{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,3,10]],"date-time":"2026-03-10T16:08:45Z","timestamp":1773158925641,"version":"3.50.1"},"reference-count":27,"publisher":"Elsevier BV","issue":"1","license":[{"start":{"date-parts":[[1980,7,1]],"date-time":"1980-07-01T00:00:00Z","timestamp":331257600000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["The Journal of Pediatrics"],"published-print":{"date-parts":[[1980,7]]},"DOI":"10.1016\/s0022-3476(80)80133-8","type":"journal-article","created":{"date-parts":[[2006,3,30]],"date-time":"2006-03-30T07:52:14Z","timestamp":1143705134000},"page":"72-78","source":"Crossref","is-referenced-by-count":194,"title":["The Wiskott-Aldrich syndrome in the United States and Canada (1892\u20131979)"],"prefix":"10.1016","volume":"97","author":[{"suffix":"III","given":"Guy S.","family":"Perry","sequence":"first","affiliation":[]},{"given":"Beatrice D.","family":"Spector","sequence":"additional","affiliation":[]},{"given":"Leonard M.","family":"Schuman","sequence":"additional","affiliation":[]},{"given":"Jack S.","family":"Mandel","sequence":"additional","affiliation":[]},{"given":"V. Elving","family":"Anderson","sequence":"additional","affiliation":[]},{"given":"Richard B.","family":"McHugh","sequence":"additional","affiliation":[]},{"given":"Margot R.","family":"Hanson","sequence":"additional","affiliation":[]},{"given":"Sharon M.","family":"Fahlstrom","sequence":"additional","affiliation":[]},{"given":"William","family":"Krivit","sequence":"additional","affiliation":[]},{"given":"John H.","family":"Kersey","sequence":"additional","affiliation":[]}],"member":"78","reference":[{"key":"10.1016\/S0022-3476(80)80133-8_bib1","first-page":"212","article-title":"Familiaerer, angeborener Morbus werlhoffii?","volume":"68","author":"Wiskott","year":"1937","journal-title":"Monatsschr Kinderheilkd"},{"key":"10.1016\/S0022-3476(80)80133-8_bib2","doi-asserted-by":"crossref","first-page":"133","DOI":"10.1542\/peds.13.2.133","article-title":"Pedigree demonstrating a sex-linked recessive condition characterized by draining ears, eczematoid dermatitis, and bloody diarrhea","volume":"13","author":"Aldrich","year":"1954","journal-title":"Pediatrics"},{"key":"10.1016\/S0022-3476(80)80133-8_bib3","first-page":"250","article-title":"Immunodeficiency in the Wiskott-Aldrich syndrome","volume":"vol 11","author":"Blaese","year":"1975"},{"key":"10.1016\/S0022-3476(80)80133-8_bib4","doi-asserted-by":"crossref","first-page":"499","DOI":"10.1056\/NEJM197203092861001","article-title":"Platelet size and kinetics in hereditary and acquired thrombocytopenia","volume":"286","author":"Murphy","year":"1972","journal-title":"N Engl J Med"},{"key":"10.1016\/S0022-3476(80)80133-8_bib5","doi-asserted-by":"crossref","first-page":"201","DOI":"10.1016\/0008-8749(75)90204-X","article-title":"The Wiskott-Aldrich syndrome. Immunologic studies in nine patients and selected family members","volume":"19","author":"Spitler","year":"1975","journal-title":"Cell Immunol"},{"key":"10.1016\/S0022-3476(80)80133-8_bib6","doi-asserted-by":"crossref","first-page":"214","DOI":"10.1111\/j.1423-0410.1972.tb04007.x","article-title":"Monocyte receptors for immunoglobulin and complement in immunologic deficiency diseases","volume":"23","author":"Douglas","year":"1972","journal-title":"Vox Sang"},{"key":"10.1016\/S0022-3476(80)80133-8_bib7","doi-asserted-by":"crossref","first-page":"437","DOI":"10.1111\/j.1749-6632.1972.tb16316.x","article-title":"Nature of the platelet defect in the Wiskott-Aldrich syndrome","volume":"201","author":"Baldini","year":"1972","journal-title":"Ann NY Acad Sci"},{"key":"10.1016\/S0022-3476(80)80133-8_bib8","doi-asserted-by":"crossref","first-page":"121","DOI":"10.1016\/S0140-6736(78)90419-1","article-title":"A metabolic abnormality in platelets from Wiskott-Aldrich syndrome heterozygotes","volume":"1","author":"Shapiro","year":"1978","journal-title":"Lancet"},{"key":"10.1016\/S0022-3476(80)80133-8_bib9","doi-asserted-by":"crossref","first-page":"772","DOI":"10.1016\/S0022-3476(73)80368-3","article-title":"Autoimmune hemolytic anemia in Wiskott-Aldrich syndrome during treatment with transfer factor","volume":"83","author":"Ballow","year":"1973","journal-title":"J Pediatr"},{"key":"10.1016\/S0022-3476(80)80133-8_bib10","doi-asserted-by":"crossref","first-page":"742","DOI":"10.1016\/S0022-3476(79)80726-X","article-title":"Fatal arteritis as a complication of Wiskott-Aldrich syndrome","volume":"95","author":"Filipovich","year":"1979","journal-title":"J