{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,4]],"date-time":"2026-09-04T02:13:34Z","timestamp":1788488014168,"version":"build-2803163510"},"reference-count":25,"publisher":"Elsevier BV","license":[{"start":{"date-parts":[[2026,11,1]],"date-time":"2026-11-01T00:00:00Z","timestamp":1793491200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2026,11,1]],"date-time":"2026-11-01T00:00:00Z","timestamp":1793491200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/legal\/tdmrep-license"},{"start":{"date-parts":[[2026,11,1]],"date-time":"2026-11-01T00:00:00Z","timestamp":1793491200000},"content-version":"stm-asf","delay-in-days":0,"URL":"https:\/\/doi.org\/10.15223\/policy-017"},{"start":{"date-parts":[[2026,11,1]],"date-time":"2026-11-01T00:00:00Z","timestamp":1793491200000},"content-version":"stm-asf","delay-in-days":0,"URL":"https:\/\/doi.org\/10.15223\/policy-037"},{"start":{"date-parts":[[2026,11,1]],"date-time":"2026-11-01T00:00:00Z","timestamp":1793491200000},"content-version":"stm-asf","delay-in-days":0,"URL":"https:\/\/doi.org\/10.15223\/policy-012"},{"start":{"date-parts":[[2026,11,1]],"date-time":"2026-11-01T00:00:00Z","timestamp":1793491200000},"content-version":"stm-asf","delay-in-days":0,"URL":"https:\/\/doi.org\/10.15223\/policy-029"},{"start":{"date-parts":[[2026,11,1]],"date-time":"2026-11-01T00:00:00Z","timestamp":1793491200000},"content-version":"stm-asf","delay-in-days":0,"URL":"https:\/\/doi.org\/10.15223\/policy-004"}],"content-domain":{"domain":["clinicalkey.com","clinicalkey.com.au","clinicalkey.es","clinicalkey.fr","clinicalkey.jp","jocn-journal.com","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Journal of Clinical Neuroscience"],"published-print":{"date-parts":[[2026,11]]},"DOI":"10.1016\/j.jocn.2026.112219","type":"journal-article","created":{"date-parts":[[2026,7,24]],"date-time":"2026-07-24T17:57:18Z","timestamp":1784915838000},"page":"112219","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":0,"special_numbering":"C","title":["Cerebrovascular involvement in Erdheim-Chester disease: a case report and systematic literature review"],"prefix":"10.1016","volume":"153","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-3487-3892","authenticated-orcid":false,"given":"Claire","family":"Delacotte","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Charlotte","family":"Arnaud","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Hubert","family":"de Boysson","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Achille","family":"Aouba","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-8887-3233","authenticated-orcid":false,"given":"Samuel","family":"Deshayes","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"key":"10.1016\/j.jocn.2026.112219_b0005","doi-asserted-by":"crossref","first-page":"1929","DOI":"10.1182\/blood.2019003507","article-title":"Erdheim-Chester disease: consensus recommendations for evaluation, diagnosis, and treatment in the molecular era","volume":"135","author":"Goyal","year":"2020","journal-title":"Blood"},{"key":"10.1016\/j.jocn.2026.112219_b0010","doi-asserted-by":"crossref","first-page":"e2746","DOI":"10.1212\/WNL.0000000000010748","article-title":"Central nervous system involvement in Erdheim-Chester disease: an observational cohort study","volume":"95","author":"Cohen Aubart","year":"2020","journal-title":"Neurology"},{"key":"10.1016\/j.jocn.2026.112219_b0015","article-title":"PRISMA 2020 explanation and elaboration: updated guidance and exemplars for reporting systematic reviews","volume":"372","author":"Page","year":"2021","journal-title":"BMJ"},{"key":"10.1016\/j.jocn.2026.112219_b0020","doi-asserted-by":"crossref","first-page":"576","DOI":"10.1002\/mds.870130335","article-title":"Erdheim-Chester disease with extensive intraaxial brain stem lesions presenting as a progressive cerebellar