{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,5,1]],"date-time":"2026-05-01T17:22:48Z","timestamp":1777656168477,"version":"3.51.4"},"reference-count":32,"publisher":"Elsevier BV","issue":"1","license":[{"start":{"date-parts":[[2011,7,1]],"date-time":"2011-07-01T00:00:00Z","timestamp":1309478400000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"}],"funder":[{"name":"Drug Discovery Training in Age-related Disorders","award":["T32 AG000260"],"award-info":[{"award-number":["T32 AG000260"]}]},{"DOI":"10.13039\/100001104","name":"Families of Spinal Muscular Atrophy","doi-asserted-by":"crossref","award":["DiD0809"],"award-info":[{"award-number":["DiD0809"]}],"id":[{"id":"10.13039\/100001104","id-type":"DOI","asserted-by":"crossref"}]},{"DOI":"10.13039\/100001104","name":"Families of Spinal Muscular Atrophy","doi-asserted-by":"crossref","award":["1ROIN5060926, 3RO1NS060926-02S3"],"award-info":[{"award-number":["1ROIN5060926, 3RO1NS060926-02S3"]}],"id":[{"id":"10.13039\/100001104","id-type":"DOI","asserted-by":"crossref"}]},{"DOI":"10.13039\/100000065","name":"NINDS","doi-asserted-by":"crossref","award":["1R21HD058311-01A1"],"award-info":[{"award-number":["1R21HD058311-01A1"]}],"id":[{"id":"10.13039\/100000065","id-type":"DOI","asserted-by":"crossref"}]},{"name":"NICHD"},{"DOI":"10.13039\/100000894","name":"SMA Foundation","doi-asserted-by":"crossref","id":[{"id":"10.13039\/100000894","id-type":"DOI","asserted-by":"crossref"}]}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Neurobiology of Disease"],"published-print":{"date-parts":[[2011,7]]},"DOI":"10.1016\/j.nbd.2011.03.002","type":"journal-article","created":{"date-parts":[[2011,3,9]],"date-time":"2011-03-09T17:17:05Z","timestamp":1299691025000},"page":"142-151","source":"Crossref","is-referenced-by-count":20,"title":["Characterization of a commonly used mouse model of SMA reveals increased seizure susceptibility and heightened fear response in FVB\/N mice"],"prefix":"10.1016","volume":"43","author":[{"given":"Rocky G.","family":"Gogliotti","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Cathleen","family":"Lutz","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Michael","family":"Jorgensen","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Kimberly","family":"Huebsch","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Sookyong","family":"Koh","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Christine J.","family":"DiDonato","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"78","reference":[{"key":"10.1016\/j.nbd.2011.03.002_bb0005","doi-asserted-by":"crossref","first-page":"659","DOI":"10.1172\/JCI29562","article-title":"Trichostatin A increases SMN expression and survival in a mouse model of spinal muscular atrophy","volume":"117","author":"Avila","year":"2007","journal-title":"J. Clin. Invest."},{"key":"10.1016\/j.nbd.2011.03.002_bb0010","doi-asserted-by":"crossref","first-page":"730","DOI":"10.1100\/tsw.2002.146","article-title":"Altered short-term synaptic plasticity in mice lacking the metabotropic glutamate receptor mGlu7","volume":"2","author":"Bushell","year":"2002","journal-title":"ScientificWorldJournal"},{"key":"10.1016\/j.nbd.2011.03.002_bb0015","doi-asserted-by":"crossref","first-page":"835","DOI":"10.1016\/j.bbrc.2009.11.148","article-title":"Effect of diet on the survival and phenotype of a mouse model for spinal muscular atrophy","volume":"391","author":"Butchbach","year":"2010","journal-title":"Biochem. Biophys. Res. Commun."