{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,7,31]],"date-time":"2026-07-31T02:01:46Z","timestamp":1785463306293,"version":"3.56.0"},"reference-count":40,"publisher":"Elsevier BV","license":[{"start":{"date-parts":[[2022,8,1]],"date-time":"2022-08-01T00:00:00Z","timestamp":1659312000000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2022,8,1]],"date-time":"2022-08-01T00:00:00Z","timestamp":1659312000000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/legal\/tdmrep-license"},{"start":{"date-parts":[[2022,4,13]],"date-time":"2022-04-13T00:00:00Z","timestamp":1649808000000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by-nc-nd\/4.0\/"}],"content-domain":{"domain":["clinicalkey.com","clinicalkey.com.au","clinicalkey.es","clinicalkey.fr","clinicalkey.jp","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Annals of Diagnostic Pathology"],"published-print":{"date-parts":[[2022,8]]},"DOI":"10.1016\/j.anndiagpath.2022.151943","type":"journal-article","created":{"date-parts":[[2022,3,28]],"date-time":"2022-03-28T20:22:21Z","timestamp":1648498941000},"page":"151943","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":7,"special_numbering":"C","title":["Exploring the pathophysiologic basis of constrictive pericarditis of Kohlmeier Degos disease: A case series and review of the literature"],"prefix":"10.1016","volume":"59","author":[{"given":"Cynthia","family":"Magro","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Lee","family":"Shapiro","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"issue":"6","key":"10.1016\/j.anndiagpath.2022.151943_bb0005","doi-asserted-by":"crossref","first-page":"783","DOI":"10.1007\/BF01828450","article-title":"Multiple skin necrosis in thrombangiitisobliterans","volume":"181","author":"K\u00f6hlmeier","year":"1941","journal-title":"Arch Dermatol Syphilis"},{"key":"10.1016\/j.anndiagpath.2022.151943_bb0010","first-page":"148","article-title":"Dermatite papulosquameuse atrophiante","volume":"49","author":"Degos","year":"1942","journal-title":"Bull Soc Fr Dermatol Syphiligr"},{"issue":"11","key":"10.1016\/j.anndiagpath.2022.151943_bb0015","doi-asserted-by":"crossref","first-page":"923","DOI":"10.1111\/j.1532-5415.1971.tb02208.x","article-title":"Degos' disease associated with a \"spontaneous cure\" of diabetes","volume":"19","author":"Salomon","year":"1971","journal-title":"J Am Geriatr Soc"},{"issue":"2","key":"10.1016\/j.anndiagpath.2022.151943_bb0020","doi-asserted-by":"crossref","first-page":"137","DOI":"10.1111\/j.1365-2133.1979.tb05551.x","article-title":"Microcylinders of endoplasmic reticulum in histiocytes in patients suffering from Kohlmeier-Degos' syndrome and dermatomyositis","volume":"100","author":"Olmos","year":"1979","journal-title":"Br J Dermatol"},{"issue":"1","key":"10.1016\/j.anndiagpath.2022.151943_bb0025","doi-asserted-by":"crossref","first-page":"10","DOI":"10.1186\/1750-1172-8-10","article-title":"Malignant atrophic papulosis (K\u00f6hlmeier-Degos disease)-a review","volume":"8","author":"Theodoridis","year":"2013","journal-title":"Orphanet J Rare Dis"},{"issue":"5","key":"10.1016\/j.anndiagpath.2022.151943_bb0030","doi-asserted-by":"crossref","first-page":"483","DOI":"10.1111\/j.1365-2230.2007.02497.x","article-title":"Malignant atrophic papulosis","volume":"32","author":"Scheinfeld","year":"2007","journal-title":"Clin Exp Dermatol"},{"issue":"2","key":"10.1016\/j.anndiagpath.2022.151943_bb0035","first-page":"101","article-title":"Lesions resembling malignant atrophic papulosis in a patient with progressive systemic sclerosis","volume":"75","author":"Liu","year":"2005","journal-title":"Cutis"},{"issue":"3","key":"10.1016\/j.anndiagpath.2022.151943_bb0040","doi-asserted-by":"crossref","first-page":"162","DOI":"10.2310\/7750.2011.10035","article-title":"Degos disease with dermatomyositis-like phenomenon: a diagnostic dilemma and a therapeutic