{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,29]],"date-time":"2026-09-29T13:23:58Z","timestamp":1790688238022,"version":"4.1.0"},"reference-count":158,"publisher":"Elsevier BV","issue":"6","license":[{"start":{"date-parts":[[2016,11,1]],"date-time":"2016-11-01T00:00:00Z","timestamp":1477958400000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2016,11,1]],"date-time":"2016-11-01T00:00:00Z","timestamp":1477958400000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/legal\/tdmrep-license"}],"content-domain":{"domain":["clinicalkey.com","clinicalkey.com.au","clinicalkey.es","clinicalkey.fr","clinicalkey.jp","jaci-inpractice.org","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["The Journal of Allergy and Clinical Immunology: In Practice"],"published-print":{"date-parts":[[2016,11]]},"DOI":"10.1016\/j.jaip.2016.08.005","type":"journal-article","created":{"date-parts":[[2016,11,8]],"date-time":"2016-11-08T04:01:03Z","timestamp":1478577663000},"page":"1039-1052","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":81,"title":["Lung Disease in Primary Antibody Deficiencies"],"prefix":"10.1016","volume":"4","author":[{"given":"Edith","family":"Schussler","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mary B.","family":"Beasley","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Paul J.","family":"Maglione","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"key":"10.1016\/j.jaip.2016.08.005_bib1","doi-asserted-by":"crossref","first-page":"519","DOI":"10.1038\/nri3466","article-title":"Primary antibody deficiencies","volume":"13","author":"Durandy","year":"2013","journal-title":"Nat Rev Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib2","doi-asserted-by":"crossref","first-page":"497","DOI":"10.1007\/s10875-007-9103-1","article-title":"Population prevalence of diagnosed primary immunodeficiency diseases in the United States","volume":"27","author":"Boyle","year":"2007","journal-title":"J\u00a0Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib3","doi-asserted-by":"crossref","first-page":"16","DOI":"10.4065\/84.1.16","article-title":"Incidence and temporal trends of primary immunodeficiency: a population-based cohort study","volume":"84","author":"Joshi","year":"2009","journal-title":"Mayo Clin Proc"},{"key":"10.1016\/j.jaip.2016.08.005_bib4","doi-asserted-by":"crossref","first-page":"687","DOI":"10.1016\/j.autrev.2012.10.017","article-title":"Chipping away at a mountain: genomic studies in common variable immunodeficiency","volume":"12","author":"Keller","year":"2013","journal-title":"Autoimmun Rev"},{"key":"10.1016\/j.jaip.2016.08.005_bib5","doi-asserted-by":"crossref","first-page":"7","DOI":"10.1182\/blood-2010-01-254417","article-title":"How I treat common variable immune deficiency","volume":"116","author":"Cunningham-Rundles","year":"2010","journal-title":"Blood"},{"key":"10.1016\/j.jaip.2016.08.005_bib6","doi-asserted-by":"crossref","first-page":"595","DOI":"10.7861\/clinmedicine.9-6-595","article-title":"Primary antibody deficiencies: recognition, clinical diagnosis and referral of patients","volume":"9","author":"Wood","year":"2009","journal-title":"Clin Med (Lond)"},{"key":"10.1016\/j.jaip.2016.08.005_bib7","doi-asserted-by":"crossref","first-page":"503","DOI":"10.1016\/j.anai.2010.04.015","article-title":"Development of pulmonary abnormalities in patients with common variable immunodeficiency: associations with clinical and immunologic factors","volume":"104","author":"Gregersen","year":"2010","journal-title":"Ann Allergy Asthma Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib8","doi-asserted-by":"crossref","first-page":"120","DOI":"10.1016\/j.jaci.2010.04.016","article-title":"Recurrent and persistent respiratory tract viral infections in patients with primary hypogammaglobulinemia","volume":"126","author":"Kainulainen","year":"2010","journal-title":"J\u00a0Allergy Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib9","doi-asserted-by":"crossref","first-page":"1001","DOI":"10.1067\/mai.2002.124999","article-title":"Efficacy of intravenous immunoglobulin in the prevention of pneumonia in patients with common variable immunodeficiency","volume":"109","author":"Busse","year":"2002","journal-title":"J\u00a0Allergy Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib10","doi-asserted-by":"crossref","first-page":"21","DOI":"10.1016\/j.clim.2010.06.012","article-title":"Impact of trough IgG on pneumonia incidence in primary immunodeficiency: a meta-analysis of clinical studies","volume":"137","author":"Orange","year":"2010","journal-title":"Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib11","doi-asserted-by":"crossref","first-page":"226","DOI":"10.1038\/361226a0","article-title":"The gene involved in X-linked agammaglobulinaemia is a member of the src family of protein-tyrosine kinases","volume":"361","author":"Vetrie","year":"1993","journal-title":"Nature"},{"key":"10.1016\/j.jaip.2016.08.005_bib12","doi-asserted-by":"crossref","first-page":"690","DOI":"10.1016\/j.jaci.2005.04.043","article-title":"A\u00a0genotype-phenotype correlation study in a group of 54 patients with X-linked agammaglobulinemia","volume":"116","author":"Lopez-Granados","year":"2005","journal-title":"J\u00a0Allergy Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib13","doi-asserted-by":"crossref","first-page":"199","DOI":"10.1146\/annurev.immunol.021908.132649","article-title":"Primary B cell immunodeficiencies: comparisons and contrasts","volume":"27","author":"Conley","year":"2009","journal-title":"Annu Rev Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib14","doi-asserted-by":"crossref","first-page":"193","DOI":"10.1097\/01.md.0000229482.27398.ad","article-title":"X-linked agammaglobulinemia: report on a United States registry of 201 patients","volume":"85","author":"Winkelstein","year":"2006","journal-title":"Medicine (Baltimore)"},{"key":"10.1016\/j.jaip.2016.08.005_bib15","doi-asserted-by":"crossref","first-page":"373","DOI":"10.1097\/01.md.0000100046.06009.b0","article-title":"The X-linked hyper-IgM syndrome: clinical and immunologic features of 79 patients","volume":"82","author":"Winkelstein","year":"2003","journal-title":"Medicine (Baltimore)"},{"key":"10.1016\/j.jaip.2016.08.005_bib16","doi-asserted-by":"crossref","first-page":"12614","DOI":"10.1073\/pnas.221456898","article-title":"Mutations of CD40 gene cause an autosomal recessive form of immunodeficiency with hyper IgM","volume":"98","author":"Ferrari","year":"2001","journal-title":"Proc Natl Acad Sci U S A"},{"key":"10.1016\/j.jaip.2016.08.005_bib17","doi-asserted-by":"crossref","first-page":"167","DOI":"10.1111\/j.1365-2141.2010.08077.x","article-title":"Update