{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,1,15]],"date-time":"2026-01-15T22:25:59Z","timestamp":1768515959835,"version":"3.49.0"},"reference-count":10,"publisher":"Elsevier BV","issue":"2","license":[{"start":{"date-parts":[[2024,2,1]],"date-time":"2024-02-01T00:00:00Z","timestamp":1706745600000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2024,2,1]],"date-time":"2024-02-01T00:00:00Z","timestamp":1706745600000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/legal\/tdmrep-license"},{"start":{"date-parts":[[2023,11,26]],"date-time":"2023-11-26T00:00:00Z","timestamp":1700956800000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by-nc-nd\/4.0\/"}],"content-domain":{"domain":["kidney-international.org","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Kidney International"],"published-print":{"date-parts":[[2024,2]]},"DOI":"10.1016\/j.kint.2023.11.008","type":"journal-article","created":{"date-parts":[[2023,11,26]],"date-time":"2023-11-26T09:57:32Z","timestamp":1700992652000},"page":"376-380","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":3,"title":["Uromodulin processing in DNAJB11-kidney disease"],"prefix":"10.1016","volume":"105","author":[{"given":"Marta","family":"Mariniello","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-3549-7796","authenticated-orcid":false,"given":"Guglielmo","family":"Schiano","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ayumi","family":"Yoshifuji","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-3319-5233","authenticated-orcid":false,"given":"Valentine","family":"Gillion","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-1881-3782","authenticated-orcid":false,"given":"John Andrew","family":"Sayer","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-2547-6593","authenticated-orcid":false,"given":"Fran\u00e7ois","family":"Jouret","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Yannick","family":"Le Meur","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Emilie","family":"Cornec-Le Gall","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Eric Gregory","family":"Olinger","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-3744-4767","authenticated-orcid":false,"given":"Olivier","family":"Devuyst","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"78","reference":[{"key":"10.1016\/j.kint.2023.11.008_bib1","doi-asserted-by":"crossref","first-page":"832","DOI":"10.1016\/j.ajhg.2018.03.013","article-title":"Monoallelic mutations to DNAJB11 cause atypical autosomal-dominant polycystic kidney disease","volume":"102","author":"Cornec-Le Gall","year":"2018","journal-title":"Am J Hum Genet"},{"key":"10.1016\/j.kint.2023.11.008_bib2","doi-asserted-by":"crossref","first-page":"476","DOI":"10.1016\/j.kint.2020.02.022","article-title":"Clinical spectrum, prognosis and estimated prevalence of DNAJB11-kidney disease","volume":"98","author":"Huynh","year":"2020","journal-title":"Kidney Int"},{"key":"10.1016\/j.kint.2023.11.008_bib3","doi-asserted-by":"crossref","first-page":"60","DOI":"10.1038\/s41572-019-0109-9","article-title":"Autosomal dominant tubulointerstitial kidney disease","volume":"5","author":"Devuyst","year":"2019","journal-title":"Nat Rev Dis Primer"},{"key":"10.1016\/j.kint.2023.11.008_bib4","doi-asserted-by":"crossref","DOI":"10.1073\/pnas.2114734119","article-title":"An intermediate-effect size variant in UMOD confers risk for chronic kidney disease","volume":"119","author":"Olinger","year":"2022","journal-title":"Proc Natl Acad Sci U S A"},{"key":"10.1016\/j.kint.2023.11.008_bib5","doi-asserted-by":"crossref","first-page":"40","DOI":"10.1091\/mbc.e04-05-0434","article-title":"ERdj3, a stress-inducible endoplasmic reticulum DnaJ homologue, serves as a cofactor for BiP's interactions with unfolded substrates","volume":"16","author":"Shen","year":"2005","journal-title":"Mol Biol Cell"},{"key":"10.1016\/j.kint.2023.11.008_bib6","doi-asserted-by":"crossref","first-page":"717","DOI":"10.1016\/j.kint.2020.04.038","article-title":"Clinical and genetic spectra of autosomal dominant tubulointerstitial kidney disease due to mutations in UMOD and MUC1","volume":"98","author":"Olinger","year":"2020","journal-title":"Kidney Int"},{"key":"10.1016\/j.kint.2023.11.008_bib7","doi-asserted-by":"crossref","first-page":"973","DOI":"10.1091\/mbc.8.6.973","article-title":"Nanomolar concentrations of nocodazole alter microtubule dynamic instability in\u00a0vivo and in\u00a0vitro","volume":"8","author":"Vasquez","year":"1997","journal-title":"Mol Biol Cell"},{"key":"10.1016\/j.kint.2023.11.008_bib8","doi-asserted-by":"crossref","first-page":"511","DOI":"10.1681\/ASN.2021040491","article-title":"Meta-GWAS reveals novel genetic variants associated with urinary excretion of uromodulin","volume":"33","author":"Joseph","year":"2022","journal-title":"J\u00a0Am Soc Nephrol"},{"key":"10.1016\/j.kint.2023.11.008_bib9","doi-asserted-by":"crossref","first-page":"1521","DOI":"10.1681\/ASN.0000000000000164","article-title":"Dnajb11-kidney disease develops from reduced polycystin-1 dosage but not unfolded protein response in mice","volume":"34","author":"Ghosh","year":"2023","journal-title":"J\u00a0Am Soc Nephrol"},{"key":"10.1016\/j.kint.2023.11.008_bib10","doi-asserted-by":"crossref","first-page":"459","DOI":"10.1097\/MNH.0b013e3283621510","article-title":"Osmoregulation, vasopressin, and cAMP signaling in autosomal dominant polycystic kidney disease","volume":"22","author":"Devuyst","year":"2013","journal-title":"Curr Opin Nephrol Hypertens"}],"container-title":["Kidney International"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0085253823007858?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0085253823007858?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2025,9,25]],"date-time":"2025-09-25T01:05:42Z","timestamp":1758762342000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0085253823007858"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2024,2]]},"references-count":10,"journal-issue":{"issue":"2","published-print":{"date-parts":[[2024,2]]}},"alternative-id":["S0085253823007858"],"URL":"https:\/\/doi.org\/10.1016\/j.kint.2023.11.008","relation":{},"ISSN":["0085-2538"],"issn-type":[{"value":"0085-2538","type":"print"}],"subject":[],"published":{"date-parts":[[2024,2]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"Uromodulin processing in DNAJB11-kidney disease","name":"articletitle","label":"Article Title"},{"value":"Kidney International","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.kint.2023.11.008","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"\u00a9 2023 International Society of Nephrology. Published by Elsevier Inc.","name":"copyright","label":"Copyright"}]}}