{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,11,3]],"date-time":"2026-11-03T20:04:29Z","timestamp":1793736269768,"version":"4.6.1"},"reference-count":373,"publisher":"Elsevier BV","issue":"5","license":[{"start":{"date-parts":[[2023,11,1]],"date-time":"2023-11-01T00:00:00Z","timestamp":1698796800000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2023,11,1]],"date-time":"2023-11-01T00:00:00Z","timestamp":1698796800000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/legal\/tdmrep-license"}],"content-domain":{"domain":["clinicalkey.com","clinicalkey.com.au","clinicalkey.es","clinicalkey.fr","clinicalkey.jp","journal-of-hepatology.eu","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Journal of Hepatology"],"published-print":{"date-parts":[[2023,11]]},"DOI":"10.1016\/j.jhep.2023.07.013","type":"journal-article","created":{"date-parts":[[2023,10,18]],"date-time":"2023-10-18T23:06:32Z","timestamp":1697670392000},"page":"1270-1301","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":74,"title":["EASL-ERN position paper on liver involvement in patients with Fontan-type circulation"],"prefix":"10.1016","volume":"79","author":[{"given":"Luis","family":"T\u00e9llez","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Audrey","family":"Payanc\u00e9","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Eric","family":"Tjwa","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mar\u00eda Jes\u00fas","family":"del Cerro","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Lars","family":"Idorn","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Stanislav","family":"Ovroutski","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ruth","family":"De Bruyne","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Henkjan J.","family":"Verkade","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Fabrizio","family":"De Rita","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Charlotte","family":"de Lange","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Annalisa","family":"Angelini","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Val\u00e9rie","family":"Paradis","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Pierre Emmanuel","family":"Rautou","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Juan Carlos","family":"Garc\u00eda-Pag\u00e1n","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"issue":"142","key":"10.1016\/j.jhep.2023.07.013_bib1","doi-asserted-by":"crossref","first-page":"438","DOI":"10.1183\/16000617.0091-2016","article-title":"Managing adult Fontan patients: where do we stand?","volume":"25","author":"Clift","year":"2016","journal-title":"Eur Respir Rev"},{"issue":"11","key":"10.1016\/j.jhep.2023.07.013_bib2","doi-asserted-by":"crossref","first-page":"1648","DOI":"10.1016\/0002-9149(84)90595-2","article-title":"Long-term follow-up after palliative operation for univentricular heart","volume":"53","author":"Moodie","year":"1984","journal-title":"Am J Cardiol"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib3","doi-asserted-by":"crossref","first-page":"194","DOI":"10.1016\/j.jtcvs.2013.07.076","article-title":"Outcomes of patients born with single-ventricle physiology and aortic arch obstruction: the 26-year Melbourne experience","volume":"148","author":"Lee","year":"2014","journal-title":"J\u00a0Thorac Cardiovasc Surg"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib4","doi-asserted-by":"crossref","first-page":"240","DOI":"10.1136\/thx.26.3.240","article-title":"Surgical repair of tricuspid atresia","volume":"26","author":"Fontan","year":"1971","journal-title":"Thorax"},{"issue":"11 Suppl 1","key":"10.1016\/j.jhep.2023.07.013_bib5","first-page":"S32","article-title":"Redefining expectations of long-term survival after the Fontan procedure: twenty-five years of follow-up from the entire population of Australia and New Zealand","volume":"130","author":"d'Udekem","year":"2014","journal-title":"Circulation"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib6","doi-asserted-by":"crossref","first-page":"1100","DOI":"10.1016\/S0003-4975(99)00877-2","article-title":"Cavo-pulmonary shunt: from the first experiments to clinical practice","volume":"68","author":"Konstantinov","year":"1999","journal-title":"Ann Thorac Surg"},{"issue":"6","key":"10.1016\/j.jhep.2023.07.013_bib7","doi-asserted-by":"crossref","first-page":"1123","DOI":"10.1016\/S0022-5223(97)70032-1","article-title":"A\u00a0temporary bidirectional superior vena cava-pulmonary artery shunt","volume":"114","author":"Glenn","year":"1997","journal-title":"J\u00a0Thorac Cardiovasc Surg"},{"issue":"5","key":"10.1016\/j.jhep.2023.07.013_bib8","doi-asserted-by":"crossref","first-page":"682","DOI":"10.1016\/S0022-5223(19)35174-8","article-title":"Total cavopulmonary connection: a logical alternative to atriopulmonary connection for complex Fontan operations. Experimental studies and early clinical experience","volume":"96","author":"de Leval","year":"1988","journal-title":"J\u00a0Thorac Cardiovasc Surg"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib9","doi-asserted-by":"crossref","first-page":"228","DOI":"10.1016\/S0022-5223(19)35562-X","article-title":"Inferior vena cava-pulmonary artery extracardiac conduit. A new form of right heart bypass","volume":"100","author":"Marcelletti","year":"1990","journal-title":"J\u00a0Thorac Cardiovasc Surg"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib10","doi-asserted-by":"crossref","first-page":"837","DOI":"10.1016\/j.athoracsur.2018.08.041","article-title":"Extracardiac versus lateral tunnel fontan: a meta-analysis of long-term results","volume":"107","author":"Ben Ali","year":"2019","journal-title":"Ann Thorac Surg"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib11","doi-asserted-by":"crossref","first-page":"1004","DOI":"10.1007\/s12325-021-02002-3","article-title":"The epidemiology of persons living with fontan in 2020 and projections for 2030: development of an epidemiology model providing multinational estimates","volume":"39","author":"Plappert","year":"2022","journal-title":"Adv Ther"},{"key":"10.1016\/j.jhep.2023.07.013_bib12","doi-asserted-by":"crossref","first-page":"14","DOI":"10.1016\/j.ijcard.2016.05.035","article-title":"The fontan epidemic: population projections from the Australia and New\u00a0Zealand fontan registry","volume":"219","author":"Schilling","year":"2016","journal-title":"Int J Cardiol"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib13","doi-asserted-by":"crossref","first-page":"1311","DOI":"10.1016\/j.ijcard.2012.03.182","article-title":"Univentricular hearts in Denmark 1977 to 2009: incidence and survival","volume":"167","author":"Idorn","year":"2013","journal-title":"Int J Cardiol"},{"issue":"6","key":"10.1016\/j.jhep.2023.07.013_bib14","doi-asserted-by":"crossref","first-page":"591","DOI":"10.1161\/CIRCULATIONAHA.120.045597","article-title":"Fontan-associated liver disease: screening, management, and transplant considerations","volume":"142","author":"Emamaullee","year":"2020","journal-title":"Circulation"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib15","doi-asserted-by":"crossref","first-page":"192","DOI":"10.1016\/j.recesp.2017.10.014","article-title":"Fontan-associated liver disease","volume":"71","author":"T\u00e9llez","year":"2018","journal-title":"Rev Esp Cardiol (Engl Ed)"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib16","article-title":"Developing methodology for the creation of clinical practice guidelines for rare diseases: a report from RARE-Bestpractices","volume":"3","author":"Pai","year":"2015","journal-title":"Rare Dis"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib17","doi-asserted-by":"crossref","first-page":"67","DOI":"10.1186\/s12874-019-0713-0","article-title":"Strategies for eliciting and synthesizing evidence for guidelines in rare diseases","volume":"19","author":"Pai","year":"2019","journal-title":"BMC Med Res Methodol"},{"issue":"5","key":"10.1016\/j.jhep.2023.07.013_bib18","doi-asserted-by":"crossref","first-page":"1084","DOI":"10.1016\/0003-4975(91)91286-5","article-title":"Partial Fontan: advantages of an adjustable interatrial communication","volume":"52","author":"Laks","year":"1991","journal-title":"Ann Thorac Surg"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib19","doi-asserted-by":"crossref","first-page":"366","DOI":"10.1016\/j.athoracsur.2022.10.015","article-title":"Konstantinov IE. Kawashima Procedure: the impact of age","volume":"116","author":"Ivanov","year":"2023","journal-title":"Ann Thorac Surg"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib20","doi-asserted-by":"crossref","first-page":"613","DOI":"10.1016\/S0022-5223(19)40598-9","article-title":"An operation for the correction of tricuspid atresia","volume":"66","author":"Kreutzer","year":"1973","journal-title":"J\u00a0Thorac Cardiovasc Surg"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib21","doi-asserted-by":"crossref","first-page":"452","DOI":"10.1016\/S0022-5223(19)40916-1","article-title":"Right atrial-right ventricular anastomosis for correction of tricuspid atresia","volume":"77","author":"Bj\u00f6rk","year":"1979","journal-title":"J\u00a0Thorac Cardiovasc Surg"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib22","doi-asserted-by":"crossref","first-page":"371","DOI":"10.1016\/0003-4975(92)91407-Z","article-title":"Extracardiac total cavopulmonary connection","volume":"54","author":"Laschinger","year":"1992","journal-title":"Ann Thorac Surg"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib23","doi-asserted-by":"crossref","first-page":"651","DOI":"10.1111\/apa.15098","article-title":"Providing a framework of principles for conceptualising the Fontan circulation","volume":"109","author":"Gewillig","year":"2020","journal-title":"Acta Paediatr"},{"issue":"14","key":"10.1016\/j.jhep.2023.07.013_bib24","doi-asserted-by":"crossref","first-page":"1081","DOI":"10.1136\/heartjnl-2015-307467","article-title":"The Fontan circulation after 45 years: update in physiology","volume":"102","author":"Gewillig","year":"2016","journal-title":"Heart"},{"issue":"5","key":"10.1016\/j.jhep.2023.07.013_bib25","doi-asserted-by":"crossref","first-page":"372","DOI":"10.1136\/hrt.66.5.372","article-title":"Doppler echocardiographic evaluation of pulmonary blood flow after the Fontan operation: the role of the lungs","volume":"66","author":"Penny","year":"1991","journal-title":"Br Heart J"},{"key":"10.1016\/j.jhep.2023.07.013_bib26","doi-asserted-by":"crossref","first-page":"87","DOI":"10.1016\/j.ijcard.2021.09.042","article-title":"Late Fontan failure in adult patients is predominantly associated with deteriorating ventricular function","volume":"344","author":"Sallmon","year":"2021","journal-title":"Int J Cardiol"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib27","doi-asserted-by":"crossref","first-page":"105","DOI":"10.1016\/j.hfc.2013.09.010","article-title":"Failure of the fontan circulation","volume":"10","author":"Gewillig","year":"2014","journal-title":"Heart Fail Clin"},{"issue":"8","key":"10.1016\/j.jhep.2023.07.013_bib28","doi-asserted-by":"crossref","first-page":"680","DOI":"10.1136\/heartjnl-2017-311661","article-title":"Leg lean mass correlates with exercise systemic output in young Fontan patients","volume":"104","author":"Avitabile","year":"2018","journal-title":"Heart"},{"issue":"11","key":"10.1016\/j.jhep.2023.07.013_bib29","doi-asserted-by":"crossref","first-page":"1866","DOI":"10.1016\/j.amjcard.2017.03.004","article-title":"Effect of fontan-associated morbidities on survival with intact fontan circulation","volume":"119","author":"Allen","year":"2017","journal-title":"Am J Cardiol"},{"key":"10.1016\/j.jhep.2023.07.013_bib30","doi-asserted-by":"crossref","DOI":"10.1161\/CIR.0000000000000696","article-title":"American heart association council on cardiovascular disease in the young\u00a0and council on cardiovascular and stroke nursing. Evaluation and management of the child and adult with fontan circulation: a scientific statement from the American heart association","author":"Rychik","year":"2019","journal-title":"Circulation"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib31","doi-asserted-by":"crossref","first-page":"1458","DOI":"10.1016\/j.ijcard.2012.12.055","article-title":"Arrhythmia and exercise intolerance in Fontan patients: current status and future burden","volume":"168","author":"Idorn","year":"2013","journal-title":"Int J Cardiol"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib32","doi-asserted-by":"crossref","first-page":"192","DOI":"10.5604\/01.3001.0010.8634","article-title":"Fontan-associated liver disease: a review","volume":"17","author":"T\u00e9llez","year":"2018","journal-title":"Ann Hepatol"},{"issue":"5","key":"10.1016\/j.jhep.2023.07.013_bib33","doi-asserted-by":"crossref","first-page":"1918","DOI":"10.1016\/j.ijcard.2012.05.002","article-title":"Single ventricle anatomy is associated with increased frequency of nonalcoholic cirrhosis","volume":"167","author":"Krieger","year":"2013","journal-title":"Int J Cardiol"},{"issue":"5","key":"10.1016\/j.jhep.2023.07.013_bib34","doi-asserted-by":"crossref","first-page":"3894","DOI":"10.1002\/ehf2.13294","article-title":"Reaching consensus for unified medical language in Fontan care","volume":"8","author":"Alsaied","year":"2021","journal-title":"ESC Heart Fail"},{"issue":"7","key":"10.1016\/j.jhep.2023.07.013_bib35","first-page":"1002","article-title":"Hepatic and renal consequences of single-ventricle physiology palliated with the fontan operation","volume":"38","author":"Rathgeber","year":"2022","journal-title":"Can J Cardiol"},{"issue":"14","key":"10.1016\/j.jhep.2023.07.013_bib36","doi-asserted-by":"crossref","first-page":"1115","DOI":"10.1136\/heartjnl-2015-308823","article-title":"Towards a proposal for a universal diagnostic definition of protein-losing enteropathy in Fontan patients: a systematic review","volume":"102","author":"Udink Ten Cate","year":"2016","journal-title":"Heart"},{"issue":"5","key":"10.1016\/j.jhep.2023.07.013_bib37","doi-asserted-by":"crossref","first-page":"698","DOI":"10.1017\/S1047951120000864","article-title":"Treatment strategies for protein-losing enteropathy in Fontan-palliated patients","volume":"30","author":"Schleiger","year":"2020","journal-title":"Cardiol Young"},{"issue":"6","key":"10.1016\/j.jhep.2023.07.013_bib38","doi-asserted-by":"crossref","first-page":"996","DOI":"10.1111\/chd.12848","article-title":"Progressive loss of bone mass in children with Fontan circulation","volume":"14","author":"Diab","year":"2019","journal-title":"Congenit Heart Dis"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib39","doi-asserted-by":"crossref","first-page":"54","DOI":"10.1093\/ejcts\/ezab298","article-title":"Persisting and reoccurring cyanosis after Fontan operation is associated with increased late mortality","volume":"61","author":"Schafstedde","year":"2021","journal-title":"Eur J Cardiothorac Surg"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib40","doi-asserted-by":"crossref","first-page":"3230","DOI":"10.1016\/j.ijcard.2013.04.008","article-title":"Quality of life and cognitive function in Fontan patients, a population-based study","volume":"168","author":"Idorn","year":"2013","journal-title":"Int J Cardiol"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib41","doi-asserted-by":"crossref","DOI":"10.1161\/CIRCIMAGING.118.008074","article-title":"Morphology and function of the lymphatic vasculature in patients with a fontan circulation","volume":"12","author":"Mohanakumar","year":"2019","journal-title":"Circ Cardiovasc Imaging"},{"key":"10.1016\/j.jhep.2023.07.013_bib42","doi-asserted-by":"crossref","DOI":"10.3389\/fped.2022.828107","article-title":"Lymphatic disorders in patients with single ventricle heart