{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,17]],"date-time":"2026-10-17T01:48:17Z","timestamp":1792201697235,"version":"4.4.0"},"reference-count":240,"publisher":"Elsevier BV","issue":"2","license":[{"start":{"date-parts":[[2017,5,1]],"date-time":"2017-05-01T00:00:00Z","timestamp":1493596800000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"}],"content-domain":{"domain":["clinicalkey.jp","clinicalkey.com","neurologic.theclinics.com","clinicalkey.es","theclinics.com","clinicalkey.com.au","clinicalkey.fr","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Neurologic Clinics"],"published-print":{"date-parts":[[2017,5]]},"DOI":"10.1016\/j.ncl.2017.01.008","type":"journal-article","created":{"date-parts":[[2017,4,11]],"date-time":"2017-04-11T09:12:43Z","timestamp":1491901963000},"page":"339-374","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":409,"title":["Frontotemporal Dementia"],"prefix":"10.1016","volume":"35","author":[{"given":"Nicholas T.","family":"Olney","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Salvatore","family":"Spina","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Bruce L.","family":"Miller","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"key":"10.1016\/j.ncl.2017.01.008_bib1","first-page":"165","article-title":"Uber die Beziehungen der Senilen Hirnatrophie zur Aphasie","volume":"17","author":"Pick","year":"1892","journal-title":"Prager Medizinische Wochenschrift"},{"issue":"11","key":"10.1016\/j.ncl.2017.01.008_bib2","doi-asserted-by":"crossref","first-page":"1006","DOI":"10.1212\/WNL.0b013e31821103e6","article-title":"Classification of primary progressive aphasia and its variants","volume":"76","author":"Gorno-Tempini","year":"2011","journal-title":"Neurology"},{"key":"10.1016\/j.ncl.2017.01.008_bib3","doi-asserted-by":"crossref","first-page":"356","DOI":"10.1007\/BF02866241","article-title":"Uber Eigenartige Krankheitsfalle des Spateren Alters","volume":"4","author":"Alzheimer","year":"1911","journal-title":"Z\u00a0Gesamte Neruol Psychiatr"},{"issue":"5","key":"10.1016\/j.ncl.2017.01.008_bib4","doi-asserted-by":"crossref","first-page":"417","DOI":"10.1080\/13554794.2012.667133","article-title":"'Limits and current knowledge of Pick's disease: its differential diagnosis'. A translation of the 1957 Delay, Brion, Escourolle article","volume":"19","author":"Thibodeau","year":"2013","journal-title":"Neurocase"},{"issue":"4","key":"10.1016\/j.ncl.2017.01.008_bib5","doi-asserted-by":"crossref","first-page":"979","DOI":"10.1016\/S0733-8619(05)70235-8","article-title":"Frontotemporal dementia","volume":"18","author":"Rosen","year":"2000","journal-title":"Neurol Clin"},{"key":"10.1016\/j.ncl.2017.01.008_bib6","series-title":"Frontotemporal dementia","author":"Miller","year":"2014"},{"issue":"4","key":"10.1016\/j.ncl.2017.01.008_bib7","doi-asserted-by":"crossref","first-page":"349","DOI":"10.1007\/s00401-006-0185-2","article-title":"The enigma of vascular cognitive disorder and vascular dementia","volume":"113","author":"Jellinger","year":"2007","journal-title":"Acta Neuropathol"},{"issue":"Suppl 1","key":"10.1016\/j.ncl.2017.01.008_bib8","doi-asserted-by":"crossref","first-page":"11","DOI":"10.1017\/S1041610203008901","article-title":"Vascular dementia: a historical background","volume":"15","author":"Roman","year":"2003","journal-title":"Int Psychogeriatr"},{"key":"10.1016\/j.ncl.2017.01.008_bib9","doi-asserted-by":"crossref","first-page":"208","DOI":"10.1159\/000114320","article-title":"Pick's disease: histological and clinical correlations","volume":"11","author":"Constantinidis","year":"1974","journal-title":"Eur Neurol"},{"issue":"Pt 12","key":"10.1016\/j.ncl.2017.01.008_bib10","doi-asserted-by":"crossref","first-page":"3816","DOI":"10.1093\/brain\/awv316","article-title":"Alzheimer's disease in the 100 years since Alzheimer's death","volume":"138","author":"Ryan","year":"2015","journal-title":"Brain"},{"issue":"4","key":"10.1016\/j.ncl.2017.01.008_bib11","doi-asserted-by":"crossref","first-page":"217","DOI":"10.1001\/archneur.1976.00500040001001","article-title":"Editorial: the prevalence and malignancy of Alzheimer disease. A major killer","volume":"33","author":"Katzman","year":"1976","journal-title":"Arch Neurol"},{"key":"10.1016\/j.ncl.2017.01.008_bib12","first-page":"126","article-title":"Frontal lobe degeneration of non-Alzheimer type