{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,1]],"date-time":"2026-10-01T19:27:32Z","timestamp":1790882852341,"version":"4.1.0"},"reference-count":57,"publisher":"Elsevier BV","issue":"3","license":[{"start":{"date-parts":[[2020,8,1]],"date-time":"2020-08-01T00:00:00Z","timestamp":1596240000000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2020,8,1]],"date-time":"2020-08-01T00:00:00Z","timestamp":1596240000000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/legal\/tdmrep-license"}],"funder":[{"DOI":"10.13039\/100000002","name":"National Institutes of Health","doi-asserted-by":"publisher","award":["AI-086037"],"award-info":[{"award-number":["AI-086037"]}],"id":[{"id":"10.13039\/100000002","id-type":"DOI","asserted-by":"publisher"}]},{"DOI":"10.13039\/100000002","name":"National Institutes of Health","doi-asserted-by":"publisher","award":["AI-48693"],"award-info":[{"award-number":["AI-48693"]}],"id":[{"id":"10.13039\/100000002","id-type":"DOI","asserted-by":"publisher"}]},{"DOI":"10.13039\/100000002","name":"National Institutes of Health","doi-asserted-by":"publisher","award":["AI-101093"],"award-info":[{"award-number":["AI-101093"]}],"id":[{"id":"10.13039\/100000002","id-type":"DOI","asserted-by":"publisher"}]}],"content-domain":{"domain":["clinicalkey.com","clinicalkey.com.au","clinicalkey.es","clinicalkey.fr","clinicalkey.jp","theclinics.com","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Immunology and Allergy Clinics of North America"],"published-print":{"date-parts":[[2020,8]]},"DOI":"10.1016\/j.iac.2020.03.002","type":"journal-article","created":{"date-parts":[[2020,6,7]],"date-time":"2020-06-07T07:33:23Z","timestamp":1591515203000},"page":"385-402","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":17,"title":["The Importance of Primary Immune Deficiency Registries"],"prefix":"10.1016","volume":"40","author":[{"given":"Joao Pedro","family":"Lopes","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Charlotte","family":"Cunningham-Rundles","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"issue":"4","key":"10.1016\/j.iac.2020.03.002_bib1","doi-asserted-by":"crossref","first-page":"607","DOI":"10.1016\/j.jaci.2004.02.018","article-title":"Primary immunodeficiency: looking backwards, looking forwards","volume":"113","author":"Shearer","year":"2004","journal-title":"J\u00a0Allergy Clin Immunol"},{"issue":"2","key":"10.1016\/j.iac.2020.03.002_bib2","doi-asserted-by":"crossref","first-page":"306","DOI":"10.1111\/j.1365-2249.2006.03292.x","article-title":"The European internet-based patient and research database for primary immunodeficiencies: results 2004-06","volume":"147","author":"Eades-Perner","year":"2007","journal-title":"Clin Exp Immunol"},{"issue":"6","key":"10.1016\/j.iac.2020.03.002_bib3","doi-asserted-by":"crossref","first-page":"477","DOI":"10.1023\/A:1026416017763","article-title":"Primary immunodeficiency diseases in Norway","volume":"20","author":"Stray-Pedersen","year":"2000","journal-title":"J\u00a0Clin Immunol"},{"issue":"3","key":"10.1016\/j.iac.2020.03.002_bib4","doi-asserted-by":"crossref","first-page":"415","DOI":"10.1016\/S0091-6749(97)70257-4","article-title":"The spectrum of primary immunodeficiency disorders in Australia","volume":"100","author":"Baumgart","year":"1997","journal-title":"J\u00a0Allergy Clin Immunol"},{"key":"10.1016\/j.iac.2020.03.002_bib5","doi-asserted-by":"crossref","first-page":"333","DOI":"10.1023\/A:1027382916924","article-title":"Primary immunodeficiency syndrome in Spain: first report of the national registry in children and adults","volume":"17","author":"Matamoros","year":"1997","journal-title":"J\u00a0Clin