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Neurosci."},{"key":"10.1016\/j.nbd.2024.106696_bb0350","doi-asserted-by":"crossref","first-page":"18","DOI":"10.1111\/j.1365-2990.1995.tb01024.x","article-title":"The cortical neuritic pathology of Huntington\u2019s disease","volume":"21","author":"Jackson","year":"1995","journal-title":"Neuropathol. Appl. Neurobiol."},{"key":"10.1016\/j.nbd.2024.106696_bb0355","doi-asserted-by":"crossref","first-page":"2009","DOI":"10.1093\/hmg\/9.13.2009","article-title":"Polyglutamine length-dependent interaction of Hsp40 and Hsp70 family chaperones with truncated N-terminal huntingtin: their role in suppression of aggregation and cellular toxicity","volume":"9","author":"Jana","year":"2000","journal-title":"Hum. Mol. 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Sci."},{"key":"10.1016\/j.nbd.2024.106696_bb0410","doi-asserted-by":"crossref","first-page":"1324","DOI":"10.1093\/brain\/awp059","article-title":"Hippocampal tau pathology is related to neuroanatomical connections: an ageing population-based study","volume":"132","author":"Lace","year":"2009","journal-title":"Brain"},{"key":"10.1016\/j.nbd.2024.106696_bb0415","doi-asserted-by":"crossref","first-page":"fcaa066","DOI":"10.1093\/braincomms\/fcaa066","article-title":"Subcellular localization and formation of huntingtin aggregates correlates with symptom onset and progression in a Huntington\u2019S disease model","volume":"2","author":"Landles","year":"2020","journal-title":"Brain Commun."},{"key":"10.1016\/j.nbd.2024.106696_bb0420","doi-asserted-by":"crossref","first-page":"27","DOI":"10.1124\/pr.57.1.2","article-title":"International union of pharmacology. XLV. 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Chem."},{"key":"10.1016\/j.nbd.2024.106696_bb0445","first-page":"11","article-title":"Reduced non-rapid eye movement sleep is associated with tau pathology in early Alzheimer\u2019s disease","author":"Lucey","year":"2019","journal-title":"Sci. Transl. Med."},{"key":"10.1016\/j.nbd.2024.106696_bb0450","doi-asserted-by":"crossref","first-page":"981","DOI":"10.1007\/s00401-019-01973-6","article-title":"Demonstration of prion-like properties of mutant huntingtin fibrils in both in vitro and in vivo paradigms","volume":"137","author":"Masnata","year":"2019","journal-title":"Acta Neuropathol."},{"key":"10.1016\/j.nbd.2024.106696_bb0455","doi-asserted-by":"crossref","DOI":"10.1177\/1179069518772380","article-title":"Tau: a common denominator and therapeutic target for neurodegenerative disorders","volume":"12","author":"Maxan","year":"2018","journal-title":"J. Exp. Neurosci."},{"key":"10.1016\/j.nbd.2024.106696_bb0460","doi-asserted-by":"crossref","first-page":"507","DOI":"10.1016\/j.tibs.2013.08.001","article-title":"Hsp70 chaperone dynamics and molecular mechanism","volume":"38","author":"Mayer","year":"2013","journal-title":"Trends Biochem. Sci."},{"key":"10.1016\/j.nbd.2024.106696_bb0465","doi-asserted-by":"crossref","first-page":"545","DOI":"10.1002\/ana.410030616","article-title":"Huntington disease associated with Alzheimer disease","volume":"3","author":"McIntosh","year":"1978","journal-title":"Ann. Neurol."},{"key":"10.1016\/j.nbd.2024.106696_bb0470","doi-asserted-by":"crossref","first-page":"788","DOI":"10.1002\/cne.21867","article-title":"Tau isoform regulation is region- and cell-specific in mouse brain","volume":"511","author":"McMillan","year":"2008","journal-title":"J. Comp. 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Chem."},{"key":"10.1016\/j.nbd.2024.106696_bb0485","doi-asserted-by":"crossref","first-page":"178","DOI":"10.1016\/j.neuron.2010.01.008","article-title":"Early increase in extrasynaptic NMDA receptor signaling and expression contributes to phenotype onset in Huntington\u2019s disease mice","volume":"65","author":"Milnerwood","year":"2010","journal-title":"Neuron"},{"key":"10.1016\/j.nbd.2024.106696_bb0490","doi-asserted-by":"crossref","first-page":"763","DOI":"10.1002\/hipo.1092","article-title":"Neurogranin null mutant mice display performance deficits on spatial learning tasks with anxiety related components","volume":"11","author":"Miyakawa","year":"2001","journal-title":"Hippocampus"},{"key":"10.1016\/j.nbd.2024.106696_bb0495","doi-asserted-by":"crossref","first-page":"3668","DOI":"10.1038\/s41467-022-31396-z","article-title":"Hsp multichaperone complex buffers pathologically modified tau","volume":"13","author":"Moll","year":"2022","journal-title":"Nat. Commun."