{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2023,10,18]],"date-time":"2023-10-18T12:19:02Z","timestamp":1697631542014},"reference-count":40,"publisher":"Elsevier BV","issue":"2-3","license":[{"start":{"date-parts":[[1998,11,1]],"date-time":"1998-11-01T00:00:00Z","timestamp":909878400000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Biochimica et Biophysica Acta (BBA) - Lipids and Lipid Metabolism"],"published-print":{"date-parts":[[1998,11]]},"DOI":"10.1016\/s0005-2760(98)00108-8","type":"journal-article","created":{"date-parts":[[2002,7,26]],"date-time":"2002-07-26T04:31:18Z","timestamp":1027657878000},"page":"177-186","source":"Crossref","is-referenced-by-count":7,"title":["Alterations in the biosynthesis of cholesterol, dolichol and dolichyl-P in the genetic cholesterol homeostasis disorder, Niemann\u2013Pick type C disease"],"prefix":"10.1016","volume":"1394","author":[{"given":"Sophia","family":"Schedin","sequence":"first","affiliation":[]},{"given":"Maria","family":"Nilsson","sequence":"additional","affiliation":[]},{"given":"Tadeusz","family":"Chojnacki","sequence":"additional","affiliation":[]},{"given":"Gustav","family":"Dallner","sequence":"additional","affiliation":[]}],"member":"78","reference":[{"key":"10.1016\/S0005-2760(98)00108-8_BIB1","doi-asserted-by":"crossref","first-page":"318","DOI":"10.1016\/0003-9861(90)90123-G","volume":"282","author":"Appelkvist","year":"1990","journal-title":"Arch. Biochem. Biophys."},{"key":"10.1016\/S0005-2760(98)00108-8_BIB2","doi-asserted-by":"crossref","first-page":"18708","DOI":"10.1016\/S0021-9258(19)37019-X","volume":"267","author":"Ericsson","year":"1992","journal-title":"J. Biol. Chem."},{"key":"10.1016\/S0005-2760(98)00108-8_BIB3","doi-asserted-by":"crossref","first-page":"230","DOI":"10.1016\/0014-5793(94)01431-Y","volume":"358","author":"Gr\u00fcnler","year":"1995","journal-title":"FEBS Lett."},{"key":"10.1016\/S0005-2760(98)00108-8_BIB4","doi-asserted-by":"crossref","first-page":"23081","DOI":"10.1016\/S0021-9258(19)49428-3","volume":"268","author":"Teclebrhan","year":"1993","journal-title":"J. Biol. Chem."},{"key":"10.1016\/S0005-2760(98)00108-8_BIB5","doi-asserted-by":"crossref","first-page":"5804","DOI":"10.1016\/S0021-9258(17)37533-6","volume":"269","author":"Runquist","year":"1994","journal-title":"J. Biol. Chem."},{"key":"10.1016\/S0005-2760(98)00108-8_BIB6","doi-asserted-by":"crossref","first-page":"79","DOI":"10.1016\/0005-2760(94)90012-4","volume":"1214","author":"Andersson","year":"1994","journal-title":"Biochim. Biophys. Acta"},{"key":"10.1016\/S0005-2760(98)00108-8_BIB7","doi-asserted-by":"crossref","first-page":"150","DOI":"10.3181\/00379727-213-44047","volume":"213","author":"Schroeder","year":"1996","journal-title":"Proc. Soc. Exp. Biol. Med."},{"key":"10.1016\/S0005-2760(98)00108-8_BIB8","doi-asserted-by":"crossref","first-page":"446","DOI":"10.1083\/jcb.101.2.446","volume":"101","author":"Kaplan","year":"1985","journal-title":"J. Cell. Biol."},{"key":"10.1016\/S0005-2760(98)00108-8_BIB9","doi-asserted-by":"crossref","first-page":"1919","DOI":"10.1016\/S0021-9258(19)39918-1","volume":"265","author":"Urbani","year":"1990","journal-title":"J. Biol. Chem."},{"key":"10.1016\/S0005-2760(98)00108-8_BIB10","doi-asserted-by":"crossref","first-page":"1003","DOI":"10.1083\/jcb.118.5.1003","volume":"118","author":"Kurzchalia","year":"1992","journal-title":"J. Cell Biol."},{"key":"10.1016\/S0005-2760(98)00108-8_BIB11","doi-asserted-by":"crossref","first-page":"29427","DOI":"10.1074\/jbc.271.11.6518","volume":"271","author":"Smart","year":"1996","journal-title":"J. Biol. Chem."