Immunol"},{"issue":"6","key":"10.1016\/j.iac.2020.03.002_bib6","doi-asserted-by":"crossref","first-page":"479","DOI":"10.1007\/BF00916954","article-title":"Primary immunodeficiencies in Switzerland: first report of the national registry in adults and children","volume":"8","author":"Ryser","year":"1988","journal-title":"J\u00a0Clin Immunol"},{"issue":"2","key":"10.1016\/j.iac.2020.03.002_bib7","doi-asserted-by":"crossref","first-page":"86","DOI":"10.1007\/BF00916891","article-title":"Primary immunodeficiency disorders in Sweden: cases among children, 1974-1979","volume":"2","author":"Fasth","year":"1982","journal-title":"J\u00a0Clin Immunol"},{"issue":"2","key":"10.1016\/j.iac.2020.03.002_bib8","doi-asserted-by":"crossref","first-page":"264","DOI":"10.1016\/j.clim.2010.02.021","article-title":"The French national registry of primary immunodeficiency diseases","volume":"135","year":"2010","journal-title":"Clin Immunol"},{"issue":"4","key":"10.1016\/j.iac.2020.03.002_bib10","doi-asserted-by":"crossref","first-page":"428","DOI":"10.1007\/s10875-014-0028-1","article-title":"USIDNET: a strategy to build a community of clinical immunologists","volume":"34","author":"Sullivan","year":"2014","journal-title":"J\u00a0Clin Immunol"},{"issue":"3","key":"10.1016\/j.iac.2020.03.002_bib11","doi-asserted-by":"crossref","first-page":"155","DOI":"10.1097\/00005792-200005000-00003","article-title":"Chronic granulomatous disease. Report on a national registry of 368 patients","volume":"79","author":"Winkelstein","year":"2000","journal-title":"Medicine (Baltimore)"},{"issue":"5","key":"10.1016\/j.iac.2020.03.002_bib12","doi-asserted-by":"crossref","first-page":"973","DOI":"10.1093\/clinids\/13.5.973","article-title":"Interferon-gamma in the management of chronic granulomatous disease","volume":"13","author":"Gallin","year":"1991","journal-title":"Rev Infect Dis"},{"issue":"12","key":"10.1016\/j.iac.2020.03.002_bib13","doi-asserted-by":"crossref","first-page":"881","DOI":"10.1056\/NEJM200103223441203","article-title":"Treatment of chronic granulomatous disease with nonmyeloablative conditioning and a T-cell-depleted hematopoietic allograft","volume":"344","author":"Horwitz","year":"2001","journal-title":"N\u00a0Engl J Med"},{"issue":"24","key":"10.1016\/j.iac.2020.03.002_bib14","doi-asserted-by":"crossref","first-page":"2416","DOI":"10.1056\/NEJMoa021931","article-title":"Itraconazole to prevent fungal infections in chronic granulomatous disease","volume":"348","author":"Gallin","year":"2003","journal-title":"N\u00a0Engl J Med"},{"issue":"5","key":"10.1016\/j.iac.2020.03.002_bib15","doi-asserted-by":"crossref","first-page":"692","DOI":"10.1086\/422993","article-title":"Long-term interferon-gamma therapy for patients with chronic granulomatous disease","volume":"39","author":"Marciano","year":"2004","journal-title":"Clin Infect Dis"},{"issue":"5","key":"10.1016\/j.iac.2020.03.002_bib16","doi-asserted-by":"crossref","first-page":"556","DOI":"10.1007\/s10875-018-0530-y","article-title":"Renal disease in chronic granulomatous disease: data from the USIDNETregistry","volume":"38","author":"Sacco","year":"2018","journal-title":"J\u00a0Clin Immunol"},{"issue":"4","key":"10.1016\/j.iac.2020.03.002_bib17","doi-asserted-by":"crossref","first-page":"448","DOI":"10.1007\/s10875-019-00635-2","article-title":"Role of allogeneic hematopoietic stem cell transplant for Chronic Granulomatous Disease (CGD): a Report of the United States Immunodeficiency Network","volume":"39","author":"Yonkof","year":"2019","journal-title":"J\u00a0Clin Immunol"},{"issue":"4","key":"10.1016\/j.iac.2020.03.002_bib18","doi-asserted-by":"crossref","first-page":"193","DOI":"10.1097\/01.md.0000229482.27398.ad","article-title":"X-linked agammaglobulinemia: report