{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,2,12]],"date-time":"2026-02-12T13:04:50Z","timestamp":1770901490732,"version":"3.50.1"},"reference-count":50,"publisher":"Elsevier BV","issue":"2","license":[{"start":{"date-parts":[[2024,4,1]],"date-time":"2024-04-01T00:00:00Z","timestamp":1711929600000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2024,4,1]],"date-time":"2024-04-01T00:00:00Z","timestamp":1711929600000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/legal\/tdmrep-license"},{"start":{"date-parts":[[2024,4,1]],"date-time":"2024-04-01T00:00:00Z","timestamp":1711929600000},"content-version":"stm-asf","delay-in-days":0,"URL":"https:\/\/doi.org\/10.15223\/policy-017"},{"start":{"date-parts":[[2024,4,1]],"date-time":"2024-04-01T00:00:00Z","timestamp":1711929600000},"content-version":"stm-asf","delay-in-days":0,"URL":"https:\/\/doi.org\/10.15223\/policy-037"},{"start":{"date-parts":[[2024,4,1]],"date-time":"2024-04-01T00:00:00Z","timestamp":1711929600000},"content-version":"stm-asf","delay-in-days":0,"URL":"https:\/\/doi.org\/10.15223\/policy-012"},{"start":{"date-parts":[[2024,4,1]],"date-time":"2024-04-01T00:00:00Z","timestamp":1711929600000},"content-version":"stm-asf","delay-in-days":0,"URL":"https:\/\/doi.org\/10.15223\/policy-029"},{"start":{"date-parts":[[2024,4,1]],"date-time":"2024-04-01T00:00:00Z","timestamp":1711929600000},"content-version":"stm-asf","delay-in-days":0,"URL":"https:\/\/doi.org\/10.15223\/policy-004"}],"content-domain":{"domain":["clinicalkey.com","clinicalkey.com.au","clinicalkey.es","clinicalkey.fr","clinicalkey.jp","theclinics.com","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Dermatologic Clinics"],"published-print":{"date-parts":[[2024,4]]},"DOI":"10.1016\/j.det.2023.08.009","type":"journal-article","created":{"date-parts":[[2023,9,15]],"date-time":"2023-09-15T04:46:27Z","timestamp":1694753187000},"page":"219-229","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":3,"title":["Neutrophilic Urticarial Dermatosis"],"prefix":"10.1016","volume":"42","author":[{"given":"Amarachi","family":"Orakwue","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Jeremy","family":"Bray","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Nneka","family":"Comfere","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Olayemi","family":"Sokumbi","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"78","reference":[{"issue":"1","key":"10.1016\/j.det.2023.08.009_bib1","doi-asserted-by":"crossref","DOI":"10.1097\/MD.0b013e3181943f5e","article-title":"Neutrophilic Urticarial Dermatosis: A Variant of Neutrophilic Urticaria Strongly Associated With Systemic Disease. Report of 9 New Cases and Review of the Literature","volume":"88","author":"Kieffer","year":"2009","journal-title":"Medicine"},{"issue":"12","key":"10.1016\/j.det.2023.08.009_bib2","doi-asserted-by":"crossref","first-page":"735","DOI":"10.1016\/j.annder.2018.06.010","article-title":"Neutrophilic urticarial dermatosis: A review","volume":"145","author":"Gusdorf","year":"2018","journal-title":"Ann Dermatol Venereol"},{"issue":"3","key":"10.1016\/j.det.2023.08.009_bib3","doi-asserted-by":"crossref","first-page":"311","DOI":"10.1111\/ced.13344","article-title":"Neutrophilic urticarial dermatosis: a novel association with poststreptococcal rheumatic disease","volume":"43","author":"Salam","year":"2018","journal-title":"Clin Exp Dermatol"},{"issue":"4","key":"10.1016\/j.det.2023.08.009_bib4","doi-asserted-by":"crossref","first-page":"685","DOI":"10.1111\/jdv.15984","article-title":"Neutrophilic urticarial dermatosis: an entity bridging monogenic and polygenic autoinflammatory disorders, and beyond","volume":"34","author":"Gusdorf","year":"2020","journal-title":"J\u00a0Eur Acad Dermatol