{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,2]],"date-time":"2026-10-02T17:31:00Z","timestamp":1790962260219,"version":"4.1.0"},"reference-count":36,"publisher":"Elsevier BV","license":[{"start":{"date-parts":[[2026,6,1]],"date-time":"2026-06-01T00:00:00Z","timestamp":1780272000000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2026,6,1]],"date-time":"2026-06-01T00:00:00Z","timestamp":1780272000000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/legal\/tdmrep-license"},{"start":{"date-parts":[[2026,6,1]],"date-time":"2026-06-01T00:00:00Z","timestamp":1780272000000},"content-version":"stm-asf","delay-in-days":0,"URL":"https:\/\/doi.org\/10.15223\/policy-017"},{"start":{"date-parts":[[2026,6,1]],"date-time":"2026-06-01T00:00:00Z","timestamp":1780272000000},"content-version":"stm-asf","delay-in-days":0,"URL":"https:\/\/doi.org\/10.15223\/policy-037"},{"start":{"date-parts":[[2026,6,1]],"date-time":"2026-06-01T00:00:00Z","timestamp":1780272000000},"content-version":"stm-asf","delay-in-days":0,"URL":"https:\/\/doi.org\/10.15223\/policy-012"},{"start":{"date-parts":[[2026,6,1]],"date-time":"2026-06-01T00:00:00Z","timestamp":1780272000000},"content-version":"stm-asf","delay-in-days":0,"URL":"https:\/\/doi.org\/10.15223\/policy-029"},{"start":{"date-parts":[[2026,6,1]],"date-time":"2026-06-01T00:00:00Z","timestamp":1780272000000},"content-version":"stm-asf","delay-in-days":0,"URL":"https:\/\/doi.org\/10.15223\/policy-004"}],"content-domain":{"domain":["annalsofvascularsurgery.com","clinicalkey.com","clinicalkey.com.au","clinicalkey.es","clinicalkey.fr","clinicalkey.jp","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Annals of Vascular Surgery"],"published-print":{"date-parts":[[2026,6]]},"DOI":"10.1016\/j.avsg.2026.01.032","type":"journal-article","created":{"date-parts":[[2026,2,3]],"date-time":"2026-02-03T07:45:14Z","timestamp":1770104714000},"page":"109-117","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":1,"special_numbering":"C","title":["Contemporary Outcomes of Thoracic Endovascular Aortic Repair in Patients with Syndromic Genetic Aortopathy: A Multi-Centre National Study"],"prefix":"10.1016","volume":"127","author":[{"given":"Daniel","family":"Willie-Permor","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0009-0005-0844-0195","authenticated-orcid":false,"given":"Narek","family":"Veranyan","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ahmed","family":"Abdelkarim","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Sabrina","family":"Straus","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Shima","family":"Rahgozar","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Hannah","family":"Wellington","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Sherene","family":"Shalhub","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mahmoud B.","family":"Malas","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"key":"10.1016\/j.avsg.2026.01.032_bib1","doi-asserted-by":"crossref","first-page":"1729","DOI":"10.1056\/NEJM199412293312601","article-title":"Transluminal placement of endovascular stent-grafts for the treatment of descending thoracic aortic aneurysms","volume":"331","author":"Dake","year":"1994","journal-title":"NEJM"},{"key":"10.1016\/j.avsg.2026.01.032_bib2","doi-asserted-by":"crossref","first-page":"369","DOI":"10.1016\/j.jtcvs.2006.07.040","article-title":"Endovascular stent grafting versus open surgical repair of descending thoracic aortic aneurysms in low-risk patients: a multicenter comparative trial","volume":"133","author":"Bavaria","year":"2007","journal-title":"J Thorac Cardiovasc Surg"},{"key":"10.1016\/j.avsg.2026.01.032_bib3","doi-asserted-by":"crossref","first-page":"49","DOI":"10.1055\/s-0040-1714089","article-title":"Complications and management of the thoracic endovascular aortic repair","volume":"8","author":"Chen","year":"2020","journal-title":"Aorta (Stamford)"},{"key":"10.1016\/j.avsg.2026.01.032_bib4","doi-asserted-by":"crossref","first-page":"e150","DOI":"10.1161\/01.CIR.0000155243.70456.F4","article-title":"Treatment of aortic disease in patients with Marfan syndrome","volume":"111","author":"Milewicz","year":"2005","journal-title":"Circ"},{"key":"10.1016\/j.avsg.2026.01.032_bib5","doi-asserted-by":"crossref","first-page":"159","DOI":"10.3390\/diseases3030159","article-title":"Endovascular repair of aortic dissection in Marfan Syndrome: current status and future perspectives","volume":"3","author":"Parisi","year":"2015","journal-title":"Diseases"},{"key":"10.1016\/j.avsg.2026.01.032_bib6","doi-asserted-by":"crossref","first-page":"104","DOI":"10.1006\/jmbi.1996.0237","article-title":"Fibrillin-1: organization in microfibrils and structural properties","volume":"258","author":"Reinhardt","year":"1996","journal-title":"J Mol Biol"},{"key":"10.1016\/j.avsg.2026.01.032_bib7","doi-asserted-by":"crossref","first-page":"717","DOI":"10.1097\/GIM.0b013e3182180c89","article-title":"COL3A1 haploinsufficiency results in a variety of Ehlers-Danlos syndrome type IV with delayed onset of complications and longer life expectancy","volume":"13","author":"Leistritz","year":"2011","journal-title":"Genet Med"},{"key":"10.1016\/j.avsg.2026.01.032_bib8","doi-asserted-by":"crossref","first-page":"1965","DOI":"10.1016\/S0140-6736(05)67789-6","article-title":"Marfan\u2019s syndrome","volume":"366","author":"Judge","year":"2005","journal-title":"Lancet"},{"key":"10.1016\/j.avsg.2026.01.032_bib9","doi-asserted-by":"crossref","first-page":"E334","DOI":"10.1161\/CIR.0000000000001106","article-title":"2022 ACC\/AHA Guideline for the diagnosis and management of aortic disease: a report of the American heart Association\/American College of Cardiology Joint Committee on clinical practice Guidelines","volume":"146","author":"Isselbacher","year":"2022","journal-title":"Circ"},{"key":"10.1016\/j.avsg.2026.01.032_bib10","doi-asserted-by":"crossref","first-page":"1234","DOI":"10.1016\/j.jvs.2011.11.089","article-title":"Endovascular treatment of acute and chronic aortic pathology in patients with Marfan syndrome","volume":"55","author":"Waterman","year":"2012","journal-title":"J Vasc Surg"},{"key":"10.1016\/j.avsg.2026.01.032_bib11","doi-asserted-by":"crossref","first-page":"144","DOI":"10.1583\/07-2286.1","article-title":"Thoracic aortic endografting in patients with connective tissue diseases","volume":"15","author":"Geisb\u00fcsch","year":"2008","journal-title":"J Endovasc Ther"},{"key":"10.1016\/j.avsg.2026.01.032_bib12","doi-asserted-by":"crossref","first-page":"141","DOI":"10.1055\/s-0042-1749171","article-title":"Retrograde type A aortic dissection 48 hours after TEVAR in a patient with a delayed diagnosis of vascular Ehlers-Danlos Syndrome","volume":"10","author":"Diebels","year":"2022","journal-title":"Aorta (Stamford)"},{"key":"10.1016\/j.avsg.2026.01.032_bib13","doi-asserted-by":"crossref","first-page":"173","DOI":"10.1136\/hrt.2008.160515","article-title":"Marfan syndrome: 30 years of research equals 30 years of additional life expectancy","volume":"95","author":"Pyeritz","year":"2009","journal-title":"Heart"},{"key":"10.1016\/j.avsg.2026.01.032_bib14","doi-asserted-by":"crossref","first-page":"977","DOI":"10.21470\/1678-9741-2019-0367","article-title":"The role of thoracic endovascular aortic repair (TEVAR) of thoracic aortic diseases in patients with connective tissue disorders \u2013 a literature review","volume":"35","author":"Harky","year":"2020","journal-title":"Braz J Cardiovasc Surg"},{"key":"10.1016\/j.avsg.2026.01.032_bib16","doi-asserted-by":"crossref","first-page":"676","DOI":"10.1177\/1538574420945070","article-title":"Outcomes of thoracic endovascular aneurysm repair (TEVAR) in patients with connective tissue disorders","volume":"54","author":"Qato","year":"2020","journal-title":"Vasc Endovasc