{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,9]],"date-time":"2026-10-09T23:18:53Z","timestamp":1791587933152,"version":"4.3.4"},"reference-count":40,"publisher":"Elsevier BV","issue":"3","license":[{"start":{"date-parts":[[2009,9,1]],"date-time":"2009-09-01T00:00:00Z","timestamp":1251763200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Journal of Hepatology"],"published-print":{"date-parts":[[2009,9]]},"DOI":"10.1016\/j.jhep.2009.05.026","type":"journal-article","created":{"date-parts":[[2009,6,18]],"date-time":"2009-06-18T04:06:43Z","timestamp":1245298003000},"page":"483-490","source":"Crossref","is-referenced-by-count":57,"title":["Liver transplantation for glycogen storage disease type Ia"],"prefix":"10.1016","volume":"51","author":[{"given":"Srinevas K.","family":"Reddy","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Stephanie L.","family":"Austin","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Michele","family":"Spencer-Manzon","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Dwight D.","family":"Koeberl","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Bryan M.","family":"Clary","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Dev M.","family":"Desai","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Alastair D.","family":"Smith","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Priya S.","family":"Kishnani","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"key":"10.1016\/j.jhep.2009.05.026_bib1","first-page":"1521","article-title":"Glycogen storage disease","volume":"vol. 1","author":"Chen","year":"2001"},{"key":"10.1016\/j.jhep.2009.05.026_bib2","doi-asserted-by":"crossref","first-page":"S20","DOI":"10.1007\/BF02679990","article-title":"Glycogen storage disease type I: diagnosis, management, clinical course, and outcome. Results of the European study on glycogen storage disease type I (ESGSD I)","volume":"161","author":"Rake","year":"2002","journal-title":"Eur J Pediatr"},{"issue":"Suppl. 1","key":"10.1016\/j.jhep.2009.05.026_bib3","doi-asserted-by":"crossref","first-page":"S52","DOI":"10.1007\/BF02072089","article-title":"The long-term outcome of patients with glycogen storage disease type Ia","volume":"152","author":"Smit","year":"1993","journal-title":"Eur J Pediatr"},{"key":"10.1016\/j.jhep.2009.05.026_bib4","doi-asserted-by":"crossref","first-page":"218","DOI":"10.7326\/0003-4819-120-3-199402010-00008","article-title":"Glycogen storage disease in adults","volume":"120","author":"Talente","year":"1994","journal-title":"Ann Intern Med"},{"key":"10.1016\/j.jhep.2009.05.026_bib5","doi-asserted-by":"crossref","first-page":"S63","DOI":"10.1007\/BF02072092","article-title":"Glycogen storage disease I and hepatocellular tumors","volume":"152","author":"Bianchi","year":"1993","journal-title":"Eur J Pediatr"},{"key":"10.1016\/j.jhep.2009.05.026_bib6","doi-asserted-by":"crossref","first-page":"153","DOI":"10.1007\/s10545-005-7500-2","article-title":"Hepatocellular carcinoma in glycogen storage disease type Ia: a case series","volume":"288","author":"Franco","year":"2005","journal-title":"J Inherit Metab Dis"},{"key":"10.1016\/j.jhep.2009.05.026_bib7","doi-asserted-by":"crossref","first-page":"879","DOI":"10.1111\/j.1432-2277.2003.tb00258.x","article-title":"Glycogenosis storage type I diseases and evolutive adenomatosis: an indication for liver transplantation","volume":"16","author":"Lerut","year":"2003","journal-title":"Transpl Int"},{"key":"10.1016\/j.jhep.2009.05.026_bib8","doi-asserted-by":"crossref","first-page":"S35","DOI":"10.1007\/BF02679991","article-title":"Effect of continuous glucose therapy with uncooked