{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,15]],"date-time":"2026-10-15T06:21:45Z","timestamp":1792045305544,"version":"4.4.0"},"reference-count":31,"publisher":"Elsevier BV","issue":"6","license":[{"start":{"date-parts":[[2006,6,1]],"date-time":"2006-06-01T00:00:00Z","timestamp":1149120000000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["The Journal of Pediatrics"],"published-print":{"date-parts":[[2006,6]]},"DOI":"10.1016\/j.jpeds.2006.01.004","type":"journal-article","created":{"date-parts":[[2006,6,12]],"date-time":"2006-06-12T12:47:11Z","timestamp":1150116431000},"page":"770-778","source":"Crossref","is-referenced-by-count":71,"title":["Renal replacement therapy in the treatment of confirmed or suspected inborn errors of metabolism"],"prefix":"10.1016","volume":"148","author":[{"given":"Kevin D.","family":"McBryde","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"David B.","family":"Kershaw","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Timothy E.","family":"Bunchman","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Norma J.","family":"Maxvold","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Theresa A.","family":"Mottes","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Timothy L.","family":"Kudelka","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Patrick D.","family":"Brophy","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"key":"10.1016\/j.jpeds.2006.01.004_bib1","doi-asserted-by":"crossref","first-page":"769","DOI":"10.1016\/S0022-3476(78)80147-4","article-title":"Severe hyperammonemia in a newborn infant with methylmalonyl-CoA mutase deficiency","volume":"92","author":"Packman","year":"1978","journal-title":"J Pediatr"},{"key":"10.1016\/j.jpeds.2006.01.004_bib2","doi-asserted-by":"crossref","first-page":"333","DOI":"10.1016\/0887-8994(92)90085-D","article-title":"Neurologic outcome of propionic acidemia","volume":"8","author":"Surtees","year":"1992","journal-title":"Pediatr Neurol"},{"key":"10.1016\/j.jpeds.2006.01.004_bib3","doi-asserted-by":"crossref","first-page":"1500","DOI":"10.1056\/NEJM198406073102304","article-title":"Neurologic outcome in children with inborn errors of urea synthesis","volume":"310","author":"Msall","year":"1984","journal-title":"N Engl J Med"},{"key":"10.1016\/j.jpeds.2006.01.004_bib4","doi-asserted-by":"crossref","first-page":"144","DOI":"10.1007\/BF02072492","article-title":"Intellectual performance of children with maple syrup urine disease","volume":"152","author":"Hilliges","year":"1993","journal-title":"Eur J Pediatr"},{"key":"10.1016\/j.jpeds.2006.01.004_bib5","doi-asserted-by":"crossref","first-page":"2","DOI":"10.1007\/BF03047365","article-title":"Neonatal management of organic acidurias","volume":"7","author":"Saudubray","year":"1984","journal-title":"J Inherit Metab Dis"},{"key":"10.1016\/j.jpeds.2006.01.004_bib6","doi-asserted-by":"crossref","first-page":"923","DOI":"10.1016\/S0022-3476(05)83044-6","article-title":"Prospective treatment of urea cycle disorders","volume":"119","author":"Maestri","year":"1991","journal-title":"J Pediatr"},{"key":"10.1016\/j.jpeds.2006.01.004_bib7","doi-asserted-by":"crossref","first-page":"67","DOI":"10.1016\/S0022-3476(79)80085-2","article-title":"Comparison of exchange transfusion, peritoneal dialysis, and hemodialysis for the treatment of hyperammonemia in an anuric newborn infant","volume":"95","author":"Donn","year":"1979","journal-title":"J Pediatr"},{"key":"10.1016\/j.jpeds.2006.01.004_bib8","doi-asserted-by":"crossref","first-page":"910","DOI":"10.1093\/ndt\/14.4.910","article-title":"Dialysis in neonates with inborn errors of metabolism","volume":"14","author":"Schaefer","year":"1999","journal-title":"Nephrol Dial