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Cell Biol."},{"issue":"2","key":"10.1016\/j.nbd.2025.107203_bb0530","doi-asserted-by":"crossref","first-page":"230","DOI":"10.4161\/auto.5384","article-title":"Roles of ESCRT in autophagy-associated neurodegeneration","volume":"4","author":"Lee","year":"2008","journal-title":"Autophagy"},{"issue":"5","key":"10.1016\/j.nbd.2025.107203_bb0535","doi-asserted-by":"crossref","first-page":"233","DOI":"10.5607\/en.2016.25.5.233","article-title":"Astrocytes and microglia as non-cell autonomous players in the pathogenesis of ALS","volume":"25","author":"Lee","year":"2016","journal-title":"Experimental Neurobiology"},{"key":"10.1016\/j.nbd.2025.107203_bb0540","doi-asserted-by":"crossref","unstructured":"Leigh, P. N., Anderton, B. H., Dodson, A., Gallo, J.-M., Swash, M., & Power, D. M. (1988). Ubiquitin deposits in anterior horn cells in motor neurone disease. Neurosci. Lett., 93(2\u20133), 197\u2013203. doi: https:\/\/doi.org\/10.1016\/0304-3940(88)90081-X.","DOI":"10.1016\/0304-3940(88)90081-X"},{"issue":"2","key":"10.1016\/j.nbd.2025.107203_bb0545","doi-asserted-by":"crossref","first-page":"775","DOI":"10.1093\/brain\/114.2.775","article-title":"Ubiquitin-IMMUNOREACTIVE INTRANEURONAL inclusions in amyotrophic lateral sclerosis","volume":"114","author":"Leigh","year":"1991","journal-title":"Brain"},{"issue":"1","key":"10.1016\/j.nbd.2025.107203_bb0550","doi-asserted-by":"crossref","first-page":"27","DOI":"10.1016\/j.cell.2007.12.018","article-title":"Autophagy in the pathogenesis of disease","volume":"132","author":"Levine","year":"2008","journal-title":"Cell"},{"issue":"5","key":"10.1016\/j.nbd.2025.107203_bb0555","doi-asserted-by":"crossref","first-page":"733","DOI":"10.1083\/jcb.200511068","article-title":"A motor neuron disease\u2013associated mutation in p150Glued perturbs dynactin function and induces protein aggregation","volume":"172","author":"Levy","year":"2006","journal-title":"J. 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Sci."},{"issue":"8","key":"10.1016\/j.nbd.2025.107203_bb0755","doi-asserted-by":"crossref","DOI":"10.1371\/journal.pone.0134830","article-title":"Time-point dependent activation of autophagy and the UPS in SOD1G93A mice skeletal muscle","volume":"10","author":"Oliv\u00e1n","year":"2015","journal-title":"PLoS ONE"},{"key":"10.1016\/j.nbd.2025.107203_bib1308","doi-asserted-by":"crossref","first-page":"652817","DOI":"10.1155\/2014\/652817","article-title":"Sex differences in constitutive autophagy","volume":"2014","author":"Oliv\u00e1n","year":"2014","journal-title":"Biomed. Res. Int."},{"key":"10.1016\/j.nbd.2025.107203_bib1304","doi-asserted-by":"crossref","first-page":"841047","DOI":"10.3389\/fnmol.2022.841047","article-title":"LIS1 and NDEL1 Regulate Axonal Trafficking of Mitochondria in Mature Neurons","volume":"15","author":"Pandey","year":"2022","journal-title":"Front. Mol. 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Sci."},{"issue":"3","key":"10.1016\/j.nbd.2025.107203_bb0800","doi-asserted-by":"crossref","first-page":"262","DOI":"10.1002\/path.5455","article-title":"Oligodendrocyte pathology exceeds axonal pathology in white matter in human amyotrophic lateral sclerosis","volume":"251","author":"Pons","year":"2020","journal-title":"J. Pathol."},{"issue":"10","key":"10.1016\/j.nbd.2025.107203_bb0805","doi-asserted-by":"crossref","first-page":"3369","DOI":"10.1523\/JNEUROSCI.21-10-03369.2001","article-title":"Neuron-specific expression of mutant superoxide dismutase 1 in transgenic mice does not lead to motor impairment","volume":"21","author":"Pramatarova","year":"2001","journal-title":"J. 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Rep."},{"key":"10.1016\/j.nbd.2025.107203_bb0890","doi-asserted-by":"crossref","DOI":"10.3389\/fimmu.2018.01024","article-title":"Optineurin: a coordinator of membrane-associated cargo trafficking and autophagy","volume":"9","author":"Ryan","year":"2018","journal-title":"Front. Immunol."},{"issue":"13","key":"10.1016\/j.nbd.2025.107203_bb0895","doi-asserted-by":"crossref","first-page":"3180","DOI":"10.1038\/sj.emboj.7601743","article-title":"SINTBAD, a novel component of innate antiviral immunity, shares a TBK1-binding domain with NAP1 and TANK","volume":"26","author":"Ryzhakov","year":"2007","journal-title":"EMBO J."},{"key":"10.1016\/j.nbd.2025.107203_bb0900","article-title":"Ubiquitin recognition by the proteasome","volume":"mvw091","author":"Saeki","year":"2017","journal-title":"J. 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Disord."},{"issue":"3","key":"10.1016\/j.nbd.2025.107203_bb0930","doi-asserted-by":"crossref","first-page":"384","DOI":"10.1038\/s41556-019-0281-x","article-title":"Ubiquilins regulate autophagic flux through mTOR signalling and lysosomal acidification","volume":"21","author":"\u015eent\u00fcrk","year":"2019","journal-title":"Nat. Cell Biol."},{"issue":"12","key":"10.1016\/j.nbd.2025.107203_bb0935","doi-asserted-by":"crossref","first-page":"4697","DOI":"10.1073\/pnas.1300398110","article-title":"Astrocyte pathology and the absence of non-cell autonomy in an induced pluripotent stem cell model of TDP-43 proteinopathy","volume":"110","author":"Serio","year":"2013","journal-title":"Proc. Natl. Acad. 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