cornstarch on the long-term clinical course of type Ia glycogen storage disease","volume":"161","author":"Weinstein","year":"2002","journal-title":"Eur J Pediatr"},{"key":"10.1016\/j.jhep.2009.05.026_bib9","first-page":"166","article-title":"Hepatic adenomata in type Ia glycogen storage disease","volume":"111","author":"Coire","year":"1987","journal-title":"Arch Pathol Lab Med"},{"key":"10.1016\/j.jhep.2009.05.026_bib10","doi-asserted-by":"crossref","first-page":"159","DOI":"10.1007\/s10545-007-0519-9","article-title":"Glycogen storage disease types I and III: treatment updates","volume":"30","author":"Koeberl","year":"2007","journal-title":"J Inherit Metab Dis"},{"key":"10.1016\/j.jhep.2009.05.026_bib11","doi-asserted-by":"crossref","first-page":"723","DOI":"10.1023\/A:1005544117285","article-title":"Long-term outcome of liver transplantation in patients with glycogen storage disease type Ia","volume":"22","author":"Faivre","year":"1999","journal-title":"J Inherit Metab Dis"},{"key":"10.1016\/j.jhep.2009.05.026_bib12","doi-asserted-by":"crossref","first-page":"S46","DOI":"10.1007\/BF02679993","article-title":"Glycogen storage disease type I: pathophysiology of liver adenomas","volume":"161","author":"Lee","year":"2002","journal-title":"Eur J Pediatr"},{"key":"10.1016\/j.jhep.2009.05.026_bib13","doi-asserted-by":"crossref","first-page":"S40","DOI":"10.1007\/BF02679992","article-title":"Type I glycogen storage disease: favourable outcome on a strict management regimen avoiding increased lactate production during childhood and adolescence","volume":"161","author":"Daublin","year":"2002","journal-title":"Eur J Pediatr"},{"key":"10.1016\/j.jhep.2009.05.026_bib14","doi-asserted-by":"crossref","first-page":"S43","DOI":"10.1007\/PL00014320","article-title":"Liver transplantation for glycogen storage disease types I, III, and IV","volume":"158","author":"Matern","year":"1999","journal-title":"Eur J Pediatr"},{"key":"10.1016\/j.jhep.2009.05.026_bib15","doi-asserted-by":"crossref","first-page":"366","DOI":"10.1016\/S0041-1345(02)03951-9","article-title":"Outcome of living done liver transplantation for glycogen storage disease","volume":"35","author":"Liu","year":"2003","journal-title":"Transplant Proc"},{"key":"10.1016\/j.jhep.2009.05.026_bib16","doi-asserted-by":"crossref","first-page":"276","DOI":"10.1097\/00005176-199703000-00008","article-title":"Hepatocellular adenomas I glycogen storage disease type I and III: a series of 43 patients and review of the literature","volume":"24","author":"Labrune","year":"1997","journal-title":"J Pediatr Gastroenterol Nutr"},{"key":"10.1016\/j.jhep.2009.05.026_bib17","doi-asserted-by":"crossref","first-page":"398","DOI":"10.1016\/j.ymgme.2007.10.134","article-title":"Hepatocellular adenoma and metabolic balance in patients with type Ia glycogen storage disease","volume":"93","author":"Rocco","year":"2008","journal-title":"Mol Gen Metabol"},{"key":"10.1016\/j.jhep.2009.05.026_bib18","doi-asserted-by":"crossref","first-page":"S53","DOI":"10.1007\/BF02679995","article-title":"Glycogen storage disease type I: indications for liver and\/or kidney transplantation","volume":"161","author":"Labrune","year":"2002","journal-title":"Eur J Pediatr"},{"key":"10.1016\/j.jhep.2009.05.026_bib19","doi-asserted-by":"crossref","first-page":"567","DOI":"10.1053\/jlts.2001.25879","article-title":"MELD and PELD: application of survival models to liver allocation","volume":"7","author":"Wiesner","year":"2001","journal-title":"Liver Transpl"},{"key":"10.1016\/j.jhep.2009.05.026_bib20","doi-asserted-by":"crossref","first-page":"134","DOI":"10.1136\/gut.52.1.134","article-title":"MELD