on the hyper immunoglobulin M syndromes","volume":"149","author":"Davies","year":"2010","journal-title":"Br J Haematol"},{"key":"10.1016\/j.jaip.2016.08.005_bib18","doi-asserted-by":"crossref","first-page":"A404","DOI":"10.1016\/j.autrev.2011.12.001","article-title":"IgM predominance in autoimmune disease: genetics and gender","volume":"11","author":"Duarte-Rey","year":"2012","journal-title":"Autoimmun Rev"},{"key":"10.1016\/j.jaip.2016.08.005_bib19","doi-asserted-by":"crossref","first-page":"602","DOI":"10.1097\/ACI.0b013e3283594219","article-title":"IgA deficiency: what is new?","volume":"12","author":"Wang","year":"2012","journal-title":"Curr Opin Allergy Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib20","doi-asserted-by":"crossref","first-page":"189","DOI":"10.1006\/clim.1999.4798","article-title":"Diagnostic guidelines\u2013an international consensus document","volume":"93","author":"Conley","year":"1999","journal-title":"Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib21","doi-asserted-by":"crossref","first-page":"10","DOI":"10.1007\/s10875-009-9357-x","article-title":"Selective IgA deficiency","volume":"30","author":"Yel","year":"2010","journal-title":"J\u00a0Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib22","doi-asserted-by":"crossref","first-page":"581","DOI":"10.1067\/mai.2002.122466","article-title":"Primary immunodeficiency disorders: antibody deficiency","volume":"109","author":"Ballow","year":"2002","journal-title":"J\u00a0Allergy Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib23","doi-asserted-by":"crossref","first-page":"444","DOI":"10.1007\/s10875-014-0009-4","article-title":"Association between IgA deficiency & other autoimmune conditions: a population-based matched cohort study","volume":"34","author":"Ludvigsson","year":"2014","journal-title":"J\u00a0Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib24","doi-asserted-by":"crossref","first-page":"134","DOI":"10.1007\/s10875-015-0230-9","article-title":"Risk of infections among 2100 individuals with IgA deficiency: a nationwide cohort study","volume":"36","author":"Ludvigsson","year":"2016","journal-title":"J\u00a0Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib25","doi-asserted-by":"crossref","first-page":"303","DOI":"10.1023\/A:1012241117984","article-title":"Physiology of IgA and IgA deficiency","volume":"21","author":"Cunningham-Rundles","year":"2001","journal-title":"J\u00a0Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib26","doi-asserted-by":"crossref","first-page":"263","DOI":"10.1006\/clim.1999.4702","article-title":"Discordance between IgA switching at the DNA level and IgA expression at the mRNA level in IgA-deficient patients","volume":"91","author":"Wang","year":"1999","journal-title":"Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib27","doi-asserted-by":"crossref","first-page":"462","DOI":"10.1159\/000323903","article-title":"Analysis of switched memory B cells in patients with IgA deficiency","volume":"156","author":"Aghamohammadi","year":"2011","journal-title":"Int Arch Allergy Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib28","first-page":"174","article-title":"Progression of selective IgA deficiency to common variable immunodeficiency in a 16 year old boy","volume":"24","author":"Litzman","year":"1996","journal-title":"Allergol Immunopathol (Madr)"},{"key":"10.1016\/j.jaip.2016.08.005_bib29","doi-asserted-by":"crossref","first-page":"333","DOI":"10.1006\/clin.1996.0132","article-title":"Development of a common variable immunodeficiency in IgA-deficient patients","volume":"80","author":"Espanol","year":"1996","journal-title":"Clin Immunol Immunopathol"},{"key":"10.1016\/j.jaip.2016.08.005_bib30","doi-asserted-by":"crossref","first-page":"87","DOI":"10.1159\/000135694","article-title":"Progression of selective IgA deficiency to common variable immunodeficiency","volume":"147","author":"Aghamohammadi","year":"2008","journal-title":"Int Arch Allergy Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib31","doi-asserted-by":"crossref","first-page":"829","DOI":"10.1038\/ng1601","article-title":"TACI is mutant in common variable immunodeficiency and IgA deficiency","volume":"37","author":"Castigli","year":"2005","journal-title":"Nat Genet"},{"key":"10.1016\/j.jaip.2016.08.005_bib32","doi-asserted-by":"crossref","first-page":"429","DOI":"10.1038\/ng0407-429","article-title":"Reexamining the role of TACI coding variants in common variable immunodeficiency and selective IgA deficiency","volume":"39","author":"Pan-Hammarstrom","year":"2007","journal-title":"Nat Genet"},{"key":"10.1016\/j.jaip.2016.08.005_bib33","doi-asserted-by":"crossref","first-page":"1186","DOI":"10.1016\/j.jaci.2015.04.049","article-title":"Practice parameter for the diagnosis and management of primary immunodeficiency","volume":"136","author":"Bonilla","year":"2015","journal-title":"J\u00a0Allergy Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib34","doi-asserted-by":"crossref","first-page":"659","DOI":"10.1016\/j.iac.2015.07.003","article-title":"Specific antibody deficiencies","volume":"35","author":"Wall","year":"2015","journal-title":"Immunol Allergy Clin North Am"},{"key":"10.1016\/j.jaip.2016.08.005_bib35","doi-asserted-by":"crossref","first-page":"93","DOI":"10.1016\/j.clim.2003.12.005","article-title":"IgA deficiency: clinical correlates and responses to pneumococcal vaccine","volume":"111","author":"Edwards","year":"2004","journal-title":"Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib36","doi-asserted-by":"crossref","first-page":"866","DOI":"10.1126\/science.1243292","article-title":"Phosphoinositide 3-kinase delta gene mutation predisposes to respiratory infection and airway damage","volume":"342","author":"Angulo","year":"2013","journal-title":"Science"},{"key":"10.1016\/j.jaip.2016.08.005_bib37","first-page":"392","article-title":"Serum IgG subclass deficiency in ataxia-telangiectasia","volume":"68","author":"Aucouturier","year":"1987","journal-title":"Clin Exp Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib38","doi-asserted-by":"crossref","first-page":"61","DOI":"10.1385\/CRIAI:20:1:61","article-title":"The Wiskott-Aldrich syndrome","volume":"20","author":"Ochs","year":"2001","journal-title":"Clin Rev Allergy Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib39","doi-asserted-by":"crossref","first-page":"24","DOI":"10.1016\/j.clim.2012.05.003","article-title":"Classification of primary immunodeficiency disorders: one-fits-all does not help