{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,10,27]],"date-time":"2025-10-27T08:48:17Z","timestamp":1761554897997,"version":"build-2065373602"},"reference-count":61,"publisher":"Elsevier BV","issue":"1","license":[{"start":{"date-parts":[[2023,1,1]],"date-time":"2023-01-01T00:00:00Z","timestamp":1672531200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2023,1,1]],"date-time":"2023-01-01T00:00:00Z","timestamp":1672531200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/legal\/tdmrep-license"},{"start":{"date-parts":[[2023,1,1]],"date-time":"2023-01-01T00:00:00Z","timestamp":1672531200000},"content-version":"stm-asf","delay-in-days":0,"URL":"https:\/\/doi.org\/10.15223\/policy-017"},{"start":{"date-parts":[[2023,1,1]],"date-time":"2023-01-01T00:00:00Z","timestamp":1672531200000},"content-version":"stm-asf","delay-in-days":0,"URL":"https:\/\/doi.org\/10.15223\/policy-037"},{"start":{"date-parts":[[2023,1,1]],"date-time":"2023-01-01T00:00:00Z","timestamp":1672531200000},"content-version":"stm-asf","delay-in-days":0,"URL":"https:\/\/doi.org\/10.15223\/policy-012"},{"start":{"date-parts":[[2023,1,1]],"date-time":"2023-01-01T00:00:00Z","timestamp":1672531200000},"content-version":"stm-asf","delay-in-days":0,"URL":"https:\/\/doi.org\/10.15223\/policy-029"},{"start":{"date-parts":[[2023,1,1]],"date-time":"2023-01-01T00:00:00Z","timestamp":1672531200000},"content-version":"stm-asf","delay-in-days":0,"URL":"https:\/\/doi.org\/10.15223\/policy-004"}],"content-domain":{"domain":["clinicalkey.com","clinicalkey.com.au","clinicalkey.es","clinicalkey.fr","clinicalkey.jp","theclinics.com","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Heart Failure Clinics"],"published-print":{"date-parts":[[2023,1]]},"DOI":"10.1016\/j.hfc.2022.08.021","type":"journal-article","created":{"date-parts":[[2022,11,23]],"date-time":"2022-11-23T14:50:39Z","timestamp":1669215039000},"page":"25-33","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":0,"title":["Unusual Forms of Pulmonary Hypertension"],"prefix":"10.1016","volume":"19","author":[{"given":"Yuri de Deus Montalverne","family":"Parente","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Natalia","family":"Fernandes da Silva","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Rogerio","family":"Souza","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"78","reference":[{"issue":"1","key":"10.1016\/j.hfc.2022.08.021_bib1","doi-asserted-by":"crossref","DOI":"10.1183\/13993003.01913-2018","article-title":"Haemodynamic definitions and updated clinical classification of pulmonary hypertension","volume":"53","author":"Simonneau","year":"2019","journal-title":"Eur Respir J"},{"issue":"5","key":"10.1016\/j.hfc.2022.08.021_bib2","doi-asserted-by":"crossref","first-page":"408","DOI":"10.1097\/MCP.0000000000000300","article-title":"Pulmonary arterial hypertension in schistosomiasis","volume":"22","author":"Gavilanes","year":"2016","journal-title":"Curr Opin Pulm Med"},{"issue":"9541","key":"10.1016\/j.hfc.2022.08.021_bib3","doi-asserted-by":"crossref","first-page":"1106","DOI":"10.1016\/S0140-6736(06)69440-3","article-title":"Human schistosomiasis","volume":"368","author":"Gryseels","year":"2006","journal-title":"Lancet"},{"issue":"9936","key":"10.1016\/j.hfc.2022.08.021_bib4","doi-asserted-by":"crossref","first-page":"2253","DOI":"10.1016\/S0140-6736(13)61949-2","article-title":"Human schistosomiasis","volume":"383","author":"Colley","year":"2014","journal-title":"Lancet"},{"issue":"11","key":"10.1016\/j.hfc.2022.08.021_bib5","doi-asserted-by":"crossref","first-page":"1518","DOI":"10.1161\/CIRCULATIONAHA.108.803221","article-title":"Cardiopulmonary Manifestations of Hepatosplenic Schistosomiasis","volume":"119","author":"Lapa","year":"2009","journal-title":"Circulation"},{"issue":"1","key":"10.1016\/j.hfc.2022.08.021_bib6","doi-asserted-by":"crossref","first-page":"15","DOI":"10.1016\/0001-706X(92)90017-R","article-title":"A\u00a0review of the literature on the use of ultrasonography in schistosomiasis with special reference to its use in field studies. 