{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,4]],"date-time":"2026-08-04T22:26:11Z","timestamp":1785882371559,"version":"3.56.0"},"reference-count":107,"publisher":"Elsevier BV","license":[{"start":{"date-parts":[[2016,12,1]],"date-time":"2016-12-01T00:00:00Z","timestamp":1480550400000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"}],"funder":[{"DOI":"10.13039\/100010551","name":"Texas Heart Institute","doi-asserted-by":"crossref","award":["765-64050"],"award-info":[{"award-number":["765-64050"]}],"id":[{"id":"10.13039\/100010551","id-type":"DOI","asserted-by":"crossref"}]},{"DOI":"10.13039\/501100004694","name":"Kaohsiung Medical University","doi-asserted-by":"publisher","award":["KMU-TP104D00"],"award-info":[{"award-number":["KMU-TP104D00"]}],"id":[{"id":"10.13039\/501100004694","id-type":"DOI","asserted-by":"publisher"}]}],"content-domain":{"domain":["elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Clinica Chimica Acta"],"published-print":{"date-parts":[[2016,12]]},"DOI":"10.1016\/j.cca.2016.10.017","type":"journal-article","created":{"date-parts":[[2016,10,17]],"date-time":"2016-10-17T09:11:44Z","timestamp":1476695504000},"page":"109-118","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":38,"special_numbering":"C","title":["Update on ADAMTS13 and VWF in cardiovascular and hematological disorders"],"prefix":"10.1016","volume":"463","author":[{"given":"Omer","family":"Akyol","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Sumeyya","family":"Akyol","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Chu-Huang","family":"Chen","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"key":"10.1016\/j.cca.2016.10.017_bb0005","doi-asserted-by":"crossref","first-page":"323","DOI":"10.5455\/bcp.20140905124459","article-title":"Evidence for the control of aggrecanases by insulin and glucose in Alzheimer's disease","volume":"24","author":"Akyol","year":"2014","journal-title":"Klinik Psikofarmakoloji Bulteni (Bulletin of Clinical Psychopharmacology)"},{"key":"10.1016\/j.cca.2016.10.017_bb0010","doi-asserted-by":"crossref","first-page":"2207","DOI":"10.1182\/blood-2006-02-002139","article-title":"Apical sorting of ADAMTS13 in vascular endothelial cells and Madin-Darby canine kidney cells depends on the CUB domains and their association with lipid rafts","volume":"108","author":"Shang","year":"2006","journal-title":"Blood"},{"key":"10.1016\/j.cca.2016.10.017_bb0015","doi-asserted-by":"crossref","first-page":"922","DOI":"10.1182\/blood-2005-01-0152","article-title":"Localization of ADAMTS13 to the stellate cells of human liver","volume":"106","author":"Uemura","year":"2005","journal-title":"Blood"},{"key":"10.1016\/j.cca.2016.10.017_bb0020","doi-asserted-by":"crossref","first-page":"375","DOI":"10.1590\/1414-431X20122603","article-title":"Plasmatic ADAMTS-13 metalloprotease and von Willebrand factor in children with cyanotic congenital heart disease","volume":"46","author":"Soares","year":"2013","journal-title":"Braz. J. Med. Biol. Res."},{"key":"10.1016\/j.cca.2016.10.017_bb0025","doi-asserted-by":"crossref","first-page":"1662","DOI":"10.1182\/blood.V98.6.1662","article-title":"Purification of human von Willebrand factor-cleaving protease and its identification as a new member of the metalloproteinase family","volume":"98","author":"Fujikawa","year":"2001","journal-title":"Blood"},{"key":"10.1016\/j.cca.2016.10.017_bb0030","doi-asserted-by":"crossref","first-page":"41059","DOI":"10.1074\/jbc.C100515200","article-title":"Structure of von Willebrand factor-cleaving protease (ADAMTS13), a metalloprotease involved in thrombotic thrombocytopenic purpura","volume":"276","author":"Zheng","year":"2001","journal-title":"J. Biol. Chem."},{"key":"10.1016\/j.cca.2016.10.017_bb0035","doi-asserted-by":"crossref","first-page":"395","DOI":"10.1146\/annurev.biochem.67.1.395","article-title":"Biochemistry and genetics of von Willebrand factor","volume":"67","author":"Sadler","year":"1998","journal-title":"Annu. Rev. Biochem."},{"key":"10.1016\/j.cca.2016.10.017_bb0040","doi-asserted-by":"crossref","first-page":"259","DOI":"10.1111\/j.1365-2141.1982.tb03888.x","article-title":"Response to infusions of polyelectrolyte fractionated human factor VIII concentrate in human haemophilia A and von Willebrand's disease","volume":"52","author":"Tuddenham","year":"1982","journal-title":"Br. J. Haematol."},{"key":"10.1016\/j.cca.2016.10.017_bb0045","doi-asserted-by":"crossref","first-page":"18578","DOI":"10.1073\/pnas.1411979112","article-title":"Conformational activation of ADAMTS13","volume":"111","author":"South","year":"2014","journal-title":"Proc. Natl. Acad. Sci. U. S. A."