disease","volume":"10","author":"Dori","year":"2022","journal-title":"Front Pediatr"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib43","doi-asserted-by":"crossref","first-page":"493","DOI":"10.1016\/S0022-5223(98)70310-1","article-title":"Thromboembolic complications after fontan procedures--the role of prophylactic anticoagulation","volume":"115","author":"Monagle","year":"1998","journal-title":"J\u00a0Thorac Cardiovasc Surg"},{"issue":"4 Pt 1","key":"10.1016\/j.jhep.2023.07.013_bib44","doi-asserted-by":"crossref","first-page":"745","DOI":"10.1016\/S0022-5223(00)70010-9","article-title":"Intracardiac thrombus formation after the Fontan operation","volume":"119","author":"Balling","year":"2000","journal-title":"J\u00a0Thorac Cardiovasc Surg"},{"key":"10.1016\/j.jhep.2023.07.013_bib45","doi-asserted-by":"crossref","first-page":"204","DOI":"10.1016\/j.thromres.2018.04.011","article-title":"Pathophysiology of thrombosis and anticoagulation post Fontan surgery","volume":"172","author":"Attard","year":"2018","journal-title":"Thromb Res"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib46","doi-asserted-by":"crossref","first-page":"144","DOI":"10.1016\/j.jacc.2010.02.048","article-title":"AARCC (alliance for adult research in congenital Cardiology) investigators. The CALF (congenital heart disease in adults lower extremity systemic venous health in fontan patients) study","volume":"56","author":"Valente","year":"2010","journal-title":"J\u00a0Am Coll Cardiol"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib47","doi-asserted-by":"crossref","first-page":"17","DOI":"10.1111\/chd.12401","article-title":"Sudden cardiac death and late arrhythmias after the Fontan operation","volume":"12","author":"Pundi","year":"2017","journal-title":"Congenit Heart Dis"},{"issue":"7","key":"10.1016\/j.jhep.2023.07.013_bib48","doi-asserted-by":"crossref","first-page":"1184","DOI":"10.1016\/j.amjcard.2013.12.025","article-title":"Prevalence of arrhythmias late after the Fontan operation","volume":"113","author":"Lasa","year":"2014","journal-title":"Am J Cardiol"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib49","doi-asserted-by":"crossref","DOI":"10.1136\/openhrt-2019-001224","article-title":"Atrial arrhythmias and thromboembolic complications in adults post Fontan surgery","volume":"7","author":"Wan","year":"2020","journal-title":"Open Heart"},{"key":"10.1016\/j.jhep.2023.07.013_bib50","article-title":"Evaluation of Fontan failure by classifying the severity of Fontan-associated liver disease: a single-centre cross-sectional study","author":"Schleiger","year":"2020","journal-title":"Eur J Cardiothorac Surg"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib51","doi-asserted-by":"crossref","first-page":"482","DOI":"10.1097\/SLA.0000000000005581","article-title":"Evaluation of fontan-associated liver disease and ethnic disparities in long-term survivors of the fontan procedure: a population-based study","volume":"276","author":"Emamaullee","year":"2022","journal-title":"Ann Surg"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib52","doi-asserted-by":"crossref","first-page":"249","DOI":"10.1016\/j.amjcard.2014.10.032","article-title":"Impact of liver disease after the fontan operation","volume":"115","author":"Lindsay","year":"2015","journal-title":"Am J Cardiol"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib53","doi-asserted-by":"crossref","first-page":"334","DOI":"10.1016\/j.jacc.2020.05.042","article-title":"Long-term kidney function after the fontan operation: JACC review topic of the week","volume":"76","author":"Zafar","year":"2020","journal-title":"J\u00a0Am Coll Cardiol"},{"key":"10.1016\/j.jhep.2023.07.013_bib54","doi-asserted-by":"crossref","first-page":"73","DOI":"10.1016\/j.ijcard.2020.01.014","article-title":"Fontan-associated nephropathy: predictors and outcomes","volume":"306","author":"Khuong","year":"2020","journal-title":"Int J Cardiol"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib55","doi-asserted-by":"crossref","first-page":"244","DOI":"10.1016\/j.ijcard.2007.11.079","article-title":"Nephropathy in patients after Fontan palliation","volume":"132","author":"Anne","year":"2009","journal-title":"Int J Cardiol"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib56","doi-asserted-by":"crossref","first-page":"104","DOI":"10.1136\/heartjnl-2016-310108","article-title":"Factors associated with long-term mortality after Fontan procedures: a systematic review","volume":"103","author":"Alsaied","year":"2017","journal-title":"Heart"},{"issue":"6","key":"10.1016\/j.jhep.2023.07.013_bib57","doi-asserted-by":"crossref","first-page":"831","DOI":"10.1017\/S1047951113001650","article-title":"End-organ consequences of the Fontan operation: liver fibrosis, protein-losing enteropathy and plastic bronchitis","volume":"23","author":"Rychik","year":"2013","journal-title":"Cardiol Young"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib58","doi-asserted-by":"crossref","first-page":"41","DOI":"10.1016\/j.ijcard.2011.07.053","article-title":"Pathophysiology of chronic venous insufficiency in adults with a Fontan circulation (a pre-defined substudy of the CALF investigation)","volume":"165","author":"Bhatt","year":"2013","journal-title":"Int J Cardiol"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib59","doi-asserted-by":"crossref","first-page":"256","DOI":"10.1007\/s00246-012-0430-5","article-title":"Demographic characteristics and estimated prevalence of Fontan-associated plastic bronchitis","volume":"34","author":"Caruthers","year":"2013","journal-title":"Pediatr Cardiol"},{"issue":"25","key":"10.1016\/j.jhep.2023.07.013_bib60","doi-asserted-by":"crossref","first-page":"2373","DOI":"10.1093\/eurheartj\/ehab826","article-title":"Predictors of long-term mortality among perioperative survivors of Fontan operation","volume":"43","author":"Inai","year":"2022","journal-title":"Eur Heart J"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib61","doi-asserted-by":"crossref","first-page":"633","DOI":"10.1007\/s10741-020-09932-0","article-title":"Diagnosis and management of the adult patient with a failing Fontan circulation","volume":"25","author":"Broda","year":"2020","journal-title":"Heart Fail Rev"},{"issue":"6","key":"10.1016\/j.jhep.2023.07.013_bib62","doi-asserted-by":"crossref","first-page":"839","DOI":"10.1136\/hrt.2004.051789","article-title":"The Fontan circulation","volume":"91","author":"Gewillig","year":"2005","journal-title":"Heart"},{"issue":"6","key":"10.1016\/j.jhep.2023.07.013_bib63","doi-asserted-by":"crossref","first-page":"785","DOI":"10.1586\/erc.11.75","article-title":"The failing Fontan: etiology, diagnosis and management","volume":"9","author":"Goldberg","year":"2011","journal-title":"Expert Rev Cardiovasc Ther"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib64","doi-asserted-by":"crossref","first-page":"296","DOI":"10.1111\/chd.12368","article-title":"Clinical phenotypes of fontan failure: implications for management","volume":"11","author":"Book","year":"2016","journal-title":"Congenit Heart Dis"},{"issue":"18","key":"10.1016\/j.jhep.2023.07.013_bib65","doi-asserted-by":"crossref","first-page":"1427","DOI":"10.1136\/heartjnl-2019-315862","article-title":"Modes of late mortality in patients with a Fontan circulation","volume":"106","author":"Poh","year":"2020","journal-title":"Heart"},{"key":"10.1016\/j.jhep.2023.07.013_bib66","article-title":"Pre- and Post-operative determinants of transplantation-free survival after Fontan. The Australia and New Zealand experience","volume":"35","author":"Poh","year":"2021","journal-title":"Int J Cardiol Heart Vasc"},{"key":"10.1016\/j.jhep.2023.07.013_bib67","doi-asserted-by":"crossref","DOI":"10.3389\/fcvm.2022.767503","article-title":"A\u00a0multimodal score accurately classifies fontan failure and late mortality in adult fontan patients","volume":"9","author":"Kramer","year":"2022","journal-title":"Front Cardiovasc Med"},{"issue":"5","key":"10.1016\/j.jhep.2023.07.013_bib68","doi-asserted-by":"crossref","first-page":"552","DOI":"10.1016\/j.hlc.2017.11.007","article-title":"Life after surviving fontan surgery: a meta-analysis of the incidence and predictors of late death","volume":"27","author":"Poh","year":"2018","journal-title":"Heart Lung Circ"},{"issue":"9","key":"10.1016\/j.jhep.2023.07.013_bib69","doi-asserted-by":"crossref","first-page":"1009","DOI":"10.1016\/j.jacc.2017.12.054","article-title":"Clinical outcomes in adolescents and adults after the fontan procedure","volume":"71","author":"Dennis","year":"2018","journal-title":"J\u00a0Am Coll Cardiol"},{"issue":"9","key":"10.1016\/j.jhep.2023.07.013_bib70","doi-asserted-by":"crossref","first-page":"520","DOI":"10.1038\/nrcardio.2010.99","article-title":"Four decades of Fontan palliation","volume":"7","author":"de Leval","year":"2010","journal-title":"Nat Rev Cardiol"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib71","doi-asserted-by":"crossref","first-page":"243","DOI":"10.1016\/j.jtcvs.2017.01.056","article-title":"Long-term survival after the Fontan operation: twenty years of experience at a single center","volume":"154","author":"Downing","year":"2017","journal-title":"J\u00a0Thorac Cardiovasc Surg"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib72","doi-asserted-by":"crossref","first-page":"1240","DOI":"10.1016\/j.athoracsur.2017.10.047","article-title":"Fontan failure and death in contemporary fontan circulation: analysis from the last two decades","volume":"105","author":"Kotani","year":"2018","journal-title":"Ann Thorac Surg"},{"issue":"5","key":"10.1016\/j.jhep.2023.07.013_bib73","doi-asserted-by":"crossref","first-page":"1520","DOI":"10.1161\/01.CIR.81.5.1520","article-title":"Outcome after a \"perfect\" Fontan operation","volume":"81","author":"Fontan","year":"1990","journal-title":"Circulation"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib74","doi-asserted-by":"crossref","first-page":"117","DOI":"10.1111\/chd.12201","article-title":"Increasing mortality burden among adults with complex congenital heart disease","volume":"10","author":"Greutmann","year":"2015","journal-title":"Congenit Heart Dis"},{"issue":"22","key":"10.1016\/j.jhep.2023.07.013_bib75","doi-asserted-by":"crossref","first-page":"2118","DOI":"10.1161\/CIRCULATIONAHA.115.017202","article-title":"Survival prospects and circumstances of death in contemporary adult congenital heart disease patients under follow-up at a large tertiary centre","volume":"132","author":"Diller","year":"2015","journal-title":"Circulation"},{"issue":"22","key":"10.1016\/j.jhep.2023.07.013_bib76","doi-asserted-by":"crossref","first-page":"2735","DOI":"10.1016\/j.jacc.2017.03.582","article-title":"Pediatric heart network investigators. Longitudinal outcomes of patients with single ventricle after the fontan procedure","volume":"69","author":"Atz","year":"2017","journal-title":"J\u00a0Am Coll Cardiol"},{"issue":"5","key":"10.1016\/j.jhep.2023.07.013_bib77","doi-asserted-by":"crossref","first-page":"757","DOI":"10.1016\/S0022-5223(19)39097-X","article-title":"Liver fibrosis (cardiac cirrhosis) five years after modified Fontan operation for tricuspid atresia","volume":"86","author":"Lemmer","year":"1983","journal-title":"J\u00a0Thorac Cardiovasc Surg"},{"issue":"21","key":"10.1016\/j.jhep.2023.07.013_bib78","doi-asserted-by":"crossref","first-page":"1750","DOI":"10.1136\/hrt.2010.201772","article-title":"Late hepatic complications after Fontan operation; non-invasive markers of hepatic fibrosis and risk factors","volume":"96","author":"Baek","year":"2010","journal-title":"Heart"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib79","doi-asserted-by":"crossref","first-page":"177","DOI":"10.1016\/j.athoracsur.2008.03.077","article-title":"Liver and cardiac function in the long term after Fontan operation","volume":"86","author":"Camposilvan","year":"2008","journal-title":"Ann Thorac Surg"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib80","doi-asserted-by":"crossref","first-page":"656","DOI":"10.1016\/j.jtcvs.2016.10.060","article-title":"Alliance for adult research in congenital Cardiology (AARCC) investigators. Liver health in adults with fontan circulation: a multicenter cross-sectional study","volume":"153","author":"Wu","year":"2017","journal-title":"J\u00a0Thorac Cardiovasc Surg"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib81","doi-asserted-by":"crossref","first-page":"211","DOI":"10.1016\/j.healun.2016.07.011","article-title":"Alliance for adult research in congenital Cardiology (AARCC) investigators. Predictive value of biomarkers of hepatic fibrosis in adult fontan patients","volume":"36","author":"Wu","year":"2017","journal-title":"J\u00a0Heart Lung Transpl"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib82","doi-asserted-by":"crossref","first-page":"19","DOI":"10.1067\/j.cpradiol.2017.04.002","article-title":"Abdominal imaging surveillance in adult patients after fontan procedure: risk of chronic liver disease and hepatocellular carcinoma","volume":"47","author":"Nandwana","year":"2018","journal-title":"Curr Probl Diagn Radiol"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib83","doi-asserted-by":"crossref","first-page":"3764","DOI":"10.1016\/j.ijcard.2013.06.008","article-title":"Features of portal hypertension are associated with major adverse events in Fontan patients: the VAST study","volume":"168","author":"Elder","year":"2013","journal-title":"Int J Cardiol"},{"key":"10.1016\/j.jhep.2023.07.013_bib84","doi-asserted-by":"crossref","first-page":"100","DOI":"10.1016\/j.ijcard.2018.07.118","article-title":"Australian and New Zealand Fontan Registry. Hepatic and renal end-organ damage in the Fontan circulation: a report from the Australian and New Zealand Fontan Registry","volume":"273","author":"Wilson","year":"2018","journal-title":"Int J Cardiol"},{"issue":"5","key":"10.1016\/j.jhep.2023.07.013_bib85","article-title":"Hepatic fibrosis is universal following fontan operation, and severity is associated with time from surgery: a liver biopsy and hemodynamic study","volume":"6","author":"Goldberg","year":"2017","journal-title":"J\u00a0Am Heart Assoc"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib86","doi-asserted-by":"crossref","first-page":"140","DOI":"10.1016\/j.jtcvs.2012.09.005","article-title":"Identifying predictors of hepatic disease in patients after the Fontan operation: a postmortem analysis","volume":"146","author":"Johnson","year":"2013","journal-title":"J\u00a0Thorac Cardiovasc Surg"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib87","doi-asserted-by":"crossref","first-page":"904","DOI":"10.1016\/j.jtcvs.2011.08.038","article-title":"Hepatic pathology may develop before the Fontan operation in children with functional single ventricle: an autopsy study","volume":"143","author":"Schwartz","year":"2012","journal-title":"J\u00a0Thorac Cardiovasc Surg"},{"issue":"5","key":"10.1016\/j.jhep.2023.07.013_bib88","doi-asserted-by":"crossref","first-page":"1300","DOI":"10.1002\/hep.32406","article-title":"Fontan-associated liver disease","volume":"75","author":"Hilscher","year":"2022","journal-title":"Hepatology"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib89","doi-asserted-by":"crossref","first-page":"504","DOI":"10.1136\/jcp.2007.052365","article-title":"Hepatic fibrosis and cirrhosis in the Fontan circulation: a detailed morphological study","volume":"61","author":"Kendall","year":"2008","journal-title":"J\u00a0Clin Pathol"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib90","doi-asserted-by":"crossref","first-page":"648","DOI":"10.1002\/hep.27387","article-title":"Chronic passive venous congestion drives hepatic fibrogenesis via sinusoidal thrombosis and mechanical