Transplant"},{"key":"10.1016\/j.jpeds.2006.01.004_bib9","doi-asserted-by":"crossref","first-page":"903","DOI":"10.1038\/ki.1994.119","article-title":"Acute hemodialysis of infants weighing less than five kilograms","volume":"45","author":"Sadowski","year":"1994","journal-title":"Kidney Int"},{"key":"10.1016\/j.jpeds.2006.01.004_bib10","doi-asserted-by":"crossref","first-page":"531","DOI":"10.1159\/000013400","article-title":"Continuous venovenous hemodiafiltration in the treatment of acute hyperammonemia","volume":"18","author":"Braun","year":"1998","journal-title":"Am J Nephrol"},{"key":"10.1016\/j.jpeds.2006.01.004_bib11","doi-asserted-by":"crossref","first-page":"592","DOI":"10.1007\/s004670050512","article-title":"Hemodialysis catheter placement and recirculation in treatment of hyperammonemia","volume":"12","author":"Vats","year":"1998","journal-title":"Pediatr Nephrol"},{"key":"10.1016\/j.jpeds.2006.01.004_bib12","doi-asserted-by":"crossref","first-page":"147","DOI":"10.1007\/BF01800040","article-title":"Haemodialysis for metabolic decompensation in propionic acidaemia","volume":"10","author":"Roth","year":"1987","journal-title":"J Inherit Metab Dis"},{"key":"10.1016\/j.jpeds.2006.01.004_bib13","doi-asserted-by":"crossref","first-page":"125","DOI":"10.1016\/S0022-3476(05)81661-0","article-title":"Neonatal hemodialysis","volume":"116","author":"Rutledge","year":"1990","journal-title":"J Pediatr"},{"key":"10.1016\/j.jpeds.2006.01.004_bib14","doi-asserted-by":"crossref","first-page":"1192","DOI":"10.1016\/0140-6736(90)92807-T","article-title":"Continuous arteriovenous haemofiltration in hyperammonemia of newborn babies","volume":"336","author":"Sperl","year":"1990","journal-title":"Lancet"},{"key":"10.1016\/j.jpeds.2006.01.004_bib15","doi-asserted-by":"crossref","first-page":"158","DOI":"10.1007\/BF01800361","article-title":"Continuous arteriovenous haemofiltration in a neonate with hyperammonaemic coma due to citrullinaemia","volume":"15","author":"Sperl","year":"1992","journal-title":"J Inherit Metab Dis"},{"key":"10.1016\/j.jpeds.2006.01.004_bib16","doi-asserted-by":"crossref","first-page":"879","DOI":"10.1016\/S0022-3476(05)82198-5","article-title":"Continuous venovenous hemofiltration in the management of acute decompensation in inborn errors of metabolism","volume":"118","author":"Thompson","year":"1991","journal-title":"J Pediatr"},{"key":"10.1016\/j.jpeds.2006.01.004_bib17","doi-asserted-by":"crossref","first-page":"463","DOI":"10.1023\/A:1005314025760","article-title":"Continuous venovenous haemodiafiltration in the acute phase of neonatal maple syrup urine disease","volume":"20","author":"Jouvet","year":"1997","journal-title":"J Inherit Metab Dis"},{"key":"10.1016\/j.jpeds.2006.01.004_bib18","doi-asserted-by":"crossref","first-page":"330","DOI":"10.1007\/BF00866350","article-title":"Continuous venovenous haemofiltration in the acute treatment of inborn errors of metabolism","volume":"8","author":"Falk","year":"1994","journal-title":"Pediatr Nephrol"},{"key":"10.1016\/j.jpeds.2006.01.004_bib19","doi-asserted-by":"crossref","first-page":"278","DOI":"10.1097\/01.PCC.0000113265.92664.91","article-title":"Amino acid clearance during acute metabolic decompensation in maple syrup urine disease treated with continuous venovenous hemodialysis with filtration","volume":"5","author":"Hmiel","year":"2004","journal-title":"Pediatr Crit Care Med"},{"key":"10.1016\/j.jpeds.2006.01.004_bib20","doi-asserted-by":"crossref","first-page":"862","DOI":"10.1007\/s004670100702","article-title":"Extracorporeal dialysis in neonatal hyperammonemia","volume":"16","author":"Picca","year":"2001","journal-title":"Pediatr Nephrol"},{"key":"10.1016\/j.jpeds.2006.01.004_bib21","doi-asserted-by":"crossref","first-page":"589","DOI":"10.1007\/s004670050511","article-title":"Ammonia clearance by peritoneal dialysis and continuous arteriovenous