{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,22]],"date-time":"2026-09-22T09:50:36Z","timestamp":1790070636831,"version":"4.0.1"},"reference-count":20,"publisher":"Elsevier BV","issue":"1","license":[{"start":{"date-parts":[[2013,3,1]],"date-time":"2013-03-01T00:00:00Z","timestamp":1362096000000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["International Journal of Cardiology"],"published-print":{"date-parts":[[2013,3]]},"DOI":"10.1016\/j.ijcard.2011.06.084","type":"journal-article","created":{"date-parts":[[2011,7,23]],"date-time":"2011-07-23T13:07:48Z","timestamp":1311426468000},"page":"106-110","source":"Crossref","is-referenced-by-count":50,"title":["Treatment of segmental pulmonary artery hypertension in adults with congenital heart disease"],"prefix":"10.1016","volume":"164","author":[{"given":"Mark J.","family":"Schuuring","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Berto J.","family":"Bouma","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Rachael","family":"Cordina","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Michael A.","family":"Gatzoulis","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Werner","family":"Budts","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mary P.","family":"Mullen","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jeroen C.","family":"Vis","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"David","family":"Celermajer","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Barbara J.M.","family":"Mulder","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"key":"10.1016\/j.ijcard.2011.06.084_bb0005","doi-asserted-by":"crossref","first-page":"1039","DOI":"10.1161\/CIRCULATIONAHA.105.592386","article-title":"Pulmonary vascular disease in adults with congenital heart disease","volume":"1158","author":"Diller","year":"2007","journal-title":"Circulation"},{"issue":"3","key":"10.1016\/j.ijcard.2011.06.084_bb0010","doi-asserted-by":"crossref","first-page":"294","DOI":"10.1016\/j.ijcard.2007.04.184","article-title":"Echocardiographic and right heart catheterization techniques in patients with pulmonary arterial hypertension","volume":"125","author":"Celermajer","year":"2008","journal-title":"Int J Cardiol"},{"issue":"2","key":"10.1016\/j.ijcard.2011.06.084_bb0015","doi-asserted-by":"crossref","first-page":"198","DOI":"10.1016\/j.ijcard.2006.09.017","article-title":"Pulmonary arterial hypertension in congenital heart disease: an epidemiologic perspective from a Dutch registry","volume":"120","author":"Duffels","year":"2007","journal-title":"Int J Cardiol"},{"key":"10.1016\/j.ijcard.2011.06.084_bb0020","author":"Cruz"},{"issue":"2","key":"10.1016\/j.ijcard.2011.06.084_bb0025","doi-asserted-by":"crossref","first-page":"349","DOI":"10.1148\/rg.262055092","article-title":"Congenital and acquired pulmonary artery anomalies in the adult: radiologic overview","volume":"26","author":"Casta\u00f1er","year":"2006","journal-title":"Radiographics"},{"issue":"1","key":"10.1016\/j.ijcard.2011.06.084_bb0030","doi-asserted-by":"crossref","first-page":"e4","DOI":"10.1016\/j.ijcard.2008.11.125","article-title":"Adult presentation of combined unilateral atresia of the right proximal pulmonary artery and left patent ductus arteriosus: case report and embryological considerations","volume":"141","author":"Deutsch","year":"2010","journal-title":"Int J Cardiol"},{"issue":"4","key":"10.1016\/j.ijcard.2011.06.084_bb0035","doi-asserted-by":"crossref","first-page":"329","DOI":"10.1097\/01.aco.0000137092.83225.05","article-title":"New developments in the transcatheter treatment of congenital heart disease","volume":"17","author":"Mertens","year":"2004","journal-title":"Curr Opin Anaesthesiol"},{"key":"10.1016\/j.ijcard.2011.06.084_bb0040","doi-asserted-by":"crossref","first-page":"48","DOI":"10.1161\/CIRCULATIONAHA.106.630715","article-title":"Bosentan Randomized Trial of Endothelin Antagonist Therapy-5 (BREATHE-5) Investigators. Bosentan therapy in patients with Eisenmenger Syndrome: a multicenter, double-blind, randomized, placebo-controlled study","volume":"114","author":"Gali\u00e8","year":"2006","journal-title":"Circulation"},{"key":"10.1016\/j.ijcard.2011.06.084_bb0045","first-page":"359","article-title":"Adult patients with pulmonary arterial hypertension due to congenital heart disease: a review on advanced medical treatment with bosentan","volume":"6","author":"Schuuring","year":"2010","journal-title":"Ther Clin Risk Manag"},{"issue":"9","key":"10.1016\/j.ijcard.2011.06.084_bb0050","doi-asserted-by":"crossref","first-page":"1309","DOI":"10.1016\/j.amjcard.2009.01.021","article-title":"Effect of bosentan on exercise capacity and quality of life in adults with pulmonary arterial hypertension associated with