{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,6,15]],"date-time":"2026-06-15T12:54:22Z","timestamp":1781528062462,"version":"3.54.1"},"reference-count":32,"publisher":"Elsevier BV","issue":"7","license":[{"start":{"date-parts":[[2026,7,1]],"date-time":"2026-07-01T00:00:00Z","timestamp":1782864000000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2026,7,1]],"date-time":"2026-07-01T00:00:00Z","timestamp":1782864000000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/legal\/tdmrep-license"},{"start":{"date-parts":[[2026,2,12]],"date-time":"2026-02-12T00:00:00Z","timestamp":1770854400000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"funder":[{"DOI":"10.13039\/100000002","name":"National Institutes of Health","doi-asserted-by":"publisher","id":[{"id":"10.13039\/100000002","id-type":"DOI","asserted-by":"publisher"}]},{"DOI":"10.13039\/100004173","name":"Sturge-Weber Foundation","doi-asserted-by":"publisher","id":[{"id":"10.13039\/100004173","id-type":"DOI","asserted-by":"publisher"}]},{"DOI":"10.13039\/100000065","name":"National Institute of Neurological Disorders and Stroke","doi-asserted-by":"publisher","award":["R01 NS041922"],"award-info":[{"award-number":["R01 NS041922"]}],"id":[{"id":"10.13039\/100000065","id-type":"DOI","asserted-by":"publisher"}]}],"content-domain":{"domain":["academicradiology.org","clinicalkey.com","clinicalkey.com.au","clinicalkey.es","clinicalkey.fr","clinicalkey.jp","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Academic Radiology"],"published-print":{"date-parts":[[2026,7]]},"DOI":"10.1016\/j.acra.2026.02.021","type":"journal-article","created":{"date-parts":[[2026,3,3]],"date-time":"2026-03-03T13:13:18Z","timestamp":1772543598000},"page":"3003-3010","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":0,"title":["Introduction of a Brain MRI Scoring System with Clinical Relevance for Sturge-Weber Syndrome"],"prefix":"10.1016","volume":"33","author":[{"given":"Csaba","family":"Juh\u00e1sz","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Aimee F.","family":"Luat","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Michael E.","family":"Behen","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-0076-1470","authenticated-orcid":false,"given":"Ajay","family":"Kumar","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"key":"10.1016\/j.acra.2026.02.021_bib1","doi-asserted-by":"crossref","first-page":"1971","DOI":"10.1056\/NEJMoa1213507","article-title":"Sturge-Weber syndrome and port-wine stains caused by somatic mutation in GNAQ","volume":"368","author":"Shirley","year":"2013","journal-title":"N Engl J Med"},{"key":"10.1016\/j.acra.2026.02.021_bib2","doi-asserted-by":"crossref","first-page":"63","DOI":"10.2147\/TACG.S363685","article-title":"Sturge-Weber syndrome: a review of pathophysiology, genetics, clinical features, and current management approache","volume":"16","author":"S\u00e1nchez-Espino","year":"2023","journal-title":"Appl Clin Genet"},{"key":"10.1016\/j.acra.2026.02.021_bib3","doi-asserted-by":"crossref","first-page":"509","DOI":"10.1177\/08830738030180080701","article-title":"Pathophysiology of Sturge-Weber syndrome","volume":"18","author":"Comi","year":"2003","journal-title":"J Child Neurol"},{"key":"10.1016\/j.acra.2026.02.021_bib4","doi-asserted-by":"crossref","first-page":"303","DOI":"10.1016\/j.pediatrneurol.2003.12.015","article-title":"Sturge-Weber syndrome: a review","volume":"30","author":"Thomas-Sohl","year":"2004","journal-title":"Pediatr