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Lupus podocytopathy with glomerular morphology of MCD or MsP usually presents with typical nephrotic syndrome and sensitive to glucocorticoid treatment, but the relapse rate could reach up to 90% on maintenance treatment with glucocorticoid alone. Glucocorticoid plus other immunosuppressive agents could significantly decrease the relapse rate. Lupus podocytopathy with FSGS presents with a higher rate of acute kidney injury and less sensitivity to glucocorticoid treatment. The long-term outcomes of lupus podocytopathy are optimistic, but pathological transition could occur after renal relapses. The unique clinical and morphological features of lupus podocytopathy indicate that this special SLE-associated glomerulopathy should be included in the upcoming revised pathological classification of lupus nephritis.<\/jats:p>","DOI":"10.1007\/s40620-017-0463-1","type":"journal-article","created":{"date-parts":[[2017,12,21]],"date-time":"2017-12-21T22:08:45Z","timestamp":1513894125000},"page":"629-634","update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":38,"title":["Lupus podocytopathy: a distinct entity of lupus nephritis"],"prefix":"10.1093","volume":"31","author":[{"given":"Duqun","family":"Chen","sequence":"first","affiliation":[{"name":"National Clinical Research Center of Kidney Diseases, Jinling Hospital, Nanjing University School of Medicine, 305 East Zhongshan Road, 210016, Nanjing, Jiangsu, China 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