{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,24]],"date-time":"2026-09-24T08:57:55Z","timestamp":1790240275234,"version":"4.1.0"},"reference-count":17,"publisher":"Elsevier BV","issue":"5","license":[{"start":{"date-parts":[[2016,9,1]],"date-time":"2016-09-01T00:00:00Z","timestamp":1472688000000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2018,9,1]],"date-time":"2018-09-01T00:00:00Z","timestamp":1535760000000},"content-version":"vor","delay-in-days":730,"URL":"https:\/\/www.elsevier.com\/open-access\/userlicense\/1.0\/"}],"funder":[{"name":"Mukoviszidose e.V.","award":["SIP CFTR_3_2010"],"award-info":[{"award-number":["SIP CFTR_3_2010"]}]},{"name":"BMBF (German Center for Lung Research, Disease Area \u2018Cystic Fibrosis\u2019 at BREATH)"}],"content-domain":{"domain":["clinicalkey.jp","clinicalkey.com","cysticfibrosisjournal.com","clinicalkey.es","clinicalkey.fr","clinicalkey.com.au","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Journal of Cystic Fibrosis"],"published-print":{"date-parts":[[2016,9]]},"DOI":"10.1016\/j.jcf.2015.10.011","type":"journal-article","created":{"date-parts":[[2015,10,31]],"date-time":"2015-10-31T01:30:40Z","timestamp":1446255040000},"page":"641-644","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":19,"title":["Non-allergic asthma as a CFTR-related disorder"],"prefix":"10.1016","volume":"15","author":[{"given":"Angela","family":"Schulz","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Burkhard","family":"T\u00fcmmler","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"key":"10.1016\/j.jcf.2015.10.011_bb0005","doi-asserted-by":"crossref","first-page":"179","DOI":"10.1016\/j.jcf.2008.03.009","article-title":"Consensus on the use and interpretation of cystic fibrosis mutation analysis in clinical practice","volume":"7","author":"Castellani","year":"2008","journal-title":"J Cyst Fibros"},{"issue":"Suppl. 2","key":"10.1016\/j.jcf.2015.10.011_bb0010","doi-asserted-by":"crossref","first-page":"S86","DOI":"10.1016\/S1569-1993(11)60014-3","article-title":"Recommendations for the classification of diseases as CFTR-related disorders","volume":"10","author":"Bombieri","year":"2011","journal-title":"J Cyst Fibros"},{"key":"10.1016\/j.jcf.2015.10.011_bb0015","doi-asserted-by":"crossref","first-page":"627","DOI":"10.1136\/thx.2005.043539","article-title":"Cystic fibrosis: terminology and diagnostic algorithms","volume":"61","author":"De Boeck","year":"2006","journal-title":"Thorax"},{"key":"10.1016\/j.jcf.2015.10.011_bb0020","doi-asserted-by":"crossref","first-page":"1160","DOI":"10.1038\/ng.2745","article-title":"Defining the disease liability of variants in the cystic fibrosis transmembrane conductance regulator gene","volume":"45","author":"Sosnay","year":"2013","journal-title":"Nat Genet"},{"issue":"Suppl. 2","key":"10.1016\/j.jcf.2015.10.011_bb0025","doi-asserted-by":"crossref","first-page":"S53","DOI":"10.1016\/S1569-1993(11)60009-X","article-title":"New clinical diagnostic procedures for cystic fibrosis in Europe","volume":"10","author":"De Boeck","year":"2011","journal-title":"J Cyst Fibros"},{"key":"10.1016\/j.jcf.2015.10.011_bb0030","series-title":"P\u00e4diatrische pneumologie","first-page":"553","article-title":"Asthma bronchiale","author":"Hamelmann","year":"2014"},{"key":"10.1016\/j.jcf.2015.10.011_bb0035","doi-asserted-by":"crossref","first-page":"69","DOI":"10.1007\/978-1-61779-117-8_6","article-title":"Nasal potential difference measurements to assess CFTR ion channel activity","volume":"741","author":"Rowe","year":"2011","journal-title":"Methods Mol Biol"},{"key":"10.1016\/j.jcf.2015.10.011_bb0040","doi-asserted-by":"crossref","DOI":"10.1007\/s00112-014-3122-9","article-title":"Handlungsempfehlung nach der Leitlinie\u201a Diagnose der Mukoviszidose","author":"N\u00e4hrlich","year":"2014","journal-title":"Monatsschr Kinderheilkd"},{"key":"10.1016\/j.jcf.2015.10.011_bb0045","doi-asserted-by":"crossref","first-page":"447","DOI":"10.1016\/j.jcf.2014.12.012","article-title":"Clinical