2. Schistosoma mansoni","volume":"51","author":"Hatz","year":"1992","journal-title":"Acta Trop"},{"key":"10.1016\/j.hfc.2022.08.021_bib7","doi-asserted-by":"crossref","first-page":"608883","DOI":"10.3389\/fimmu.2020.608883","article-title":"Schistosomiasis Pulmonary Arterial Hypertension","volume":"11","author":"Sibomana","year":"2020","journal-title":"Front Immunol"},{"key":"10.1016\/j.hfc.2022.08.021_bib8","doi-asserted-by":"crossref","first-page":"118","DOI":"10.1186\/s12890-015-0115-y","article-title":"Pulmonary artery enlargement in schistosomiasis associated pulmonary arterial hypertension","volume":"15","author":"Hoette","year":"2015","journal-title":"BMC Pulm Med"},{"issue":"1","key":"10.1016\/j.hfc.2022.08.021_bib9","first-page":"90","article-title":"Immunopathological aspects of schistosomiasis-associated pulmonary arterial hypertension","volume":"68","author":"Mauad","year":"2014","journal-title":"J\u00a0Infect"},{"issue":"9","key":"10.1016\/j.hfc.2022.08.021_bib10","doi-asserted-by":"crossref","first-page":"715","DOI":"10.1016\/j.jacc.2010.03.065","article-title":"Survival in schistosomiasis-associated pulmonary arterial hypertension","volume":"56","author":"dos Santos Fernandes","year":"2010","journal-title":"J\u00a0Am Coll Cardiol"},{"issue":"4","key":"10.1016\/j.hfc.2022.08.021_bib11","doi-asserted-by":"crossref","first-page":"923","DOI":"10.1378\/chest.11-0483","article-title":"The role of target therapies in schistosomiasis-associated pulmonary arterial hypertension","volume":"141","author":"Fernandes","year":"2012","journal-title":"Chest Apr"},{"issue":"6","key":"10.1016\/j.hfc.2022.08.021_bib12","doi-asserted-by":"crossref","DOI":"10.1183\/13993003.00307-2018","article-title":"Survival of patients with schistosomiasis-associated pulmonary arterial hypertension in the modern management era","volume":"51","author":"Fernandes","year":"2018","journal-title":"Eur Respir J"},{"issue":"4","key":"10.1016\/j.hfc.2022.08.021_bib13","doi-asserted-by":"crossref","first-page":"750","DOI":"10.36660\/abc.20200702","article-title":"Update on the Treatment of Pulmonary Arterial Hypertension","volume":"117","author":"Fernandes","year":"2021","journal-title":"Arq Bras Cardiol"},{"issue":"8","key":"10.1016\/j.hfc.2022.08.021_bib14","doi-asserted-by":"crossref","first-page":"1244","DOI":"10.1513\/AnnalsATS.201511-760OC","article-title":"Sarcoidosis in America. Analysis Based on Health Care Use","volume":"13","author":"Baughman","year":"2016","journal-title":"Ann Am Thorac Soc"},{"issue":"9","key":"10.1016\/j.hfc.2022.08.021_bib15","doi-asserted-by":"crossref","first-page":"856","DOI":"10.1001\/jama.2022.1570","article-title":"Diagnosis and Treatment of Pulmonary Sarcoidosis: A Review","volume":"327","author":"Belperio","year":"2022","journal-title":"JAMA"},{"issue":"1","key":"10.1016\/j.hfc.2022.08.021_bib16","doi-asserted-by":"crossref","first-page":"105","DOI":"10.1016\/j.chest.2017.07.008","article-title":"Predictors of Mortality in Pulmonary Sarcoidosis","volume":"153","author":"Kirkil","year":"2018","journal-title":"Chest"},{"key":"10.1016\/j.hfc.2022.08.021_bib17","first-page":"105997","article-title":"Predictors of mortality in fibrosing pulmonary sarcoidosis. Respiratory medicine","volume":"169","author":"Jeny","year":"2020","journal-title":"Aug"},{"issue":"2","key":"10.1016\/j.hfc.2022.08.021_bib18","doi-asserted-by":"crossref","first-page":"296","DOI":"10.1183\/09031936.00175907","article-title":"Clinical predictors of pulmonary hypertension in