},{"key":"10.1016\/S0005-2760(98)00108-8_BIB12","doi-asserted-by":"crossref","first-page":"1503","DOI":"10.1016\/S0022-2275(20)37169-8","volume":"38","author":"Fielding","year":"1997","journal-title":"J. Lipid Res."},{"key":"10.1016\/S0005-2760(98)00108-8_BIB13","doi-asserted-by":"crossref","first-page":"232","DOI":"10.1126\/science.277.5323.232","volume":"277","author":"Loftus","year":"1997","journal-title":"Science"},{"key":"10.1016\/S0005-2760(98)00108-8_BIB14","doi-asserted-by":"crossref","first-page":"235","DOI":"10.1016\/0925-4439(94)90001-9","volume":"1225","author":"Pentchev","year":"1994","journal-title":"Biochim. Biophys. Acta"},{"key":"10.1016\/S0005-2760(98)00108-8_BIB15","doi-asserted-by":"crossref","first-page":"15902","DOI":"10.1016\/S0021-9258(19)49619-1","volume":"267","author":"Roff","year":"1992","journal-title":"J. Biol. Chem."},{"key":"10.1016\/S0005-2760(98)00108-8_BIB16","doi-asserted-by":"crossref","first-page":"670","DOI":"10.1046\/j.1471-4159.1995.65020670.x","volume":"65","author":"Schedin","year":"1995","journal-title":"J. Neurochem."},{"key":"10.1016\/S0005-2760(98)00108-8_BIB17","doi-asserted-by":"crossref","first-page":"214","DOI":"10.2183\/pjab.72.214","volume":"72","author":"Yano","year":"1996","journal-title":"Proc. Jpn. Acad. Series B. Phys. Biol. Sci."},{"key":"10.1016\/S0005-2760(98)00108-8_BIB18","doi-asserted-by":"crossref","first-page":"6245","DOI":"10.1074\/jbc.272.10.6245","volume":"272","author":"Schedin","year":"1997","journal-title":"J. Biol. Chem."},{"key":"10.1016\/S0005-2760(98)00108-8_BIB19","doi-asserted-by":"crossref","first-page":"1560","DOI":"10.1016\/S0022-2275(20)37854-8","volume":"24","author":"Kase","year":"1983","journal-title":"J. Lipid Res."},{"key":"10.1016\/S0005-2760(98)00108-8_BIB20","doi-asserted-by":"crossref","first-page":"191","DOI":"10.1016\/0300-9084(93)90077-6","volume":"75","author":"Ossendorp","year":"1993","journal-title":"Biochimie"},{"key":"10.1016\/S0005-2760(98)00108-8_BIB21","doi-asserted-by":"crossref","first-page":"21277","DOI":"10.1016\/S0021-9258(17)31960-9","volume":"269","author":"Seedorf","year":"1994","journal-title":"J. Biol. Chem."},{"key":"10.1016\/S0005-2760(98)00108-8_BIB22","doi-asserted-by":"crossref","first-page":"1589","DOI":"10.1016\/S0022-2275(20)42343-0","volume":"31","author":"Hamilton","year":"1990","journal-title":"J. Lipid Res."},{"key":"10.1016\/S0005-2760(98)00108-8_BIB23","doi-asserted-by":"crossref","first-page":"12053","DOI":"10.1016\/S0021-9258(18)67201-1","volume":"261","author":"Keller","year":"1986","journal-title":"J. Biol. Chem."},{"key":"10.1016\/S0005-2760(98)00108-8_BIB24","doi-asserted-by":"crossref","first-page":"789","DOI":"10.1111\/j.1432-1033.1991.tb16434.x","volume":"202","author":"Ericsson","year":"1991","journal-title":"Eur. J. Biochem."},{"key":"10.1016\/S0005-2760(98)00108-8_BIB25","doi-asserted-by":"crossref","first-page":"139","DOI":"10.1007\/BF01116458","volume":"8","author":"Edlund","year":"1988","journal-title":"Biosci. Rep."},{"key":"10.1016\/S0005-2760(98)00108-8_BIB26","doi-asserted-by":"crossref","first-page":"497","DOI":"10.1016\/S0021-9258(18)64849-5","volume":"226","author":"Folch","year":"1957","journal-title":"J. Biol. Chem."},{"key":"10.1016\/S0005-2760(98)00108-8_BIB27","doi-asserted-by":"crossref","first-page":"5144","DOI":"10.1016\/S0021-9258(18)50571-8","volume":"254","author":"Brown","year":"1979","journal-title":"J. Biol. Chem."