},{"key":"10.1016\/j.cca.2016.10.017_bb0050","doi-asserted-by":"crossref","first-page":"2939","DOI":"10.1182\/blood.V88.8.2939.bloodjournal8882939","article-title":"Shear-dependent changes in the three-dimensional structure of human von Willebrand factor","volume":"88","author":"Siedlecki","year":"1996","journal-title":"Blood"},{"key":"10.1016\/j.cca.2016.10.017_bb0055","doi-asserted-by":"crossref","first-page":"19098","DOI":"10.1074\/jbc.M002292200","article-title":"Mapping the glycoprotein Ib-binding site in the von Willebrand factor A1 domain","volume":"275","author":"Cruz","year":"2000","journal-title":"J. Biol. Chem."},{"key":"10.1016\/j.cca.2016.10.017_bb0060","doi-asserted-by":"crossref","first-page":"55","DOI":"10.1016\/0049-3848(96)00161-2","article-title":"Effect of multimerization of human and recombinant von Willebrand factor on platelet aggregation, binding to collagen and binding of coagulation factor VIII","volume":"84","author":"Fischer","year":"1996","journal-title":"Thromb. Res."},{"key":"10.1016\/j.cca.2016.10.017_bb0065","doi-asserted-by":"crossref","first-page":"4235","DOI":"10.1182\/blood.V87.10.4235.bloodjournal87104235","article-title":"Physiologic cleavage of von Willebrand factor by a plasma protease is dependent on its conformation and requires calcium ion","volume":"87","author":"Tsai","year":"1996","journal-title":"Blood"},{"key":"10.1016\/j.cca.2016.10.017_bb0070","doi-asserted-by":"crossref","first-page":"1330","DOI":"10.1126\/science.1170905","article-title":"Mechanoenzymatic cleavage of the ultralarge vascular protein von Willebrand factor","volume":"324","author":"Zhang","year":"2009","journal-title":"Science"},{"key":"10.1016\/j.cca.2016.10.017_bb0075","doi-asserted-by":"crossref","first-page":"1456","DOI":"10.1172\/JCI112736","article-title":"Involvement of large plasma von Willebrand factor (vWF) multimers and unusually large vWF forms derived from endothelial cells in shear stress-induced platelet aggregation","volume":"78","author":"Moake","year":"1986","journal-title":"J. Clin. Invest."},{"key":"10.1016\/j.cca.2016.10.017_bb0080","doi-asserted-by":"crossref","first-page":"292","DOI":"10.1182\/asheducation-2013.1.292","article-title":"Thrombotic thrombocytopenic purpura: basic pathophysiology and therapeutic strategies","volume":"2013","author":"Crawley","year":"2013","journal-title":"Hematology Am. Soc. Hematol. Educ. Program"},{"key":"10.1016\/j.cca.2016.10.017_bb0085","doi-asserted-by":"crossref","first-page":"11","DOI":"10.1002\/humu.21143","article-title":"ADAMTS13 mutations and polymorphisms in congenital thrombotic thrombocytopenic purpura","volume":"31","author":"Lotta","year":"2010","journal-title":"Hum. Mutat."},{"key":"10.1016\/j.cca.2016.10.017_bb0090","doi-asserted-by":"crossref","first-page":"488","DOI":"10.1038\/35097008","article-title":"Mutations in a member of the ADAMTS gene family cause thrombotic thrombocytopenic purpura","volume":"413","author":"Levy","year":"2001","journal-title":"Nature"},{"key":"10.1016\/j.cca.2016.10.017_bb0095","doi-asserted-by":"crossref","first-page":"593","DOI":"10.1160\/TH07-01-0059","article-title":"Molecular characterization of four ADAMTS13 mutations responsible for congenital thrombotic thrombocytopenic purpura (Upshaw-Schulman syndrome)","volume":"98","author":"Hommais","year":"2007","journal-title":"Thromb. Haemost."},{"key":"10.1016\/j.cca.2016.10.017_bb0100","doi-asserted-by":"crossref","first-page":"118","DOI":"10.1182\/blood-2005-06-2482","article-title":"Modulation of ADAMTS13 secretion and specific activity by a combination of common amino acid polymorphisms and a missense mutation","volume":"107","author":"Plaimauer","year":"2006","journal-title":"Blood"},{"key":"10.1016\/j.cca.2016.10.017_bb0105","doi-asserted-by":"crossref","first-page":"4514","DOI":"10.1182\/blood-2003-12-4165","article-title":"Epitope mapping of ADAMTS13 autoantibodies in acquired thrombotic thrombocytopenic purpura","volume":"103","author":"Klaus","year":"2004","journal-title":"Blood"},{"key":"10.1016\/j.cca.2016.10.017_bb0110","doi-asserted-by":"crossref","first-page":"3241","DOI":"10.1182\/blood-2003-05-1616","article-title":"Nonneutralizing IgM and IgG antibodies to von Willebrand factor-cleaving protease (ADAMTS-13) in a patient with thrombotic thrombocytopenic purpura","volume":"102","author":"Scheiflinger","year":"2003","journal-title":"Blood"},{"key":"10.1016\/j.cca.2016.10.017_bb0115","doi-asserted-by":"crossref","first-page":"267","DOI":"10.1160\/TH04-05-0301","article-title":"The spacer domain of ADAMTS13 contains a major binding site for antibodies in patients with thrombotic thrombocytopenic purpura","volume":"93","author":"Luken","year":"2005","journal-title":"Thromb. Haemost."