{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,27]],"date-time":"2026-09-27T13:43:09Z","timestamp":1790516589602,"version":"4.1.0"},"reference-count":31,"publisher":"Elsevier BV","issue":"2","content-domain":{"domain":["elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Gene"],"published-print":{"date-parts":[[2013,9]]},"DOI":"10.1016\/j.gene.2013.07.006","type":"journal-article","created":{"date-parts":[[2013,7,13]],"date-time":"2013-07-13T06:03:09Z","timestamp":1373695389000},"page":"448-455","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":9,"title":["Regulation of fibrillin-1 gene expression by Sp1"],"prefix":"10.1016","volume":"527","author":[{"given":"Gao","family":"Guo","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Christian","family":"R\u00f6delsperger","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Martin","family":"Digweed","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Peter N.","family":"Robinson","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"key":"10.1016\/j.gene.2013.07.006_bb0005","doi-asserted-by":"crossref","first-page":"2169","DOI":"10.1128\/JVI.74.5.2169-2177.2000","article-title":"Identification of poly(ADP-ribose) polymerase as a transcriptional coactivator of the human T-cell leukemia virus type 1 Tax protein","volume":"74","author":"Anderson","year":"2000","journal-title":"J. Virol."},{"key":"10.1016\/j.gene.2013.07.006_bb0010","doi-asserted-by":"crossref","first-page":"430","DOI":"10.1016\/j.jaci.2010.11.013","article-title":"Specificity protein 1 is pivotal in the skin's antiviral response","volume":"127","author":"Bin","year":"2011","journal-title":"J. Allergy Clin. Immunol."},{"key":"10.1016\/j.gene.2013.07.006_bb0015","doi-asserted-by":"crossref","first-page":"10692","DOI":"10.1074\/jbc.275.14.10692","article-title":"Poly(ADP-ribose) polymerase is a B-MYB coactivator","volume":"275","author":"Cervellera","year":"2000","journal-title":"J. Biol. Chem."},{"key":"10.1016\/j.gene.2013.07.006_bb0025","doi-asserted-by":"crossref","first-page":"3367","DOI":"10.1093\/nar\/20.13.3367","article-title":"Functional elements of the ribosomal protein l7a (rpl7a) gene promoter region and their conservation between mammals and birds","volume":"20","author":"Colombo","year":"1992","journal-title":"Nucleic Acids Res."},{"key":"10.1016\/j.gene.2013.07.006_bb0030","doi-asserted-by":"crossref","first-page":"94","DOI":"10.1111\/j.1749-6632.1999.tb09513.x","article-title":"Sp1 and its likes: biochemical and functional predictions for a growing family of zinc finger transcription factors","volume":"880","author":"Cook","year":"1999","journal-title":"Ann. N. Y. Acad. Sci."},{"key":"10.1016\/j.gene.2013.07.006_bb0020","doi-asserted-by":"crossref","first-page":"476","DOI":"10.1006\/geno.1993.1350","article-title":"Fibrillin binds calcium and is coded by cDNAs that reveal a multidomain structure and alternatively spliced exons at the 5\u2032 end","volume":"17","author":"Corson","year":"1993","journal-title":"Genomics"},{"key":"10.1016\/j.gene.2013.07.006_bb0035","doi-asserted-by":"crossref","first-page":"2238","DOI":"10.1126\/science.1072613","article-title":"Sp1 and TAFII130 transcriptional activity disrupted in early Huntington's disease","volume":"296","author":"Dunah","year":"2002","journal-title":"Science"},{"key":"10.1016\/j.gene.2013.07.006_bb0040","doi-asserted-by":"crossref","first-page":"638","DOI":"10.1016\/j.biocel.2007.09.004","article-title":"A short ultraconserved sequence drives transcription from an alternate FBN1 promoter","volume":"40","author":"Guo","year":"2008","journal-title":"Int. J. Biochem. Cell Biol."},{"key":"10.1016\/j.gene.2013.07.006_bb0045","doi-asserted-by":"crossref","first-page":"5519","DOI":"10.1093\/nar\/20.21.5519","article-title":"Cloning by recognition site screening of two novel GT box binding proteins: a family of Sp1 related genes","volume":"11","author":"Hagen","year":"1992","journal-title":"Nucleic Acids Res."