{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,19]],"date-time":"2026-08-19T20:16:41Z","timestamp":1787170601921,"version":"build-2736575974"},"reference-count":33,"publisher":"Elsevier BV","issue":"6","license":[{"start":{"date-parts":[[2013,6,1]],"date-time":"2013-06-01T00:00:00Z","timestamp":1370044800000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2016,7,6]],"date-time":"2016-07-06T00:00:00Z","timestamp":1467763200000},"content-version":"vor","delay-in-days":1131,"URL":"https:\/\/www.elsevier.com\/open-access\/userlicense\/1.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["The Journal of Thoracic and Cardiovascular Surgery"],"published-print":{"date-parts":[[2013,6]]},"DOI":"10.1016\/j.jtcvs.2013.02.030","type":"journal-article","created":{"date-parts":[[2013,3,13]],"date-time":"2013-03-13T08:02:15Z","timestamp":1363161735000},"page":"1493-1503","source":"Crossref","is-referenced-by-count":103,"title":["The natural and unnatural history of the systemic right ventricle in adult survivors"],"prefix":"10.1016","volume":"145","author":[{"given":"Richard","family":"Dobson","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mark","family":"Danton","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Walker","family":"Nicola","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Walker","family":"Hamish","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"key":"10.1016\/j.jtcvs.2013.02.030_bib1","doi-asserted-by":"crossref","first-page":"1905","DOI":"10.1161\/CIRCULATIONAHA.105.606046","article-title":"Presence of a ventricular septal defect and the Mustard operation are risk factors for late mortality after the atrial switch operation: thirty years of follow-up in 417 patients at a single center","volume":"114","author":"Lange","year":"2006","journal-title":"Circulation"},{"key":"10.1016\/j.jtcvs.2013.02.030_bib2","doi-asserted-by":"crossref","first-page":"307","DOI":"10.1136\/hrt.2002.007138","article-title":"Long term outcome up to 30 years after the Mustard or Senning operation: a nationwide multicentre study in Belgium","volume":"90","author":"Moons","year":"2004","journal-title":"Heart"},{"key":"10.1016\/j.jtcvs.2013.02.030_bib3","doi-asserted-by":"crossref","first-page":"159","DOI":"10.1016\/j.athoracsur.2009.08.071","article-title":"Outcomes of biventricular repair for congenitally corrected transposition of the great arteries","volume":"89","author":"Lim","year":"2010","journal-title":"Ann Thorac Surg"},{"key":"10.1016\/j.jtcvs.2013.02.030_bib4","doi-asserted-by":"crossref","first-page":"51","DOI":"10.1053\/j.pcsu.2005.02.003","article-title":"The double switch for atrioventricular discordance","author":"Brawn","year":"2005","journal-title":"Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu"},{"key":"10.1016\/j.jtcvs.2013.02.030_bib5","doi-asserted-by":"crossref","first-page":"879","DOI":"10.1016\/j.ejcts.2009.01.051","article-title":"Results of the double switch operation for congenitally corrected transposition of the great arteries","volume":"35","author":"Ly","year":"2009","journal-title":"Eur J Cardiothoracic Surg"},{"key":"10.1016\/j.jtcvs.2013.02.030_bib6","doi-asserted-by":"crossref","first-page":"1318","DOI":"10.1016\/j.jtcvs.2006.11.063","article-title":"Outcomes of definitive surgical repair for congenitally corrected transposition of the great arteries or double outlet right ventricle with discordant atrioventricular connections: risk analyses in 189 patients","volume":"133","author":"Shin'oka","year":"2007","journal-title":"J Thorac Cardiovasc Surg"},{"key":"10.1016\/j.jtcvs.2013.02.030_bib7","doi-asserted-by":"crossref","first-page":"1952","DOI":"10.1016\/j.athoracsur.2009.08.014","article-title":"Early and intermediate outcome after anatomic repair of congenitally corrected transposition of the great arteries","volume":"88","author":"Gaies","year":"2009","journal-title":"Ann Thorac Surg"},{"key":"10.1016\/j.jtcvs.2013.02.030_bib8","doi-asserted-by":"crossref","first-page":"1529","DOI":"10.1016\/j.athoracsur.2005.09.035","article-title":"Physiologic versus anatomic repair of congenitally corrected transposition of the great arteries: meta-analysis of individual patient data","volume":"81","author":"Alghamdi","year":"2006","journal-title":"Ann Thorac Surg"},{"key":"10.1016\/j.jtcvs.2013.02.030_bib9","doi-asserted-by":"crossref","first-page":"2699","DOI":"10.1161\/CIRCULATIONAHA.105.592352","article-title":"Transposition of the great arteries","volume":"114","author":"Warnes","year":"2006","journal-title":"Circulation"},{"key":"10.1016\/j.jtcvs.2013.02.030_bib10","doi-asserted-by":"crossref","first-page":"1467","DOI":"10.1161\/CIRCULATIONAHA.108.805135","article-title":"Tricuspid