{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,2,19]],"date-time":"2026-02-19T23:19:57Z","timestamp":1771543197968,"version":"3.50.1"},"reference-count":228,"publisher":"Wiley","issue":"4","license":[{"start":{"date-parts":[[2015,2,17]],"date-time":"2015-02-17T00:00:00Z","timestamp":1424131200000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"funder":[{"DOI":"10.13039\/501100000268","name":"Biotechnology and Biological Sciences Research Council","doi-asserted-by":"publisher","award":["BB\/K006231\/1"],"award-info":[{"award-number":["BB\/K006231\/1"]}],"id":[{"id":"10.13039\/501100000268","id-type":"DOI","asserted-by":"publisher"}]}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["J of Inher Metab Disea"],"published-print":{"date-parts":[[2015,7]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>Peroxisomes and mitochondria are ubiquitous, highly dynamic organelles with an oxidative type of metabolism in eukaryotic cells. Over the years, substantial evidence has been provided that peroxisomes and mitochondria exhibit a close functional interplay which impacts on human health and development. The so\u2010called \u201cperoxisome\u2010mitochondria connection\u201d includes metabolic cooperation in the degradation of fatty acids, a redox\u2010sensitive relationship, an overlap in key components of the membrane fission machineries and cooperation in anti\u2010viral signalling and defence. Furthermore, combined peroxisome\u2010mitochondria disorders with defects in organelle division have been revealed. In this review, we present the latest progress in the emerging field of peroxisomal and mitochondrial interplay in mammals with a particular emphasis on cooperative fatty acid \u03b2\u2010oxidation, redox interplay, organelle dynamics, cooperation in anti\u2010viral signalling and the resulting implications for disease.<\/jats:p>","DOI":"10.1007\/s10545-015-9819-7","type":"journal-article","created":{"date-parts":[[2015,2,17]],"date-time":"2015-02-17T09:53:54Z","timestamp":1424166834000},"page":"681-702","update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":181,"title":["Peroxisome\u2010mitochondria interplay and disease"],"prefix":"10.1002","volume":"38","author":[{"given":"Michael","family":"Schrader","sequence":"first","affiliation":[{"name":"College of Life and Environmental Sciences, Biosciences University of Exeter Geoffrey Pope Building, Stocker Road Exeter EX4 4QD UK"},{"name":"Centre for Cell Biology &amp; Department of Biology University of Aveiro Aveiro 3810\u2010193 Portugal"}]},{"given":"Joseph","family":"Costello","sequence":"additional","affiliation":[{"name":"College of Life and Environmental Sciences, Biosciences University of Exeter Geoffrey Pope Building, Stocker Road Exeter EX4 4QD UK"}]},{"given":"Luis F.","family":"Godinho","sequence":"additional","affiliation":[{"name":"Centre for Cell Biology &amp; Department of Biology University of Aveiro Aveiro 3810\u2010193 Portugal"}]},{"given":"Markus","family":"Islinger","sequence":"additional","affiliation":[{"name":"Neuroanatomy, Center for Biomedicine and Medical Technology Mannheim University of Heidelberg Mannheim 68167 