forces","volume":"61","author":"Simonetto","year":"2015","journal-title":"Hepatology"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib91","doi-asserted-by":"crossref","first-page":"193","DOI":"10.1053\/j.gastro.2019.03.013","article-title":"Mechanical stretch increases expression of CXCL1 in liver sinusoidal endothelial cells to recruit neutrophils, generate sinusoidal microthombi, and promote portal hypertension","volume":"157","author":"Hilscher","year":"2019","journal-title":"Gastroenterology"},{"issue":"5","key":"10.1016\/j.jhep.2023.07.013_bib92","doi-asserted-by":"crossref","first-page":"262","DOI":"10.1038\/s41575-019-0146-6","article-title":"LSEC stretch promotes fibrosis during hepatic vascular congestion","volume":"16","author":"Thomas","year":"2019","journal-title":"Nat Rev Gastroenterol Hepatol"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib93","doi-asserted-by":"crossref","first-page":"319","DOI":"10.3350\/cmh.2015.21.4.319","article-title":"Nitric oxide in liver fibrosis: the role of inducible nitric oxide synthase","volume":"21","author":"Iwakiri","year":"2015","journal-title":"Clin Mol Hepatol"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib94","doi-asserted-by":"crossref","first-page":"1481","DOI":"10.1016\/j.jtcvs.2013.11.060","article-title":"Fontan hemodynamics from 100 patient-specific cardiac magnetic resonance studies: a computational fluid dynamics analysis","volume":"148","author":"Haggerty","year":"2014","journal-title":"J\u00a0Thorac Cardiovasc Surg"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib95","first-page":"223","article-title":"Fontan-associated liver disease: a review","volume":"74","author":"Gordon-Walker","year":"2019","journal-title":"J\u00a0Cardiol"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib96","doi-asserted-by":"crossref","first-page":"158","DOI":"10.1097\/MOG.0000000000000355","article-title":"Current concepts in ischemic hepatitis","volume":"33","author":"Lightsey","year":"2017","journal-title":"Curr Opin Gastroenterol"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib97","doi-asserted-by":"crossref","DOI":"10.1371\/journal.pone.0173149","article-title":"Diminished liver microperfusion in Fontan patients: a biexponential DWI study","volume":"12","author":"Dijkstra","year":"2017","journal-title":"PLoS One"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib98","doi-asserted-by":"crossref","first-page":"785","DOI":"10.1016\/S0735-1097(96)00568-2","article-title":"Cardiorespiratory response to exercise after modified Fontan operation: determinants of performance","volume":"29","author":"Durongpisitkul","year":"1997","journal-title":"J\u00a0Am Coll Cardiol"},{"key":"10.1016\/j.jhep.2023.07.013_bib99","doi-asserted-by":"crossref","DOI":"10.3389\/fped.2022.713219","article-title":"Pulmonary arteriovenous fistulae after fontan operation: incidence, clinical characteristics, and impact on all-cause mortality","volume":"10","author":"Ohuchi","year":"2022","journal-title":"Front Pediatr"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib100","doi-asserted-by":"crossref","DOI":"10.1136\/openhrt-2020-001460","article-title":"Cross-sectional assessment of haemostatic profile and hepatic dysfunction in Fontan patients","volume":"8","author":"Daems","year":"2021","journal-title":"Open Heart"},{"issue":"24","key":"10.1016\/j.jhep.2023.07.013_bib101","first-page":"5976","article-title":"Properties of plasma clots in adult patients following fontan procedure: relation to clot permeability and lysis time-multicenter study","volume":"10","author":"Skubera","year":"2021","journal-title":"J\u00a0Clin Med"},{"issue":"22","key":"10.1016\/j.jhep.2023.07.013_bib102","article-title":"UNIVERSE study investigators \u2217. Thromboprophylaxis for children post-fontan procedure: insights from the UNIVERSE study","volume":"10","author":"McCrindle","year":"2021","journal-title":"J\u00a0Am Heart Assoc"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib103","doi-asserted-by":"crossref","first-page":"1284","DOI":"10.1016\/j.jtcvs.2013.06.011","article-title":"Abnormalities in blood coagulation, fibrinolysis, and platelet activation in adult patients after the Fontan procedure","volume":"147","author":"Tomkiewicz-Pajak","year":"2014","journal-title":"J\u00a0Thorac Cardiovasc Surg"},{"issue":"5","key":"10.1016\/j.jhep.2023.07.013_bib104","doi-asserted-by":"crossref","first-page":"866","DOI":"10.1016\/j.ejcts.2007.01.033","article-title":"Coagulation abnormalities and liver function after hemi-Fontan and Fontan procedures - the importance of hemodynamics in the early postoperative period","volume":"31","author":"Procelewska","year":"2007","journal-title":"Eur J Cardiothorac Surg"},{"issue":"5","key":"10.1016\/j.jhep.2023.07.013_bib105","doi-asserted-by":"crossref","first-page":"678","DOI":"10.1055\/s-0037-1613891","article-title":"Hemostatic changes following the modified Fontan operation (total cavopulmonary connection)","volume":"83","author":"Rauch","year":"2000","journal-title":"Thromb Haemost"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib106","doi-asserted-by":"crossref","first-page":"206","DOI":"10.1016\/j.jhep.2022.01.025","article-title":"Hepatic lymphatic vascular system in health and disease","volume":"77","author":"Jeong","year":"2022","journal-title":"J\u00a0Hepatol"},{"key":"10.1016\/j.jhep.2023.07.013_bib107","doi-asserted-by":"crossref","first-page":"137","DOI":"10.1016\/j.coi.2018.04.028","article-title":"Lymphatics in the liver","volume":"53","author":"Tanaka","year":"2018","journal-title":"Curr Opin Immunol"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib108","doi-asserted-by":"crossref","DOI":"10.1136\/openhrt-2020-001434","article-title":"Myocardial fibrosis, diastolic dysfunction and elevated liver stiffness in the Fontan circulation","volume":"7","author":"Alsaied","year":"2020","journal-title":"Open Heart"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib109","doi-asserted-by":"crossref","first-page":"638","DOI":"10.1111\/liv.14375","article-title":"Fontan protein-losing enteropathy is associated with advanced liver disease and a proinflammatory intestinal and systemic state","volume":"40","author":"Rodr\u00edguez de Santiago","year":"2020","journal-title":"Liver Int"},{"issue":"8","key":"10.1016\/j.jhep.2023.07.013_bib110","doi-asserted-by":"crossref","first-page":"1307","DOI":"10.1016\/j.amjcard.2007.05.059","article-title":"Prevalence of hepatitis C infection in adult patients who underwent congenital heart surgery prior to screening in 1992","volume":"100","author":"Wang","year":"2007","journal-title":"Am J Cardiol"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib111","doi-asserted-by":"crossref","first-page":"503","DOI":"10.1177\/2150135114547587","article-title":"Outcomes of a hepatitis C screening protocol in at-risk adults with prior cardiac surgery","volume":"5","author":"Cox","year":"2014","journal-title":"World J Pediatr Congenit Heart Surg"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib112","doi-asserted-by":"crossref","first-page":"325","DOI":"10.1002\/hep.24627","article-title":"Amiodarone hepatotoxicity","volume":"55","author":"Sung","year":"2012","journal-title":"Hepatology"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib113","doi-asserted-by":"crossref","first-page":"736","DOI":"10.1007\/s00246-020-02291-5","article-title":"Severity of fontan-associated liver disease correlates with fontan hemodynamics","volume":"41","author":"Schleiger","year":"2020","journal-title":"Pediatr Cardiol"},{"key":"10.1016\/j.jhep.2023.07.013_bib114","doi-asserted-by":"crossref","DOI":"10.3389\/fcvm.2022.952080","article-title":"Functional hepatic deterioration determined by 13C-methacetin breath test is associated with impaired hemodynamics and late Fontan failure in adults","volume":"9","author":"Schleiger","year":"2022","journal-title":"Front Cardiovasc Med"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib115","doi-asserted-by":"crossref","first-page":"642","DOI":"10.1053\/j.semtcvs.2021.04.005","article-title":"Surveillance of fontan associated liver disease in childhood and adolescence","volume":"34","author":"Hansen","year":"2022","journal-title":"Semin Thorac Cardiovasc Surg"},{"issue":"7","key":"10.1016\/j.jhep.2023.07.013_bib116","doi-asserted-by":"crossref","first-page":"1805","DOI":"10.3390\/cancers12071805","article-title":"Risk of liver cirrhosis and hepatocellular carcinoma after fontan operation: a need for surveillance","volume":"12","author":"Yoon","year":"2020","journal-title":"Cancers (Basel)"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib117","doi-asserted-by":"crossref","first-page":"153","DOI":"10.1111\/chd.12422","article-title":"Serial cardiac MRIs in adult Fontan patients detect progressive hepatic enlargement and congestion","volume":"12","author":"Lewis","year":"2017","journal-title":"Congenit Heart Dis"},{"key":"10.1016\/j.jhep.2023.07.013_bib118","doi-asserted-by":"crossref","first-page":"60","DOI":"10.1016\/j.ijcard.2016.02.041","article-title":"Fontan circulation causes early, severe liver damage. Should we offer\u00a0patients a tailored strategy?","volume":"209","author":"Agnoletti","year":"2016","journal-title":"Int J Cardiol"},{"issue":"5","key":"10.1016\/j.jhep.2023.07.013_bib119","doi-asserted-by":"crossref","first-page":"579","DOI":"10.1136\/hrt.2006.094516","article-title":"Hepatic changes in the failing Fontan circulation","volume":"93","author":"Kiesewetter","year":"2007","journal-title":"Heart"},{"key":"10.1016\/j.jhep.2023.07.013_bib120","doi-asserted-by":"crossref","first-page":"106","DOI":"10.1016\/j.humpath.2016.07.006","article-title":"Prevalence and characterization of fibrosis in surveillance liver biopsies of patients with Fontan circulation","volume":"57","author":"Surrey","year":"2016","journal-title":"Hum Pathol"},{"issue":"6","key":"10.1016\/j.jhep.2023.07.013_bib121","doi-asserted-by":"crossref","first-page":"1348","DOI":"10.1016\/j.jtcvs.2004.10.005","article-title":"Progression of liver pathology in patients undergoing the Fontan procedure: chronic passive congestion, cardiac cirrhosis, hepatic adenoma, and hepatocellular carcinoma","volume":"129","author":"Ghaferi","year":"2005","journal-title":"J\u00a0Thorac Cardiovasc Surg"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib122","doi-asserted-by":"crossref","first-page":"456","DOI":"10.1016\/j.amjcard.2015.11.014","article-title":"Liver disease in patients after the fontan operation","volume":"117","author":"Pundi","year":"2016","journal-title":"Am J Cardiol"},{"key":"10.1016\/j.jhep.2023.07.013_bib123","doi-asserted-by":"crossref","first-page":"38","DOI":"10.1016\/j.ijcard.2022.06.037","article-title":"Older age at Fontan completion is associated with reduced lung volumes and increased lung reactance","volume":"364","author":"Laohachai","year":"2022","journal-title":"Int J Cardiol"},{"issue":"11","key":"10.1016\/j.jhep.2023.07.013_bib124","doi-asserted-by":"crossref","first-page":"3520","DOI":"10.1111\/jocs.16880","article-title":"Hepatic fibrosis gender differences in extracardiac Fontan patients","volume":"37","author":"Evans","year":"2022","journal-title":"J\u00a0Card Surg"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib125","doi-asserted-by":"crossref","first-page":"168","DOI":"10.1177\/2150135120969388","article-title":"Fontan-associated anatomical variants and hepatic fibrosis","volume":"12","author":"Evans","year":"2021","journal-title":"World J Pediatr Congenit Heart Surg"},{"issue":"5","key":"10.1016\/j.jhep.2023.07.013_bib126","doi-asserted-by":"crossref","first-page":"905","DOI":"10.1007\/s00246-020-02331-0","article-title":"The rate of hepatic fibrosis progression in patients post-fontan","volume":"41","author":"Evans","year":"2020","journal-title":"Pediatr Cardiol"},{"issue":"11","key":"10.1016\/j.jhep.2023.07.013_bib127","doi-asserted-by":"crossref","first-page":"2974","DOI":"10.1111\/jocs.14951","article-title":"Fontan venovenous collaterals and hepatic fibrosis","volume":"35","author":"Evans","year":"2020","journal-title":"J\u00a0Card Surg"},{"issue":"6","key":"10.1016\/j.jhep.2023.07.013_bib128","doi-asserted-by":"crossref","first-page":"589","DOI":"10.1111\/chd.12345","article-title":"Catheter-measured hemodynamics of adult fontan circulation: associations with adverse event and end-organ dysfunctions","volume":"11","author":"Mori","year":"2016","journal-title":"Congenit Heart Dis"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib129","doi-asserted-by":"crossref","first-page":"600","DOI":"10.1111\/chd.12770","article-title":"Evaluation of Fontan liver disease: correlation of transjugular liver biopsy with magnetic resonance and hemodynamics","volume":"14","author":"Silva-Sepulveda","year":"2019","journal-title":"Congenit Heart Dis"},{"key":"10.1016\/j.jhep.2023.07.013_bib130","article-title":"Predictors of liver cirrhosis and hepatocellular carcinoma among perioperative survivors of the Fontan operation","author":"Inuzuka","year":"2022","journal-title":"Heart"},{"issue":"22","key":"10.1016\/j.jhep.2023.07.013_bib131","first-page":"924","article-title":"Liver cirrhosis after the fontan procedure: impact of atrioventricular valve failure","volume":"S0003\u20134975","author":"Wilson","year":"2022","journal-title":"Ann Thorac Surg"},{"issue":"12","key":"10.1016\/j.jhep.2023.07.013_bib132","doi-asserted-by":"crossref","first-page":"1552","DOI":"10.1038\/modpathol.2014.79","article-title":"Congestive hepatic fibrosis score: a novel histologic assessment of clinical severity","volume":"27","author":"Dai","year":"2014","journal-title":"Mod Pathol"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib133","doi-asserted-by":"crossref","first-page":"393","DOI":"10.1053\/jhep.2003.50062","article-title":"Cardiac hepatopathy: clinical, hemodynamic, and histologic characteristics and correlations","volume":"37","author":"Myers","year":"2003","journal-title":"Hepatology"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib134","first-page":"159","article-title":"Hepatic morphology in cardiac dysfunction: a clinicopathologic study of 1000 subjects at autopsy","volume":"104","author":"Arcidi","year":"1981","journal-title":"Am J Pathol"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib135","doi-asserted-by":"crossref","first-page":"313","DOI":"10.1016\/S0168-8278(86)80043-5","article-title":"Morphologic features of hepatic injury in cardiac disease and shock","volume":"2","author":"Lefkowitch","year":"1986","journal-title":"J\u00a0Hepatol"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib136","doi-asserted-by":"crossref","first-page":"135","DOI":"10.1007\/s00246-012-0402-9","article-title":"Portal and sinusoidal fibrosis are common on liver biopsy after Fontan surgery","volume":"34","author":"Schwartz","year":"2013","journal-title":"Pediatr Cardiol"},{"issue":"7","key":"10.1016\/j.jhep.2023.07.013_bib137","doi-asserted-by":"crossref","first-page":"883","DOI":"10.1016\/j.healun.2015.01.993","article-title":"Portal and centrilobular hepatic fibrosis in Fontan circulation and clinical outcomes","volume":"34","author":"Wu","year":"2015","journal-title":"J\u00a0Heart Lung Transpl"},{"key":"10.1016\/j.jhep.2023.07.013_bib138","doi-asserted-by":"crossref","first-page":"141","DOI":"10.1016\/j.humpath.2017.04.029","article-title":"Defining the role of liver biopsy in the assessment of liver fibrosis in patients with Fontan circulation-reply","volume":"69","author":"Surrey","year":"2017","journal-title":"Hum Pathol"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib139","doi-asserted-by":"crossref","first-page":"380","DOI":"10.1111\/chd.12730","article-title":"Focal liver lesions following Fontan palliation of single ventricle physiology: a radiology-pathology case series","volume":"14","author":"Engelhardt","year":"2019","journal-title":"Congenit