Venereol"},{"issue":"3","key":"10.1016\/j.det.2023.08.009_bib5","first-page":"20","article-title":"Neutrophilic Urticarial Dermatosis Without Underlying Systemic Disease","volume":"13","author":"Gillihan","year":"2020","journal-title":"J\u00a0Clin Aesthet Dermatol"},{"issue":"6","key":"10.1016\/j.det.2023.08.009_bib6","doi-asserted-by":"crossref","first-page":"1289","DOI":"10.1016\/j.jaad.2012.04.027","article-title":"Clinical and histopathologic review of Schnitzler syndrome: the Mayo Clinic experience (1972-2011)","volume":"67","author":"Sokumbi","year":"2012","journal-title":"J\u00a0Am Acad Dermatol"},{"key":"10.1016\/j.det.2023.08.009_bib7","doi-asserted-by":"crossref","first-page":"5739","DOI":"10.2147\/JIR.S343261","article-title":"Improving Diagnosis and Clinical Management of Acquired Systemic Autoinflammatory Diseases","volume":"15","author":"Al-Hakim","year":"2022","journal-title":"J\u00a0Inflamm Res"},{"key":"10.1016\/j.det.2023.08.009_bib8","doi-asserted-by":"crossref","first-page":"38","DOI":"10.1186\/1750-1172-5-38","article-title":"The Schnitzler syndrome","volume":"5","author":"Lipsker","year":"2010","journal-title":"Orphanet J Rare Dis"},{"issue":"1","key":"10.1016\/j.det.2023.08.009_bib9","doi-asserted-by":"crossref","first-page":"260","DOI":"10.1016\/j.jaci.2007.09.021","article-title":"IL-1 blockade in Schnitzler syndrome: ex\u00a0vivo findings correlate with clinical remission","volume":"121","author":"Ryan","year":"2008","journal-title":"J\u00a0Allergy Clin Immunol"},{"key":"10.1016\/j.det.2023.08.009_bib10","doi-asserted-by":"crossref","DOI":"10.1177\/1759720X221117880","article-title":"New insights on multigenic autoinflammatory diseases","volume":"14","author":"Efthimiou","year":"2022","journal-title":"Ther Adv Musculoskelet Dis"},{"issue":"2","key":"10.1016\/j.det.2023.08.009_bib11","doi-asserted-by":"crossref","first-page":"177","DOI":"10.1111\/all.13035","article-title":"Schnitzler syndrome: validation and applicability of diagnostic criteria in real-life patients","volume":"72","author":"Gusdorf","year":"2017","journal-title":"Allergy"},{"issue":"6","key":"10.1016\/j.det.2023.08.009_bib12","first-page":"625","article-title":"Schnitzler Syndrome With Delirium and Vertigo: The Utility of Neurologic Manifestations in Diagnosis","volume":"16","author":"Tolkachjov","year":"2017","journal-title":"J\u00a0Drugs Dermatol JDD"},{"issue":"3","key":"10.1016\/j.det.2023.08.009_bib13","doi-asserted-by":"crossref","first-page":"395","DOI":"10.1053\/j.seminoncol.2016.02.017","article-title":"Cutaneous manifestations of multiple myeloma and other plasma cell proliferative disorders","volume":"43","author":"Bhutani","year":"2016","journal-title":"Semin Oncol"},{"issue":"9","key":"10.1016\/j.det.2023.08.009_bib14","doi-asserted-by":"crossref","first-page":"1361","DOI":"10.2169\/internalmedicine.0359-22","article-title":"Schnitzler Syndrome Presenting as a Fever of Unknown Origin with Elevated Alkaline Phosphatase Levels","volume":"62","author":"Kano","year":"2023","journal-title":"Intern Med"},{"issue":"1","key":"10.1016\/j.det.2023.08.009_bib15","doi-asserted-by":"crossref","first-page":"151","DOI":"10.1186\/s13023-019-1117-2","article-title":"Schnitzler\u2019s syndrome - a novel hypothesis of a shared pathophysiologic mechanism with Waldenstr\u00f6m\u2019s disease","volume":"14","author":"van Leersum","year":"2019","journal-title":"Orphanet J Rare Dis"},{"issue":"2","key":"10.1016\/j.det.2023.08.009_bib16","doi-asserted-by":"crossref","first-page":"91","DOI":"10.1097\/MD.0000000000000021","article-title":"Adult-onset Still disease: manifestations, treatment, outcome, and prognostic factors in 57 patients","volume":"93","author":"Gerfaud-Valentin","year":"2014","journal-title":"Medicine (Baltim)"},{"issue":"6","key":"10.1016\/j.det.2023.08.009_bib17","doi-asserted-by":"crossref","first-page":"1003","DOI":"10.1016\/j.jaad.2005.02.032","article-title":"Histopathology of persistent papules and plaques in adult-onset Still's disease","volume":"52","author":"Lee","year":"2005","journal-title":"J\u00a0Am Acad Dermatol"},{"issue":"2","key":"10.1016\/j.det.2023.08.009_bib18","doi-asserted-by":"crossref","first-page":"121","DOI":"10.1136\/ard.30.2.121","article-title":"Still's disease in the adult","volume":"30","author":"Bywaters","year":"1971","journal-title":"Ann Rheum Dis"},{"issue":"3","key":"10.1016\/j.det.2023.08.009_bib19","first-page":"424","article-title":"Preliminary criteria for classification of adult Still's disease","volume":"19","author":"Yamaguchi","year":"1992","journal-title":"J\u00a0Rheumatol"},{"issue":"8","key":"10.1016\/j.det.2023.08.009_bib20","first-page":"1058","article-title":"Adult Still's disease: a multicenter survey of Japanese patients","volume":"17","author":"Ohta","year":"1990","journal-title":"J\u00a0Rheumatol"},{"issue":"5","key":"10.1016\/j.det.2023.08.009_bib21","doi-asserted-by":"crossref","first-page":"683","DOI":"10.1136\/ard.51.5.683","article-title":"Evaluation of serum ferritin as a marker for adult Still's disease activity","volume":"51","author":"Schwarz-Eywill","year":"1992","journal-title":"Ann Rheum Dis"},{"issue":"5","key":"10.1016\/j.det.2023.08.009_bib22","doi-asserted-by":"crossref","first-page":"454","DOI":"10.1093\/rheumatology\/34.5.454","article-title":"Inflammatory cytokine responses in juvenile chronic arthritis","volume":"34","author":"Rooney","year":"1995","journal-title":"Br J Rheumatol"},{"issue":"6","key":"10.1016\/j.det.2023.08.009_bib23","first-page":"653","article-title":"Interleukin 6: a possible marker of disease activity in adult onset Still's disease","volume":"14","author":"Scheinberg","year":"1996","journal-title":"Clin Exp Rheumatol"},{"issue":"2","key":"10.1016\/j.det.2023.08.009_bib24","first-page":"396","article-title":"Elevated serum interleukin 6, interferon-gamma, and tumor necrosis factor-alpha levels in patients with adult Still's disease","volume":"25","author":"Hoshino","year":"1998","journal-title":"J\u00a0Rheumatol"},{"issue":"7","key":"10.1016\/j.det.2023.08.009_bib25","doi-asserted-by":"crossref","first-page":"1716","DOI":"10.1002\/1529-0131(200107)44:7<1716::AID-ART298>3.0.CO;2-I","article-title":"Interleukin-18 as a novel diagnostic marker and indicator of disease severity in adult-onset Still's disease","volume":"44","author":"Kawaguchi","year":"2001","journal-title":"Arthritis Rheum"},{"issue":"4","key":"10.1016\/j.det.2023.08.009_bib26","doi-asserted-by":"crossref","first-page":"710","DOI":"10.1046\/j.1365-2133.1999.03115.x","article-title":"Adult-onset Still's disease with persistent plaques","volume":"141","author":"L\u00fcbbe","year":"1999","journal-title":"Br J Dermatol"},{"issue":"4","key":"10.1016\/j.det.2023.08.009_bib27","doi-asserted-by":"crossref","first-page":"333","DOI":"10.1159\/000051669","article-title":"Persistent plaques and linear pigmentation in adult-onset Still's disease","volume":"202","author":"Suzuki","year":"2001","journal-title":"Dermatology"},{"key":"10.1016\/j.det.2023.08.009_bib28","article-title":"A\u00a0challenging diagnosis of adult-onset Still\u2019s disease in the setting of raised anti-streptolysin O titres","volume":"3","author":"Joy","year":"2019","journal-title":"Rheumatol Adv Pract"},{"issue":"12","key":"10.1016\/j.det.2023.08.009_bib29","article-title":"Clinical Phenotypes of Adult-Onset Still's Disease: New Insights from Pathophysiology and Literature Findings","volume":"10","author":"Mitrovic","year":"2021","journal-title":"J\u00a0Clin