anymore","volume":"144","author":"Al-Herz","year":"2012","journal-title":"Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib40","doi-asserted-by":"crossref","first-page":"1425","DOI":"10.1016\/j.jaci.2012.03.025","article-title":"Common variable immunodeficiency","volume":"129","author":"Cunningham-Rundles","year":"2012","journal-title":"J\u00a0Allergy Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib41","doi-asserted-by":"crossref","first-page":"301","DOI":"10.1182\/asheducation.V2012.1.301.3798316","article-title":"The many faces of common variable immunodeficiency","volume":"2012","author":"Cunningham-Rundles","year":"2012","journal-title":"Hematology Am Soc Hematol Educ Program"},{"key":"10.1016\/j.jaip.2016.08.005_bib42","doi-asserted-by":"crossref","first-page":"3932","DOI":"10.4049\/jimmunol.178.6.3932","article-title":"Unravelling the complexity of T cell abnormalities in common variable immunodeficiency","volume":"178","author":"Giovannetti","year":"2007","journal-title":"J\u00a0Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib43","doi-asserted-by":"crossref","first-page":"77","DOI":"10.1182\/blood-2007-06-091744","article-title":"The EUROclass trial: defining subgroups in common variable immunodeficiency","volume":"111","author":"Wehr","year":"2008","journal-title":"Blood"},{"key":"10.1016\/j.jaip.2016.08.005_bib44","doi-asserted-by":"crossref","first-page":"277","DOI":"10.1182\/blood-2007-11-124545","article-title":"Common variable immunodeficiency disorders: division into distinct clinical phenotypes","volume":"112","author":"Chapel","year":"2008","journal-title":"Blood"},{"key":"10.1016\/j.jaip.2016.08.005_bib45","doi-asserted-by":"crossref","first-page":"1650","DOI":"10.1182\/blood-2011-09-377945","article-title":"Morbidity and mortality in common variable immune deficiency over 4 decades","volume":"119","author":"Resnick","year":"2012","journal-title":"Blood"},{"key":"10.1016\/j.jaip.2016.08.005_bib46","doi-asserted-by":"crossref","first-page":"19","DOI":"10.1007\/s11882-016-0597-6","article-title":"Autoimmune and lymphoproliferative complications of common variable immunodeficiency","volume":"16","author":"Maglione","year":"2016","journal-title":"Curr Allergy Asthma Rep"},{"key":"10.1016\/j.jaip.2016.08.005_bib47","doi-asserted-by":"crossref","first-page":"1623","DOI":"10.1126\/science.1255904","article-title":"Immune dysregulation in human subjects with heterozygous germline mutations in CTLA4","volume":"345","author":"Kuehn","year":"2014","journal-title":"Science"},{"key":"10.1016\/j.jaip.2016.08.005_bib48","doi-asserted-by":"crossref","first-page":"1410","DOI":"10.1038\/nm.3746","article-title":"Autosomal dominant immune dysregulation syndrome in humans with CTLA4 mutations","volume":"20","author":"Schubert","year":"2014","journal-title":"Nat Med"},{"key":"10.1016\/j.jaip.2016.08.005_bib49","doi-asserted-by":"crossref","first-page":"303","DOI":"10.1084\/jem.192.2.303","article-title":"Immunologic self-tolerance maintained by CD25(+)CD4(+) regulatory T cells constitutively expressing cytotoxic T lymphocyte-associated antigen 4","volume":"192","author":"Takahashi","year":"2000","journal-title":"J\u00a0Exp Med"},{"key":"10.1016\/j.jaip.2016.08.005_bib50","doi-asserted-by":"crossref","first-page":"852","DOI":"10.1038\/nri3108","article-title":"The emerging role of CTLA4 as a cell-extrinsic regulator of T cell responses","volume":"11","author":"Walker","year":"2011","journal-title":"Nat Rev Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib51","doi-asserted-by":"crossref","first-page":"986","DOI":"10.1016\/j.ajhg.2012.04.015","article-title":"Deleterious mutations in LRBA are associated with a syndrome of immune deficiency and autoimmunity","volume":"90","author":"Lopez-Herrera","year":"2012","journal-title":"Am J Hum Genet"},{"key":"10.1016\/j.jaip.2016.08.005_bib52","doi-asserted-by":"crossref","first-page":"202","DOI":"10.1007\/s13238-011-1018-1","article-title":"Structure and function of WD40 domain proteins","volume":"2","author":"Xu","year":"2011","journal-title":"Protein Cell"},{"key":"10.1016\/j.jaip.2016.08.005_bib53","doi-asserted-by":"crossref","first-page":"436","DOI":"10.1126\/science.aaa1663","article-title":"AUTOIMMUNE DISEASE. Patients with LRBA deficiency show CTLA4 loss and immune dysregulation responsive to abatacept therapy","volume":"349","author":"Lo","year":"2015","journal-title":"Science"},{"key":"10.1016\/j.jaip.2016.08.005_bib54","doi-asserted-by":"crossref","first-page":"33","DOI":"10.1007\/s10875-015-0224-7","article-title":"Spectrum of phenotypes associated with mutations in LRBA","volume":"36","author":"Alkhairy","year":"2016","journal-title":"J\u00a0Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib55","doi-asserted-by":"crossref","first-page":"223","DOI":"10.1016\/j.jaci.2015.09.025","article-title":"The extended phenotype of LPS-responsive beige-like anchor protein (LRBA) deficiency","volume":"137","author":"Gamez-Diaz","year":"2016","journal-title":"J\u00a0Allergy Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib56","doi-asserted-by":"crossref","first-page":"88","DOI":"10.1038\/ni.2771","article-title":"Dominant-activating germline mutations in the gene encoding the PI(3)K catalytic subunit p110delta result in T cell senescence and human immunodeficiency","volume":"15","author":"Lucas","year":"2014","journal-title":"Nat Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib57","doi-asserted-by":"crossref","first-page":"272","DOI":"10.1007\/s10875-014-0012-9","article-title":"Mutations in PIK3CD can cause hyper IgM syndrome (HIGM) associated with increased cancer susceptibility","volume":"34","author":"Crank","year":"2014","journal-title":"J\u00a0Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib58","doi-asserted-by":"crossref","first-page":"591","DOI":"10.1182\/blood-2014-09-602763","article-title":"Early-onset lymphoproliferation and autoimmunity caused by germline STAT3 gain-of-function mutations","volume":"125","author":"Milner","year":"2015","journal-title":"Blood"},{"key":"10.1016\/j.jaip.2016.08.005_bib59","doi-asserted-by":"crossref","first-page":"812","DOI":"10.1038\/ng.3040","article-title":"Activating germline mutations in STAT3 cause early-onset multi-organ autoimmune disease","volume":"46","author":"Flanagan","year":"2014","journal-title":"Nat Genet"},{"key":"10.1016\/j.jaip.2016.08.005_bib60","doi-asserted-by":"crossref","first-page":"639","DOI":"10.1182\/blood-2014-04-570101","article-title":"Autoimmunity, hypogammaglobulinemia, lymphoproliferation, and mycobacterial disease in patients with activating mutations in