Heart Dis"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib140","doi-asserted-by":"crossref","first-page":"205","DOI":"10.1097\/PAS.0000000000000099","article-title":"Aberrant centrizonal features in chronic hepatic venous outflow obstruction: centrilobular mimicry of portal-based disease","volume":"38","author":"Krings","year":"2014","journal-title":"Am J Surg Pathol"},{"issue":"13","key":"10.1016\/j.jhep.2023.07.013_bib141","doi-asserted-by":"crossref","first-page":"1057","DOI":"10.1093\/eurheartj\/ehy620","article-title":"The clinical spectrum of Fontan-associated liver disease: results from a prospective multimodality screening cohort","volume":"40","author":"Munsterman","year":"2019","journal-title":"Eur Heart J"},{"issue":"7","key":"10.1016\/j.jhep.2023.07.013_bib142","doi-asserted-by":"crossref","first-page":"932","DOI":"10.1038\/modpathol.2015.40","article-title":"The liver in heart failure: a biopsy and explant series of the histopathologic and laboratory findings with a particular focus on pre-cardiac transplant evaluation","volume":"28","author":"Louie","year":"2015","journal-title":"Mod Pathol"},{"issue":"13","key":"10.1016\/j.jhep.2023.07.013_bib143","doi-asserted-by":"crossref","first-page":"2598","DOI":"10.1007\/s00247-021-05173-x","article-title":"Surveillance of fontan-associated liver disease: current standards and a proposal from the European society of paediatric radiology abdominal task force","volume":"51","author":"Perucca","year":"2021","journal-title":"Pediatr Radiol"},{"issue":"13","key":"10.1016\/j.jhep.2023.07.013_bib144","doi-asserted-by":"crossref","first-page":"2607","DOI":"10.1007\/s00247-021-05172-y","article-title":"Radiologic follow-up in Fontan-associated liver disease in Europe: European Society of Paediatric Radiology survey demonstrates the need for a consensus protocol","volume":"51","author":"Perucca","year":"2021","journal-title":"Pediatr Radiol"},{"issue":"12","key":"10.1016\/j.jhep.2023.07.013_bib145","doi-asserted-by":"crossref","DOI":"10.1111\/ctr.14120","article-title":"Does liver biopsy accurately measure fibrosis in Fontan-associated liver disease? A comparison of liver biopsy pre-combined heart and liver transplant and liver explant post-transplant","volume":"34","author":"Vaikunth","year":"2020","journal-title":"Clin Transpl"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib146","doi-asserted-by":"crossref","first-page":"135","DOI":"10.1093\/ejcts\/ezw243","article-title":"Impact of mode of failure and end-organ dysfunction on the survival of adult Fontan patients undergoing cardiac transplantation","volume":"51","author":"Murtuza","year":"2017","journal-title":"Eur J Cardiothorac Surg"},{"key":"10.1016\/j.jhep.2023.07.013_bib147","doi-asserted-by":"crossref","first-page":"140","DOI":"10.1016\/j.humpath.2017.04.028","article-title":"Defining the role of liver biopsy in the assessment of liver fibrosis in patients with Fontan circulation","volume":"69","author":"Haugk","year":"2017","journal-title":"Hum Pathol"},{"issue":"7","key":"10.1016\/j.jhep.2023.07.013_bib148","doi-asserted-by":"crossref","first-page":"1001","DOI":"10.1007\/s00246-012-0315-7","article-title":"The precarious state of the liver after a Fontan operation: summary of a multidisciplinary symposium","volume":"33","author":"Rychik","year":"2012","journal-title":"Pediatr Cardiol"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib149","doi-asserted-by":"crossref","first-page":"110","DOI":"10.1007\/s00246-018-1966-9","article-title":"Surveillance testing and preventive care after fontan operation: a multi-institutional survey","volume":"40","author":"Di Maria","year":"2019","journal-title":"Pediatr Cardiol"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib150","doi-asserted-by":"crossref","first-page":"538","DOI":"10.1055\/s-0041-1732355","article-title":"Fontan-associated liver disease: pathophysiology, staging, and management","volume":"41","author":"T\u00e9llez","year":"2021","journal-title":"Semin Liver Dis"},{"key":"10.1016\/j.jhep.2023.07.013_bib151","doi-asserted-by":"crossref","first-page":"83","DOI":"10.1016\/j.ijcard.2020.11.037","article-title":"Transjugular liver biopsy for Fontan associated liver disease surveillance: technique, outcomes and hemodynamic correlation","volume":"328","author":"Borquez","year":"2021","journal-title":"Int J Cardiol"},{"issue":"6","key":"10.1016\/j.jhep.2023.07.013_bib152","doi-asserted-by":"crossref","first-page":"1449","DOI":"10.1016\/j.hep.2003.09.022","article-title":"Sampling variability of liver fibrosis in chronic hepatitis C","volume":"38","author":"Bedossa","year":"2003","journal-title":"Hepatology"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib153","doi-asserted-by":"crossref","first-page":"342","DOI":"10.1007\/s00247-018-4311-9","article-title":"Percutaneous liver biopsy in Fontan patients","volume":"49","author":"Srinivasan","year":"2019","journal-title":"Pediatr Radiol"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib154","doi-asserted-by":"crossref","first-page":"124","DOI":"10.1111\/chd.12446","article-title":"Surveillance for liver complications after the Fontan procedure","volume":"12","author":"Hilscher","year":"2017","journal-title":"Congenit Heart Dis"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib155","doi-asserted-by":"crossref","first-page":"959","DOI":"10.1016\/j.jhep.2021.12.022","article-title":"Baveno VII - renewing consensus in portal hypertension","volume":"76","author":"de Franchis","year":"2022","journal-title":"J\u00a0Hepatol"},{"issue":"5","key":"10.1016\/j.jhep.2023.07.013_bib156","doi-asserted-by":"crossref","first-page":"360","DOI":"10.1016\/j.cjco.2020.04.011","article-title":"Hepatic venous pressure gradient in fontan physiology has limited diagnostic and prognostic significance","volume":"2","author":"Egbe","year":"2020","journal-title":"CJC Open"},{"issue":"5","key":"10.1016\/j.jhep.2023.07.013_bib157","doi-asserted-by":"crossref","first-page":"593","DOI":"10.1111\/hepr.13627","article-title":"Assessing liver stiffness with conventional cut-off values overestimates liver fibrosis staging in patients who received the Fontan procedure","volume":"51","author":"Cho","year":"2021","journal-title":"Hepatol Res"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib158","doi-asserted-by":"crossref","first-page":"436","DOI":"10.1067\/mtc.2001.112527","article-title":"Subdiaphragmatic venous hemodynamics in the Fontan circulation","volume":"121","author":"Hsia","year":"2001","journal-title":"J\u00a0Thorac Cardiovasc Surg"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib159","doi-asserted-by":"crossref","first-page":"230","DOI":"10.1017\/S104795112100175X","article-title":"Developing an adolescent and adult fontan management programme","volume":"32","author":"Lubert","year":"2022","journal-title":"Cardiol Young"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib160","doi-asserted-by":"crossref","first-page":"98","DOI":"10.1007\/s00059-013-3811-5","article-title":"Serial evaluation of hepatic function profile after Fontan operation","volume":"39","author":"Kaulitz","year":"2014","journal-title":"Herz"},{"issue":"6","key":"10.1016\/j.jhep.2023.07.013_bib161","article-title":"Non-invasive biomarkers of Fontan-associated liver disease","volume":"3","author":"Emamaullee","year":"2021","journal-title":"JHEP Rep"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib162","first-page":"181","article-title":"Noninvasive assessment of liver status in adult patients after the Fontan procedure","volume":"129","author":"Sma\u015b-Suska","year":"2019","journal-title":"Pol Arch Intern Med"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib163","doi-asserted-by":"crossref","first-page":"557","DOI":"10.1148\/radiol.211037","article-title":"Abdominal CT and MRI findings of portal hypertension in children and adults with fontan circulation","volume":"303","author":"Zafar","year":"2022","journal-title":"Radiology"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib164","article-title":"From congestive hepatopathy to hepatocellular carcinoma, how can we improve patient management?","volume":"3","author":"Sessa","year":"2021","journal-title":"JHEP Rep"},{"key":"10.1016\/j.jhep.2023.07.013_bib165","doi-asserted-by":"crossref","first-page":"142","DOI":"10.1016\/j.ahj.2019.04.018","article-title":"Creatinine versus cystatin C to estimate glomerular filtration rate in adults with congenital heart disease: results of the Boston Adult Congenital Heart Disease Biobank","volume":"214","author":"Opotowsky","year":"2019","journal-title":"Am Heart J"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib166","first-page":"363","article-title":"Protein-losing enteropathy: integrating a new disease paradigm into recommendations for prevention and treatment","volume":"21","author":"Meadows","year":"2011","journal-title":"Cardiol\u00a0Young"},{"key":"10.1016\/j.jhep.2023.07.013_bib167","doi-asserted-by":"crossref","first-page":"21","DOI":"10.1016\/j.ppedcard.2018.09.004","article-title":"Pediatric fontan associated liver disease: non-invasive evaluation with serologic markers and acoustic radiation force impulse (ARFI) elastography","volume":"53","author":"Ofei","year":"2019","journal-title":"Prog Pediatr Cardiol"},{"issue":"5","key":"10.1016\/j.jhep.2023.07.013_bib168","doi-asserted-by":"crossref","first-page":"765","DOI":"10.1111\/chd.12820","article-title":"More than the heart: hepatic, renal, and cardiac dysfunction in adult Fontan patients","volume":"14","author":"Byrne","year":"2019","journal-title":"Congenit Heart Dis"},{"key":"10.1016\/j.jhep.2023.07.013_bib169","doi-asserted-by":"crossref","first-page":"64","DOI":"10.1016\/j.ijcard.2020.08.009","article-title":"Early development of hepatic fibrosis after Fontan procedure: a non-invasive study of a subclinical liver disease","volume":"320","author":"An","year":"2020","journal-title":"Int J Cardiol"},{"issue":"8","key":"10.1016\/j.jhep.2023.07.013_bib170","doi-asserted-by":"crossref","first-page":"1604","DOI":"10.1007\/s00246-018-1937-1","article-title":"Hepatic changes in the fontan circulation: identification of liver dysfunction and an attempt to streamline follow-up screening","volume":"39","author":"Ackerman","year":"2018","journal-title":"Pediatr Cardiol"},{"issue":"8","key":"10.1016\/j.jhep.2023.07.013_bib171","doi-asserted-by":"crossref","first-page":"1639","DOI":"10.1007\/s00246-020-02422-y","article-title":"Associated factors of liver disease after fontan operation in relation to ultrasound liver elastography","volume":"41","author":"Sethasathien","year":"2020","journal-title":"Pediatr Cardiol"},{"issue":"9","key":"10.1016\/j.jhep.2023.07.013_bib172","doi-asserted-by":"crossref","first-page":"1514","DOI":"10.1007\/s00380-015-0743-4","article-title":"Risk factors and serological markers of liver cirrhosis after Fontan procedure","volume":"31","author":"Shimizu","year":"2016","journal-title":"Heart Vessels"},{"issue":"7","key":"10.1016\/j.jhep.2023.07.013_bib173","doi-asserted-by":"crossref","first-page":"1274","DOI":"10.1007\/s00246-016-1428-1","article-title":"MELD-XI scores correlate with post-fontan hepatic biopsy fibrosis scores","volume":"37","author":"Evans","year":"2016","journal-title":"Pediatr Cardiol"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib174","doi-asserted-by":"crossref","first-page":"77","DOI":"10.1016\/j.ijcard.2011.06.062","article-title":"Structural and functional uncoupling of liver performance in the Fontan circulation","volume":"164","author":"Guha","year":"2013","journal-title":"Int J Cardiol"},{"issue":"8","key":"10.1016\/j.jhep.2023.07.013_bib175","doi-asserted-by":"crossref","first-page":"1437","DOI":"10.1002\/hep4.1721","article-title":"Cluster of differentiation 44 promotes liver fibrosis and serves as a biomarker in congestive hepatopathy","volume":"5","author":"Osawa","year":"2021","journal-title":"Hepatol Commun"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib176","doi-asserted-by":"crossref","first-page":"330","DOI":"10.1007\/s00247-012-2531-y","article-title":"Hepatic pathology after Fontan palliation: spectrum of imaging findings","volume":"43","author":"Wallihan","year":"2013","journal-title":"Pediatr Radiol"},{"key":"10.1016\/j.jhep.2023.07.013_bib177","first-page":"1","article-title":"The prognostic role of liver volumetry in Fontan patients","author":"Najashi","year":"2022","journal-title":"Cardiol Young"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib178","doi-asserted-by":"crossref","first-page":"850","DOI":"10.1016\/j.ejrad.2016.02.002","article-title":"Fontan-associated liver disease: spectrum of US findings","volume":"85","author":"Bae","year":"2016","journal-title":"Eur J Radiol"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib179","doi-asserted-by":"crossref","first-page":"702","DOI":"10.1016\/j.jhep.2019.10.027","article-title":"VALDIG an EASL consortium. Prevalence, features and predictive factors of liver nodules in Fontan surgery patients: the VALDIG Fonliver prospective cohort","volume":"72","author":"T\u00e9llez","year":"2020","journal-title":"J\u00a0Hepatol"},{"issue":"7","key":"10.1016\/j.jhep.2023.07.013_bib180","doi-asserted-by":"crossref","first-page":"3205","DOI":"10.1007\/s00261-021-02994-0","article-title":"Spectrum of Fontan-associated liver disease assessed by MRI and US in young adolescents","volume":"46","author":"Thrane","year":"2021","journal-title":"Abdom Radiol (NY)"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib181","doi-asserted-by":"crossref","first-page":"159","DOI":"10.1007\/s00431-021-04163-3","article-title":"Non-invasive assessment of liver abnormalities in pediatric Fontan patients","volume":"181","author":"De Bruyne","year":"2022","journal-title":"Eur J Pediatr"},{"issue":"5","key":"10.1016\/j.jhep.2023.07.013_bib182","doi-asserted-by":"crossref","first-page":"1008","DOI":"10.1536\/ihj.17-349","article-title":"Imaging assessment of hepatic changes after fontan surgery","volume":"59","author":"Song","year":"2018","journal-title":"Int Heart J"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib183","doi-asserted-by":"crossref","first-page":"174","DOI":"10.1136\/heartjnl-2015-308298","article-title":"Role of imaging in the evaluation of single ventricle with the Fontan palliation","volume":"102","author":"Kutty","year":"2016","journal-title":"Heart"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib184","doi-asserted-by":"crossref","first-page":"167","DOI":"10.1007\/s00247-021-05053-4","article-title":"Liver magnetic resonance imaging: how we do it","volume":"52","author":"Chavhan","year":"2022","journal-title":"Pediatr Radiol"},{"key":"10.1016\/j.jhep.2023.07.013_bib185","doi-asserted-by":"crossref","first-page":"595","DOI":"10.1016\/j.ijcard.2015.09.088","article-title":"The Fontan circulation and the liver: a magnetic resonance diffusion-weighted imaging study","volume":"202","author":"Wolff","year":"2016","journal-title":"Int J Cardiol"},{"issue":"11","key":"10.1016\/j.jhep.2023.07.013_bib186","doi-asserted-by":"crossref","first-page":"1528","DOI":"10.1007\/s00247-020-04776-0","article-title":"Imaging of Fontan-associated liver disease","volume":"50","author":"Dillman","year":"2020","journal-title":"Pediatr Radiol"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib187","doi-asserted-by":"crossref","first-page":"483","DOI":"10.1007\/s00247-021-05221-6","article-title":"Semiquantitative characterization of dynamic magnetic resonance perfusion of the liver in pediatric Fontan patients","volume":"52","author":"Navallas","year":"2022","journal-title":"Pediatr Radiol"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib188","doi-asserted-by":"crossref","first-page":"357","DOI":"10.1007\/s13244-018-0609-2","article-title":"Abdominal