{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,20]],"date-time":"2026-08-20T21:24:21Z","timestamp":1787261061854,"version":"build-2736575974"},"reference-count":33,"publisher":"Elsevier BV","issue":"1","license":[{"start":{"date-parts":[[2026,7,1]],"date-time":"2026-07-01T00:00:00Z","timestamp":1782864000000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2026,7,1]],"date-time":"2026-07-01T00:00:00Z","timestamp":1782864000000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/legal\/tdmrep-license"}],"funder":[{"DOI":"10.13039\/100000025","name":"National Institute of Mental Health","doi-asserted-by":"publisher","id":[{"id":"10.13039\/100000025","id-type":"DOI","asserted-by":"publisher"}]},{"DOI":"10.13039\/100003227","name":"Osteogenesis Imperfecta Foundation Inc","doi-asserted-by":"publisher","id":[{"id":"10.13039\/100003227","id-type":"DOI","asserted-by":"publisher"}]},{"DOI":"10.13039\/100006108","name":"National Center for Advancing Translational Sciences","doi-asserted-by":"publisher","id":[{"id":"10.13039\/100006108","id-type":"DOI","asserted-by":"publisher"}]},{"DOI":"10.13039\/100009633","name":"Eunice Kennedy Shriver National Institute of Child Health and Human Development","doi-asserted-by":"publisher","id":[{"id":"10.13039\/100009633","id-type":"DOI","asserted-by":"publisher"}]},{"DOI":"10.13039\/100000069","name":"National Institute of Arthritis and Musculoskeletal and Skin Diseases","doi-asserted-by":"publisher","id":[{"id":"10.13039\/100000069","id-type":"DOI","asserted-by":"publisher"}]},{"DOI":"10.13039\/100000072","name":"National Institute of Dental and Craniofacial Research","doi-asserted-by":"publisher","id":[{"id":"10.13039\/100000072","id-type":"DOI","asserted-by":"publisher"}]},{"DOI":"10.13039\/100016650","name":"Rare Diseases Clinical Research Network","doi-asserted-by":"publisher","award":["1U54AR068069-0"],"award-info":[{"award-number":["1U54AR068069-0"]}],"id":[{"id":"10.13039\/100016650","id-type":"DOI","asserted-by":"publisher"}]}],"content-domain":{"domain":["clinicalkey.com","clinicalkey.com.au","clinicalkey.es","clinicalkey.fr","clinicalkey.jp","journal.chestnet.org","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["CHEST"],"published-print":{"date-parts":[[2026,7]]},"DOI":"10.1016\/j.chest.2026.02.030","type":"journal-article","created":{"date-parts":[[2026,3,20]],"date-time":"2026-03-20T16:17:27Z","timestamp":1774023447000},"page":"181-189","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":1,"title":["Evaluation of Lung Disease in Adults With Osteogenesis Imperfecta"],"prefix":"10.1016","volume":"170","author":[{"ORCID":"https:\/\/orcid.org\/0009-0006-7333-9859","authenticated-orcid":false,"given":"Chloe E.","family":"Derocher","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Erin M.","family":"Carter","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Debra","family":"Dyer","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Deborah","family":"Krakow","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Malinda","family":"Wu","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Robert A.","family":"Sandhaus","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Cathleen L.","family":"Raggio","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"issue":"8","key":"10.1016\/j.chest.2026.02.030_bib1","doi-asserted-by":"crossref","DOI":"10.1002\/jbm4.10174","article-title":"Osteogenesis imperfecta: new perspectives from clinical and translational research","volume":"3","author":"Tauer","year":"2019","journal-title":"JBMR