{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2024,9,16]],"date-time":"2024-09-16T13:13:39Z","timestamp":1726492419434},"reference-count":19,"publisher":"Elsevier BV","issue":"1-2","license":[{"start":{"date-parts":[[2010,10,1]],"date-time":"2010-10-01T00:00:00Z","timestamp":1285891200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Journal of the Neurological Sciences"],"published-print":{"date-parts":[[2010,10]]},"DOI":"10.1016\/j.jns.2010.07.004","type":"journal-article","created":{"date-parts":[[2010,8,3]],"date-time":"2010-08-03T09:24:49Z","timestamp":1280827489000},"page":"92-96","source":"Crossref","is-referenced-by-count":6,"title":["Frontotemporal lobar degeneration with motor neuron disease showing severe and circumscribed atrophy of anterior temporal lobes"],"prefix":"10.1016","volume":"297","author":[{"given":"Hiroya","family":"Kuwahara","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Kuniaki","family":"Tsuchiya","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Yukinobu","family":"Saito","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Zen","family":"Kobayashi","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Hiroshi","family":"Miyazaki","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Yoko","family":"Izumiyama","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Haruhiko","family":"Akiyama","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Tetsuaki","family":"Arai","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Hidehiro","family":"Mizusawa","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"78","reference":[{"key":"10.1016\/j.jns.2010.07.004_bb0005","doi-asserted-by":"crossref","first-page":"1546","DOI":"10.1212\/WNL.51.6.1546","article-title":"Frontotemporal lobar degeneration: a consensus on clinical diagnostic criteria","volume":"51","author":"Neary","year":"1998","journal-title":"Neurology"},{"key":"10.1016\/j.jns.2010.07.004_bb0010","doi-asserted-by":"crossref","first-page":"5","DOI":"10.1007\/s00401-007-0237-2","article-title":"Consortium for frontotemporal lobar degeneration. Neuropathologic diagnostic and nosologic criteria for frontotemporal lobar degeneration: consensus of the consortium for frontotemporal lobar degeneration","volume":"114","author":"Cairns","year":"2007","journal-title":"Acta Neuropathol"},{"key":"10.1016\/j.jns.2010.07.004_bb0015","doi-asserted-by":"crossref","first-page":"15","DOI":"10.1007\/s00401-008-0460-5","article-title":"Nomenclature for neuropathologic subtypes of frontotemporal lobar degeneration: consensus recommendations","volume":"117","author":"Mackenzie","year":"2009","journal-title":"Acta Neuropathol"},{"key":"10.1016\/j.jns.2010.07.004_bb0020","doi-asserted-by":"crossref","first-page":"702","DOI":"10.1038\/31508","article-title":"Association of missense and 5\u2032-splice-site mutations in tau with the inherited dementia FTDP-17","volume":"393","author":"Hutton","year":"1998","journal-title":"Nature"},{"key":"10.1016\/j.jns.2010.07.004_bb0025","doi-asserted-by":"crossref","first-page":"916","DOI":"10.1038\/nature05016","article-title":"Mutations in progranulin cause tau-negative frontotemporal dementia linked to chromosome 17","volume":"442","author":"Baker","year":"2006","journal-title":"Nature"},{"key":"10.1016\/j.jns.2010.07.004_bb0030","doi-asserted-by":"crossref","first-page":"920","DOI":"10.1038\/nature05017","article-title":"Null mutations in progranulin cause ubiquitin-positive frontotemporal dementia linked to chromosome 17q21","volume":"442","author":"Cruts","year":"2006","journal-title":"Nature"},{"key":"10.1016\/j.jns.2010.07.004_bb0035","doi-asserted-by":"crossref","first-page":"152","DOI":"10.1097\/nen.0b013e31803020b9","article-title":"TDP-43 in the ubiquitin pathology of frontotemporal dementia with VCP gene mutations","volume":"66","author":"Neumann","year":"2007","journal-title":"J Neuropathol Exp Neurol"},{"key":"10.1016\/j.jns.2010.07.004_bb0040","doi-asserted-by":"crossref","first-page":"87","DOI":"10.1111\/j.1440-1789.2003.00544.x","article-title":"Amyotrophic lateral sclerosis with dementia: the clinicopathological spectrum","volume":"24","author":"Yoshida","year":"2004","journal-title":"Neuropathology"},{"key":"10.1016\/j.jns.2010.07.004_bb0045","doi-asserted-by":"crossref","first-page":"60","DOI":"10.1002\/ana.21425","article-title":"Phosphorylated