revisited","volume":"4","author":"Brun","year":"1993","journal-title":"Dementia"},{"issue":"Suppl 43","key":"10.1016\/j.ncl.2017.01.008_bib13","first-page":"42+","article-title":"Regional cerebral blood flow in organic dementia with early onset","volume":"46","author":"Ingvar","year":"1970","journal-title":"Acta Neurol Scand"},{"issue":"6","key":"10.1016\/j.ncl.2017.01.008_bib14","doi-asserted-by":"crossref","first-page":"592","DOI":"10.1002\/ana.410110607","article-title":"Slowly progressive aphasia without generalized dementia","volume":"11","author":"Mesulam","year":"1982","journal-title":"Ann Neurol"},{"issue":"4","key":"10.1016\/j.ncl.2017.01.008_bib15","doi-asserted-by":"crossref","first-page":"425","DOI":"10.1002\/ana.91","article-title":"Primary progressive aphasia","volume":"49","author":"Mesulam","year":"2001","journal-title":"Ann Neurol"},{"key":"10.1016\/j.ncl.2017.01.008_bib16","doi-asserted-by":"crossref","first-page":"167","DOI":"10.1155\/1989\/124043","article-title":"Semantic dementia: a form of circumscribed cerebral atrophy","volume":"2","author":"Snowden","year":"1989","journal-title":"Behav Neurol"},{"issue":"Pt 6","key":"10.1016\/j.ncl.2017.01.008_bib17","doi-asserted-by":"crossref","first-page":"1027","DOI":"10.1093\/brain\/120.6.1027","article-title":"The temporal variant of frontotemporal dementia","volume":"120","author":"Edwards-Lee","year":"1997","journal-title":"Brain"},{"issue":"4","key":"10.1016\/j.ncl.2017.01.008_bib18","doi-asserted-by":"crossref","first-page":"416","DOI":"10.1136\/jnnp.57.4.416","article-title":"Clinical and neuropathological criteria for frontotemporal dementia. The Lund and Manchester Groups","volume":"57","year":"1994","journal-title":"J\u00a0Neurol Neurosurg Psychiatr"},{"issue":"6","key":"10.1016\/j.ncl.2017.01.008_bib19","doi-asserted-by":"crossref","first-page":"1546","DOI":"10.1212\/WNL.51.6.1546","article-title":"Frontotemporal lobar degeneration: a consensus on clinical diagnostic criteria","volume":"51","author":"Neary","year":"1998","journal-title":"Neurology"},{"issue":"Pt 9","key":"10.1016\/j.ncl.2017.01.008_bib20","doi-asserted-by":"crossref","first-page":"2456","DOI":"10.1093\/brain\/awr179","article-title":"Sensitivity of revised diagnostic criteria for the behavioural variant of frontotemporal dementia","volume":"134","author":"Rascovsky","year":"2011","journal-title":"Brain"},{"issue":"18","key":"10.1016\/j.ncl.2017.01.008_bib21","doi-asserted-by":"crossref","first-page":"1736","DOI":"10.1212\/WNL.0000000000002638","article-title":"Prevalence, characteristics, and survival of frontotemporal lobar degeneration syndromes","volume":"86","author":"Coyle-Gilchrist","year":"2016","journal-title":"Neurology"},{"issue":"3","key":"10.1016\/j.ncl.2017.01.008_bib22","doi-asserted-by":"crossref","first-page":"330","DOI":"10.1007\/s12031-011-9538-y","article-title":"Estimating the number of persons with frontotemporal lobar degeneration in the US population","volume":"45","author":"Knopman","year":"2011","journal-title":"J\u00a0Mol Neurosci"},{"issue":"3","key":"10.1016\/j.ncl.2017.01.008_bib23","doi-asserted-by":"crossref","first-page":"349","DOI":"10.1212\/01.WNL.0000078928.20107.52","article-title":"Survival in frontotemporal dementia","volume":"61","author":"Hodges","year":"2003","journal-title":"Neurology"},{"key":"10.1016\/j.ncl.2017.01.008_bib24","doi-asserted-by":"crossref","first-page":"140","DOI":"10.1192\/bjp.180.2.140","article-title":"Frontotemporal dementia","volume":"180","author":"Snowden","year":"2002","journal-title":"Br J Psychiatry"},{"issue":"Suppl 1","key":"10.1016\/j.ncl.2017.01.008_bib25","doi-asserted-by":"crossref","first-page":"S96","DOI":"10.1017\/cjn.2016.25","article-title":"The prevalence and incidence of frontotemporal dementia: a systematic review","volume":"43","author":"Hogan","year":"2016","journal-title":"Can J Neurol Sci"},{"issue":"2","key":"10.1016\/j.ncl.2017.01.008_bib26","doi-asserted-by":"crossref","first-page":"130","DOI":"10.3109\/09540261.2013.776523","article-title":"The epidemiology of frontotemporal dementia","volume":"25","author":"Onyike","year":"2013","journal-title":"Int Rev Psychiatry"},{"issue":"5","key":"10.1016\/j.ncl.2017.01.008_bib27","doi-asserted-by":"crossref","first-page":"501","DOI":"10.1136\/jnnp-2015-310697","article-title":"The behavioural variant frontotemporal dementia (bvFTD) syndrome in