Plus"},{"issue":"9","key":"10.1016\/j.chest.2026.02.030_bib2","doi-asserted-by":"crossref","first-page":"540","DOI":"10.1038\/nrendo.2011.81","article-title":"New perspectives on osteogenesis imperfecta","volume":"7","author":"Forlino","year":"2011","journal-title":"Nat Rev Endocrinol"},{"issue":"9418","key":"10.1016\/j.chest.2026.02.030_bib3","doi-asserted-by":"crossref","first-page":"1377","DOI":"10.1016\/S0140-6736(04)16051-0","article-title":"Osteogenesis imperfecta","volume":"363","author":"Rauch","year":"2004","journal-title":"Lancet"},{"key":"10.1016\/j.chest.2026.02.030_bib4","doi-asserted-by":"crossref","first-page":"1470","DOI":"10.1002\/ajmg.a.36545","article-title":"Osteogenesis imperfecta: clinical diagnosis, nomenclature and severity assessment","volume":"164A","author":"Van Dijk","year":"2014","journal-title":"Am J Med Genet A"},{"issue":"4","key":"10.1016\/j.chest.2026.02.030_bib5","article-title":"Mortality and morbidity in patients with osteogenesis imperfecta in Denmark","volume":"65","author":"Folkestad","year":"2018","journal-title":"Dan Med J"},{"issue":"3","key":"10.1016\/j.chest.2026.02.030_bib6","doi-asserted-by":"crossref","first-page":"806","DOI":"10.1016\/j.chest.2024.09.004","article-title":"Risk of pulmonary diseases in osteogenesis imperfecta in Denmark: a register-based cohort study","volume":"167","author":"Andersen","year":"2025","journal-title":"Chest"},{"issue":"8","key":"10.1016\/j.chest.2026.02.030_bib7","doi-asserted-by":"crossref","first-page":"627","DOI":"10.1136\/jcp.49.8.627","article-title":"Causes of death in osteogenesis imperfecta","volume":"49","author":"McAllion","year":"1996","journal-title":"J Clin Pathol"},{"issue":"16","key":"10.1016\/j.chest.2026.02.030_bib8","doi-asserted-by":"crossref","first-page":"1673","DOI":"10.1097\/00007632-199908150-00008","article-title":"Spinal deformity, pulmonary compromise, and quality of life in osteogenesis imperfecta","volume":"24","author":"Widmann","year":"1999","journal-title":"Spine"},{"issue":"9","key":"10.1016\/j.chest.2026.02.030_bib9","doi-asserted-by":"crossref","first-page":"2295","DOI":"10.1007\/s00586-022-07260-5","article-title":"Prevalence of scoliosis and impaired pulmonary function in patients with type III osteogenesis imperfecta","volume":"31","author":"Keuning","year":"2022","journal-title":"Eur Spine J"},{"key":"10.1016\/j.chest.2026.02.030_bib10","series-title":"Osteogenesis Imperfecta","first-page":"335","article-title":"Pulmonary function in osteogenesis imperfecta","author":"Sandhaus","year":"2014"},{"issue":"15","key":"10.1016\/j.chest.2026.02.030_bib11","doi-asserted-by":"crossref","first-page":"1057","DOI":"10.1097\/BRS.0000000000003012","article-title":"Scoliosis and cardiopulmonary outcomes in osteogenesis imperfecta patients","volume":"44","author":"Bronheim","year":"2019","journal-title":"Spine"},{"issue":"1","key":"10.1016\/j.chest.2026.02.030_bib12","doi-asserted-by":"crossref","first-page":"455","DOI":"10.1186\/s13023-024-03452-y","article-title":"Lung function in adult patients with osteogenesis imperfecta: a cohort study","volume":"19","author":"Lenoir","year":"2024","journal-title":"Orphanet J Rare Dis"},{"key":"10.1016\/j.chest.2026.02.030_bib13","doi-asserted-by":"crossref","first-page":"250","DOI":"10.1016\/j.ijcard.2016.09.107","article-title":"Cardiovascular disease in patients with osteogenesis imperfecta\u2014a nationwide, register-based cohort study","volume":"225","author":"Folkestad","year":"2016","journal-title":"Int J Cardiol"},{"issue":"1","key":"10.1016\/j.chest.2026.02.030_bib14","doi-asserted-by":"crossref","first-page":"54","DOI":"10.1161\/01.CIR.73.1.54","article-title":"Cardiovascular involvement in osteogenesis