI":"10.1016\/j.jid.2019.10.020","volume":"140","author":"C Cassius","year":"2020","unstructured":"Cassius C, Amode R, Delord M, Battistella M, Poirot J, How-Kit A, Lepelletier C, Jachiet M, de Masson A, Frumholtz L, Cordoliani F, Boccara D, Lehmann-Che J, Wong J, Dubanchet S, Alberdi AJ, Merandet M, Bagot M, Bensussan A, Bouazia J-D, Le Buanec H (2020) MDA5(+) D dermatomyositis is associated with stronger skin type I interferon transcriptomic signature with upregulation of IFN-kappa transcript. Journal of Investigative Dermatology 140(6):1276\u20131279. https:\/\/doi.org\/10.1016\/j.jid.2019.10.020","journal-title":"Journal of Investigative Dermatology"},{"issue":"5","key":"8822_CR25","doi-asserted-by":"publisher","first-page":"786","DOI":"10.1093\/rheumatology\/key386","volume":"58","author":"N Ono","year":"2019","unstructured":"Ono N, Kai K, Maruyama A, Sakai M, Sadanaga Y, Koarada S, Inoue T, Tada Y (2019) The relationship between type 1 IFN and vasculopathy in anti-MDA5 antibody-positive dermatomyositis patients. Rheumatology (Oxford) 58(5):786\u2013791. https:\/\/doi.org\/10.1093\/rheumatology\/key386","journal-title":"Rheumatology (Oxford)"},{"issue":"9","key":"8822_CR26","doi-asserted-by":"publisher","first-page":"1234","DOI":"10.1136\/annrheumdis-2019-216599","volume":"79","author":"I Pinal-Fernandez","year":"2020","unstructured":"Pinal-Fernandez I, Casal-Dominguez M, Derfoul A, Pak K, Miller FW, Milisenda JC, Grau-Junyent JM, Selva-O\u2019Callaghan A, Carrion-Ribas C, Paik JJ, Albayda J, Christopher-Stine L, Lloyd TE, Corse AM, Mammen AL (2020) Machine learning algorithms reveal unique gene expression profiles in muscle biopsies from patients with different types of myositis. Ann Rheum Dis 79(9):1234\u20131242. https:\/\/doi.org\/10.1136\/annrheumdis-2019-216599","journal-title":"Ann Rheum Dis"},{"issue":"3","key":"8822_CR27","doi-asserted-by":"publisher","first-page":"691","DOI":"10.1016\/j.ajpath.2015.11.010","volume":"186","author":"Y Allenbach","year":"2016","unstructured":"Allenbach Y, Leroux G, Suarez-Calvet X, Preusse C, Gallardo E, Hervier B, Rigolet A, Hie M, Pehl D, Limal N, Hufnagl P, Zerbe N, Meyer A, Aouizerate J, Uzunhan Y, Maisonobe T, Goebel HH, Benveniste O, Stenzel W, French Myositis N (2016) Dermatomyositis with or without anti-melanoma differentiation-associated gene 5 antibodies: common interferon signature but distinct NOS2 expression. Am J Pathol 186(3):691\u2013700. https:\/\/doi.org\/10.1016\/j.ajpath.2015.11.010","journal-title":"Am J Pathol"},{"issue":"1","key":"8822_CR28","doi-asserted-by":"publisher","first-page":"85","DOI":"10.3109\/14397595.2014.900843","volume":"25","author":"Y Horai","year":"2015","unstructured":"Horai Y, Koga T, Fujikawa K, Takatani A, Nishino A, Nakashima Y, Suzuki T, Kawashiri S-y, Iwamoto N, Ichinose K, Tamai M, Nakamura H, Ida H, Kakugawa T, Sakamoto N, Ishimatsu Y, Mukae H, Hamaguchi Y, Fujimoto M, Kuwana M, Origuchi T, Kohno S, Kawakami A (2015) Serum interferon-alpha is a useful biomarker in patients with anti-melanoma differentiation-associated gene 5 (MDA5) antibody-positive dermatomyositis. Mod Rheumatol 25(1):85\u201389. https:\/\/doi.org\/10.3109\/14397595.2014.900843","journal-title":"Mod Rheumatol"},{"issue":"5","key":"8822_CR29","doi-asserted-by":"publisher","first-page":"1090","DOI":"10.1111\/bjd.16917","volume":"180","author":"SH Zhang","year":"2019","unstructured":"Zhang SH, Zhao Y, Xie QB, Jiang Y, Wu YK, Yan B (2019) Aberrant activation of the type I interferon system may contribute to the pathogenesis of anti-melanoma differentiation-associated gene 5 dermatomyositis. Br J Dermatol 180(5):1090\u20131098. https:\/\/doi.org\/10.1111\/bjd.16917","journal-title":"Br J Dermatol"},{"issue":"12","key":"8822_CR30","doi-asserted-by":"publisher","first-page":"2196","DOI":"10.1093\/rheumatology\/keu258","volume":"53","author":"T