sarcoidosis","volume":"32","author":"Bourbonnais","year":"2008","journal-title":"Eur Respir J Aug"},{"issue":"5","key":"10.1016\/j.hfc.2022.08.021_bib19","doi-asserted-by":"crossref","DOI":"10.1183\/13993003.01747-2019","article-title":"Physiological predictors of survival in patients with sarcoidosis-associated pulmonary hypertension: results from an international registry","volume":"55","author":"Shlobin","year":"2020","journal-title":"Eur Respir J"},{"issue":"5","key":"10.1016\/j.hfc.2022.08.021_bib20","doi-asserted-by":"crossref","first-page":"783","DOI":"10.1183\/09031936.05.00083404","article-title":"Pulmonary hypertension in advanced sarcoidosis: epidemiology and clinical characteristics","volume":"25","author":"Shorr","year":"2005","journal-title":"Eur Respir J"},{"issue":"4","key":"10.1016\/j.hfc.2022.08.021_bib21","doi-asserted-by":"crossref","DOI":"10.1183\/13993003.00897-2019","article-title":"Prevalence of pulmonary hypertension in pulmonary sarcoidosis: the first large European prospective study","volume":"54","author":"Huitema","year":"2019","journal-title":"Eur Respir J"},{"key":"10.1016\/j.hfc.2022.08.021_bib22","doi-asserted-by":"crossref","first-page":"299","DOI":"10.1007\/978-94-007-4546-9_38","article-title":"Pulmonary arterial hypertension in patients with sarcoidosis: the Pulsar single center experience","volume":"755","author":"Pabst","year":"2013","journal-title":"Adv Exp Med Biol"},{"issue":"5","key":"10.1016\/j.hfc.2022.08.021_bib23","doi-asserted-by":"crossref","first-page":"582","DOI":"10.1097\/MCP.0000000000000701","article-title":"An update on sarcoidosis-associated pulmonary hypertension","volume":"26","author":"Bandyopadhyay","year":"2020","journal-title":"Curr Opin Pulm Med"},{"issue":"1","key":"10.1016\/j.hfc.2022.08.021_bib24","doi-asserted-by":"crossref","first-page":"68","DOI":"10.1136\/thx.2005.042838","article-title":"Pulmonary hypertension associated with sarcoidosis: mechanisms, haemodynamics and prognosis","volume":"61","author":"Nunes","year":"2006","journal-title":"Thorax"},{"key":"10.1016\/j.hfc.2022.08.021_bib25","doi-asserted-by":"crossref","first-page":"72","DOI":"10.1016\/j.rmed.2018.04.015","article-title":"Clinical features of sarcoidosis associated pulmonary hypertension: Results of a multi-national registry","volume":"139","author":"Baughman","year":"2018","journal-title":"Respir Med"},{"issue":"4","key":"10.1016\/j.hfc.2022.08.021_bib26","first-page":"285","article-title":"The frequency of diastolic dysfunction in patients with sarcoidosis and it's relationship with HLA DRB1\u2217 alleles","volume":"36","author":"Ozyilmaz","year":"2019","journal-title":"Sarcoidosis Vasculitis Diffuse Lung Dis"},{"issue":"2","key":"10.1016\/j.hfc.2022.08.021_bib27","doi-asserted-by":"crossref","first-page":"425","DOI":"10.1016\/j.chest.2016.09.009","article-title":"Association of Sarcoidosis With Increased Risk of VTE: A Population-Based Study, 1976 to 2013","volume":"151","author":"Ungprasert","year":"2017","journal-title":"Chest"},{"issue":"163","key":"10.1016\/j.hfc.2022.08.021_bib28","first-page":"31","article-title":"WASOG statement on the diagnosis and management of sarcoidosis-associated pulmonary hypertension","author":"Savale","year":"2022","journal-title":"Eur Respir Rev"},{"issue":"12","key":"10.1016\/j.hfc.2022.08.021_bib29","doi-asserted-by":"crossref","first-page":"1935","DOI":"10.1513\/AnnalsATS.202102-212CME","article-title":"Clinical Presentation and Treatment of High-Risk Sarcoidosis","volume":"18","author":"Perlman","year":"2021","journal-title":"Ann Am Thorac Soc"},{"issue":"2","key":"10.1016\/j.hfc.2022.08.021_bib30","first-page":"82","article-title":"Treatment of sarcoidosis-associated pulmonary hypertension: A single centre retrospective experience using targeted therapies","volume":"31","author":"Keir","year":"2014","journal-title":"Sarcoidosis