psychiatry","volume":"87","author":"Lanata","year":"2016","journal-title":"J\u00a0Neurol Neurosurg Psychiatr"},{"issue":"2","key":"10.1016\/j.ncl.2017.01.008_bib28","doi-asserted-by":"crossref","first-page":"126","DOI":"10.4088\/JCP.10m06382oli","article-title":"The diagnostic challenge of psychiatric symptoms in neurodegenerative disease: rates of and risk factors for prior psychiatric diagnosis in patients with early neurodegenerative disease","volume":"72","author":"Woolley","year":"2011","journal-title":"J\u00a0Clin Psychiatry"},{"issue":"Pt 11","key":"10.1016\/j.ncl.2017.01.008_bib29","doi-asserted-by":"crossref","first-page":"2612","DOI":"10.1093\/brain\/awh628","article-title":"Neuroanatomical correlates of behavioural disorders in dementia","volume":"128","author":"Rosen","year":"2005","journal-title":"Brain"},{"issue":"2","key":"10.1016\/j.ncl.2017.01.008_bib30","doi-asserted-by":"crossref","first-page":"249","DOI":"10.1001\/archneurol.2007.38","article-title":"Frontal paralimbic network atrophy in very mild behavioral variant frontotemporal dementia","volume":"65","author":"Seeley","year":"2008","journal-title":"Arch Neurol"},{"issue":"6","key":"10.1016\/j.ncl.2017.01.008_bib31","doi-asserted-by":"crossref","first-page":"660","DOI":"10.1002\/ana.21055","article-title":"Early frontotemporal dementia targets neurons unique to apes and humans","volume":"60","author":"Seeley","year":"2006","journal-title":"Ann Neurol"},{"issue":"6","key":"10.1016\/j.ncl.2017.01.008_bib32","doi-asserted-by":"crossref","first-page":"701","DOI":"10.1097\/WCO.0b013e3283168e2d","article-title":"Selective functional, regional, and neuronal vulnerability in frontotemporal dementia","volume":"21","author":"Seeley","year":"2008","journal-title":"Curr Opin Neurol"},{"issue":"3","key":"10.1016\/j.ncl.2017.01.008_bib33","doi-asserted-by":"crossref","first-page":"418","DOI":"10.1016\/j.neurobiolaging.2006.10.023","article-title":"Neural networks in frontotemporal dementia\u2013a meta-analysis","volume":"29","author":"Schroeter","year":"2008","journal-title":"Neurobiol Aging"},{"issue":"9","key":"10.1016\/j.ncl.2017.01.008_bib34","doi-asserted-by":"crossref","first-page":"2349","DOI":"10.1523\/JNEUROSCI.5587-06.2007","article-title":"Dissociable intrinsic connectivity networks for salience processing and executive control","volume":"27","author":"Seeley","year":"2007","journal-title":"J\u00a0Neurosci"},{"issue":"4","key":"10.1016\/j.ncl.2017.01.008_bib35","doi-asserted-by":"crossref","first-page":"373","DOI":"10.1177\/1073858411410354","article-title":"Frontotemporal dementia: what can the behavioral variant teach us about human brain organization?","volume":"18","author":"Seeley","year":"2012","journal-title":"Neuroscientist"},{"issue":"23","key":"10.1016\/j.ncl.2017.01.008_bib36","doi-asserted-by":"crossref","first-page":"19440","DOI":"10.1074\/jbc.M112.346072","article-title":"Trans-cellular propagation of Tau aggregation by fibrillar species","volume":"287","author":"Kfoury","year":"2012","journal-title":"J\u00a0Biol Chem"},{"key":"10.1016\/j.ncl.2017.01.008_bib37","doi-asserted-by":"crossref","first-page":"87","DOI":"10.1146\/annurev-neuro-071714-033828","article-title":"Neurodegenerative diseases: expanding the prion concept","volume":"38","author":"Walker","year":"2015","journal-title":"Annu Rev Neurosci"},{"issue":"4","key":"10.1016\/j.ncl.2017.01.008_bib38","doi-asserted-by":"crossref","first-page":"211","DOI":"10.1097\/00146965-200312000-00002","article-title":"Distinctive neuropsychological patterns in frontotemporal dementia, semantic dementia, and Alzheimer disease","volume":"16","author":"Kramer","year":"2003","journal-title":"Cogn Behav Neurol"},{"issue":"2","key":"10.1016\/j.ncl.2017.01.008_bib39","doi-asserted-by":"crossref","first-page":"647","DOI":"10.1016\/S0022-3999(02)00428-2","article-title":"Frontal-subcortical neuronal circuits and clinical neuropsychiatry: an update","volume":"53","author":"Tekin","year":"2002","journal-title":"J\u00a0Psychosom Res"},{"issue":"4","key":"10.1016\/j.ncl.2017.01.008_bib40","doi-asserted-by":"crossref","first-page":"589","DOI":"10.1016\/S0010-9452(08)70024-8","article-title":"Asymmetric functional roles of right and left ventromedial prefrontal cortices in social conduct, decision-making, and emotional