Neurol"},{"key":"10.1016\/j.acra.2026.02.021_bib5","doi-asserted-by":"crossref","first-page":"214","DOI":"10.1111\/j.1469-8749.2011.04169.x","article-title":"Brain Vascular Malformation Consortium National Sturge-Weber Syndrome Workgroup. Updates and future horizons on the understanding, diagnosis, and treatment of Sturge-Weber syndrome brain involvement","volume":"54","author":"Lo","year":"2012","journal-title":"Dev Med Child Neurol"},{"key":"10.1016\/j.acra.2026.02.021_bib6","doi-asserted-by":"crossref","first-page":"315","DOI":"10.1016\/B978-0-444-52891-9.00037-3","article-title":"Sturge-Weber syndrome","volume":"111","author":"Nabbout","year":"2013","journal-title":"Handb Clin Neurol"},{"key":"10.1016\/j.acra.2026.02.021_bib7","doi-asserted-by":"crossref","first-page":"2182","DOI":"10.3390\/jcm14072182","article-title":"Sturge-Weber syndrome: a narrative review of clinical presentation and updates on management","volume":"14","author":"Shah","year":"2025","journal-title":"J Clin Med"},{"key":"10.1016\/j.acra.2026.02.021_bib8","doi-asserted-by":"crossref","first-page":"300","DOI":"10.1002\/jmri.21435","article-title":"MR susceptibility weighted imaging (SWI) complements conventional contrast enhanced T1 weighted MRI in characterizing brain abnormalities of Sturge-Weber Syndrome","volume":"28","author":"Hu","year":"2008","journal-title":"J Magn Reson Imaging"},{"key":"10.1016\/j.acra.2026.02.021_bib9","doi-asserted-by":"crossref","first-page":"952","DOI":"10.1111\/dmcn.13433","article-title":"Clinical and metabolic correlates of cerebral calcifications in Sturge-Weber syndrome","volume":"59","author":"Pilli","year":"2017","journal-title":"Dev Med Child Neurol"},{"key":"10.1016\/j.acra.2026.02.021_bib10","doi-asserted-by":"crossref","first-page":"63","DOI":"10.1016\/j.pediatrneurol.2025.07.009","article-title":"Absence of deep and basal veins is common and clinically relevant in Sturge-Weber syndrome","volume":"171","author":"Albazron","year":"2025","journal-title":"Pediatr Neurol"},{"key":"10.1016\/j.acra.2026.02.021_bib11","doi-asserted-by":"crossref","first-page":"49","DOI":"10.1016\/j.pediatrneurol.2022.11.011","article-title":"Deep venous remodeling in unilateral Sturge-Weber syndrome: robust hemispheric differences and clinical correlates","volume":"139","author":"Juh\u00e1sz","year":"2023","journal-title":"Pediatr Neurol"},{"key":"10.1016\/j.acra.2026.02.021_bib12","doi-asserted-by":"crossref","first-page":"2704","DOI":"10.1007\/s00247-025-06402-3","article-title":"Beyond the leptomeningeal angioma: a comprehensive review of MR imaging features of Sturge-Weber syndrome, from early vascular responses to tissue necrosis","volume":"55","author":"Cerron-Vela","year":"2025","journal-title":"Pediatr Radiol"},{"key":"10.1016\/j.acra.2026.02.021_bib13","doi-asserted-by":"crossref","first-page":"2553","DOI":"10.1007\/s00381-020-04695-3","article-title":"Sturge-Weber syndrome: an update on the relevant issues for neurosurgeons","volume":"36","author":"Bianchi","year":"2020","journal-title":"Childs Nerv Syst"},{"key":"10.1016\/j.acra.2026.02.021_bib14","doi-asserted-by":"crossref","first-page":"31","DOI":"10.1016\/j.pediatrneurol.2019.05.013","article-title":"Neurological\u00a0complications of Sturge-Weber syndrome: current status and unmet needs","volume":"98","author":"Luat","year":"2019","journal-title":"Pediatr Neurol"},{"key":"10.1016\/j.acra.2026.02.021_bib15","doi-asserted-by":"crossref","first-page":"59","DOI":"10.1016\/j.pediatrneurol.2021.04.013","article-title":"Consensus