},{"key":"10.1016\/j.nbd.2011.03.002_bb0020","doi-asserted-by":"crossref","first-page":"6573","DOI":"10.1523\/JNEUROSCI.1497-06.2006","article-title":"Concomitant deficits in working memory and fear extinction are functionally dissociated from reduced anxiety in metabotropic glutamate receptor 7-deficient mice","volume":"26","author":"Callaerts-Vegh","year":"2006","journal-title":"J. Neurosci."},{"key":"10.1016\/j.nbd.2011.03.002_bb0025","doi-asserted-by":"crossref","first-page":"251","DOI":"10.1073\/pnas.0510051103","article-title":"mGluR7's lucky number","volume":"103","author":"Conn","year":"2006","journal-title":"Proc. Natl. Acad. Sci. USA"},{"key":"10.1016\/j.nbd.2011.03.002_bb0035","doi-asserted-by":"crossref","first-page":"97","DOI":"10.1006\/nbdi.1996.0010","article-title":"The neurobiology of childhood spinal muscular atrophy","volume":"3","author":"Crawford","year":"1996","journal-title":"Neurobiol. Dis."},{"key":"10.1016\/j.nbd.2011.03.002_bb0040","doi-asserted-by":"crossref","first-page":"2409","DOI":"10.1046\/j.1460-9568.2003.02667.x","article-title":"Antidepressant and anxiolytic-like effects in mice lacking the group III metabotropic glutamate receptor mGluR7","volume":"17","author":"Cryan","year":"2003","journal-title":"Eur. J. Neurosci."},{"key":"10.1016\/j.nbd.2011.03.002_bb0045","first-page":"1218","article-title":"Association between Ag1-CA alleles and severity of autosomal recessive proximal spinal muscular atrophy","volume":"55","author":"DiDonato","year":"1994","journal-title":"Am. J. Hum. Genet."},{"key":"10.1016\/j.nbd.2011.03.002_bb0050","doi-asserted-by":"crossref","first-page":"271","DOI":"10.1038\/nbt.1610","article-title":"Rescue of the spinal muscular atrophy phenotype in a mouse model by early postnatal delivery of SMN","volume":"28","author":"Foust","year":"2010","journal-title":"Nat. Biotechnol."},{"key":"10.1016\/j.nbd.2011.03.002_bb0055","doi-asserted-by":"crossref","first-page":"517","DOI":"10.1016\/j.bbrc.2009.11.090","article-title":"Molecular and phenotypic reassessment of an infrequently used mouse model for spinal muscular atrophy","volume":"391","author":"Gogliotti","year":"2010","journal-title":"Biochem. Biophys. Res. Commun."},{"key":"10.1016\/j.nbd.2011.03.002_bb0060","doi-asserted-by":"crossref","first-page":"1310","DOI":"10.1093\/hmg\/ddp030","article-title":"Translational readthrough by the aminoglycoside geneticin (G418) modulates SMN stability in vitro and improves motor function in SMA mice in vivo","volume":"18","author":"Heier","year":"2009","journal-title":"Hum. Mol. Genet."},{"key":"10.1016\/j.nbd.2011.03.002_bb0065","doi-asserted-by":"crossref","first-page":"1013","DOI":"10.1177\/0883073807305669","article-title":"SMN transcript stability: could modulation of messenger RNA degradation provide a novel therapy for spinal muscular atrophy?","volume":"22","author":"Heier","year":"2007","journal-title":"J. Child Neurol."},{"key":"10.1016\/j.nbd.2011.03.002_bb0070","doi-asserted-by":"crossref","first-page":"473","DOI":"10.1016\/j.bbr.2004.03.015","article-title":"Lack of the metabotropic glutamate receptor subtype 7 selectively impairs short-term working memory but not long-term memory","volume":"154","author":"Holscher","year":"2004","journal-title":"Behav. Brain Res."},{"key":"10.1016\/j.nbd.2011.03.002_bb0075","doi-asserted-by":"crossref","first-page":"66","DOI":"10.1038\/71709","article-title":"A mouse model for spinal muscular atrophy","volume":"24","author":"Hsieh-Li","year":"2000","journal-title":"Nat. Genet."