STAT3","volume":"125","author":"Haapaniemi","year":"2015","journal-title":"Blood"},{"key":"10.1016\/j.jaip.2016.08.005_bib61","doi-asserted-by":"crossref","first-page":"615","DOI":"10.1007\/s10875-015-0187-8","article-title":"The ying and yang of STAT3 in human disease","volume":"35","author":"Vogel","year":"2015","journal-title":"J\u00a0Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib62","doi-asserted-by":"crossref","first-page":"773","DOI":"10.1038\/nature06764","article-title":"Impaired T(H)17 cell differentiation in subjects with autosomal dominant hyper-IgE syndrome","volume":"452","author":"Milner","year":"2008","journal-title":"Nature"},{"key":"10.1016\/j.jaip.2016.08.005_bib63","doi-asserted-by":"crossref","first-page":"264","DOI":"10.1159\/000101784","article-title":"Genetic causes of bronchiectasis: primary immune deficiencies and the lung","volume":"74","author":"Notarangelo","year":"2007","journal-title":"Respiration"},{"key":"10.1016\/j.jaip.2016.08.005_bib64","doi-asserted-by":"crossref","first-page":"289","DOI":"10.1111\/j.1440-1843.2009.01679.x","article-title":"Comparison of pulmonary diseases in common variable immunodeficiency and X-linked agammaglobulinaemia","volume":"15","author":"Aghamohammadi","year":"2010","journal-title":"Respirology"},{"key":"10.1016\/j.jaip.2016.08.005_bib65","doi-asserted-by":"crossref","first-page":"96","DOI":"10.1016\/0091-6749(91)90306-9","article-title":"Retrospective analysis of the incidence of pulmonary disease in hypogammaglobulinemia","volume":"88","author":"Sweinberg","year":"1991","journal-title":"J\u00a0Allergy Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib66","doi-asserted-by":"crossref","first-page":"28","DOI":"10.3349\/ymj.2008.49.1.28","article-title":"Analysis of clinical presentations of Bruton disease: a review of 20 years of accumulated data from pediatric patients at Severance Hospital","volume":"49","author":"Chun","year":"2008","journal-title":"Yonsei Med J"},{"key":"10.1016\/j.jaip.2016.08.005_bib67","doi-asserted-by":"crossref","first-page":"S225","DOI":"10.1016\/S1526-0542(04)90043-7","article-title":"Pulmonary complications of primary immunodeficiencies","volume":"5","author":"Buckley","year":"2004","journal-title":"Paediatr Respir Rev"},{"key":"10.1016\/j.jaip.2016.08.005_bib68","doi-asserted-by":"crossref","first-page":"165","DOI":"10.7326\/0003-4819-135-3-200108070-00008","article-title":"The effect of two different dosages of intravenous immunoglobulin on the incidence of recurrent infections in patients with primary hypogammaglobulinemia: a randomized, double-blind, multicenter crossover trial","volume":"135","author":"Eijkhout","year":"2001","journal-title":"Ann Intern Med"},{"key":"10.1016\/j.jaip.2016.08.005_bib69","doi-asserted-by":"crossref","first-page":"69","DOI":"10.1016\/0090-1229(86)90070-X","article-title":"Infectious complications of the primary immunodeficiencies","volume":"40","author":"Stiehm","year":"1986","journal-title":"Clin Immunol Immunopathol"},{"key":"10.1016\/j.jaip.2016.08.005_bib70","doi-asserted-by":"crossref","first-page":"826","DOI":"10.1056\/NEJM196610132751508","article-title":"The gamma globulins, IV: therapeutic uses of gamma globulin","volume":"275","author":"Janeway","year":"1966","journal-title":"N\u00a0Engl J Med"},{"key":"10.1016\/j.jaip.2016.08.005_bib71","doi-asserted-by":"crossref","first-page":"145","DOI":"10.1097\/00005792-198505000-00001","article-title":"X-linked agammaglobulinemia: an analysis of 96 patients","volume":"64","author":"Lederman","year":"1985","journal-title":"Medicine (Baltimore)"},{"key":"10.1016\/j.jaip.2016.08.005_bib72","first-page":"31","article-title":"Primary hypogammaglobulinaemia: a survey of clinical manifestations and complications","volume":"86","author":"Hermaszewski","year":"1993","journal-title":"Q\u00a0J Med"},{"key":"10.1016\/j.jaip.2016.08.005_bib73","doi-asserted-by":"crossref","first-page":"412","DOI":"10.1016\/j.jaci.2004.10.048","article-title":"The loss of IgM memory B cells correlates with clinical disease in common variable immunodeficiency","volume":"115","author":"Carsetti","year":"2005","journal-title":"J\u00a0Allergy Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib74","doi-asserted-by":"crossref","first-page":"770","DOI":"10.1016\/j.jaci.2011.09.047","article-title":"Protective effect of IgM against colonization of the respiratory tract by nontypeable Haemophilus influenzae in patients with hypogammaglobulinemia","volume":"129","author":"Micol","year":"2012","journal-title":"J\u00a0Allergy Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib75","doi-asserted-by":"crossref","first-page":"793","DOI":"10.1111\/j.1399-3038.2009.00963.x","article-title":"Detection of pulmonary complications in common variable immunodeficiency","volume":"21","author":"Touw","year":"2010","journal-title":"Pediatr Allergy Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib76","doi-asserted-by":"crossref","first-page":"490","DOI":"10.1378\/chest.106.2.490","article-title":"Radiologic findings of adult primary immunodeficiency disorders: contribution of CT","volume":"106","author":"Obregon","year":"1994","journal-title":"Chest"},{"key":"10.1016\/j.jaip.2016.08.005_bib77","doi-asserted-by":"crossref","first-page":"415","DOI":"10.1016\/j.jaci.2004.05.057","article-title":"Granulomatous-lymphocytic lung disease shortens survival in common variable immunodeficiency","volume":"114","author":"Bates","year":"2004","journal-title":"J\u00a0Allergy Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib78","doi-asserted-by":"crossref","first-page":"369","DOI":"10.1097\/01.bor.0000231905.12172.b5","article-title":"Hyper-IgM syndromes","volume":"18","author":"Durandy","year":"2006","journal-title":"Curr Opin Rheumatol"},{"key":"10.1016\/j.jaip.2016.08.005_bib79","doi-asserted-by":"crossref","first-page":"1383","DOI":"10.1056\/NEJMra012519","article-title":"Bronchiectasis","volume":"346","author":"Barker","year":"2002","journal-title":"N\u00a0Engl J Med"},{"key":"10.1016\/j.jaip.2016.08.005_bib80","first-page":"6","article-title":"Inflammation: a two-edged sword\u2013the model of bronchiectasis","volume":"147","author":"Cole","year":"1986","journal-title":"Eur J Respir Dis Suppl"},{"key":"10.1016\/j.jaip.2016.08.005_bib81","doi-asserted-by":"crossref","first-page":"27","DOI":"10.1081\/COPD-200050685","article-title":"Outcome in adult bronchiectasis","volume":"2","author":"King","year":"2005","journal-title":"COPD"},{"key":"10.1016\/j.jaip.2016.08.005_bib82","doi-asserted-by":"crossref","first-page":"414","DOI":"10.1136\/thx.2005.047332","article-title":"Longitudinal pulmonary function of childhood bronchiectasis and comparison with cystic