challenge","volume":"15","author":"Gupta","year":"2011","journal-title":"J Cutan Med Surg"},{"issue":"7","key":"10.1016\/j.anndiagpath.2022.151943_bb0045","doi-asserted-by":"crossref","first-page":"770","DOI":"10.1111\/ijd.13629","article-title":"Systemic lupus erythematosus with degos disease: role of dermatoscopy in diagnosis","volume":"56","author":"Vinay","year":"2017","journal-title":"Int J Dermatol"},{"issue":"2","key":"10.1016\/j.anndiagpath.2022.151943_bb0050","doi-asserted-by":"crossref","first-page":"215","DOI":"10.5021\/ad.2017.29.2.215","article-title":"Degos-like lesions associated with systemic lupus erythematosus","volume":"29","author":"Jang","year":"2017","journal-title":"Ann Dermatol"},{"issue":"2","key":"10.1016\/j.anndiagpath.2022.151943_bb0055","doi-asserted-by":"crossref","first-page":"219","DOI":"10.4103\/0378-6323.77477","article-title":"Degos disease-like presentation in systemic lupus erythematosus","volume":"77","author":"Riyaz","year":"2011","journal-title":"Indian J Dermatol Venereol Leprol"},{"issue":"9","key":"10.1016\/j.anndiagpath.2022.151943_bb0060","first-page":"414","article-title":"Diabetes mellitus and Degos disease","volume":"109","author":"Fernandez-Flores","year":"2008","journal-title":"Bratisl Lek Listy"},{"issue":"1","key":"10.1016\/j.anndiagpath.2022.151943_bb0065","doi-asserted-by":"crossref","first-page":"10","DOI":"10.1186\/1750-1172-8-10","article-title":"Malignant atrophic papulosis (K\u00f6hlmeier-Degos disease)-a review","volume":"8","author":"Theodoridis","year":"2013","journal-title":"Orphanet J Rare Dis"},{"key":"10.1016\/j.anndiagpath.2022.151943_bb0070","first-page":"1361","article-title":"Case 18-2014. A man with rash, myalgia, and weakness","volume":"371","author":"Shapiro","year":"2014"},{"issue":"1","key":"10.1016\/j.anndiagpath.2022.151943_bb0075","doi-asserted-by":"crossref","first-page":"110","DOI":"10.1111\/bjd.12642","article-title":"Malignant and benign forms of atrophic papulosis (K\u00f6hlmeier-degos disease): systemic involvement determines the prognosis","volume":"170","author":"Theodoridis","year":"2014","journal-title":"Br J Dermatol"},{"issue":"10","key":"10.1016\/j.anndiagpath.2022.151943_bb0080","doi-asserted-by":"crossref","first-page":"1753","DOI":"10.1111\/jdv.14355","article-title":"Benign atrophic papulosis (K\u00f6hlmeier-Degos disease): the wedge-shaped dermal necrosis can resolve with time","volume":"31","author":"Zouboulis","year":"2017","journal-title":"J Eur Acad Dermatol Venereol"},{"key":"10.1016\/j.anndiagpath.2022.151943_bb0085","doi-asserted-by":"crossref","DOI":"10.1111\/1346-8138.14280","article-title":"Malignant atrophic papulosis with motor aphasia and intestinal perforation: a case report and review of published works","author":"Hu","year":"2018","journal-title":"J Dermatol"},{"issue":"2","key":"10.1016\/j.anndiagpath.2022.151943_bb0090","doi-asserted-by":"crossref","first-page":"215","DOI":"10.5021\/ad.2017.29.2.215","article-title":"Degos-like lesions associated with systemic lupus erythematosus","volume":"29","author":"Jang","year":"2017","journal-title":"Ann Dermatol."},{"issue":"1","key":"10.1016\/j.anndiagpath.2022.151943_bb0095","doi-asserted-by":"crossref","first-page":"110","DOI":"10.1111\/bjd.12642","article-title":"Malignant and benign forms of atrophic papulosis (K\u00f6hlmeier-degos disease): systemic involvement determines the prognosis","volume":"170","author":"Theodoridis","year":"2014","journal-title":"Br J Dermatol"},{"issue":"8","key":"10.1016\/j.anndiagpath.2022.151943_bb0100","doi-asserted-by":"crossref","first-page":"185","DOI":"10.1186\/1750-1172-8-185","article-title":"The effects of eculizumab on the pathology of malignant atrophic papulosis","volume":"26","author":"Magro","year":"2013","journal-title":"Orphanet J Rare Dis"},{"issue":"3","key":"10.1016\/j.anndiagpath.2022.151943_bb0105","doi-asserted-by":"crossref","first-page":"1164","DOI":"10.1177\/147323001003800346","article-title":"Malignant