Germany"}]}],"member":"311","published-online":{"date-parts":[[2015,2,17]]},"reference":[{"key":"e_1_2_10_2_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.bbadis.2011.12.011"},{"key":"e_1_2_10_3_1","doi-asserted-by":"publisher","DOI":"10.1089\/ars.2009.2996"},{"key":"e_1_2_10_4_1","doi-asserted-by":"publisher","DOI":"10.1111\/tra.12129"},{"key":"e_1_2_10_5_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.neuro.2011.10.007"},{"key":"e_1_2_10_6_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.neuroscience.2012.03.058"},{"key":"e_1_2_10_7_1","doi-asserted-by":"crossref","unstructured":"BaarineMBeesonCSinghASinghIABCD1 deletion\u2010induced mitochondrial dysfunction is corrected by SAHA: implication for adrenoleukodystrophyJ Neurochem2014.","DOI":"10.1111\/jnc.12992"},{"key":"e_1_2_10_8_1","doi-asserted-by":"publisher","DOI":"10.1073\/pnas.1009176107"},{"key":"e_1_2_10_9_1","doi-asserted-by":"publisher","DOI":"10.1074\/jbc.274.37.26217"},{"key":"e_1_2_10_10_1","doi-asserted-by":"crossref","unstructured":"BakerMJ TatsutaT LangerT(2011)Quality control of mitochondrial proteostasis.Cold Spring Harb Perspect Biol 3. doi: 10.1101\/cshperspect.a007559","DOI":"10.1101\/cshperspect.a007559"},{"key":"e_1_2_10_11_1","doi-asserted-by":"publisher","DOI":"10.1016\/S1097-2765(00)80209-9"},{"key":"e_1_2_10_12_1","doi-asserted-by":"publisher","DOI":"10.1046\/j.1432-1033.2003.03947.x"},{"key":"e_1_2_10_13_1","doi-asserted-by":"publisher","DOI":"10.1016\/S0002-9440(10)62534-5"},{"key":"e_1_2_10_14_1","doi-asserted-by":"publisher","DOI":"10.1371\/journal.pone.0029291"},{"key":"e_1_2_10_15_1","doi-asserted-by":"publisher","DOI":"10.1002\/ana.101"},{"key":"e_1_2_10_16_1","doi-asserted-by":"crossref","unstructured":"BolteKRensingSAMaierUGThe evolution of eukaryotic cells from the perspective of peroxisomes: phylogenetic analyses of peroxisomal beta\u2010oxidation enzymes support mitochondria\u2010first models of eukaryotic cell evolutionBioEssays2014.","DOI":"10.1002\/bies.201400151"},{"key":"e_1_2_10_17_1","doi-asserted-by":"publisher","DOI":"10.1371\/journal.pone.0086196"},{"key":"e_1_2_10_18_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.yexcr.2010.07.020"},{"key":"e_1_2_10_19_1","doi-asserted-by":"publisher","DOI":"10.1111\/j.1600-0854.2012.01356.x"},{"key":"e_1_2_10_20_1","doi-asserted-by":"publisher","DOI":"10.1371\/journal.pone.0053424"},{"key":"e_1_2_10_21_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.mam.2004.06.004"},{"key":"e_1_2_10_22_1","doi-asserted-by":"publisher","DOI":"10.1016\/0968-0004(83)90077-4"},{"key":"e_1_2_10_23_1","doi-asserted-by":"publisher","DOI":"10.1016\/0167-4781(86)90044-8"},{"key":"e_1_2_10_24_1","doi-asserted-by":"publisher","DOI":"10.1186\/1742-2094-9-61"},{"key":"e_1_2_10_25_1","doi-asserted-by":"publisher","DOI":"10.1080\/713803732"},{"key":"e_1_2_10_26_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.cardiores.2004.08.007"},{"key":"e_1_2_10_27_1","doi-asserted-by":"publisher","DOI":"10.1042\/bj2240709"},{"key":"e_1_2_10_28_1","doi-asserted-by":"publisher","DOI":"10.1038\/nbt1175"},{"key":"e_1_2_10_29_1","doi-asserted-by":"publisher","DOI":"10.1038\/onc.2008.21"},{"key":"e_1_2_10_30_1","doi-asserted-by":"publisher","DOI":"10.1007\/s10545-008-1018-3"},{"key":"e_1_2_10_31_