{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,21]],"date-time":"2026-10-21T12:42:52Z","timestamp":1792586572418,"version":"4.5.0"},"reference-count":16,"publisher":"Elsevier BV","license":[{"start":{"date-parts":[[2026,1,1]],"date-time":"2026-01-01T00:00:00Z","timestamp":1767225600000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2026,1,1]],"date-time":"2026-01-01T00:00:00Z","timestamp":1767225600000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/legal\/tdmrep-license"},{"start":{"date-parts":[[2026,6,26]],"date-time":"2026-06-26T00:00:00Z","timestamp":1782432000000},"content-version":"vor","delay-in-days":176,"URL":"http:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"funder":[{"DOI":"10.13039\/501100001691","name":"Japan Society for the Promotion of Science","doi-asserted-by":"publisher","award":["25K02979"],"award-info":[{"award-number":["25K02979"]}],"id":[{"id":"10.13039\/501100001691","id-type":"DOI","asserted-by":"publisher"}]},{"DOI":"10.13039\/501100001691","name":"Japan Society for the Promotion of Science","doi-asserted-by":"publisher","award":["23H02827"],"award-info":[{"award-number":["23H02827"]}],"id":[{"id":"10.13039\/501100001691","id-type":"DOI","asserted-by":"publisher"}]}],"content-domain":{"domain":["clinicalkey.com","clinicalkey.com.au","clinicalkey.es","clinicalkey.fr","clinicalkey.jp","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Clinical Neurophysiology Practice"],"published-print":{"date-parts":[[2026]]},"DOI":"10.1016\/j.cnp.2026.06.011","type":"journal-article","created":{"date-parts":[[2026,6,26]],"date-time":"2026-06-26T23:44:03Z","timestamp":1782517443000},"page":"522-527","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":0,"special_numbering":"C","title":["Decremental responses following repetitive nerve stimulation in spinal and bulbar muscular atrophy"],"prefix":"10.1016","volume":"11","author":[{"given":"Keisuke","family":"Tachiyama","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Masahiro","family":"Nakamori","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Yuki","family":"Fujii","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Keiichi","family":"Hokkoku","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Dai","family":"Agari","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Shoji","family":"Hemmi","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Eiichi","family":"Nomura","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Yuki","family":"Hatanaka","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Katsumi","family":"Kurokawa","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Masahiro","family":"Sonoo","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Hirofumi","family":"Maruyama","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"key":"10.1016\/j.cnp.2026.06.011_bb0005","doi-asserted-by":"crossref","first-page":"481","DOI":"10.1113\/jphysiol.1973.sp010319","article-title":"The formation of synapses in reinnervated mammalian striated muscle","volume":"233","author":"Bennett","year":"1973","journal-title":"J. Physiol."},{"key":"10.1016\/j.cnp.2026.06.011_bb0010","doi-asserted-by":"crossref","first-page":"204","DOI":"10.1212\/WNL.31.2.202","article-title":"Motor neuron disease: decremental responses to repetitive nerve stimulation","volume":"31","author":"Bernstein","year":"1981","journal-title":"Neurology"},{"key":"10.1016\/j.cnp.2026.06.011_bb0015","doi-asserted-by":"crossref","first-page":"40","DOI":"10.1016\/j.cnp.2025.02.003","article-title":"Correlation between decremental responses in repetitive nerve stimulation and disease progression rate in patients with amyotrophic lateral sclerosis","volume":"10","author":"Fujii","year":"2025","journal-title":"Clin. Neurophysiol. Pract."},{"key":"10.1016\/j.cnp.2026.06.011_bb0020","doi-asserted-by":"crossref","first-page":"823","DOI":"10.1016\/j.clinph.2017.02.021","article-title":"Utility of repetitive nerve stimulation test for ALS diagnosis","volume":"128","author":"Hatanaka","year":"2017","journal-title":"Clin. Neurophysiol."},{"key":"10.1016\/j.cnp.2026.06.011_bb0025","doi-asserted-by":"crossref","first-page":"76","DOI":"10.1111\/j.1468-1331.2008.02349.x","article-title":"Muscular fatigue and decremental response to repetitive nerve stimulation in X-linked spinobulbar muscular atrophy","volume":"16","author":"Inoue","year":"2009","journal-title":"Eur. J. Neurol."