},{"key":"10.1016\/j.gene.2013.07.006_bb0050","doi-asserted-by":"crossref","first-page":"1534","DOI":"10.1007\/s00018-002-8527-2","article-title":"The functional role of poly(ADP-ribose)polymerase 1 as novel coactivator of NF-kappaB in inflammatory disorders","volume":"59","author":"Hassa","year":"2002","journal-title":"Cell. Mol. Life Sci."},{"key":"10.1016\/j.gene.2013.07.006_bb0055","doi-asserted-by":"crossref","first-page":"8878","DOI":"10.1016\/S0021-9258(18)81875-0","article-title":"The effect of poly(ADP-ribosyl) ation on native and H1-depleted chromatin. A role of poly(ADP-ribosyl)ation on core nucleosome structure","volume":"264","author":"Huletsky","year":"1989","journal-title":"J. Biol. Chem."},{"key":"10.1016\/j.gene.2013.07.006_bb0060","doi-asserted-by":"crossref","first-page":"8931","DOI":"10.1128\/JVI.78.16.8931-8934.2004","article-title":"RNA interference directed against Poly(ADP-ribose) polymerase 1 efficiently suppresses human immunodeficiency virus type 1 replication in human cells","volume":"78","author":"Kameoka","year":"2004","journal-title":"J. Virol."},{"key":"10.1016\/j.gene.2013.07.006_bb0070","doi-asserted-by":"crossref","first-page":"23","DOI":"10.1007\/s00439-007-0371-x","article-title":"Large genomic fibrillin-1 (FBN1) gene deletions provide evidence for true haploinsufficiency in Marfan syndrome","volume":"122","author":"M\u00e1ty\u00e1s","year":"2007","journal-title":"Hum. Genet."},{"key":"10.1016\/j.gene.2013.07.006_bb0075","doi-asserted-by":"crossref","first-page":"2261","DOI":"10.1073\/pnas.94.6.2261","article-title":"Poly(ADP-ribose) polymerase enhances activator-dependent transcription in vitro","volume":"94","author":"Meisterernst","year":"1997","journal-title":"Proc. Natl. Acad. Sci. U. S. A."},{"key":"10.1016\/j.gene.2013.07.006_bb0080","doi-asserted-by":"crossref","first-page":"245","DOI":"10.1093\/dnares\/dsq016","article-title":"Comprehensive analysis of the palindromic motif TCTCGCGAGA: a regulatory element of the HNRNPK promoter","volume":"17","author":"Mikula","year":"2010","journal-title":"DNA Res."},{"key":"10.1016\/j.gene.2013.07.006_bb0085","doi-asserted-by":"crossref","first-page":"27","DOI":"10.1016\/S0014-5793(98)00131-8","article-title":"Interaction of Oct-1 and automodification domain of poly(ADP-ribose) synthetase","volume":"424","author":"Nie","year":"1998","journal-title":"FEBS Lett."},{"key":"10.1016\/j.gene.2013.07.006_bb0090","doi-asserted-by":"crossref","first-page":"15","DOI":"10.1186\/1471-2148-5-15","article-title":"The architecture of mammalian ribosomal protein promoters","volume":"5","author":"Perry","year":"2005","journal-title":"BMC Evol. Biol."},{"key":"10.1016\/j.gene.2013.07.006_bb0100","doi-asserted-by":"crossref","first-page":"14670","DOI":"10.1021\/bi050755o","article-title":"DNA-induced dimerization of poly(ADP-ribose) polymerase-1 triggers its activation","volume":"44","author":"Pion","year":"2005","journal-title":"Biochemistry"},{"key":"10.1016\/j.gene.2013.07.006_bb0095","doi-asserted-by":"crossref","first-page":"1935","DOI":"10.1101\/gad.5.11.1935","article-title":"Transcription from a TATA-less promoter requires a multisubunit TFIID complex","volume":"5","author":"Pugh","year":"1991","journal-title":"Genes Dev."},{"key":"10.1016\/j.gene.2013.07.006_bb0105","doi-asserted-by":"crossref","first-page":"2003","DOI":"10.1172\/JCI114110","article-title":"Mithramycin blocks protein binding and function of the SV40 early promoter","volume":"83","author":"Ray","year":"1989","journal-title":"J. Clin. Invest."},{"key":"10.1016\/j.gene.2013.07.006_bb0110","doi-asserted-by":"crossref","first-page":"769","DOI":"10.1136\/jmg.2005.039669","article-title":"The molecular genetics of Marfan syndrome and related disorders","volume":"43","author":"Robinson","year":"2006","journal-title":"J. Med. Genet."