{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,5]],"date-time":"2026-10-05T19:44:18Z","timestamp":1791229458247,"version":"4.1.0"},"reference-count":17,"publisher":"Elsevier BV","issue":"4","license":[{"start":{"date-parts":[[2022,7,1]],"date-time":"2022-07-01T00:00:00Z","timestamp":1656633600000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2022,7,1]],"date-time":"2022-07-01T00:00:00Z","timestamp":1656633600000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/legal\/tdmrep-license"},{"start":{"date-parts":[[2024,7,1]],"date-time":"2024-07-01T00:00:00Z","timestamp":1719792000000},"content-version":"vor","delay-in-days":731,"URL":"http:\/\/www.elsevier.com\/open-access\/userlicense\/1.0\/"}],"content-domain":{"domain":["clinicalkey.com","clinicalkey.com.au","clinicalkey.es","clinicalkey.fr","clinicalkey.jp","cysticfibrosisjournal.com","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Journal of Cystic Fibrosis"],"published-print":{"date-parts":[[2022,7]]},"DOI":"10.1016\/j.jcf.2022.04.005","type":"journal-article","created":{"date-parts":[[2022,4,11]],"date-time":"2022-04-11T17:01:01Z","timestamp":1649696461000},"page":"721-724","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":107,"title":["A case report of CFTR modulator administration via carrier mother to treat meconium ileus in a F508del homozygous fetus"],"prefix":"10.1016","volume":"21","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-4616-7426","authenticated-orcid":false,"given":"Sylvia","family":"Szentpetery","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-7926-2297","authenticated-orcid":false,"given":"Kimberly","family":"Foil","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-7089-7074","authenticated-orcid":false,"given":"Sara","family":"Hendrix","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Sue","family":"Gray","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-9369-8505","authenticated-orcid":false,"given":"Christina","family":"Mingora","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Barbara","family":"Head","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Donna","family":"Johnson","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Patrick A.","family":"Flume","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"key":"10.1016\/j.jcf.2022.04.005_bib0001","unstructured":"Annual Data Report [Internet]. Cystic Fibrosis Foundation. 2020."},{"issue":"12","key":"10.1016\/j.jcf.2022.04.005_bib0002","article-title":"Corrector therapies (with or without potentiators) for people with cystic fibrosis with class II CFTR gene variants (most commonly F508del)","volume":"12","author":"Southern","year":"2020","journal-title":"Cochrane Database Syst Rev"},{"issue":"2","key":"10.1016\/j.jcf.2022.04.005_bib0003","doi-asserted-by":"crossref","first-page":"107","DOI":"10.1016\/S2213-2600(15)00545-7","article-title":"Safety, pharmacokinetics, and pharmacodynamics of ivacaftor in patients aged 2\u20135 years with cystic fibrosis and a CFTR gating mutation (KIWI): an open-label, single-arm study","volume":"4","author":"Davies","year":"2016","journal-title":"Lancet Respir Med"},{"issue":"7","key":"10.1016\/j.jcf.2022.04.005_bib0004","doi-asserted-by":"crossref","first-page":"545","DOI":"10.1016\/S2213-2600(18)30202-9","article-title":"Ivacaftor treatment of cystic fibrosis in children aged 12 to <24 months and with a CFTR gating mutation (ARRIVAL): a phase 3 single-arm study","volume":"6","author":"Rosenfeld","year":"2018","journal-title":"Lancet Respir Med"},{"issue":"5","key":"10.1016\/j.jcf.2022.04.005_bib0005","doi-asserted-by":"crossref","first-page":"835","DOI":"10.1016\/j.jcf.2021.03.018","article-title":"Normal pancreatic function and false-negative CF newborn screen in a child born to a mother taking CFTR modulator therapy during pregnancy","volume":"20","author":"Fortner","year":"2021","journal-title":"J Cyst Fibros"},{"key":"10.1016\/j.jcf.2022.04.005_bib0006","article-title":"Drug exposure to infants born to mothers taking elexacaftor, tezacaftor, and ivacaftor","author":"Collins","year":"2021","journal-title":"J Cyst Fibros"},{"key":"10.1016\/j.jcf.2022.04.005_bib0007","article-title":"Pregnancy in cystic fibrosis: review of the literature and expert recommendations","author":"Jain","year":"2021","journal-title":"J Cyst