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.bbamcr.2014.10.005"},{"key":"e_1_2_10_32_1","doi-asserted-by":"publisher","DOI":"10.1074\/jbc.M110.142430"},{"key":"e_1_2_10_33_1","doi-asserted-by":"publisher","DOI":"10.1093\/hmg\/ddp326"},{"key":"e_1_2_10_34_1","doi-asserted-by":"publisher","DOI":"10.1007\/s13238-012-2063-0"},{"key":"e_1_2_10_35_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.bbrc.2003.11.127"},{"key":"e_1_2_10_36_1","doi-asserted-by":"publisher","DOI":"10.1074\/jbc.M000536200"},{"key":"e_1_2_10_37_1","doi-asserted-by":"publisher","DOI":"10.1006\/bbrc.2000.3739"},{"key":"e_1_2_10_38_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.expneurol.2013.12.012"},{"key":"e_1_2_10_39_1","doi-asserted-by":"publisher","DOI":"10.1074\/jbc.273.45.29577"},{"key":"e_1_2_10_40_1","doi-asserted-by":"publisher","DOI":"10.1038\/nrm2256"},{"key":"e_1_2_10_41_1","doi-asserted-by":"publisher","DOI":"10.1083\/jcb.27.1.25"},{"key":"e_1_2_10_42_1","doi-asserted-by":"publisher","DOI":"10.1073\/pnas.1218034110"},{"key":"e_1_2_10_43_1","doi-asserted-by":"publisher","DOI":"10.1007\/s00418-009-0561-9"},{"key":"e_1_2_10_44_1","doi-asserted-by":"publisher","DOI":"10.1242\/jcs.062109"},{"key":"e_1_2_10_45_1","doi-asserted-by":"publisher","DOI":"10.1038\/nm.2421"},{"key":"e_1_2_10_46_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.celrep.2013.08.032"},{"key":"e_1_2_10_47_1","doi-asserted-by":"publisher","DOI":"10.1002\/hep.20628"},{"key":"e_1_2_10_48_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.cell.2010.04.018"},{"key":"e_1_2_10_49_1","doi-asserted-by":"publisher","DOI":"10.1007\/s10545-008-0844-7"},{"key":"e_1_2_10_50_1","doi-asserted-by":"publisher","DOI":"10.1093\/hmg\/ddi303"},{"key":"e_1_2_10_51_1","doi-asserted-by":"publisher","DOI":"10.1136\/jmedgenet-2012-100778"},{"issue":"1","key":"e_1_2_10_52_1","article-title":"PEX11\u03b2 deficiency: a novel human peroxisome biogenesis disorder affecting peroxisome division","volume":"37","author":"Ebberink M","year":"2014","journal-title":"J Inherit Metab Dis"},{"key":"e_1_2_10_53_1","doi-asserted-by":"publisher","DOI":"10.1016\/0014-4800(80)90048-9"},{"key":"e_1_2_10_54_1","doi-asserted-by":"publisher","DOI":"10.1111\/1567-1364.12196"},{"key":"e_1_2_10_55_1","doi-asserted-by":"publisher","DOI":"10.2337\/db09-1401"},{"key":"e_1_2_10_56_1","doi-asserted-by":"publisher","DOI":"10.1667\/RR1424.1"},{"key":"e_1_2_10_57_1","doi-asserted-by":"publisher","DOI":"10.1152\/ajpendo.00226.2010"},{"key":"e_1_2_10_58_1","doi-asserted-by":"publisher","DOI":"10.1016\/0003-9861(83)90509-X"},{"key":"e_1_2_10_59_1","doi-asserted-by":"publisher","DOI":"10.1002\/humu.20535"},{"key":"e_1_2_10_60_1","doi-asserted-by":"crossref","unstructured":"FerdinandusseS Jimenez\u2010SanchezG KosterJ et al (2014)A novel bile acid biosynthesis defect due to a deficiency of peroxisomal ABCD3.Hum Mol