{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,10,11]],"date-time":"2025-10-11T01:54:18Z","timestamp":1760147658216},"reference-count":9,"publisher":"Elsevier BV","issue":"9","license":[{"start":{"date-parts":[[2019,10,1]],"date-time":"2019-10-01T00:00:00Z","timestamp":1569888000000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"}],"content-domain":{"domain":["clinicalkey.jp","clinicalkey.com","clinicalkey.es","clinicalkey.com.au","clinicalkey.fr","brainanddevelopment.com","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Brain and Development"],"published-print":{"date-parts":[[2019,10]]},"DOI":"10.1016\/j.braindev.2019.05.001","type":"journal-article","created":{"date-parts":[[2019,5,21]],"date-time":"2019-05-21T01:55:51Z","timestamp":1558403751000},"page":"817-819","update-policy":"http:\/\/dx.doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":8,"title":["Perampanel attenuates myoclonus in a patient with neuronal ceroid lipofuscinoses type 2 disease"],"prefix":"10.1016","volume":"41","author":[{"given":"Lee Chin","family":"Wong","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Chia-Jui","family":"Hsu","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Wang-Tso","family":"Lee","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"78","reference":[{"key":"10.1016\/j.braindev.2019.05.001_b0005","doi-asserted-by":"crossref","first-page":"160","DOI":"10.1016\/j.ymgme.2016.07.011","article-title":"Diagnosis of neuronal ceroid lipofuscinosis type 2 (CLN2 disease): expert recommendations for early detection and laboratory diagnosis","volume":"119","author":"Fietz","year":"2016","journal-title":"Mol Genet Metab"},{"key":"10.1016\/j.braindev.2019.05.001_b0010","doi-asserted-by":"crossref","first-page":"1898","DOI":"10.1056\/NEJMoa1712649","article-title":"Study of intraventricular cerliponase alfa for CLN2 disease","volume":"378","author":"Schulz","year":"2018","journal-title":"N Engl J Med"},{"key":"10.1016\/j.braindev.2019.05.001_b0015","doi-asserted-by":"crossref","first-page":"102","DOI":"10.1016\/j.pediatrneurol.2017.01.034","article-title":"Management strategies for CLN2 disease","volume":"69","author":"Williams","year":"2017","journal-title":"Pediatr Neurol"},{"key":"10.1016\/j.braindev.2019.05.001_b0020","doi-asserted-by":"crossref","first-page":"1085","DOI":"10.1007\/s40263-012-0021-2","article-title":"Perampanel: as adjunctive therapy in patients with partial-onset seizures","volume":"26","author":"Plosker","year":"2012","journal-title":"CNS Drugs"},{"key":"10.1016\/j.braindev.2019.05.001_b0025","doi-asserted-by":"crossref","first-page":"1657","DOI":"10.1007\/s40265-015-0465-z","article-title":"Perampanel: a review in drug-resistant epilepsy","volume":"75","author":"Frampton","year":"2015","journal-title":"Drugs"},{"key":"10.1016\/j.braindev.2019.05.001_b0030","doi-asserted-by":"crossref","first-page":"543","DOI":"10.1111\/epi.13662","article-title":"Perampanel in 12 patients with Unverricht-Lundborg disease","volume":"58","author":"Crespel","year":"2017","journal-title":"Epilepsia"},{"key":"10.1016\/j.braindev.2019.05.001_b0035","doi-asserted-by":"crossref","first-page":"132","DOI":"10.1016\/j.yebeh.2016.06.041","article-title":"Efficacy and tolerability of perampanel in ten patients with Lafora disease","volume":"62","author":"Goldsmith","year":"2016","journal-title":"Epilepsy Behav"},{"key":"10.1016\/j.braindev.2019.05.001_b0040","doi-asserted-by":"crossref","first-page":"32","DOI":"10.1016\/j.ebcr.2018.02.005","article-title":"Seizure remission and improvement of neurological function in sialidosis with perampanel therapy","volume":"10","author":"Hu","year":"2018","journal-title":"Epilepsy Behav Case Rep"},{"key":"10.1016\/j.braindev.2019.05.001_b0045","doi-asserted-by":"crossref","first-page":"164","DOI":"10.1016\/j.ebcr.2014.09.003","article-title":"Seizure control and improvement of neurological dysfunction in Lafora disease with perampanel","volume":"2","author":"Dirani","year":"2014","journal-title":"Epilepsy Behav Case Rep"}],"container-title":["Brain and Development"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0387760419302001?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0387760419302001?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2019,8,27]],"date-time":"2019-08-27T17:10:17Z","timestamp":1566925817000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0387760419302001"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2019,10]]},"references-count":9,"journal-issue":{"issue":"9","published-print":{"date-parts":[[2019,10]]}},"alternative-id":["S0387760419302001"],"URL":"https:\/\/doi.org\/10.1016\/j.braindev.2019.05.001","relation":{},"ISSN":["0387-7604"],"issn-type":[{"value":"0387-7604","type":"print"}],"subject":[],"published":{"date-parts":[[2019,10]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"Perampanel attenuates myoclonus in a patient with neuronal ceroid lipofuscinoses type 2 disease","name":"articletitle","label":"Article Title"},{"value":"Brain and Development","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.braindev.2019.05.001","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"\u00a9 2019 The Japanese Society of Child Neurology. Published by Elsevier B.V. All rights reserved.","name":"copyright","label":"Copyright"}]}}