processing","volume":"38","author":"Tranel","year":"2002","journal-title":"Cortex"},{"issue":"2","key":"10.1016\/j.ncl.2017.01.008_bib41","doi-asserted-by":"crossref","first-page":"73","DOI":"10.1097\/WNN.0b013e31829cff11","article-title":"Guilty by suspicion? Criminal behavior in frontotemporal lobar degeneration","volume":"26","author":"Diehl-Schmid","year":"2013","journal-title":"Cogn Behav Neurol"},{"issue":"3","key":"10.1016\/j.ncl.2017.01.008_bib42","doi-asserted-by":"crossref","first-page":"295","DOI":"10.1001\/jamaneurol.2014.3781","article-title":"Criminal behavior in frontotemporal dementia and Alzheimer disease","volume":"72","author":"Liljegren","year":"2015","journal-title":"JAMA Neurol"},{"issue":"5","key":"10.1016\/j.ncl.2017.01.008_bib43","doi-asserted-by":"crossref","first-page":"632","DOI":"10.1136\/jnnp.2004.042879","article-title":"Self awareness and personality change in dementia","volume":"76","author":"Rankin","year":"2005","journal-title":"J\u00a0Neurol Neurosurg Psychiatr"},{"issue":"7","key":"10.1016\/j.ncl.2017.01.008_bib44","doi-asserted-by":"crossref","first-page":"888","DOI":"10.1001\/archneurol.2009.92","article-title":"Apathy symptom profile and behavioral associations in frontotemporal dementia vs dementia of Alzheimer type","volume":"66","author":"Chow","year":"2009","journal-title":"Arch Neurol"},{"issue":"6","key":"10.1016\/j.ncl.2017.01.008_bib45","doi-asserted-by":"crossref","first-page":"515","DOI":"10.1080\/13554790903061371","article-title":"Rest-activity and behavioral disruption in a patient with frontotemporal dementia","volume":"15","author":"Merrilees","year":"2009","journal-title":"Neurocase"},{"issue":"2","key":"10.1016\/j.ncl.2017.01.008_bib46","doi-asserted-by":"crossref","first-page":"122","DOI":"10.1016\/j.tics.2011.12.008","article-title":"Motivation of extended behaviors by anterior cingulate cortex","volume":"16","author":"Holroyd","year":"2012","journal-title":"Trends Cogn Sci"},{"issue":"2","key":"10.1016\/j.ncl.2017.01.008_bib47","doi-asserted-by":"crossref","first-page":"198","DOI":"10.1212\/WNL.58.2.198","article-title":"Patterns of brain atrophy in frontotemporal dementia and semantic dementia","volume":"58","author":"Rosen","year":"2002","journal-title":"Neurology"},{"issue":"4","key":"10.1016\/j.ncl.2017.01.008_bib48","doi-asserted-by":"crossref","first-page":"1690","DOI":"10.1016\/j.concog.2011.09.005","article-title":"Loss of emotional insight in behavioral variant frontotemporal dementia or \u201cfrontal anosodiaphoria\u201d","volume":"20","author":"Mendez","year":"2011","journal-title":"Conscious Cogn"},{"issue":"Pt 11","key":"10.1016\/j.ncl.2017.01.008_bib49","doi-asserted-by":"crossref","first-page":"2945","DOI":"10.1093\/brain\/awl254","article-title":"Structural anatomy of empathy in neurodegenerative disease","volume":"129","author":"Rankin","year":"2006","journal-title":"Brain"},{"issue":"2","key":"10.1016\/j.ncl.2017.01.008_bib50","doi-asserted-by":"crossref","first-page":"100","DOI":"10.1176\/jnp.6.2.100","article-title":"Repetitive and compulsive behavior in frontal lobe degenerations","volume":"6","author":"Ames","year":"1994","journal-title":"J\u00a0Neuropsychiatry Clin Neurosci"},{"issue":"12","key":"10.1016\/j.ncl.2017.01.008_bib51","doi-asserted-by":"crossref","first-page":"1859","DOI":"10.1016\/j.neurobiolaging.2007.04.027","article-title":"Anatomic correlates of stereotypies in frontotemporal lobar degeneration","volume":"29","author":"Josephs","year":"2008","journal-title":"Neurobiol Aging"},{"issue":"6","key":"10.1016\/j.ncl.2017.01.008_bib52","doi-asserted-by":"crossref","first-page":"911","DOI":"10.1111\/j.1468-1331.2011.03656.x","article-title":"Voxel-based morphometry in patients with obsessive-compulsive behaviors in behavioral variant frontotemporal dementia","volume":"19","author":"Perry","year":"2012","journal-title":"Eur J Neurol"},{"issue":"11","key":"10.1016\/j.ncl.2017.01.008_bib53","first-page":"965","article-title":"Complex compulsive behaviour in the temporal variant of frontotemporal dementia","volume":"248","author":"Rosso","year":"2001","journal-title":"J\u00a0Neurol"},{"issue":"4","key":"10.1016\/j.ncl.2017.01.008_bib54","first-page":"195","article-title":"Dietary changes, compulsions and sexual behavior in frontotemporal degeneration","volume":"6","author":"Miller","year":"1995","journal-title":"Dementia"},{"issue":"14","key":"10.1016\/j.ncl.2017.01.008_bib55","doi-asserted-by":"crossref","first-page":"1424","DOI":"10.1212\/01.wnl.0000277461.06713.23","article-title":"Binge