Genet.","DOI":"10.1093\/hmg\/ddu448"},{"key":"e_1_2_10_61_1","doi-asserted-by":"publisher","DOI":"10.1093\/hmg\/ddi384"},{"key":"e_1_2_10_62_1","doi-asserted-by":"publisher","DOI":"10.1042\/bj1960705"},{"key":"e_1_2_10_63_1","doi-asserted-by":"publisher","DOI":"10.1093\/hmg\/ddn085"},{"key":"e_1_2_10_64_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.biochi.2013.09.012"},{"key":"e_1_2_10_65_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.bbadis.2011.12.001"},{"key":"e_1_2_10_66_1","doi-asserted-by":"publisher","DOI":"10.1007\/978-94-007-6889-5_3"},{"key":"e_1_2_10_67_1","doi-asserted-by":"publisher","DOI":"10.1038\/nature11051"},{"key":"e_1_2_10_68_1","doi-asserted-by":"publisher","DOI":"10.1126\/science.1207385"},{"key":"e_1_2_10_69_1","doi-asserted-by":"publisher","DOI":"10.1038\/emboj.2013.74"},{"key":"e_1_2_10_70_1","doi-asserted-by":"publisher","DOI":"10.1007\/s00018-014-1640-1"},{"key":"e_1_2_10_71_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.gene.2010.06.004"},{"key":"e_1_2_10_72_1","doi-asserted-by":"publisher","DOI":"10.1089\/ars.2010.3877"},{"key":"e_1_2_10_73_1","doi-asserted-by":"publisher","DOI":"10.1091\/mbc.E07-12-1287"},{"key":"e_1_2_10_74_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.bbadis.2012.03.013"},{"key":"e_1_2_10_75_1","doi-asserted-by":"publisher","DOI":"10.1074\/jbc.R113.464131"},{"key":"e_1_2_10_76_1","doi-asserted-by":"publisher","DOI":"10.1126\/science.182.4107.62"},{"key":"e_1_2_10_77_1","doi-asserted-by":"publisher","DOI":"10.1186\/1742-2094-9-63"},{"key":"e_1_2_10_78_1","doi-asserted-by":"publisher","DOI":"10.1371\/journal.pone.0057395"},{"key":"e_1_2_10_79_1","doi-asserted-by":"publisher","DOI":"10.1007\/s00705-014-2105-4"},{"key":"e_1_2_10_80_1","doi-asserted-by":"publisher","DOI":"10.1210\/er.2006-0037"},{"key":"e_1_2_10_81_1","doi-asserted-by":"publisher","DOI":"10.1074\/jbc.274.27.19228"},{"key":"e_1_2_10_82_1","doi-asserted-by":"publisher","DOI":"10.1074\/jbc.M910350199"},{"key":"e_1_2_10_83_1","doi-asserted-by":"publisher","DOI":"10.1086\/519219"},{"key":"e_1_2_10_84_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.ymgme.2010.12.005"},{"key":"e_1_2_10_85_1","doi-asserted-by":"publisher","DOI":"10.1093\/hmg\/ddn066"},{"key":"e_1_2_10_86_1","doi-asserted-by":"publisher","DOI":"10.1038\/208856a0"},{"key":"e_1_2_10_87_1","doi-asserted-by":"publisher","DOI":"10.1007\/BF00222413"},{"key":"e_1_2_10_88_1","doi-asserted-by":"publisher","DOI":"10.1073\/pnas.1110133108"},{"key":"e_1_2_10_89_1","doi-asserted-by":"publisher","DOI":"10.1007\/s10545-010-9061-2"},{"key":"e_1_2_10_90_1","doi-asserted-by":"publisher","DOI":"10.1194\/jlr.M024463"},{"key":"e_1_2_10_91_1","doi-asserted-by":"publisher","DOI":"10.1038\/embor.2013.56"},{"key":"e_1_2_10_92_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.biochi.2013.12.018"},{"key":"e_1_2_10_93_1","doi-asserted-by":"publisher","DOI":"10.1111\/j.1600-0854.2009.00970.x"},{"key":"e_1_2_10_94_1","doi-asserted-by":"publisher","DOI":"10.1038\/ncb1907"},{"key":"e_1_2_10_95_1","doi-asserted-by":"publisher","DOI":"10.1074\/jbc.M610910200"},{"key":"e_1_2_10_96_1","doi-asserted-by":"publisher","DOI":"10.1021\/pr9004663"},{"key":"e_1_2_10_97_1","doi-asserted-by":"publisher","DOI":"10.1007\/s00418-012-0941-4"},{"key":"e_1_2_10_98_1","doi-asserted-by":"publisher","DOI":"10.1038\/347645a0"},{"key":"e_1_2_10_99_1","doi-asserted-by":"publisher","DOI":"10.1242\/bio.20135298"},{"key":"e_1_2_10_100_1","doi-asserted-by":"publisher","DOI":"10.1091\/mbc.E10-11-0919"},{"key":"e_1_2_10_101_1","doi-asserted-by":"publisher","DOI":