{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,6,3]],"date-time":"2026-06-03T19:12:52Z","timestamp":1780513972960,"version":"3.54.1"},"reference-count":62,"publisher":"Elsevier BV","license":[{"start":{"date-parts":[[2021,2,1]],"date-time":"2021-02-01T00:00:00Z","timestamp":1612137600000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2021,2,1]],"date-time":"2021-02-01T00:00:00Z","timestamp":1612137600000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/legal\/tdmrep-license"},{"start":{"date-parts":[[2021,10,22]],"date-time":"2021-10-22T00:00:00Z","timestamp":1634860800000},"content-version":"am","delay-in-days":263,"URL":"http:\/\/www.elsevier.com\/open-access\/userlicense\/1.0\/"}],"funder":[{"name":"French association Vaincre les Maladies Lysosomales"},{"DOI":"10.13039\/501100001677","name":"Institut National de la Sant\u00e9 et de la Recherche M\u00e9dicale","doi-asserted-by":"crossref","id":[{"id":"10.13039\/501100001677","id-type":"DOI","asserted-by":"crossref"}]},{"name":"University of Tours and GagoSciences (Structure, function and regulation of glycosaminoglycans","award":["GDR 3739"],"award-info":[{"award-number":["GDR 3739"]}]},{"DOI":"10.13039\/501100004794","name":"Centre National de la Recherche Scientifique)","doi-asserted-by":"publisher","id":[{"id":"10.13039\/501100004794","id-type":"DOI","asserted-by":"publisher"}]},{"name":"Faculty of Chemistry, University of Gda\u0144sk","award":["BMN-538-8370-B249-18"],"award-info":[{"award-number":["BMN-538-8370-B249-18"]}]},{"DOI":"10.13039\/501100004281","name":"National Science Centre of Poland","doi-asserted-by":"crossref","award":["UMO-2018\/31\/N\/ST4\/01677"],"award-info":[{"award-number":["UMO-2018\/31\/N\/ST4\/01677"]}],"id":[{"id":"10.13039\/501100004281","id-type":"DOI","asserted-by":"crossref"}]},{"DOI":"10.13039\/501100004281","name":"National Science Centre of Poland","doi-asserted-by":"crossref","award":["2018\/30\/E\/ST4\/00037"],"award-info":[{"award-number":["2018\/30\/E\/ST4\/00037"]}],"id":[{"id":"10.13039\/501100004281","id-type":"DOI","asserted-by":"crossref"}]}],"content-domain":{"domain":["elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Carbohydrate Polymers"],"published-print":{"date-parts":[[2021,2]]},"DOI":"10.1016\/j.carbpol.2020.117261","type":"journal-article","created":{"date-parts":[[2020,10,20]],"date-time":"2020-10-20T01:06:47Z","timestamp":1603156007000},"page":"117261","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":22,"special_numbering":"C","title":["The abnormal accumulation of heparan sulfate in patients with mucopolysaccharidosis prevents the elastolytic activity of cathepsin V"],"prefix":"10.1016","volume":"253","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-2224-9582","authenticated-orcid":false,"given":"Thibault","family":"Chazeirat","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Sophie","family":"Denamur","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Krzysztof K.","family":"Bojarski","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Pierre-Marie","family":"Andrault","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Damien","family":"Sizaret","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Fuming","family":"Zhang","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ahlame","family":"Saidi","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Marine","family":"Tardieu","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Robert J.","family":"Linhardt","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Fran\u00e7ois","family":"Labarthe","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Dieter","family":"Br\u00f6mme","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Sergey