on a United States registry of 201 patients","volume":"85","author":"Winkelstein","year":"2006","journal-title":"Medicine"},{"issue":"1","key":"10.1016\/j.iac.2020.03.002_bib19","first-page":"3","article-title":"Search for poliovirus carriers among people with primary immune deficiency diseases in the United States, Mexico, Brazil, and the United Kingdom","volume":"82","author":"Halsey","year":"2004","journal-title":"Bull WorldHealthOrgan"},{"issue":"5","key":"10.1016\/j.iac.2020.03.002_bib20","doi-asserted-by":"crossref","first-page":"253","DOI":"10.1097\/MD.0b013e318187ed81","article-title":"Adults with X-linked agammaglobulinemia: impact of disease on daily lives, quality of life, educational and socioeconomic status, knowledge of inheritance, and reproductive attitudes","volume":"87","author":"Winkelstein","year":"2008","journal-title":"Medicine"},{"issue":"6","key":"10.1016\/j.iac.2020.03.002_bib21","doi-asserted-by":"crossref","first-page":"627","DOI":"10.1007\/s10875-014-0056-x","article-title":"Autoimmunity and inflammation in X-linked agammaglobulinemia","volume":"34","author":"Hernandez-Trujillo","year":"2014","journal-title":"J\u00a0Clin Immunol"},{"issue":"3","key":"10.1016\/j.iac.2020.03.002_bib22","doi-asserted-by":"crossref","first-page":"287","DOI":"10.1007\/s10875-017-0374-x","article-title":"Gastrointestinal Manifestations in X-linked Agammaglobulinemia","volume":"37","author":"Barmettler","year":"2017","journal-title":"J\u00a0Clin Immunol"},{"issue":"3","key":"10.1016\/j.iac.2020.03.002_bib23","first-page":"100018","article-title":"X-linked agammaglobulinemia (XLA):phenotype, diagnosis, and therapeutic challenges around the world","volume":"12","author":"El-Sayed","year":"2019","journal-title":"WorldAllergyOrgan J"},{"issue":"1 Pt 1","key":"10.1016\/j.iac.2020.03.002_bib24","doi-asserted-by":"crossref","first-page":"47","DOI":"10.1016\/S0022-3476(97)70123-9","article-title":"Clinical spectrum of X-linked hyper-IgM syndrome","volume":"131","author":"Levy","year":"1997","journal-title":"J\u00a0Pediatr"},{"issue":"2","key":"10.1016\/j.iac.2020.03.002_bib25","doi-asserted-by":"crossref","first-page":"977","DOI":"10.4049\/jimmunol.158.2.977","article-title":"Cholangiopathy and tumors of the pancreas, liver, and biliary tree in boys with X-linked immunodeficiency with hyper-IgM","volume":"158","author":"Hayward","year":"1997","journal-title":"J\u00a0Immunol"},{"issue":"6","key":"10.1016\/j.iac.2020.03.002_bib26","doi-asserted-by":"crossref","first-page":"373","DOI":"10.1097\/01.md.0000100046.06009.b0","article-title":"The X-linked hyper-IgM syndrome: clinical and immunologic features of 79 patients","volume":"82","author":"Winkelstein","year":"2003","journal-title":"Medicine"},{"issue":"14","key":"10.1016\/j.iac.2020.03.002_bib27","doi-asserted-by":"crossref","first-page":"3811","DOI":"10.1182\/blood-2011-04-351254","article-title":"Partial immune reconstitution of X-linked hyper IgM syndrome with recombinant CD40 ligand","volume":"118","author":"Jain","year":"2011","journal-title":"Blood"},{"issue":"5","key":"10.1016\/j.iac.2020.03.002_bib28","doi-asserted-by":"crossref","first-page":"490","DOI":"10.1007\/s10875-016-0291-4","article-title":"Hyper IgM Syndrome: a report from the USIDNETregistry","volume":"36","author":"Leven","year":"2016","journal-title":"J\u00a0Clin Immunol"},{"issue":"4","key":"10.1016\/j.iac.2020.03.002_bib29","doi-asserted-by":"crossref","first-page":"1282","DOI":"10.1016\/j.jaci.2016.07.039","article-title":"Long-term outcomes of 176 patients with X-linked hyper-IgM syndrome treated with or without hematopoietic cell transplantation","volume":"139","author":"de la Morena","year":"2017","journal-title":"J\u00a0Allergy