eating is associated with right orbitofrontal-insular-striatal atrophy in frontotemporal dementia","volume":"69","author":"Woolley","year":"2007","journal-title":"Neurology"},{"issue":"1","key":"10.1016\/j.ncl.2017.01.008_bib56","doi-asserted-by":"crossref","first-page":"207","DOI":"10.1016\/j.neuroimage.2006.12.006","article-title":"VBM signatures of abnormal eating behaviours in frontotemporal lobar degeneration","volume":"35","author":"Whitwell","year":"2007","journal-title":"Neuroimage"},{"issue":"3","key":"10.1016\/j.ncl.2017.01.008_bib57","doi-asserted-by":"crossref","first-page":"589","DOI":"10.1007\/s12031-011-9547-x","article-title":"Eating disturbance in behavioural-variant frontotemporal dementia","volume":"45","author":"Piguet","year":"2011","journal-title":"J\u00a0Mol Neurosci"},{"issue":"2","key":"10.1016\/j.ncl.2017.01.008_bib58","first-page":"128","article-title":"Early diagnosis of the frontal variant of frontotemporal dementia: how sensitive are standard neuroimaging and neuropsychologic tests?","volume":"12","author":"Gregory","year":"1999","journal-title":"Neuropsychiatry Neuropsychol Behav Neurol"},{"issue":"6","key":"10.1016\/j.ncl.2017.01.008_bib59","doi-asserted-by":"crossref","first-page":"628","DOI":"10.1097\/WCO.0b013e3283404309","article-title":"Nonprogressive behavioural frontotemporal dementia: recent developments and clinical implications of the 'bvFTD phenocopy syndrome'","volume":"23","author":"Kipps","year":"2010","journal-title":"Curr Opin Neurol"},{"issue":"4","key":"10.1016\/j.ncl.2017.01.008_bib60","doi-asserted-by":"crossref","first-page":"358","DOI":"10.1136\/jnnp-2011-301883","article-title":"Atypical, slowly progressive behavioural variant frontotemporal dementia associated with C9ORF72 hexanucleotide expansion","volume":"83","author":"Khan","year":"2012","journal-title":"J\u00a0Neurol Neurosurg Psychiatr"},{"issue":"7","key":"10.1016\/j.ncl.2017.01.008_bib61","doi-asserted-by":"crossref","first-page":"600","DOI":"10.1212\/WNL.0000000000002373","article-title":"Cognition and neuropsychiatry in behavioral variant frontotemporal dementia by disease stage","volume":"86","author":"Ranasinghe","year":"2016","journal-title":"Neurology"},{"issue":"13","key":"10.1016\/j.ncl.2017.01.008_bib62","doi-asserted-by":"crossref","first-page":"1073","DOI":"10.1212\/WNL.0b013e3181b9c8a6","article-title":"Characterizing radiology reports in patients with frontotemporal dementia","volume":"73","author":"Suarez","year":"2009","journal-title":"Neurology"},{"key":"10.1016\/j.ncl.2017.01.008_bib63","first-page":"1448","article-title":"Primary progressive aphasia: differentiation from Alzheimer's disease","volume":"37","author":"Mesulam","year":"1987","journal-title":"Ann Neurol"},{"issue":"3","key":"10.1016\/j.ncl.2017.01.008_bib64","doi-asserted-by":"crossref","first-page":"335","DOI":"10.1002\/ana.10825","article-title":"Cognition and anatomy in three variants of primary progressive aphasia","volume":"55","author":"Gorno-Tempini","year":"2004","journal-title":"Ann Neurol"},{"issue":"6","key":"10.1016\/j.ncl.2017.01.008_bib65","doi-asserted-by":"crossref","first-page":"709","DOI":"10.1002\/ana.21388","article-title":"Alzheimer and frontotemporal pathology in subsets of primary progressive aphasia","volume":"63","author":"Mesulam","year":"2008","journal-title":"Ann Neurol"},{"issue":"4","key":"10.1016\/j.ncl.2017.01.008_bib66","doi-asserted-by":"crossref","first-page":"388","DOI":"10.1002\/ana.21451","article-title":"Abeta amyloid and glucose metabolism in three variants of primary progressive aphasia","volume":"64","author":"Rabinovici","year":"2008","journal-title":"Ann Neurol"},{"issue":"8","key":"10.1016\/j.ncl.2017.01.008_bib67","doi-asserted-by":"crossref","first-page":"1384","DOI":"10.1212\/01.WNL.0000158425.46019.5C","article-title":"The natural history of temporal variant frontotemporal dementia","volume":"64","author":"Seeley","year":"2005","journal-title":"Neurology"},{"issue":"Pt 1","key":"10.1016\/j.ncl.2017.01.008_bib68","doi-asserted-by":"crossref","first-page":"300","DOI":"10.1093\/brain\/awp248","article-title":"Semantic dementia: demography, familial factors and survival in a consecutive series of 100 cases","volume":"133","author":"Hodges","year":"2010","journal-title":"Brain"},{"issue":"5\u20136","key":"10.1016\/j.ncl.2017.01.008_bib69","doi-asserted-by":"crossref","first-page":"281","DOI":"10.1159\/000375299","article-title":"Dominant