{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,27]],"date-time":"2026-09-27T09:02:27Z","timestamp":1790499747075,"version":"4.1.0"},"reference-count":66,"publisher":"Elsevier BV","license":[{"start":{"date-parts":[[2016,7,1]],"date-time":"2016-07-01T00:00:00Z","timestamp":1467331200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2016,7,1]],"date-time":"2016-07-01T00:00:00Z","timestamp":1467331200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/legal\/tdmrep-license"}],"content-domain":{"domain":["clinicalkey.com","clinicalkey.com.au","clinicalkey.es","clinicalkey.fr","clinicalkey.jp","journalofinfection.com","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Journal of Infection"],"published-print":{"date-parts":[[2016,7]]},"DOI":"10.1016\/j.jinf.2016.04.022","type":"journal-article","created":{"date-parts":[[2016,5,11]],"date-time":"2016-05-11T00:14:39Z","timestamp":1462925679000},"page":"S50-S55","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":75,"special_numbering":"S","title":["Aspergillus infections in cystic fibrosis"],"prefix":"10.1016","volume":"72","author":[{"given":"Jill","family":"King","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Shan F.","family":"Brunel","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Adilia","family":"Warris","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"key":"10.1016\/j.jinf.2016.04.022_bib1","doi-asserted-by":"crossref","first-page":"1891","DOI":"10.1016\/S0140-6736(09)60327-5","article-title":"Cystic fibrosis","volume":"373","author":"O'Sullivan","year":"2009","journal-title":"Lancet"},{"key":"10.1016\/j.jinf.2016.04.022_bib2","doi-asserted-by":"crossref","first-page":"1033","DOI":"10.1136\/archdischild-2013-304400","article-title":"Recent advances in the management of cystic fibrosis","volume":"99","author":"Davies","year":"2014","journal-title":"Arch Dis Child"},{"key":"10.1016\/j.jinf.2016.04.022_bib3","series-title":"UK Cystic Fibrosis Registry 2014 Annual Data Report","author":"Siobhan","year":"2015"},{"key":"10.1016\/j.jinf.2016.04.022_bib4","doi-asserted-by":"crossref","first-page":"509","DOI":"10.1038\/nm.2715","article-title":"Cystic fibrosis: a mucosal immunodeficiency syndrome","volume":"18","author":"Cohen","year":"2012","journal-title":"Nat Med"},{"key":"10.1016\/j.jinf.2016.04.022_bib5","doi-asserted-by":"crossref","first-page":"148","DOI":"10.1016\/S2213-2600(13)70026-2","article-title":"Early lung disease in cystic fibrosis","volume":"1","author":"Grasemann","year":"2013","journal-title":"Lancet Respir Med"},{"key":"10.1016\/j.jinf.2016.04.022_bib6","doi-asserted-by":"crossref","first-page":"e98502","DOI":"10.1371\/journal.pone.0098502","article-title":"Multi-country estimate of different manifestations of aspergillosis in cystic fibrosis","volume":"9","author":"Armstead","year":"2014","journal-title":"PLoS One"},{"key":"10.1016\/j.jinf.2016.04.022_bib7","doi-asserted-by":"crossref","first-page":"301","DOI":"10.1164\/rccm.201106-1027OC","article-title":"Cystic fibrosis transmembrane conductance regulator regulates epithelial cell response to Aspergillus and resultant pulmonary inflammation","volume":"185","author":"Chaudhary","year":"2012","journal-title":"Am J Respir Crit Care Med"},{"key":"10.1016\/j.jinf.2016.04.022_bib8","doi-asserted-by":"crossref","first-page":"351","DOI":"10.1097\/01.TP.0000437434.42851.d4","article-title":"Pretransplant Aspergillus colonization of cystic fibrosis patients and the incidence of post-lung transplant invasive aspergillosis","volume":"97","author":"Luong","year":"2014","journal-title":"Transplantion"},{"key":"10.1016\/j.jinf.2016.04.022_bib9","doi-asserted-by":"crossref","first-page":"890","DOI":"10.1016\/j.healun.2007.07.002","article-title":"Post-operative infections in cystic fibrosis and non-cystic fibrosis patients after lung transplantation","volume":"26","author":"Bonvillain","year":"2007","journal-title":"J