Med"},{"issue":"5","key":"10.1016\/j.det.2023.08.009_bib30","doi-asserted-by":"crossref","first-page":"822","DOI":"10.1002\/acr.21901","article-title":"Anakinra in adult-onset Still's disease: long-term treatment in patients resistant to conventional therapy","volume":"65","author":"Giampietro","year":"2013","journal-title":"Arthritis Care Res"},{"issue":"6","key":"10.1016\/j.det.2023.08.009_bib31","doi-asserted-by":"crossref","first-page":"1659","DOI":"10.1002\/art.38398","article-title":"Efficacy of tocilizumab in conventional treatment-refractory adult-onset Still's disease: multicenter retrospective open-label study of thirty-four patients","volume":"66","author":"Ortiz-Sanju\u00e1n","year":"2014","journal-title":"Arthritis Rheumatol"},{"issue":"3","key":"10.1016\/j.det.2023.08.009_bib32","doi-asserted-by":"crossref","first-page":"159","DOI":"10.4081\/reumatismo.2016.888","article-title":"Successful treatment of refractory adult onset Still's disease with rituximab","volume":"68","author":"Belfeki","year":"2016","journal-title":"Reumatismo"},{"issue":"11","key":"10.1016\/j.det.2023.08.009_bib33","doi-asserted-by":"crossref","first-page":"2043","DOI":"10.1136\/annrheumdis-2013-204991","article-title":"Phenotypic and genotypic characteristics of cryopyrin-associated periodic syndrome: a series of 136 patients from the Eurofever Registry","volume":"74","author":"Levy","year":"2015","journal-title":"Ann Rheum Dis"},{"issue":"1","key":"10.1016\/j.det.2023.08.009_bib34","first-page":"1","article-title":"Cryopyrin-associated periodic syndromes and autoinflammation","volume":"33","author":"Shinkai","year":"2008","journal-title":"Clin Exp Dermatol"},{"issue":"6","key":"10.1016\/j.det.2023.08.009_bib35","doi-asserted-by":"crossref","first-page":"942","DOI":"10.1136\/annrheumdis-2016-209686","article-title":"Diagnostic criteria for cryopyrin-associated periodic syndrome (CAPS)","volume":"76","author":"Kuemmerle-Deschner","year":"2017","journal-title":"Ann Rheum Dis"},{"issue":"1","key":"10.1016\/j.det.2023.08.009_bib36","doi-asserted-by":"crossref","first-page":"12","DOI":"10.1007\/s11882-010-0160-9","article-title":"Cryopyrin-associated periodic syndrome: an update on diagnosis and treatment response","volume":"11","author":"Yu","year":"2011","journal-title":"Curr Allergy Asthma Rep"},{"issue":"2","key":"10.1016\/j.det.2023.08.009_bib37","doi-asserted-by":"crossref","first-page":"109","DOI":"10.2165\/11595040-000000000-00000","article-title":"Cryopyrin-associated periodic syndromes: diagnosis and management","volume":"14","author":"Miyamae","year":"2012","journal-title":"Paediatr Drugs"},{"issue":"1","key":"10.1016\/j.det.2023.08.009_bib38","doi-asserted-by":"crossref","first-page":"79","DOI":"10.1016\/S0022-3476(81)80961-4","article-title":"Arthropathy with rash, chronic meningitis, eye lesions, and mental retardation","volume":"99","author":"Prieur","year":"1981","journal-title":"J Pediatr"},{"issue":"5","key":"10.1016\/j.det.2023.08.009_bib39","doi-asserted-by":"crossref","first-page":"668","DOI":"10.1002\/art.1780260515","article-title":"Neonatal onset multisystem inflammatory disease","volume":"26","author":"Hassink","year":"1983","journal-title":"Arthritis Rheum"},{"issue":"7","key":"10.1016\/j.det.2023.08.009_bib40","doi-asserted-by":"crossref","first-page":"481","DOI":"10.1136\/jcp.56.7.481","article-title":"Pathogenesis of systemic lupus erythematosus","volume":"56","author":"Mok","year":"2003","journal-title":"J\u00a0Clini Pathol"},{"key":"10.1016\/j.det.2023.08.009_bib41","series-title":"Cutaneous lupus erythematosus","article-title":"Classification of Cutaneous Lupus Erythematosus","author":"Kuhn","year":"2005"},{"issue":"5","key":"10.1016\/j.det.2023.08.009_bib42","doi-asserted-by":"crossref","first-page":"862","DOI":"10.1016\/j.jaad.2015.12.029","article-title":"Using