Gono","year":"2014","unstructured":"Gono T, Kaneko H, Kawaguchi Y, Hanaoka M, Kataoka S, Kuwana M, Takagi K, Ichida H, Katsumata Y, Ota Y, Kawasumi H, Yamanaka H (2014) Cytokine profiles in polymyositis and dermatomyositis complicated by rapidly progressive or chronic interstitial lung disease. Rheumatology (Oxford) 53(12):2196\u20132203. https:\/\/doi.org\/10.1093\/rheumatology\/keu258","journal-title":"Rheumatology (Oxford)"},{"key":"8822_CR31","doi-asserted-by":"publisher","first-page":"7","DOI":"10.1016\/j.rmed.2018.06.012","volume":"141","author":"T Takada","year":"2018","unstructured":"Takada T, Ohashi K, Hayashi M, Asakawa K, Sakagami T, Kikuchi T, Sato S (2018) Role of IL-15 in interstitial lung diseases in amyopathic dermatomyositis with anti-MDA-5 antibody. Respir Med 141:7\u201313. https:\/\/doi.org\/10.1016\/j.rmed.2018.06.012","journal-title":"Respir Med"},{"issue":"1","key":"8822_CR32","doi-asserted-by":"publisher","first-page":"240","DOI":"10.1186\/s13075-018-1737-2","volume":"20","author":"Y Ishikawa","year":"2018","unstructured":"Ishikawa Y, Iwata S, Hanami K, Nawata A, Zhang M, Yamagata K, Hirata S, Sakata K, Todoroki Y, Nakano K, Nakayamada S, Satoh M, Tanaka Y (2018) Relevance of interferon-gamma in pathogenesis of life-threatening rapidly progressive interstitial lung disease in patients with dermatomyositis. Arthritis Res Ther 20(1):240. https:\/\/doi.org\/10.1186\/s13075-018-1737-2","journal-title":"Arthritis Res Ther"},{"issue":"6","key":"8822_CR33","doi-asserted-by":"publisher","first-page":"1334","DOI":"10.1111\/bjd.17079","volume":"179","author":"M Chen","year":"2018","unstructured":"Chen M, Quan C, Diao L, Xue F, Xue K, Wang B, Li X, Zhu X, Zheng J, Cao H (2018) Measurement of cytokines and chemokines and association with clinical severity of dermatomyositis and clinically amyopathic dermatomyositis. Br J Dermatol 179(6):1334\u20131341. https:\/\/doi.org\/10.1111\/bjd.17079","journal-title":"Br J Dermatol"},{"issue":"9","key":"8822_CR34","doi-asserted-by":"publisher","first-page":"1492","DOI":"10.1093\/rheumatology\/kex188","volume":"56","author":"Y Abe","year":"2017","unstructured":"Abe Y, Matsushita M, Tada K, Yamaji K, Takasaki Y, Tamura N (2017) Clinical characteristics and change in the antibody titres of patients with anti-MDA5 antibody-positive inflammatory myositis. Rheumatology (Oxford) 56(9):1492\u20131497. https:\/\/doi.org\/10.1093\/rheumatology\/kex188","journal-title":"Rheumatology (Oxford)"},{"issue":"8","key":"8822_CR35","doi-asserted-by":"publisher","first-page":"1316","DOI":"10.1002\/acr.21985","volume":"65","author":"Z Chen","year":"2013","unstructured":"Chen Z, Cao M, Nieves Plana M, Liang J, Cai H, Kuwana M, Sun L (2013) Utility of anti-melanoma differentiation-associated gene 5 antibody measurement in identifying patients with dermatomyositis and a high risk for developing rapidly progressive interstitial lung disease: a review of the literature and a meta-analysis. Arthritis Care & Research 65(8):1316\u20131324. https:\/\/doi.org\/10.1002\/acr.21985","journal-title":"Arthritis Care & Research"},{"issue":"9","key":"8822_CR36","doi-asserted-by":"publisher","first-page":"1563","DOI":"10.1093\/rheumatology\/kes102","volume":"51","author":"T Gono","year":"2012","unstructured":"Gono T, Sato S, Kawaguchi Y, Kuwana M, Hanaoka M, Katsumata Y, Takagi K, Baba S, Okamoto Y, Ota Y, Yamanaka H (2012) Anti-MDA5 antibody, ferritin and IL-18 are useful for the evaluation of response to treatment in interstitial lung disease with anti-MDA5 antibody-positive dermatomyositis. Rheumatology 51(9):1563\u20131570. https:\/\/doi.org\/10.1093\/rheumatology\/kes102","journal-title":"Rheumatology"},{"issue":"5","key":"8822_CR37","doi-asserted-by":"publisher","first-page":"1076","DOI":"10.1111\/1756-185x.13268","volume":"21","author":"H