"10.1371\/journal.pone.0088838"},{"key":"e_1_2_10_102_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.cell.2012.11.011"},{"key":"e_1_2_10_103_1","doi-asserted-by":"publisher","DOI":"10.1002\/ajmg.1320160409"},{"key":"e_1_2_10_104_1","doi-asserted-by":"publisher","DOI":"10.1172\/JCI6223"},{"key":"e_1_2_10_105_1","doi-asserted-by":"publisher","DOI":"10.1128\/EC.00231-06"},{"key":"e_1_2_10_106_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.yexcr.2007.02.028"},{"key":"e_1_2_10_107_1","doi-asserted-by":"publisher","DOI":"10.1242\/jcs.102178"},{"key":"e_1_2_10_108_1","doi-asserted-by":"publisher","DOI":"10.1074\/jbc.M211761200"},{"key":"e_1_2_10_109_1","doi-asserted-by":"publisher","DOI":"10.1242\/jcs.01268"},{"key":"e_1_2_10_110_1","doi-asserted-by":"publisher","DOI":"10.1111\/j.1600-0854.2007.00633.x"},{"key":"e_1_2_10_111_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.taap.2008.06.004"},{"key":"e_1_2_10_112_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.spen.2008.05.008"},{"key":"e_1_2_10_113_1","doi-asserted-by":"publisher","DOI":"10.1016\/0005-2760(85)90041-4"},{"key":"e_1_2_10_114_1","doi-asserted-by":"publisher","DOI":"10.1126\/science.1228360"},{"key":"e_1_2_10_115_1","doi-asserted-by":"publisher","DOI":"10.1128\/EC.00129-12"},{"key":"e_1_2_10_116_1","doi-asserted-by":"publisher","DOI":"10.1128\/EC.00128-12"},{"key":"e_1_2_10_117_1","doi-asserted-by":"publisher","DOI":"10.1128\/JVI.01825-10"},{"key":"e_1_2_10_118_1","doi-asserted-by":"publisher","DOI":"10.1093\/oxfordjournals.jbchem.a123836"},{"key":"e_1_2_10_119_1","doi-asserted-by":"publisher","DOI":"10.1016\/S0021-9258(17)34897-4"},{"key":"e_1_2_10_120_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.mib.2011.07.009"},{"key":"e_1_2_10_121_1","doi-asserted-by":"publisher","DOI":"10.1073\/pnas.73.6.2043"},{"key":"e_1_2_10_122_1","doi-asserted-by":"publisher","DOI":"10.1021\/bi00468a027"},{"key":"e_1_2_10_123_1","doi-asserted-by":"publisher","DOI":"10.1091\/mbc.E02-06-0322"},{"key":"e_1_2_10_124_1","doi-asserted-by":"publisher","DOI":"10.1074\/jbc.M102036200"},{"key":"e_1_2_10_125_1","doi-asserted-by":"publisher","DOI":"10.1016\/S0003-9861(02)00247-3"},{"key":"e_1_2_10_126_1","doi-asserted-by":"publisher","DOI":"10.1074\/jbc.M212031200"},{"key":"e_1_2_10_127_1","doi-asserted-by":"publisher","DOI":"10.1128\/MCB.22.23.8226-8240.2002"},{"key":"e_1_2_10_128_1","doi-asserted-by":"publisher","DOI":"10.1128\/MCB.22.12.4358-4365.2002"},{"key":"e_1_2_10_129_1","doi-asserted-by":"publisher","DOI":"10.1371\/journal.pone.0006673"},{"key":"e_1_2_10_130_1","doi-asserted-by":"publisher","DOI":"10.1073\/pnas.1203405109"},{"key":"e_1_2_10_131_1","doi-asserted-by":"publisher","DOI":"10.1038\/ncb2791"},{"key":"e_1_2_10_132_1","doi-asserted-by":"publisher","DOI":"10.1093\/hmg\/ddt186"},{"key":"e_1_2_10_133_1","doi-asserted-by":"publisher","DOI":"10.1073\/pnas.94.17.9366"},{"key":"e_1_2_10_134_1","doi-asserted-by":"publisher","DOI":"10.1093\/abbs\/gmr048"},{"key":"e_1_2_10_135_1","doi-asserted-by":"publisher","DOI":"10.1111\/j.1365-2958.2004.04340.x"},{"key":"e_1_2_10_136_1","doi-asserted-by":"publisher","DOI":"10.1007\/s00018-003-3216-3"},{"key":"e_1_2_10_137_1","doi-asserted-by":"publisher","DOI":"10