fibrosis","volume":"61","author":"Twiss","year":"2006","journal-title":"Thorax"},{"key":"10.1016\/j.jaip.2016.08.005_bib83","doi-asserted-by":"crossref","first-page":"1565","DOI":"10.1378\/chest.07-0490","article-title":"Factors associated with lung function decline in adult patients with stable non-cystic fibrosis bronchiectasis","volume":"132","author":"Martinez-Garcia","year":"2007","journal-title":"Chest"},{"key":"10.1016\/j.jaip.2016.08.005_bib84","doi-asserted-by":"crossref","first-page":"1547","DOI":"10.1086\/587669","article-title":"Infections in 252 patients with common variable immunodeficiency","volume":"46","author":"Oksenhendler","year":"2008","journal-title":"Clin Infect Dis"},{"key":"10.1016\/j.jaip.2016.08.005_bib85","doi-asserted-by":"crossref","first-page":"201","DOI":"10.1016\/j.clim.2005.11.002","article-title":"The health status and quality of life of adults with X-linked agammaglobulinemia","volume":"118","author":"Howard","year":"2006","journal-title":"Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib86","doi-asserted-by":"crossref","first-page":"1031","DOI":"10.1016\/S0091-6749(99)70085-0","article-title":"Pulmonary abnormalities in patients with primary hypogammaglobulinemia","volume":"104","author":"Kainulainen","year":"1999","journal-title":"J\u00a0Allergy Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib87","doi-asserted-by":"crossref","first-page":"68","DOI":"10.1007\/s10875-013-9942-x","article-title":"Activity, severity and impact of respiratory disease in primary antibody deficiency syndromes","volume":"34","author":"Hurst","year":"2014","journal-title":"J\u00a0Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib88","doi-asserted-by":"crossref","first-page":"283","DOI":"10.1016\/j.ccm.2012.02.002","article-title":"Bronchiectasis and nontuberculous mycobacterial disease","volume":"33","author":"Griffith","year":"2012","journal-title":"Clin Chest Med"},{"key":"10.1016\/j.jaip.2016.08.005_bib89","doi-asserted-by":"crossref","first-page":"452","DOI":"10.1016\/j.anai.2014.04.024","article-title":"Pulmonary radiologic findings in common variable immunodeficiency: clinical and immunological correlations","volume":"113","author":"Maglione","year":"2014","journal-title":"Ann Allergy Asthma Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib90","doi-asserted-by":"crossref","first-page":"315","DOI":"10.1007\/s10875-011-9511-0","article-title":"Effectiveness of immunoglobulin replacement therapy on clinical outcome in patients with primary antibody deficiencies: results from a multicenter prospective cohort study","volume":"31","author":"Quinti","year":"2011","journal-title":"J\u00a0Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib91","doi-asserted-by":"crossref","first-page":"116","DOI":"10.1016\/j.jaci.2013.12.1077","article-title":"Clinical picture and treatment of 2212 patients with common variable immunodeficiency","volume":"134","author":"Gathmann","year":"2014","journal-title":"J\u00a0Allergy Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib92","doi-asserted-by":"crossref","first-page":"587","DOI":"10.1016\/j.crad.2011.10.028","article-title":"Respiratory disease in common variable immunodeficiency and other primary immunodeficiency disorders","volume":"67","author":"Hampson","year":"2012","journal-title":"Clin Radiol"},{"key":"10.1016\/j.jaip.2016.08.005_bib93","doi-asserted-by":"crossref","first-page":"130","DOI":"10.1007\/s10875-008-9229-9","article-title":"IgA deficiency: correlation between clinical and immunological phenotypes","volume":"29","author":"Aghamohammadi","year":"2009","journal-title":"J\u00a0Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib94","doi-asserted-by":"crossref","first-page":"720","DOI":"10.1056\/NEJM198509193131203","article-title":"Impaired lung function in patients with IgA deficiency and low levels of IgG2 or IgG3","volume":"313","author":"Bjorkander","year":"1985","journal-title":"N\u00a0Engl J Med"},{"key":"10.1016\/j.jaip.2016.08.005_bib95","first-page":"703","article-title":"Serum IgG subclasses in chronic and recurrent respiratory infections","volume":"58","author":"Stanley","year":"1984","journal-title":"Clin Exp Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib96","doi-asserted-by":"crossref","first-page":"650","DOI":"10.1164\/ajrccm.153.2.8564113","article-title":"IgG subclass deficiencies associated with bronchiectasis","volume":"153","author":"De Gracia","year":"1996","journal-title":"Am J Respir Crit Care Med"},{"key":"10.1016\/j.jaip.2016.08.005_bib97","doi-asserted-by":"crossref","first-page":"482","DOI":"10.1183\/09031936.05.00073204","article-title":"Impaired pneumococcal antibody response in bronchiectasis of unknown aetiology","volume":"25","author":"van Kessel","year":"2005","journal-title":"Eur Respir J"},{"key":"10.1016\/j.jaip.2016.08.005_bib98","doi-asserted-by":"crossref","first-page":"1446","DOI":"10.1183\/09031936.00119114","article-title":"Management of bronchiectasis in adults","volume":"45","author":"Chalmers","year":"2015","journal-title":"Eur Respir J"},{"key":"10.1016\/j.jaip.2016.08.005_bib99","doi-asserted-by":"crossref","first-page":"S1","DOI":"10.1016\/S1081-1206(10)61142-8","article-title":"Practice parameter for the diagnosis and management of primary immunodeficiency","volume":"94","author":"Bonilla","year":"2005","journal-title":"Ann Allergy Asthma Immunol"},{"issue":"7","key":"10.1016\/j.jaip.2016.08.005_bib100","first-page":"CD010337","article-title":"Interventions for bronchiectasis: an overview of Cochrane systematic reviews","author":"Welsh","year":"2015","journal-title":"Cochrane Database Syst Rev"},{"key":"10.1016\/j.jaip.2016.08.005_bib101","doi-asserted-by":"crossref","first-page":"1251","DOI":"10.1001\/jama.2013.1937","article-title":"Effect of azithromycin maintenance treatment on infectious exacerbations among patients with non-cystic fibrosis bronchiectasis: the BAT randomized controlled trial","volume":"309","author":"Altenburg","year":"2013","journal-title":"JAMA"},{"key":"10.1016\/j.jaip.2016.08.005_bib102","doi-asserted-by":"crossref","first-page":"660","DOI":"10.1016\/S0140-6736(12)60953-2","article-title":"Azithromycin for prevention of exacerbations in non-cystic fibrosis bronchiectasis (EMBRACE): a randomised, double-blind, placebo-controlled trial","volume":"380","author":"Wong","year":"2012","journal-title":"Lancet"},{"key":"10.1016\/j.jaip.2016.08.005_bib103","doi-asserted-by":"crossref","first-page":"160","DOI":"10.1186\/s12879-015-0872-5","article-title":"Effects of long-term use of macrolides in patients with non-cystic fibrosis bronchiectasis: a meta-analysis of randomized controlled