statement for the management and treatment of Sturge-Weber syndrome: neurology, neuroimaging, and ophthalmology recommendations","volume":"121","author":"Sabeti","year":"2021","journal-title":"Pediatr Neurol"},{"key":"10.1016\/j.acra.2026.02.021_bib16","doi-asserted-by":"crossref","first-page":"3769","DOI":"10.1161\/STROKEAHA.122.038585","article-title":"Updates on Sturge-Weber syndrome","volume":"53","author":"Yeom","year":"2022","journal-title":"Stroke"},{"key":"10.1016\/j.acra.2026.02.021_bib17","doi-asserted-by":"crossref","DOI":"10.3389\/fneur.2024.1493873","article-title":"Sturge-Weber syndrome: updates in translational neurology","volume":"15","author":"Solomon","year":"2024","journal-title":"Front Neurol"},{"key":"10.1016\/j.acra.2026.02.021_bib18","doi-asserted-by":"crossref","first-page":"867","DOI":"10.1177\/08830738050200110201","article-title":"Quantitative analysis of cerebral cortical atrophy and correlation with clinical severity in unilateral Sturge-Weber syndrome","volume":"20","author":"Kelley","year":"2005","journal-title":"J Child Neurol"},{"key":"10.1016\/j.acra.2026.02.021_bib19","doi-asserted-by":"crossref","first-page":"343","DOI":"10.1177\/08830738241272064","article-title":"Feasibility and potential diagnostic value of noncontrast brain MRI in nonsedated children with Sturge-Weber syndrome and healthy siblings","volume":"39","author":"Juh\u00e1sz","year":"2024","journal-title":"J Child Neurol"},{"key":"10.1016\/j.acra.2026.02.021_bib20","doi-asserted-by":"crossref","first-page":"50","DOI":"10.1186\/s11689-025-09640-6","article-title":"Biomarker development in Sturge-Weber syndrome","volume":"17","author":"Gupta","year":"2025","journal-title":"J Neurodev Disord"},{"key":"10.1016\/j.acra.2026.02.021_bib21","doi-asserted-by":"crossref","first-page":"191","DOI":"10.1111\/j.1528-1167.2006.00630.x","article-title":"Quantitative EEG asymmetry correlates with clinical severity in unilateral Sturge-Weber syndrome","volume":"48","author":"Hatfield","year":"2007","journal-title":"Epilepsia"},{"key":"10.1016\/j.acra.2026.02.021_bib22","doi-asserted-by":"crossref","first-page":"1025","DOI":"10.1016\/S1388-2457(02)00105-0","article-title":"Diazepam-enhanced beta activity in Sturge Weber syndrome: its diagnostic significance in comparison with MRI","volume":"113","author":"Jansen","year":"2002","journal-title":"Clin Neurophysiol"},{"key":"10.1016\/j.acra.2026.02.021_bib23","doi-asserted-by":"crossref","first-page":"289","DOI":"10.1111\/j.2517-6161.1995.tb02031.x","article-title":"Controlling the false discovery rate: a practical and powerful approach to multiple testing","volume":"57","author":"Benjamini","year":"1995","journal-title":"J R Stat Soc Series B Methodol"},{"key":"10.1016\/j.acra.2026.02.021_bib24","doi-asserted-by":"crossref","first-page":"155","DOI":"10.1016\/j.jcm.2016.02.012","article-title":"A guideline of selecting and reporting intraclass correlation coefficients for reliability research","volume":"15","author":"Koo","year":"2016","journal-title":"J Chiropr Med"},{"key":"10.1016\/j.acra.2026.02.021_bib25","doi-asserted-by":"crossref","first-page":"205","DOI":"10.1016\/j.jpeds.2017.05.053","article-title":"Size of facial port-wine birthmark may predict neurologic outcome in Sturge-Weber syndrome","volume":"188","author":"Dymerska","year":"2017","journal-title":"J Pediatr"},{"key":"10.1016\/j.acra.2026.02.021_bib26","doi-asserted-by":"crossref","first-page":"352","DOI":"10.1016\/j.yebeh.2011.07.010","article-title":"Brain