.1016\/S0021-9258(17)30051-0"},{"key":"e_1_2_10_138_1","doi-asserted-by":"publisher","DOI":"10.1016\/S0021-9258(19)43946-X"},{"key":"e_1_2_10_139_1","doi-asserted-by":"publisher","DOI":"10.1242\/dmm.007419"},{"key":"e_1_2_10_140_1","doi-asserted-by":"publisher","DOI":"10.1128\/MCB.23.2.744-753.2003"},{"key":"e_1_2_10_141_1","doi-asserted-by":"publisher","DOI":"10.1038\/nri2634"},{"key":"e_1_2_10_142_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.bbrc.2013.09.137"},{"key":"e_1_2_10_143_1","doi-asserted-by":"publisher","DOI":"10.2174\/156802612799436669"},{"key":"e_1_2_10_144_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.cell.2005.04.011"},{"key":"e_1_2_10_145_1","doi-asserted-by":"publisher","DOI":"10.1093\/bioinformatics\/19.1.10"},{"key":"e_1_2_10_146_1","doi-asserted-by":"publisher","DOI":"10.1128\/jvi.76.5.2543-2547.2002"},{"key":"e_1_2_10_147_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.bbadis.2012.02.009"},{"key":"e_1_2_10_148_1","doi-asserted-by":"publisher","DOI":"10.1042\/BJ20081386"},{"key":"e_1_2_10_149_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.cub.2007.12.038"},{"key":"e_1_2_10_150_1","doi-asserted-by":"publisher","DOI":"10.1083\/jcb.200507087"},{"key":"e_1_2_10_151_1","doi-asserted-by":"publisher","DOI":"10.1385\/NMM:8:1-2:217"},{"key":"e_1_2_10_152_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.nbd.2009.09.011"},{"key":"e_1_2_10_153_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.biochi.2013.07.026"},{"key":"e_1_2_10_154_1","doi-asserted-by":"publisher","DOI":"10.1007\/978-94-007-6889-5_4"},{"key":"e_1_2_10_155_1","doi-asserted-by":"publisher","DOI":"10.1038\/ni.2915"},{"key":"e_1_2_10_156_1","doi-asserted-by":"publisher","DOI":"10.1093\/hmg\/ddi125"},{"key":"e_1_2_10_157_1","doi-asserted-by":"publisher","DOI":"10.1242\/jcs.111211"},{"key":"e_1_2_10_158_1","doi-asserted-by":"publisher","DOI":"10.1038\/emboj.2010.299"},{"key":"e_1_2_10_159_1","doi-asserted-by":"publisher","DOI":"10.1016\/0014-5793(79)80975-8"},{"key":"e_1_2_10_160_1","doi-asserted-by":"publisher","DOI":"10.1083\/jcb.201007152"},{"key":"e_1_2_10_161_1","doi-asserted-by":"publisher","DOI":"10.1016\/S0368-1319(63)80059-9"},{"key":"e_1_2_10_162_1","doi-asserted-by":"publisher","DOI":"10.1074\/jbc.M113.479873"},{"key":"e_1_2_10_163_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.bbamcr.2014.11.017"},{"key":"e_1_2_10_164_1","doi-asserted-by":"publisher","DOI":"10.1097\/01.jnen.0000190064.28559.a4"},{"key":"e_1_2_10_165_1","doi-asserted-by":"publisher","DOI":"10.1038\/sj.ijo.0802905"},{"key":"e_1_2_10_166_1","first-page":"e002","article-title":"PPARalpha: energy combustion, hypolipidemia, inflammation and cancer","volume":"16","author":"Pyper SR","year":"2010","journal-title":"Nucl Recept Signal"},{"key":"e_1_2_10_167_1","doi-asserted-by":"publisher","DOI":"10.1146\/annurev.nutr.21.1.193"},{"key":"e_1_2_10_168_1","doi-asserted-by":"publisher","DOI":"10.1146\/annurev.physiol.64.082201.154705"},{"key":"e_1_2_10_169_1","doi-asserted-by":"publisher","DOI":"10.1186\/gb-2011-12-8-r75"},{"key":"e_1_2_10_170_1","doi-asserted-by":"publisher","DOI":"10.3748\/wjg.v20.i10.2624"},{"key":"e_1_2_10_171_1","doi-asserted-by":"publisher","DOI":"10.1146\/annurev.nutr.28.061807.155434"},{"key":"e_1_2_10_172_1","doi-asserted-by":"publisher","DOI":"10.1186\/1476-4598-13-224"},{"key":"e_1_2_10_173_1","doi-asserted-by":"crossref","unstructured":"SalpietroV