trials","volume":"15","author":"Fan","year":"2015","journal-title":"BMC Infect Dis"},{"key":"10.1016\/j.jaip.2016.08.005_bib104","doi-asserted-by":"crossref","first-page":"503","DOI":"10.1097\/MCP.0b013e3283642c47","article-title":"Common variable immunodeficiency-associated granulomatous and interstitial lung disease","volume":"19","author":"Prasse","year":"2013","journal-title":"Curr Opin Pulm Med"},{"key":"10.1016\/j.jaip.2016.08.005_bib105","doi-asserted-by":"crossref","first-page":"941","DOI":"10.1016\/j.jaip.2015.07.004","article-title":"Progression of common variable immunodeficiency interstitial lung disease accompanies distinct pulmonary and laboratory findings","volume":"3","author":"Maglione","year":"2015","journal-title":"J\u00a0Allergy Clin Immunol Pract"},{"key":"10.1016\/j.jaip.2016.08.005_bib106","doi-asserted-by":"crossref","first-page":"109","DOI":"10.1159\/000050475","article-title":"Pulmonary mucosa-associated lymphoid tissue lymphoma in a patient with common variable immunodeficiency syndrome","volume":"68","author":"Reichenberger","year":"2001","journal-title":"Respiration"},{"key":"10.1016\/j.jaip.2016.08.005_bib107","doi-asserted-by":"crossref","first-page":"535","DOI":"10.1016\/j.jaci.2013.08.022","article-title":"Tertiary lymphoid neogenesis is a component of pulmonary lymphoid hyperplasia in patients with common variable immunodeficiency","volume":"133","author":"Maglione","year":"2014","journal-title":"J\u00a0Allergy Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib108","first-page":"121","article-title":"Lymphoid hyperplasia of the lung and Evans' syndrome in IgA deficiency","volume":"106","author":"Roca","year":"1999","journal-title":"Am J Med"},{"key":"10.1016\/j.jaip.2016.08.005_bib109","first-page":"69","article-title":"IgA and\/or IgG subclass deficiency in children with recurrent respiratory infections and its relationship with chronic pulmonary damage","volume":"15","author":"Ozkan","year":"2005","journal-title":"J\u00a0Investig Allergol Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib110","doi-asserted-by":"crossref","first-page":"22","DOI":"10.1016\/j.clim.2003.10.007","article-title":"Clinical, immunologic and genetic analysis of 29 patients with autosomal recessive hyper-IgM syndrome due to activation-induced cytidine deaminase deficiency","volume":"110","author":"Quartier","year":"2004","journal-title":"Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib111","doi-asserted-by":"crossref","first-page":"146","DOI":"10.1007\/s10875-013-9980-4","article-title":"First report of the Hyper-IgM syndrome Registry of the Latin American Society for Immunodeficiencies: novel mutations, unique infections, and outcomes","volume":"34","author":"Cabral-Marques","year":"2014","journal-title":"J\u00a0Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib112","doi-asserted-by":"crossref","first-page":"128","DOI":"10.1016\/j.aller.2010.12.003","article-title":"Pulmonary complications in patients with antibody deficiency","volume":"39","author":"Costa-Carvalho","year":"2011","journal-title":"Allergol Immunopathol (Madr)"},{"key":"10.1016\/j.jaip.2016.08.005_bib113","doi-asserted-by":"crossref","first-page":"2140","DOI":"10.1016\/j.molimm.2009.03.012","article-title":"Genetic and demographic features of X-linked agammaglobulinemia in Eastern and Central Europe: a cohort study","volume":"46","author":"Toth","year":"2009","journal-title":"Mol Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib114","doi-asserted-by":"crossref","first-page":"121","DOI":"10.1007\/s10875-009-9341-5","article-title":"Clinical characteristics and genotype-phenotype correlation in 62 patients with X-linked agammaglobulinemia","volume":"30","author":"Lee","year":"2010","journal-title":"J\u00a0Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib115","doi-asserted-by":"crossref","first-page":"187","DOI":"10.1007\/s10875-016-0251-z","article-title":"X-linked agammagobulinemia in a large series of North African patients: frequency, clinical features and novel BTK mutations","volume":"36","author":"Aadam","year":"2016","journal-title":"J\u00a0Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib116","doi-asserted-by":"crossref","first-page":"38","DOI":"10.1016\/j.clim.2016.02.010","article-title":"Clinical and mutational features of X-linked agammaglobulinemia in Mexico","volume":"165","author":"Garcia-Garcia","year":"2016","journal-title":"Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib117","doi-asserted-by":"crossref","first-page":"525","DOI":"10.1053\/j.sult.2013.05.002","article-title":"Lymphoproliferative lung disorders: a radiologic-pathologic overview, part I: reactive disorders","volume":"34","author":"Carrillo","year":"2013","journal-title":"Semin Ultrasound CT MR"},{"key":"10.1016\/j.jaip.2016.08.005_bib118","doi-asserted-by":"crossref","first-page":"198","DOI":"10.1016\/j.clim.2009.05.001","article-title":"Granulomatous disease in common variable immunodeficiency","volume":"133","author":"Ardeniz","year":"2009","journal-title":"Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib119","doi-asserted-by":"crossref","first-page":"2244","DOI":"10.1007\/s00330-011-2191-6","article-title":"Organizing pneumonia: a kaleidoscope of concepts and morphologies","volume":"21","author":"Roberton","year":"2011","journal-title":"Eur Radiol"},{"key":"10.1016\/j.jaip.2016.08.005_bib120","doi-asserted-by":"crossref","first-page":"1306","DOI":"10.1016\/j.humpath.2015.05.011","article-title":"Granulomatous and lymphocytic interstitial lung disease: a spectrum of pulmonary histopathologic lesions in common variable immunodeficiency\u2013histologic and immunohistochemical analyses of 16 cases","volume":"46","author":"Rao","year":"2015","journal-title":"Hum Pathol"},{"key":"10.1016\/j.jaip.2016.08.005_bib121","doi-asserted-by":"crossref","first-page":"450","DOI":"10.1055\/s-0032-1325156","article-title":"Lymphocytic interstitial pneumonia and other benign lymphoid disorders","volume":"33","author":"Tian","year":"2012","journal-title":"Semin Respir Crit Care Med"},{"key":"10.1016\/j.jaip.2016.08.005_bib122","doi-asserted-by":"crossref","first-page":"691","DOI":"10.5858\/134.5.691","article-title":"Update on nonneoplastic pulmonary lymphoproliferative disorders and related entities","volume":"134","author":"Guinee","year":"2010","journal-title":"Arch Pathol Lab Med"},{"key":"10.1016\/j.jaip.2016.08.005_bib123","doi-asserted-by":"crossref","first-page":"59","DOI":"10.1016\/j.coi.2015.12.008","article-title":"Regulation of germinal center responses, memory B cells and plasma cell formation\u2014an update","volume":"39","author":"Corcoran","year":"2016","journal-title":"Curr