imaging findings in adult patients with Fontan circulation","volume":"9","author":"Kim","year":"2018","journal-title":"Insights Imaging"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib189","doi-asserted-by":"crossref","first-page":"39","DOI":"10.1186\/s12968-019-0545-4","article-title":"Increased extracellular volume in the liver of pediatric Fontan patients","volume":"21","author":"de Lange","year":"2019","journal-title":"J\u00a0Cardiovasc Magn Reson"},{"issue":"7","key":"10.1016\/j.jhep.2023.07.013_bib190","doi-asserted-by":"crossref","first-page":"2403","DOI":"10.1007\/s00261-019-01990-9","article-title":"Assessment of liver T1 mapping in fontan patients and its correlation with magnetic resonance elastography-derived liver stiffness","volume":"44","author":"Ramachandran","year":"2019","journal-title":"Abdom Radiol (NY)"},{"issue":"10","key":"10.1016\/j.jhep.2023.07.013_bib191","doi-asserted-by":"crossref","first-page":"2679","DOI":"10.1007\/s00261-018-1528-x","article-title":"Using T1 mapping in cardiovascular magnetic resonance to assess congestive hepatopathy","volume":"43","author":"Kazour","year":"2018","journal-title":"Abdom Radiol (NY)"},{"issue":"6","key":"10.1016\/j.jhep.2023.07.013_bib192","doi-asserted-by":"crossref","first-page":"2434","DOI":"10.1007\/s00330-016-4614-x","article-title":"Effect of Fontan operation on liver stiffness in children with single ventricle physiology","volume":"27","author":"DiPaola","year":"2017","journal-title":"Eur Radiol"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib193","doi-asserted-by":"crossref","first-page":"513","DOI":"10.1093\/icvts\/ivw186","article-title":"Liver stiffness modifications shortly after total cavopulmonary connection","volume":"23","author":"Deorsola","year":"2016","journal-title":"Interact Cardiovasc Thorac Surg"},{"key":"10.1016\/j.jhep.2023.07.013_bib194","doi-asserted-by":"crossref","DOI":"10.1155\/2016\/7125193","article-title":"Assessment of liver stiffness in pediatric fontan patients using transient elastography","volume":"2016","author":"Chen","year":"2016","journal-title":"Can J Gastroenterol Hepatol"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib195","doi-asserted-by":"crossref","first-page":"251","DOI":"10.1002\/hep.26631","article-title":"Liver Adult-Pediatric-Congenital-Heart-Disease Dysfunction Study (LADS) Group. Increased hepatic stiffness as consequence of high hepatic afterload in the Fontan circulation: a vascular Doppler and elastography study","volume":"59","author":"Kutty","year":"2014","journal-title":"Hepatology"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib196","first-page":"202","article-title":"Non-invasive assessment of liver fibrosis by magnetic resonance elastography in patients with congenital heart disease undergoing the Fontan procedure and intracardiac repair","volume":"68","author":"Sugimoto","year":"2016","journal-title":"J\u00a0Cardiol"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib197","doi-asserted-by":"crossref","first-page":"365","DOI":"10.1177\/2150135114530172","article-title":"Fontan circulation in adult patients: acoustic radiation force impulse elastography as a useful tool for liver assessment","volume":"5","author":"Melero-Ferrer","year":"2014","journal-title":"World J Pediatr Congenit Heart Surg"},{"issue":"10","key":"10.1016\/j.jhep.2023.07.013_bib198","doi-asserted-by":"crossref","first-page":"1333","DOI":"10.1007\/s00247-020-04682-5","article-title":"Imaging of complications following Fontan circulation in children - diagnosis and surveillance","volume":"50","author":"de Lange","year":"2020","journal-title":"Pediatr Radiol"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib199","doi-asserted-by":"crossref","first-page":"824","DOI":"10.1148\/radiol.2018172099","article-title":"Diagnostic performance of MR elastography for liver fibrosis in children and young adults with a spectrum of liver diseases","volume":"287","author":"Trout","year":"2018","journal-title":"Radiology"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib200","doi-asserted-by":"crossref","first-page":"1498","DOI":"10.1016\/j.jtcvs.2014.04.010","article-title":"Congestive hepatopathy after Fontan operation and related factors assessed by transient elastography","volume":"148","author":"Yoo","year":"2014","journal-title":"J\u00a0Thorac Cardiovasc Surg"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib201","doi-asserted-by":"crossref","first-page":"38","DOI":"10.1111\/chd.12558","article-title":"A\u00a0composite noninvasive index correlates with liver fibrosis scores in post-Fontan patients: preliminary findings","volume":"13","author":"Evans","year":"2018","journal-title":"Congenit Heart Dis"},{"issue":"5","key":"10.1016\/j.jhep.2023.07.013_bib202","doi-asserted-by":"crossref","first-page":"764","DOI":"10.1111\/chd.12650","article-title":"FibroSURE and elastography poorly predict the severity of liver fibrosis in Fontan-associated liver disease","volume":"13","author":"Schachter","year":"2018","journal-title":"Congenit Heart Dis"},{"issue":"5","key":"10.1016\/j.jhep.2023.07.013_bib203","doi-asserted-by":"crossref","first-page":"438","DOI":"10.1111\/chd.12159","article-title":"Transient elastography may identify Fontan patients with unfavorable hemodynamics and advanced hepatic fibrosis","volume":"9","author":"Wu","year":"2014","journal-title":"Congenit Heart Dis"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib204","first-page":"217","article-title":"Fontan-associated liver disease: evidence for early surveillance of liver health in pediatric fontan patients","volume":"35","author":"Rathgeber","year":"2019","journal-title":"Can J Cardiol"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib205","doi-asserted-by":"crossref","first-page":"1176","DOI":"10.1016\/j.jtcvs.2021.12.028","article-title":"Noninvasive surrogates are poor predictors of liver fibrosis in patients with Fontan circulation","volume":"164","author":"Shin","year":"2022","journal-title":"J\u00a0Thorac Cardiovasc Surg"},{"issue":"7","key":"10.1016\/j.jhep.2023.07.013_bib206","doi-asserted-by":"crossref","first-page":"882","DOI":"10.1016\/j.mayocp.2015.04.020","article-title":"Magnetic resonance elastography: a novel technique for the detection of hepatic fibrosis and hepatocellular carcinoma after the fontan operation","volume":"90","author":"Poterucha","year":"2015","journal-title":"Mayo Clin Proc"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib207","article-title":"Fontan-associated liver disease: spectrum of disease in children and adolescents","volume":"9","author":"Rathgeber","year":"2020","journal-title":"J\u00a0Am Heart Assoc"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib208","doi-asserted-by":"crossref","first-page":"560","DOI":"10.1016\/j.jtcvs.2007.09.039","article-title":"Noninvasive assessment of liver fibrosis in patients with Fontan circulation using transient elastography and biochemical fibrosis markers","volume":"135","author":"Friedrich-Rust","year":"2008","journal-title":"J\u00a0Thorac Cardiovasc Surg"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib209","doi-asserted-by":"crossref","first-page":"7","DOI":"10.1111\/chd.12144","article-title":"Magnetic resonance elastography of the liver in patients status-post fontan procedure: feasibility and preliminary results","volume":"9","author":"Serai","year":"2014","journal-title":"Congenit Heart Dis"},{"issue":"10","key":"10.1016\/j.jhep.2023.07.013_bib210","first-page":"117","article-title":"Role of transient elastography to stage fontan-associated liver disease (FALD) in adults with single ventricle congenital heart disease correction","volume":"8","author":"Chemello","year":"2021","journal-title":"J\u00a0Cardiovasc Dev Dis"},{"issue":"9","key":"10.1016\/j.jhep.2023.07.013_bib211","doi-asserted-by":"crossref","first-page":"1454","DOI":"10.1016\/j.amjcard.2019.07.052","article-title":"Relation of magnetic resonance elastography to fontan failure and portal hypertension","volume":"124","author":"Alsaied","year":"2019","journal-title":"Am J Cardiol"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib212","doi-asserted-by":"crossref","first-page":"99","DOI":"10.1007\/s00247-018-4264-z","article-title":"MRI measured liver stiffness does not predict focal liver lesions after the Fontan operation","volume":"49","author":"Diaz","year":"2019","journal-title":"Pediatr Radiol"},{"key":"10.1016\/j.jhep.2023.07.013_bib213","doi-asserted-by":"crossref","first-page":"299","DOI":"10.1016\/j.ijcard.2018.01.108","article-title":"Temporal changes in liver stiffness after Fontan operation: results of serial magnetic resonance elastography","volume":"258","author":"Egbe","year":"2018","journal-title":"Int J Cardiol"},{"issue":"8","key":"10.1016\/j.jhep.2023.07.013_bib214","doi-asserted-by":"crossref","first-page":"1871","DOI":"10.1007\/s00246-021-02707-w","article-title":"Relation of magnetic resonance elastography to fontan circulatory failure in a cohort of pediatric and adult patients","volume":"42","author":"Brayer","year":"2021","journal-title":"Pediatr Cardiol"},{"issue":"6","key":"10.1016\/j.jhep.2023.07.013_bib215","doi-asserted-by":"crossref","first-page":"1328","DOI":"10.1002\/jmri.24496","article-title":"Relationship of MR elastography determined liver stiffness with cardiac function after Fontan palliation","volume":"40","author":"Wallihan","year":"2014","journal-title":"J\u00a0Magn Reson Imaging"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib216","doi-asserted-by":"crossref","first-page":"79","DOI":"10.1002\/jmri.22610","article-title":"Portal hypertension correlates with splenic stiffness as measured with MR elastography","volume":"34","author":"Nedredal","year":"2011","journal-title":"J\u00a0Magn Reson Imaging"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib217","doi-asserted-by":"crossref","first-page":"308","DOI":"10.1016\/j.jhep.2018.04.023","article-title":"A\u00a0combined model based on spleen stiffness measurement and Baveno VI criteria to rule out high-risk varices in advanced chronic liver disease","volume":"69","author":"Colecchia","year":"2018","journal-title":"J\u00a0Hepatol"},{"issue":"5","key":"10.1016\/j.jhep.2023.07.013_bib218","doi-asserted-by":"crossref","first-page":"1068","DOI":"10.1016\/j.jhep.2014.12.007","article-title":"Real-time shear-wave elastography: applicability, reliability and accuracy for clinically significant portal hypertension","volume":"62","author":"Procopet","year":"2015","journal-title":"J\u00a0Hepatol"},{"key":"10.1016\/j.jhep.2023.07.013_bib219","doi-asserted-by":"crossref","first-page":"147","DOI":"10.1016\/j.clinimag.2022.06.022","article-title":"Liver and spleen volume\u00a0and stiffness in patients post-Fontan procedure and patients with ARPKD compared to normal controls","volume":"89","author":"Serai","year":"2022","journal-title":"Clin Imaging"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib220","first-page":"30","article-title":"Prognostic value of liver and spleen stiffness in patients with fontan associated liver disease (FALD): a case series with histopathologic comparison","volume":"8","author":"Padalino","year":"2021","journal-title":"J\u00a0Cardiovasc Dev Dis"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib221","doi-asserted-by":"crossref","first-page":"350","DOI":"10.1097\/RUQ.0000000000000541","article-title":"Quantification of hepatic and splenic stiffness after fontan procedure in children and clinical implications","volume":"36","author":"Aliyev","year":"2020","journal-title":"Ultrasound Q"},{"key":"10.1016\/j.jhep.2023.07.013_bib222","doi-asserted-by":"crossref","first-page":"61","DOI":"10.1016\/j.ijcard.2020.09.047","article-title":"A\u00a0window into portal hemodynamics in adult fontan patients?","volume":"323","author":"Simmons","year":"2021","journal-title":"Int J Cardiol"},{"issue":"25","key":"10.1016\/j.jhep.2023.07.013_bib223","doi-asserted-by":"crossref","first-page":"3173","DOI":"10.1016\/j.jacc.2017.10.045","article-title":"Fontan-associated liver disease: proceedings from the American college of Cardiology stakeholders meeting, October 1 to 2, 2015, Washington DC","volume":"70","author":"Daniels","year":"2017","journal-title":"J\u00a0Am Coll Cardiol"},{"issue":"12","key":"10.1016\/j.jhep.2023.07.013_bib224","doi-asserted-by":"crossref","first-page":"1943","DOI":"10.1016\/j.amjcard.2013.08.023","article-title":"Hemodynamic phenotype of the failing Fontan in an adult population","volume":"112","author":"Hebson","year":"2013","journal-title":"Am J Cardiol"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib225","doi-asserted-by":"crossref","first-page":"615","DOI":"10.1159\/000510332","article-title":"An emphasis on screening to detect liver cirrhosis and hepatocellular carcinoma in patients having undergone the fontan procedure in early childhood","volume":"14","author":"Madala","year":"2020","journal-title":"Case Rep Gastroenterol"},{"issue":"7","key":"10.1016\/j.jhep.2023.07.013_bib226","doi-asserted-by":"crossref","first-page":"1727","DOI":"10.1016\/0735-1097(91)90511-7","article-title":"Early and late results of the modified Fontan procedure for double-inlet left ventricle: the Mayo Clinic experience","volume":"18","author":"Mair","year":"1991","journal-title":"J\u00a0Am Coll Cardiol"},{"key":"10.1016\/j.jhep.2023.07.013_bib227","series-title":"Portal hypertension VII","article-title":"Medical approach to fontan patients","author":"T\u00e9llez","year":"2022"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib228","doi-asserted-by":"crossref","first-page":"175","DOI":"10.1111\/j.1747-0803.2010.00451.x","article-title":"Direct measurement of porto-systemic gradient in a failing Fontan circulation","volume":"6","author":"Velpula","year":"2011","journal-title":"Congenit Heart Dis"},{"issue":"11","key":"10.1016\/j.jhep.2023.07.013_bib229","doi-asserted-by":"crossref","first-page":"51","DOI":"10.1007\/s11936-015-0412-z","article-title":"Fontan liver disease: review of an emerging epidemic and management options","volume":"17","author":"Bradley","year":"2015","journal-title":"Curr Treat Options Cardiovasc Med"},{"issue":"6","key":"10.1016\/j.jhep.2023.07.013_bib230","doi-asserted-by":"crossref","first-page":"803","DOI":"10.1002\/ejhf.1365","article-title":"Haemodynamic profiles in adult Fontan patients: associated haemodynamics and prognosis","volume":"21","author":"Miranda","year":"2019","journal-title":"Eur J Heart Fail"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib231","doi-asserted-by":"crossref","first-page":"215","DOI":"10.7326\/0003-4819-117-3-215","article-title":"The serum-ascites albumin gradient is superior to the exudate-transudate concept in the differential diagnosis of ascites","volume":"117","author":"Runyon","year":"1992","journal-title":"Ann Intern Med"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib232","doi-asserted-by":"crossref","first-page":"1160","DOI":"10.1002\/hep.25692","article-title":"Congenital heart disease and the liver","volume":"56","author":"Asrani","year":"2012","journal-title":"Hepatology"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib233","doi-asserted-by":"crossref","first-page":"1014","DOI":"10.1002\/hep.31884","article-title":"Diagnosis, evaluation, and management of ascites, spontaneous bacterial peritonitis and hepatorenal syndrome: 2021 practice guidance by the American association for the study of liver diseases","volume":"74","author":"Biggins","year":"2021","journal-title":"Hepatology"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib234","doi-asserted-by":"crossref","first-page":"410","DOI":"10.1097\/00004836-198808000-00013","article-title":"Cardiac ascites: a characterization","volume":"10","author":"Runyon","year":"1988","journal-title":"J\u00a0Clin