So","year":"2018","unstructured":"So H, Ip RWK, Wong VTL, Yip RML (2018) Analysis of anti-melanoma differentiation-associated gene 5 antibody in Hong Kong Chinese patients with idiopathic inflammatory myopathies: diagnostic utility and clinical correlations. International Journal of Rheumatic Diseases 21(5):1076\u20131081. https:\/\/doi.org\/10.1111\/1756-185x.13268","journal-title":"International Journal of Rheumatic Diseases"},{"issue":"10","key":"8822_CR38","doi-asserted-by":"publisher","first-page":"1647","DOI":"10.1007\/s10067-007-0562-9","volume":"26","author":"S Ye","year":"2007","unstructured":"Ye S, Chen X-x, Lu X-y, Wu M-f, Deng Y, Huang W-q, Guo Q, Yang C-d, Gu Y-y, Bao C-d, Chen S-l (2007) Adult clinically amyopathic dermatomyositis with rapid progressive interstitial lung disease: a retrospective cohort study. Clin Rheumatol 26(10):1647\u20131654. https:\/\/doi.org\/10.1007\/s10067-007-0562-9","journal-title":"Clin Rheumatol"},{"issue":"3","key":"8822_CR39","doi-asserted-by":"publisher","first-page":"488","DOI":"10.1002\/art.41105","volume":"72","author":"H Tsuji","year":"2020","unstructured":"Tsuji H, Nakashima R, Hosono Y, Imura Y, Yagita M, Yoshifuji H, Hirata S, Nojima T, Sugiyama E, Hatta K, Taguchi Y, Katayama M, Tanizawa K, Handa T, Uozumi R, Akizuki S, Murakami K, Hashimoto M, Tanaka M, Ohmura K, Mimori T (2020) Multicenter prospective study of the efficacy and safety of combined immunosuppressive therapy with high-dose glucocorticoid, tacrolimus, and cyclophosphamide in interstitial lung diseases accompanied by anti-melanoma differentiation-associated gene 5-positive dermatomyositis. Arthritis Rheumatol 72(3):488\u2013498. https:\/\/doi.org\/10.1002\/art.41105","journal-title":"Arthritis Rheumatol"},{"issue":"1","key":"8822_CR40","doi-asserted-by":"publisher","first-page":"133","DOI":"10.1080\/14397595.2017.1318468","volume":"28","author":"Y Fujiki","year":"2018","unstructured":"Fujiki Y, Kotani T, Isoda K, Ishida T, Shoda T, Yoshida S, Takeuchi T, Makino S (2018) Evaluation of clinical prognostic factors for interstitial pneumonia in anti-MDA5 antibody-positive dermatomyositis patients. Mod Rheumatol 28(1):133\u2013140. https:\/\/doi.org\/10.1080\/14397595.2017.1318468","journal-title":"Mod Rheumatol"},{"issue":"12","key":"8822_CR41","doi-asserted-by":"publisher","first-page":"3443","DOI":"10.1007\/s10067-019-04729-5","volume":"38","author":"K Yamaguchi","year":"2019","unstructured":"Yamaguchi K, Yamaguchi A, Itai M, Kashiwagi C, Takehara K, Aoki S, Sawada Y, Taguchi K, Umetsu K, Oshima K, Uchida M, Takemura M, Hara K, Motegi S-I, Muro Y, Nakasatomi M, Sakairi T, Hiromura K, Kurabayashi M, Maeno T (2019) Clinical features of patients with anti-melanoma differentiation-associated gene-5 antibody-positive dermatomyositis complicated by spontaneous pneumomediastinum. Clin Rheumatol 38(12):3443\u20133450. https:\/\/doi.org\/10.1007\/s10067-019-04729-5","journal-title":"Clin Rheumatol"},{"issue":"6","key":"8822_CR42","doi-asserted-by":"publisher","first-page":"1919","DOI":"10.1007\/s10067-019-04918-2","volume":"39","author":"M Zhou","year":"2020","unstructured":"Zhou M, Ye Y, Yan N, Lian X, Bao C, Guo Q (2020) Noninvasive positive pressure ventilator deteriorates the outcome of pneumomediastinum in anti-MDA5 antibody-positive clinically amyopathic dermatomyositis. Clin Rheumatol 39(6):1919\u20131927. https:\/\/doi.org\/10.1007\/s10067-019-04918-2","journal-title":"Clin Rheumatol"},{"key":"8822_CR43","doi-asserted-by":"publisher","first-page":"91","DOI":"10.1016\/j.rmed.2016.10.019","volume":"121","author":"H Hozumi","year":"2016","unstructured":"Hozumi H, Fujisawa T, Nakashima R, Johkoh T, Sumikawa H, Murakami A, Enomoto N, Inui N, Nakamura Y, Hosono Y, Imura Y, Mimori T, Suda T (2016) Comprehensive