Pediatr"},{"key":"10.1016\/S0022-3476(80)80133-8_bib11","doi-asserted-by":"crossref","first-page":"59","DOI":"10.1016\/0002-9343(79)90074-3","article-title":"Transfer factor therapy in the Wiskott-Aldrich syndrome. Results of long-term follow-up in 32 patients","volume":"67","author":"Spitler","year":"1979","journal-title":"Am J Med"},{"key":"10.1016\/S0022-3476(80)80133-8_bib12","doi-asserted-by":"crossref","first-page":"12","DOI":"10.1016\/0090-1229(78)90200-3","article-title":"Genetically determined immunodeficiency diseases (GDID) and malignancy: Report from the Immunodeficiency-Cancer Registry","volume":"11","author":"Spector","year":"1978","journal-title":"Clin Immunol Immunopathol"},{"key":"10.1016\/S0022-3476(80)80133-8_bib13","doi-asserted-by":"crossref","first-page":"927","DOI":"10.1542\/peds.47.5.927","article-title":"Special article: Primary immunodeficiencies: Report of a World Health Organization committee","volume":"47","author":"Fudenberg","year":"1971","journal-title":"Pediatrics"},{"key":"10.1016\/S0022-3476(80)80133-8_bib14","year":"1978"},{"key":"10.1016\/S0022-3476(80)80133-8_bib15","series-title":"End results in cancer","first-page":"101","article-title":"The relative survival rate: A statistical methodology in end results and mortality trends in cancer","author":"Ederer","year":"1961"},{"key":"10.1016\/S0022-3476(80)80133-8_bib16","first-page":"5","volume":"vol 11","year":"1978"},{"key":"10.1016\/S0022-3476(80)80133-8_bib17","doi-asserted-by":"crossref","first-page":"55","DOI":"10.1016\/S0140-6736(73)93256-X","article-title":"Risk of cancer in renal transplant recipients","volume":"2","author":"Hoover","year":"1973","journal-title":"Lancet"},{"key":"10.1016\/S0022-3476(80)80133-8_bib18","first-page":"2","article-title":"Illness from cancer in the US","volume":"vol 59","author":"Dorn","year":"1944"},{"key":"10.1016\/S0022-3476(80)80133-8_bib19","volume":"vol 56","author":"Dorn","year":"1959"},{"key":"10.1016\/S0022-3476(80)80133-8_bib20","series-title":"Third national cancer survey: Incidence data","year":"1975"},{"key":"10.1016\/S0022-3476(80)80133-8_bib21","first-page":"85","article-title":"Das Wiskott-Aldrich syndrome","volume":"vol 41","author":"Behloradsky","year":"1978"},{"key":"10.1016\/S0022-3476(80)80133-8_bib22","first-page":"22","article-title":"Aldrich's syndrome","volume":"17","author":"Coleman","year":"1961","journal-title":"Clin Proc Child Hosp (Wash)"},{"key":"10.1016\/S0022-3476(80)80133-8_bib23","doi-asserted-by":"crossref","first-page":"761","DOI":"10.1016\/S0022-3476(66)80450-X","article-title":"The development of malignancy in the course of the Aldrich syndrome","volume":"68","author":"ten Bensel","year":"1966","journal-title":"J Pediatr"},{"key":"10.1016\/S0022-3476(80)80133-8_bib24","doi-asserted-by":"crossref","first-page":"204","DOI":"10.1016\/S0022-3476(74)80393-8","article-title":"Monoclonal gammopathy in the Wiskott-Aldrich syndrome","volume":"85","author":"Bruce","year":"1974","journal-title":"J Pediatr"},{"key":"10.1016\/S0022-3476(80)80133-8_bib25","series-title":"Advances in surgery","first-page":"155","article-title":"Development of cancer in transplantation patients","author":"Penn","year":"1978"},{"key":"10.1016\/S0022-3476(80)80133-8_bib26","doi-asserted-by":"crossref","first-page":"1364","DOI":"10.1016\/S0140-6736(68)92672-X","article-title":"Bone marrow transplantation in a patient with the Wiskott-Aldrich syndrome","volume":"2","author":"Bach","year":"1968","journal-title":"Lancet"},{"key":"10.1016\/S0022-3476(80)80133-8_bib27","doi-asserted-by":"crossref","first-page":"921","DOI":"10.1056\/NEJM197804272981701","article-title":"Complete correction of the Wiskott-Aldrich syndrome by allogeneic bone-marrow transplantation","volume":"298","author":"Parkman","year":"1978","journal-title":"N Engl J Med"}],"container-title":["The Journal of Pediatrics"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0022347680801338?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0022347680801338?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2023,5,6]],"date-time":"2023-05-06T18:10:15Z","timestamp":1683396615000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0022347680801338"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[1980,7]]},"references-count":27,"journal-issue":{"issue":"1","published-print":{"date-parts":[[1980,7]]}},"alternative-id":["S0022347680801338"],"URL":"https:\/\/doi.org\/10.1016\/s0022-3476(80)80133-8","relation":{},"ISSN":["0022-3476"],"issn-type":[{"value":"0022-3476","type":"print"}],"subject":[],"published":{"date-parts":[[1980,7]]}}}