the American College of Rheumatology (ACR) and Systemic Lupus International Collaborating Clinics (SLICC) criteria to determine the diagnosis of systemic lupus erythematosus (SLE) in patients with subacute cutaneous lupus erythematosus (SCLE)","volume":"74","author":"Tiao","year":"2016","journal-title":"J\u00a0Am Acad Dermatol"},{"issue":"29","key":"10.1016\/j.det.2023.08.009_bib43","doi-asserted-by":"crossref","DOI":"10.1097\/MD.0000000000000351","article-title":"Lupus erythematosus and neutrophilic urticarial dermatosis: a retrospective study of 7 patients","volume":"93","author":"Gusdorf","year":"2014","journal-title":"Medicine"},{"issue":"4","key":"10.1016\/j.det.2023.08.009_bib44","doi-asserted-by":"crossref","first-page":"283","DOI":"10.1159\/000113940","article-title":"Neutrophilic cutaneous lupus erythematosus","volume":"216","author":"Lipsker","year":"2008","journal-title":"Dermatology"},{"issue":"1","key":"10.1016\/j.det.2023.08.009_bib45","first-page":"93","article-title":"Diagnosis and treatment of urticaria in primary care","volume":"6","author":"Kayiran","year":"2019","journal-title":"North Clin Istanb"},{"issue":"2","key":"10.1016\/j.det.2023.08.009_bib46","doi-asserted-by":"crossref","first-page":"248","DOI":"10.1046\/j.1365-2133.1998.02069.x","article-title":"Neutrophilic urticaria: clinical features, histological changes and possible mechanisms","volume":"138","author":"Toppe","year":"1998","journal-title":"Br J Dermatol"},{"issue":"1","key":"10.1016\/j.det.2023.08.009_bib47","doi-asserted-by":"crossref","first-page":"25","DOI":"10.1111\/j.1365-2133.1985.tb02040.x","article-title":"Neutrophilic urticaria","volume":"113","author":"Peters","year":"1985","journal-title":"Br J Dermatol"},{"issue":"2","key":"10.1016\/j.det.2023.08.009_bib48","doi-asserted-by":"crossref","first-page":"458","DOI":"10.1016\/j.jaci.2018.09.007","article-title":"Treatment of urticarial vasculitis: A systematic review","volume":"143","author":"Kolkhir","year":"2019","journal-title":"J\u00a0Allergy Clini Immunol"},{"issue":"2","key":"10.1016\/j.det.2023.08.009_bib49","doi-asserted-by":"crossref","first-page":"201","DOI":"10.1385\/CRIAI:23:2:201","article-title":"Urticarial vasculitis","volume":"23","author":"Venzor","year":"2002","journal-title":"Clin Rev Allergy Immunol"},{"issue":"1","key":"10.1016\/j.det.2023.08.009_bib50","doi-asserted-by":"crossref","first-page":"34","DOI":"10.1186\/1750-1172-2-34","article-title":"Sweet's syndrome - A comprehensive review of an acute febrile neutrophilic dermatosis","volume":"2","author":"Cohen","year":"2007","journal-title":"Orphanet J Rare Dis"}],"container-title":["Dermatologic Clinics"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0733863523000906?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0733863523000906?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2025,10,9]],"date-time":"2025-10-09T10:47:18Z","timestamp":1760006838000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0733863523000906"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2024,4]]},"references-count":50,"journal-issue":{"issue":"2","published-print":{"date-parts":[[2024,4]]}},"alternative-id":["S0733863523000906"],"URL":"https:\/\/doi.org\/10.1016\/j.det.2023.08.009","relation":{},"ISSN":["0733-8635"],"issn-type":[{"value":"0733-8635","type":"print"}],"subject":[],"published":{"date-parts":[[2024,4]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"Neutrophilic Urticarial Dermatosis","name":"articletitle","label":"Article Title"},{"value":"Dermatologic Clinics","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.det.2023.08.009","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"\u00a9 2023 Elsevier Inc. All rights reserved.","name":"copyright","label":"Copyright"}]}}