assessment of myositis-specific autoantibodies in polymyositis\/dermatomyositis-associated interstitial lung disease. Respir Med 121:91\u201399. https:\/\/doi.org\/10.1016\/j.rmed.2016.10.019","journal-title":"Respir Med"},{"issue":"4","key":"8822_CR44","doi-asserted-by":"publisher","first-page":"707","DOI":"10.1007\/s10067-015-2866-5","volume":"34","author":"J Zou","year":"2015","unstructured":"Zou J, Guo Q, Chi J, Wu H, Bao C (2015) HRCT score and serum ferritin level are factors associated to the 1-year mortality of acute interstitial lung disease in clinically amyopathic dermatomyositis patients. Clin Rheumatol 34(4):707\u2013714. https:\/\/doi.org\/10.1007\/s10067-015-2866-5","journal-title":"Clin Rheumatol"},{"issue":"10","key":"8822_CR45","doi-asserted-by":"publisher","first-page":"2829","DOI":"10.1093\/rheumatology\/keaa034","volume":"59","author":"Y Zuo","year":"2020","unstructured":"Zuo Y, Ye L, Liu M, Li S, Liu W, Chen F, Lu X, Gordon P, Wang G, Shu X (2020) Clinical significance of radiological patterns of HRCT and their association with macrophage activation in dermatomyositis. Rheumatology (Oxford) 59(10):2829\u20132837. https:\/\/doi.org\/10.1093\/rheumatology\/keaa034","journal-title":"Rheumatology (Oxford)"},{"issue":"9","key":"8822_CR46","doi-asserted-by":"publisher","first-page":"1380","DOI":"10.1016\/j.rmed.2011.05.006","volume":"105","author":"K Tanizawa","year":"2011","unstructured":"Tanizawa K, Handa T, Nakashima R, Kubo T, Hosono Y, Watanabe K, Aihara K, Oga T, Chin K, Nagai S, Mimori T, Mishima M (2011) HRCT features of interstitial lung disease in dermatomyositis with anti-CADM-140 antibody. Respir Med 105(9):1380\u20131387. https:\/\/doi.org\/10.1016\/j.rmed.2011.05.006","journal-title":"Respir Med"},{"issue":"16","key":"8822_CR47","doi-asserted-by":"publisher","first-page":"2241","DOI":"10.2169\/internalmedicine.55.5774","volume":"55","author":"H Chino","year":"2016","unstructured":"Chino H, Sekine A, Baba T, Iwasawa T, Okudela K, Takemura T, Itoh H, Sato S, Suzuki Y, Ogura T (2016) Radiological and pathological correlation in anti-MDA5 antibody-positive interstitial lung disease: rapidly progressive perilobular opacities and diffuse alveolar damage. Intern Med 55(16):2241\u20132246. https:\/\/doi.org\/10.2169\/internalmedicine.55.5774","journal-title":"Intern Med"},{"issue":"18","key":"8822_CR48","doi-asserted-by":"publisher","first-page":"2605","DOI":"10.2169\/internalmedicine.2328-18","volume":"58","author":"H Chino","year":"2019","unstructured":"Chino H, Sekine A, Baba T, Kitamura H, Iwasawa T, Okudela K, Takemura T, Itoh H, Sato S, Suzuki Y, Ogura T (2019) Interstitial lung disease with anti-melanoma differentiation-associated protein 5 antibody: rapidly progressive perilobular opacity. Intern Med 58(18):2605\u20132613. https:\/\/doi.org\/10.2169\/internalmedicine.2328-18","journal-title":"Intern Med"},{"issue":"5","key":"8822_CR49","doi-asserted-by":"publisher","first-page":"814","DOI":"10.1080\/14397595.2018.1548918","volume":"29","author":"A Nishioka","year":"2019","unstructured":"Nishioka A, Tsunoda S, Abe T, Yoshikawa T, Takata M, Kitano M, Matsui K, Nakashima R, Hosono Y, Ohmura K, Mimori T, Sano H (2019) Serum neopterin as well as ferritin, soluble interleukin-2 receptor, KL-6 and anti-MDA5 antibody titer provide markers of the response to therapy in patients with interstitial lung disease complicating anti-MDA5 antibody-positive dermatomyositis. Mod Rheumatol 29(5):814\u2013820. https:\/\/doi.org\/10.1080\/14397595.2018.1548918","journal-title":"Mod Rheumatol"},{"issue":"2","key":"8822_CR50","doi-asserted-by":"publisher","first-page":"395","DOI":"10.1111\/bjd.14882","volume":"176","author":"T Matsushita","year":"2017","unstructured":"Matsushita T, Mizumaki K, Kano M, Yagi N, Tennichi M, Takeuchi A, Okamoto Y, Hamaguchi