{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,4]],"date-time":"2026-09-04T04:48:25Z","timestamp":1788497305085,"version":"build-2803163510"},"reference-count":17,"publisher":"Elsevier BV","issue":"6","license":[{"start":{"date-parts":[[2024,12,1]],"date-time":"2024-12-01T00:00:00Z","timestamp":1733011200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2024,12,1]],"date-time":"2024-12-01T00:00:00Z","timestamp":1733011200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/legal\/tdmrep-license"},{"start":{"date-parts":[[2025,10,28]],"date-time":"2025-10-28T00:00:00Z","timestamp":1761609600000},"content-version":"am","delay-in-days":331,"URL":"http:\/\/www.elsevier.com\/open-access\/userlicense\/1.0\/"}],"funder":[{"DOI":"10.13039\/100000002","name":"National Institutes of Health","doi-asserted-by":"publisher","id":[{"id":"10.13039\/100000002","id-type":"DOI","asserted-by":"publisher"}]},{"DOI":"10.13039\/100009633","name":"NICHD","doi-asserted-by":"publisher","award":["HD009003-01"],"award-info":[{"award-number":["HD009003-01"]}],"id":[{"id":"10.13039\/100009633","id-type":"DOI","asserted-by":"publisher"}]},{"DOI":"10.13039\/100009633","name":"NICHD","doi-asserted-by":"publisher","award":["Z1A HD008985"],"award-info":[{"award-number":["Z1A HD008985"]}],"id":[{"id":"10.13039\/100009633","id-type":"DOI","asserted-by":"publisher"}]}],"content-domain":{"domain":["clinicalkey.com","clinicalkey.com.au","clinicalkey.es","clinicalkey.fr","clinicalkey.jp","jpagonline.org","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Journal of Pediatric and Adolescent Gynecology"],"published-print":{"date-parts":[[2024,12]]},"DOI":"10.1016\/j.jpag.2024.06.005","type":"journal-article","created":{"date-parts":[[2024,6,25]],"date-time":"2024-06-25T19:43:16Z","timestamp":1719344596000},"page":"625-628","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":1,"title":["Kaposiform Lymphangiomatosis as a Cause of Vaginal Bleeding &amp; Discharge: A Case Report"],"prefix":"10.1016","volume":"37","author":[{"given":"Kirsten","family":"Das","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Sarah","family":"Sheppard","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Bhupender","family":"Yadav","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Joyce Tannenbaum","family":"Turner","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Miriam","family":"Bornhorst","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Alan H.","family":"Siegel","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jacqueline C.","family":"Yano","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Veronica","family":"Gomez Lobo","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"issue":"5","key":"10.1016\/j.jpag.2024.06.005_bib0001","doi-asserted-by":"crossref","first-page":"901","DOI":"10.1002\/pbc.25278","article-title":"Kaposiform lymphangiomatosis: unifying features of a heterogeneous disorder","volume":"62","author":"Fernandes","year":"2015","journal-title":"Pediatr Blood Cancer"},{"issue":"4","key":"10.1016\/j.jpag.2024.06.005_bib0002","doi-asserted-by":"crossref","first-page":"e30219","DOI":"10.1002\/pbc.30219","article-title":"Kaposiform lymphangiomatosis: diagnosis, pathogenesis, and treatment","volume":"70","author":"McDaniel","year":"2023","journal-title":"Pediatr Blood Cancer"},{"issue":"7","key":"10.1016\/j.jpag.2024.06.005_bib0003","doi-asserted-by":"crossref","first-page":"1517","DOI":"10.1038\/s41436-018-0390-0","article-title":"A somatic activating NRAS variant associated with Kaposiform lymphangiomatosis","volume":"21","author":"Barclay","year":"2019","journal-title":"Genet Med"},{"issue":"suppl 3","key":"10.1016\/j.jpag.2024.06.005_bib0004","doi-asserted-by":"crossref","first-page":"e28985","DOI":"10.1002\/pbc.28985","article-title":"How we approach the diagnosis and management of complex lymphatic anomalies","volume":"69","author":"Ricci","year":"2022","journal-title":"Pediatr Blood Cancer"},{"key":"10.1016\/j.jpag.2024.06.005_bib0005","doi-asserted-by":"crossref","first-page":"72","DOI":"10.1016\/j.humpath.2022.02.010","article-title":"Cellular variant of Kaposiform lymphangiomatosis: a report of three cases, expanding the morphologic and molecular genetic spectrum of this rare entity","volume":"122","author":"Allen-Rhoades","year":"2022","journal-title":"Hum Pathol"},{"key":"10.1016\/j.jpag.2024.06.005_bib0006","doi-asserted-by":"crossref","first-page":"e30419","DOI":"10.1002\/pbc.30419","article-title":"Pathogenic variants in PIK3CA are associated with clinical phenotypes of Kaposiform lymphangiomatosis, generalized lymphatic anomaly, and central conducting lymphatic anomaly","volume":"70","author":"Grenier","year":"2023","journal-title":"Pediatr Blood