},{"key":"10.1016\/j.nbd.2011.03.002_bb0080","doi-asserted-by":"crossref","first-page":"332","DOI":"10.1002\/(SICI)1096-9861(19980413)393:3<332::AID-CNE6>3.0.CO;2-2","article-title":"Immunohistochemical localization of metabotropic glutamate receptors, mGluR7a and mGluR7b, in the central nervous system of the adult rat and mouse: a light and electron microscopic study","volume":"393","author":"Kinoshita","year":"1998","journal-title":"J. Comp. Neurol."},{"key":"10.1016\/j.nbd.2011.03.002_bb0085","doi-asserted-by":"crossref","first-page":"266","DOI":"10.1002\/(SICI)1096-9861(19991213)415:2<266::AID-CNE9>3.0.CO;2-7","article-title":"Localization of metabotropic glutamate receptor 7 mRNA and mGluR7a protein in the rat basal ganglia","volume":"415","author":"Kosinski","year":"1999","journal-title":"J. Comp. Neurol."},{"key":"10.1016\/j.nbd.2011.03.002_bb0090","doi-asserted-by":"crossref","first-page":"845","DOI":"10.1093\/hmg\/ddi078","article-title":"SMNDelta7, the major product of the centromeric survival motor neuron (SMN2) gene, extends survival in mice with spinal muscular atrophy and associates with full-length SMN","volume":"14","author":"Le","year":"2005","journal-title":"Hum. Mol. Genet."},{"key":"10.1016\/j.nbd.2011.03.002_bb0095","doi-asserted-by":"crossref","first-page":"155","DOI":"10.1016\/0092-8674(95)90460-3","article-title":"Identification and characterization of a spinal muscular atrophy-determining gene","volume":"80","author":"Lefebvre","year":"1995","journal-title":"Cell"},{"key":"10.1016\/j.nbd.2011.03.002_bb0100","doi-asserted-by":"crossref","first-page":"955","DOI":"10.1523\/JNEUROSCI.19-03-00955.1999","article-title":"Metabotropic glutamate receptor subtype 7 ablation causes deficit in fear response and conditioned taste aversion","volume":"19","author":"Masugi","year":"1999","journal-title":"J. Neurosci."},{"key":"10.1016\/j.nbd.2011.03.002_bb0105","doi-asserted-by":"crossref","first-page":"767","DOI":"10.1038\/344767a0","article-title":"Gene for chronic proximal spinal muscular atrophies maps to chromosome 5q","volume":"344","author":"Melki","year":"1990","journal-title":"Nature"},{"key":"10.1016\/j.nbd.2011.03.002_bb0110","doi-asserted-by":"crossref","first-page":"1474","DOI":"10.1126\/science.7910982","article-title":"De novo and inherited deletions of the 5q13 region in spinal muscular atrophies","volume":"264","author":"Melki","year":"1994","journal-title":"Science"},{"key":"10.1016\/j.nbd.2011.03.002_bb0115","doi-asserted-by":"crossref","first-page":"333","DOI":"10.1093\/hmg\/9.3.333","article-title":"The human centromeric survival motor neuron gene (SMN2) rescues embryonic lethality in Smn(\u2212\/\u2212) mice and results in a mouse with spinal muscular atrophy","volume":"9","author":"Monani","year":"2000","journal-title":"Hum. Mol. Genet."},{"key":"10.1016\/j.nbd.2011.03.002_bb0120","doi-asserted-by":"crossref","first-page":"41","DOI":"10.1083\/jcb.200208079","article-title":"A transgene carrying an A2G missense mutation in the SMN gene modulates phenotypic severity in mice with severe (type I) spinal muscular atrophy","volume":"160","author":"Monani","year":"2003","journal-title":"J. Cell Biol."},{"key":"10.1016\/j.nbd.2011.03.002_bb0125","doi-asserted-by":"crossref","first-page":"465","DOI":"10.1002\/ana.21449","article-title":"Sustained improvement of spinal muscular atrophy mice treated with trichostatin A plus nutrition","volume":"64","author":"Narver","year":"2008","journal-title":"Ann. Neurol."