{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,6,16]],"date-time":"2026-06-16T22:06:46Z","timestamp":1781647606195,"version":"3.54.5"},"reference-count":19,"publisher":"Elsevier BV","license":[{"start":{"date-parts":[[2020,5,1]],"date-time":"2020-05-01T00:00:00Z","timestamp":1588291200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2020,5,1]],"date-time":"2020-05-01T00:00:00Z","timestamp":1588291200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/legal\/tdmrep-license"}],"content-domain":{"domain":["clinicalkey.com","clinicalkey.com.au","clinicalkey.es","clinicalkey.fr","clinicalkey.jp","ejpn-journal.com","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["European Journal of Paediatric Neurology"],"published-print":{"date-parts":[[2020,5]]},"DOI":"10.1016\/j.ejpn.2020.03.003","type":"journal-article","created":{"date-parts":[[2020,3,18]],"date-time":"2020-03-18T01:12:56Z","timestamp":1584493976000},"page":"39-45","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":6,"special_numbering":"C","title":["Management of PHACES syndrome: Risk of stroke and its prevention from a neurosurgical perspective"],"prefix":"10.1016","volume":"26","author":[{"given":"Mikaeel","family":"Habib","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Rui","family":"Manilha","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-5077-6622","authenticated-orcid":false,"given":"Nadia","family":"Khan","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"issue":"3","key":"10.1016\/j.ejpn.2020.03.003_bib1","doi-asserted-by":"crossref","first-page":"307","DOI":"10.1001\/archderm.1996.03890270083012","article-title":"PHACE syndrome. The association of posterior fossa brain malformations, hemangiomas, arterial anomalies, coarctation of the aorta and cardiac defects, and eye abnormalities","volume":"132","author":"Frieden","year":"1996","journal-title":"Arch. Dermatol."},{"issue":"1","key":"10.1016\/j.ejpn.2020.03.003_bib2","doi-asserted-by":"crossref","first-page":"117","DOI":"10.1067\/mpd.2001.114880","article-title":"The many faces of PHACE syndrome","volume":"139","author":"Metry","year":"2001","journal-title":"J.\u00a0Pediatr."},{"issue":"2","key":"10.1016\/j.ejpn.2020.03.003_bib3","doi-asserted-by":"crossref","first-page":"181","DOI":"10.1016\/j.ijporl.2008.10.017","article-title":"PHACES syndrome: a review","volume":"73","author":"Hartemink","year":"2009","journal-title":"Int. J. Pediatr. Otorhinolaryngol."},{"issue":"5","key":"10.1016\/j.ejpn.2020.03.003_bib4","doi-asserted-by":"crossref","first-page":"1447","DOI":"10.1542\/peds.2009-0082","article-title":"Consensus statement on diagnostic criteria for PHACE syndrome","volume":"124","author":"Metry","year":"2009","journal-title":"Pediatrics"},{"key":"10.1016\/j.ejpn.2020.03.003_bib5","doi-asserted-by":"crossref","first-page":"418","DOI":"10.1542\/peds.2009-3166","article-title":"Risk of PHACE syndrome in infants with larger facial hemangiomas","volume":"126","author":"Haggstrom","year":"2010","journal-title":"Pediatrics"},{"key":"10.1016\/j.ejpn.2020.03.003_bib6","doi-asserted-by":"crossref","first-page":"24","DOI":"10.1016\/j.jpeds.2016.07.054","article-title":"PHACE syndrome: consensus-derived diagnosis and care recommendations","volume":"178","author":"Garzon","year":"2016","journal-title":"J.\u00a0Pediatr."},{"issue":"1","key":"10.1016\/j.ejpn.2020.03.003_bib7","doi-asserted-by":"crossref","first-page":"70","DOI":"10.3171\/2015.5.PEDS1578","article-title":"Bilateral pial synangiosis in a child with PHACE syndrome","volume":"17","author":"Jack","year":"2016","journal-title":"J.\u00a0Neurosurg. Pediatr."},{"issue":"9","key":"10.1016\/j.ejpn.2020.03.003_bib8","doi-asserted-by":"crossref","first-page":"1129","DOI":"10.1007\/s00247-011-2142-z","article-title":"PHACE syndrome: MRI of intracerebral vascular anomalies and clinical findings in a series of 12 patients","volume":"41","author":"Bracken","year":"2011","journal-title":"Pediatr. Radiol."},{"issue":"6","key":"10.1016\/j.ejpn.2020.03.003_bib9","doi-asserted-by":"crossref","first-page":"1672","DOI":"10.1161\/STROKEAHA.112.650952","article-title":"Stroke in children with posterior fossa brain malformations, hemangiomas, arterial anomalies, coarctation of the aorta and cardiac defects, and eye abnormalities (PHACE) syndrome","volume":"43","author":"Siegel","year":"2012","journal-title":"Stroke"},{"issue":"5","key":"10.1016\/j.ejpn.2020.03.003_bib10","doi-asserted-by":"crossref","first-page":"559","DOI":"10.1007\/s00381-006-0247-8","article-title":"A\u00a0report of two cases with dolichosegmental intracranial arteries as a new feature of PHACES syndrome","volume":"23","author":"Baccin","year":"2006","journal-title":"Child's Nerv. Syst."