},{"key":"10.1016\/j.cca.2016.10.017_bb0120","doi-asserted-by":"crossref","first-page":"3097","DOI":"10.1182\/blood.V89.9.3097","article-title":"Deficient activity of von Willebrand factor-cleaving protease in chronic relapsing thrombotic thrombocytopenic purpura","volume":"89","author":"Furlan","year":"1997","journal-title":"Blood"},{"key":"10.1016\/j.cca.2016.10.017_bb0125","doi-asserted-by":"crossref","first-page":"393","DOI":"10.1056\/NEJM199108083250604","article-title":"Comparison of plasma exchange with plasma infusion in the treatment of thrombotic thrombocytopenic purpura. Canadian Apheresis Study Group","volume":"325","author":"Rock","year":"1991","journal-title":"N. Engl. J. Med."},{"key":"10.1016\/j.cca.2016.10.017_bb0130","doi-asserted-by":"crossref","first-page":"5217","DOI":"10.1182\/blood-2012-06-439935","article-title":"Protective anti-inflammatory effect of ADAMTS13 on myocardial ischemia\/reperfusion injury in mice","volume":"120","author":"De Meyer","year":"2012","journal-title":"Blood"},{"key":"10.1016\/j.cca.2016.10.017_bb0135","doi-asserted-by":"crossref","first-page":"1901","DOI":"10.1161\/ATVBAHA.107.145797","article-title":"Thrombotic thrombocytopenic purpura in humans and mice","volume":"27","author":"Desch","year":"2007","journal-title":"Arterioscler. Thromb. Vasc. Biol."},{"key":"10.1016\/j.cca.2016.10.017_bb0140","doi-asserted-by":"crossref","first-page":"3329","DOI":"10.1182\/blood-2009-03-213264","article-title":"von Willebrand factor-cleaving protease ADAMTS13 reduces ischemic brain injury in experimental stroke","volume":"114","author":"Zhao","year":"2009","journal-title":"Blood"},{"key":"10.1016\/j.cca.2016.10.017_bb0145","doi-asserted-by":"crossref","first-page":"2005","DOI":"10.1182\/blood-2010-04-280479","article-title":"Thrombotic thrombocytopenic purpura directly linked with ADAMTS13 inhibition in the baboon (Papio ursinus)","volume":"116","author":"Feys","year":"2010","journal-title":"Blood"},{"key":"10.1016\/j.cca.2016.10.017_bb0150","doi-asserted-by":"crossref","first-page":"2081","DOI":"10.1182\/blood-2004-02-0715","article-title":"Identification of novel mutations in ADAMTS13 in an adult patient with congenital thrombotic thrombocytopenic purpura","volume":"104","author":"Uchida","year":"2004","journal-title":"Blood"},{"key":"10.1016\/j.cca.2016.10.017_bb0155","doi-asserted-by":"crossref","first-page":"331","DOI":"10.1111\/j.1538-7836.2008.02846.x","article-title":"Prevalence of the ADAMTS-13 missense mutation R1060W in late onset adult thrombotic thrombocytopenic purpura","volume":"6","author":"Camilleri","year":"2008","journal-title":"J. Thromb. Haemost."},{"key":"10.1016\/j.cca.2016.10.017_bb0160","doi-asserted-by":"crossref","first-page":"1792","DOI":"10.1111\/j.1538-7836.2012.04852.x","article-title":"A phenotype-genotype correlation of ADAMTS13 mutations in congenital thrombotic thrombocytopenic purpura patients treated in the United Kingdom","volume":"10","author":"Camilleri","year":"2012","journal-title":"J. Thromb. Haemost."},{"key":"10.1016\/j.cca.2016.10.017_bb0165","doi-asserted-by":"crossref","first-page":"1746","DOI":"10.1182\/blood-2011-03-341131","article-title":"A phase 2 study of the safety and efficacy of rituximab with plasma exchange in acute acquired thrombotic thrombocytopenic purpura","volume":"118","author":"Scully","year":"2011","journal-title":"Blood"},{"key":"10.1016\/j.cca.2016.10.017_bb0170","first-page":"127","article-title":"Advantages and limits of ADAMTS13 testing in thrombotic thrombocytopenic purpura","volume":"6","author":"Franchini","year":"2008","journal-title":"Blood Transfus."},{"key":"10.1016\/j.cca.2016.10.017_bb0175","doi-asserted-by":"crossref","first-page":"2752","DOI":"10.1172\/JCI26007","article-title":"Shigatoxin triggers thrombotic thrombocytopenic purpura in genetically susceptible ADAMTS13-deficient mice","volume":"115","author":"Motto","year":"2005","journal-title":"J. Clin. Invest."},{"key":"10.1016\/j.cca.2016.10.017_bb0180","doi-asserted-by":"crossref","first-page":"742","DOI":"10.1111\/j.1365-2141.2008.07515.x","article-title":"Pregnancy-induced thrombocytopenia and TTP, and the risk of fetal death, in Upshaw-Schulman syndrome: a series of 15 pregnancies in 9 genotyped patients","volume":"144","author":"Fujimura","year":"2009","journal-title":"Br. J. Haematol."},{"key":"10.1016\/j.cca.2016.10.017_bb0185","doi-asserted-by":"crossref","first-page":"21","DOI":"10.1002\/jca.20114","article-title":"Do infections provoke exacerbations and relapses of thrombotic thrombocytopenic purpura?","volume":"22","author":"Cserti","year":"2007","journal-title":"J. Clin. Apher."},{"key":"10.1016\/j.cca.2016.10.017_bb0190","doi-asserted-by":"crossref","first-page":"169","DOI":"10.1111\/j.1368-5031.2004.0080.x","article-title":"Post-operative thrombotic thrombocytopenic purpura: a review","volume":"58","author":"Naqvi","year":"2004","journal-title":"Int. J. Clin. Pract."