Heart Lung Transp"},{"key":"10.1016\/j.jinf.2016.04.022_bib10","doi-asserted-by":"crossref","first-page":"387","DOI":"10.1080\/13693780802609604","article-title":"Occurrence and relevance of filamentous fungi in respiratory secretions of patients with cystic fibrosis\u2013a review","volume":"47","author":"Pihet","year":"2009","journal-title":"Med Mycol"},{"key":"10.1016\/j.jinf.2016.04.022_bib11","doi-asserted-by":"crossref","first-page":"187","DOI":"10.1016\/j.jcf.2013.02.003","article-title":"What is the clinical significance of filamentous fungi positive sputum cultures in patients with cystic fibrosis?","volume":"12","author":"Liu","year":"2013","journal-title":"J Cyst Fibros"},{"key":"10.1016\/j.jinf.2016.04.022_bib12","doi-asserted-by":"crossref","first-page":"310","DOI":"10.1128\/CMR.12.2.310","article-title":"Aspergillus fumigatus and aspergillosis","volume":"12","author":"Latge","year":"1999","journal-title":"Clin Microbiol Rev"},{"key":"10.1016\/j.jinf.2016.04.022_bib13","doi-asserted-by":"crossref","first-page":"632","DOI":"10.1097\/MCP.0b013e328358d50b","article-title":"Effects of Aspergillus fumigatus colonization on lung function in cystic fibrosis","volume":"18","author":"Speirs","year":"2012","journal-title":"Curr Opin Pulm Med"},{"key":"10.1016\/j.jinf.2016.04.022_bib14","doi-asserted-by":"crossref","first-page":"161","DOI":"10.1016\/j.biocel.2014.03.001","article-title":"Fungi in the cystic fibrosis lung: bystanders or pathogens?","volume":"52","author":"Chotirmally","year":"2014","journal-title":"Int J Biochem Cell Biol"},{"key":"10.1016\/j.jinf.2016.04.022_bib15","doi-asserted-by":"crossref","first-page":"222","DOI":"10.1378\/chest.130.1.222","article-title":"Aspergillus bronchitis in cystic fibrosis","volume":"130","author":"Shoseyov","year":"2006","journal-title":"Chest"},{"key":"10.1016\/j.jinf.2016.04.022_bib16","doi-asserted-by":"crossref","first-page":"560","DOI":"10.1016\/j.jaci.2013.04.007","article-title":"Novel immunologic classification of aspergillosis in adult cystic fibrosis","volume":"132","author":"Baxter","year":"2013","journal-title":"J Allergy Clin Immunol"},{"key":"10.1016\/j.jinf.2016.04.022_bib17","doi-asserted-by":"crossref","first-page":"850","DOI":"10.1111\/cea.12141","article-title":"Allergic bronchopulmonary aspergillosis: review of literature and proposal of new diagnostic and classification criteria","volume":"43","author":"Agarwal","year":"2013","journal-title":"Clin Exp Allergy"},{"key":"10.1016\/j.jinf.2016.04.022_bib18","doi-asserted-by":"crossref","first-page":"6","DOI":"10.1002\/(SICI)1099-0496(199601)21:1<6::AID-PPUL1>3.0.CO;2-R","article-title":"Clinical significance of the recovery of Aspergillus species from the respiratory secretions of cystic fibrosis patients","volume":"21","author":"Milla","year":"1996","journal-title":"Pediatr Pulmonol"},{"key":"10.1016\/j.jinf.2016.04.022_bib19","doi-asserted-by":"crossref","first-page":"e197","DOI":"10.1016\/j.ejrad.2011.01.114","article-title":"Radiological abnormalities associated with Aspergillus colonization in a cystic fibrosis population","volume":"81","author":"McMahon","year":"2012","journal-title":"Eur J Radiol"},{"key":"10.1016\/j.jinf.2016.04.022_bib20","doi-asserted-by":"crossref","first-page":"1381","DOI":"10.1111\/j.1469-0691.2010.03429.x","article-title":"Aspergillus fumigatus colonization in cystic fibrosis: implications for lung function?","volume":"17","author":"de Vrankrijker","year":"2011","journal-title":"Clin Microbiol Infect"},{"key":"10.1016\/j.jinf.2016.04.022_bib21","doi-asserted-by":"crossref","first-page":"764","DOI":"10.1002\/ppul.21240","article-title":"Risk factors for Aspergillus colonization and allergic bronchopulmonary aspergillosis in children with cystic fibrosis","volume":"45","author":"Jubin","year":"2010","journal-title":"Pediatr