valve surgery in adults with a dysfunctional systemic right ventricle: repair or replace?","volume":"119","author":"Scherptong","year":"2009","journal-title":"Circulation"},{"key":"10.1016\/j.jtcvs.2013.02.030_bib11","doi-asserted-by":"crossref","first-page":"2008","DOI":"10.1016\/j.jacc.2010.11.021","article-title":"Congenitally corrected transposition of the great arteries ventricular function at the time of systemic atrioventricular valve replacement predicts long-term ventricular function","volume":"57","author":"Mongeon","year":"2011","journal-title":"J Am Coll Cardiol"},{"key":"10.1016\/j.jtcvs.2013.02.030_bib12","doi-asserted-by":"crossref","first-page":"642","DOI":"10.1016\/S0022-5223(95)70345-4","article-title":"Late results of systemic atrioventricular valve replacement in corrected transposition","volume":"109","author":"van Son","year":"1995","journal-title":"J Thorac Cardiovasc Surg"},{"key":"10.1016\/j.jtcvs.2013.02.030_bib13","doi-asserted-by":"crossref","first-page":"479","DOI":"10.1136\/hrt.80.5.479","article-title":"Maintaining tricuspid valve competence in double discordance: a challenge for the paediatric cardiologist","volume":"80","author":"Acar","year":"1998","journal-title":"Heart"},{"key":"10.1016\/j.jtcvs.2013.02.030_bib14","doi-asserted-by":"crossref","first-page":"E8","DOI":"10.1016\/j.ahj.2003.09.015","article-title":"Arterial switch operation after Mustard procedures in adult patients with transposition of the great arteries: is it time to revise our strategy?","volume":"147","author":"Benzaquen","year":"2004","journal-title":"Am Heart J"},{"key":"10.1016\/j.jtcvs.2013.02.030_bib15","doi-asserted-by":"crossref","first-page":"728","DOI":"10.1016\/j.ejcts.2010.03.065","article-title":"Early prophylactic pulmonary artery banding in isolated congenitally corrected transposition of the great arteries","volume":"38","author":"Metton","year":"2010","journal-title":"Eur J Cardiothorac Surg"},{"key":"10.1016\/j.jtcvs.2013.02.030_bib16","doi-asserted-by":"crossref","first-page":"405","DOI":"10.1161\/01.CIR.0000153355.92687.FA","article-title":"Intention-to-treat analysis of pulmonary artery banding in conditions with a morphological right ventricle in the systemic circulation with a view to anatomic biventricular repair","volume":"111","author":"Winlaw","year":"2005","journal-title":"Circulation"},{"key":"10.1016\/j.jtcvs.2013.02.030_bib17","doi-asserted-by":"crossref","first-page":"913","DOI":"10.1093\/ejcts\/ezr078","article-title":"Pulmonary artery banding as 'open end' palliation of systemic right ventricles: an interim analysis","volume":"41","author":"Cools","year":"2012","journal-title":"Eur J Cardiothorac Surg"},{"key":"10.1016\/j.jtcvs.2013.02.030_bib18","doi-asserted-by":"crossref","first-page":"42","DOI":"10.1016\/S0022-5223(96)70443-9","article-title":"Regression of tricuspid regurgitation after two-stage arterial switch operation for failing systemic right ventricle after atrial inversion operation","volume":"111","author":"van Son","year":"1996","journal-title":"J Thorac Cardiovasc Surg"},{"key":"10.1016\/j.jtcvs.2013.02.030_bib19","doi-asserted-by":"crossref","first-page":"1229","DOI":"10.1016\/S0022-5223(02)73246-7","article-title":"Midterm results after restoration of the morphologically left ventricle to the systemic circulation in patients with congenitally corrected transposition of the great arteries","volume":"125","author":"Langley","year":"2003","journal-title":"J Thorac Cardiovasc Surg"},{"key":"10.1016\/j.jtcvs.2013.02.030_bib20","doi-asserted-by":"crossref","first-page":"2277","DOI":"10.1016\/j.jacc.2005.05.096","article-title":"Resynchronization therapy in pediatric and congenital heart disease patients: an international multicenter study","volume":"46","author":"Dubin","year":"2005","journal-title":"J Am Coll Cardiol"},{"key":"10.1016\/j.jtcvs.2013.02.030_bib21","doi-asserted-by":"crossref","first-page":"159","DOI":"10.1111\/j.1540-8159.2007.00963.x","article-title":"Left ventricular dysfunction after cardiac resynchronization therapy in congenital heart disease patients with a failing systemic right ventricle","volume":"31","author":"Kiesewetter","year":"2008","journal-title":"Pacing Clin Electrophysiol"},{"key":"10.1016\/j.jtcvs.2013.02.030_bib22","doi-asserted-by":"crossref","first-page":"407","DOI":"10.1017\/S104795110100052X","article-title":"Cardiopulmonary exercise performance in adult survivors of the Mustard