Y, Murakami A, Hasegawa M, Kuwana M, Fujimoto M, Takehara K (2017) Antimelanoma differentiation-associated protein 5 antibody level is a novel tool for monitoring disease activity in rapidly progressive interstitial lung disease with dermatomyositis. Br J Dermatol 176(2):395\u2013402. https:\/\/doi.org\/10.1111\/bjd.14882","journal-title":"Br J Dermatol"},{"issue":"26","key":"8822_CR51","doi-asserted-by":"publisher","first-page":"e11024","DOI":"10.1097\/MD.0000000000011024","volume":"97","author":"Y Endo","year":"2018","unstructured":"Endo Y, Koga T, Ishida M, Fujita Y, Tsuji S, Takatani A, Shimizu T, Sumiyoshi R, Igawa T, Umeda M, Fukui S, Nishino A, Kawashiri SY, Iwamoto N, Ichinose K, Tamai M, Nakamura H, Origuchi T, Kuwana M, Hosono Y, Mimori T, Kawakami A (2018) Recurrence of anti-MDA5 antibody-positive clinically amyopathic dermatomyositis after long-term remission: a case report. Medicine (Baltimore) 97(26):e11024. https:\/\/doi.org\/10.1097\/MD.0000000000011024","journal-title":"Medicine (Baltimore)"},{"issue":"9","key":"8822_CR52","doi-asserted-by":"publisher","first-page":"1713","DOI":"10.1093\/rheumatology\/keq149","volume":"49","author":"T Gono","year":"2010","unstructured":"Gono T, Kawaguchi Y, Satoh T, Kuwana M, Katsumata Y, Takagi K, Masuda I, Tochimoto A, Baba S, Okamoto Y, Ota Y, Yamanaka H (2010) Clinical manifestation and prognostic factor in anti-melanoma differentiation-associated gene 5 antibody-associated interstitial lung disease as a complication of dermatomyositis. Rheumatology (Oxford) 49(9):1713\u20131719. https:\/\/doi.org\/10.1093\/rheumatology\/keq149","journal-title":"Rheumatology (Oxford)"},{"issue":"1","key":"8822_CR53","doi-asserted-by":"publisher","first-page":"113","DOI":"10.1007\/s10067-015-3139-z","volume":"35","author":"Y Xu","year":"2016","unstructured":"Xu Y, Yang CS, Li YJ, Liu XD, Wang JN, Zhao Q, Xiao WG, Yang PT (2016) Predictive factors of rapidly progressive-interstitial lung disease in patients with clinically amyopathic dermatomyositis. Clin Rheumatol 35(1):113\u2013116. https:\/\/doi.org\/10.1007\/s10067-015-3139-z","journal-title":"Clin Rheumatol"},{"issue":"12","key":"8822_CR54","doi-asserted-by":"publisher","first-page":"2114","DOI":"10.1093\/rheumatology\/key188","volume":"57","author":"K Kurasawa","year":"2018","unstructured":"Kurasawa K, Arai S, Namiki Y, Tanaka A, Takamura Y, Owada T, Arima M, Maezawa R (2018) Tofacitinib for refractory interstitial lung diseases in anti-melanoma differentiation-associated 5 gene antibody-positive dermatomyositis. Rheumatology (Oxford) 57(12):2114\u20132119. https:\/\/doi.org\/10.1093\/rheumatology\/key188","journal-title":"Rheumatology (Oxford)"},{"issue":"6","key":"8822_CR55","doi-asserted-by":"publisher","first-page":"462","DOI":"10.1007\/s100670050139","volume":"18","author":"M Ito","year":"1999","unstructured":"Ito M, Kaise S, Suzuki S, Kazuta Y, Sato Y, Miyata M, Nishimaki T, Nakamura N, Kasukawa R (1999) Clinico-laboratory characteristics of patients with dermatomyositis accompanied by rapidly progressive interstitial lung disease. Clin Rheumatol 18(6):462\u2013467. https:\/\/doi.org\/10.1007\/s100670050139","journal-title":"Clin Rheumatol"},{"issue":"Suppl 1","key":"8822_CR56","doi-asserted-by":"publisher","first-page":"141","DOI":"10.4137\/CCRPM.S36748","volume":"9","author":"H Yoshifuji","year":"2015","unstructured":"Yoshifuji H (2015) Biomarkers and autoantibodies of interstitial lung disease with idiopathic inflammatory myopathies. Clin Med Insights Circ Respir Pulm Med 9(Suppl 1):141\u2013146. https:\/\/doi.org\/10.4137\/CCRPM.S36748","journal-title":"Clin Med Insights Circ Respir Pulm Med"},{"issue":"3","key":"8822_CR57","first-page":"203","volume":"18","author":"N Kohno","year":"1988","unstructured":"Kohno N, Akiyama M, Kyoizumi S, Hakoda M, Kobuke K, Yamakido