A.","family":"Samsonov","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-8562-4821","authenticated-orcid":false,"given":"Gilles","family":"Lalmanach","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-1060-4222","authenticated-orcid":false,"given":"Fabien","family":"Lecaille","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"issue":"10","key":"10.1016\/j.carbpol.2020.117261_bib0005","first-page":"8","article-title":"Isolation and characterization of human cathepsin V: A major proteinase in corneal Epithelium","volume":"39","author":"Adachi","year":"1998","journal-title":"Investigate Ophtalmology and Visual Science"},{"issue":"3","key":"10.1016\/j.carbpol.2020.117261_bib0010","doi-asserted-by":"crossref","first-page":"198","DOI":"10.1177\/0003489414550154","article-title":"Airway-related symptoms and surgeries in patients with mucopolysaccharidosis I","volume":"124","author":"Arn","year":"2015","journal-title":"The Annals of Otology, Rhinology, and Laryngology"},{"key":"10.1016\/j.carbpol.2020.117261_bib0015","doi-asserted-by":"crossref","first-page":"45","DOI":"10.1016\/j.carpath.2017.01.001","article-title":"Progressive heart disease in mucopolysaccharidosis type I mice may be mediated by increased cathepsin B activity","volume":"27","author":"Baldo","year":"2017","journal-title":"Cardiovascular Pathology"},{"issue":"9","key":"10.1016\/j.carbpol.2020.117261_bib0020","doi-asserted-by":"crossref","first-page":"647","DOI":"10.1093\/glycob\/cwg082","article-title":"Improved and simple micro assay for sulfated glycosaminoglycans quantification in biological extracts and its use in skin and muscle tissue studies","volume":"13","author":"Barbosa","year":"2003","journal-title":"Glycobiology"},{"issue":"1","key":"10.1016\/j.carbpol.2020.117261_bib0025","doi-asserted-by":"crossref","first-page":"189","DOI":"10.1042\/bj2010189","article-title":"L-trans-Epoxysuccinyl-leucylamido(4-guanidino)butane (E-64) and its analogues as inhibitors of cysteine proteinases including cathepsins B, H and L","volume":"201","author":"Barrett","year":"1982","journal-title":"The Biochemical Journal"},{"issue":"8","key":"10.1016\/j.carbpol.2020.117261_bib0030","doi-asserted-by":"crossref","first-page":"1258","DOI":"10.1016\/j.febslet.2013.02.035","article-title":"Extracellular matrix components: an intricate network of possible biomarkers for lysosomal storage disorders?","volume":"587","author":"Batzios","year":"2013","journal-title":"FEBS Letters"},{"issue":"2","key":"10.1016\/j.carbpol.2020.117261_bib0035","doi-asserted-by":"crossref","first-page":"201","DOI":"10.1007\/s10545-012-9555-1","article-title":"Respiratory and sleep disorders in mucopolysaccharidosis","volume":"36","author":"Berger","year":"2013","journal-title":"Journal of Inherited Metabolic Disease"},{"key":"10.1016\/j.carbpol.2020.117261_bib0040","doi-asserted-by":"crossref","first-page":"23","DOI":"10.1007\/978-3-642-16861-1_2","article-title":"Role of cysteine cathepsins in extracellular proteolysis","author":"Br\u00f6mme","year":"2011","journal-title":"Extracellular Matrix Degradation"},{"issue":"8","key":"10.1016\/j.carbpol.2020.117261_bib0045","doi-asserted-by":"crossref","first-page":"2377","DOI":"10.1021\/bi982175f","article-title":"Human cathepsin V functional expression, tissue distribution, electrostatic surface potential, enzymatic characterization, and chromosomal localization","volume":"38","author":"Br\u00f6mme","year":"1999","journal-title":"Biochemistry"},{"issue":"6","key":"10.1016\/j.carbpol.2020.117261_bib0050","doi-asserted-by":"crossref","first-page":"2203","DOI":"10.1016\/S0002-9440(10)63777-7","article-title":"Pivotal role of cathepsin K in lung fibrosis","volume":"164","author":"B\u00fchling","year":"2004","journal-title":"The