PhadkeR SaggarA et al (2014)Zellweger syndrome and secondary mitochondrial myopathy.Eur J Pediatr.","DOI":"10.1007\/s00431-014-2431-2"},{"key":"e_1_2_10_174_1","doi-asserted-by":"publisher","DOI":"10.1023\/A:1005556207210"},{"key":"e_1_2_10_175_1","doi-asserted-by":"publisher","DOI":"10.1016\/S0074-7696(06)55005-3"},{"key":"e_1_2_10_176_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.bbamcr.2006.09.006"},{"key":"e_1_2_10_177_1","doi-asserted-by":"publisher","DOI":"10.1002\/bies.20659"},{"key":"e_1_2_10_178_1","doi-asserted-by":"publisher","DOI":"10.1074\/jbc.273.45.29607"},{"key":"e_1_2_10_179_1","doi-asserted-by":"publisher","DOI":"10.1242\/jcs.113.20.3663"},{"key":"e_1_2_10_180_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.bbadis.2011.12.014"},{"key":"e_1_2_10_181_1","doi-asserted-by":"publisher","DOI":"10.1007\/978-94-007-6889-5_1"},{"key":"e_1_2_10_182_1","doi-asserted-by":"publisher","DOI":"10.1126\/science.1106653"},{"key":"e_1_2_10_183_1","doi-asserted-by":"publisher","DOI":"10.1194\/jlr.M800535-JLR200"},{"key":"e_1_2_10_184_1","doi-asserted-by":"publisher","DOI":"10.1136\/jmedgenet-2012-100836"},{"key":"e_1_2_10_185_1","doi-asserted-by":"publisher","DOI":"10.1093\/nar\/gkp566"},{"key":"e_1_2_10_186_1","doi-asserted-by":"publisher","DOI":"10.1111\/j.1365-313X.2009.03863.x"},{"key":"e_1_2_10_187_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.bbrc.2014.01.126"},{"key":"e_1_2_10_188_1","doi-asserted-by":"publisher","DOI":"10.1073\/pnas.81.13.4203"},{"key":"e_1_2_10_189_1","doi-asserted-by":"publisher","DOI":"10.1002\/bies.201000097"},{"key":"e_1_2_10_190_1","doi-asserted-by":"publisher","DOI":"10.1002\/bies.201400033"},{"key":"e_1_2_10_191_1","doi-asserted-by":"publisher","DOI":"10.1007\/s10545-009-1125-9"},{"key":"e_1_2_10_192_1","doi-asserted-by":"publisher","DOI":"10.15252\/embj.201488104"},{"key":"e_1_2_10_193_1","doi-asserted-by":"publisher","DOI":"10.1254\/jjp.84.113"},{"key":"e_1_2_10_194_1","doi-asserted-by":"publisher","DOI":"10.1083\/jcb.30.2.442"},{"key":"e_1_2_10_195_1","doi-asserted-by":"publisher","DOI":"10.1111\/j.1749-6632.1982.tb21416.x"},{"key":"e_1_2_10_196_1","doi-asserted-by":"publisher","DOI":"10.1194\/jlr.M049148"},{"key":"e_1_2_10_197_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.bbamcr.2006.08.017"},{"key":"e_1_2_10_198_1","doi-asserted-by":"publisher","DOI":"10.1042\/bj1900485"},{"key":"e_1_2_10_199_1","doi-asserted-by":"publisher","DOI":"10.1111\/j.1742-4658.2005.04939.x"},{"key":"e_1_2_10_200_1","doi-asserted-by":"publisher","DOI":"10.1136\/jmedgenet-2012-100899"},{"key":"e_1_2_10_201_1","doi-asserted-by":"publisher","DOI":"10.1146\/annurev.bi.50.070181.001025"},{"key":"e_1_2_10_202_1","doi-asserted-by":"publisher","DOI":"10.1093\/oxfordjournals.jbchem.a021279"},{"key":"e_1_2_10_203_1","doi-asserted-by":"publisher","DOI":"10.1096\/fj.08-110866"},{"key":"e_1_2_10_204_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.bbalip.2010.11.010"},{"key":"e_1_2_10_205_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