},{"key":"10.1016\/j.gene.2013.07.006_bb0115","doi-asserted-by":"crossref","first-page":"308","DOI":"10.1016\/j.ygeno.2009.07.005","article-title":"Short ultraconserved promoter regions delineate a class of preferentially expressed alternatively spliced transcripts","volume":"94","author":"R\u00f6delsperger","year":"2009","journal-title":"Genomics"},{"key":"10.1016\/j.gene.2013.07.006_bb0120","doi-asserted-by":"crossref","first-page":"48","DOI":"10.1016\/j.gene.2005.09.033","article-title":"Identification of highly specific localized sequence motifs in human ribosomal protein gene promoters","volume":"365","author":"Roepcke","year":"2006","journal-title":"Gene"},{"key":"10.1016\/j.gene.2013.07.006_bb0125","doi-asserted-by":"crossref","first-page":"2499","DOI":"10.1083\/jcb.103.6.2499","article-title":"Fibrillin, a new 350-kD glycoprotein, is a component of extracellular microfibrils","volume":"103","author":"Sakai","year":"1986","journal-title":"J. Cell Biol."},{"key":"10.1016\/j.gene.2013.07.006_bb0130","doi-asserted-by":"crossref","first-page":"233","DOI":"10.1016\/j.ygeno.2009.06.005","article-title":"Experimental and bioinformatic characterisation of the promoter region of the Marfan syndrome gene, FBN1","volume":"94","author":"Summers","year":"2009","journal-title":"Genomics"},{"key":"10.1016\/j.gene.2013.07.006_bb0135","doi-asserted-by":"crossref","first-page":"755","DOI":"10.1046\/j.1523-1747.2001.01326.x","article-title":"Blocking sp1 transcription factor broadly inhibits extracellular matrix gene expression in vitro and in vivo: implications for the treatment of tissue fibrosis","volume":"116","author":"Verrecchia","year":"2001","journal-title":"J. Invest. Dermatol."},{"key":"10.1016\/j.gene.2013.07.006_bb0140","doi-asserted-by":"crossref","first-page":"375","DOI":"10.1124\/pr.54.3.375","article-title":"The therapeutic potential of poly(ADP-ribose) polymerase inhibitors","volume":"54","author":"Virag","year":"2002","journal-title":"Pharmacol. Rev."},{"key":"10.1016\/j.gene.2013.07.006_bb0145","doi-asserted-by":"crossref","first-page":"89","DOI":"10.18388\/abp.2007_3273","article-title":"A common cis-element in promoters of protein synthesis and cell cycle genes","volume":"54","author":"Wyrwicz","year":"2007","journal-title":"Acta Biochim. Pol."},{"key":"10.1016\/j.gene.2013.07.006_bb0155","doi-asserted-by":"crossref","first-page":"338","DOI":"10.1038\/nature03441","article-title":"Systematic discovery of regulatory motifs in human promoters and 3\u2032 UTRs by comparison of several mammals","volume":"434","author":"Xie","year":"2005","journal-title":"Nature"},{"key":"10.1016\/j.gene.2013.07.006_bb0165","doi-asserted-by":"crossref","first-page":"423","DOI":"10.1042\/BJ20041718","article-title":"Regulation of the poly(ADP-ribose) polymerase-1 gene expression by the transcription factors Sp1 and Sp3 is under the influence of cell density in primary cultured cells","volume":"389","author":"Zaniolo","year":"2005","journal-title":"Biochem. J."},{"key":"10.1016\/j.gene.2013.07.006_bb0160","doi-asserted-by":"crossref","first-page":"96","DOI":"10.1186\/1471-2199-8-96","article-title":"Regulation of poly(ADP-ribose) polymerase-1 (PARP-1) gene expression through the post-translational modification of Sp1: a nuclear target protein of PARP-1","volume":"8","author":"Zaniolo","year":"2007","journal-title":"BMC Mol. Biol."}],"container-title":["Gene"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0378111913008639?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0378111913008639?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2022,2,28]],"date-time":"2022-02-28T22:15:42Z","timestamp":1646086542000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0378111913008639"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2013,9]]},"references-count":31,"journal-issue":{"issue":"2","published-print":{"date-parts":[[2013,9]]}},"alternative-id":["S0378111913008639"],"URL":"https:\/\/doi.org\/10.1016\/j.gene.2013.07.006","relation":{},"ISSN":["0378-1119"],"issn-type":[{"value":"0378-1119","type":"print"}],"subject":[],"published":{"date-parts":[[2013,9]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"Regulation of fibrillin-1 gene expression by Sp1","name":"articletitle","label":"Article Title"},{"value":"Gene","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.gene.2013.07.006","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"Copyright \u00a9 2013 Elsevier B.V. All rights reserved.","name":"copyright","label":"Copyright"}]}}