Gastroenterol"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib235","doi-asserted-by":"crossref","first-page":"1043","DOI":"10.1002\/hep.26643","article-title":"Serum B-type natriuretic peptide in the initial workup of patients with new onset ascites: a diagnostic accuracy study","volume":"59","author":"Farias","year":"2014","journal-title":"Hepatology"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib236","doi-asserted-by":"crossref","first-page":"172","DOI":"10.1016\/j.jhep.2018.06.024","article-title":"Electronic address: easloffice@easloffice.eu; European Association for the Study of the Liver. EASL Clinical Practice Guidelines on nutrition in chronic liver disease","volume":"70","year":"2019","journal-title":"J\u00a0Hepatol"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib237","doi-asserted-by":"crossref","first-page":"406","DOI":"10.1016\/j.jhep.2018.03.024","article-title":"Electronic address: easloffice@easloffice.eu; European association for the study of the liver. EASL clinical practice guidelines for the management of patients with decompensated cirrhosis","volume":"69","year":"2018","journal-title":"J\u00a0Hepatol"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib238","doi-asserted-by":"crossref","first-page":"128","DOI":"10.1111\/chd.12685","article-title":"Frontiers in Fontan failure: innovation and improving outcomes: a conference summary","volume":"14","author":"Ephrem","year":"2019","journal-title":"Congenit Heart Dis"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib239","doi-asserted-by":"crossref","first-page":"38","DOI":"10.1111\/j.1540-8183.2007.00323.x","article-title":"Dilatation and stenting of the fontan pathway: impact of the stenosis\u00a0treatment on chronic ascites","volume":"21","author":"Ovroutski","year":"2008","journal-title":"J\u00a0Interv Cardiol"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib240","doi-asserted-by":"crossref","first-page":"366","DOI":"10.1007\/s00270-017-1863-2","article-title":"Modern techniques of lymphangiography and interventions: current status and future development","volume":"41","author":"Itkin","year":"2018","journal-title":"Cardiovasc Intervent Radiol"},{"key":"10.1016\/j.jhep.2023.07.013_bib241","doi-asserted-by":"crossref","first-page":"34","DOI":"10.1053\/j.pcsu.2020.01.002","article-title":"Innominate vein turn-down procedure for failing fontan circulation","volume":"23","author":"Hraska","year":"2020","journal-title":"Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu"},{"issue":"7","key":"10.1016\/j.jhep.2023.07.013_bib242","doi-asserted-by":"crossref","DOI":"10.1161\/CIRCINTERVENTIONS.121.011733","article-title":"Transcatheter thoracic duct decompression for multicompartment lymphatic failure after fontan palliation","volume":"15","author":"Smith","year":"2022","journal-title":"Circ Cardiovasc Interv"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib243","doi-asserted-by":"crossref","first-page":"357","DOI":"10.1177\/2150135118779351","article-title":"Hemodynamic effects of paracentesis in a patient with a fontan circulation","volume":"10","author":"Rajpal","year":"2019","journal-title":"World J Pediatr Congenit Heart Surg"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib244","doi-asserted-by":"crossref","first-page":"735","DOI":"10.1111\/jocs.15244","article-title":"Intraperitoneal corticosteroids for recurrent ascites in patients with Fontan circulation: initial clinical experience","volume":"36","author":"Wu","year":"2021","journal-title":"J\u00a0Card Surg"},{"issue":"6","key":"10.1016\/j.jhep.2023.07.013_bib245","doi-asserted-by":"crossref","first-page":"1083","DOI":"10.1016\/j.ejcts.2009.02.043","article-title":"Portal-systemic encephalopathy after Fontan-type operation in patient with polysplenia syndrome","volume":"35","author":"Koteda","year":"2009","journal-title":"Eur J Cardiothorac Surg"},{"issue":"7","key":"10.1016\/j.jhep.2023.07.013_bib246","doi-asserted-by":"crossref","first-page":"811","DOI":"10.1007\/s00234-019-02208-x","article-title":"Altered brain diffusion tensor imaging indices in adolescents with the Fontan palliation","volume":"61","author":"Singh","year":"2019","journal-title":"Neuroradiology"},{"issue":"6","key":"10.1016\/j.jhep.2023.07.013_bib247","doi-asserted-by":"crossref","first-page":"868","DOI":"10.1017\/S1047951118000537","article-title":"Western Canadian complex pediatric therapies follow-up program. Deterioration of functional abilities in children surviving the fontan operation","volume":"28","author":"Ricci","year":"2018","journal-title":"Cardiol Young"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib248","doi-asserted-by":"crossref","first-page":"700","DOI":"10.1007\/s00246-020-02532-7","article-title":"Systemic artery vasoconstrictor therapy in fontan patients with high cardiac output-heart failure: a single-center experience","volume":"42","author":"Miike","year":"2021","journal-title":"Pediatr Cardiol"},{"issue":"6","key":"10.1016\/j.jhep.2023.07.013_bib249","doi-asserted-by":"crossref","first-page":"457","DOI":"10.1007\/s00246-007-9006-1","article-title":"Thromboembolism and the role of anticoagulation in the Fontan patient","volume":"28","author":"Jacobs","year":"2007","journal-title":"Pediatr Cardiol"},{"issue":"5","key":"10.1016\/j.jhep.2023.07.013_bib250","doi-asserted-by":"crossref","first-page":"484","DOI":"10.1177\/1076029613520464","article-title":"Thrombosis and thromboembolic complications in fontan patients: a literature review","volume":"20","author":"Firdouse","year":"2014","journal-title":"Clin Appl Thromb Hemost"},{"issue":"6","key":"10.1016\/j.jhep.2023.07.013_bib251","doi-asserted-by":"crossref","first-page":"883","DOI":"10.1017\/S1047951120000992","article-title":"Portal vein thrombosis in Fontan-associated liver disease","volume":"30","author":"Kaulitz","year":"2020","journal-title":"Cardiol Young"},{"issue":"11","key":"10.1016\/j.jhep.2023.07.013_bib252","doi-asserted-by":"crossref","first-page":"2623","DOI":"10.1007\/s00261-017-1181-9","article-title":"Benign nodules in post-Fontan livers can show imaging features considered diagnostic for hepatocellular carcinoma","volume":"42","author":"Wells","year":"2017","journal-title":"Abdom Radiol (NY)"},{"issue":"6","key":"10.1016\/j.jhep.2023.07.013_bib253","doi-asserted-by":"crossref","first-page":"1212","DOI":"10.2214\/AJR.18.19762","article-title":"Multimodality screening of hepatic nodules in patients with congenital heart disease after fontan procedure: role of ultrasound, ARFI elastography, CT, and MRI","volume":"211","author":"Horvat","year":"2018","journal-title":"AJR Am J Roentgenol"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib254","doi-asserted-by":"crossref","first-page":"268","DOI":"10.1016\/j.ijcard.2010.05.047","article-title":"Arterialised hepatic nodules in the Fontan circulation: hepatico-cardiac interactions","volume":"151","author":"Bryant","year":"2011","journal-title":"Int J Cardiol"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib255","doi-asserted-by":"crossref","first-page":"201","DOI":"10.1016\/j.jpeds.2012.12.071","article-title":"Magnetic resonance imaging identifies unsuspected liver abnormalities in patients after the Fontan procedure","volume":"163","author":"Bulut","year":"2013","journal-title":"J\u00a0Pediatr"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib256","doi-asserted-by":"crossref","first-page":"1155","DOI":"10.1253\/circj.CJ-17-1053","article-title":"Research committee of the Japanese society of pediatric Cardiology and cardiac surgery. Liver cirrhosis and\/or hepatocellular carcinoma occurring late after the fontan procedure - a nationwide survey in Japan","volume":"82","author":"Kuwabara","year":"2018","journal-title":"Circ J"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib257","doi-asserted-by":"crossref","first-page":"33","DOI":"10.1007\/s00428-018-2373-6","article-title":"Hepatocellular nodules in vascular liver diseases","volume":"473","author":"Sempoux","year":"2018","journal-title":"Virchows Arch"},{"issue":"5","key":"10.1016\/j.jhep.2023.07.013_bib258","doi-asserted-by":"crossref","first-page":"1173","DOI":"10.1016\/j.jhep.2015.06.017","article-title":"Hepatocellular nodules expressing markers of hepatocellular adenomas in Budd-Chiari syndrome and other rare hepatic vascular disorders","volume":"63","author":"Sempoux","year":"2015","journal-title":"J\u00a0Hepatol"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib259","doi-asserted-by":"crossref","first-page":"613","DOI":"10.1111\/imj.15267","article-title":"Hepatic adenoma masquerading as a hepatocellular carcinoma in a patient with a Fontan procedure on the oral contraceptive pill","volume":"51","author":"Yao","year":"2021","journal-title":"Intern Med J"},{"issue":"6","key":"10.1016\/j.jhep.2023.07.013_bib260","doi-asserted-by":"crossref","first-page":"861","DOI":"10.1007\/s00246-010-9685-x","article-title":"Hepatic adenomatosis in a 7-year-old child treated earlier with a Fontan procedure","volume":"31","author":"Babaoglu","year":"2010","journal-title":"Pediatr Cardiol"},{"issue":"18","key":"10.1016\/j.jhep.2023.07.013_bib261","doi-asserted-by":"crossref","first-page":"1756","DOI":"10.1056\/NEJMc1214222","article-title":"Hepatocellular carcinoma after the Fontan procedure","volume":"368","author":"Asrani","year":"2013","journal-title":"N\u00a0Engl J Med"},{"issue":"5","key":"10.1016\/j.jhep.2023.07.013_bib262","doi-asserted-by":"crossref","first-page":"1174","DOI":"10.1002\/hep.510300507","article-title":"The\u00a0vascular profile of regenerative and dysplastic nodules of the cirrhotic\u00a0liver: implications for diagnosis and classification","volume":"30","author":"Roncalli","year":"1999","journal-title":"Hepatology"},{"issue":"6","key":"10.1016\/j.jhep.2023.07.013_bib263","doi-asserted-by":"crossref","first-page":"930","DOI":"10.1017\/S1047951121003309","article-title":"Liver nodules after the Fontan operation: role of the computerised tomography scan","volume":"32","author":"Sethasathien","year":"2022","journal-title":"Cardiol Young"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib264","doi-asserted-by":"crossref","first-page":"111","DOI":"10.1016\/j.diii.2021.09.001","article-title":"MR imaging features and long-term evolution of benign focal liver lesions in Budd-Chiari syndrome and Fontan-associated liver disease","volume":"103","author":"Panvini","year":"2022","journal-title":"Diagn Interv Imaging"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib265","doi-asserted-by":"crossref","first-page":"116","DOI":"10.1111\/hepr.13582","article-title":"Hepatocellular carcinoma after Fontan surgery: a systematic review","volume":"51","author":"Rodriguez De Santiago","year":"2021","journal-title":"Hepatol Res"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib266","doi-asserted-by":"crossref","first-page":"42","DOI":"10.5005\/jp-journals-10018-1315","article-title":"Benign hepatic nodules mimicking hepatocellular carcinoma in the setting of fontan-associated liver disease: a case report","volume":"10","author":"\u00c7olaklar","year":"2020","journal-title":"Euroasian J Hepatogastroenterol"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib267","doi-asserted-by":"crossref","first-page":"188","DOI":"10.1007\/s00261-019-02119-8","article-title":"CT and MR imaging findings of the livers in adults with Fontan palliation: an observational study","volume":"45","author":"Yang","year":"2020","journal-title":"Abdom Radiol (NY)"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib268","doi-asserted-by":"crossref","first-page":"175","DOI":"10.1016\/j.jaccas.2019.05.031","article-title":"Fontan liver lesions: not always HCC","volume":"1","author":"Haeffele","year":"2019","journal-title":"JACC Case Rep"},{"key":"10.1016\/j.jhep.2023.07.013_bib269","doi-asserted-by":"crossref","first-page":"142","DOI":"10.1016\/j.ijcard.2020.08.057","article-title":"Hepatocellular carcinoma and the Fontan circulation: clinical presentation and outcomes","volume":"322","author":"Possner","year":"2021","journal-title":"Int J Cardiol"},{"issue":"7","key":"10.1016\/j.jhep.2023.07.013_bib270","doi-asserted-by":"crossref","first-page":"746","DOI":"10.1161\/CIRCULATIONAHA.117.032717","article-title":"Hepatocellular carcinoma after fontan operation: multicenter case series","volume":"138","author":"Egbe","year":"2018","journal-title":"Circulation"},{"issue":"25","key":"10.1016\/j.jhep.2023.07.013_bib271","doi-asserted-by":"crossref","first-page":"2043","DOI":"10.1161\/CIRCULATIONAHA.121.056870","article-title":"Incidence and expected probability of liver cirrhosis and hepatocellular carcinoma after fontan operation","volume":"144","author":"Nii","year":"2021","journal-title":"Circulation"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib272","doi-asserted-by":"crossref","first-page":"111","DOI":"10.1007\/s00535-021-01842-8","article-title":"The absence of warfarin treatment and situs inversus are associated with the occurrence of hepatocellular carcinoma after Fontan surgery","volume":"57","author":"Sakamori","year":"2022","journal-title":"J\u00a0Gastroenterol"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib273","article-title":"Incidence, predictors, and mortality in patients with liver cancer after fontan operation","volume":"10","author":"Ohuchi","year":"2021","journal-title":"J\u00a0Am Heart Assoc"},{"key":"10.1016\/j.jhep.2023.07.013_bib274","unstructured":"Globalcan, http:\/\/gco.iarc.fr\/today)."