damage and IQ in unilateral Sturge-Weber syndrome: support for a \"fresh start\" hypothesis","volume":"22","author":"Behen","year":"2011","journal-title":"Epilepsy Behav"},{"key":"10.1016\/j.acra.2026.02.021_bib27","doi-asserted-by":"crossref","first-page":"1596","DOI":"10.1002\/hbm.23937","article-title":"Metabolic correlates of cognitive function in children with unilateral Sturge-Weber syndrome: evidence for regional functional reorganization and crowding","volume":"39","author":"Kim","year":"2018","journal-title":"Hum Brain Mapp"},{"key":"10.1016\/j.acra.2026.02.021_bib28","doi-asserted-by":"crossref","first-page":"277","DOI":"10.1016\/j.ejpn.2007.02.001","article-title":"Evolution of cortical metabolic abnormalities and their clinical correlates in Sturge-Weber syndrome","volume":"11","author":"Juh\u00e1sz","year":"2007","journal-title":"Eur J Paediatr Neurol"},{"key":"10.1016\/j.acra.2026.02.021_bib29","doi-asserted-by":"crossref","first-page":"226","DOI":"10.1097\/00004728-198703000-00005","article-title":"Accelerated myelination in early Sturge-Weber syndrome demonstrated by MR imaging","volume":"11","author":"Jacoby","year":"1987","journal-title":"J Comput Assist Tomogr"},{"key":"10.1016\/j.acra.2026.02.021_bib30","doi-asserted-by":"crossref","first-page":"186","DOI":"10.3174\/ajnr.A8426","article-title":"Alternative venous pathways: a potential key imaging feature for early diagnosis of Sturge-Weber syndrome type 1","volume":"46","author":"Cerron-Vela","year":"2025","journal-title":"AJNR Am J Neuroradiol"},{"key":"10.1016\/j.acra.2026.02.021_bib31","doi-asserted-by":"crossref","first-page":"32","DOI":"10.1016\/j.pediatrneurol.2018.04.004","article-title":"Quantitative apparent diffusion coefficient mapping may predict seizure onset in children with Sturge-Weber syndrome","volume":"84","author":"Pinto","year":"2018","journal-title":"Pediatr Neurol"},{"key":"10.1016\/j.acra.2026.02.021_bib32","doi-asserted-by":"crossref","first-page":"25","DOI":"10.1016\/j.pediatrneurol.2015.11.005","article-title":"Sturge-Weber syndrome: brain magnetic resonance imaging and neuropathology findings","volume":"58","author":"Pinto","year":"2016","journal-title":"Pediatr Neurol"}],"container-title":["Academic Radiology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1076633226001091?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1076633226001091?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2026,6,15]],"date-time":"2026-06-15T12:11:19Z","timestamp":1781525479000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S1076633226001091"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2026,7]]},"references-count":32,"journal-issue":{"issue":"7","published-print":{"date-parts":[[2026,7]]}},"alternative-id":["S1076633226001091"],"URL":"https:\/\/doi.org\/10.1016\/j.acra.2026.02.021","relation":{},"ISSN":["1076-6332"],"issn-type":[{"value":"1076-6332","type":"print"}],"subject":[],"published":{"date-parts":[[2026,7]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"Introduction of a Brain MRI Scoring System with Clinical Relevance for Sturge-Weber Syndrome","name":"articletitle","label":"Article Title"},{"value":"Academic Radiology","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.acra.2026.02.021","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"\u00a9 2026 The Association of Academic Radiology. Published by Elsevier Inc.","name":"copyright","label":"Copyright"}]}}