Cancer"},{"issue":"10","key":"10.1016\/j.jpag.2024.06.005_bib0007","doi-asserted-by":"crossref","first-page":"e12324","DOI":"10.15252\/emmm.202012324","article-title":"Kaposiform lymphangiomatosis effectively treated with MEK inhibition","volume":"12","author":"Foster","year":"2020","journal-title":"EMBO Mol Med"},{"issue":"7","key":"10.1016\/j.jpag.2024.06.005_bib0008","doi-asserted-by":"crossref","first-page":"1291","DOI":"10.1002\/pbc.25422","article-title":"Successful treatment of Kaposiform lymphangiomatosis with sirolimus","volume":"62","author":"Wang","year":"2015","journal-title":"Pediatr Blood Cancer"},{"issue":"1","key":"10.1016\/j.jpag.2024.06.005_bib0009","doi-asserted-by":"crossref","first-page":"260","DOI":"10.1186\/s13023-021-01893-3","article-title":"Sirolimus in the treatment of Kaposiform lymphangiomatosis","volume":"16","author":"Zhou","year":"2021","journal-title":"Orphanet J Rare Dis"},{"issue":"1","key":"10.1016\/j.jpag.2024.06.005_bib0010","doi-asserted-by":"crossref","first-page":"e203","DOI":"10.1542\/peds.2014-3673","article-title":"Vascular anomalies classification: recommendations from the International Society for the Study of Vascular Anomalies","volume":"136","author":"Wassef","year":"2015","journal-title":"Pediatrics"},{"issue":"4","key":"10.1016\/j.jpag.2024.06.005_bib0011","doi-asserted-by":"crossref","first-page":"2358","DOI":"10.3390\/ijms23042358","article-title":"ISSVA classification of vascular anomalies and molecular biology","volume":"23","author":"Kunimoto","year":"2022","journal-title":"Int J Mol Sci"},{"issue":"1","key":"10.1016\/j.jpag.2024.06.005_bib0012","doi-asserted-by":"crossref","first-page":"e28036","DOI":"10.1002\/pbc.28036","article-title":"Multidisciplinary guidelines for initial evaluation of complicated lymphatic anomalies-expert opinion consensus","volume":"67","author":"Iacobas","year":"2020","journal-title":"Pediatr Blood Cancer"},{"issue":"6","key":"10.1016\/j.jpag.2024.06.005_bib0013","doi-asserted-by":"crossref","first-page":"1530","DOI":"10.1038\/s41591-023-02364-x","article-title":"Genomic profiling informs diagnoses and treatment in vascular anomalies","volume":"29","author":"Li","year":"2023","journal-title":"Nat Med"},{"issue":"1","key":"10.1016\/j.jpag.2024.06.005_bib0014","doi-asserted-by":"crossref","first-page":"318","DOI":"10.1016\/j.jvs.2019.06.217","article-title":"Efficacy and safety of sirolimus in the treatment of vascular anomalies: a systematic review","volume":"71","author":"Freixo","year":"2020","journal-title":"J Vasc Surg"},{"issue":"6","key":"10.1016\/j.jpag.2024.06.005_bib0015","doi-asserted-by":"crossref","first-page":"1911","DOI":"10.1038\/s41390-022-01986-0","article-title":"Treatment of severe Kaposiform lymphangiomatosis positive for NRAS mutation by MEK inhibition","volume":"94","author":"Chowers","year":"2023","journal-title":"Pediatr Res"},{"issue":"1","key":"10.1016\/j.jpag.2024.06.005_bib0016","doi-asserted-by":"crossref","first-page":"163","DOI":"10.1007\/s10456-016-9537-2","article-title":"Angiopoietins as serum biomarkers for lymphatic anomalies","volume":"20","author":"Le Cras","year":"2017","journal-title":"Angiogenesis"},{"issue":"1","key":"10.1016\/j.jpag.2024.06.005_bib0017","doi-asserted-by":"crossref","first-page":"1","DOI":"10.1016\/j.jvscit.2019.10.003","article-title":"Vaginal discharge caused by lymphatic malformation identified by lymphoscintigraphy combined with T2-weighted magnetic resonance imaging","volume":"6","author":"Tang","year":"2020","journal-title":"J Vasc Surg Cases Innov Tech"}],"container-title":["Journal of Pediatric and Adolescent Gynecology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1083318824002353?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1083318824002353?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2026,5,12]],"date-time":"2026-05-12T12:23:33Z","timestamp":1778588613000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S1083318824002353"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2024,12]]},"references-count":17,"journal-issue":{"issue":"6","published-print":{"date-parts":[[2024,12]]}},"alternative-id":["S1083318824002353"],"URL":"https:\/\/doi.org\/10.1016\/j.jpag.2024.06.005","relation":{},"ISSN":["1083-3188"],"issn-type":[{"value":"1083-3188","type":"print"}],"subject":[],"published":{"date-parts":[[2024,12]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"Kaposiform Lymphangiomatosis as a Cause of Vaginal Bleeding & Discharge: A Case Report","name":"articletitle","label":"Article Title"},{"value":"Journal of Pediatric and Adolescent Gynecology","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.jpag.2024.06.005","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"Published by Elsevier Inc. on behalf of North American Society for Pediatric and Adolescent Gynecology.","name":"copyright","label":"Copyright"}]}}