},{"key":"10.1016\/j.nbd.2024.106696_bb0500","doi-asserted-by":"crossref","first-page":"2560","DOI":"10.1074\/jbc.M114.603332","article-title":"Molecular interaction between the chaperone Hsc70 and the N-terminal flank of huntingtin exon 1 modulates aggregation","volume":"290","author":"Monsellier","year":"2015","journal-title":"J. Biol. Chem."},{"key":"10.1016\/j.nbd.2024.106696_bb0505","doi-asserted-by":"crossref","first-page":"237","DOI":"10.1111\/j.1532-5415.1988.tb01807.x","article-title":"The coexistence and differentiation of late onset Huntington\u2019s disease and Alzheimer\u2019s disease. A case report and review of the literature","volume":"36","author":"Moss","year":"1988","journal-title":"J. Am. Geriatr. Soc."},{"key":"10.1016\/j.nbd.2024.106696_bb0510","doi-asserted-by":"crossref","first-page":"530","DOI":"10.1136\/jnnp.48.6.530","article-title":"Late onset of Huntington\u2019s disease","volume":"48","author":"Myers","year":"1985","journal-title":"J. Neurol. Neurosurg. Psychiatry"},{"key":"10.1016\/j.nbd.2024.106696_bb0515","doi-asserted-by":"crossref","first-page":"362","DOI":"10.1097\/NEN.0b013e31825018f7","article-title":"Correlation of Alzheimer disease neuropathologic changes with cognitive status: a review of the literature","volume":"71","author":"Nelson","year":"2012","journal-title":"J. Neuropathol. Exp. Neurol."},{"key":"10.1016\/j.nbd.2024.106696_bb0520","doi-asserted-by":"crossref","first-page":"297","DOI":"10.1016\/B978-0-12-381328-2.00013-4","article-title":"Huntington\u2019s disease: clinical presentation and treatment","volume":"98","author":"Novak","year":"2011","journal-title":"Int. Rev. Neurobiol."},{"key":"10.1016\/j.nbd.2024.106696_bb0525","doi-asserted-by":"crossref","DOI":"10.1371\/journal.pone.0220393","article-title":"The interaction between RE1-silencing transcription factor (REST) and heat shock protein 90 as new therapeutic target against Huntington\u2019s disease","volume":"14","author":"Orozco-D\u00edaz","year":"2019","journal-title":"PLoS One"},{"key":"10.1016\/j.nbd.2024.106696_bb0530","doi-asserted-by":"crossref","first-page":"134","DOI":"10.1016\/j.cell.2013.06.003","article-title":"PolyQ proteins interfere with nuclear degradation of cytosolic proteins by sequestering the Sis1p chaperone","volume":"154","author":"Park","year":"2013","journal-title":"Cell"},{"key":"10.1016\/j.nbd.2024.106696_bb0535","doi-asserted-by":"crossref","first-page":"151","DOI":"10.1016\/j.bbr.2009.05.022","article-title":"Spatial memory: theoretical basis and comparative review on experimental methods in rodents","volume":"203","author":"Paul","year":"2009","journal-title":"Behav. 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Dis."},{"key":"10.1016\/j.nbd.2024.106696_bb0565","article-title":"Characterization of behavioral, neuropathological, brain metabolic and key molecular changes in zQ175 Knock-in mouse model of Huntington\u2019s disease","volume":"11","author":"Peng","year":"2016","journal-title":"PLoS One"},{"key":"10.1016\/j.nbd.2024.106696_bb0570","article-title":"Differential regulation of tau exon 2 and 10 isoforms in Huntington\u2019s disease brain","author":"Petry","year":"2022","journal-title":"Neuroscience"},{"key":"10.1016\/j.nbd.2024.106696_bb0575","doi-asserted-by":"crossref","first-page":"54","DOI":"10.1016\/j.neuroscience.2022.07.014","article-title":"Differential regulation of tau exon 2 and 10 isoforms in Huntington\u2019s disease brain","volume":"518","author":"Petry","year":"2023","journal-title":"Neuroscience"},{"key":"10.1016\/j.nbd.2024.106696_bb0580","first-page":"8","article-title":"Barnes maze procedure for spatial learning and memory in mice","author":"Pitts","year":"2018","journal-title":"Bio-Protocol"},{"key":"10.1016\/j.nbd.2024.106696_bb0585","doi-asserted-by":"crossref","first-page":"3090","DOI":"10.1523\/JNEUROSCI.4854-06.2007","article-title":"Anesthesia leads to tau hyperphosphorylation through inhibition of phosphatase activity by hypothermia","volume":"27","author":"Planel","year":"2007","journal-title":"J. Neurosci."},{"key":"10.1016\/j.nbd.2024.106696_bb0590","doi-asserted-by":"crossref","first-page":"353","DOI":"10.1146\/annurev-pharmtox-010814-124332","article-title":"Targeting Hsp90\/Hsp70-based protein quality control for treatment of adult onset neurodegenerative diseases","volume":"55","author":"Pratt","year":"2015","journal-title":"Annu. Rev. Pharmacol. Toxicol."},{"key":"10.1016\/j.nbd.2024.106696_bb0595","doi-asserted-by":"crossref","first-page":"2551","DOI":"10.1016\/j.neurobiolaging.2013.05.010","article-title":"Impact of N-tau on adult hippocampal neurogenesis, anxiety, and memory","volume":"34","author":"Prister\u00e0","year":"2013","journal-title":"Neurobiol. 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