{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,6,2]],"date-time":"2026-06-02T17:41:21Z","timestamp":1780422081132,"version":"3.54.1"},"reference-count":15,"publisher":"Elsevier BV","license":[{"start":{"date-parts":[[2022,1,1]],"date-time":"2022-01-01T00:00:00Z","timestamp":1640995200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2022,1,1]],"date-time":"2022-01-01T00:00:00Z","timestamp":1640995200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/legal\/tdmrep-license"},{"start":{"date-parts":[[2022,5,5]],"date-time":"2022-05-05T00:00:00Z","timestamp":1651708800000},"content-version":"vor","delay-in-days":124,"URL":"http:\/\/creativecommons.org\/licenses\/by-nc-nd\/4.0\/"}],"content-domain":{"domain":["elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Epilepsy &amp; Behavior Reports"],"published-print":{"date-parts":[[2022]]},"DOI":"10.1016\/j.ebr.2022.100551","type":"journal-article","created":{"date-parts":[[2022,5,13]],"date-time":"2022-05-13T04:05:43Z","timestamp":1652414743000},"page":"100551","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":4,"special_numbering":"C","title":["FDG-PET findings and alcohol-responsive myoclonus in a patient with Unverricht-Lundborg disease"],"prefix":"10.1016","volume":"19","author":[{"given":"Lorenzo","family":"Muccioli","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Andrea","family":"Farolfi","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Federica","family":"Pondrelli","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Eleonora","family":"Matteo","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Lorenzo","family":"Ferri","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Laura","family":"Licchetta","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Lara","family":"Alvisi","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Paolo","family":"Tinuper","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Francesca","family":"Bisulli","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"issue":"S2","key":"10.1016\/j.ebr.2022.100551_b0005","doi-asserted-by":"crossref","first-page":"28","DOI":"10.1684\/epd.2016.0841","article-title":"Unverricht-Lundborg disease","volume":"18","author":"Crespel","year":"2016","journal-title":"Epileptic Disord"},{"issue":"3","key":"10.1016\/j.ebr.2022.100551_b0010","doi-asserted-by":"crossref","first-page":"219","DOI":"10.1016\/j.eplepsyres.2006.10.006","article-title":"Long-term evolution of EEG in Unverricht-Lundborg disease","volume":"73","author":"Ferlazzo","year":"2007","journal-title":"Epilepsy Res"},{"issue":"1","key":"10.1016\/j.ebr.2022.100551_b0015","doi-asserted-by":"crossref","first-page":"43","DOI":"10.5692\/clinicalneurol.49.43","article-title":"Unverricht-Lundborg disease manifesting tremulous myoclonus with rare convulsive seizures: a case report","volume":"49","author":"Kondo","year":"2009","journal-title":"Rinsho Shinkeigaku"},{"issue":"1","key":"10.1016\/j.ebr.2022.100551_b0020","article-title":"Multimodal imaging finding in Unverricht-Lundborg disease. The Internet","volume":"5","author":"Tanaka","year":"2004","journal-title":"J Neurol"},{"key":"10.1016\/j.ebr.2022.100551_b0025","doi-asserted-by":"crossref","first-page":"490","DOI":"10.1093\/brain\/44.4.490","article-title":"Dyssynergia cerebellaris myoclonica\u2014primary atrophy of the dentate system: a contribution to the pathology and symptomatology of the cerebellum","volume":"44","author":"Ramsay","year":"1922","journal-title":"Brain"},{"key":"10.1016\/j.ebr.2022.100551_b0030","doi-asserted-by":"crossref","unstructured":"Genton P, Guerrini R. Antimyoclonic effects of alcohol in progressive myoclonus epilepsy. Neurology 1990;40(9).","DOI":"10.1212\/WNL.40.9.1412"},{"issue":"10","key":"10.1016\/j.ebr.2022.100551_b0035","doi-asserted-by":"crossref","first-page":"905","DOI":"10.1136\/jnnp.54.10.905","article-title":"Effects of alcohol on myoclonus and