{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,27]],"date-time":"2026-10-27T20:05:30Z","timestamp":1793131530976,"version":"4.5.0"},"reference-count":12,"publisher":"Elsevier BV","issue":"5","license":[{"start":{"date-parts":[[2023,5,1]],"date-time":"2023-05-01T00:00:00Z","timestamp":1682899200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2023,5,1]],"date-time":"2023-05-01T00:00:00Z","timestamp":1682899200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/legal\/tdmrep-license"}],"content-domain":{"domain":["clinicalkey.com","clinicalkey.com.au","clinicalkey.es","clinicalkey.fr","clinicalkey.jp","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Current Problems in Cardiology"],"published-print":{"date-parts":[[2023,5]]},"DOI":"10.1016\/j.cpcardiol.2022.101110","type":"journal-article","created":{"date-parts":[[2022,1,7]],"date-time":"2022-01-07T10:59:34Z","timestamp":1641553174000},"page":"101110","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":1,"title":["Review of the Myelodysplastic Syndrome as a Cause of Group 5 Pulmonary Arterial Hypertension: An Orphan Disease in an Orphan Pulmonary Hypertension Group"],"prefix":"10.1016","volume":"48","author":[{"given":"Diana-Laura","family":"Carrillo-Rocha","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ernesto","family":"Roldan-Valadez","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Guillermo","family":"Cueto-Robledo","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Marisol","family":"Garcia-Cesar","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Hector-Daniel","family":"Cueto-Romero","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"key":"10.1016\/j.cpcardiol.2022.101110_bib0001","doi-asserted-by":"crossref","first-page":"129","DOI":"10.1002\/ajh.24930","article-title":"Myelodysplastic syndromes: 2018 update on diagnosis, risk-stratification and management","volume":"93","author":"Montalban-Bravo","year":"2018","journal-title":"Am J Hematol"},{"key":"10.1016\/j.cpcardiol.2022.101110_bib0002","doi-asserted-by":"crossref","first-page":"869","DOI":"10.1378\/chest.112.4.869","article-title":"Portopulmonary hypertension: the next step","volume":"112","author":"Krowka","year":"1997","journal-title":"Chest"},{"key":"10.1016\/j.cpcardiol.2022.101110_bib0003","doi-asserted-by":"crossref","first-page":"555","DOI":"10.1007\/BF03401794","article-title":"Molecular defects in chronic myeloproliferative disorders","volume":"6","author":"Albitar","year":"2000","journal-title":"Mol Med"},{"key":"10.1016\/j.cpcardiol.2022.101110_bib0004","first-page":"40","article-title":"The Story of Group 5 Pulmonary Hypertension","volume":"20","author":"Doran-Bostwick","year":"2021","journal-title":"Advances in Pulmonary Hypertension"},{"key":"10.1016\/j.cpcardiol.2022.101110_bib0005","doi-asserted-by":"crossref","DOI":"10.1016\/j.cpcardiol.2020.100747","article-title":"Portopulmonary Hypertension: Prevalence, Clinical and Hemodynamic Features","volume":"46","author":"Navarro-Vergara","year":"2021","journal-title":"Curr Probl Cardiol"},{"key":"10.1016\/j.cpcardiol.2022.101110_bib0006","article-title":"Corrigendum to \"Portopulmonary Hypertension: Prevalence, Clinical and Hemodynamic Features\". [Current Problems in Cardiology 46\/3 (March 2021) 100747]","volume":"46","author":"Navarro-Vergara","year":"2021","journal-title":"Curr Probl Cardiol"},{"key":"10.1016\/j.cpcardiol.2022.101110_bib0007","doi-asserted-by":"crossref","DOI":"10.1183\/13993003.01897-2018","article-title":"Pulmonary hypertension due to left heart disease","volume":"53","author":"Vachiery","year":"2019","journal-title":"Eur Respir J"},{"key":"10.1016\/j.cpcardiol.2022.101110_bib0008","article-title":"Epidemiology, pathogenesis, and clinical approach in group 5 pulmonary hypertension","volume":"7","author":"Al-Qadi","year":"2020","journal-title":"Front Med (Lausanne)"},{"key":"10.1016\/j.cpcardiol.2022.101110_bib0009","doi-asserted-by":"crossref","first-page":"801","DOI":"10.1378\/chest.120.3.801","article-title":"Unexplained pulmonary hypertension in chronic myeloproliferative disorders","volume":"120","author":"Dingli","year":"2001","journal-title":"Chest"},{"key":"10.1016\/j.cpcardiol.2022.101110_bib0010","doi-asserted-by":"crossref","first-page":"2391","DOI":"10.1182\/blood-2016-03-643544","article-title":"The 2016 revision to the World Health Organization classification of myeloid neoplasms and acute leukemia","volume":"127","author":"Arber","year":"2016","journal-title":"Blood"},{"key":"10.1016\/j.cpcardiol.2022.101110_bib0011","doi-asserted-by":"crossref","first-page":"883","DOI":"10.1007\/s00277-013-1904-0","article-title":"Effectiveness of bosentan in a case of pulmonary arterial hypertension associated with myelodysplastic syndrome","volume":"93","author":"Gamez-Lopez","year":"2014","journal-title":"Ann Hematol"},{"key":"10.1016\/j.cpcardiol.2022.101110_bib0012","doi-asserted-by":"crossref","first-page":"2723","DOI":"10.3109\/10428194.2016.1160086","article-title":"Pulmonary arterial pressure in patients with myelodysplastic syndromes","volume":"57","author":"Sill","year":"2016","journal-title":"Leuk Lymphoma"}],"container-title":["Current Problems in Cardiology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0146280622000093?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0146280622000093?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2025,9,27]],"date-time":"2025-09-27T02:17:39Z","timestamp":1758939459000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0146280622000093"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2023,5]]},"references-count":12,"journal-issue":{"issue":"5","published-print":{"date-parts":[[2023,5]]}},"alternative-id":["S0146280622000093"],"URL":"https:\/\/doi.org\/10.1016\/j.cpcardiol.2022.101110","relation":{},"ISSN":["0146-2806"],"issn-type":[{"value":"0146-2806","type":"print"}],"subject":[],"published":{"date-parts":[[2023,5]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"Review of the Myelodysplastic Syndrome as a Cause of Group 5 Pulmonary Arterial Hypertension: An Orphan Disease in an Orphan Pulmonary Hypertension Group","name":"articletitle","label":"Article Title"},{"value":"Current Problems in Cardiology","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.cpcardiol.2022.101110","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"name":"copyright","label":"Copyright"}],"article-number":"101110"}}