Pulmonol"},{"key":"10.1016\/j.jinf.2016.04.022_bib22","doi-asserted-by":"crossref","first-page":"171","DOI":"10.1378\/chest.09-1103","article-title":"The effect of chronic infection with Aspergillus fumigatus on lung function and hospitalization in patients with cystic fibrosis","volume":"137","author":"Amin","year":"2010","journal-title":"Chest"},{"key":"10.1016\/j.jinf.2016.04.022_bib23","doi-asserted-by":"crossref","first-page":"S88","DOI":"10.3109\/13693786.2010.511287","article-title":"Lack of standardization in the procedures for mycological examination of sputum samples from CF patients: a possible cause for variations in the prevalence of filamentous fungi","volume":"48","author":"Borman","year":"2010","journal-title":"Med Mycol"},{"key":"10.1016\/j.jinf.2016.04.022_bib24","doi-asserted-by":"crossref","first-page":"10241","DOI":"10.1038\/srep10241","article-title":"Lung microbiota across age and disease stage in cystic fibrosis","volume":"5","author":"Coburn","year":"2015","journal-title":"Sci Rep"},{"key":"10.1016\/j.jinf.2016.04.022_bib25","doi-asserted-by":"crossref","first-page":"1513","DOI":"10.1164\/ajrccm.150.6.7952609","article-title":"Development of immune responses to Aspergillus at an early age in children with cystic fibrosis","volume":"150","author":"El-Dahr","year":"1994","journal-title":"Am J Respir Crit Care Med"},{"key":"10.1016\/j.jinf.2016.04.022_bib26","doi-asserted-by":"crossref","first-page":"680","DOI":"10.1097\/INF.0000000000000231","article-title":"Aspergillus sensitization or carriage in cystic fibrosis patients","volume":"33","author":"Fillaux","year":"2014","journal-title":"Pediatr Infect Dis J"},{"key":"10.1016\/j.jinf.2016.04.022_bib27","doi-asserted-by":"crossref","first-page":"367","DOI":"10.1099\/0022-1317-50-4-367","article-title":"Molecular epidemiology of airway colonisation by Aspergillus fumigatus in cystic fibrosis patients","volume":"50","author":"Cimon","year":"2001","journal-title":"J Med Microbiol"},{"key":"10.1016\/j.jinf.2016.04.022_bib28","doi-asserted-by":"crossref","first-page":"e36313","DOI":"10.1371\/journal.pone.0036313","article-title":"The airway microbiota in cystic fibrosis: a complex fungal and bacterial community\u2013implications for therapeutic management","volume":"7","author":"Delhaes","year":"2012","journal-title":"PLoS One"},{"key":"10.1016\/j.jinf.2016.04.022_bib29","doi-asserted-by":"crossref","first-page":"425","DOI":"10.1093\/cid\/cir399","article-title":"Inflammatory responses to individual microorganisms in the lungs of children with cystic fibrosis","volume":"53","author":"Gangell","year":"2011","journal-title":"Clin Infect Dis"},{"key":"10.1016\/j.jinf.2016.04.022_bib30","doi-asserted-by":"crossref","first-page":"609","DOI":"10.1358\/dnp.2006.19.10.1068008","article-title":"Neutrophilic inflammation as a major determinant in the progression of cystic fibrosis","volume":"19","author":"Tirouvanziam","year":"2006","journal-title":"Drug News Perspect"},{"key":"10.1016\/j.jinf.2016.04.022_bib31","doi-asserted-by":"crossref","first-page":"75","DOI":"10.1164\/rccm.201011-1892OC","article-title":"Infection, inflammation, and lung function decline in infants with cystic fibrosis","volume":"184","author":"Pillarisetti","year":"2011","journal-title":"Am J Respir Crit Care Med"},{"key":"10.1016\/j.jinf.2016.04.022_bib32","doi-asserted-by":"crossref","first-page":"e36077","DOI":"10.1371\/journal.pone.0036077","article-title":"Treatment of Aspergillus fumigatus in patients with cystic fibrosis: a randomized, placebo-controlled pilot study","volume":"7","author":"Aaron","year":"2012","journal-title":"PLoS One"},{"key":"10.1016\/j.jinf.2016.04.022_bib33","doi-asserted-by":"crossref","first-page":"73","DOI":"10.1111\/j.1749-6632.2012.06816.x","article-title":"Aspergillus bronchitis without significant immunocompromise","volume":"1272","author":"Chrdle","year":"2012","journal-title":"Ann