},{"key":"10.1016\/j.cca.2016.10.017_bb0195","doi-asserted-by":"crossref","first-page":"3161","DOI":"10.1182\/blood-2005-07-2765","article-title":"Complete deficiency in ADAMTS13 is prothrombotic, but it alone is not sufficient to cause thrombotic thrombocytopenic purpura","volume":"107","author":"Banno","year":"2006","journal-title":"Blood"},{"key":"10.1016\/j.cca.2016.10.017_bb0200","doi-asserted-by":"crossref","first-page":"1666","DOI":"10.1182\/blood-2009-01-195461","article-title":"Leukocyte proteases cleave von Willebrand factor at or near the ADAMTS13 cleavage site","volume":"114","author":"Raife","year":"2009","journal-title":"Blood"},{"key":"10.1016\/j.cca.2016.10.017_bb0205","doi-asserted-by":"crossref","first-page":"24","DOI":"10.1053\/j.seminhematol.2003.10.006","article-title":"Expression and characterization of recombinant human ADAMTS-13","volume":"41","author":"Plaimauer","year":"2004","journal-title":"Semin. Hematol."},{"key":"10.1016\/j.cca.2016.10.017_bb0210","doi-asserted-by":"crossref","first-page":"6128","DOI":"10.1182\/blood-2011-09-380535","article-title":"A new mouse model mimicking thrombotic thrombocytopenic purpura: correction of symptoms by recombinant human ADAMTS13","volume":"119","author":"Schiviz","year":"2012","journal-title":"Blood"},{"key":"10.1016\/j.cca.2016.10.017_bb0215","doi-asserted-by":"crossref","first-page":"849","DOI":"10.1016\/j.thromres.2007.08.003","article-title":"ADAMTS13 related markers and von Willebrand factor in plasma from patients with thrombotic microangiopathy (TMA)","volume":"121","author":"Kobayashi","year":"2008","journal-title":"Thromb. Res."},{"key":"10.1016\/j.cca.2016.10.017_bb0220","doi-asserted-by":"crossref","first-page":"1305","DOI":"10.1182\/blood-2003-06-1796","article-title":"Molecular characterization of ADAMTS13 gene mutations in Japanese patients with Upshaw-Schulman syndrome","volume":"103","author":"Matsumoto","year":"2004","journal-title":"Blood"},{"key":"10.1016\/j.cca.2016.10.017_bb0225","doi-asserted-by":"crossref","first-page":"1085","DOI":"10.1182\/blood-2004-03-1101","article-title":"Proteolytic inactivation of ADAMTS13 by thrombin and plasmin","volume":"105","author":"Crawley","year":"2005","journal-title":"Blood"},{"key":"10.1016\/j.cca.2016.10.017_bb0230","doi-asserted-by":"crossref","first-page":"528","DOI":"10.1182\/blood-2005-03-1087","article-title":"Severe secondary deficiency of von Willebrand factor-cleaving protease (ADAMTS13) in patients with sepsis-induced disseminated intravascular coagulation: its correlation with development of renal failure","volume":"107","author":"Ono","year":"2006","journal-title":"Blood"},{"key":"10.1016\/j.cca.2016.10.017_bb0235","doi-asserted-by":"crossref","first-page":"106","DOI":"10.1002\/jca.20196","article-title":"Value of ADAMTS13 activity and inhibitor in the postmortem diagnosis of thrombotic thrombocytopenic purpura","volume":"24","author":"Dwyre","year":"2009","journal-title":"J. Clin. Apher."},{"key":"10.1016\/j.cca.2016.10.017_bb0240","doi-asserted-by":"crossref","first-page":"1386","DOI":"10.1055\/s-0037-1614780","article-title":"Assay of von Willebrand factor (vWF)-cleaving protease based on decreased collagen binding affinity of degraded vWF: a tool for the diagnosis of thrombotic thrombocytopenic purpura (TTP)","volume":"82","author":"Gerritsen","year":"1999","journal-title":"Thromb. Haemost."},{"key":"10.1016\/j.cca.2016.10.017_bb0245","doi-asserted-by":"crossref","first-page":"269","DOI":"10.1016\/j.blre.2014.09.001","article-title":"De novo thrombotic microangiopathy after non-renal solid organ transplantation","volume":"28","author":"Verbiest","year":"2014","journal-title":"Blood Rev."},{"key":"10.1016\/j.cca.2016.10.017_bb0250","doi-asserted-by":"crossref","first-page":"1320","DOI":"10.1161\/CIRCULATIONAHA.113.006727","article-title":"Plasmin cleavage of von Willebrand factor as an emergency bypass for ADAMTS13 deficiency in thrombotic microangiopathy","volume":"129","author":"Tersteeg","year":"2014","journal-title":"Circulation"},{"key":"10.1016\/j.cca.2016.10.017_bb0255","doi-asserted-by":"crossref","first-page":"e41","DOI":"10.1016\/j.thromres.2011.11.021","article-title":"Modulation of the von Willebrand factor-dependent platelet adhesion through alternative proteolytic pathways","volume":"129","author":"Wohner","year":"2012","journal-title":"Thromb. Res."