frontotemporal dementia mutations in 140 cases of primary progressive aphasia and speech apraxia","volume":"39","author":"Flanagan","year":"2015","journal-title":"Dement Geriatr Cogn Disord"},{"issue":"11","key":"10.1016\/j.ncl.2017.01.008_bib70","doi-asserted-by":"crossref","first-page":"1817","DOI":"10.1212\/01.wnl.0000187068.92184.63","article-title":"Comparison of family histories in FTLD subtypes and related tauopathies","volume":"65","author":"Goldman","year":"2005","journal-title":"Neurology"},{"issue":"1","key":"10.1016\/j.ncl.2017.01.008_bib71","doi-asserted-by":"crossref","first-page":"31","DOI":"10.1037\/0894-4105.13.1.31","article-title":"The differentiation of semantic dementia and frontal lobe dementia (temporal and frontal variants of frontotemporal dementia) from early Alzheimer's disease: a comparative neuropsychological study","volume":"13","author":"Hodges","year":"1999","journal-title":"Neuropsychology"},{"issue":"3\u20134","key":"10.1016\/j.ncl.2017.01.008_bib72","first-page":"204","article-title":"Progressive right frontotemporal degeneration: clinical, neuropsychological and SPECT characteristics","volume":"4","author":"Miller","year":"1993","journal-title":"Dementia"},{"issue":"Pt 10","key":"10.1016\/j.ncl.2017.01.008_bib73","doi-asserted-by":"crossref","first-page":"2286","DOI":"10.1093\/brain\/awf225","article-title":"Emotion comprehension in the temporal variant of frontotemporal dementia","volume":"125","author":"Rosen","year":"2002","journal-title":"Brain"},{"key":"10.1016\/j.ncl.2017.01.008_bib74","doi-asserted-by":"crossref","first-page":"458","DOI":"10.1192\/bjp.176.5.458","article-title":"Functional correlates of musical and visual ability in frontotemporal dementia","volume":"176","author":"Miller","year":"2000","journal-title":"Br J Psychiatry"},{"issue":"4","key":"10.1016\/j.ncl.2017.01.008_bib75","doi-asserted-by":"crossref","first-page":"978","DOI":"10.1212\/WNL.51.4.978","article-title":"Emergence of artistic talent in frontotemporal dementia","volume":"51","author":"Miller","year":"1998","journal-title":"Neurology"},{"issue":"9043","key":"10.1016\/j.ncl.2017.01.008_bib76","doi-asserted-by":"crossref","first-page":"1744","DOI":"10.1016\/S0140-6736(05)65881-3","article-title":"Enhanced artistic creativity with temporal lobe degeneration [letter]","volume":"348","author":"Miller","year":"1996","journal-title":"Lancet"},{"issue":"3","key":"10.1016\/j.ncl.2017.01.008_bib77","doi-asserted-by":"crossref","first-page":"235","DOI":"10.1080\/13554790802633213","article-title":"A\u00a0case study of an emerging visual artist with frontotemporal lobar degeneration and amyotrophic lateral sclerosis","volume":"15","author":"Liu","year":"2009","journal-title":"Neurocase"},{"issue":"2","key":"10.1016\/j.ncl.2017.01.008_bib78","doi-asserted-by":"crossref","first-page":"221","DOI":"10.3109\/09540261.2013.778822","article-title":"Neuroimaging in frontotemporal dementia","volume":"25","author":"Rohrer","year":"2013","journal-title":"Int Rev Psychiatry"},{"issue":"3","key":"10.1016\/j.ncl.2017.01.008_bib79","doi-asserted-by":"crossref","first-page":"343","DOI":"10.1016\/j.bandl.2006.01.008","article-title":"Clinical and anatomical correlates of apraxia of speech","volume":"97","author":"Ogar","year":"2006","journal-title":"Brain Lang"},{"issue":"10","key":"10.1016\/j.ncl.2017.01.008_bib80","doi-asserted-by":"crossref","first-page":"1849","DOI":"10.1212\/01.wnl.0000237038.55627.5b","article-title":"Anatomical correlates of early mutism in progressive nonfluent aphasia","volume":"67","author":"Gorno-Tempini","year":"2006","journal-title":"Neurology"},{"issue":"7","key":"10.1016\/j.ncl.2017.01.008_bib81","doi-asserted-by":"crossref","first-page":"1077","DOI":"10.1212\/WNL.59.7.1077","article-title":"The overlap of amyotrophic lateral sclerosis and frontotemporal dementia","volume":"59","author":"Lomen-Hoerth","year":"2002","journal-title":"Neurology"},{"issue":"2","key":"10.1016\/j.ncl.2017.01.008_bib82","doi-asserted-by":"crossref","first-page":"400","DOI":"10.1212\/WNL.49.2.400","article-title":"Familial nature and continuing morbidity of the amyotrophic lateral sclerosis-parkinsonism dementia complex of