},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib275","doi-asserted-by":"crossref","first-page":"352","DOI":"10.1097\/MEG.0000000000000527","article-title":"Hepatocellular carcinoma in cirrhotic versus noncirrhotic livers: results from a large cohort in the Netherlands","volume":"28","author":"van Meer","year":"2016","journal-title":"Eur J Gastroenterol Hepatol"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib276","doi-asserted-by":"crossref","first-page":"911","DOI":"10.1002\/hep.30194","article-title":"Hepatocellular carcinoma as a complication of vascular disease of the liver after fontan procedure","volume":"69","author":"Mazzarelli","year":"2019","journal-title":"Hepatology"},{"issue":"7","key":"10.1016\/j.jhep.2023.07.013_bib277","doi-asserted-by":"crossref","first-page":"853","DOI":"10.1111\/hepr.13500","article-title":"Characteristics of hepatocellular carcinoma arising from\u00a0Fontan-associated liver disease","volume":"50","author":"Sagawa","year":"2020","journal-title":"Hepatol Res"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib278","doi-asserted-by":"crossref","first-page":"182","DOI":"10.1016\/j.jhep.2018.03.019","article-title":"Electronic address: easloffice@easloffice.eu; European association for the study of the liver. EASL clinical practice guidelines: management of hepatocellular carcinoma","volume":"69","year":"2018","journal-title":"J\u00a0Hepatol"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib279","doi-asserted-by":"crossref","first-page":"422","DOI":"10.1016\/S0002-9343(96)00197-0","article-title":"Cost-effectiveness of screening for detection of small hepatocellular carcinoma in western patients with Child-Pugh class A cirrhosis","volume":"101","author":"Sarasin","year":"1996","journal-title":"Am J Med"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib280","doi-asserted-by":"crossref","first-page":"389","DOI":"10.1055\/s-0034-1394139","article-title":"Hepatocellular carcinoma screening and diagnosis","volume":"34","author":"Sherman","year":"2014","journal-title":"Semin Liver Dis"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib281","doi-asserted-by":"crossref","first-page":"161","DOI":"10.2217\/hep.13.22","article-title":"Limitations of screening for hepatocellular carcinoma","volume":"1","author":"Sherman","year":"2014","journal-title":"Hepat Oncol"},{"issue":"6","key":"10.1016\/j.jhep.2023.07.013_bib282","doi-asserted-by":"crossref","first-page":"1001","DOI":"10.1016\/j.bpg.2016.10.006","article-title":"Surveillance for hepatocellular carcinoma","volume":"30","author":"Forner","year":"2016","journal-title":"Best\u00a0Pract Res Clin Gastroenterol"},{"issue":"6","key":"10.1016\/j.jhep.2023.07.013_bib283","doi-asserted-by":"crossref","first-page":"828","DOI":"10.1136\/gut.2007.139477","article-title":"Hepatocellular carcinoma in Budd-Chiari syndrome: characteristics and risk factors","volume":"57","author":"Moucari","year":"2008","journal-title":"Gut"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib284","doi-asserted-by":"crossref","first-page":"179","DOI":"10.1016\/j.jhep.2015.07.040","article-title":"Electronic address: easloffice@easloffice.eu. EASL Clinical Practice Guidelines: vascular diseases of the liver","volume":"64","year":"2016","journal-title":"J\u00a0Hepatol"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib285","doi-asserted-by":"crossref","first-page":"5","DOI":"10.1016\/j.hlc.2019.09.010","article-title":"Management of people with a fontan circulation: a cardiac society of Australia and New Zealand position statement","volume":"29","author":"Zentner","year":"2020","journal-title":"Heart Lung Circ"},{"issue":"6","key":"10.1016\/j.jhep.2023.07.013_bib286","doi-asserted-by":"crossref","DOI":"10.1371\/journal.pone.0270230","article-title":"Risk factors for Fontan-associated hepatocellular carcinoma","volume":"17","author":"Kogiso","year":"2022","journal-title":"PLoS One"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib287","doi-asserted-by":"crossref","first-page":"132","DOI":"10.1002\/hep.1840160122","article-title":"Natural history of small untreated hepatocellular carcinoma in cirrhosis: a multivariate analysis of prognostic factors of tumor growth rate and patient survival","volume":"16","author":"Barbara","year":"1992","journal-title":"Hepatology"},{"issue":"Suppl 3","key":"10.1016\/j.jhep.2023.07.013_bib288","first-page":"1214","article-title":"Natural course of small hepatocellular carcinoma with underlying cirrhosis. A study of 30 patients","volume":"45","author":"Ebara","year":"1998","journal-title":"Hepatogastroenterology"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib289","doi-asserted-by":"crossref","first-page":"259","DOI":"10.1016\/0016-5085(85)90324-5","article-title":"Growth rate of asymptomatic hepatocellular carcinoma and its clinical implications","volume":"89","author":"Sheu","year":"1985","journal-title":"Gastroenterology"},{"issue":"12","key":"10.1016\/j.jhep.2023.07.013_bib290","doi-asserted-by":"crossref","first-page":"1418","DOI":"10.1016\/j.cgh.2008.08.005","article-title":"Cost effectiveness of alternative surveillance strategies for hepatocellular carcinoma in patients with cirrhosis","volume":"6","author":"Andersson","year":"2008","journal-title":"Clin Gastroenterol Hepatol"},{"issue":"7","key":"10.1016\/j.jhep.2023.07.013_bib291","first-page":"1048","article-title":"Cardiac implantable electronic devices in the fontan patient","volume":"38","author":"Mond\u00e9sert","year":"2022","journal-title":"Can J Cardiol"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib292","doi-asserted-by":"crossref","first-page":"69","DOI":"10.1038\/bjc.2014.536","article-title":"A\u00a0new approach to the use of \u03b1-fetoprotein as surveillance test for hepatocellular carcinoma in patients with cirrhosis","volume":"112","author":"Biselli","year":"2015","journal-title":"Br J Cancer"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib293","doi-asserted-by":"crossref","first-page":"434","DOI":"10.1016\/j.jhep.2005.03.019","article-title":"Serum alpha-fetoprotein levels in patients with advanced hepatitis C: results from the HALT-C Trial","volume":"43","author":"Di Bisceglie","year":"2005","journal-title":"J\u00a0Hepatol"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib294","doi-asserted-by":"crossref","first-page":"681","DOI":"10.1016\/j.jhep.2021.11.018","article-title":"BCLC strategy for prognosis prediction and treatment recommendation: the 2022 update","volume":"76","author":"Reig","year":"2022","journal-title":"J\u00a0Hepatol"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib295","first-page":"E55","article-title":"Surgical management of hepatocellular carcinoma after Fontan procedure","volume":"6","author":"Kwon","year":"2015","journal-title":"J\u00a0Gastrointest Oncol"},{"key":"10.1016\/j.jhep.2023.07.013_bib296","doi-asserted-by":"crossref","first-page":"144","DOI":"10.1016\/j.ijscr.2019.05.029","article-title":"Laparoscopic liver resection for hepatocellular carcinoma in Fontan-associated chronic liver disease. The first case report","volume":"59","author":"Angelico","year":"2019","journal-title":"Int J Surg Case Rep"},{"issue":"8","key":"10.1016\/j.jhep.2023.07.013_bib297","first-page":"99","article-title":"Anesthetic implications of extended right hepatectomy in a patient with fontan physiology","volume":"2","author":"Weyker","year":"2014","journal-title":"A\u00a0A Case Rep"},{"key":"10.1016\/j.jhep.2023.07.013_bib298","doi-asserted-by":"crossref","first-page":"51","DOI":"10.21037\/tgh.2018.07.10","article-title":"Left hepatectomy in a patient with a Fontan circulation","volume":"3","author":"Lo","year":"2018","journal-title":"Transl Gastroenterol Hepatol"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib299","doi-asserted-by":"crossref","first-page":"115","DOI":"10.1186\/s40792-021-01198-4","article-title":"Laparoscopic partial liver resection for hepatocellular carcinoma arising from Fontan-associated liver disease: a case report","volume":"7","author":"Iwata","year":"2021","journal-title":"Surg Case Rep"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib300","doi-asserted-by":"crossref","first-page":"80","DOI":"10.1186\/s12893-020-00741-8","article-title":"A\u00a0case report of Fontan procedure-related hepatocellular carcinoma: pure laparoscopic approach by low and stable pneumoperitoneum","volume":"20","author":"Yokota","year":"2020","journal-title":"BMC Surg"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib301","doi-asserted-by":"crossref","first-page":"104","DOI":"10.1186\/s40792-020-00866-1","article-title":"A\u00a0patient with post-Fontan operation underwent left hepatectomy and caudate lobectomy for hepatocellular carcinoma: a case report","volume":"6","author":"Nemoto","year":"2020","journal-title":"Surg Case Rep"},{"key":"10.1016\/j.jhep.2023.07.013_bib302","doi-asserted-by":"crossref","first-page":"21","DOI":"10.1016\/j.ijcard.2015.12.033","article-title":"Three cases of hepatocellular carcinoma in Fontan patients: review of the literature and suggestions for hepatic screening","volume":"206","author":"Josephus Jitta","year":"2016","journal-title":"Int J Cardiol"},{"issue":"9","key":"10.1016\/j.jhep.2023.07.013_bib303","doi-asserted-by":"crossref","first-page":"2564","DOI":"10.1016\/j.radcr.2021.06.031","article-title":"Repeated TACE in HCC after Fontan surgery and situs viscerum inversus: a case report","volume":"16","author":"Gasparrini","year":"2021","journal-title":"Radiol Case Rep"},{"issue":"12","key":"10.1016\/j.jhep.2023.07.013_bib304","doi-asserted-by":"crossref","first-page":"2602","DOI":"10.1016\/j.radcr.2020.09.056","article-title":"Transarterial chemoembolization for hepatocellular carcinoma in Fontan surgery patient","volume":"15","author":"Orlacchio","year":"2020","journal-title":"Radiol Case Rep"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib305","doi-asserted-by":"crossref","first-page":"E140","DOI":"10.1111\/j.1440-1754.2010.01932.x","article-title":"Cardiac cirrhosis and hepatocellular carcinoma in a 13-year-old treated with doxorubicin microbead transarterial chemoembolization","volume":"48","author":"Rosenbaum","year":"2012","journal-title":"J\u00a0Paediatr Child Health"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib306","doi-asserted-by":"crossref","first-page":"766","DOI":"10.1111\/ped.12619","article-title":"Transarterial embolization for pediatric hepatocellular carcinoma with cardiac cirrhosis","volume":"57","author":"Yamada","year":"2015","journal-title":"Pediatr Int"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib307","doi-asserted-by":"crossref","first-page":"275","DOI":"10.1159\/000501198","article-title":"Transplant-amenable hepatocellular carcinoma in a fontan patient","volume":"13","author":"Rutledge","year":"2019","journal-title":"Case Rep Gastroenterol"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib308","doi-asserted-by":"crossref","first-page":"73","DOI":"10.1007\/s12328-019-01010-9","article-title":"A\u00a0case of Fontan-related hepatocellular carcinoma successfully treated with proton beam therapy","volume":"13","author":"Ogasawara","year":"2020","journal-title":"Clin J Gastroenterol"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib309","doi-asserted-by":"crossref","first-page":"960","DOI":"10.1016\/j.jhep.2021.07.004","article-title":"Systemic treatment of hepatocellular carcinoma: an EASL position paper","volume":"75","author":"Bruix","year":"2021","journal-title":"J\u00a0Hepatol"},{"issue":"8","key":"10.1016\/j.jhep.2023.07.013_bib310","doi-asserted-by":"crossref","first-page":"1145","DOI":"10.2169\/internalmedicine.8154-21","article-title":"Robust effect of hepatic arterial infusion chemotherapy and radiation therapy on hepatocellular carcinoma arising from fontan-associated liver disease","volume":"61","author":"Suzuki","year":"2022","journal-title":"Intern Med"},{"issue":"41","key":"10.1016\/j.jhep.2023.07.013_bib311","doi-asserted-by":"crossref","DOI":"10.1097\/MD.0000000000004823","article-title":"Hepatocellular carcinoma after the Fontan procedure in a 16-year-old girl: a case report","volume":"95","author":"Oh","year":"2016","journal-title":"Medicine (Baltimore)"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib312","doi-asserted-by":"crossref","first-page":"466","DOI":"10.17085\/apm.20037","article-title":"Liver transplantation in an adult patient with hepatocellular carcinoma following liver cirrhosis as a complication of the Fontan procedure -A case report","volume":"15","author":"Cho","year":"2020","journal-title":"Anesth Pain Med (Seoul)"},{"key":"10.1016\/j.jhep.2023.07.013_bib313","series-title":"StatPearls [internet]","article-title":"Heart transplantation patient selection","author":"Brown","year":"2022"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib314","doi-asserted-by":"crossref","first-page":"134","DOI":"10.1007\/s15010-004-2209-y","article-title":"Prevalence and risk factors of hepatitis C infection after cardiac surgery in childhood before and after blood donor screening","volume":"32","author":"Vogt","year":"2004","journal-title":"Infection"},{"issue":"6B","key":"10.1016\/j.jhep.2023.07.013_bib315","doi-asserted-by":"crossref","first-page":"16S","DOI":"10.1016\/S0002-9343(99)00375-7","article-title":"Discovery of non-A, non-B hepatitis and identification of its etiology","volume":"107","author":"Alter","year":"1999","journal-title":"Am J Med"},{"issue":"6","key":"10.1016\/j.jhep.2023.07.013_bib316","doi-asserted-by":"crossref","first-page":"1425","DOI":"10.1007\/s00246-021-02628-8","article-title":"Sizing up fontan failure: association with increasing weight in adulthood","volume":"42","author":"Byrne","year":"2021","journal-title":"Pediatr Cardiol"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib317","doi-asserted-by":"crossref","first-page":"589","DOI":"10.1016\/j.cld.2019.06.001","article-title":"Frailty, sarcopenia, and malnutrition in cirrhotic patients","volume":"23","author":"Aby","year":"2019","journal-title":"Clin Liver Dis"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib318","first-page":"10","article-title":"Secondary sarcopenia assessed by computed tomography can predict hospitalization for heart failure in adults with Fontan circulation","volume":"77","author":"Shiina","year":"2021","journal-title":"J\u00a0Cardiol"},{"issue":"6","key":"10.1016\/j.jhep.2023.07.013_bib319","doi-asserted-by":"crossref","first-page":"704","DOI":"10.1016\/j.healun.2022.02.023","article-title":"Exercise invasive hemodynamics in adults post-Fontan: a novel tool in understanding functional limitation and liver disease","volume":"41","author":"Miranda","year":"2022","journal-title":"J\u00a0Heart Lung Transpl"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib320","first-page":"418","article-title":"Thromboembolic events are independently associated with liver stiffness in patients with fontan circulation","volume":"9","author":"Alsaied","year":"2020","journal-title":"J\u00a0Clin Med"},{"issue":"21","key":"10.1016\/j.jhep.2023.07.013_bib321","doi-asserted-by":"crossref","first-page":"1731","DOI":"10.1136\/heartjnl-2015-307930","article-title":"Strategies for thromboprophylaxis in Fontan circulation: a meta-analysis","volume":"101","author":"Alsaied","year":"2015","journal-title":"Heart"},{"issue":"6","key":"10.1016\/j.jhep.2023.07.013_bib322","doi-asserted-by":"crossref","first-page":"645","DOI":"10.1016\/j.jacc.2011.01.061","article-title":"A\u00a0multicenter, randomized trial comparing heparin\/warfarin and acetylsalicylic acid as primary thromboprophylaxis for 2 years after the Fontan procedure in children","volume":"58","author":"Monagle","year":"2011","journal-title":"J\u00a0Am Coll Cardiol"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib323","doi-asserted-by":"crossref","first-page":"1218","DOI":"10.1016\/j.jtcvs.2020.12.102","article-title":"Long-term outcomes of warfarin versus aspirin after Fontan surgery","volume":"162","author":"Attard","year":"2021","journal-title":"J\u00a0Thorac Cardiovasc Surg"},{"key":"10.1016\/j.jhep.2023.07.013_bib324","article-title":"Regular aspirin use is associated with a reduced risk of hepatocellular carcinoma (HCC) in chronic liver disease: a systematic review and meta-analysis","author":"Tan","year":"2022","journal-title":"J\u00a0Gastrointest Cancer"},{"key":"10.1016\/j.jhep.2023.07.013_bib325","article-title":"A\u00a0multisite retrospective review of direct oral anticoagulants compared to warfarin in adult fontan patients","author":"Kazerouninia","year":"2022","journal-title":"Cardiovasc Drugs Ther"},{"issue":"8","key":"10.1016\/j.jhep.2023.07.013_bib326","doi-asserted-by":"crossref","first-page":"770","DOI":"10.1161\/CIR.0000000000000352","volume":"133","author":"Stout","year":"2016","journal-title":"Circulation"},{"key":"10.1016\/j.jhep.2023.07.013_bib327","doi-asserted-by":"crossref","first-page":"123","DOI":"10.1016\/j.ijcard.2019.06.014","article-title":"Non-vitamin K antagonist oral anticoagulants (NOACs) for thromboembolic prevention, are they safe in congenital heart disease? Results of a worldwide study","volume":"299","author":"Yang","year":"2020","journal-title":"Int J Cardiol"},{"issue":"9","key":"10.1016\/j.jhep.2023.07.013_bib328","doi-asserted-by":"crossref","first-page":"2159","DOI":"10.1111\/liv.14992","article-title":"Safety of direct oral anticoagulants in patients with advanced liver disease","volume":"41","author":"Semmler","year":"2021","journal-title":"Liver Int"},{"key":"10.1016\/j.jhep.2023.07.013_bib329","doi-asserted-by":"crossref","first-page":"95","DOI":"10.1016\/j.ijcard.2016.02.089","article-title":"Australia and New Zealand fontan registry. Use of ACE inhibitors in fontan: rational or irrational?","volume":"210","author":"Wilson","year":"2016","journal-title":"Int J Cardiol"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib330","doi-asserted-by":"crossref","first-page":"59","DOI":"10.1016\/0003-4975(94)90365-4","article-title":"Comparison of the hormonal response after bidirectional Glenn and Fontan procedures","volume":"57","author":"Mainwaring","year":"1994","journal-title":"Ann