scoring system is useful for predicting prognosis in patients with liver cirrhosis and is correlated with residual liver function: a European study","volume":"52","author":"Botta","year":"2003","journal-title":"Gut"},{"key":"10.1016\/j.jhep.2009.05.026_bib21","doi-asserted-by":"crossref","first-page":"91","DOI":"10.1053\/gast.2003.50016","article-title":"Model for end stage liver disease (MELD) and allocation of donor livers","volume":"124","author":"Wiesner","year":"2003","journal-title":"Gastroenterology"},{"key":"10.1016\/j.jhep.2009.05.026_bib22","doi-asserted-by":"crossref","first-page":"658","DOI":"10.1016\/j.jhep.2007.05.012","article-title":"Resection of hepatocellular adenoma in patients with glycogen storage disease type Ia","volume":"47","author":"Reddy","year":"2007","journal-title":"J Hepatol"},{"key":"10.1016\/j.jhep.2009.05.026_bib23","doi-asserted-by":"crossref","first-page":"464","DOI":"10.1053\/jhep.2001.22172","article-title":"A model to predict survival in patients with end-stage liver disease","volume":"33","author":"Kamath","year":"2001","journal-title":"Hepatology"},{"key":"10.1016\/j.jhep.2009.05.026_bib24","doi-asserted-by":"crossref","first-page":"2244","DOI":"10.1111\/j.1600-6143.2005.01008.x","article-title":"Regional variations in peer reviewed liver allocation under the MELD system","volume":"5","author":"Rodriguez-Luna","year":"2005","journal-title":"Am J Transplant"},{"key":"10.1016\/j.jhep.2009.05.026_bib25","doi-asserted-by":"crossref","first-page":"137","DOI":"10.1111\/j.1399-3046.2007.00803.x","article-title":"Liver transplantation in children with glycogen storage disease: controversies and evaluation of the risk\/benefit of this procedure","volume":"12","author":"Davis","year":"2008","journal-title":"Pediatr Transplant"},{"key":"10.1016\/j.jhep.2009.05.026_bib26","doi-asserted-by":"crossref","first-page":"S112","DOI":"10.1007\/BF02680007","article-title":"Guidelines for management of glycogen storage disease type I\u2014European study on glycogen storage disease type I (ESGSD I)","volume":"161","author":"Rake","year":"2002","journal-title":"Eur J Pediatr"},{"key":"10.1016\/j.jhep.2009.05.026_bib27","doi-asserted-by":"crossref","first-page":"693","DOI":"10.1056\/NEJM199603143341104","article-title":"Liver transplantation for the treatment of small hepatocellular carcinoma in patients with cirrhosis","volume":"334","author":"Mazzaferro","year":"1996","journal-title":"N Engl J Med"},{"key":"10.1016\/j.jhep.2009.05.026_bib28","doi-asserted-by":"crossref","first-page":"3776","DOI":"10.1182\/blood-2002-04-1260","article-title":"Inappropriate expression of hepcidin is associated with iron refractory anemia: implications for anemia of chronic disease","volume":"100","author":"Weinstein","year":"2002","journal-title":"Blood"},{"key":"10.1016\/j.jhep.2009.05.026_bib29","doi-asserted-by":"crossref","first-page":"507","DOI":"10.1203\/01.PDR.0000049513.67410.2D","article-title":"The molecular biology of the anemia of chronic disease: a hypothesis","volume":"53","author":"Roy","year":"2003","journal-title":"Pediatr Res"},{"key":"10.1016\/j.jhep.2009.05.026_bib30","doi-asserted-by":"crossref","first-page":"8780","DOI":"10.1073\/pnas.151179498","article-title":"Lack of hepcidin gene expression and severe tissue iron overload in upstream stimulatory factor 2 (USF2) knockout mice","volume":"98","author":"Nicolas","year":"2001","journal-title":"Proc Natl Acad Sci USA"},{"key":"10.1016\/j.jhep.2009.05.026_bib31","doi-asserted-by":"crossref","first-page":"19","DOI":"10.1111\/j.1365-2265.2005.02292.x","article-title":"Efficacy of ACE-inhibitor therapy