M (1988) Detection of soluble tumor-associated antigens in sera and effusions using novel monoclonal antibodies, KL-3 and KL-6, against lung adenocarcinoma. Jpn J Clin Oncol 18(3):203\u2013216","journal-title":"Jpn J Clin Oncol"},{"issue":"4","key":"8822_CR58","doi-asserted-by":"publisher","first-page":"257","DOI":"10.1136\/ard.59.4.257","volume":"59","author":"S Bandoh","year":"2000","unstructured":"Bandoh S, Fujita J, Ohtsuki Y, Ueda Y, Hojo S, Tokuda M, Dobashi H, Kurata N, Yoshinouchi T, Kohno N, Takahara J (2000) Sequential changes of KL-6 in sera of patients with interstitial pneumonia associated with polymyositis\/dermatomyositis. Ann Rheum Dis 59(4):257\u2013262. https:\/\/doi.org\/10.1136\/ard.59.4.257","journal-title":"Ann Rheum Dis"},{"issue":"8","key":"8822_CR59","doi-asserted-by":"publisher","first-page":"e22978","DOI":"10.1002\/jcla.22978","volume":"33","author":"Y Ye","year":"2019","unstructured":"Ye Y, Fu Q, Wang R, Guo Q, Bao C (2019) Serum KL-6 level is a prognostic marker in patients with anti-MDA5 antibody-positive dermatomyositis associated with interstitial lung disease. J Clin Lab Anal 33(8):e22978. https:\/\/doi.org\/10.1002\/jcla.22978","journal-title":"J Clin Lab Anal"},{"issue":"3","key":"8822_CR60","doi-asserted-by":"publisher","first-page":"511","DOI":"10.1093\/rheumatology\/key341","volume":"58","author":"K Wang","year":"2019","unstructured":"Wang K, Zhao J, Chen Z, Li T, Tan X, Zheng Y, Gu L, Guo L, Sun F, Wang H, Li J, Wang X, Riemekasten G, Ye S (2019) CD4+CXCR4+ T cells as a novel prognostic biomarker in patients with idiopathic inflammatory myopathy-associated interstitial lung disease. Rheumatology (Oxford) 58(3):511\u2013521. https:\/\/doi.org\/10.1093\/rheumatology\/key341","journal-title":"Rheumatology (Oxford)"},{"issue":"11","key":"8822_CR61","first-page":"2389","volume":"28","author":"J Suzuki","year":"2001","unstructured":"Suzuki J, Morimoto S, Amano H, Tokano Y, Takasaki Y, Hashimoto H (2001) Serum levels of interleukin 15 in patients with rheumatic diseases. J Rheumatol 28(11):2389\u20132391","journal-title":"J Rheumatol"},{"issue":"6","key":"8822_CR62","doi-asserted-by":"publisher","first-page":"1055","DOI":"10.1136\/annrheumdis-2011-200495","volume":"71","author":"M Zong","year":"2012","unstructured":"Zong M, Loell I, Lindroos E, Nader GA, Alexanderson H, Hallengren CS, Borg K, Arnardottir S, McInnes IB, Lundberg IE (2012) Effects of immunosuppressive treatment on interleukin-15 and interleukin-15 receptor alpha expression in muscle tissue of patients with polymyositis or dermatomyositis. Ann Rheum Dis 71(6):1055\u20131063. https:\/\/doi.org\/10.1136\/annrheumdis-2011-200495","journal-title":"Ann Rheum Dis"},{"key":"8822_CR63","doi-asserted-by":"publisher","DOI":"10.1111\/joim.13154","author":"T Shimizu","year":"2020","unstructured":"Shimizu T, Koga T, Furukawa K, Horai Y, Fujikawa K, Okada A, Okamoto M, Endo Y, Tsuji S, Takatani A, Umeda M, Fukui S, Sumiyoshi R, Kawashiri SY, Iwamoto N, Igawa T, Ichinose K, Tamai M, Sakamoto N, Nakamura H, Origuchi T, Mukae H, Kuwana M, Kawakami A (2020) IL-15 is a biomarker involved in the development of rapidly progressive interstitial lung disease complicated with polymyositis\/dermatomyositis. J Intern Med. https:\/\/doi.org\/10.1111\/joim.13154","journal-title":"J Intern Med"},{"issue":"4","key":"8822_CR64","doi-asserted-by":"publisher","first-page":"633","DOI":"10.3109\/14397595.2013.844390","volume":"24","author":"M Nara","year":"2014","unstructured":"Nara M, Komatsuda A, Omokawa A, Togashi M, Okuyama S, Sawada K, Wakui H (2014) Serum interleukin 6 levels as a useful prognostic predictor of clinically amyopathic dermatomyositis with rapidly progressive interstitial lung disease. Mod Rheumatol 24(4):633\u2013636. https:\/\/doi.org\/10.3109\/14397595.2013.844390","journal-title":"Mod