{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,29]],"date-time":"2026-09-29T15:19:49Z","timestamp":1790695189888,"version":"4.1.0"},"reference-count":22,"publisher":"Elsevier BV","issue":"3","license":[{"start":{"date-parts":[[2016,3,1]],"date-time":"2016-03-01T00:00:00Z","timestamp":1456790400000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"}],"content-domain":{"domain":["heartlungcirc.org","clinicalkey.jp","clinicalkey.com","clinicalkey.es","clinicalkey.com.au","clinicalkey.fr","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Heart, Lung and Circulation"],"published-print":{"date-parts":[[2016,3]]},"DOI":"10.1016\/j.hlc.2015.08.019","type":"journal-article","created":{"date-parts":[[2015,9,30]],"date-time":"2015-09-30T04:40:40Z","timestamp":1443588040000},"page":"275-281","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":19,"title":["High Arrhythmic Burden but Low Mortality during Long-term Follow-up in Arrhythmogenic Right Ventricular Cardiomyopathy"],"prefix":"10.1016","volume":"25","author":[{"given":"Andrew","family":"Martin","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jackie","family":"Crawford","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jonathan R.","family":"Skinner","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Warren","family":"Smith","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"key":"10.1016\/j.hlc.2015.08.019_bib0115","doi-asserted-by":"crossref","first-page":"2226","DOI":"10.1016\/S0735-1097(00)00997-9","article-title":"Clinical profile and long-term follow-up of 37 families with arrhythmogenic right ventricular cardiomyopathy","volume":"36","author":"Nava","year":"2000","journal-title":"J Am Coll Cardiol."},{"key":"10.1016\/j.hlc.2015.08.019_bib0120","doi-asserted-by":"crossref","first-page":"384","DOI":"10.1161\/01.CIR.65.2.384","article-title":"Right ventricular dysplasia: a report of 24 adult cases","volume":"65","author":"Marcus","year":"1982","journal-title":"Circulation."},{"key":"10.1016\/j.hlc.2015.08.019_bib0125","doi-asserted-by":"crossref","first-page":"1879","DOI":"10.1161\/01.CIR.0000143375.93288.82","article-title":"Natural history and risk stratification of arrhythmogenic right ventricular dysplasia\/cardiomyopathy","volume":"110","author":"Hulot","year":"2004","journal-title":"Circulation."},{"key":"10.1016\/j.hlc.2015.08.019_bib0130","doi-asserted-by":"crossref","first-page":"E101","DOI":"10.1161\/01.CIR.101.11.e101","volume":"101","author":"Corrado","year":"2000","journal-title":"Circulation"},{"key":"10.1016\/j.hlc.2015.08.019_bib0135","doi-asserted-by":"crossref","first-page":"1503","DOI":"10.1161\/01.CIR.0000121738.88273.43","article-title":"Implantable cardioverter\/defibrillator therapy in arrhythmogenic right ventricular cardiomyopathy: single-center experience of long-term follow-up and complications in 60 patients","volume":"109","author":"Wichter","year":"2004","journal-title":"Circulation."},{"key":"10.1016\/j.hlc.2015.08.019_bib0140","doi-asserted-by":"crossref","first-page":"161","DOI":"10.1046\/j.1542-474X.2003.08212.x","article-title":"Noninvasive risk stratification in arrhythmogenic right ventricular cardiomyopathy","volume":"8","author":"Turrini","year":"2003","journal-title":"Ann Noninvasive Electrocardiol."},{"key":"10.1016\/j.hlc.2015.08.019_bib0145","doi-asserted-by":"crossref","first-page":"53","DOI":"10.1136\/heart.85.1.53","article-title":"Long term results of cardioverter-defibrillator implantation in patients with right ventricular dysplasia and malignant ventricular tachyarrhythmias","volume":"85","author":"Tavernier","year":"2001","journal-title":"Heart."},{"key":"10.1016\/j.hlc.2015.08.019_bib0150","doi-asserted-by":"crossref","first-page":"1843","DOI":"10.1016\/j.jacc.2004.01.030","article-title":"Implantable cardioverter-defibrillators in patients with arrhythmogenic right ventricular dysplasia\/cardiomyopathy","volume":"43","author":"Roguin","year":"2004","journal-title":"J Am Coll Cardiol."},{"key":"10.1016\/j.hlc.2015.08.019_bib0155","doi-asserted-by":"crossref","first-page":"1188","DOI":"10.1016\/j.hrthm.2005.08.022","article-title":"Predictors of appropriate implantable defibrillator therapies in patients with arrhythmogenic right ventricular dysplasia","volume":"2","author":"Piccini","year":"2005","journal-title":"Heart Rhythm."},{"key":"10.1016\/j.hlc.2015.08.019_bib0160","doi-asserted-by":"crossref","first-page":"41","DOI":"10.1023\/A:1009714718034","article-title":"Arrhythmogenic right ventricular dysplasia: clinical results with implantable cardioverter defibrillators","volume":"1","author":"Pacing Clin Electrophysiol Link","year":"1997","journal-title":"J Interv Card Electrophysiol."},{"key":"10.1016\/j.hlc.2015.08.019_bib0165","doi-asserted-by":"crossref","first-page":"e350","DOI":"10.1161\/CIRCUALTIONAHA.108.189742","volume":"117","author":"Epstein","year":"2008","journal-title":"Circulation."