N Y Acad Sci"},{"key":"10.1016\/j.jinf.2016.04.022_bib34","doi-asserted-by":"crossref","first-page":"464","DOI":"10.1034\/j.1399-3003.2000.016003464.x","article-title":"Allergic bronchopulmonary aspergillosis in cystic fibrosis. A European epidemiological study. Epidemiologic Registry of Cystic Fibrosis","volume":"16","author":"Mastella","year":"2000","journal-title":"Eur Respir J"},{"key":"10.1016\/j.jinf.2016.04.022_bib35","doi-asserted-by":"crossref","first-page":"37","DOI":"10.1016\/j.prrv.2009.01.001","article-title":"Diagnosing allergic bronchopulmonary aspergillosis in children with cystic fibrosis","volume":"10","author":"Thia","year":"2009","journal-title":"Paediatr Respir Rev"},{"key":"10.1016\/j.jinf.2016.04.022_bib36","doi-asserted-by":"crossref","first-page":"1765","DOI":"10.1111\/cea.12595","article-title":"Prevalence of Aspergillus sensitization and allergic bronchopulmonary aspergillosis in cystic fibrosis: systematic review and meta-analysis","volume":"45","author":"Maturu","year":"2015","journal-title":"Clin Exp Allergy"},{"key":"10.1016\/j.jinf.2016.04.022_bib37","doi-asserted-by":"crossref","first-page":"842","DOI":"10.3109\/00365548.2012.695454","article-title":"Assessment of Aspergillus sensitization or persistent carriage as a factor in lung function impairment in cystic fibrosis patients","volume":"44","author":"Fillaux","year":"2012","journal-title":"Scand J Infect Dis"},{"key":"10.1016\/j.jinf.2016.04.022_bib38","doi-asserted-by":"crossref","first-page":"1902","DOI":"10.1164\/ajrccm.155.6.9196093","article-title":"Sensitization to Aspergillus fumigatus and lung function in children with cystic fibrosis","volume":"155","author":"Wojnarowski","year":"1997","journal-title":"Am J Respir Crit Care Med"},{"key":"10.1016\/j.jinf.2016.04.022_bib39","doi-asserted-by":"crossref","first-page":"1211","DOI":"10.1164\/rccm.200603-423OC","article-title":"Effect of allergic bronchopulmonary aspergillosis on lung function in children with cystic fibrosis","volume":"174","author":"Kraemer","year":"2006","journal-title":"Am J Respir Crit Care Med"},{"key":"10.1016\/j.jinf.2016.04.022_bib40","doi-asserted-by":"crossref","first-page":"67","DOI":"10.1016\/j.prrv.2005.09.003","article-title":"Allergic bronchopulmonary aspergillosis in paediatric cystic fibrosis patients","volume":"7","author":"de Almeida","year":"2006","journal-title":"Paediatr Respir Rev"},{"key":"10.1016\/j.jinf.2016.04.022_bib41","doi-asserted-by":"crossref","first-page":"598","DOI":"10.1097\/MCP.0b013e32833e24a6","article-title":"Allergic bronchopulmonary aspergillosis and Aspergillus infection in cystic fibrosis","volume":"16","author":"Moss","year":"2010","journal-title":"Curr Opin Pulm Med"},{"key":"10.1016\/j.jinf.2016.04.022_bib42","first-page":"CD002204","article-title":"Antifungal therapies for allergic bronchopulmonary aspergillosis in people with cystic fibrosis","volume":"11","author":"Elphick","year":"2014","journal-title":"Cochrane Database Syst Rev"},{"key":"10.1016\/j.jinf.2016.04.022_bib43","doi-asserted-by":"crossref","first-page":"1210","DOI":"10.1111\/cea.12333","article-title":"Antifungal treatment in allergic bronchopulmonary aspergillosis with and without cystic fibrosis: a systematic review","volume":"44","author":"Moreira","year":"2014","journal-title":"Clin Exp Allergy"},{"key":"10.1016\/j.jinf.2016.04.022_bib44","doi-asserted-by":"crossref","first-page":"215","DOI":"10.1016\/j.jcf.2005.05.019","article-title":"Voriconazole therapy in children with cystic fibrosis","volume":"4","author":"Hilliard","year":"2005","journal-title":"J Cyst Fibros"},{"key":"10.1016\/j.jinf.2016.04.022_bib45","doi-asserted-by":"crossref","first-page":"604","DOI":"10.1136\/archdischild-2011-301570","article-title":"The oral corticosteroid-sparing effect of omalizumab in children with severe