Clin Immunol"},{"issue":"4","key":"10.1016\/j.iac.2020.03.002_bib30","doi-asserted-by":"crossref","first-page":"760","DOI":"10.1016\/j.jaci.2007.08.043","article-title":"Population-based newborn screening for severe combined immunodeficiency: steps toward implementation","volume":"120","author":"Puck","year":"2007","journal-title":"The J Allergy Clin Immunol"},{"issue":"2","key":"10.1016\/j.iac.2020.03.002_bib31","doi-asserted-by":"crossref","first-page":"131","DOI":"10.1007\/s12016-013-8379-6","article-title":"Recent advances in transplantation for primary immune deficiency diseases: a comprehensive review","volume":"46","author":"de la Morena","year":"2014","journal-title":"Clin Rev Allergy Immunol"},{"issue":"3","key":"10.1016\/j.iac.2020.03.002_bib32","doi-asserted-by":"crossref","first-page":"658","DOI":"10.1016\/j.jaci.2012.11.033","article-title":"Combined immunodeficiency: the Middle East experience","volume":"131","author":"Al-Herz","year":"2013","journal-title":"J\u00a0Allergy Clin Immunol"},{"issue":"2","key":"10.1016\/j.iac.2020.03.002_bib33","doi-asserted-by":"crossref","first-page":"170","DOI":"10.1016\/j.clim.2015.07.013","article-title":"Combined immunodeficiency in the United States and Kuwait: comparison of patients' characteristics and molecular diagnosis","volume":"161","author":"Al-Herz","year":"2015","journal-title":"Clin Immunol"},{"issue":"1\u20133","key":"10.1016\/j.iac.2020.03.002_bib34","doi-asserted-by":"crossref","first-page":"78","DOI":"10.1007\/s12026-007-0024-0","article-title":"Common variable immune deficiency: reviews, continued puzzles, and a new registry","volume":"38","author":"Cunningham-Rundles","year":"2007","journal-title":"Immunol Res"},{"issue":"2","key":"10.1016\/j.iac.2020.03.002_bib35","doi-asserted-by":"crossref","first-page":"143","DOI":"10.1016\/S1081-1206(10)60638-2","article-title":"Subspecialty evaluation of chronically ill hospitalized patients with suspected immune defects","volume":"99","author":"Mehra","year":"2007","journal-title":"Ann Allergy Asthma Immunol"},{"issue":"1","key":"10.1016\/j.iac.2020.03.002_bib36","doi-asserted-by":"crossref","first-page":"28","DOI":"10.1007\/s10875-017-0456-9","article-title":"Autoimmune cytopenias and associated conditions in CVID: a report from the USIDNETregistry","volume":"38","author":"Feuille","year":"2018","journal-title":"J\u00a0Clin Immunol"},{"issue":"2","key":"10.1016\/j.iac.2020.03.002_bib37","doi-asserted-by":"crossref","first-page":"318","DOI":"10.1016\/j.semarthrit.2018.02.013","article-title":"Phenotypic characterization of patients with rheumatologic manifestations of common variable immunodeficiency","volume":"48","author":"Gutierrez","year":"2018","journal-title":"Semin Arthritis Rheum"},{"issue":"4","key":"10.1016\/j.iac.2020.03.002_bib38","doi-asserted-by":"crossref","first-page":"440","DOI":"10.1007\/s10875-019-00640-5","article-title":"Factors beyond lack of antibody govern pulmonary complications in primary antibody deficiency","volume":"39","author":"Weinberger","year":"2019","journal-title":"J\u00a0Clin Immunol"},{"issue":"6","key":"10.1016\/j.iac.2020.03.002_bib39","doi-asserted-by":"crossref","first-page":"569","DOI":"10.1007\/s10875-019-00657-w","article-title":"Cellular defects in CVID patients with chronic lung disease in the USIDNETregistry","volume":"39","author":"Kellner","year":"2019","journal-title":"J\u00a0Clin Immunol"},{"key":"10.1016\/j.iac.2020.03.002_bib40","doi-asserted-by":"crossref","first-page":"1740","DOI":"10.3389\/fimmu.2017.01740","article-title":"Common variable immunodeficiency non-infectious disease endotypes redefined using unbiased network clustering in large electronic