American Journal of Pathology"},{"key":"10.1016\/j.carbpol.2020.117261_bib0055","series-title":"Amber 2017","author":"Case","year":"2017"},{"issue":"18","key":"10.1016\/j.carbpol.2020.117261_bib0060","doi-asserted-by":"crossref","first-page":"12824","DOI":"10.1074\/jbc.M513331200","article-title":"Substrate profiling of cysteine proteases using a combinatorial peptide library identifies functionally unique specificities","volume":"281","author":"Choe","year":"2006","journal-title":"The Journal of Biological Chemistry"},{"issue":"24","key":"10.1016\/j.carbpol.2020.117261_bib0065","doi-asserted-by":"crossref","first-page":"5321","DOI":"10.1021\/jm020238t","article-title":"Design of noncovalent inhibitors of human cathepsin L. From the 96-residue proregion to optimized tripeptides","volume":"45","author":"Chowdhury","year":"2002","journal-title":"Journal of Medicinal Chemistry"},{"issue":"2","key":"10.1016\/j.carbpol.2020.117261_bib0070","doi-asserted-by":"crossref","first-page":"181","DOI":"10.1016\/j.ymgme.2006.08.001","article-title":"Effect of neonatal administration of a retroviral vector expressing \u03b1-l-iduronidase upon lysosomal storage in brain and other organs in mucopolysaccharidosis I mice","volume":"90","author":"Chung","year":"2007","journal-title":"Molecular Genetics and Metabolism"},{"issue":"S2","key":"10.1016\/j.carbpol.2020.117261_bib0075","doi-asserted-by":"crossref","DOI":"10.1186\/s13052-018-0562-1","article-title":"Enzyme replacement therapy: Efficacy and limitations","volume":"44","author":"Concolino","year":"2018","journal-title":"Italian Journal of Pediatrics"},{"issue":"11","key":"10.1016\/j.carbpol.2020.117261_bib0080","doi-asserted-by":"crossref","first-page":"165539","DOI":"10.1016\/j.bbadis.2019.165539","article-title":"Heparan sulfate proteoglycans: The sweet side of development turns sour in mucopolysaccharidoses","volume":"1865","author":"De Pasquale","year":"2019","journal-title":"Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease"},{"issue":"4","key":"10.1016\/j.carbpol.2020.117261_bib0085","doi-asserted-by":"crossref","first-page":"979","DOI":"10.3390\/cells9040979","article-title":"Cathepsins in the pathophysiology of mucopolysaccharidoses: New perspectives for therapy","volume":"9","author":"De Pasquale","year":"2020","journal-title":"Cells"},{"key":"10.1016\/j.carbpol.2020.117261_bib0090","doi-asserted-by":"crossref","first-page":"8","DOI":"10.1016\/j.omtm.2018.05.002","article-title":"Targeting heparan sulfate proteoglycans as a novel therapeutic strategy for mucopolysaccharidoses","volume":"10","author":"De Pasquale","year":"2018","journal-title":"Molecular Therapy - Methods & Clinical Development"},{"issue":"48","key":"10.1016\/j.carbpol.2020.117261_bib0095","doi-asserted-by":"crossref","first-page":"34871","DOI":"10.1074\/jbc.M113.510008","article-title":"Elastin degradation by cathepsin V requires two exosites","volume":"288","author":"Du","year":"2013","journal-title":"The Journal of Biological Chemistry"},{"issue":"5","key":"10.1016\/j.carbpol.2020.117261_bib0100","doi-asserted-by":"crossref","first-page":"443","DOI":"10.1093\/glycob\/cwh049","article-title":"Glycosaminoglycan degradation fragments in mucopolysaccharidosis I","volume":"14","author":"Fuller","year":"2004","journal-title":"Glycobiology"},{"key":"10.1016\/j.carbpol.2020.117261_bib0105","doi-asserted-by":"crossref","first-page":"102","DOI":"10.1016\/j.lfs.2018.01.020","article-title":"Cathepsin B inhibition attenuates cardiovascular pathology in mucopolysaccharidosis I mice","volume":"196","author":"Gonzalez","year":"2018","journal-title":"Life Sciences"},{"key":"10.1016\/j.carbpol.2020.117261_bib0110","doi-asserted-by":"crossref","first-page":"285","DOI":"10.1016\/j.matbio.2016.09.003","article-title":"A