},{"key":"10.1016\/j.cca.2016.10.017_bb0260","doi-asserted-by":"crossref","first-page":"3300","DOI":"10.1182\/blood.V91.9.3300","article-title":"Hypoxia stimulates urokinase receptor expression through a heme protein-dependent pathway","volume":"91","author":"Graham","year":"1998","journal-title":"Blood"},{"key":"10.1016\/j.cca.2016.10.017_bb0265","doi-asserted-by":"crossref","first-page":"1555","DOI":"10.1182\/blood-2011-09-380618","article-title":"High VWF, low ADAMTS13, and oral contraceptives increase the risk of ischemic stroke and myocardial infarction in young women","volume":"119","author":"Andersson","year":"2012","journal-title":"Blood"},{"key":"10.1016\/j.cca.2016.10.017_bb0270","doi-asserted-by":"crossref","first-page":"250","DOI":"10.1016\/j.atherosclerosis.2009.04.013","article-title":"Lower levels of ADAMTS13 are associated with cardiovascular disease in young patients","volume":"207","author":"Bongers","year":"2009","journal-title":"Atherosclerosis"},{"key":"10.1016\/j.cca.2016.10.017_bb0275","doi-asserted-by":"crossref","first-page":"583","DOI":"10.1111\/j.1538-7836.2008.02902.x","article-title":"Evidence that high von Willebrand factor and low ADAMTS-13 levels independently increase the risk of a non-fatal heart attack","volume":"6","author":"Crawley","year":"2008","journal-title":"J. Thromb. Haemost."},{"key":"10.1016\/j.cca.2016.10.017_bb0280","doi-asserted-by":"crossref","first-page":"1998","DOI":"10.1182\/blood-2006-07-038166","article-title":"ADAMTS13 and von Willebrand factor and the risk of myocardial infarction in men","volume":"109","author":"Chion","year":"2007","journal-title":"Blood"},{"key":"10.1016\/j.cca.2016.10.017_bb0285","doi-asserted-by":"crossref","first-page":"301","DOI":"10.1007\/s00380-008-1053-x","article-title":"Acute myocardial infarction as a systemic prothrombotic condition evidenced by increased von Willebrand factor protein over ADAMTS13 activity in coronary and systemic circulation","volume":"23","author":"Horii","year":"2008","journal-title":"Heart Vessel."},{"key":"10.1016\/j.cca.2016.10.017_bb0290","doi-asserted-by":"crossref","first-page":"1653","DOI":"10.1111\/j.1538-7836.2010.03896.x","article-title":"Active platelet-binding conformation of plasma von Willebrand factor in young women with acute myocardial infarction","volume":"8","author":"Peyvandi","year":"2010","journal-title":"J. Thromb. Haemost."},{"key":"10.1016\/j.cca.2016.10.017_bb0295","doi-asserted-by":"crossref","first-page":"167","DOI":"10.1016\/j.blre.2014.04.003","article-title":"Von Willebrand factor and ADAMTS13 in arterial thrombosis: a systematic review and meta-analysis","volume":"28","author":"Sonneveld","year":"2014","journal-title":"Blood Rev."},{"key":"10.1016\/j.cca.2016.10.017_bb0300","doi-asserted-by":"crossref","first-page":"58","DOI":"10.1002\/ana.23735","article-title":"Role of reduced ADAMTS13 in arterial ischemic stroke: a pediatric cohort study","volume":"73","author":"Lambers","year":"2013","journal-title":"Ann. Neurol."},{"key":"10.1016\/j.cca.2016.10.017_bb0305","doi-asserted-by":"crossref","first-page":"2672","DOI":"10.1161\/01.STR.0000244767.39962.f7","article-title":"High von Willebrand factor levels increase the risk of first ischemic stroke: influence of ADAMTS13, inflammation, and genetic variability","volume":"37","author":"Bongers","year":"2006","journal-title":"Stroke"},{"key":"10.1016\/j.cca.2016.10.017_bb0310","doi-asserted-by":"crossref","first-page":"64","DOI":"10.1177\/2048872614534388","article-title":"Plasma levels of active Von Willebrand factor are increased in patients with first ST-segment elevation myocardial infarction: a multicenter and multiethnic study","volume":"4","author":"Rutten","year":"2015","journal-title":"Eur. Heart J. Acute Cardiovasc. Care"},{"key":"10.1016\/j.cca.2016.10.017_bb0315","doi-asserted-by":"crossref","first-page":"1396","DOI":"10.1111\/jth.13032","article-title":"Plasma ADAMTS-13 levels and the risk of myocardial infarction: an individual patient data meta-analysis","volume":"13","author":"Maino","year":"2015","journal-title":"J. Thromb. Haemost."},{"key":"10.1016\/j.cca.2016.10.017_bb0320","doi-asserted-by":"crossref","first-page":"1650","DOI":"10.1182\/blood-2009-06-230110","article-title":"ADAMTS13 gene deletion aggravates ischemic brain damage: a possible neuroprotective role of ADAMTS13 by ameliorating postischemic hypoperfusion","volume":"115","author":"Fujioka","year":"2010","journal-title":"Blood"},{"key":"10.1016\/j.cca.2016.10.017_bb0325","doi-asserted-by":"crossref","first-page":"2065","DOI":"10.1084\/jem.20080130","article-title":"ADAMTS13: a new link between thrombosis and inflammation","volume":"205","author":"Chauhan","year":"2008","journal-title":"J. Exp. Med."},{"key":"10.1016\/j.cca.2016.10.017_bb0330","doi-asserted-by":"crossref","first-page":"1236","DOI":"10.1160\/TH12-09-0674","article-title":"ADAMTS13 safeguards the myocardium in a mouse model of acute myocardial infarction","volume":"108","author":"Doi","year":"2012","journal-title":"Thromb. Haemost."