.bbalip.2013.12.001"},{"key":"e_1_2_10_206_1","doi-asserted-by":"publisher","DOI":"10.1194\/jlr.R005959"},{"key":"e_1_2_10_207_1","doi-asserted-by":"publisher","DOI":"10.1016\/S0021-9258(19)88666-0"},{"key":"e_1_2_10_208_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.bbalip.2013.06.007"},{"key":"e_1_2_10_209_1","doi-asserted-by":"publisher","DOI":"10.1016\/S0960-8966(01)00308-X"},{"key":"e_1_2_10_210_1","doi-asserted-by":"publisher","DOI":"10.1083\/jcb.200903065"},{"key":"e_1_2_10_211_1","doi-asserted-by":"publisher","DOI":"10.3389\/fphys.2012.00108"},{"key":"e_1_2_10_212_1","doi-asserted-by":"publisher","DOI":"10.1007\/978-94-007-6889-5_2"},{"key":"e_1_2_10_213_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.bbamcr.2006.08.010"},{"key":"e_1_2_10_214_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.bbalip.2010.01.001"},{"key":"e_1_2_10_215_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.bbalip.2011.06.006"},{"key":"e_1_2_10_216_1","doi-asserted-by":"publisher","DOI":"10.1016\/S0092-8674(03)00269-1"},{"key":"e_1_2_10_217_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.freeradbiomed.2013.08.173"},{"key":"e_1_2_10_218_1","doi-asserted-by":"publisher","DOI":"10.1056\/NEJMoa064436"},{"key":"e_1_2_10_219_1","doi-asserted-by":"publisher","DOI":"10.1038\/nrm3013"},{"key":"e_1_2_10_220_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.bbabio.2012.02.033"},{"key":"e_1_2_10_221_1","doi-asserted-by":"publisher","DOI":"10.1007\/s00018-008-7576-6"},{"key":"e_1_2_10_222_1","doi-asserted-by":"publisher","DOI":"10.1074\/mcp.M700169-MCP200"},{"key":"e_1_2_10_223_1","doi-asserted-by":"publisher","DOI":"10.1074\/jbc.M112.445445"},{"key":"e_1_2_10_224_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.bbamcr.2012.04.006"},{"key":"e_1_2_10_225_1","doi-asserted-by":"publisher","DOI":"10.1128\/jvi.70.8.5363-5372.1996"},{"key":"e_1_2_10_226_1","first-page":"655","article-title":"Reduction of serum free fatty acids and triglycerides by liver\u2010targeted expression of long chain acyl\u2010CoA synthetase 3","volume":"27","author":"Wu M","year":"2011","journal-title":"Int J Mol Med"},{"key":"e_1_2_10_227_1","doi-asserted-by":"publisher","DOI":"10.7554\/eLife.01612"},{"key":"e_1_2_10_228_1","doi-asserted-by":"publisher","DOI":"10.1371\/journal.pone.0102758"},{"key":"e_1_2_10_229_1","doi-asserted-by":"publisher","DOI":"10.1016\/S0006-291X(02)02336-7"}],"container-title":["Journal of Inherited Metabolic Disease"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1007\/s10545-015-9819-7","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,9,15]],"date-time":"2023-09-15T19:27:12Z","timestamp":1694806032000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1007\/s10545-015-9819-7"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2015,2,17]]},"references-count":228,"journal-issue":{"issue":"4","published-print":{"date-parts":[[2015,7]]}},"alternative-id":["10.1007\/s10545-015-9819-7"],"URL":"https:\/\/doi.org\/10.1007\/s10545-015-9819-7","archive":["Portico"],"relation":{},"ISSN":["0141-8955","1573-2665"],"issn-type":[{"value":"0141-8955","type":"print"},{"value":"1573-2665","type":"electronic"}],"subject":[],"published":{"date-parts":[[2015,2,17]]}}}