asthma","volume":"97","author":"Brodlie","year":"2012","journal-title":"Arch Dis Child"},{"key":"10.1016\/j.jinf.2016.04.022_bib46","doi-asserted-by":"crossref","first-page":"503","DOI":"10.1002\/ppul.22937","article-title":"Omalizumab therapy for allergic bronchopulmonary aspergillosis in children with cystic fibrosis: a synthesis of published evidence","volume":"49","author":"Tanou","year":"2014","journal-title":"Pediatr Pulmonol"},{"key":"10.1016\/j.jinf.2016.04.022_bib47","doi-asserted-by":"crossref","first-page":"363","DOI":"10.1378\/chest.110.2.363","article-title":"A 12-year longitudinal study of Aspergillus sensitivity in patients with cystic fibrosis","volume":"110","author":"Hutcheson","year":"1996","journal-title":"Chest"},{"key":"10.1016\/j.jinf.2016.04.022_bib48","doi-asserted-by":"crossref","first-page":"3669","DOI":"10.2174\/13816128113199990349","article-title":"Immune response, diagnosis and treatment of allergic bronchopulmonary aspergillosis in cystic fibrosis lung disease","volume":"19","author":"Eickmeier","year":"2013","journal-title":"Curr Pharm Des"},{"key":"10.1016\/j.jinf.2016.04.022_bib49","doi-asserted-by":"crossref","first-page":"219","DOI":"10.1159\/000346568","article-title":"Cystic fibrosis transmembrane conductance regulator recruitment to phagosomes in neutrophils","volume":"5","author":"Zhou","year":"2013","journal-title":"J Innate Imm"},{"key":"10.1016\/j.jinf.2016.04.022_bib50","doi-asserted-by":"crossref","first-page":"611","DOI":"10.1002\/cyto.a.22456","article-title":"Detection of CFTR protein in human leukocytes by flow cytometry","volume":"85","author":"Johansson","year":"2014","journal-title":"Cytom A"},{"key":"10.1016\/j.jinf.2016.04.022_bib51","doi-asserted-by":"crossref","first-page":"108","DOI":"10.1016\/j.biocel.2014.01.017","article-title":"Current concepts of immune dysregulation in cystic fibrosis","volume":"52","author":"Rieber","year":"2014","journal-title":"Int J Biochem Cell Biol"},{"key":"10.1016\/j.jinf.2016.04.022_bib52","doi-asserted-by":"crossref","first-page":"715","DOI":"10.1165\/rcmb.2011-0399RT","article-title":"Immune responses in cystic fibrosis: are they intrinsically defective?","volume":"46","author":"Ratner","year":"2012","journal-title":"Am J Respir Cell Mol Biol"},{"key":"10.1016\/j.jinf.2016.04.022_bib53","doi-asserted-by":"crossref","first-page":"221","DOI":"10.1007\/s00011-007-6187-2","article-title":"Is cystic fibrosis a TH17 disease?","volume":"56","author":"Dubin","year":"2007","journal-title":"Inflamm Res"},{"key":"10.1016\/j.jinf.2016.04.022_bib54","doi-asserted-by":"crossref","first-page":"638","DOI":"10.1093\/infdis\/175.3.638","article-title":"Nasal and bronchoalveolar lavage fluid cytokines in early cystic fibrosis","volume":"175","author":"Noah","year":"1997","journal-title":"J Infect Dis"},{"key":"10.1016\/j.jinf.2016.04.022_bib55","doi-asserted-by":"crossref","first-page":"186","DOI":"10.1164\/ajrccm.160.1.9808096","article-title":"Quantitation of inflammatory responses to bacteria in young cystic fibrosis and control patients","volume":"160","author":"Muhlebach","year":"1999","journal-title":"Am J Respir Crit Care Med"},{"key":"10.1016\/j.jinf.2016.04.022_bib56","doi-asserted-by":"crossref","first-page":"2111","DOI":"10.1164\/ajrccm.152.6.8520783","article-title":"Inflammatory cytokines in cystic fibrosis lungs","volume":"152","author":"Bonfield","year":"1995","journal-title":"Am J Respir Crit Care Med"},{"key":"10.1016\/j.jinf.2016.04.022_bib57","first-page":"1075","article-title":"Early pulmonary inflammation in infants with cystic fibrosis","volume":"151","author":"Khan","year":"1995","journal-title":"Am J Respir Crit Care Med"},{"key":"10.1016\/j.jinf.2016.04.022_bib58","doi-asserted-by":"crossref","first-page":"1345","DOI":"10.1189\/jlb.0907658","article-title":"The role of chloride anion and CFTR in killing of Pseudomonas aeruginosa by normal and CF