Opin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib124","doi-asserted-by":"crossref","first-page":"141","DOI":"10.1111\/imm.12554","article-title":"Ectopic lymphoid follicles: inducible centres for generating antigen-specific immune responses within tissues","volume":"147","author":"Jones","year":"2016","journal-title":"Immunology"},{"key":"10.1016\/j.jaip.2016.08.005_bib125","doi-asserted-by":"crossref","first-page":"84","DOI":"10.1007\/s10875-012-9778-9","article-title":"Granulomatous disease in CVID: retrospective analysis of clinical characteristics and treatment efficacy in a cohort of 59 patients","volume":"33","author":"Boursiquot","year":"2013","journal-title":"J\u00a0Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib126","doi-asserted-by":"crossref","first-page":"30","DOI":"10.1007\/s10875-012-9755-3","article-title":"Use of combination chemotherapy for treatment of granulomatous and lymphocytic interstitial lung disease (GLILD) in patients with common variable immunodeficiency (CVID)","volume":"33","author":"Chase","year":"2013","journal-title":"J\u00a0Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib127","doi-asserted-by":"crossref","first-page":"162","DOI":"10.1097\/RTI.0b013e318166d32f","article-title":"Granulomatous-lymphocytic interstitial lung disease associated with common variable immunodeficiency: CT findings","volume":"23","author":"Torigian","year":"2008","journal-title":"J\u00a0Thorac Imaging"},{"key":"10.1016\/j.jaip.2016.08.005_bib128","doi-asserted-by":"crossref","first-page":"395","DOI":"10.1097\/RCT.0b013e3181cad9da","article-title":"Common variable immunodeficiency: computed tomography evaluation of bronchopulmonary changes including nodular lesions in 40 patients: correlation with clinical and immunological data","volume":"34","author":"Bondioni","year":"2010","journal-title":"J\u00a0Comput Assist Tomogr"},{"key":"10.1016\/j.jaip.2016.08.005_bib129","doi-asserted-by":"crossref","first-page":"514","DOI":"10.1097\/ACI.0000000000000218","article-title":"The autoimmune conundrum in common variable immunodeficiency disorders","volume":"15","author":"van de Ven","year":"2015","journal-title":"Curr Opin Allergy Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib130","doi-asserted-by":"crossref","first-page":"57","DOI":"10.1007\/s10875-016-0294-1","article-title":"Autoimmunity and primary immunodeficiency disorders","volume":"36","author":"Allenspach","year":"2016","journal-title":"J\u00a0Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib131","doi-asserted-by":"crossref","first-page":"784","DOI":"10.1007\/s10875-011-9565-z","article-title":"Lymphoid proliferations of indeterminate malignant potential arising in adults with common variable immunodeficiency disorders: unusual case studies and immunohistological review in the light of possible causative events","volume":"31","author":"da Silva","year":"2011","journal-title":"J\u00a0Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib132","doi-asserted-by":"crossref","first-page":"201","DOI":"10.1016\/j.reuma.2015.09.003","article-title":"Sjogren's syndrome-associated interstitial lung disease: a multicenter study","volume":"12","author":"Reina","year":"2015","journal-title":"Reumatol Clin"},{"key":"10.1016\/j.jaip.2016.08.005_bib133","doi-asserted-by":"crossref","first-page":"377","DOI":"10.1159\/000214841","article-title":"Pulmonary manifestations of Sjogren's syndrome","volume":"78","author":"Shi","year":"2009","journal-title":"Respiration"},{"key":"10.1016\/j.jaip.2016.08.005_bib134","doi-asserted-by":"crossref","first-page":"479","DOI":"10.1084\/jem.20050381","article-title":"Possible role of human herpesvirus 8 in the lymphoproliferative disorders in common variable immunodeficiency","volume":"202","author":"Wheat","year":"2005","journal-title":"J\u00a0Exp Med"},{"key":"10.1016\/j.jaip.2016.08.005_bib135","doi-asserted-by":"crossref","first-page":"2924","DOI":"10.1182\/blood-2013-12-545087","article-title":"HHV-8-negative, idiopathic multicentric Castleman disease: novel insights into biology, pathogenesis, and therapy","volume":"123","author":"Fajgenbaum","year":"2014","journal-title":"Blood"},{"key":"10.1016\/j.jaip.2016.08.005_bib136","doi-asserted-by":"crossref","first-page":"1390","DOI":"10.1016\/S0140-6736(85)92557-7","article-title":"Opportunistic lymphoproliferations associated with Epstein-Barr viral DNA in infants and children with AIDS","volume":"2","author":"Andiman","year":"1985","journal-title":"Lancet"},{"key":"10.1016\/j.jaip.2016.08.005_bib137","doi-asserted-by":"crossref","first-page":"940","DOI":"10.1164\/ajrccm\/145.4_Pt_1.940","article-title":"Detection of Epstein-Barr virus in lymphocytic interstitial pneumonia by in situ hybridization","volume":"145","author":"Barbera","year":"1992","journal-title":"Am Rev Respir Dis"},{"key":"10.1016\/j.jaip.2016.08.005_bib138","doi-asserted-by":"crossref","first-page":"109","DOI":"10.1111\/1469-0691.12534","article-title":"Epstein-Barr virus-related post-transplant lymphoproliferative disorder in solid organ transplant recipients","volume":"20","author":"San-Juan","year":"2014","journal-title":"Clin Microbiol Infect"},{"key":"10.1016\/j.jaip.2016.08.005_bib139","doi-asserted-by":"crossref","first-page":"615","DOI":"10.1007\/s10875-014-0052-1","article-title":"Ill-defined germinal centers and severely reduced plasma cells are histological hallmarks of lymphadenopathy in patients with common variable immunodeficiency","volume":"34","author":"Unger","year":"2014","journal-title":"J\u00a0Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib140","doi-asserted-by":"crossref","first-page":"468","DOI":"10.1016\/j.mib.2013.05.001","article-title":"Viral pathogen discovery","volume":"16","author":"Chiu","year":"2013","journal-title":"Curr Opin Microbiol"},{"key":"10.1016\/j.jaip.2016.08.005_bib141","doi-asserted-by":"crossref","first-page":"330","DOI":"10.1055\/s-0034-1376862","article-title":"Sarcoidosis and common variable immunodeficiency: similarities and differences","volume":"35","author":"Verbsky","year":"2014","journal-title":"Semin Respir Crit Care Med"},{"key":"10.1016\/j.jaip.2016.08.005_bib142","doi-asserted-by":"crossref","first-page":"467","DOI":"10.1111\/j.1600-0560.2007.00854.x","article-title":"Immunohistochemical features of cutaneous granulomas in primary immunodeficiency disorders: a comparison with cutaneous sarcoidosis","volume":"35","author":"de Jager","year":"2008","journal-title":"J\u00a0Cutan Pathol"},{"key":"10.1016\/j.jaip.2016.08.005_bib143","doi-asserted-by":"crossref","first-page":"e0130148","DOI":"10.1371\/journal.pone.0130148","article-title":"Patterns