Thorac Surg"},{"issue":"21","key":"10.1016\/j.jhep.2023.07.013_bib331","doi-asserted-by":"crossref","first-page":"2579","DOI":"10.3748\/wjg.15.2579","article-title":"Renin-angiotensin system in the pathogenesis of liver fibrosis","volume":"15","author":"Pereira","year":"2009","journal-title":"World J Gastroenterol"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib332","doi-asserted-by":"crossref","first-page":"376","DOI":"10.1016\/S0168-8278(01)00146-5","article-title":"Effect of angiotensin II type 1 receptor blockade on experimental hepatic fibrogenesis","volume":"35","author":"Paizis","year":"2001","journal-title":"J\u00a0Hepatol"},{"issue":"6","key":"10.1016\/j.jhep.2023.07.013_bib333","doi-asserted-by":"crossref","first-page":"348","DOI":"10.1159\/000069792","article-title":"Angiotensin-I-converting enzyme inhibitors may be an alternative anti-angiogenic strategy in the treatment of liver fibrosis and hepatocellular carcinoma. Possible role of vascular endothelial growth factor","volume":"23","author":"Yoshiji","year":"2002","journal-title":"Tumour Biol"},{"issue":"6","key":"10.1016\/j.jhep.2023.07.013_bib334","doi-asserted-by":"crossref","first-page":"824","DOI":"10.3748\/wjg.v6.i6.824","article-title":"The regulatory role of AT 1 receptor on activated HSCs in hepatic fibrogenesis:effects of RAS inhibitors on hepatic fibrosis induced by CCl(4)","volume":"6","author":"Wei","year":"2000","journal-title":"World J Gastroenterol"},{"issue":"6","key":"10.1016\/j.jhep.2023.07.013_bib335","doi-asserted-by":"crossref","first-page":"773","DOI":"10.1016\/S0168-8278(02)00307-0","article-title":"Hemodynamic and antifibrotic effects of losartan in rats with liver fibrosis and\/or portal hypertension","volume":"37","author":"Croquet","year":"2002","journal-title":"J\u00a0Hepatol"},{"key":"10.1016\/j.jhep.2023.07.013_bib336","doi-asserted-by":"crossref","first-page":"98","DOI":"10.1016\/j.amjcard.2021.10.013","article-title":"3-Month enalapril treatment in pediatric fontan patients with moderate to good systolic ventricular function","volume":"163","author":"Harteveld","year":"2022","journal-title":"Am J Cardiol"},{"issue":"5","key":"10.1016\/j.jhep.2023.07.013_bib337","doi-asserted-by":"crossref","first-page":"979","DOI":"10.1536\/ihj.20-059","article-title":"Risk factors for mid-term liver disease after the fontan procedure","volume":"61","author":"Oka","year":"2020","journal-title":"Int Heart J"},{"issue":"25","key":"10.1016\/j.jhep.2023.07.013_bib338","doi-asserted-by":"crossref","first-page":"3204","DOI":"10.1161\/01.CIR.0000074210.49434.40","article-title":"Basal pulmonary vascular resistance and nitric oxide responsiveness late after Fontan-type operation","volume":"107","author":"Khambadkone","year":"2003","journal-title":"Circulation"},{"key":"10.1016\/j.jhep.2023.07.013_bib339","doi-asserted-by":"crossref","first-page":"36","DOI":"10.1186\/1471-2261-13-36","article-title":"The effect of\u00a0bosentan on exercise capacity in Fontan patients; rationale and design\u00a0for the TEMPO study","volume":"13","author":"Hebert","year":"2013","journal-title":"BMC Cardiovasc Disord"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib340","doi-asserted-by":"crossref","first-page":"2435","DOI":"10.1016\/j.ijcard.2013.03.014","article-title":"Effect of inhaled iloprost on the exercise function of Fontan patients: a demonstration of concept","volume":"168","author":"Rhodes","year":"2013","journal-title":"Int J Cardiol"},{"issue":"13","key":"10.1016\/j.jhep.2023.07.013_bib341","doi-asserted-by":"crossref","first-page":"1681","DOI":"10.1093\/eurheartj\/ehn215","article-title":"Effect of sildenafil on haemodynamic response to exercise and exercise capacity in Fontan patients","volume":"29","author":"Giardini","year":"2008","journal-title":"Eur Heart J"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib342","doi-asserted-by":"crossref","DOI":"10.1177\/2045894018790450","article-title":"The efficacy and safety of pulmonary vasodilators in patients with Fontan circulation: a meta-analysis of randomized controlled trials","volume":"9","author":"Wang","year":"2019","journal-title":"Pulm Circ"},{"issue":"6","key":"10.1016\/j.jhep.2023.07.013_bib343","doi-asserted-by":"crossref","first-page":"1468","DOI":"10.1016\/j.jtcvs.2017.01.051","article-title":"Endothelin inhibitors lower pulmonary vascular resistance and improve functional capacity in patients with Fontan circulation","volume":"153","author":"Agnoletti","year":"2017","journal-title":"J\u00a0Thorac Cardiovasc Surg"},{"issue":"8","key":"10.1016\/j.jhep.2023.07.013_bib344","first-page":"1489","article-title":"Pulmonary vasodilator therapy in the failing Fontan circulation: rationale and efficacy","volume":"25","author":"Snarr","year":"2015","journal-title":"Cardiol\u00a0Young"},{"issue":"8","key":"10.1016\/j.jhep.2023.07.013_bib345","doi-asserted-by":"crossref","first-page":"1269","DOI":"10.1016\/j.amjcard.2017.01.001","article-title":"Meta-Analysis of the effectiveness of heart transplantation in patients with a failing fontan","volume":"119","author":"Tabarsi","year":"2017","journal-title":"Am J Cardiol"},{"issue":"5","key":"10.1016\/j.jhep.2023.07.013_bib346","doi-asserted-by":"crossref","first-page":"1183","DOI":"10.1016\/j.jtcvs.2011.12.039","article-title":"Outcomes after transplantation for \"failed\" Fontan: a single-institution experience","volume":"143","author":"Davies","year":"2012","journal-title":"J\u00a0Thorac Cardiovasc Surg"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib347","doi-asserted-by":"crossref","first-page":"665","DOI":"10.1093\/ejcts\/ezu280","article-title":"Favourable mid-term outcome after heart transplantation for late Fontan failure","volume":"47","author":"Michielon","year":"2015","journal-title":"Eur J Cardiothorac Surg"},{"issue":"7","key":"10.1016\/j.jhep.2023.07.013_bib348","doi-asserted-by":"crossref","first-page":"877","DOI":"10.1016\/j.healun.2016.02.005","article-title":"Improved survival after heart transplant for failed Fontan patients with preserved ventricular function","volume":"35","author":"Miller","year":"2016","journal-title":"J\u00a0Heart Lung Transpl"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib349","doi-asserted-by":"crossref","first-page":"558","DOI":"10.1016\/j.athoracsur.2009.03.085","article-title":"Evaluating failing Fontans for heart transplantation: predictors of death","volume":"88","author":"Griffiths","year":"2009","journal-title":"Ann Thorac Surg"},{"issue":"12","key":"10.1016\/j.jhep.2023.07.013_bib350","first-page":"1807","article-title":"Clinical importance of fontan circuit thrombus in the adult population: significant association with increased risk of cardiovascular events","volume":"35","author":"Sathananthan","year":"2019","journal-title":"Can J Cardiol"},{"issue":"7","key":"10.1016\/j.jhep.2023.07.013_bib351","first-page":"1072","article-title":"Heart transplant indications, considerations, and outcomes in fontan patients: age-related nuances, transplant listing, and disease-specific indications","volume":"38","author":"Dipchand","year":"2022","journal-title":"Can J Cardiol"},{"issue":"5","key":"10.1016\/j.jhep.2023.07.013_bib352","doi-asserted-by":"crossref","DOI":"10.1111\/petr.13951","article-title":"Fontan-associated plastic bronchitis waitlist and heart transplant outcomes: a PHTS analysis","volume":"25","author":"Bearl","year":"2021","journal-title":"Pediatr Transpl"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib353","doi-asserted-by":"crossref","first-page":"283","DOI":"10.1016\/j.healun.2021.10.020","article-title":"Fate of the liver in the survivors of adult heart transplant for a failing Fontan circulation","volume":"41","author":"Broda","year":"2022","journal-title":"J\u00a0Heart Lung Transpl"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib354","doi-asserted-by":"crossref","first-page":"26","DOI":"10.1016\/j.healun.2015.10.015","article-title":"Fontan-associated liver disease: implications for heart transplantation","volume":"35","author":"Greenway","year":"2016","journal-title":"J\u00a0Heart Lung Transpl"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib355","doi-asserted-by":"crossref","first-page":"1462","DOI":"10.1016\/j.jtcvs.2021.02.014","article-title":"Hepatorenal dysfunction assessment with the Model for End-Stage Liver Disease Excluding INR score predicts worse survival after heart transplant in pediatric Fontan patients","volume":"163","author":"Amdani","year":"2022","journal-title":"J\u00a0Thorac Cardiovasc Surg"},{"issue":"11","key":"10.1016\/j.jhep.2023.07.013_bib356","first-page":"1742","article-title":"Determinants and prognostic implications of hepatorenal dysfunction in adults with congenital heart disease","volume":"38","author":"Egbe","year":"2022","journal-title":"Can J Cardiol"},{"issue":"10","key":"10.1016\/j.jhep.2023.07.013_bib357","doi-asserted-by":"crossref","first-page":"1675","DOI":"10.1016\/j.amjcard.2017.02.005","article-title":"Mortality risk stratification in fontan patients who underwent heart transplantation","volume":"119","author":"Berg","year":"2017","journal-title":"Am J Cardiol"},{"issue":"7","key":"10.1016\/j.jhep.2023.07.013_bib358","doi-asserted-by":"crossref","first-page":"491","DOI":"10.1136\/heartjnl-2012-303347","article-title":"MELD-XI score and cardiac mortality or transplantation in patients after Fontan surgery","volume":"99","author":"Assenza","year":"2013","journal-title":"Heart"},{"issue":"7","key":"10.1016\/j.jhep.2023.07.013_bib359","doi-asserted-by":"crossref","first-page":"578","DOI":"10.1016\/j.cardfail.2015.09.002","article-title":"Outcomes of adult patients with congenital heart disease after heart transplantation: impact of disease type, previous thoracic surgeries, and bystander organ dysfunction","volume":"22","author":"Lewis","year":"2016","journal-title":"J\u00a0Card Fail"},{"issue":"3","key":"10.1016\/j.jhep.2023.07.013_bib360","doi-asserted-by":"crossref","DOI":"10.1111\/ctr.12892","article-title":"Single-center outcomes of combined heart and liver transplantation in the failing Fontan","volume":"31","author":"D'Souza","year":"2017","journal-title":"Clin Transpl"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib361","doi-asserted-by":"crossref","first-page":"9","DOI":"10.1007\/s40472-021-00315-4","article-title":"Orthotopic heart and combined heart liver transplantation: the ultimate treatment option for failing fontan physiology","volume":"8","author":"Reardon","year":"2021","journal-title":"Curr Transpl Rep"},{"issue":"4","key":"10.1016\/j.jhep.2023.07.013_bib362","doi-asserted-by":"crossref","first-page":"298","DOI":"10.1016\/j.healun.2020.12.008","article-title":"Comparison of combined heart\u2012liver vs heart-only transplantation in pediatric and young adult Fontan recipients","volume":"40","author":"Sganga","year":"2021","journal-title":"J\u00a0Heart Lung Transpl"},{"key":"10.1016\/j.jhep.2023.07.013_bib363","doi-asserted-by":"crossref","first-page":"790","DOI":"10.1016\/j.ijcard.2016.11.121","article-title":"Isolated heart transplant and combined heart-liver transplant in adult congenital heart disease patients: insights from the united network of organ sharing","volume":"228","author":"Bradley","year":"2017","journal-title":"Int J Cardiol"},{"issue":"2","key":"10.1016\/j.jhep.2023.07.013_bib364","doi-asserted-by":"crossref","first-page":"170","DOI":"10.1016\/j.healun.2013.10.033","article-title":"Liver cirrhosis in Fontan patients does not affect 1-year post-heart transplant mortality or markers of liver function","volume":"33","author":"Simpson","year":"2014","journal-title":"J\u00a0Heart Lung Transpl"},{"key":"10.1016\/j.jhep.2023.07.013_bib365","doi-asserted-by":"crossref","first-page":"78","DOI":"10.1016\/j.jpeds.2020.09.044","article-title":"Pretransplantation and post-transplantation liver disease assessment in adolescents undergoing isolated heart transplantation for fontan failure","volume":"229","author":"Rodriguez","year":"2021","journal-title":"J\u00a0Pediatr"},{"issue":"8","key":"10.1016\/j.jhep.2023.07.013_bib366","doi-asserted-by":"crossref","DOI":"10.1111\/petr.13061","article-title":"Liver abnormalities and post-transplant survival in pediatric Fontan patients","volume":"21","author":"Hofferberth","year":"2017","journal-title":"Pediatr Transpl"},{"issue":"11","key":"10.1016\/j.jhep.2023.07.013_bib367","doi-asserted-by":"crossref","DOI":"10.1161\/CIRCHEARTFAILURE.117.003754","article-title":"Regression of advanced liver fibrosis after heart transplantation in a patient with prior fontan surgery for complex congenital heart disease","volume":"11","author":"Bouchardy","year":"2018","journal-title":"Circ Heart Fail"},{"issue":"8","key":"10.1016\/j.jhep.2023.07.013_bib368","doi-asserted-by":"crossref","DOI":"10.1111\/petr.14094","article-title":"Heterogeneous outcomes of liver disease after heart transplantation for a failed Fontan procedure","volume":"25","author":"Ybarra","year":"2021","journal-title":"Pediatr Transpl"},{"key":"10.1016\/j.jhep.2023.07.013_bib369","article-title":"Fontan-associated liver disease after heart transplant","author":"Griffiths","year":"2022","journal-title":"Pediatr Transpl"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib370","doi-asserted-by":"crossref","first-page":"18","DOI":"10.1097\/TP.0000000000003308","article-title":"Big data in transplantation practice-the devil is in the detail-fontan-associated liver disease","volume":"105","author":"Kim","year":"2021","journal-title":"Transplantation"},{"issue":"23","key":"10.1016\/j.jhep.2023.07.013_bib371","doi-asserted-by":"crossref","first-page":"e143","DOI":"10.1016\/j.jacc.2008.10.001","volume":"52","author":"Warnes","year":"2008","journal-title":"J\u00a0Am Coll Cardiol"},{"issue":"1","key":"10.1016\/j.jhep.2023.07.013_bib372","doi-asserted-by":"crossref","first-page":"56","DOI":"10.1007\/s00246-016-1484-6","article-title":"The long-term management of children and adults with a fontan circulation: a systematic review and survey of current practice in Australia and New Zealand","volume":"38","author":"Gnanappa","year":"2017","journal-title":"Pediatr Cardiol"},{"issue":"8","key":"10.1016\/j.jhep.2023.07.013_bib373","doi-asserted-by":"crossref","first-page":"907","DOI":"10.1097\/MEG.0000000000001641","article-title":"Fontan-associated liver disease: pathophysiology, investigations, predictors of severity and management","volume":"32","author":"Keung","year":"2020","journal-title":"Eur J Gastroenterol Hepatol"}],"container-title":["Journal of Hepatology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0168827823049929?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0168827823049929?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2025,9,29]],"date-time":"2025-09-29T19:50:53Z","timestamp":1759175453000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0168827823049929"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2023,11]]},"references-count":373,"journal-issue":{"issue":"5","published-print":{"date-parts":[[2023,11]]}},"alternative-id":["S0168827823049929"],"URL":"https:\/\/doi.org\/10.1016\/j.jhep.2023.07.013","relation":{},"ISSN":["0168-8278"],"issn-type":[{"value":"0168-8278","type":"print"}],"subject":[],"published":{"date-parts":[[2023,11]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"EASL-ERN position paper on liver involvement in patients with Fontan-type circulation","name":"articletitle","label":"Article Title"},{"value":"Journal of Hepatology","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.jhep.2023.07.013","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"\u00a9 2023 European Association for the Study of the Liver. Published by Elsevier B.V. All rights reserved.","name":"copyright","label":"Copyright"}]}}