on renal disease in glycogen storage disease type I: a multicentre retrospective study","volume":"63","author":"Melis","year":"2005","journal-title":"Clin Endocrinol"},{"key":"10.1016\/j.jhep.2009.05.026_bib32","doi-asserted-by":"crossref","first-page":"716","DOI":"10.1038\/sj.ki.5002718","article-title":"Angiotensin mediates renal fibrosis in the nephropathy of glycogen storage disease type Ia","volume":"73","author":"Yiu","year":"2008","journal-title":"Kidney Int"},{"key":"10.1016\/j.jhep.2009.05.026_bib33","doi-asserted-by":"crossref","first-page":"S60","DOI":"10.1007\/BF02072091","article-title":"Renal complications in glycogen storage disease type I","volume":"152","author":"Reitsma-Bierens","year":"1993","journal-title":"Eur J Pediatr"},{"key":"10.1016\/j.jhep.2009.05.026_bib34","doi-asserted-by":"crossref","first-page":"1345","DOI":"10.1038\/ki.1989.133","article-title":"Hyperfiltration and renal disease in glycogen storage disease, type I","volume":"35","author":"Baker","year":"1989","journal-title":"Kidney Int"},{"key":"10.1016\/j.jhep.2009.05.026_bib35","doi-asserted-by":"crossref","first-page":"7","DOI":"10.1056\/NEJM198801073180102","article-title":"Renal disease in type I glycogen storage disease","volume":"318","author":"Chen","year":"1988","journal-title":"NEJM"},{"key":"10.1016\/j.jhep.2009.05.026_bib36","doi-asserted-by":"crossref","first-page":"1483","DOI":"10.1016\/j.transproceed.2004.05.070","article-title":"Simultaneous liver-kidney transplantation for glycogen storage disease type Ia (von Gierke\u2019s disease)","volume":"36","author":"Panaro","year":"2004","journal-title":"Transplant Proc"},{"key":"10.1016\/j.jhep.2009.05.026_bib37","doi-asserted-by":"crossref","first-page":"537","DOI":"10.1023\/B:BOLI.0000037397.39725.57","article-title":"Successful pregnancy after combined renal-hepatic transplantation in glycogen storage disease type Ia","volume":"27","author":"Lee","year":"2004","journal-title":"J Inherit Metab Dis"},{"key":"10.1016\/j.jhep.2009.05.026_bib38","doi-asserted-by":"crossref","first-page":"762","DOI":"10.1002\/lt.21147","article-title":"Combined liver-kidney transplantation in glycogen storage disease Ia: a case beyond the guidelines","volume":"13","author":"Belingheri","year":"2007","journal-title":"Liver Transpl"},{"key":"10.1016\/j.jhep.2009.05.026_bib39","doi-asserted-by":"crossref","first-page":"773","DOI":"10.1016\/j.transproceed.2009.01.038","article-title":"Chronic liver allograft dysfunction","volume":"41","author":"Desai","year":"2009","journal-title":"Transplant Proc"},{"key":"10.1016\/j.jhep.2009.05.026_bib40","doi-asserted-by":"crossref","first-page":"848","DOI":"10.1002\/lt.21151","article-title":"Long-term results of living donor liver transplantation for glycogen storage disorders in children","volume":"13","author":"Iyer","year":"2007","journal-title":"Liver Transpl"}],"container-title":["Journal of Hepatology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0168827809003961?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0168827809003961?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2018,12,18]],"date-time":"2018-12-18T18:59:41Z","timestamp":1545159581000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0168827809003961"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2009,9]]},"references-count":40,"journal-issue":{"issue":"3","published-print":{"date-parts":[[2009,9]]}},"alternative-id":["S0168827809003961"],"URL":"https:\/\/doi.org\/10.1016\/j.jhep.2009.05.026","relation":{},"ISSN":["0168-8278"],"issn-type":[{"value":"0168-8278","type":"print"}],"subject":[],"published":{"date-parts":[[2009,9]]}}}