Vasculitis Diffuse Lung Dis"},{"issue":"4","key":"10.1016\/j.hfc.2022.08.021_bib31","doi-asserted-by":"crossref","DOI":"10.1183\/13993003.00465-2017","article-title":"Management and long-term outcomes of sarcoidosis-associated pulmonary hypertension","volume":"50","author":"Boucly","year":"2017","journal-title":"Eur Respir J"},{"issue":"2","key":"10.1016\/j.hfc.2022.08.021_bib32","doi-asserted-by":"crossref","first-page":"448","DOI":"10.1016\/j.chest.2021.07.2162","article-title":"Riociguat for Sarcoidosis-Associated Pulmonary Hypertension: Results of a 1-Year Double-Blind, Placebo-Controlled Trial","volume":"161","author":"Baughman","year":"2022","journal-title":"Chest"},{"issue":"4","key":"10.1016\/j.hfc.2022.08.021_bib33","doi-asserted-by":"crossref","first-page":"325","DOI":"10.1056\/NEJMoa2008470","article-title":"Inhaled Treprostinil in Pulmonary Hypertension Due to Interstitial Lung Disease","volume":"384","author":"Waxman","year":"2021","journal-title":"N\u00a0Engl J Med"},{"issue":"6","key":"10.1016\/j.hfc.2022.08.021_bib34","doi-asserted-by":"crossref","first-page":"1159","DOI":"10.1016\/j.ajpath.2019.02.007","article-title":"Understanding the Similarities and Differences between Hepatic and Pulmonary Veno-Occlusive Disease","volume":"189","author":"Gunther","year":"2019","journal-title":"Am J Pathol"},{"issue":"4","key":"10.1016\/j.hfc.2022.08.021_bib35","doi-asserted-by":"crossref","first-page":"220","DOI":"10.1097\/MD.0b013e31818193bb","article-title":"Pulmonary veno-occlusive disease: clinical, functional, radiologic, and hemodynamic characteristics and outcome of 24 cases confirmed by histology","volume":"87","author":"Montani","year":"2008","journal-title":"Medicine (Baltimore)"},{"issue":"6","key":"10.1016\/j.hfc.2022.08.021_bib36","doi-asserted-by":"crossref","first-page":"1721","DOI":"10.1183\/13993003.00814-2015","article-title":"Occupational exposure to organic solvents: a risk factor for pulmonary veno-occlusive disease","volume":"46","author":"Montani","year":"2015","journal-title":"Eur Respir J"},{"issue":"4","key":"10.1016\/j.hfc.2022.08.021_bib37","doi-asserted-by":"crossref","first-page":"1069","DOI":"10.1183\/09031936.00088914","article-title":"Mechanisms of exertional dyspnoea in pulmonary veno-occlusive disease with EIF2AK4 mutations","volume":"44","author":"Laveneziana","year":"2014","journal-title":"Eur Respir J"},{"issue":"156","key":"10.1016\/j.hfc.2022.08.021_bib38","first-page":"29","article-title":"Pulmonary capillary haemangiomatosis: a distinct entity?","author":"Weatherald","year":"2020","journal-title":"Eur Respir Rev : official J Eur Respir Soc"},{"issue":"2","key":"10.1016\/j.hfc.2022.08.021_bib39","doi-asserted-by":"crossref","first-page":"183","DOI":"10.1016\/j.resinv.2018.10.004","article-title":"Use of vasodilators for the treatment of pulmonary veno-occlusive disease and pulmonary capillary hemangiomatosis: A systematic review","volume":"57","author":"Ogawa","year":"2019","journal-title":"Respir Investig"},{"issue":"2","key":"10.1016\/j.hfc.2022.08.021_bib40","doi-asserted-by":"crossref","first-page":"125","DOI":"10.1016\/S2213-2600(16)30438-6","article-title":"Clinical phenotypes and outcomes of heritable and sporadic pulmonary veno-occlusive disease: a population-based study","volume":"5","author":"Montani","year":"2017","journal-title":"Lancet Respir Med"},{"issue":"10295","key":"10.1016\/j.hfc.2022.08.021_bib41","doi-asserted-by":"crossref","first-page":"157","DOI":"10.1016\/S0140-6736(21)00311-1","article-title":"Histiocytosis","volume":"398","author":"Emile","year":"2021","journal-title":"Lancet"},{"key":"10.1016\/j.hfc.2022.08.021_bib42","doi-asserted-by":"crossref","first-page":"582581","DOI":"10.3389\/fmed.2020.582581","article-title":"Update on Pulmonary