syndrome","volume":"13","author":"Evidente","year":"1998","journal-title":"Mov Disord"},{"key":"10.1016\/j.jocn.2026.112219_b0025","doi-asserted-by":"crossref","first-page":"586","DOI":"10.1148\/radiol.10090320","article-title":"Cerebral, facial, and orbital involvement in Erdheim-Chester disease: CT and MR imaging findings","volume":"255","author":"Drier","year":"2010","journal-title":"Radiology"},{"key":"10.1016\/j.jocn.2026.112219_b0030","first-page":"70","article-title":"A case of Erdheim Chester disease with multiple cerebral infarcts","volume":"10","author":"Pana","year":"2015","journal-title":"Internal Journal of Stroke"},{"key":"10.1016\/j.jocn.2026.112219_b0035","doi-asserted-by":"crossref","first-page":"e63","DOI":"10.1016\/j.jstrokecerebrovasdis.2016.01.042","article-title":"Erdheim-Chester Disease: an Unusual Cause of Intracranial Vasculitis and Progressive Leukoencephalopathy","volume":"25","author":"Sagnier","year":"2016","journal-title":"J Stroke Cerebrovasc Dis"},{"key":"10.1016\/j.jocn.2026.112219_b0040","doi-asserted-by":"crossref","first-page":"e4813","DOI":"10.1097\/MD.0000000000004813","article-title":"Long-term outcome of basilar stenosis in Erdheim-Chester disease: a case report","volume":"95","author":"Mathis","year":"2016","journal-title":"Medicine (Baltimore)"},{"key":"10.1016\/j.jocn.2026.112219_b0045","doi-asserted-by":"crossref","first-page":"e153","DOI":"10.1016\/j.jstrokecerebrovasdis.2017.04.029","article-title":"Association between Ischemic Stroke and Erdheim-Chester Disease: a Case Report and Review of Literature","volume":"26","author":"Fargeot","year":"2017","journal-title":"J Stroke Cerebrovasc Dis"},{"key":"10.1016\/j.jocn.2026.112219_b0050","first-page":"120","article-title":"Unusual Manifestations of a Rare Clinical Entity: Erdheim-Chester Disease","volume":"26","author":"Martins","year":"2019","journal-title":"Med Interna"},{"key":"10.1016\/j.jocn.2026.112219_b0055","doi-asserted-by":"crossref","first-page":"1179","DOI":"10.2214\/AJR.19.21523","article-title":"Multisystemic Imaging Findings in chinese patients with Erdheim-Chester Disease","volume":"213","author":"Wang","year":"2019","journal-title":"AJR Am J Roentgenol"},{"key":"10.1016\/j.jocn.2026.112219_b0060","doi-asserted-by":"crossref","DOI":"10.1212\/WNL.94.15_supplement.4915","article-title":"A rare presentation of intracranial vasculopathy in a patient with erdheim-Chester disease (4915)","volume":"94","author":"Hassett","year":"2020","journal-title":"Neurology"},{"key":"10.1016\/j.jocn.2026.112219_b0065","doi-asserted-by":"crossref","DOI":"10.1161\/CIRCIMAGING.119.010123","article-title":"Multisystem Erdheim-Chester Disease with Extensive Pericardial and Vascular Involvement","volume":"13","author":"S\u00e1nchez-Nadales","year":"2020","journal-title":"Circ Cardiovasc Imaging"},{"key":"10.1016\/j.jocn.2026.112219_b0070","doi-asserted-by":"crossref","first-page":"746","DOI":"10.1159\/000516803","article-title":"Cerebral Microvascular Erdheim-Chester Disease: a Perivascular Hematopoietic Vasculopathy","volume":"50","author":"Moussouttas","year":"2021","journal-title":"Cerebrovasc Dis"},{"key":"10.1016\/j.jocn.2026.112219_b0075","article-title":"Double Subclavian Steal Syndrome As initial Manifestation of Erdheim-Chester Disease: a Case Report","volume":"15","author":"Finsterer","year":"2023","journal-title":"Cureus"},{"key":"10.1016\/j.jocn.2026.112219_b0080","doi-asserted-by":"crossref","first-page":"4070","DOI":"10.1182\/blood-2010-04-279240","article-title":"Rationale and efficacy of interleukin-1 targeting in Erdheim-Chester disease","volume":"116","author":"Aouba","year":"2010","journal-title":"Blood"},{"key":"10.1016\/j.jocn.2026.112219_b0085","doi-asserted-by":"crossref","first-page":"576","DOI":"10.1002\/mds.870130335","article-title":"Erdheim-Chester Disease with Extensive Intraaxial