Guam","volume":"49","author":"McGeer","year":"1997","journal-title":"Neurology"},{"issue":"3","key":"10.1016\/j.ncl.2017.01.008_bib83","doi-asserted-by":"crossref","first-page":"656","DOI":"10.1007\/s12031-011-9636-x","article-title":"Clinical phenomenology and neuroimaging correlates in ALS-FTD","volume":"45","author":"Lomen-Hoerth","year":"2011","journal-title":"J\u00a0Mol Neurosci"},{"issue":"7","key":"10.1016\/j.ncl.2017.01.008_bib84","doi-asserted-by":"crossref","first-page":"2684","DOI":"10.1016\/j.clinph.2016.04.005","article-title":"Awaji criteria improves the diagnostic sensitivity in amyotrophic lateral sclerosis: a systematic review using individual patient data","volume":"127","author":"Geevasinga","year":"2016","journal-title":"Clin Neurophysiol"},{"issue":"Suppl","key":"10.1016\/j.ncl.2017.01.008_bib85","doi-asserted-by":"crossref","first-page":"96","DOI":"10.1016\/0022-510X(94)90191-0","volume":"124","author":"Brooks","year":"1994","journal-title":"J\u00a0Neurol Sci"},{"issue":"1","key":"10.1016\/j.ncl.2017.01.008_bib86","doi-asserted-by":"crossref","first-page":"53","DOI":"10.1080\/17482960802521126","article-title":"Awaji diagnostic algorithm increases sensitivity of El Escorial criteria for ALS diagnosis","volume":"10","author":"Carvalho","year":"2009","journal-title":"Amyotroph Lateral Scler"},{"issue":"11","key":"10.1016\/j.ncl.2017.01.008_bib87","doi-asserted-by":"crossref","first-page":"1774","DOI":"10.1212\/01.wnl.0000188759.87240.8b","article-title":"The effects of executive and behavioral dysfunction on the course of ALS","volume":"65","author":"Olney","year":"2005","journal-title":"Neurology"},{"issue":"8","key":"10.1016\/j.ncl.2017.01.008_bib88","doi-asserted-by":"crossref","first-page":"730","DOI":"10.1097\/01.jnen.0000174335.27708.0a","article-title":"Ubiquitin immunohistochemistry suggests classic motor neuron disease, motor neuron disease with dementia, and frontotemporal dementia of the motor neuron disease type represent a clinicopathologic spectrum","volume":"64","author":"Mackenzie","year":"2005","journal-title":"J\u00a0Neuropathol Exp Neurol"},{"issue":"3","key":"10.1016\/j.ncl.2017.01.008_bib89","doi-asserted-by":"crossref","first-page":"602","DOI":"10.1016\/j.bbrc.2006.10.093","article-title":"TDP-43 is a component of ubiquitin-positive tau-negative inclusions in frontotemporal lobar degeneration and amyotrophic lateral sclerosis","volume":"351","author":"Arai","year":"2006","journal-title":"Biochem Biophys Res Commun"},{"issue":"1","key":"10.1016\/j.ncl.2017.01.008_bib90","doi-asserted-by":"crossref","first-page":"111","DOI":"10.1007\/s00401-011-0845-8","article-title":"A\u00a0harmonized classification system for FTLD-TDP pathology","volume":"122","author":"Mackenzie","year":"2011","journal-title":"Acta Neuropathol"},{"issue":"5796","key":"10.1016\/j.ncl.2017.01.008_bib91","doi-asserted-by":"crossref","first-page":"130","DOI":"10.1126\/science.1134108","article-title":"Ubiquitinated TDP-43 in frontotemporal lobar degeneration and amyotrophic lateral sclerosis","volume":"314","author":"Neumann","year":"2006","journal-title":"Science"},{"issue":"5918","key":"10.1016\/j.ncl.2017.01.008_bib92","doi-asserted-by":"crossref","first-page":"1205","DOI":"10.1126\/science.1166066","article-title":"Mutations in the FUS\/TLS gene on chromosome 16 cause familial amyotrophic lateral sclerosis","volume":"323","author":"Kwiatkowski","year":"2009","journal-title":"Science"},{"issue":"Pt 9","key":"10.1016\/j.ncl.2017.01.008_bib93","doi-asserted-by":"crossref","first-page":"2595","DOI":"10.1093\/brain\/awr201","article-title":"FET proteins TAF15 and EWS are selective markers that distinguish FTLD with FUS pathology from amyotrophic lateral sclerosis with FUS mutations","volume":"134","author":"Neumann","year":"2011","journal-title":"Brain"},{"issue":"5918","key":"10.1016\/j.ncl.2017.01.008_bib94","doi-asserted-by":"crossref","first-page":"1208","DOI":"10.1126\/science.1165942","article-title":"Mutations in FUS, an RNA processing protein, cause familial amyotrophic lateral sclerosis type 6","volume":"323","author":"Vance","year":"2009","journal-title":"Science"},{"issue":"10","key":"10.1016\/j.ncl.2017.01.008_bib95","doi-asserted-by":"crossref","first-page":"995","DOI":"10.1016\/S1474-4422(10)70195-2","article-title":"TDP-43 and FUS in amyotrophic lateral sclerosis and frontotemporal dementia","volume":"9","author":"Mackenzie","year":"2010","journal-title":"Lancet Neurol"},{"issue":"Pt 