Langerhans Cell Histiocytosis","volume":"7","author":"Radzikowska","year":"2020","journal-title":"Front Med (Lausanne)"},{"issue":"6","key":"10.1016\/j.hfc.2022.08.021_bib43","doi-asserted-by":"crossref","first-page":"2440","DOI":"10.1016\/j.chest.2020.05.609","article-title":"Mechanisms of Exercise Limitation and Prevalence of Pulmonary Hypertension in Pulmonary Langerhans Cell Histiocytosis","volume":"158","author":"Heiden","year":"2020","journal-title":"Chest"},{"issue":"5","key":"10.1016\/j.hfc.2022.08.021_bib44","doi-asserted-by":"crossref","first-page":"746","DOI":"10.1097\/01.tp.0000200304.64613.af","article-title":"Lung transplantation for pulmonary langerhans' cell histiocytosis: a multicenter analysis","volume":"81","author":"Dauriat","year":"2006","journal-title":"Transplantation"},{"issue":"1","key":"10.1016\/j.hfc.2022.08.021_bib45","doi-asserted-by":"crossref","first-page":"216","DOI":"10.1164\/ajrccm.161.1.9807024","article-title":"Severe pulmonary hypertension in histiocytosis X","volume":"161","author":"Fartoukh","year":"2000","journal-title":"Am J Respir Crit Care Med"},{"issue":"5","key":"10.1016\/j.hfc.2022.08.021_bib46","doi-asserted-by":"crossref","first-page":"1150","DOI":"10.1378\/chest.11-2490","article-title":"Pulmonary Langerhans cell histiocytosis-associated pulmonary hypertension: clinical characteristics and impact of pulmonary arterial hypertension therapies","volume":"142","author":"Le Pavec","year":"2012","journal-title":"Chest"},{"issue":"1","key":"10.1016\/j.hfc.2022.08.021_bib47","doi-asserted-by":"crossref","first-page":"57","DOI":"10.1001\/jama.2022.10233","article-title":"Sickle Cell Disease: A Review","volume":"328","author":"Kavanagh","year":"2022","journal-title":"JAMA"},{"issue":"7","key":"10.1016\/j.hfc.2022.08.021_bib48","doi-asserted-by":"crossref","first-page":"e1001484","DOI":"10.1371\/journal.pmed.1001484","article-title":"Global burden of sickle cell anaemia in children under five, 2010-2050: modelling based on demographics, excess mortality, and interventions","volume":"10","author":"Piel","year":"2013","journal-title":"Plos Med"},{"issue":"5","key":"10.1016\/j.hfc.2022.08.021_bib49","doi-asserted-by":"crossref","first-page":"1313","DOI":"10.1016\/j.chest.2015.11.016","article-title":"Chronic Pulmonary Complications of Sickle Cell Disease","volume":"149","author":"Mehari","year":"2016","journal-title":"Chest"},{"issue":"5","key":"10.1016\/j.hfc.2022.08.021_bib50","doi-asserted-by":"crossref","first-page":"561","DOI":"10.1055\/s-0037-1606577","article-title":"Pulmonary Hypertension: Definition, Classification, and Diagnosis","volume":"38","author":"Alves","year":"2017","journal-title":"Semin Respir Crit Care Med"},{"issue":"1","key":"10.1016\/j.hfc.2022.08.021_bib51","doi-asserted-by":"crossref","first-page":"44","DOI":"10.1056\/NEJMoa1005565","article-title":"A\u00a0hemodynamic study of pulmonary hypertension in sickle cell disease","volume":"365","author":"Parent","year":"2011","journal-title":"N\u00a0Engl J Med"},{"issue":"1","key":"10.1016\/j.hfc.2022.08.021_bib52","doi-asserted-by":"crossref","first-page":"112","DOI":"10.1183\/09031936.00134410","article-title":"Pulmonary hypertension diagnosed by right heart catheterisation in sickle cell disease","volume":"39","author":"Fonseca","year":"2012","journal-title":"Eur Respir J"},{"issue":"12","key":"10.1016\/j.hfc.2022.08.021_bib53","doi-asserted-by":"crossref","first-page":"1254","DOI":"10.1001\/jama.2012.358","article-title":"Mortality in adults with sickle cell disease and pulmonary hypertension","volume":"307","author":"Mehari","year":"2012","journal-title":"JAMA"},{"issue":"9","key":"10.1016\/j.hfc.2022.08.021_bib54","doi-asserted-by":"crossref","first-page":"886","DOI":"10.1056\/NEJMoa035477","article-title":"Pulmonary hypertension as a risk