},{"key":"10.1016\/j.hlc.2015.08.019_bib0170","doi-asserted-by":"crossref","first-page":"3084","DOI":"10.1161\/01.CIR.0000103130.33451.D2","article-title":"Implantable cardioverter-defibrillator therapy for prevention of sudden death in patients with arrhythmogenic right ventricular cardiomyopathy\/dysplasia","volume":"108","author":"Corrado","year":"2003","journal-title":"Circulation."},{"key":"10.1016\/j.hlc.2015.08.019_bib0175","doi-asserted-by":"crossref","first-page":"400","DOI":"10.1016\/j.jacc.2004.08.068","article-title":"The impact of implantable cardioverter-defibrillator therapy on survival in autosomal-dominant arrhythmogenic right ventricular cardiomyopathy (ARVD5)","volume":"45","author":"Hodgkinson","year":"2005","journal-title":"J Am Coll Cardiol."},{"key":"10.1016\/j.hlc.2015.08.019_bib0180","doi-asserted-by":"crossref","first-page":"750","DOI":"10.1111\/j.1540-8167.2011.02288.x","article-title":"Long-term follow-up in patients with arrhythmogenic right ventricular cardiomyopathy","volume":"23","author":"Li","year":"2012","journal-title":"J Cardiovasc Electrophysiol."},{"key":"10.1016\/j.hlc.2015.08.019_bib0185","doi-asserted-by":"crossref","first-page":"1144","DOI":"10.1161\/CIRCULATIONAHA.109.913871","article-title":"Prophylactic implantable defibrillator in patients with arrhythmogenic right ventricular cardiomyopathy\/dysplasia and no prior ventricular fibrillation or sustained ventricular tachycardia","volume":"122","author":"Corrado","year":"2010","journal-title":"Circulation."},{"key":"10.1016\/j.hlc.2015.08.019_bib0190","doi-asserted-by":"crossref","first-page":"1485","DOI":"10.1016\/j.jacc.2011.06.043","article-title":"Incidence and predictors of implantable cardioverter-defibrillator therapy in patients with arrhythmogenic right ventricular dysplasia\/cardiomyopathy undergoing implantable cardioverter-defibrillator implantation for primary prevention","volume":"58","author":"Bhonsale","year":"2011","journal-title":"J Am Coll Cardiol."},{"key":"10.1016\/j.hlc.2015.08.019_bib0195","doi-asserted-by":"crossref","first-page":"1306","DOI":"10.1016\/j.hrthm.2007.06.022","article-title":"Long QT and Brugada syndrome gene mutations in New Zealand","volume":"4","author":"Chung","year":"2007","journal-title":"Heart Rhythm."},{"key":"10.1016\/j.hlc.2015.08.019_bib0200","doi-asserted-by":"crossref","first-page":"593","DOI":"10.1016\/j.hlc.2011.04.036","article-title":"Symptoms and signs associated with syncope in young people with primary cardiac arrhythmias","volume":"20","author":"MacCormick","year":"2011","journal-title":"Heart Lung Circ."},{"key":"10.1016\/j.hlc.2015.08.019_bib0205","doi-asserted-by":"crossref","first-page":"233","DOI":"10.1016\/j.hrthm.2012.10.043","article-title":"Community detection of long QT syndrome with a clinical registry: an alternative to ECG screening programs?","volume":"10","author":"Earle","year":"2013","journal-title":"Heart Rhythm."},{"issue":"3","key":"10.1016\/j.hlc.2015.08.019_bib0210","doi-asserted-by":"crossref","first-page":"412","DOI":"10.1016\/j.hrthm.2010.11.016","article-title":"Prospective, population-based long QT molecular autopsy study of postmortem negative sudden death in 1 to 40 year olds","volume":"8","author":"Skinner","year":"2011","journal-title":"Heart Rhythm."},{"key":"10.1016\/j.hlc.2015.08.019_bib0215","unstructured":"New Zealand Ministry of Health 2013 [Accessed 02\/05\/2013]. Available from: http:\/\/www.health.govt.nz."},{"key":"10.1016\/j.hlc.2015.08.019_bib0220","doi-asserted-by":"crossref","first-page":"1533","DOI":"10.1161\/CIRCULATIONAHA.108.840827","article-title":"Diagnosis of arrhythmogenic right ventricular cardiomyopathy\/dysplasia: proposed modification of the task force criteria","volume":"121","author":"Marcus","year":"2010","journal-title":"Circulation"}],"container-title":["Heart, Lung and Circulation"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1443950615013876?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1443950615013876?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2018,9,19]],"date-time":"2018-09-19T01:56:41Z","timestamp":1537322201000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S1443950615013876"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2016,3]]},"references-count":22,"journal-issue":{"issue":"3","published-print":{"date-parts":[[2016,3]]}},"alternative-id":["S1443950615013876"],"URL":"https:\/\/doi.org\/10.1016\/j.hlc.2015.08.019","relation":{},"ISSN":["1443-9506"],"issn-type":[{"value":"1443-9506","type":"print"}],"subject":[],"published":{"date-parts":[[2016,3]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"High Arrhythmic Burden but Low Mortality during Long-term Follow-up in Arrhythmogenic Right Ventricular Cardiomyopathy","name":"articletitle","label":"Article Title"},{"value":"Heart, Lung and Circulation","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.hlc.2015.08.019","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"Copyright \u00a9 2015 Australian and New Zealand Society of Cardiac and Thoracic Surgeons (ANZSCTS) and the Cardiac Society of Australia and New Zealand (CSANZ). Published by Elsevier Ltd. All rights reserved.","name":"copyright","label":"Copyright"}]}}