current view of perlecan in physiology and pathology: A mosaic of functions","volume":"57\u201358","author":"Gubbiotti","year":"2017","journal-title":"Matrix Biology"},{"key":"10.1016\/j.carbpol.2020.117261_bib0115","doi-asserted-by":"crossref","first-page":"119","DOI":"10.1007\/8904_2013_213","article-title":"Fatal and unanticipated cardiorespiratory disease in a two-year-old child with Hurler syndrome following successful stem cell transplant","volume":"7","author":"Gupta","year":"2013","journal-title":"JIMD Reports"},{"issue":"2","key":"10.1016\/j.carbpol.2020.117261_bib0120","doi-asserted-by":"crossref","first-page":"112","DOI":"10.1177\/030098589202900203","article-title":"Hepatic storage of glycosaminoglycans in feline and canine models of mucopolysaccharidoses I, VI, and VII","volume":"29","author":"Haskins","year":"1992","journal-title":"Veterinary Pathology"},{"issue":"1","key":"10.1016\/j.carbpol.2020.117261_bib0125","doi-asserted-by":"crossref","first-page":"33","DOI":"10.1016\/0263-7855(96)00018-5","article-title":"VMD: Visual molecular dynamics","volume":"14","author":"Humphrey","year":"1996","journal-title":"Journal of Molecular Graphics"},{"key":"10.1016\/j.carbpol.2020.117261_bib0130","doi-asserted-by":"crossref","first-page":"1","DOI":"10.1016\/j.matbio.2018.03.023","article-title":"Extracellular matrix: The driving force of mammalian diseases","volume":"71\u201372","author":"Iozzo","year":"2018","journal-title":"Matrix Biology"},{"issue":"4","key":"10.1016\/j.carbpol.2020.117261_bib0135","doi-asserted-by":"crossref","first-page":"622","DOI":"10.1002\/jcc.20820","article-title":"GLYCAM06: A generalizable biomolecular force field. Carbohydrates","volume":"29","author":"Kirschner","year":"2008","journal-title":"Journal of Computational Chemistry"},{"issue":"10","key":"10.1016\/j.carbpol.2020.117261_bib0140","doi-asserted-by":"crossref","first-page":"873","DOI":"10.1016\/j.tips.2017.06.003","article-title":"The future of cysteine cathepsins in disease management","volume":"38","author":"Kramer","year":"2017","journal-title":"Trends in Pharmacological Sciences"},{"issue":"6","key":"10.1016\/j.carbpol.2020.117261_bib0145","doi-asserted-by":"crossref","first-page":"1944","DOI":"10.3390\/ijms21061944","article-title":"Regulation of the proteolytic activity of cysteine cathepsins by oxidants","volume":"21","author":"Lalmanach","year":"2020","journal-title":"International Journal of Molecular Sciences"},{"issue":"12","key":"10.1016\/j.carbpol.2020.117261_bib0150","doi-asserted-by":"crossref","first-page":"4459","DOI":"10.1021\/cr0101656","article-title":"Human and parasitic papain-like cysteine proteases: Their role in physiology and pathology and recent developments in inhibitor design","volume":"102","author":"Lecaille","year":"2002","journal-title":"Chemical Reviews"},{"issue":"2","key":"10.1016\/j.carbpol.2020.117261_bib0155","doi-asserted-by":"crossref","first-page":"127","DOI":"10.1016\/S0165-5876(01)00417-7","article-title":"Disordered breathing during sleep in patients with mucopolysaccharidoses","volume":"58","author":"Leighton","year":"2001","journal-title":"International Journal of Pediatric Otorhinolaryngology"},{"issue":"3","key":"10.1016\/j.carbpol.2020.117261_bib0160","doi-asserted-by":"crossref","first-page":"529","DOI":"10.1021\/bi992251u","article-title":"Collagenolytic activity of cathepsin K is specifically modulated by cartilage-resident chondroitin sulfates","volume":"39","author":"Li","year":"2000","journal-title":"Biochemistry"},{"issue":"44","key":"10.1016\/j.carbpol.2020.117261_bib0165","doi-asserted-by":"crossref","first-page":"34240","DOI":"10.1074\/jbc.M110.159152","article-title":"Chemoenzymatic