},{"key":"10.1016\/S0005-2760(98)00108-8_BIB28","doi-asserted-by":"crossref","first-page":"2159","DOI":"10.1016\/S0022-2275(20)42102-9","volume":"31","author":"\u00c5kerlund","year":"1990","journal-title":"J. Lipid Res."},{"key":"10.1016\/S0005-2760(98)00108-8_BIB29","doi-asserted-by":"crossref","first-page":"599","DOI":"10.1093\/carcin\/16.3.599","volume":"16","author":"Olsson","year":"1995","journal-title":"Carcinogenesis"},{"key":"10.1016\/S0005-2760(98)00108-8_BIB30","doi-asserted-by":"crossref","first-page":"832","DOI":"10.1016\/S0021-9258(18)54009-6","volume":"268","author":"Ericsson","year":"1993","journal-title":"J. Biol. Chem."},{"key":"10.1016\/S0005-2760(98)00108-8_BIB31","doi-asserted-by":"crossref","first-page":"580","DOI":"10.1007\/BF01797928","volume":"14","author":"Vanier","year":"1991","journal-title":"J. Inherit. Metab. Dis."},{"key":"10.1016\/S0005-2760(98)00108-8_BIB32","doi-asserted-by":"crossref","first-page":"228","DOI":"10.1126\/science.277.5323.228","volume":"277","author":"Carstea","year":"1997","journal-title":"Science"},{"key":"10.1016\/S0005-2760(98)00108-8_BIB33","doi-asserted-by":"crossref","first-page":"6245","DOI":"10.1096\/fasebj.1.1.3609608","volume":"1","author":"Pentchev","year":"1987","journal-title":"FASEB J."},{"key":"10.1016\/S0005-2760(98)00108-8_BIB34","doi-asserted-by":"crossref","first-page":"370","DOI":"10.1006\/geno.1994.1630","volume":"24","author":"Ohba","year":"1994","journal-title":"Genomics"},{"key":"10.1016\/S0005-2760(98)00108-8_BIB35","doi-asserted-by":"crossref","first-page":"189","DOI":"10.1006\/bbrc.1997.6929","volume":"236","author":"Garver","year":"1997","journal-title":"Biochem. Biophys. Res. Commun."},{"key":"10.1016\/S0005-2760(98)00108-8_BIB36","doi-asserted-by":"crossref","first-page":"1625","DOI":"10.1083\/jcb.108.5.1625","volume":"108","author":"Liscum","year":"1989","journal-title":"J. Cell Biol."},{"key":"10.1016\/S0005-2760(98)00108-8_BIB37","doi-asserted-by":"crossref","first-page":"2772","DOI":"10.1016\/S0021-9258(17)35852-0","volume":"261","author":"Pentchev","year":"1986","journal-title":"J. Biol. Chem."},{"key":"10.1016\/S0005-2760(98)00108-8_BIB38","doi-asserted-by":"crossref","first-page":"339","DOI":"10.1007\/BF01799976","volume":"10","author":"Maziere","year":"1987","journal-title":"J. Inher. Metab. Dis."},{"key":"10.1016\/S0005-2760(98)00108-8_BIB39","doi-asserted-by":"crossref","first-page":"231","DOI":"10.1247\/csf.18.231","volume":"18","author":"Ohno","year":"1993","journal-title":"Cell Struct. Funct."},{"key":"10.1016\/S0005-2760(98)00108-8_BIB40","doi-asserted-by":"crossref","first-page":"259","DOI":"10.1016\/0005-2760(94)90200-3","volume":"1212","author":"Gr\u00fcnler","year":"1994","journal-title":"Biochim. Biophys. Acta"}],"container-title":["Biochimica et Biophysica Acta (BBA) - Lipids and Lipid Metabolism"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0005276098001088?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0005276098001088?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2021,5,15]],"date-time":"2021-05-15T03:20:45Z","timestamp":1621048845000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0005276098001088"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[1998,11]]},"references-count":40,"journal-issue":{"issue":"2-3","published-print":{"date-parts":[[1998,11]]}},"alternative-id":["S0005276098001088"],"URL":"https:\/\/doi.org\/10.1016\/s0005-2760(98)00108-8","relation":{},"ISSN":["0005-2760"],"issn-type":[{"value":"0005-2760","type":"print"}],"subject":[],"published":{"date-parts":[[1998,11]]}}}