somatosensory evoked potentials in dyssynergia cerebellaris myoclonica","volume":"54","author":"Lu","year":"1991","journal-title":"J Neurol Neurosurg Psychiatry"},{"issue":"5","key":"10.1016\/j.ebr.2022.100551_b0040","doi-asserted-by":"crossref","first-page":"575","DOI":"10.1046\/j.1440-1819.1999.00608.x","article-title":"Progressive myoclonic epilepsies syndrome (Ramsay Hunt syndrome) with mental disorder: report of two cases","volume":"53","author":"Hsiao","year":"1999","journal-title":"Psychiatry Clin Neurosci"},{"key":"10.1016\/j.ebr.2022.100551_b0045","doi-asserted-by":"crossref","unstructured":"Wu J, Tang H, Chen S, Cao L. Mechanisms and pharmacotherapy for ethanol-responsive movement disorders. Front Neurol. 2020;11:892. Published 2020 Aug 25. doi:10.3389\/fneur.2020.00892.","DOI":"10.3389\/fneur.2020.00892"},{"issue":"1","key":"10.1016\/j.ebr.2022.100551_b0050","doi-asserted-by":"crossref","first-page":"107","DOI":"10.1016\/S0370-4475(78)80126-9","article-title":"La maladie de Lafora","volume":"8","author":"Tassinari","year":"1978","journal-title":"Rev Electroencephalogr Neurophysiol Clin"},{"issue":"1","key":"10.1016\/j.ebr.2022.100551_b0055","doi-asserted-by":"crossref","first-page":"107","DOI":"10.1002\/mds.21812","article-title":"The natural history of Unverricht-Lundborg disease: a report of eight genetically proven cases","volume":"23","author":"Chew","year":"2008","journal-title":"Mov Disord"},{"issue":"9","key":"10.1016\/j.ebr.2022.100551_b0060","doi-asserted-by":"crossref","first-page":"1768","DOI":"10.1111\/j.1528-1167.2007.01118.x","article-title":"Substantial thalamostriatal dopaminergic defect in Unverricht-Lundborg disease","volume":"48","author":"Korja","year":"2007","journal-title":"Epilepsia"},{"issue":"8","key":"10.1016\/j.ebr.2022.100551_b0065","doi-asserted-by":"crossref","first-page":"606","DOI":"10.1212\/WNL.0b013e3181b3888b","article-title":"Motor cortex and thalamic atrophy in Unverricht-Lundborg disease: voxel-based morphometric study","volume":"73","author":"Koskenkorva","year":"2009","journal-title":"Neurology"},{"issue":"6","key":"10.1016\/j.ebr.2022.100551_b0070","doi-asserted-by":"crossref","first-page":"1576","DOI":"10.1007\/s00259-019-04647-3","article-title":"FDG-PET assessment and metabolic patterns in Lafora disease","volume":"47","author":"Muccioli","year":"2020","journal-title":"Eur J Nucl Med Mol Imaging"},{"issue":"11","key":"10.1016\/j.ebr.2022.100551_b0075","doi-asserted-by":"crossref","first-page":"1151","DOI":"10.1097\/00001756-200508010-00004","article-title":"Correlation of interictal spike-wave with thalamic glucose metabolism in juvenile myoclonic epilepsy","volume":"16","author":"Kim","year":"2005","journal-title":"NeuroReport"}],"container-title":["Epilepsy &amp; Behavior Reports"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S2589986422000284?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S2589986422000284?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2025,11,12]],"date-time":"2025-11-12T00:08:07Z","timestamp":1762906087000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S2589986422000284"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2022]]},"references-count":15,"alternative-id":["S2589986422000284"],"URL":"https:\/\/doi.org\/10.1016\/j.ebr.2022.100551","relation":{},"ISSN":["2589-9864"],"issn-type":[{"value":"2589-9864","type":"print"}],"subject":[],"published":{"date-parts":[[2022]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"FDG-PET findings and alcohol-responsive myoclonus in a patient with Unverricht-Lundborg disease","name":"articletitle","label":"Article Title"},{"value":"Epilepsy & Behavior Reports","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.ebr.2022.100551","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"\u00a9 2022 The Authors. Published by Elsevier Inc.","name":"copyright","label":"Copyright"}],"article-number":"100551"}}