design of heparan sulfate oligosaccharides","volume":"285","author":"Liu","year":"2010","journal-title":"The Journal of Biological Chemistry"},{"issue":"14","key":"10.1016\/j.carbpol.2020.117261_bib0170","doi-asserted-by":"crossref","first-page":"1639","DOI":"10.1002\/(SICI)1096-987X(19981115)19:14<1639::AID-JCC10>3.0.CO;2-B","article-title":"Automated docking using a Lamarckian genetic algorithm and an empirical binding free energy function","volume":"19","author":"Morris","year":"1998","journal-title":"Journal of Computational Chemistry"},{"issue":"suppl 5","key":"10.1016\/j.carbpol.2020.117261_bib0175","doi-asserted-by":"crossref","first-page":"v4","DOI":"10.1093\/rheumatology\/ker394","article-title":"Overview of the mucopolysaccharidoses","volume":"50","author":"Muenzer","year":"2011","journal-title":"Rheumatology"},{"issue":"2","key":"10.1016\/j.carbpol.2020.117261_bib0180","doi-asserted-by":"crossref","first-page":"133","DOI":"10.1016\/j.prrv.2010.10.005","article-title":"Respiratory manifestations in mucopolysaccharidoses","volume":"12","author":"Muhlebach","year":"2011","journal-title":"Paediatric Respiratory Reviews"},{"key":"10.1016\/j.carbpol.2020.117261_bib0185","doi-asserted-by":"crossref","first-page":"e25577","DOI":"10.1371\/journal.pone.0025577","article-title":"Human cysteine cathepsins are not reliable markers of infection by Pseudomonas aeruginosa in cystic fibrosis","volume":"6","author":"Naudin","year":"2011","journal-title":"PloS One"},{"key":"10.1016\/j.carbpol.2020.117261_bib0190","doi-asserted-by":"crossref","first-page":"55","DOI":"10.1007\/5584_2014_26","article-title":"Endostatin and cathepsin-V in bronchoalveolar lavage fluid of patients with pulmonary sarcoidosis","author":"Naumnik","year":"2014","journal-title":"Lung Cancer and Autoimmune Disorders"},{"key":"10.1016\/j.carbpol.2020.117261_bib0195","doi-asserted-by":"crossref","first-page":"1","DOI":"10.1155\/2014\/309718","article-title":"Cysteine cathepsin activity regulation by glycosaminoglycans","volume":"2014","author":"Novinec","year":"2014","journal-title":"BioMed Research International"},{"issue":"4","key":"10.1016\/j.carbpol.2020.117261_bib0200","doi-asserted-by":"crossref","first-page":"1902","DOI":"10.1073\/pnas.252784899","article-title":"Activated microglia in cortex of mouse models of mucopolysaccharidoses I and IIIB","volume":"100","author":"Ohmi","year":"2003","journal-title":"Proceedings of the National Academy of Sciences"},{"issue":"14","key":"10.1016\/j.carbpol.2020.117261_bib0205","doi-asserted-by":"crossref","first-page":"1297","DOI":"10.1002\/jcc.10126","article-title":"Effective born radii in the generalized Born approximation: The importance of being perfect","volume":"23","author":"Onufriev","year":"2002","journal-title":"Journal of Computational Chemistry"},{"issue":"9","key":"10.1016\/j.carbpol.2020.117261_bib0210","doi-asserted-by":"crossref","first-page":"e0203216","DOI":"10.1371\/journal.pone.0203216","article-title":"Substrate accumulation and extracellular matrix remodelling promote persistent upper airway disease in mucopolysaccharidosis patients on enzyme replacement therapy","volume":"13","author":"Pal","year":"2018","journal-title":"PloS One"},{"issue":"6","key":"10.1016\/j.carbpol.2020.117261_bib0215","doi-asserted-by":"crossref","first-page":"1956","DOI":"10.1182\/blood-2005-02-0657","article-title":"Functional abnormalities of heparan sulfate in mucopolysaccharidosis-I are associated with defective biologic activity of FGF-2 on human multipotent progenitor cells","volume":"106","author":"Pan","year":"2005","journal-title":"Blood"},{"issue":"11","key":"10.1016\/j.carbpol.2020.117261_bib0220","first-page":"1209","article-title":"The structural investigation