Fibros"},{"issue":"3","key":"10.1016\/j.jcf.2022.04.005_bib0008","doi-asserted-by":"crossref","first-page":"402","DOI":"10.1016\/j.jcf.2021.03.006","article-title":"Maternal and fetal outcomes following elexacaftor-tezacaftor-ivacaftor use during pregnancy and lactation","volume":"20","author":"Taylor-Cousar","year":"2021","journal-title":"J Cyst Fibros"},{"issue":"4","key":"10.1016\/j.jcf.2022.04.005_bib0009","doi-asserted-by":"crossref","first-page":"560","DOI":"10.1016\/j.surg.2005.06.049","article-title":"Surgical considerations in cystic fibrosis: a 32-year evaluation of outcomes","volume":"138","author":"Escobar","year":"2005","journal-title":"Surgery"},{"issue":"Suppl 2","key":"10.1016\/j.jcf.2022.04.005_bib0010","doi-asserted-by":"crossref","first-page":"S32","DOI":"10.1016\/j.jcf.2017.06.007","article-title":"Meconium ileus in cystic fibrosis","volume":"16","author":"Sathe","year":"2017","journal-title":"J Cyst Fibros"},{"issue":"12","key":"10.1016\/j.jcf.2022.04.005_bib0011","doi-asserted-by":"crossref","first-page":"1295","DOI":"10.1002\/ppul.23554","article-title":"Innovative assessment of inpatient and pulmonary drug costs for children with cystic fibrosis","volume":"51","author":"Levy","year":"2016","journal-title":"Pediatr Pulmonol"},{"issue":"14","key":"10.1016\/j.jcf.2022.04.005_bib0012","doi-asserted-by":"crossref","first-page":"2375","DOI":"10.1080\/14767058.2019.1660767","article-title":"Making neonatal intensive care: cost effective","volume":"34","author":"Sharma","year":"2021","journal-title":"J Matern Fetal Neonatal Med"},{"issue":"4","key":"10.1016\/j.jcf.2022.04.005_bib0013","doi-asserted-by":"crossref","first-page":"772","DOI":"10.1016\/j.jpedsurg.2012.02.019","article-title":"A review of pathophysiology and management of fetuses and neonates with meconium ileus for the pediatric surgeon","volume":"47","author":"BE","year":"2012","journal-title":"J Pediatr Surg"},{"issue":"1","key":"10.1016\/j.jcf.2022.04.005_bib0014","doi-asserted-by":"crossref","first-page":"71","DOI":"10.1016\/j.jpedsurg.2008.10.010","article-title":"Neonatal outcomes associated with intestinal abnormalities diagnosed by fetal ultrasound","volume":"44","author":"Ruiz","year":"2009","journal-title":"J Pediatr Surg"},{"issue":"3","key":"10.1016\/j.jcf.2022.04.005_bib0015","doi-asserted-by":"crossref","first-page":"677","DOI":"10.1148\/radiology.183.3.1584918","article-title":"Prevalence of cystic fibrosis in fetuses with dilated bowel","volume":"183","author":"Estroff","year":"1992","journal-title":"Radiology"},{"issue":"485","key":"10.1016\/j.jcf.2022.04.005_bib0016","doi-asserted-by":"crossref","first-page":"eaau7531","DOI":"10.1126\/scitranslmed.aau7531","article-title":"In utero and postnatal VX-770 administration rescues multiorgan disease in a ferret model of cystic fibrosis","volume":"11","author":"Sun","year":"2019","journal-title":"Sci Transl Med"},{"issue":"2","key":"10.1016\/j.jcf.2022.04.005_bib0017","doi-asserted-by":"crossref","first-page":"F106","DOI":"10.1136\/fn.88.2.F106","article-title":"Faecal elastase 1 levels in premature and full term infants","volume":"88","author":"Kori","year":"2003","journal-title":"Arch Dis Child Fetal Neonatal Ed"}],"container-title":["Journal of Cystic Fibrosis"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1569199322000959?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1569199322000959?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2025,10,27]],"date-time":"2025-10-27T21:46:05Z","timestamp":1761601565000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S1569199322000959"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2022,7]]},"references-count":17,"journal-issue":{"issue":"4","published-print":{"date-parts":[[2022,7]]}},"alternative-id":["S1569199322000959"],"URL":"https:\/\/doi.org\/10.1016\/j.jcf.2022.04.005","relation":{},"ISSN":["1569-1993"],"issn-type":[{"value":"1569-1993","type":"print"}],"subject":[],"published":{"date-parts":[[2022,7]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"A case report of CFTR modulator administration via carrier mother to treat meconium ileus in a F508del homozygous fetus","name":"articletitle","label":"Article Title"},{"value":"Journal of Cystic Fibrosis","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.jcf.2022.04.005","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"\u00a9 2022 European Cystic Fibrosis Society. Published by Elsevier B.V.","name":"copyright","label":"Copyright"}]}}