Rheumatol"},{"issue":"4","key":"8822_CR65","doi-asserted-by":"publisher","first-page":"776","DOI":"10.1016\/j.semarthrit.2020.03.007","volume":"50","author":"F Romero-Bueno","year":"2020","unstructured":"Romero-Bueno F, Diaz Del Campo P, Trallero-Araguas E, Ruiz-Rodriguez JC, Castellvi I, Rodriguez-Nieto MJ, Martinez-Becerra MJ, Sanchez-Pernaute O, Pinal-Fernandez I, Solanich X, Gono T, Gonzalez-Gay MA, Plana MN, Selva-O\u2019Callaghan A, group M, (2020) Recommendations for the treatment of anti-melanoma differentiation-associated gene 5-positive dermatomyositis-associated rapidly progressive interstitial lung disease. Semin Arthritis Rheum 50(4):776\u2013790. https:\/\/doi.org\/10.1016\/j.semarthrit.2020.03.007","journal-title":"Semin Arthritis Rheum"},{"issue":"3","key":"8822_CR66","doi-asserted-by":"publisher","first-page":"291","DOI":"10.1056\/NEJMc1900045","volume":"381","author":"Z Chen","year":"2019","unstructured":"Chen Z, Wang X, Ye S (2019) Tofacitinib in amyopathic dermatomyositis-associated interstitial lung disease. N Engl J Med 381(3):291\u2013293. https:\/\/doi.org\/10.1056\/NEJMc1900045","journal-title":"N Engl J Med"},{"issue":"7","key":"8822_CR67","doi-asserted-by":"publisher","first-page":"1983","DOI":"10.1007\/s10067-018-4122-2","volume":"37","author":"H So","year":"2018","unstructured":"So H, Wong VTL, Lao VWN, Pang HT, Yip RML (2018) Rituximab for refractory rapidly progressive interstitial lung disease related to anti-MDA5 antibody-positive amyopathic dermatomyositis. Clin Rheumatol 37(7):1983\u20131989. https:\/\/doi.org\/10.1007\/s10067-018-4122-2","journal-title":"Clin Rheumatol"},{"issue":"8","key":"8822_CR68","doi-asserted-by":"publisher","first-page":"1591","DOI":"10.1136\/annrheumdis-2014-205278","volume":"73","author":"J Zou","year":"2014","unstructured":"Zou J, Li T, Huang X, Chen S, Guo Q, Bao C (2014) Basiliximab may improve the survival rate of rapidly progressive interstitial pneumonia in patients with clinically amyopathic dermatomyositis with anti-MDA5 antibody. Ann Rheum Dis 73(8):1591\u20131593. https:\/\/doi.org\/10.1136\/annrheumdis-2014-205278","journal-title":"Ann Rheum Dis"},{"issue":"3","key":"8822_CR69","doi-asserted-by":"publisher","first-page":"536","DOI":"10.3109\/14397595.2015.1014140","volume":"27","author":"Y Koichi","year":"2017","unstructured":"Koichi Y, Aya Y, Megumi U, Shunichi K, Masafumi S, Hiroaki M, Masahiko K, Shinsuke K, Manabu U, Kenichiro H, Fumiaki A, Nozomi A, Toshitaka M, Masayoshi Y, Chikako K, Yoshinao M, Tatsuo S, Masahiko K (2017) A case of anti-MDA5-positive rapidly progressive interstitial lung disease in a patient with clinically amyopathic dermatomyositis ameliorated by rituximab, in addition to standard immunosuppressive treatment. Mod Rheumatol 27(3):536\u2013540. https:\/\/doi.org\/10.3109\/14397595.2015.1014140","journal-title":"Mod Rheumatol"},{"issue":"4","key":"8822_CR70","doi-asserted-by":"publisher","first-page":"767","DOI":"10.1093\/rheumatology\/kez357","volume":"59","author":"Y Abe","year":"2020","unstructured":"Abe Y, Kusaoi M, Tada K, Yamaji K, Tamura N (2020) Successful treatment of anti-MDA5 antibody-positive refractory interstitial lung disease with plasma exchange therapy. Rheumatology (Oxford) 59(4):767\u2013771. https:\/\/doi.org\/10.1093\/rheumatology\/kez357","journal-title":"Rheumatology (Oxford)"},{"key":"8822_CR71","doi-asserted-by":"publisher","first-page":"101016","DOI":"10.1016\/j.rmcr.2020.101016","volume":"29","author":"H Kagawa","year":"2020","unstructured":"Kagawa H, Tsujino K, Yamamoto Y, Iwai A, Hara R, Matsuki T, Fukushima K, Oshitani Y, Yoshimura K, Miki M, Miki K, Kitada S, Mori M, Kida H (2020) Acute lung injury after plasma exchange in a patient with anti-MDA5 antibody-positive, rapidly progressive, interstitial lung disease: a