},{"key":"10.1016\/j.cnp.2026.06.011_bb0030","doi-asserted-by":"crossref","first-page":"2530","DOI":"10.1016\/j.clinph.2011.05.019","article-title":"Decremental responses to repetitive nerve stimulation (RNS) in motor neuron disease","volume":"122","author":"Iwanami","year":"2011","journal-title":"Clin. Neurophysiol."},{"key":"10.1016\/j.cnp.2026.06.011_bb0035","doi-asserted-by":"crossref","first-page":"613","DOI":"10.1002\/mus.880120802","article-title":"AAEE Minimonograph #33: electrodiagnostic approach to defects of neuromuscular transmission","volume":"12","author":"Keesey","year":"1989","journal-title":"Muscle Nerve"},{"key":"10.1016\/j.cnp.2026.06.011_bb0040","doi-asserted-by":"crossref","first-page":"747","DOI":"10.1002\/mus.880170708","article-title":"Decremental motor responses to repetitive nerve stimulation in ALS","volume":"17","author":"Killian","year":"1994","journal-title":"Muscle Nerve"},{"key":"10.1016\/j.cnp.2026.06.011_bb0045","doi-asserted-by":"crossref","first-page":"32","DOI":"10.3988\/jcn.2013.9.1.32","article-title":"Decremental responses to repetitive nerve stimulation in X-linked bulbospinal muscular atrophy","volume":"9","author":"Kim","year":"2013","journal-title":"J. Clin. Neurol."},{"key":"10.1016\/j.cnp.2026.06.011_bb0050","doi-asserted-by":"crossref","first-page":"269","DOI":"10.1111\/j.1600-0404.1983.tb04838.x","article-title":"Evoked responses in normal and diseased muscle with particular reference to twitch potentiation","volume":"68","author":"Krarup","year":"1983","journal-title":"Acta Neurol. Scand."},{"key":"10.1016\/j.cnp.2026.06.011_bb0055","doi-asserted-by":"crossref","first-page":"627","DOI":"10.1212\/WNL.9.10.627","article-title":"Myasthenic syndrome in patients with amyotrophic lateral sclerosis","volume":"9","author":"Mulder","year":"1959","journal-title":"Neurology"},{"key":"10.1016\/j.cnp.2026.06.011_bb0060","doi-asserted-by":"crossref","first-page":"167","DOI":"10.1097\/00004691-199304000-00004","article-title":"Clinical neurophysiology of disorders of the neuromuscular junction","volume":"10","author":"Sanders","year":"1993","journal-title":"J. Clin. Neurophysiol."},{"key":"10.1016\/j.cnp.2026.06.011_bb0065","doi-asserted-by":"crossref","first-page":"185","DOI":"10.1016\/S1047-9651(02)00129-8","article-title":"Repetitive nerve stimulation and exercise testing","volume":"14","author":"Shapiro","year":"2003","journal-title":"Phys. Med. Rehabil. Clin. N. Am."},{"key":"10.1016\/j.cnp.2026.06.011_bb0070","doi-asserted-by":"crossref","first-page":"403","DOI":"10.1016\/0022-510X(75)90166-5","article-title":"Single fibre electromyography in various processes affecting the anterior horn cell","volume":"24","author":"St\u00e5lberg","year":"1975","journal-title":"J. Neurol. Sci."},{"key":"10.1016\/j.cnp.2026.06.011_bb0075","doi-asserted-by":"crossref","first-page":"1","DOI":"10.1097\/CND.0000000000000479","article-title":"Utility of the repetitive nerve stimulation test and needle EMG in the trapezius muscle for the early diagnosis of ALS","volume":"26","author":"Takahashi","year":"2024","journal-title":"J. Clin. Neuromuscl. Dis."},{"key":"10.1016\/j.cnp.2026.06.011_bb0080","doi-asserted-by":"crossref","first-page":"211","DOI":"10.1016\/j.cnp.2024.06.003","article-title":"The speed of completion of the decremental responses on repetitive nerve stimulation","volume":"28","author":"Ueta","year":"2024","journal-title":"Clin. Neurophysiol. Pract."}],"container-title":["Clinical Neurophysiology Practice"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S2467981X26000569?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S2467981X26000569?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2026,10,21]],"date-time":"2026-10-21T12:01:11Z","timestamp":1792584071000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S2467981X26000569"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2026]]},"references-count":16,"alternative-id":["S2467981X26000569"],"URL":"https:\/\/doi.org\/10.1016\/j.cnp.2026.06.011","relation":{},"ISSN":["2467-981X"],"issn-type":[{"value":"2467-981X","type":"print"}],"subject":[],"published":{"date-parts":[[2026]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"Decremental responses following repetitive nerve stimulation in spinal and bulbar muscular atrophy","name":"articletitle","label":"Article Title"},{"value":"Clinical Neurophysiology Practice","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.cnp.2026.06.011","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"\u00a9 2026 The Authors. Published by Elsevier B.V. on behalf of International Federation of Clinical Neurophysiology.","name":"copyright","label":"Copyright"}]}}