atrophic papulosis with severe gastrointestinal perforation and omental necrosis: a case report","volume":"38","author":"Zheng","year":"2010","journal-title":"J Int Med Res"},{"issue":"7","key":"10.1016\/j.anndiagpath.2022.151943_bb0110","doi-asserted-by":"crossref","first-page":"1508","DOI":"10.1001\/jama.1968.03150070046007","article-title":"Disease (malignant papulosis). Report of three cases with clues to etiology","volume":"206","author":"Roenigk","year":"1968","journal-title":"JAMA"},{"issue":"5","key":"10.1016\/j.anndiagpath.2022.151943_bb0115","doi-asserted-by":"crossref","first-page":"609","DOI":"10.1097\/00007611-197805000-00039","article-title":"Calcific constrictive pericarditis in Degos' disease","volume":"71","author":"McLoud","year":"1978","journal-title":"South Med J"},{"issue":"1","key":"10.1016\/j.anndiagpath.2022.151943_bb0120","doi-asserted-by":"crossref","first-page":"79","DOI":"10.1378\/chest.73.1.79","article-title":"Intrathoracic manifestations of Degos' disease (malignant atrophic papulosis)","volume":"73","author":"Pierce","year":"1978","journal-title":"Chest"},{"issue":"1","key":"10.1016\/j.anndiagpath.2022.151943_bb0125","doi-asserted-by":"crossref","first-page":"84","DOI":"10.1046\/j.1365-2559.1996.t01-1-258289.x","article-title":"Malignant atrophic papulosis (Degos' disease) with extensive cardiopulmonary involvement","volume":"28","author":"Mauad","year":"1996","journal-title":"Histopathology"},{"issue":"6","key":"10.1016\/j.anndiagpath.2022.151943_bb0130","doi-asserted-by":"crossref","first-page":"464","DOI":"10.1253\/jcj.64.464","article-title":"Degos' disease with constrictive pericarditis: a case report","volume":"64","author":"Yukiiri","year":"2000","journal-title":"Jpn Circ J"},{"issue":"5","key":"10.1016\/j.anndiagpath.2022.151943_bb0135","doi-asserted-by":"crossref","first-page":"493","DOI":"10.1111\/j.1365-4632.2008.03394.x","article-title":"A case of Degos disease with pleuropericardial fibrosis, jejunal perforation, hemiparesis, and widespread cutaneous lesions","volume":"47","author":"Shahshahani","year":"2008","journal-title":"Int J Dermatol"},{"issue":"1","key":"10.1016\/j.anndiagpath.2022.151943_bb0140","first-page":"133","article-title":"Lethal systemic Degos disease with prominent cardio-pulmonary involvement","volume":"29","author":"Notash","year":"2008","journal-title":"Saudi Med J"},{"issue":"8","key":"10.1016\/j.anndiagpath.2022.151943_bb0145","doi-asserted-by":"crossref","first-page":"185","DOI":"10.1186\/1750-1172-8-185","article-title":"The effects of eculizumab on the pathology of malignant atrophic papulosis","volume":"26","author":"Magro","year":"2013","journal-title":"Orphanet J Rare Dis"},{"issue":"4","key":"10.1016\/j.anndiagpath.2022.151943_bb0150","doi-asserted-by":"crossref","first-page":"195","DOI":"10.1056\/NEJM196701262760402","article-title":"Progressive arterial occlusivedisease (K\u00f6hlmeier-Degos). A frequently fatal cutaneosystemic disorder","volume":"276","author":"Strole","year":"1967","journal-title":"N Engl J Med"},{"key":"10.1016\/j.anndiagpath.2022.151943_bb0155","doi-asserted-by":"crossref","first-page":"52","DOI":"10.1186\/1750-1172-8-52","article-title":"Effective treatment of malignantatrophic papulosis (K\u00f6hlmeier-Degos disease) with treprostinil-early experience","volume":"8","author":"Shapiro","year":"2013","journal-title":"Orphanet J Rare Dis"},{"issue":"12","key":"10.1016\/j.anndiagpath.2022.151943_bb0160","doi-asserted-by":"crossref","first-page":"2208","DOI":"10.1111\/jdv.15120","article-title":"CD34 stromal expression is inversely proportional to smooth muscle actin expression and extent of morphea","volume":"32","author":"Lee","year":"2018","journal-title":"J Eur Acad Dermatol Venereol"},{"issue":"4","key":"10.1016\/j.anndiagpath.2022.151943_bb0165","doi-asserted-by":"crossref","first-page":"599","DOI":"10.1309\/AJCP66QIMFARLZKI","article-title":"Degos