case report. Respir Med Case Rep 29:101016. https:\/\/doi.org\/10.1016\/j.rmcr.2020.101016","journal-title":"Respir Med Case Rep"},{"issue":"1","key":"8822_CR72","doi-asserted-by":"publisher","first-page":"134","DOI":"10.1186\/s12890-017-0479-2","volume":"17","author":"H Okabayashi","year":"2017","unstructured":"Okabayashi H, Ichiyasu H, Hirooka S, Akaike K, Kojima K, Jodai T, Sakamoto Y, Ideguchi H, Hamada S, Yoshida C, Hirosako S, Okamoto S, Kohrogi H (2017) Clinical effects of direct hemoperfusion using a polymyxin B-immobilized fiber column in clinically amyopathic dermatomyositis-associated rapidly progressive interstitial pneumonias. BMC Pulm Med 17(1):134. https:\/\/doi.org\/10.1186\/s12890-017-0479-2","journal-title":"BMC Pulm Med"},{"key":"8822_CR73","doi-asserted-by":"publisher","first-page":"33226","DOI":"10.1038\/srep33226","volume":"6","author":"T Li","year":"2016","unstructured":"Li T, Guo L, Chen Z, Gu L, Sun F, Tan X, Chen S, Wang X, Ye S (2016) Pirfenidone in patients with rapidly progressive interstitial lung disease associated with clinically amyopathic dermatomyositis. Sci Rep 6:33226. https:\/\/doi.org\/10.1038\/srep33226","journal-title":"Sci Rep"},{"issue":"4","key":"8822_CR74","doi-asserted-by":"publisher","first-page":"581","DOI":"10.3899\/jrheum.171047","volume":"45","author":"V Leclair","year":"2018","unstructured":"Leclair V, Labirua-Iturburu A, Lundberg IE (2018) Successful lung transplantation in a case of rapidly progressive interstitial lung disease associated with antimelanoma differentiation-associated gene 5 antibodies. J Rheumatol 45(4):581\u2013583. https:\/\/doi.org\/10.3899\/jrheum.171047","journal-title":"J Rheumatol"},{"issue":"8","key":"8822_CR75","doi-asserted-by":"publisher","first-page":"2161","DOI":"10.1093\/rheumatology\/keaa032","volume":"59","author":"K Huang","year":"2020","unstructured":"Huang K, Levy RD, Avina-Zubieta JA (2020) Successful lung transplant in rapid progressive interstitial lung disease associated with anti-melanoma differentiation associated gene 5. Rheumatology (Oxford) 59(8):2161\u20132163. https:\/\/doi.org\/10.1093\/rheumatology\/keaa032","journal-title":"Rheumatology (Oxford)"}],"container-title":["Clinical Reviews in Allergy &amp; Immunology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1007\/s12016-020-08822-5.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/link.springer.com\/article\/10.1007\/s12016-020-08822-5\/fulltext.html","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1007\/s12016-020-08822-5.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2022,7,29]],"date-time":"2022-07-29T07:26:18Z","timestamp":1659079578000},"score":1,"resource":{"primary":{"URL":"https:\/\/link.springer.com\/10.1007\/s12016-020-08822-5"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2021,1,6]]},"references-count":75,"journal-issue":{"issue":"2","published-print":{"date-parts":[[2021,4]]}},"alternative-id":["8822"],"URL":"https:\/\/doi.org\/10.1007\/s12016-020-08822-5","relation":{},"ISSN":["1080-0549","1559-0267"],"issn-type":[{"value":"1080-0549","type":"print"},{"value":"1559-0267","type":"electronic"}],"subject":[],"published":{"date-parts":[[2021,1,6]]},"assertion":[{"value":"2 November 2020","order":1,"name":"accepted","label":"Accepted","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"6 January 2021","order":2,"name":"first_online","label":"First Online","group":{"name":"ArticleHistory","label":"Article History"}},{"order":1,"name":"Ethics","group":{"name":"EthicsHeading","label":"Compliance with Ethical Standards"}},{"value":"The authors declare that they have no conflict of interest.","order":2,"name":"Ethics","group":{"name":"EthicsHeading","label":"Conflict of Interest"}},{"value":"This content has been made available to all.","name":"free","label":"Free to read"}]}}