Brain Stem Lesions Presenting as a Progressive Cerebellar Syndrome","volume":"13","author":"Evidente","year":"1998","journal-title":"Mov Disord"},{"key":"10.1016\/j.jocn.2026.112219_b0090","doi-asserted-by":"crossref","first-page":"986","DOI":"10.1093\/jnen\/nlx095","article-title":"CNS Erdheim-Chester Disease: a Challenge to Diagnose","volume":"76","author":"Pan","year":"2017","journal-title":"J Neuropathol Exp Neurol"},{"key":"10.1016\/j.jocn.2026.112219_b0095","doi-asserted-by":"crossref","first-page":"399","DOI":"10.1177\/1971400917710251","article-title":"Misdiagnosis: CNS Erdheim-Chester disease mimicking CLIPPERS","volume":"31","author":"Berkman","year":"2018","journal-title":"Neuroradiol J"},{"key":"10.1016\/j.jocn.2026.112219_b0100","first-page":"1115","article-title":"Erdheim-Chester disease mimicking a primary brain tumor","volume":"100","author":"Rushing","year":"2004","journal-title":"Case report J Neurosurg"},{"key":"10.1016\/j.jocn.2026.112219_b0105","doi-asserted-by":"crossref","first-page":"1647","DOI":"10.1136\/ard-2022-223480","article-title":"2022 American College of Rheumatology\/EULAR classification criteria for giant cell arteritis","volume":"81","author":"Ponte","year":"2022","journal-title":"Ann Rheum Dis"},{"key":"10.1016\/j.jocn.2026.112219_b0110","doi-asserted-by":"crossref","first-page":"357","DOI":"10.1182\/bloodadvances.2016001784","article-title":"The clinical spectrum of Erdheim-Chester disease: an observational cohort study","volume":"1","author":"Estrada-Veras","year":"2017","journal-title":"Blood Adv"},{"key":"10.1016\/j.jocn.2026.112219_b0115","doi-asserted-by":"crossref","first-page":"21","DOI":"10.1097\/BOR.0000000000000229","article-title":"Management of primary and secondary central nervous system vasculitis","volume":"28","author":"Salvarani","year":"2016","journal-title":"Curr Opin Rheumatol"},{"key":"10.1016\/j.jocn.2026.112219_b0120","doi-asserted-by":"crossref","first-page":"3017","DOI":"10.1007\/s00296-013-2814-0","article-title":"Characteristics of cerebrovascular accidents at time of diagnosis in a series of 98 patients with giant cell arteritis","volume":"33","author":"Zenone","year":"2013","journal-title":"Rheumatol Int"},{"key":"10.1016\/j.jocn.2026.112219_b0125","doi-asserted-by":"crossref","unstructured":"Aouba A, Bienvenu B, Launay D, Hermine O. Role of iconographic examinations in the treatment algorithm in Erdheim-Chester disease. J Clin Oncol 2011;29:4466\u20137; author reply 4468-4469. https:\/\/doi.org\/10.1200\/JCO.2011.37.9834.","DOI":"10.1200\/JCO.2011.37.9834"}],"container-title":["Journal of Clinical Neuroscience"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S096758682600370X?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S096758682600370X?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2026,9,4]],"date-time":"2026-09-04T01:44:23Z","timestamp":1788486263000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S096758682600370X"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2026,11]]},"references-count":25,"alternative-id":["S096758682600370X"],"URL":"https:\/\/doi.org\/10.1016\/j.jocn.2026.112219","relation":{},"ISSN":["0967-5868"],"issn-type":[{"value":"0967-5868","type":"print"}],"subject":[],"published":{"date-parts":[[2026,11]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"Cerebrovascular involvement in Erdheim-Chester disease: a case report and systematic literature review","name":"articletitle","label":"Article Title"},{"value":"Journal of Clinical Neuroscience","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.jocn.2026.112219","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"\u00a9 2026 Elsevier Ltd. All rights are reserved, including those for text and data mining, AI training, and similar technologies.","name":"copyright","label":"Copyright"}],"article-number":"112219"}}