datasets","volume":"8","author":"Farmer","year":"2017","journal-title":"Front Immunol"},{"issue":"5","key":"10.1016\/j.iac.2020.03.002_bib41","doi-asserted-by":"crossref","first-page":"950","DOI":"10.1016\/j.jpeds.2012.06.018","article-title":"Immunoglobulin deficiencies: the B-lymphocyte side of DiGeorge Syndrome","volume":"161","author":"Patel","year":"2012","journal-title":"J\u00a0Pediatr"},{"issue":"3","key":"10.1016\/j.iac.2020.03.002_bib42","doi-asserted-by":"crossref","first-page":"996","DOI":"10.1016\/j.jaip.2017.06.041","article-title":"Autosomal dominant Hyper-IgE syndrome in the USIDNETregistry","volume":"6","author":"Gernez","year":"2018","journal-title":"J\u00a0Allergy Clin Immunol Pract"},{"issue":"3","key":"10.1016\/j.iac.2020.03.002_bib43","doi-asserted-by":"crossref","first-page":"284","DOI":"10.1006\/clim.2001.5132","article-title":"Outcome of intravenous immunoglobulin-transmitted hepatitis C virus infection in primary immunodeficiency","volume":"101","author":"Razvi","year":"2001","journal-title":"Clin Immunol"},{"issue":"Suppl 1","key":"10.1016\/j.iac.2020.03.002_bib44","doi-asserted-by":"crossref","first-page":"153","DOI":"10.1111\/cei.12551","article-title":"Intravenous immunoglobulin-related thromboembolic events - an accusation that proves the opposite","volume":"178","author":"Basta","year":"2014","journal-title":"Clin Exp Immunol"},{"issue":"3","key":"10.1016\/j.iac.2020.03.002_bib45","doi-asserted-by":"crossref","first-page":"1028","DOI":"10.1016\/j.jaci.2017.05.024","article-title":"Cancer in primary immunodeficiency diseases: cancer incidence in the United States Immune Deficiency Network Registry","volume":"141","author":"Mayor","year":"2018","journal-title":"J\u00a0Allergy Clin Immunol"},{"issue":"6","key":"10.1016\/j.iac.2020.03.002_bib46","doi-asserted-by":"crossref","first-page":"717","DOI":"10.1007\/s10875-018-0534-7","article-title":"Prevalence of granulomas in patients with primary immunodeficiency disorders, united states: data from National Health Care Claims and the US Immunodeficiency Network Registry","volume":"38","author":"Leung","year":"2018","journal-title":"J\u00a0Clin Immunol"},{"issue":"5","key":"10.1016\/j.iac.2020.03.002_bib47","doi-asserted-by":"crossref","first-page":"1436","DOI":"10.1016\/j.jaci.2016.06.030","article-title":"Rubella persistence in epidermal keratinocytes and granuloma M2 macrophages in patients with primary immunodeficiencies","volume":"138","author":"Perelygina","year":"2016","journal-title":"J\u00a0Allergy Clin Immunol"},{"issue":"1","key":"10.1016\/j.iac.2020.03.002_bib48","doi-asserted-by":"crossref","first-page":"273","DOI":"10.1016\/j.jaci.2014.09.024","article-title":"Food allergy in patients with primary immunodeficiency diseases: prevalence within the US Immunodeficiency Network (USIDNET)","volume":"135","author":"Tuano","year":"2015","journal-title":"J\u00a0Allergy Clin Immunol"},{"issue":"1","key":"10.1016\/j.iac.2020.03.002_bib49","doi-asserted-by":"crossref","first-page":"22","DOI":"10.1007\/s10875-016-0353-7","article-title":"Lack of clinical hypersensitivity to penicillin antibiotics in common variable immunodeficiency","volume":"37","author":"Hartman","year":"2017","journal-title":"J\u00a0Clin Immunol"},{"issue":"4","key":"10.1016\/j.iac.2020.03.002_bib50","doi-asserted-by":"crossref","first-page":"259","DOI":"10.1016\/j.anai.2010.08.002","article-title":"Drug allergy: an updated practice parameter","volume":"105","year":"2010","journal-title":"Ann Allergy Asthma Immunol"},{"issue":"3","key":"10.1016\/j.iac.2020.03.002_bib51","doi-asserted-by":"crossref","first-page":"225","DOI":"10.1007\/s10875-018-0476-0","article-title":"Low serum IgE is a sensitive and specific marker for Common Variable