of glycosaminoglycan binding to CXCL12 displays distinct interaction sites","volume":"26","author":"Panitz","year":"2016","journal-title":"Glycobiology"},{"issue":"1","key":"10.1016\/j.carbpol.2020.117261_bib0225","doi-asserted-by":"crossref","first-page":"134","DOI":"10.1093\/glycob\/cwr120","article-title":"Characterization of the interaction of interleukin-8 with hyaluronan, chondroitin sulfate, dermatan sulfate and their sulfated derivatives by spectroscopy and molecular modeling","volume":"22","author":"Pichert","year":"2012","journal-title":"Glycobiology"},{"issue":"10","key":"10.1016\/j.carbpol.2020.117261_bib0230","doi-asserted-by":"crossref","first-page":"3421","DOI":"10.1172\/JCI42918","article-title":"Specialized roles for cysteine cathepsins in health and disease","volume":"120","author":"Reiser","year":"2010","journal-title":"The Journal of Clinical Investigation"},{"issue":"1","key":"10.1016\/j.carbpol.2020.117261_bib0235","doi-asserted-by":"crossref","first-page":"50","DOI":"10.1186\/s13023-016-0425-z","article-title":"Severe tracheal and bronchial collapse in adults with type II mucopolysaccharidosis","volume":"11","author":"Rutten","year":"2016","journal-title":"Orphanet Journal of Rare Diseases"},{"issue":"37","key":"10.1016\/j.carbpol.2020.117261_bib0240","doi-asserted-by":"crossref","first-page":"6487","DOI":"10.1021\/bi400925g","article-title":"Binding of chondroitin 4-sulfate to cathepsin S regulates its enzymatic activity","volume":"52","author":"Sage","year":"2013","journal-title":"Biochemistry"},{"issue":"1","key":"10.1016\/j.carbpol.2020.117261_bib0245","doi-asserted-by":"crossref","first-page":"13","DOI":"10.1186\/1465-9921-12-13","article-title":"Lack of cathepsin activities alter or prevent the development of lung granulomas in a mouse model of sarcoidosis","volume":"12","author":"Samokhin","year":"2011","journal-title":"Respiratory Research"},{"key":"10.1016\/j.carbpol.2020.117261_bib0250","doi-asserted-by":"crossref","first-page":"850","DOI":"10.1093\/glycob\/cww055","article-title":"). Computational analysis of interactions in structurally available protein\u2013glycosaminoglycan complexes","volume":"8","author":"Samsonov","year":"2016","journal-title":"Glycobiology"},{"key":"10.1016\/j.carbpol.2020.117261_bib0255","first-page":"1624","article-title":"Cathepsin L2, a novel human cysteine proteinase produced by breast and colorectal carcinomas","volume":"8","author":"Santamar\u00eda","year":"1998","journal-title":"Cancer Research"},{"issue":"35","key":"10.1016\/j.carbpol.2020.117261_bib0260","doi-asserted-by":"crossref","first-page":"13075","DOI":"10.1073\/pnas.0805862105","article-title":"Surfen, a small molecule antagonist of heparan sulfate","volume":"105","author":"Schuksz","year":"2008","journal-title":"Proceedings of the National Academy of Sciences"},{"issue":"51","key":"10.1016\/j.carbpol.2020.117261_bib0265","doi-asserted-by":"crossref","first-page":"37045","DOI":"10.1074\/jbc.M703447200","article-title":"Cell type-specific functions of the lysosomal protease cathepsin L in the heart","volume":"282","author":"Spira","year":"2007","journal-title":"The Journal of Biological Chemistry"},{"issue":"1\u20132","key":"10.1016\/j.carbpol.2020.117261_bib0270","doi-asserted-by":"crossref","first-page":"4","DOI":"10.1016\/j.ymgme.2018.01.003","article-title":"Clinical presentation and diagnosis of mucopolysaccharidoses","volume":"125","author":"Stapleton","year":"2018","journal-title":"Molecular Genetics and Metabolism"},{"issue":"4","key":"10.1016\/j.carbpol.2020.117261_bib0275","doi-asserted-by":"crossref","first-page":"517","DOI":"10.1172\/JCI200318028","article-title":"Cathepsin V is involved in the degradation of invariant chain in human