of lymph node pathology; fine needle aspiration biopsy as an evaluation tool for lymphadenopathy: a retrospective descriptive study conducted at the largest hospital in Africa","volume":"10","author":"Reddy","year":"2015","journal-title":"PLoS One"},{"key":"10.1016\/j.jaip.2016.08.005_bib144","doi-asserted-by":"crossref","first-page":"1023","DOI":"10.1002\/dc.21741","article-title":"Diagnosis and subclassification of lymphomas and non-neoplastic lesions involving mediastinal lymph nodes using endobronchial ultrasound-guided transbronchial needle aspiration","volume":"41","author":"Ko","year":"2013","journal-title":"Diagn Cytopathol"},{"key":"10.1016\/j.jaip.2016.08.005_bib145","doi-asserted-by":"crossref","first-page":"447","DOI":"10.1016\/j.imbio.2007.10.018","article-title":"Chromosomal radiosensitivity in patients with common variable immunodeficiency","volume":"213","author":"Aghamohammadi","year":"2008","journal-title":"Immunobiology"},{"key":"10.1016\/j.jaip.2016.08.005_bib146","doi-asserted-by":"crossref","first-page":"180","DOI":"10.1006\/clin.1997.4478","article-title":"In\u00a0vitro chromosomal radiosensitivity in common variable immune deficiency","volume":"86","author":"Palanduz","year":"1998","journal-title":"Clin Immunol Immunopathol"},{"key":"10.1016\/j.jaip.2016.08.005_bib147","doi-asserted-by":"crossref","first-page":"255","DOI":"10.1016\/0027-5107(93)90166-D","article-title":"Chromosomal radiosensitivity in common variable immune deficiency","volume":"290","author":"Vorechovsky","year":"1993","journal-title":"Mutat Res"},{"key":"10.1016\/j.jaip.2016.08.005_bib148","doi-asserted-by":"crossref","first-page":"1096","DOI":"10.1136\/thx.2004.029819","article-title":"Lymphocytic interstitial pneumonia associated with common variable immunodeficiency resolved with intravenous immunoglobulins","volume":"61","author":"Arish","year":"2006","journal-title":"Thorax"},{"key":"10.1016\/j.jaip.2016.08.005_bib149","doi-asserted-by":"crossref","first-page":"1531","DOI":"10.1164\/ajrccm.154.5.8912776","article-title":"Bronchiolar disease in rheumatoid arthritis","volume":"154","author":"Hayakawa","year":"1996","journal-title":"Am J Respir Crit Care Med"},{"key":"10.1016\/j.jaip.2016.08.005_bib150","doi-asserted-by":"crossref","first-page":"1277","DOI":"10.1164\/rccm.200301-053SO","article-title":"Bronchiolar disorders","volume":"168","author":"Ryu","year":"2003","journal-title":"Am J Respir Crit Care Med"},{"key":"10.1016\/j.jaip.2016.08.005_bib151","doi-asserted-by":"crossref","first-page":"307","DOI":"10.1016\/j.rmed.2007.07.032","article-title":"Follicular bronchiolitis in surgical lung biopsies: clinical implications in 12 patients","volume":"102","author":"Aerni","year":"2008","journal-title":"Respir Med"},{"key":"10.1016\/j.jaip.2016.08.005_bib152","doi-asserted-by":"crossref","first-page":"299","DOI":"10.1016\/0091-6749(82)90066-5","article-title":"Common variable hypogammaglobulinemia with T-cell nodular lymphoid interstitial pneumonitis and B-cell nodular lymphoid hyperplasia: different lymphocyte populations with a similar response to prednisone therapy","volume":"70","author":"Kohler","year":"1982","journal-title":"J\u00a0Allergy Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib153","doi-asserted-by":"crossref","first-page":"88","DOI":"10.1136\/thorax.55.1.88","article-title":"Lymphoid interstitial pneumonitis associated with common variable hypogammaglobulinaemia treated with cyclosporin A","volume":"55","author":"Davies","year":"2000","journal-title":"Thorax"},{"key":"10.1016\/j.jaip.2016.08.005_bib154","doi-asserted-by":"crossref","first-page":"293","DOI":"10.1016\/S1081-1206(10)61228-8","article-title":"Infliximab treatment for severe granulomatous disease in common variable immunodeficiency: a case report and review of the literature","volume":"95","author":"Thatayatikom","year":"2005","journal-title":"Ann Allergy Asthma Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib155","doi-asserted-by":"crossref","first-page":"820","DOI":"10.1007\/s10875-014-0079-3","article-title":"Infliximab for treatment of granulomatous disease in patients with common variable immunodeficiency","volume":"34","author":"Franxman","year":"2014","journal-title":"J\u00a0Clin Immunol"},{"key":"10.1016\/j.jaip.2016.08.005_bib156","doi-asserted-by":"crossref","first-page":"4834","DOI":"10.1182\/blood-2008-10-186999","article-title":"Progressive multifocal leukoencephalopathy after rituximab therapy in HIV-negative patients: a report of 57 cases from the Research on Adverse Drug Events and Reports project","volume":"113","author":"Carson","year":"2009","journal-title":"Blood"},{"key":"10.1016\/j.jaip.2016.08.005_bib157","doi-asserted-by":"crossref","first-page":"177","DOI":"10.1038\/bjc.2014.523","article-title":"Use of azathioprine for graft-vs-host disease is the major risk for development of secondary malignancies after haematopoietic stem cell transplantation: a nationwide population-based study","volume":"112","author":"Chien","year":"2015","journal-title":"Br J Cancer"},{"key":"10.1016\/j.jaip.2016.08.005_bib158","doi-asserted-by":"crossref","first-page":"362","DOI":"10.1080\/00365540600978955","article-title":"Common variable immune deficiency and lung transplantation","volume":"39","author":"Burton","year":"2007","journal-title":"Scand J Infect Dis"}],"container-title":["The Journal of Allergy and Clinical Immunology: In Practice"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S2213219816303804?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S2213219816303804?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2025,11,1]],"date-time":"2025-11-01T05:12:48Z","timestamp":1761973968000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S2213219816303804"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2016,11]]},"references-count":158,"journal-issue":{"issue":"6","published-print":{"date-parts":[[2016,11]]}},"alternative-id":["S2213219816303804"],"URL":"https:\/\/doi.org\/10.1016\/j.jaip.2016.08.005","relation":{},"ISSN":["2213-2198"],"issn-type":[{"value":"2213-2198","type":"print"}],"subject":[],"published":{"date-parts":[[2016,11]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"Lung Disease in Primary Antibody Deficiencies","name":"articletitle","label":"Article Title"},{"value":"The Journal of Allergy and Clinical Immunology: In Practice","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.jaip.2016.08.005","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"\u00a9 2016 American Academy of Allergy, Asthma & Immunology","name":"copyright","label":"Copyright"}]}}