Surg"},{"key":"10.1016\/j.avsg.2026.01.032_bib17","doi-asserted-by":"crossref","first-page":"364","DOI":"10.1016\/j.jvs.2017.11.095","article-title":"Endovascular thoracic aortic repair in confirmed or suspected genetically triggered thoracic aortic dissection","volume":"68","author":"Shalhub","year":"2018","journal-title":"J Vasc Surg"},{"key":"10.1016\/j.avsg.2026.01.032_bib18","doi-asserted-by":"crossref","first-page":"1108","DOI":"10.1016\/j.jtcvs.2009.03.014","article-title":"Stent graft repair of descending aortic dissection in patients with Marfan syndrome: an effective alternative to open reoperation?","volume":"138","author":"Botta","year":"2009","journal-title":"J Thorac Cardiovasc Surg"},{"key":"10.1016\/j.avsg.2026.01.032_bib19","doi-asserted-by":"crossref","first-page":"82","DOI":"10.1583\/04-1415MR.1","article-title":"Stent-grafts in patients with Marfan syndrome","volume":"12","author":"Ince","year":"2005","journal-title":"J Endovasc Ther"},{"key":"10.1016\/j.avsg.2026.01.032_bib20","doi-asserted-by":"crossref","first-page":"375","DOI":"10.1007\/s10140-008-0759-5","article-title":"Emergency stent grafting of type B aortic dissection: technical considerations","volume":"15","author":"Lupattelli","year":"2008","journal-title":"Emerg Radiol"},{"key":"10.1016\/j.avsg.2026.01.032_bib21","doi-asserted-by":"crossref","first-page":"190","DOI":"10.1016\/j.jvs.2009.01.045","article-title":"Proximal aortic perforation after endovascular repair of a type B dissection in a patient with Marfan syndrome","volume":"50","author":"van Keulen","year":"2009","journal-title":"J Vasc Surg"},{"key":"10.1016\/j.avsg.2026.01.032_bib22","doi-asserted-by":"crossref","first-page":"1541","DOI":"10.1016\/S0022-5223(02)73606-4","article-title":"Stent graft placement of the thoracoabdominal aorta in a patient with Marfan syndrome","volume":"125","author":"Fleck","year":"2003","journal-title":"J Thorac Cardiovasc Surg"},{"key":"10.1016\/j.avsg.2026.01.032_bib23","doi-asserted-by":"crossref","first-page":"608","DOI":"10.1016\/j.ejvs.2009.07.009","article-title":"Successful endovascular repair of acute type B aortic dissection in undiagnosed Ehlers-Danlos Syndrome type IV","volume":"38","author":"Khalique","year":"2009","journal-title":"Eur J Vasc Endovasc Surg"},{"key":"10.1016\/j.avsg.2026.01.032_bib24","doi-asserted-by":"crossref","first-page":"2091","DOI":"10.1161\/CIRCULATIONAHA.120.051171","article-title":"Extracellular tuning of mitochondrial respiration leads to aortic aneurysm","volume":"143","author":"Oller","year":"2021","journal-title":"Circ"},{"key":"10.1016\/j.avsg.2026.01.032_bib25","series-title":"Mechanisms of Vascular Disease: A Reference Book for Vascular Specialists, South Australia: The University of Adelaide","first-page":"255","article-title":"Pathophysiology of aortic dissection and connective tissue disorders","author":"Hamilton","year":"2011"},{"key":"10.1016\/j.avsg.2026.01.032_bib26","doi-asserted-by":"crossref","first-page":"804","DOI":"10.1056\/NEJM197204132861502","article-title":"Life expectancy and causes of death in the Marfan syndrome","volume":"286","author":"Murdoch","year":"1972","journal-title":"NEJM"},{"key":"10.1016\/j.avsg.2026.01.032_bib27","doi-asserted-by":"crossref","first-page":"1406","DOI":"10.1016\/j.jvs.2017.03.451","article-title":"A 10-year institutional experience with open branched graft reconstruction of aortic aneurysms in connective tissue disorders versus degenerative disease","volume":"66","author":"Hicks","year":"2017","journal-title":"J Vasc Surg"},{"key":"10.1016\/j.avsg.2026.01.032_bib28","doi-asserted-by":"crossref","first-page":"59","DOI":"10.2147\/vhrm.2008.04.01.59","article-title":"Current role of endovascular therapy in Marfan patients with previous aortic surgery","volume":"4","author":"Akin","year":"2008","journal-title":"Vasc Health Risk Manag"},{"key":"10.1016\/j.avsg.2026.01.032_bib29","doi-asserted-by":"crossref","first-page":"1257","DOI":"10.1016\/j.jvs.2018.06.199","article-title":"Treatment