hemodiafiltration","volume":"12","author":"Wong","year":"1998","journal-title":"Pediatr Nephrol"},{"key":"10.1016\/j.jpeds.2006.01.004_bib22","doi-asserted-by":"crossref","first-page":"142","DOI":"10.1016\/S0022-3476(80)80352-0","article-title":"The management of life-threatening hyperammonemia","volume":"96","author":"Wiegand","year":"1980","journal-title":"J Pediatr"},{"key":"10.1016\/j.jpeds.2006.01.004_bib23","doi-asserted-by":"crossref","first-page":"1387","DOI":"10.1056\/NEJM198206103062303","article-title":"Treatment of inborn errors of urea synthesis","volume":"306","author":"Batshaw","year":"1982","journal-title":"N Engl J Med"},{"key":"10.1016\/j.jpeds.2006.01.004_bib24","doi-asserted-by":"crossref","first-page":"421","DOI":"10.1016\/S0022-3476(78)81149-4","article-title":"Treatment of complete ornithine transcarbamylase deficiency with nitrogen-free analogues of essential amino acids","volume":"93","author":"McReynolds","year":"1978","journal-title":"J Pediatr"},{"key":"10.1016\/j.jpeds.2006.01.004_bib25","doi-asserted-by":"crossref","first-page":"410","DOI":"10.1007\/s00431-003-1347-z","article-title":"Outcome and survival of 88 patients with urea cycle disorders","volume":"162","author":"Bachmann","year":"2003","journal-title":"Eur J Pediatr"},{"issue":"Suppl 1","key":"10.1016\/j.jpeds.2006.01.004_bib26","doi-asserted-by":"crossref","first-page":"151","DOI":"10.1023\/A:1005374027693","article-title":"Neurodevelopmental outcome of long-term therapy of urea cycle disorders in Japan","volume":"21","author":"Uchino","year":"1998","journal-title":"J Inherit Metab Dis"},{"key":"10.1016\/j.jpeds.2006.01.004_bib27","article-title":"Early experience with the safety and effectiveness of the Cobe PRISMA for pediatric CRRT","volume":"18","author":"Smoyer","year":"2000","journal-title":"Blood Purif"},{"key":"10.1016\/j.jpeds.2006.01.004_bib28","doi-asserted-by":"crossref","first-page":"S84","DOI":"10.1016\/S0272-6386(97)90547-3","article-title":"Management of acute renal failure in the pediatric patient","volume":"30","author":"Maxvold","year":"1997","journal-title":"Am J Kidney Dis"},{"key":"10.1016\/j.jpeds.2006.01.004_bib29","doi-asserted-by":"crossref","first-page":"1161","DOI":"10.1097\/00003246-200004000-00041","article-title":"Amino acid loss and nitrogen balance in critically ill children with acute renal failure","volume":"28","author":"Maxvold","year":"2000","journal-title":"Crit Care Med"},{"key":"10.1016\/j.jpeds.2006.01.004_bib30","doi-asserted-by":"crossref","first-page":"479","DOI":"10.1111\/j.0894-0959.2004.17609.x","article-title":"The dose of dialysis in hemodialysis patients","volume":"17","author":"Schulman","year":"2004","journal-title":"Semin Dial"},{"key":"10.1016\/j.jpeds.2006.01.004_bib31","doi-asserted-by":"crossref","first-page":"536","DOI":"10.1016\/j.jpeds.2004.01.037","article-title":"Clearance of amino acids by hemodialysis in argininosuccinate synthetase deficiency","volume":"144","author":"McBryde","year":"2004","journal-title":"J Pediatr"}],"container-title":["The Journal of Pediatrics"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0022347606000059?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0022347606000059?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2019,1,15]],"date-time":"2019-01-15T17:24:00Z","timestamp":1547573040000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0022347606000059"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2006,6]]},"references-count":31,"journal-issue":{"issue":"6","published-print":{"date-parts":[[2006,6]]}},"alternative-id":["S0022347606000059"],"URL":"https:\/\/doi.org\/10.1016\/j.jpeds.2006.01.004","relation":{},"ISSN":["0022-3476"],"issn-type":[{"value":"0022-3476","type":"print"}],"subject":[],"published":{"date-parts":[[2006,6]]}}}