disease: a C5b-9\/interferon-\u03b1-mediated endotheliopathy syndrome","volume":"135","author":"Magro","year":"2011","journal-title":"Am J Clin Pathol"},{"issue":"10","key":"10.1016\/j.anndiagpath.2022.151943_bb0170","doi-asserted-by":"crossref","first-page":"1777","DOI":"10.1084\/jem.191.10.1777","article-title":"Type I interferon as a powerful adjuvant for monocyte-derived dendritic cell development and activity in vitro and in hu-PBL-SCID mice","volume":"191","author":"Santini","year":"2000","journal-title":"J Exp Med"},{"issue":"1","key":"10.1016\/j.anndiagpath.2022.151943_bb0175","doi-asserted-by":"crossref","first-page":"369","DOI":"10.2353\/ajpath.2010.090545","article-title":"Cellular plasticity of inflammatory myeloid cells in the peritoneal foreign body response","volume":"176","author":"Mooney","year":"2010","journal-title":"Am J Pathol"},{"issue":"3","key":"10.1016\/j.anndiagpath.2022.151943_bb0180","doi-asserted-by":"crossref","DOI":"10.1371\/journal.pone.0033508","article-title":"Differentiation potential of CD14+ monocytes into myofibroblasts in patients with systemic sclerosis","volume":"7","author":"Binai","year":"2012","journal-title":"PLoS One"},{"issue":"1","key":"10.1016\/j.anndiagpath.2022.151943_bb0185","doi-asserted-by":"crossref","first-page":"56","DOI":"10.1186\/s12931-020-1319-0","article-title":"TGF-\u03b2 pathway activation by idiopathic pulmonary fibrosis (IPF) fibroblast derived soluble factors is mediated by IL-6 trans-signaling","volume":"21","author":"Epstein Shochet","year":"2020","journal-title":"Respir Res"},{"issue":"4","key":"10.1016\/j.anndiagpath.2022.151943_bb0190","doi-asserted-by":"crossref","first-page":"319","DOI":"10.1080\/15384101.2016.1259037","article-title":"STAT3-mediated SMAD3 activation underlies Oncostatin M-induced senescence","volume":"16","author":"Bryson","year":"2017","journal-title":"Cell Cycle"},{"issue":"14","key":"10.1016\/j.anndiagpath.2022.151943_bb0195","doi-asserted-by":"crossref","first-page":"9952","DOI":"10.1074\/jbc.M113.545822","article-title":"Interleukin-6 (IL-6) trans signaling drives a STAT3-dependent pathway that leads to hyperactive transforming growth factor-\u03b2 (TGF-\u03b2) signaling promoting SMAD3 activation and fibrosis via Gremlin protein","volume":"289","author":"O'Reilly","year":"2014","journal-title":"J. Biol. Chem."},{"issue":"8","key":"10.1016\/j.anndiagpath.2022.151943_bb0200","doi-asserted-by":"crossref","first-page":"869","DOI":"10.1016\/j.molimm.2004.11.008","article-title":"Type I interferons and the innate immune response--more than just antiviral cytokines","volume":"42","author":"Smith","year":"2005","journal-title":"Mol Immunol"}],"container-title":["Annals of Diagnostic Pathology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1092913422000454?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1092913422000454?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2025,10,21]],"date-time":"2025-10-21T20:35:18Z","timestamp":1761078918000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S1092913422000454"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2022,8]]},"references-count":40,"alternative-id":["S1092913422000454"],"URL":"https:\/\/doi.org\/10.1016\/j.anndiagpath.2022.151943","relation":{},"ISSN":["1092-9134"],"issn-type":[{"value":"1092-9134","type":"print"}],"subject":[],"published":{"date-parts":[[2022,8]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"Exploring the pathophysiologic basis of constrictive pericarditis of Kohlmeier Degos disease: A case series and review of the literature","name":"articletitle","label":"Article Title"},{"value":"Annals of Diagnostic Pathology","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.anndiagpath.2022.151943","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"Published by Elsevier Inc.","name":"copyright","label":"Copyright"}],"article-number":"151943"}}