congenital heart disease with and without Down's syndrome","volume":"103","author":"Duffels","year":"2009","journal-title":"Am J Cardiol"},{"issue":"1","key":"10.1016\/j.ijcard.2011.06.084_bb0055","doi-asserted-by":"crossref","first-page":"6","DOI":"10.1007\/BF02020210","article-title":"Radiological evaluation of pulmonary vein obstruction including two examinations by magnetic resonance imaging","volume":"23","author":"Kim","year":"1993","journal-title":"Pediatr Radiol"},{"issue":"1","key":"10.1016\/j.ijcard.2011.06.084_bb0060","doi-asserted-by":"crossref","first-page":"73","DOI":"10.1007\/s00246-002-0220-6","article-title":"Congenital unilateral pulmonary venous atresia: definitive diagnosis and treatment","volume":"24","author":"Pourmoghadam","year":"2003","journal-title":"Pediatr Cardiol"},{"issue":"4","key":"10.1016\/j.ijcard.2011.06.084_bb0065","doi-asserted-by":"crossref","first-page":"776","DOI":"10.1016\/j.ahj.2007.06.003","article-title":"Long-term effect of bosentan in adults versus children with pulmonary arterial hypertension associated with systemic-to-pulmonary shunt: does the beneficial effect persist?","volume":"154","author":"van Loon","year":"2007","journal-title":"Am Heart J"},{"key":"10.1016\/j.ijcard.2011.06.084_bb0070","doi-asserted-by":"crossref","unstructured":"Vis JC, Duffels MG, Mulder P, de Bruin-Bon HACM, Bouma BJ, Berger RMF, Hoendermis ES, van Dijk APJ, Mulder BJM. 2011. Prolonged beneficial effect of bosentan treatment and 4-year survival rates in adult patients with pulmonary arterial hypertension associated with congenital heart disease. Int J Cardiol, doi:10.1016\/j.ijcard.2011.06.064.","DOI":"10.1016\/j.ijcard.2011.06.064"},{"issue":"118","key":"10.1016\/j.ijcard.2011.06.084_bb0075","doi-asserted-by":"crossref","first-page":"300","DOI":"10.1183\/09059180.00004510","article-title":"Therapeutic approaches in adults with congenital heart disease-associated pulmonary arterial hypertension","volume":"19","author":"Cordina","year":"2010","journal-title":"Eur Respir Rev"},{"issue":"6","key":"10.1016\/j.ijcard.2011.06.084_bb0080","doi-asserted-by":"crossref","first-page":"682","DOI":"10.1136\/hrt.2006.098848","article-title":"Pulmonary arterial hypertension in adults born with a heart septal defect: the Euro Heart Survey on adult congenital heart disease","volume":"93","author":"Engelfriet","year":"2007","journal-title":"Heart"},{"issue":"6","key":"10.1016\/j.ijcard.2011.06.084_bb0085","doi-asserted-by":"crossref","first-page":"2280","DOI":"10.1161\/01.CIR.84.6.2280","article-title":"Plasma endothelin concentrations in patients with pulmonary hypertension associated with congenital heart defects. Evidence for increased production of endothelin in pulmonary circulation","volume":"84","author":"Yoshibayashi","year":"1991","journal-title":"Circulation"},{"issue":"6","key":"10.1016\/j.ijcard.2011.06.084_bb0090","first-page":"632","article-title":"Pulmonary artery endothelial abnormalities in patients with congenital heart defects and pulmonary hypertension. A correlation of light with scanning electron microscopy and transmission electron microscopy.","volume":"55","author":"Rabinovitch","year":"1986","journal-title":"Lab Invest"},{"issue":"2 Suppl.","key":"10.1016\/j.ijcard.2011.06.084_bb0095","doi-asserted-by":"crossref","first-page":"S23","DOI":"10.1097\/PCC.0b013e3181c7683a","article-title":"Diagnostic strategies for acute presentation of pulmonary hypertension in children: particular focus on use of echocardiography, cardiac catheterization, magnetic resonance imaging, chest computed tomography, and lung biopsy","volume":"11","author":"Mullen","year":"2010","journal-title":"Pediatr Crit Care Med"},{"issue":"2","key":"10.1016\/j.ijcard.2011.06.084_bb0100","doi-asserted-by":"crossref","first-page":"139","DOI":"10.1007\/s11883-009-0022-x","article-title":"Pulmonary arterial hypertension","volume":"11","author":"Uzunpinar","year":"2009","journal-title":"Curr Atheroscler Rep"}],"container-title":["International Journal of Cardiology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0167527311006243?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0167527311006243?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2018,12,1]],"date-time":"2018-12-01T11:21:16Z","timestamp":1543663276000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0167527311006243"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2013,3]]},"references-count":20,"journal-issue":{"issue":"1","published-print":{"date-parts":[[2013,3]]}},"alternative-id":["S0167527311006243"],"URL":"https:\/\/doi.org\/10.1016\/j.ijcard.2011.06.084","relation":{},"ISSN":["0167-5273"],"issn-type":[{"value":"0167-5273","type":"print"}],"subject":[],"published":{"date-parts":[[2013,3]]}}}