},{"key":"10.1016\/j.cca.2016.10.017_bb0335","doi-asserted-by":"crossref","first-page":"1065","DOI":"10.1016\/j.ahj.2008.07.008","article-title":"Uncontrolled immune response in acute myocardial infarction: unraveling the thread","volume":"156","author":"Bodi","year":"2008","journal-title":"Am. Heart J."},{"key":"10.1016\/j.cca.2016.10.017_bb0340","doi-asserted-by":"crossref","first-page":"31","DOI":"10.1016\/S0008-6363(01)00434-5","article-title":"The inflammatory response in myocardial infarction","volume":"53","author":"Frangogiannis","year":"2002","journal-title":"Cardiovasc. Res."},{"key":"10.1016\/j.cca.2016.10.017_bb0345","doi-asserted-by":"crossref","first-page":"2312","DOI":"10.1046\/j.1538-7836.2003.00467.x","article-title":"Associations of plasma fibrinogen assays, C-reactive protein and interleukin-6 with previous myocardial infarction","volume":"1","author":"Lowe","year":"2003","journal-title":"J. Thromb. Haemost."},{"key":"10.1016\/j.cca.2016.10.017_bb0350","doi-asserted-by":"crossref","first-page":"946","DOI":"10.1161\/01.CIR.98.10.946","article-title":"Impact of atrial fibrillation on the risk of death: the Framingham Heart Study","volume":"98","author":"Benjamin","year":"1998","journal-title":"Circulation"},{"key":"10.1016\/j.cca.2016.10.017_bb0355","doi-asserted-by":"crossref","first-page":"2N","DOI":"10.1016\/S0002-9149(98)00583-9","article-title":"Prevalence, incidence, prognosis, and predisposing conditions for atrial fibrillation: population-based estimates","volume":"82","author":"Kannel","year":"1998","journal-title":"Am. J. Cardiol."},{"key":"10.1016\/j.cca.2016.10.017_bb0360","doi-asserted-by":"crossref","first-page":"1926","DOI":"10.1016\/S0735-1097(00)00627-6","article-title":"A cross-sectional and diurnal study of thrombogenesis among patients with chronic atrial fibrillation","volume":"35","author":"Li-Saw-Hee","year":"2000","journal-title":"J. Am. Coll. Cardiol."},{"key":"10.1016\/j.cca.2016.10.017_bb0365","doi-asserted-by":"crossref","first-page":"929","DOI":"10.1378\/chest.111.4.929","article-title":"Platelet activation in embolic and preembolic status of patients with nonrheumatic atrial fibrillation","volume":"111","author":"Pongratz","year":"1997","journal-title":"Chest"},{"key":"10.1016\/j.cca.2016.10.017_bb0370","doi-asserted-by":"crossref","first-page":"1411","DOI":"10.1056\/NEJM200105103441901","article-title":"Use of transesophageal echocardiography to guide cardioversion in patients with atrial fibrillation","volume":"344","author":"Klein","year":"2001","journal-title":"N. Engl. J. Med."},{"key":"10.1016\/j.cca.2016.10.017_bb0375","doi-asserted-by":"crossref","first-page":"2760","DOI":"10.1161\/ATVBAHA.111.232991","article-title":"Left atrial blood stasis and Von Willebrand factor-ADAMTS13 homeostasis in atrial fibrillation","volume":"31","author":"Ammash","year":"2011","journal-title":"Arterioscler. Thromb. Vasc. Biol."},{"key":"10.1016\/j.cca.2016.10.017_bb0380","doi-asserted-by":"crossref","first-page":"589","DOI":"10.1056\/NEJMra020528","article-title":"Thrombotic microangiopathies","volume":"347","author":"Moake","year":"2002","journal-title":"N. Engl. J. Med."},{"key":"10.1016\/j.cca.2016.10.017_bb0385","doi-asserted-by":"crossref","first-page":"767","DOI":"10.1084\/jem.20051732","article-title":"Systemic antithrombotic effects of ADAMTS13","volume":"203","author":"Chauhan","year":"2006","journal-title":"J. Exp. Med."},{"key":"10.1016\/j.cca.2016.10.017_bb0390","doi-asserted-by":"crossref","first-page":"1041","DOI":"10.1056\/NEJM199404143301503","article-title":"Genetic susceptibility to death from coronary heart disease in a study of twins","volume":"330","author":"Marenberg","year":"1994","journal-title":"N. Engl. J. Med."},{"key":"10.1016\/j.cca.2016.10.017_bb0395","doi-asserted-by":"crossref","first-page":"163","DOI":"10.1038\/nrg1805","article-title":"Genetic susceptibility to coronary artery disease: from promise to progress","volume":"7","author":"Watkins","year":"2006","journal-title":"Nat. Rev. Genet."},{"key":"10.1016\/j.cca.2016.10.017_bb0400","doi-asserted-by":"crossref","first-page":"49","DOI":"10.1053\/j.seminhematol.2004.09.009","article-title":"von Willebrand factor and factor VIII as risk factors for arterial and venous thrombosis","volume":"42","author":"Martinelli","year":"2005","journal-title":"Semin. Hematol."},{"key":"10.1016\/j.cca.2016.10.017_bb0405","doi-asserted-by":"crossref","first-page":"454","DOI":"10.1160\/TH06-05-0236","article-title":"In-vitro and in-vivo consequences of mutations in the von Willebrand factor cleaving protease ADAMTS13 in thrombotic thrombocytopenic purpura","volume":"96","author":"Donadelli","year":"2006","journal-title":"Thromb. Haemost."