procedure","volume":"11","author":"Hechter","year":"2001","journal-title":"Cardiol Young"},{"key":"10.1016\/j.jtcvs.2013.02.030_bib23","doi-asserted-by":"crossref","first-page":"191","DOI":"10.1136\/heart.85.2.191","article-title":"Exercise capacity in adult patients with congenitally corrected transposition of the great arteries","volume":"85","author":"Fredriksen","year":"2001","journal-title":"Heart"},{"key":"10.1016\/j.jtcvs.2013.02.030_bib24","doi-asserted-by":"crossref","first-page":"1250","DOI":"10.1016\/j.jacc.2006.05.051","article-title":"Heart rate response during exercise predicts survival in adults with congenital heart disease","volume":"48","author":"Diller","year":"2006","journal-title":"J Am Coll Cardiol"},{"key":"10.1016\/j.jtcvs.2013.02.030_bib25","doi-asserted-by":"crossref","first-page":"828","DOI":"10.1161\/CIRCULATIONAHA.104.529800","article-title":"Exercise intolerance in adult congenital heart disease: comparative severity, correlates, and prognostic implication","volume":"112","author":"Diller","year":"2005","journal-title":"Circulation"},{"key":"10.1016\/j.jtcvs.2013.02.030_bib26","doi-asserted-by":"crossref","first-page":"59","DOI":"10.1016\/j.ijcard.2008.01.032","article-title":"Impaired heart rate response to exercise in adult patients with a systemic right ventricle or univentricular circulation: prevalence, relation to exercise, and potential therapeutic implications","volume":"134","author":"Diller","year":"2009","journal-title":"Int J Cardiol"},{"key":"10.1016\/j.jtcvs.2013.02.030_bib27","doi-asserted-by":"crossref","first-page":"284","DOI":"10.1017\/S1047951104003063","article-title":"Long-term outcomes after the atrial switch for surgical correction of transposition: a meta-analysis comparing the Mustard and Senning procedures","volume":"14","author":"Khairy","year":"2004","journal-title":"Cardiol Young"},{"key":"10.1016\/j.jtcvs.2013.02.030_bib28","doi-asserted-by":"crossref","first-page":"500","DOI":"10.1067\/mtc.2003.158","article-title":"Combined arterial switch and Senning operation for congenitally corrected transposition of the great arteries: patient selection and intermediate results","volume":"125","author":"Devaney","year":"2003","journal-title":"J Thorac Cardiovasc Surg"},{"key":"10.1016\/j.jtcvs.2013.02.030_bib29","doi-asserted-by":"crossref","first-page":"2915","DOI":"10.1093\/eurheartj\/ehq249","article-title":"ESC Guidelines for the management of grown-up congenital heart disease (new version 2010)","volume":"31","author":"Baumgartner","year":"2010","journal-title":"Eur Heart J"},{"issue":"S2","key":"10.1016\/j.jtcvs.2013.02.030_bib30","first-page":"176","article-title":"Comparison of long-term outcomes of atrial repair of simple transposition with implications for a late arterial switch strategy","volume":"100","author":"Sarkar","year":"1999","journal-title":"Circulation"},{"key":"10.1016\/j.jtcvs.2013.02.030_bib31","doi-asserted-by":"crossref","first-page":"758","DOI":"10.1016\/S0735-1097(98)00309-X","article-title":"Long-term outcome after the Mustard repair for simple transposition of the great arteries","volume":"32","author":"Wilson","year":"1998","journal-title":"J Am Coll Cardiol"},{"key":"10.1016\/j.jtcvs.2013.02.030_bib32","doi-asserted-by":"crossref","first-page":"182","DOI":"10.1016\/j.jtcvs.2004.02.046","article-title":"Long-term outcome of surgically treated patients with corrected transposition of the great arteries","volume":"129","author":"Hraska","year":"2005","journal-title":"J Thorac Cardiovasc Surg"},{"key":"10.1016\/j.jtcvs.2013.02.030_bib33","doi-asserted-by":"crossref","first-page":"1190","DOI":"10.1016\/S0022-5223(99)70259-X","article-title":"Atrioventricular discordance: results of repair in 127 patients","volume":"117","author":"Yeh","year":"1999","journal-title":"J Thorac Cardiovasc Surg"}],"container-title":["The Journal of Thoracic and Cardiovascular Surgery"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0022522313001815?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0022522313001815?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2018,10,18]],"date-time":"2018-10-18T00:31:47Z","timestamp":1539822707000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0022522313001815"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2013,6]]},"references-count":33,"journal-issue":{"issue":"6","published-print":{"date-parts":[[2013,6]]}},"alternative-id":["S0022522313001815"],"URL":"https:\/\/doi.org\/10.1016\/j.jtcvs.2013.02.030","relation":{},"ISSN":["0022-5223"],"issn-type":[{"value":"0022-5223","type":"print"}],"subject":[],"published":{"date-parts":[[2013,6]]}}}