of thoracoabdominal aortic disease in patients with connective tissue disorders","volume":"68","author":"Glebova","year":"2018","journal-title":"J Vasc Surg"},{"key":"10.1016\/j.avsg.2026.01.032_bib30","doi-asserted-by":"crossref","first-page":"1083","DOI":"10.1111\/jocs.15340","article-title":"Thoracic aortic aneurysms in patients with heritable connective tissue disease","volume":"36","author":"Odofin","year":"2021","journal-title":"J Card Surg"},{"key":"10.1016\/j.avsg.2026.01.032_bib31","first-page":"518","article-title":"Aortic treatment in connective tissue disease","volume":"60","author":"Tinelli","year":"2019","journal-title":"J Cardiovasc Surg (Torino)"},{"key":"10.1016\/j.avsg.2026.01.032_bib32","doi-asserted-by":"crossref","first-page":"60","DOI":"10.1583\/08-2561.1","article-title":"Treating the thoracic aorta in Marfan syndrome: surgery or TEVAR?","volume":"16","author":"Cooper","year":"2009","journal-title":"J Endovasc Ther"},{"key":"10.1016\/j.avsg.2026.01.032_bib33","doi-asserted-by":"crossref","first-page":"S1877","DOI":"10.1016\/S0003-4975(02)04147-4","article-title":"Natural history of thoracic aortic aneurysms: indications for surgery, and surgical versus nonsurgical risks","volume":"74","author":"Elefteriades","year":"2002","journal-title":"Ann Thorac Surg"},{"key":"10.1016\/j.avsg.2026.01.032_bib34","doi-asserted-by":"crossref","first-page":"1","DOI":"10.1186\/s13019-017-0663-8","article-title":"Impact of connective tissue disease on the surgical outcomes of aortic dissection in patients with cystic medial necrosis","volume":"12","author":"Fujiyoshi","year":"2017","journal-title":"J Cardiothorac Surg"},{"key":"10.1016\/j.avsg.2026.01.032_bib35","doi-asserted-by":"crossref","first-page":"144","DOI":"10.1016\/j.ejvs.2014.05.011","article-title":"Total endovascular treatment of an aortic arch aneurysm in a patient with a mechanical aortic valve","volume":"48","author":"Spear","year":"2014","journal-title":"Eur J Vasc Endovasc Surg"},{"key":"10.1016\/j.avsg.2026.01.032_bib36","doi-asserted-by":"crossref","first-page":"158","DOI":"10.1016\/j.avsg.2017.05.013","article-title":"Endovascular repair of thoracoabdominal and arch aneurysms in patients with connective tissue disease using branched and fenestrated devices","volume":"44","author":"Clough","year":"2017","journal-title":"Ann Vasc Surg"},{"key":"10.1016\/j.avsg.2026.01.032_bib37","doi-asserted-by":"crossref","first-page":"8","DOI":"10.1002\/ajmg.c.31552","article-title":"The 2017 international classification of the Ehlers\u2013Danlos syndromes","volume":"175","author":"Malfait","year":"2017","journal-title":"Am J Med Genet C Semin Med Genet"}],"container-title":["Annals of Vascular Surgery"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0890509626000592?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0890509626000592?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2026,4,4]],"date-time":"2026-04-04T14:53:26Z","timestamp":1775314406000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0890509626000592"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2026,6]]},"references-count":36,"alternative-id":["S0890509626000592"],"URL":"https:\/\/doi.org\/10.1016\/j.avsg.2026.01.032","relation":{},"ISSN":["0890-5096"],"issn-type":[{"value":"0890-5096","type":"print"}],"subject":[],"published":{"date-parts":[[2026,6]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"Contemporary Outcomes of Thoracic Endovascular Aortic Repair in Patients with Syndromic Genetic Aortopathy: A Multi-Centre National Study","name":"articletitle","label":"Article Title"},{"value":"Annals of Vascular Surgery","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.avsg.2026.01.032","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"\u00a9 2026 Elsevier Inc. All rights are reserved, including those for text and data mining, AI training, and similar technologies.","name":"copyright","label":"Copyright"}]}}