neutrophils","volume":"83","author":"Painter","year":"2008","journal-title":"J Leuk Biol"},{"key":"10.1016\/j.jinf.2016.04.022_bib59","doi-asserted-by":"crossref","first-page":"e19970","DOI":"10.1371\/journal.pone.0019970","article-title":"Dysfunctional CFTR alters the bactericidal activity of human macrophages against Pseudomonas aeruginosa","volume":"6","author":"Del Porto","year":"2011","journal-title":"PLoS One"},{"key":"10.1016\/j.jinf.2016.04.022_bib60","doi-asserted-by":"crossref","first-page":"6990","DOI":"10.4049\/jimmunol.1100396","article-title":"Abnormal trafficking and degradation of TLR4 underlie the elevated inflammatory response in cystic fibrosis","volume":"186","author":"Bruscia","year":"2011","journal-title":"J Immunol"},{"key":"10.1016\/j.jinf.2016.04.022_bib61","doi-asserted-by":"crossref","first-page":"922","DOI":"10.1165\/rcmb.2010-0224OC","article-title":"Lack of cystic fibrosis transmembrane conductance regulator in CD3+ lymphocytes leads to aberrant cytokine secretion and hyperinflammatory adaptive immune responses","volume":"44","author":"Mueller","year":"2011","journal-title":"Am J Respir Cell Mol Bio"},{"key":"10.1016\/j.jinf.2016.04.022_bib62","doi-asserted-by":"crossref","first-page":"18825","DOI":"10.1073\/pnas.0904709106","article-title":"Rescue of CF airway epithelial cell function in\u00a0vitro by a CFTR potentiator, VX-770","volume":"106","author":"Van Goor","year":"2009","journal-title":"Proc Natl Acad Sci USA"},{"key":"10.1016\/j.jinf.2016.04.022_bib63","doi-asserted-by":"crossref","first-page":"1663","DOI":"10.1056\/NEJMoa1105185","article-title":"A CFTR potentiator in patients with cystic fibrosis and the G551D mutation","volume":"365","author":"Ramsey","year":"2011","journal-title":"N Engl J Med"},{"key":"10.1016\/j.jinf.2016.04.022_bib64","doi-asserted-by":"crossref","first-page":"1219","DOI":"10.1164\/rccm.201301-0153OC","article-title":"Efficacy and safety of ivacaftor in patients aged 6 to 11 years with cystic fibrosis with a G551D mutation","volume":"187","author":"Davies","year":"2013","journal-title":"Am J Respir Crit Care Med"},{"key":"10.1016\/j.jinf.2016.04.022_bib65","doi-asserted-by":"crossref","first-page":"703","DOI":"10.1093\/cid\/ciu944","article-title":"Pseudomonas aeruginosa in cystic fibrosis patients with G551D-CFTR treated with ivacaftor","volume":"60","author":"Heltshe","year":"2015","journal-title":"Clin Infect Dis"},{"key":"10.1016\/j.jinf.2016.04.022_bib66","doi-asserted-by":"crossref","first-page":"999","DOI":"10.1182\/blood-2014-02-555268","article-title":"A neutrophil intrinsic impairment affecting Rab27a and degranulation in cystic fibrosis is corrected by CFTR potentiator therapy","volume":"124","author":"Pohl","year":"2014","journal-title":"Blood"}],"container-title":["Journal of Infection"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0163445316300494?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0163445316300494?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2025,9,27]],"date-time":"2025-09-27T21:23:15Z","timestamp":1759008195000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0163445316300494"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2016,7]]},"references-count":66,"alternative-id":["S0163445316300494"],"URL":"https:\/\/doi.org\/10.1016\/j.jinf.2016.04.022","relation":{},"ISSN":["0163-4453"],"issn-type":[{"value":"0163-4453","type":"print"}],"subject":[],"published":{"date-parts":[[2016,7]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"Aspergillus infections in cystic fibrosis","name":"articletitle","label":"Article Title"},{"value":"Journal of Infection","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.jinf.2016.04.022","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"\u00a9 2016 Published by Elsevier Ltd on behalf of The British Infection Association.","name":"copyright","label":"Copyright"}]}}