TDP-43 in frontotemporal lobar degeneration and amyotrophic lateral sclerosis","volume":"64","author":"Hasegawa","year":"2008","journal-title":"Ann Neurol"},{"key":"10.1016\/j.jns.2010.07.004_bb0050","doi-asserted-by":"crossref","first-page":"409","DOI":"10.1016\/j.expneurol.2007.11.019","article-title":"Relationship of phosphorylated alpha-synuclein and tau accumulation to Abeta deposition in the cerebral cortex of dementia with Lewy bodies","volume":"210","author":"Obi","year":"2008","journal-title":"Exp Neurol"},{"key":"10.1016\/j.jns.2010.07.004_bb0055","doi-asserted-by":"crossref","first-page":"81","DOI":"10.1007\/PL00007411","article-title":"Rapidly progressive aphasia and motor neuron disease: a clinical, radiological, and pathological study of an autopsy case with circumscribed lobar atrophy","volume":"99","author":"Tsuchiya","year":"2000","journal-title":"Acta Neuropathol"},{"key":"10.1016\/j.jns.2010.07.004_bb0060","doi-asserted-by":"crossref","first-page":"644","DOI":"10.1212\/01.wnl.0000225184.14578.d3","article-title":"Valosin-containing protein gene mutations: clinical and neuropathologic features","volume":"67","author":"Guyant-Mar\u00e9chal","year":"2006","journal-title":"Neurology"},{"key":"10.1016\/j.jns.2010.07.004_bb0065","doi-asserted-by":"crossref","first-page":"953","DOI":"10.1136\/jnnp.47.9.953","article-title":"Presenile dementia with motor neuron disease in Japan: clinico-pathological review of 26 cases","volume":"47","author":"Mitsuyama","year":"1984","journal-title":"J Neurol Neurosurg Psychiatry"},{"key":"10.1016\/j.jns.2010.07.004_bb0070","doi-asserted-by":"crossref","first-page":"645","DOI":"10.1212\/01.wnl.0000173178.67986.7f","article-title":"Survival in two variants of tau-negative frontotemporal lobar degeneration: FTLD-U vs FTLD\u2013MND","volume":"65","author":"Josephs","year":"2005","journal-title":"Neurology"},{"key":"10.1016\/j.jns.2010.07.004_bb0075","doi-asserted-by":"crossref","first-page":"216","DOI":"10.1212\/WNL.57.2.216","article-title":"Differing patterns of temporal atrophy in Alzheimer's disease and semantic dementia","volume":"57","author":"Galton","year":"2001","journal-title":"Neurology"},{"key":"10.1016\/j.jns.2010.07.004_bb0080","doi-asserted-by":"crossref","first-page":"433","DOI":"10.1002\/ana.92","article-title":"Patterns of temporal lobe atrophy in semantic dementia and Alzheimer's disease","volume":"49","author":"Chan","year":"2001","journal-title":"Ann Neurol"},{"key":"10.1016\/j.jns.2010.07.004_bb0085","doi-asserted-by":"crossref","first-page":"1783","DOI":"10.1093\/brain\/115.6.1783","article-title":"Semantic dementia. Progressive fluent aphasia with temporal lobe atrophy","volume":"115","author":"Hodges","year":"1992","journal-title":"Brain"},{"key":"10.1016\/j.jns.2010.07.004_bb0090","doi-asserted-by":"crossref","first-page":"1","DOI":"10.1093\/brain\/118.1.1","article-title":"Progressive prosopagnosia associated with selective right temporal lobe atrophy. A new syndrome?","volume":"118","author":"Evans","year":"1995","journal-title":"Brain"},{"key":"10.1016\/j.jns.2010.07.004_bb0095","doi-asserted-by":"crossref","first-page":"429","DOI":"10.1007\/s00401-009-0493-4","article-title":"Clinicopathological characterization of Pick's disease versus frontotemporal lobar degeneration with ubiquitin\/TDP-43-positive inclusions","volume":"117","author":"Yokota","year":"2009","journal-title":"Acta Neuropathol"}],"container-title":["Journal of the Neurological Sciences"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0022510X10003059?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0022510X10003059?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2018,12,9]],"date-time":"2018-12-09T03:26:52Z","timestamp":1544326012000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0022510X10003059"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2010,10]]},"references-count":19,"journal-issue":{"issue":"1-2","published-print":{"date-parts":[[2010,10]]}},"alternative-id":["S0022510X10003059"],"URL":"https:\/\/doi.org\/10.1016\/j.jns.2010.07.004","relation":{},"ISSN":["0022-510X"],"issn-type":[{"type":"print","value":"0022-510X"}],"subject":[],"published":{"date-parts":[[2010,10]]}}}