imperfecta","volume":"73","author":"Hortop","year":"1986","journal-title":"Circulation"},{"issue":"3","key":"10.1016\/j.chest.2026.02.030_bib15","doi-asserted-by":"crossref","first-page":"523","DOI":"10.1016\/j.ahj.2010.11.006","article-title":"Cardiovascular abnormalities in adults with osteogenesis imperfecta","volume":"161","author":"Radunovic","year":"2011","journal-title":"Am Heart J"},{"issue":"2","key":"10.1016\/j.chest.2026.02.030_bib16","doi-asserted-by":"crossref","first-page":"211","DOI":"10.1093\/jbmr\/zjae197","article-title":"Cardiovascular disease in adults with osteogenesis imperfecta: clinical characteristics, care recommendations, and research priorities identified using a modified Delphi technique","volume":"40","author":"Folkestad","year":"2025","journal-title":"J Bone Miner Res"},{"issue":"12","key":"10.1016\/j.chest.2026.02.030_bib17","doi-asserted-by":"crossref","first-page":"2833","DOI":"10.1097\/CORR.0000000000001400","article-title":"Cardiopulmonary status in adults with osteogenesis imperfecta: intrinsic lung disease may contribute more than scoliosis","volume":"478","author":"Khan","year":"2020","journal-title":"Clin Orthop Relat Res"},{"key":"10.1016\/j.chest.2026.02.030_bib18","unstructured":"Cobb JR. Outline for the study of scoliosis. In: Edwards JW, ed. The American Academy of Orthopedic Surgeons Instructional Course Lectures. Vol 5. 1948;261-275."},{"issue":"4","key":"10.1016\/j.chest.2026.02.030_bib19","doi-asserted-by":"crossref","first-page":"248","DOI":"10.1136\/thx.53.4.248","article-title":"Airway wall thickness in patients with near fatal asthma and control groups: assessment with high resolution computed tomographic scanning","volume":"53","author":"Awadh","year":"1998","journal-title":"Thorax"},{"key":"10.1016\/j.chest.2026.02.030_bib20","series-title":"SF36 Health Survey: Manual and Interpretation Guide","author":"Ware","year":"1993"},{"key":"10.1016\/j.chest.2026.02.030_bib21","series-title":"St George\u2019s Respiratory Questionnaire Manual","author":"Jones","year":"2009"},{"issue":"2","key":"10.1016\/j.chest.2026.02.030_bib22","doi-asserted-by":"crossref","first-page":"193","DOI":"10.1016\/0165-1781(89)90047-4","article-title":"The Pittsburgh Sleep Quality Index: a new instrument for psychiatric practice and research","volume":"28","author":"Buysse","year":"1989","journal-title":"Psychiatry Res"},{"key":"10.1016\/j.chest.2026.02.030_bib23","first-page":"835","article-title":"An instrument to measure functional status outcomes for disorders of excessive sleepiness","volume":"20","author":"Weaver","year":"1997","journal-title":"Sleep"},{"key":"10.1016\/j.chest.2026.02.030_bib24","doi-asserted-by":"crossref","first-page":"149","DOI":"10.1016\/j.ijcard.2015.06.001","article-title":"Heart disease in patients with osteogenesis imperfecta. A systematic review","volume":"196","author":"Ashournia","year":"2015","journal-title":"Int J Cardiol"},{"issue":"3","key":"10.1016\/j.chest.2026.02.030_bib25","doi-asserted-by":"crossref","first-page":"H565","DOI":"10.1152\/ajpheart.00535.2024","article-title":"Cardiac health, type I collagen, and aging in the oim\/oim mouse model of osteogenesis imperfecta and a cohort of adults with OI","volume":"328","author":"Lafaver","year":"2025","journal-title":"Am J Physiol Heart Circ Physiol"},{"issue":"2","key":"10.1016\/j.chest.2026.02.030_bib26","doi-asserted-by":"crossref","first-page":"111","DOI":"10.15386\/cjmed-1060","article-title":"Short review on the diagnosis and treatment of bronchiectasis","volume":"92","author":"Lesan","year":"2019","journal-title":"Med Pharm