factor for death in patients with sickle cell disease","volume":"350","author":"Gladwin","year":"2004","journal-title":"N\u00a0Engl J Med"},{"issue":"2","key":"10.1016\/j.hfc.2022.08.021_bib55","doi-asserted-by":"crossref","first-page":"317","DOI":"10.1111\/bjh.15795","article-title":"Clinical relevance of pulmonary vasculature involvement in sickle cell disease","volume":"185","author":"Carstens","year":"2019","journal-title":"Br J Haematol"},{"issue":"3","key":"10.1016\/j.hfc.2022.08.021_bib56","doi-asserted-by":"crossref","first-page":"422","DOI":"10.1016\/j.healun.2017.11.011","article-title":"Morphologic and immunohistochemical features of pulmonary vasculopathy in end-stage left ventricular systolic failure","volume":"37","author":"Ribeiro de Campos","year":"2018","journal-title":"J\u00a0Heart Lung Transplant"},{"issue":"8","key":"10.1016\/j.hfc.2022.08.021_bib57","doi-asserted-by":"crossref","first-page":"562","DOI":"10.1136\/heartjnl-2019-314810","article-title":"Sickle cell disease: at the crossroads of pulmonary hypertension and diastolic heart failure","volume":"106","author":"Wood","year":"2020","journal-title":"Heart"},{"issue":"6","key":"10.1016\/j.hfc.2022.08.021_bib58","doi-asserted-by":"crossref","first-page":"727","DOI":"10.1164\/rccm.201401-0065ST","article-title":"An official American Thoracic Society clinical practice guideline: diagnosis, risk stratification, and management of pulmonary hypertension of sickle cell disease","volume":"189","author":"Klings","year":"2014","journal-title":"Am J Respir Crit Care Med"},{"issue":"4","key":"10.1016\/j.hfc.2022.08.021_bib59","doi-asserted-by":"crossref","first-page":"855","DOI":"10.1182\/blood-2010-09-306167","article-title":"Hospitalization for pain in patients with sickle cell disease treated with sildenafil for elevated TRV and low exercise capacity","volume":"118","author":"Machado","year":"2011","journal-title":"Blood"},{"issue":"1","key":"10.1016\/j.hfc.2022.08.021_bib60","doi-asserted-by":"crossref","first-page":"54","DOI":"10.1111\/ejh.13612","article-title":"Long-term tolerability of phosphodiesterase-5 inhibitors in pulmonary hypertension of sickle cell disease","volume":"107","author":"Cramer-Bour","year":"2021","journal-title":"Eur J Haematol"},{"issue":"3","key":"10.1016\/j.hfc.2022.08.021_bib61","doi-asserted-by":"crossref","first-page":"426","DOI":"10.1111\/j.1365-2141.2010.08097.x","article-title":"Exercise capacity and haemodynamics in patients with sickle cell disease with pulmonary hypertension treated with bosentan: results of the ASSET studies","volume":"149","author":"Barst","year":"2010","journal-title":"Br J Haematol"}],"container-title":["Heart Failure Clinics"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1551713622000733?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1551713622000733?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2025,10,27]],"date-time":"2025-10-27T08:42:41Z","timestamp":1761554561000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S1551713622000733"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2023,1]]},"references-count":61,"journal-issue":{"issue":"1","published-print":{"date-parts":[[2023,1]]}},"alternative-id":["S1551713622000733"],"URL":"https:\/\/doi.org\/10.1016\/j.hfc.2022.08.021","relation":{},"ISSN":["1551-7136"],"issn-type":[{"type":"print","value":"1551-7136"}],"subject":[],"published":{"date-parts":[[2023,1]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"Unusual Forms of Pulmonary Hypertension","name":"articletitle","label":"Article Title"},{"value":"Heart Failure Clinics","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.hfc.2022.08.021","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"\u00a9 2022 Elsevier Inc. All rights reserved.","name":"copyright","label":"Copyright"}]}}