},{"key":"10.1016\/j.nbd.2011.03.002_bb0130","doi-asserted-by":"crossref","first-page":"191","DOI":"10.1016\/j.expneurol.2009.08.028","article-title":"Lenalidomide (Revlimid) administration at symptom onset is neuroprotective in a mouse model of amyotrophic lateral sclerosis","volume":"220","author":"Neymotin","year":"2009","journal-title":"Exp. Neurol."},{"key":"10.1016\/j.nbd.2011.03.002_bb0135","doi-asserted-by":"crossref","first-page":"615","DOI":"10.1016\/S0092-8674(00)81632-3","article-title":"A novel function for SMN, the spinal muscular atrophy disease gene product, in pre-mRNA splicing","volume":"95","author":"Pellizzoni","year":"1998","journal-title":"Cell"},{"key":"10.1016\/j.nbd.2011.03.002_bb0140","doi-asserted-by":"crossref","first-page":"8734","DOI":"10.1523\/JNEUROSCI.21-22-08734.2001","article-title":"Increased seizure susceptibility in mice lacking metabotropic glutamate receptor 7","volume":"21","author":"Sansig","year":"2001","journal-title":"J. Neurosci."},{"key":"10.1016\/j.nbd.2011.03.002_bb0145","doi-asserted-by":"crossref","first-page":"4103","DOI":"10.1073\/pnas.94.8.4103","article-title":"Genetic determinants of susceptibility to excitotoxic cell death: implications for gene targeting approaches","volume":"94","author":"Schauwecker","year":"1997","journal-title":"Proc. Natl. Acad. Sci. USA"},{"key":"10.1016\/j.nbd.2011.03.002_bb0150","doi-asserted-by":"crossref","first-page":"9920","DOI":"10.1073\/pnas.94.18.9920","article-title":"Inactivation of the survival motor neuron gene, a candidate gene for human spinal muscular atrophy, leads to massive cell death in early mouse embryos","volume":"94","author":"Schrank","year":"1997","journal-title":"Proc. Natl. Acad. Sci. USA"},{"key":"10.1016\/j.nbd.2011.03.002_bb0155","doi-asserted-by":"crossref","first-page":"341","DOI":"10.4161\/rna.6.3.8723","article-title":"A short antisense oligonucleotide masking a unique intronic motif prevents skipping of a critical exon in spinal muscular atrophy","volume":"6","author":"Singh","year":"2009","journal-title":"RNA Biol."},{"key":"10.1016\/j.nbd.2011.03.002_bb0160","doi-asserted-by":"crossref","first-page":"2215","DOI":"10.1093\/hmg\/ddp157","article-title":"A SMN missense mutation complements SMN2 restoring snRNPs and rescuing SMA mice","volume":"18","author":"Workman","year":"2009","journal-title":"Hum. Mol. Genet."},{"key":"10.1016\/j.nbd.2011.03.002_bb0165","doi-asserted-by":"crossref","first-page":"518","DOI":"10.1001\/archneur.1995.00540290108025","article-title":"Natural history in proximal spinal muscular atrophy. Clinical analysis of 445 patients and suggestions for a modification of existing classifications","volume":"52","author":"Zerres","year":"1995","journal-title":"Arch. Neurol."}],"container-title":["Neurobiology of Disease"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0969996111000738?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0969996111000738?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2020,5,6]],"date-time":"2020-05-06T22:15:29Z","timestamp":1588803329000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0969996111000738"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2011,7]]},"references-count":32,"journal-issue":{"issue":"1","published-print":{"date-parts":[[2011,7]]}},"alternative-id":["S0969996111000738"],"URL":"https:\/\/doi.org\/10.1016\/j.nbd.2011.03.002","relation":{},"ISSN":["0969-9961"],"issn-type":[{"value":"0969-9961","type":"print"}],"subject":[],"published":{"date-parts":[[2011,7]]}}}