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Affected children may experience life-threatening symptoms, mainly during fever. The percentage of\n                    <jats:italic>SCN5A<\/jats:italic>\n                    variant carriers in children is higher than in adults. Current diagnostic and follow-up policies for children with (a\u00a0family history of) BrS vary between centres. Here, we present a\u00a0consensus statement based on the current literature and expert opinions to standardise the approach for all children with BrS and those from BrS families in the Netherlands. In summary, BrS is diagnosed in patients with a\u00a0spontaneous type\u00a01\u00a0electrocardiogram (ECG) pattern or with a\u00a0Shanghai score \u2265\u202f3.5 including \u2265\u202f1\u00a0ECG finding. A\u00a0sodium channel-blocking drug challenge test should only be performed after puberty with a\u00a0few exceptions. A\u00a0fever ECG is indicated in children with suspected BrS, in children with a\u00a0first-degree family member with definite or possible BrS according to the Shanghai criteria with a\u00a0\n                    <jats:italic>SCN5A<\/jats:italic>\n                    variant and in paediatric\n                    <jats:italic>SCN5A<\/jats:italic>\n                    variant carriers. In-hospital rhythm monitoring during fever is indicated in patients with an existing type\u00a01\u00a0ECG pattern and in those who develop such a\u00a0pattern. Genetic testing should be restricted to\n                    <jats:italic>SCN5A<\/jats:italic>\n                    . Children with BrS and children who carry an\n                    <jats:italic>SCN5A<\/jats:italic>\n                    variant should avoid medication listed at\n                    <jats:ext-link xmlns:xlink=\"http:\/\/www.w3.org\/1999\/xlink\" ext-link-type=\"uri\" xlink:href=\"http:\/\/www.brugadadrugs.org\">www.brugadadrugs.org<\/jats:ext-link>\n                    and fever should be suppressed. Ventricular arrhythmias or electrical storms should be treated with isoproterenol infusion.\n                  <\/jats:p>","DOI":"10.1007\/s12471-022-01723-6","type":"journal-article","created":{"date-parts":[[2022,10,12]],"date-time":"2022-10-12T02:02:45Z","timestamp":1665540165000},"page":"133-137","update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":15,"title":["Screening, diagnosis and follow-up of Brugada syndrome in children: a\u00a0Dutch expert consensus statement"],"prefix":"10.1007","volume":"31","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-8942-164X","authenticated-orcid":false,"given":"P. J.","family":"Peltenburg","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Y. M.","family":"Hoedemaekers","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"S. A. 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