Rep"},{"issue":"11","key":"10.1016\/j.chest.2026.02.030_bib27","doi-asserted-by":"crossref","first-page":"1335","DOI":"10.6061\/clinics\/2012(11)19","article-title":"Airway disease: similarities and differences between asthma, COPD and bronchiectasis","volume":"67","author":"Athanazio","year":"2012","journal-title":"Clinics (Sao Paulo)"},{"key":"10.1016\/j.chest.2026.02.030_bib28","doi-asserted-by":"crossref","first-page":"266","DOI":"10.1186\/s12887-025-05573-0","article-title":"Pulmonary function and exercise capacity in mild early-onset idiopathic scoliosis: a case-control study","volume":"25","author":"Wang","year":"2025","journal-title":"BMC Pediatrics"},{"key":"10.1016\/j.chest.2026.02.030_bib29","doi-asserted-by":"crossref","first-page":"2135","DOI":"10.1016\/j.spinee.2024.07.006","article-title":"Pulmonary function in patients with idiopathic scoliosis 40 years after diagnosis","volume":"24","author":"Ragborg","year":"2024","journal-title":"Spine J"},{"key":"10.1016\/j.chest.2026.02.030_bib30","doi-asserted-by":"crossref","first-page":"537","DOI":"10.2106\/JBJS.22.00277","article-title":"Retrospective analysis of associated anomalies in 636 patients with operatively treated congenital scoliosis","volume":"105","author":"Wu","year":"2023","journal-title":"J Bone Joint Surg"},{"key":"10.1016\/j.chest.2026.02.030_bib31","doi-asserted-by":"crossref","first-page":"635","DOI":"10.1007\/s43390-024-00819-w","article-title":"Respiratory function and respiratory muscle strength in adolescent idiopathic scoliosis","volume":"12","author":"Cetinkaya","year":"2024","journal-title":"Spine Deform"},{"key":"10.1016\/j.chest.2026.02.030_bib32","doi-asserted-by":"crossref","unstructured":"LoMauro A, Aliverti A. Changes in interpretation of lung volumes according to respiratory references: the emblematic case of osteogenesis imperfecta. 2025 IEEE International Conference on Metrology for eXtended Reality, Artificial Intelligence and Neural Engineering (MetroXRAINE); Ancona, Italy; October 22-24. 2025;347-351.","DOI":"10.1109\/MetroXRAINE66377.2025.11340485"},{"issue":"5","key":"10.1016\/j.chest.2026.02.030_bib33","doi-asserted-by":"crossref","first-page":"1164","DOI":"10.1002\/ajmg.a.63132","article-title":"Nosology of genetic skeletal disorders: 2023 revision","volume":"191","author":"Unger","year":"2023","journal-title":"Am J Med Genet A"}],"container-title":["CHEST"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0012369226003752?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0012369226003752?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2026,8,20]],"date-time":"2026-08-20T20:31:49Z","timestamp":1787257909000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0012369226003752"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2026,7]]},"references-count":33,"journal-issue":{"issue":"1","published-print":{"date-parts":[[2026,7]]}},"alternative-id":["S0012369226003752"],"URL":"https:\/\/doi.org\/10.1016\/j.chest.2026.02.030","relation":{},"ISSN":["0012-3692"],"issn-type":[{"value":"0012-3692","type":"print"}],"subject":[],"published":{"date-parts":[[2026,7]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"Evaluation of Lung Disease in Adults With Osteogenesis Imperfecta","name":"articletitle","label":"Article Title"},{"value":"CHEST","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.chest.2026.02.030","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"\u00a9 2026 American College of Chest Physicians. Published by Elsevier Inc. All rights are reserved, including those for text and data mining, AI training, and similar technologies.","name":"copyright","label":"Copyright"}]}}