},{"key":"10.1016\/j.cca.2016.10.017_bb0410","first-page":"801A","article-title":"Modulation of the von Willebrand factor cleaving protease (ADAMTS-13) activity by polymorphisms in the ADAMTS-13 gene","author":"Peyvandi","year":"2003","journal-title":"Blood"},{"key":"10.1016\/j.cca.2016.10.017_bb0415","doi-asserted-by":"crossref","first-page":"827","DOI":"10.1016\/j.jhep.2012.11.003","article-title":"Porto-pulmonary hypertension exacerbated by platelet transfusion in a patient with ADAMTS13 deficiency","volume":"58","author":"Elias","year":"2013","journal-title":"J. Hepatol."},{"key":"10.1016\/j.cca.2016.10.017_bb0420","doi-asserted-by":"crossref","first-page":"2456","DOI":"10.1007\/s10620-011-1729-4","article-title":"Idiopathic noncirrhotic intrahepatic portal hypertension is associated with sustained ADAMTS13 Deficiency","volume":"56","author":"Mackie","year":"2011","journal-title":"Dig. Dis. Sci."},{"key":"10.1016\/j.cca.2016.10.017_bb0425","doi-asserted-by":"crossref","first-page":"31","DOI":"10.1093\/europace\/euq346","article-title":"A study of blood soluble P-selectin, fibrinogen, and von Willebrand factor levels in idiopathic and lone atrial fibrillation","volume":"13","author":"Fu","year":"2011","journal-title":"Europace"},{"key":"10.1016\/j.cca.2016.10.017_bb0430","doi-asserted-by":"crossref","first-page":"20","DOI":"10.1007\/s12185-009-0481-4","article-title":"Pivotal role of ADAMTS13 function in liver diseases","volume":"91","author":"Uemura","year":"2010","journal-title":"Int. J. Hematol."},{"key":"10.1016\/j.cca.2016.10.017_bb0435","doi-asserted-by":"crossref","first-page":"254","DOI":"10.1016\/j.amjcard.2006.01.083","article-title":"Pathogenesis of thrombocytopenia in cyanotic congenital heart disease","volume":"98","author":"Lill","year":"2006","journal-title":"Am. J. Cardiol."},{"key":"10.1016\/j.cca.2016.10.017_bb0440","doi-asserted-by":"crossref","first-page":"58","DOI":"10.1080\/10739680802651477","article-title":"Platelet adhesion under flow","volume":"16","author":"Ruggeri","year":"2009","journal-title":"Microcirculation"},{"key":"10.1016\/j.cca.2016.10.017_bb0445","doi-asserted-by":"crossref","first-page":"289","DOI":"10.1016\/S0092-8674(00)80983-6","article-title":"Initiation of platelet adhesion by arrest onto fibrinogen or translocation on von Willebrand factor","volume":"84","author":"Savage","year":"1996","journal-title":"Cell"},{"key":"10.1016\/j.cca.2016.10.017_bb0450","doi-asserted-by":"crossref","first-page":"531","DOI":"10.6061\/clinics\/2013(04)15","article-title":"Decreased plasma ADAMTS-13 activity as a predictor of postoperative bleeding in cyanotic congenital heart disease","volume":"68","author":"Soares","year":"2013","journal-title":"Clinics (Sao Paulo)"},{"key":"10.1016\/j.cca.2016.10.017_bb0455","doi-asserted-by":"crossref","first-page":"305","DOI":"10.1160\/TH08-05-0330","article-title":"Increased plasma von Willebrand factor antigen levels but normal von Willebrand factor cleaving protease (ADAMTS13) activity in preeclampsia","volume":"101","author":"Molvarec","year":"2009","journal-title":"Thromb. Haemost."},{"key":"10.1016\/j.cca.2016.10.017_bb0460","doi-asserted-by":"crossref","first-page":"1295","DOI":"10.1182\/blood-2007-09-110700","article-title":"Functional imaging of shear-dependent activity of ADAMTS13 in regulating mural thrombus growth under whole blood flow conditions","volume":"111","author":"Shida","year":"2008","journal-title":"Blood"},{"key":"10.1016\/j.cca.2016.10.017_bb0465","doi-asserted-by":"crossref","first-page":"11","DOI":"10.1182\/blood-2008-02-078170","article-title":"Von Willebrand factor, ADAMTS13, and thrombotic thrombocytopenic purpura","volume":"112","author":"Sadler","year":"2008","journal-title":"Blood"},{"key":"10.1016\/j.cca.2016.10.017_bb0470","doi-asserted-by":"crossref","first-page":"239","DOI":"10.1160\/TH08-03-0161","article-title":"Variations in the ratio between von Willebrand factor and its cleaving protease during systemic inflammation and association with severity and prognosis of organ failure","volume":"101","author":"Claus","year":"2009","journal-title":"Thromb. Haemost."},{"key":"10.1016\/j.cca.2016.10.017_bb0475","doi-asserted-by":"crossref","first-page":"493","DOI":"10.1172\/JCI118440","article-title":"Hypoxia-induced exocytosis of endothelial cell Weibel-Palade bodies. A mechanism for rapid neutrophil recruitment after cardiac preservation","volume":"97","author":"Pinsky","year":"1996","journal-title":"J. Clin. Invest."