Immunodeficiency (CVID)","volume":"38","author":"Lawrence","year":"2018","journal-title":"J\u00a0Clin Immunol"},{"issue":"6","key":"10.1016\/j.iac.2020.03.002_bib52","doi-asserted-by":"crossref","first-page":"592","DOI":"10.1007\/s10875-017-0415-5","article-title":"Two sides of the same coin: pediatric-onset and adult-onset common variable immune deficiency","volume":"37","author":"Sanchez","year":"2017","journal-title":"J\u00a0Clin Immunol"},{"issue":"5","key":"10.1016\/j.iac.2020.03.002_bib53","doi-asserted-by":"crossref","first-page":"852","DOI":"10.1111\/j.1399-3038.2010.01004.x","article-title":"Pediatric common variable immunodeficiency: immunologic and phenotypic associations with switched memory B cells","volume":"21","author":"Yong","year":"2010","journal-title":"Pediatr Allergy Immunol"},{"issue":"7","key":"10.1016\/j.iac.2020.03.002_bib54","doi-asserted-by":"crossref","first-page":"638","DOI":"10.1007\/s10875-015-0196-7","article-title":"Perceived health in patients with primary immune deficiency","volume":"35","author":"Seeborg","year":"2015","journal-title":"J\u00a0Clin Immunol"},{"issue":"2","key":"10.1016\/j.iac.2020.03.002_bib55","doi-asserted-by":"crossref","first-page":"153","DOI":"10.1007\/s10875-016-0367-1","article-title":"Increasedincidence of fatigue in patients with primary immunodeficiency disorders: prevalence and associations within the US immunodeficiency network registry","volume":"37","author":"Hajjar","year":"2017","journal-title":"J\u00a0Clin Immunol"},{"issue":"3","key":"10.1016\/j.iac.2020.03.002_bib56","doi-asserted-by":"crossref","first-page":"283","DOI":"10.1007\/s10875-018-0492-0","article-title":"Complications associated with underweight primary immunodeficiency patients: prevalence and associations within the USIDNET Registry","volume":"38","author":"Ruffner","year":"2018","journal-title":"J\u00a0Clin Immunol"},{"key":"10.1016\/j.iac.2020.03.002_bib57","doi-asserted-by":"crossref","first-page":"430","DOI":"10.1111\/vox.12651","article-title":"Latent therapeutic demand model for the immunoglobulin replacement therapy of primary immune deficiency disorders in the USA","volume":"113","author":"Stonebraker","year":"2018","journal-title":"Vox Sang"},{"key":"10.1016\/j.iac.2020.03.002_bib58","doi-asserted-by":"crossref","first-page":"627","DOI":"10.3389\/fimmu.2014.00627","article-title":"Primary immune deficiencies - principles of care","volume":"5","author":"Chapel","year":"2014","journal-title":"Front Immunol"}],"container-title":["Immunology and Allergy Clinics of North America"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S088985612030014X?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S088985612030014X?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2025,10,11]],"date-time":"2025-10-11T10:43:25Z","timestamp":1760179405000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S088985612030014X"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2020,8]]},"references-count":57,"journal-issue":{"issue":"3","published-print":{"date-parts":[[2020,8]]}},"alternative-id":["S088985612030014X"],"URL":"https:\/\/doi.org\/10.1016\/j.iac.2020.03.002","relation":{},"ISSN":["0889-8561"],"issn-type":[{"value":"0889-8561","type":"print"}],"subject":[],"published":{"date-parts":[[2020,8]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"The Importance of Primary Immune Deficiency Registries","name":"articletitle","label":"Article Title"},{"value":"Immunology and Allergy Clinics of North America","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.iac.2020.03.002","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"\u00a9 2020 Elsevier Inc. All rights reserved.","name":"copyright","label":"Copyright"}]}}