expression of patients with the D1152H CFTR mutation","volume":"14","author":"Terlizzi","year":"2015","journal-title":"J Cyst Fibros"},{"key":"10.1016\/j.jcf.2015.10.011_bb0050","doi-asserted-by":"crossref","first-page":"929","DOI":"10.1164\/rccm.201003-0382OC","article-title":"Clinical phenotype and genotype of children with borderline sweat test and abnormal nasal epithelial chloride transport","volume":"182","author":"Sermet-Gaudelus","year":"2010","journal-title":"Am J Respir Crit Care Med"},{"key":"10.1016\/j.jcf.2015.10.011_bb0055","doi-asserted-by":"crossref","first-page":"1208","DOI":"10.1183\/09031936.01.00092501","article-title":"Nasal potential difference measurements in patients with atypical cystic fibrosis","volume":"17","author":"Wilschanski","year":"2001","journal-title":"Eur Respir J"},{"key":"10.1016\/j.jcf.2015.10.011_bb0060","doi-asserted-by":"crossref","first-page":"1771","DOI":"10.1093\/hmg\/9.12.1771","article-title":"Cellular and viral splicing factors can modify the splicing pattern of CFTR transcripts carrying splicing mutations","volume":"9","author":"Nissim-Rafinia","year":"2000","journal-title":"Hum Mol Genet"},{"key":"10.1016\/j.jcf.2015.10.011_bb0065","doi-asserted-by":"crossref","first-page":"7273","DOI":"10.1093\/nar\/gkq573","article-title":"CELF proteins regulate CFTR pre-mRNA splicing: essential role of the divergent domain of ETR-3","volume":"38","author":"Dujardin","year":"2010","journal-title":"Nucleic Acids Res"},{"key":"10.1016\/j.jcf.2015.10.011_bb0070","doi-asserted-by":"crossref","first-page":"116","DOI":"10.1183\/09031936.00113214","article-title":"Transcription factors and miRNAs that regulate fetal to adult CFTR expression change are new targets for cystic fibrosis","volume":"45","author":"Viart","year":"2015","journal-title":"Eur Respir J"},{"key":"10.1016\/j.jcf.2015.10.011_bb0075","doi-asserted-by":"crossref","first-page":"543","DOI":"10.3390\/genes6030543","article-title":"Chromatin dynamics in the regulation of CFTR expression","volume":"6","author":"Gosalia","year":"2015","journal-title":"Genes (Basel)"},{"key":"10.1016\/j.jcf.2015.10.011_bb0080","doi-asserted-by":"crossref","first-page":"4396","DOI":"10.1111\/febs.12392","article-title":"Control of cystic fibrosis transmembrane conductance regulator membrane trafficking: not just from the endoplasmic reticulum to the Golgi","volume":"280","author":"Farinha","year":"2013","journal-title":"FEBS J"},{"issue":"5","key":"10.1016\/j.jcf.2015.10.011_bb0085","doi-asserted-by":"crossref","first-page":"646","DOI":"10.1016\/j.jcf.2015.02.012","article-title":"Should diffuse bronchiectasis still be considered a CFTR-related disorder?","volume":"14","author":"Bergougnoux","year":"2015","journal-title":"J Cyst Fibros"}],"container-title":["Journal of Cystic Fibrosis"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1569199315002532?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1569199315002532?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2018,9,18]],"date-time":"2018-09-18T00:52:24Z","timestamp":1537231944000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S1569199315002532"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2016,9]]},"references-count":17,"journal-issue":{"issue":"5","published-print":{"date-parts":[[2016,9]]}},"alternative-id":["S1569199315002532"],"URL":"https:\/\/doi.org\/10.1016\/j.jcf.2015.10.011","relation":{},"ISSN":["1569-1993"],"issn-type":[{"value":"1569-1993","type":"print"}],"subject":[],"published":{"date-parts":[[2016,9]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"Non-allergic asthma as a CFTR-related disorder","name":"articletitle","label":"Article Title"},{"value":"Journal of Cystic Fibrosis","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.jcf.2015.10.011","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"\u00a9 2015 European Cystic Fibrosis Society. Published by Elsevier B.V.","name":"copyright","label":"Copyright"}]}}