thymus and is overexpressed in myasthenia gravis","volume":"112","author":"Tolosa","year":"2003","journal-title":"The Journal of Clinical Investigation"},{"issue":"2","key":"10.1016\/j.carbpol.2020.117261_bib0280","doi-asserted-by":"crossref","first-page":"396","DOI":"10.3390\/jcm9020396","article-title":"Brain pathology in mucopolysaccharidoses (MPS) patients with neurological forms","volume":"9","author":"Viana","year":"2020","journal-title":"Journal of Clinical Medicine"},{"issue":"3","key":"10.1016\/j.carbpol.2020.117261_bib0285","doi-asserted-by":"crossref","first-page":"264","DOI":"10.3390\/cells8030264","article-title":"Cysteine cathepsins and their extracellular roles: Shaping the microenvironment","volume":"8","author":"Vidak","year":"2019","journal-title":"Cells"},{"key":"10.1016\/j.carbpol.2020.117261_bib0290","doi-asserted-by":"crossref","first-page":"141","DOI":"10.1016\/j.matbio.2018.01.024","article-title":"Cysteine cathepsins in extracellular matrix remodeling: Extracellular matrix degradation and beyond","volume":"75\u201376","author":"Vizovi\u0161ek","year":"2019","journal-title":"Matrix Biology"},{"issue":"6","key":"10.1016\/j.carbpol.2020.117261_bib0295","doi-asserted-by":"crossref","first-page":"573","DOI":"10.1080\/14728222.2020.1746765","article-title":"Cysteine cathepsins as therapeutic targets in inflammatory diseases","volume":"24","author":"Vizovi\u0161ek","year":"2020","journal-title":"Expert Opinion on Therapeutic Targets"},{"issue":"7","key":"10.1016\/j.carbpol.2020.117261_bib0300","doi-asserted-by":"crossref","first-page":"2745","DOI":"10.1021\/cr010213m","article-title":"Heparan sulfate: A complex polymer charged with biological activity","volume":"105","author":"Whitelock","year":"2005","journal-title":"Chemical Reviews"},{"issue":"5","key":"10.1016\/j.carbpol.2020.117261_bib0305","doi-asserted-by":"crossref","first-page":"2053","DOI":"10.2353\/ajpath.2009.090211","article-title":"Glycosaminoglycan-mediated loss of cathepsin K collagenolytic activity in MPS I contributes to osteoclast and growth plate abnormalities","volume":"175","author":"Wilson","year":"2009","journal-title":"The American Journal of Pathology"},{"issue":"35","key":"10.1016\/j.carbpol.2020.117261_bib0310","doi-asserted-by":"crossref","first-page":"36761","DOI":"10.1074\/jbc.M403986200","article-title":"Cathepsin V, a novel and potent elastolytic activity expressed in activated macrophages","volume":"279","author":"Yasuda","year":"2004","journal-title":"The Journal of Biological Chemistry"}],"container-title":["Carbohydrate Polymers"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S014486172031434X?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S014486172031434X?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2025,9,27]],"date-time":"2025-09-27T00:00:39Z","timestamp":1758931239000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S014486172031434X"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2021,2]]},"references-count":62,"alternative-id":["S014486172031434X"],"URL":"https:\/\/doi.org\/10.1016\/j.carbpol.2020.117261","relation":{},"ISSN":["0144-8617"],"issn-type":[{"value":"0144-8617","type":"print"}],"subject":[],"published":{"date-parts":[[2021,2]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"The abnormal accumulation of heparan sulfate in patients with mucopolysaccharidosis prevents the elastolytic activity of cathepsin V","name":"articletitle","label":"Article Title"},{"value":"Carbohydrate Polymers","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.carbpol.2020.117261","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"\u00a9 2020 Elsevier Ltd. All rights reserved.","name":"copyright","label":"Copyright"}],"article-number":"117261"}}