},{"key":"10.1016\/j.cca.2016.10.017_bb0480","doi-asserted-by":"crossref","first-page":"3164","DOI":"10.1182\/blood.V85.11.3164.bloodjournal85113164","article-title":"Reactive oxygen intermediates induce regulated secretion of von Willebrand factor from cultured human vascular endothelial cells","volume":"85","author":"Vischer","year":"1995","journal-title":"Blood"},{"key":"10.1016\/j.cca.2016.10.017_bb0485","doi-asserted-by":"crossref","first-page":"3993","DOI":"10.4049\/jimmunol.142.11.3993","article-title":"IL-1 and related cytokines enhance thrombin-stimulated PGI2 production in cultured endothelial cells without affecting thrombin-stimulated von Willebrand factor secretion or platelet-activating factor biosynthesis","volume":"142","author":"Zavoico","year":"1989","journal-title":"J. Immunol."},{"key":"10.1016\/j.cca.2016.10.017_bb0490","doi-asserted-by":"crossref","first-page":"3080","DOI":"10.1161\/CIRCULATIONAHA.105.557132","article-title":"Which hemostatic markers add to the predictive value of conventional risk factors for coronary heart disease and ischemic stroke? The Caerphilly study","volume":"112","author":"Smith","year":"2005","journal-title":"Circulation"},{"key":"10.1016\/j.cca.2016.10.017_bb0495","doi-asserted-by":"crossref","first-page":"2151","DOI":"10.1161\/STROKEAHA.110.586289","article-title":"High von Willebrand factor levels increase the risk of stroke: the Rotterdam study","volume":"41","author":"Wieberdink","year":"2010","journal-title":"Stroke"},{"key":"10.1016\/j.cca.2016.10.017_bb0500","doi-asserted-by":"crossref","first-page":"275","DOI":"10.1111\/j.1538-7836.2010.04134.x","article-title":"Plasma levels of von Willebrand factor in the etiologic subtypes of ischemic stroke","volume":"9","author":"Hanson","year":"2011","journal-title":"J. Thromb. Haemost."},{"key":"10.1016\/j.cca.2016.10.017_bb0505","doi-asserted-by":"crossref","first-page":"47","DOI":"10.1161\/01.STR.21.1.47","article-title":"Coagulation factors and the increased risk of stroke in nonvalvular atrial fibrillation","volume":"21","author":"Gustafsson","year":"1990","journal-title":"Stroke"},{"key":"10.1016\/j.cca.2016.10.017_bb0510","doi-asserted-by":"crossref","first-page":"28","DOI":"10.1016\/j.thromres.2008.09.012","article-title":"Changes in plasma von Willebrand factor and ADAMTS13 levels associated with left atrial remodeling in atrial fibrillation","volume":"124","author":"Uemura","year":"2009","journal-title":"Thromb. Res."},{"key":"10.1016\/j.cca.2016.10.017_bb0515","doi-asserted-by":"crossref","first-page":"1387","DOI":"10.1056\/NEJMoa032804","article-title":"C-reactive protein and other circulating markers of inflammation in the prediction of coronary heart disease","volume":"350","author":"Danesh","year":"2004","journal-title":"N. Engl. J. Med."},{"key":"10.1016\/j.cca.2016.10.017_bb0520","doi-asserted-by":"crossref","first-page":"1212","DOI":"10.1016\/j.clinbiochem.2010.07.013","article-title":"The impact of acute atrial fibrillation on the prothrombotic state in patients with essential hypertension","volume":"43","author":"Hou","year":"2010","journal-title":"Clin. Biochem."},{"key":"10.1016\/j.cca.2016.10.017_bb0525","first-page":"5636","article-title":"The application of vWF\/ADAMTS13 in essential hypertension","volume":"7","author":"Ma","year":"2014","journal-title":"Int. J. Clin. Exp. Med."},{"key":"10.1016\/j.cca.2016.10.017_bb0530","doi-asserted-by":"crossref","first-page":"21","DOI":"10.1160\/TH06-04-0211","article-title":"Relatively increased von Willebrand factor activity after off-pump coronary artery bypass graft surgery","volume":"97","author":"Lo","year":"2007","journal-title":"Thromb. Haemost."},{"key":"10.1016\/j.cca.2016.10.017_bb0535","doi-asserted-by":"crossref","first-page":"408","DOI":"10.1160\/TH09-06-0391","article-title":"Loss of high-molecular-weight von Willebrand factor multimers mainly affects platelet aggregation in patients with aortic stenosis","volume":"103","author":"Panzer","year":"2010","journal-title":"Thromb. Haemost."}],"container-title":["Clinica Chimica Acta"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0009898116304223?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0009898116304223?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2023,8,20]],"date-time":"2023-08-20T13:33:46Z","timestamp":1692538426000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0009898116304223"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2016,12]]},"references-count":107,"alternative-id":["S0009898116304223"],"URL":"https:\/\/doi.org\/10.1016\/j.cca.2016.10.017","relation":{},"ISSN":["0009-8981"],"issn-type":[{"value":"0009-8981","type":"print"}],"subject":[],"published":{"date-parts":[[2016,12]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"Update on ADAMTS13 and VWF in cardiovascular and hematological disorders","name":"articletitle","label":"Article Title"},{"value":"Clinica Chimica Acta","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.cca.2016.10.017","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"\u00a9 2016 Elsevier B.V. All rights reserved.","name":"copyright","label":"Copyright"}]}}