},{"issue":"6","key":"10.1016\/j.ejpn.2020.03.003_bib11","doi-asserted-by":"crossref","first-page":"1334","DOI":"10.1111\/bjd.18246","article-title":"Risk of associated cerebrovascular anomalies in children with segmental facial haemangiomas","volume":"181","author":"Schmid","year":"2019","journal-title":"Br. J. Dermatol."},{"issue":"2","key":"10.1016\/j.ejpn.2020.03.003_bib12","doi-asserted-by":"crossref","first-page":"308","DOI":"10.1161\/STROKEAHA.107.485185","article-title":"The cerebral vasculopathy of PHACES syndrome","volume":"39","author":"Heyer","year":"2008","journal-title":"Stroke"},{"issue":"3","key":"10.1016\/j.ejpn.2020.03.003_bib13","doi-asserted-by":"crossref","first-page":"227","DOI":"10.1007\/s00234-002-0902-z","article-title":"PHACES syndrome: a review of eight previously unreported cases with late arterial occlusions","volume":"46","author":"Bhattacharya","year":"2004","journal-title":"Neuroradiology"},{"issue":"3","key":"10.1016\/j.ejpn.2020.03.003_bib14","doi-asserted-by":"crossref","first-page":"601","DOI":"10.1148\/radiology.207.3.9609880","article-title":"Cerebral vasculopathy and neurologic sequelae in infants with cervicofacial hemangioma: report of eight patients","volume":"207","author":"Burrows","year":"1998","journal-title":"Radiology"},{"key":"10.1016\/j.ejpn.2020.03.003_bib15","doi-asserted-by":"crossref","first-page":"291","DOI":"10.1016\/j.wneu.2017.08.176","article-title":"Moyamoya vasculopathy in PHACE syndrome: six new cases and review of the literature","volume":"108","author":"Tortora","year":"2017","journal-title":"World Neurosurg"},{"issue":"4","key":"10.1016\/j.ejpn.2020.03.003_bib16","doi-asserted-by":"crossref","first-page":"493","DOI":"10.3171\/2018.10.PEDS18582","article-title":"Moyamoya syndrome and PHACE syndrome: clinical and radiographic characterization of the intracranial arteriopathy and response to surgical revascularization","volume":"23","author":"Jernigan","year":"2019","journal-title":"J.\u00a0Neurosurg. Pediatr."},{"issue":"3","key":"10.1016\/j.ejpn.2020.03.003_bib17","doi-asserted-by":"crossref","first-page":"288","DOI":"10.1001\/archneur.1969.00480090076012","article-title":"Cerebrovascular \"moyamoya\" disease","volume":"20","author":"Suzuki","year":"1969","journal-title":"Arch. Neurol."},{"issue":"10","key":"10.1016\/j.ejpn.2020.03.003_bib18","doi-asserted-by":"crossref","first-page":"591","DOI":"10.1007\/BF00300998","article-title":"Clinical and angiographic follow-up of childhood-onset moyamoya disease","volume":"11","author":"Ezura","year":"1995","journal-title":"Child's Nerv. Syst."},{"issue":"10","key":"10.1016\/j.ejpn.2020.03.003_bib19","doi-asserted-by":"crossref","first-page":"1980","DOI":"10.3174\/ajnr.A2206","article-title":"Cervical and intracranial arterial anomalies in 70 patients with PHACE syndrome","volume":"31","author":"Hess","year":"2010","journal-title":"Am. J. Neuroradiol."}],"container-title":["European Journal of Paediatric Neurology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1090379820300702?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1090379820300702?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2025,10,21]],"date-time":"2025-10-21T18:36:41Z","timestamp":1761071801000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S1090379820300702"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2020,5]]},"references-count":19,"alternative-id":["S1090379820300702"],"URL":"https:\/\/doi.org\/10.1016\/j.ejpn.2020.03.003","relation":{},"ISSN":["1090-3798"],"issn-type":[{"value":"1090-3798","type":"print"}],"subject":[],"published":{"date-parts":[[2020,5]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"Management of PHACES syndrome: Risk of stroke and its prevention from a neurosurgical perspective","name":"articletitle","label":"Article Title"},{"value":"European Journal of Paediatric Neurology","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.ejpn.2020.03.003","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"\u00a9 2020 European Paediatric Neurology Society. Published by Elsevier Ltd. All rights reserved.","name":"copyright","label":"Copyright"}]}}