11","key":"10.1016\/j.ncl.2017.01.008_bib96","doi-asserted-by":"crossref","first-page":"2922","DOI":"10.1093\/brain\/awp214","article-title":"A\u00a0new subtype of frontotemporal lobar degeneration with FUS pathology","volume":"132","author":"Neumann","year":"2009","journal-title":"Brain"},{"issue":"1","key":"10.1016\/j.ncl.2017.01.008_bib97","doi-asserted-by":"crossref","first-page":"99","DOI":"10.1007\/s00401-011-0816-0","article-title":"The most common type of FTLD-FUS (aFTLD-U) is associated with a distinct clinical form of frontotemporal dementia but is not related to mutations in the FUS gene","volume":"122","author":"Snowden","year":"2011","journal-title":"Acta Neuropathol"},{"issue":"1","key":"10.1016\/j.ncl.2017.01.008_bib98","doi-asserted-by":"crossref","first-page":"33","DOI":"10.1007\/s00401-010-0698-6","article-title":"FUS pathology defines the majority of tau- and TDP-43-negative frontotemporal lobar degeneration","volume":"120","author":"Urwin","year":"2010","journal-title":"Acta Neuropathol"},{"issue":"13","key":"10.1016\/j.ncl.2017.01.008_bib99","doi-asserted-by":"crossref","first-page":"1664","DOI":"10.1001\/jama.284.13.1664","article-title":"Linkage of familial amyotrophic lateral sclerosis with frontotemporal dementia to chromosome 9q21-q22","volume":"284","author":"Hosler","year":"2000","journal-title":"JAMA"},{"issue":"2","key":"10.1016\/j.ncl.2017.01.008_bib100","doi-asserted-by":"crossref","first-page":"245","DOI":"10.1016\/j.neuron.2011.09.011","article-title":"Expanded GGGGCC hexanucleotide repeat in noncoding region of C9ORF72 causes chromosome 9p-linked FTD and ALS","volume":"72","author":"DeJesus-Hernandez","year":"2011","journal-title":"Neuron"},{"issue":"2","key":"10.1016\/j.ncl.2017.01.008_bib101","doi-asserted-by":"crossref","first-page":"257","DOI":"10.1016\/j.neuron.2011.09.010","article-title":"A\u00a0hexanucleotide repeat expansion in C9ORF72 is the cause of chromosome 9p21-linked ALS-FTD","volume":"72","author":"Renton","year":"2011","journal-title":"Neuron"},{"issue":"1","key":"10.1016\/j.ncl.2017.01.008_bib102","doi-asserted-by":"crossref","first-page":"20","DOI":"10.1001\/archneur.1968.00470310034003","article-title":"Corticodentatonigral degeneration with neuronal achromasia","volume":"18","author":"Rebeiz","year":"1968","journal-title":"Arch Neurol"},{"issue":"5","key":"10.1016\/j.ncl.2017.01.008_bib103","doi-asserted-by":"crossref","first-page":"496","DOI":"10.1212\/WNL.0b013e31827f0fd1","article-title":"Criteria for the diagnosis of corticobasal degeneration","volume":"80","author":"Armstrong","year":"2013","journal-title":"Neurology"},{"issue":"4","key":"10.1016\/j.ncl.2017.01.008_bib104","doi-asserted-by":"crossref","first-page":"795","DOI":"10.1212\/WNL.53.4.795","article-title":"Pathologic heterogeneity in clinically diagnosed corticobasal degeneration","volume":"53","author":"Boeve","year":"1999","journal-title":"Neurology"},{"issue":"1","key":"10.1016\/j.ncl.2017.01.008_bib105","doi-asserted-by":"crossref","first-page":"41","DOI":"10.1212\/01.wnl.0000191307.69661.c3","article-title":"Clinicopathologic analysis of frontotemporal and corticobasal degenerations and PSP","volume":"66","author":"Josephs","year":"2006","journal-title":"Neurology"},{"issue":"2","key":"10.1016\/j.ncl.2017.01.008_bib106","doi-asserted-by":"crossref","first-page":"327","DOI":"10.1002\/ana.22424","article-title":"Clinicopathological correlations in corticobasal degeneration","volume":"70","author":"Lee","year":"2011","journal-title":"Ann Neurol"},{"issue":"Pt 7","key":"10.1016\/j.ncl.2017.01.008_bib107","doi-asserted-by":"crossref","first-page":"2045","DOI":"10.1093\/brain\/awq123","article-title":"Does corticobasal degeneration exist? A clinicopathological re-evaluation","volume":"133","author":"Ling","year":"2010","journal-title":"Brain"},{"issue":"3","key":"10.1016\/j.ncl.2017.01.008_bib108","doi-asserted-by":"crossref","first-page":"208","DOI":"10.1016\/j.parkreldis.2009.11.013","article-title":"Symmetric corticobasal degeneration (S-CBD)","volume":"16","author":"Hassan","year":"2010","journal-title":"Parkinsonism Relat Disord"},{"issue":"5","key":"10.1016\/j.ncl.2017.01.008_bib109","doi-asserted-by":"crossref","first-page":"710","DOI":"10.1017\/S1355617703950041","article-title":"Primary progressive aphasia: diagnosis, varieties, evolution","volume":"9","author":"Kertesz","year":"2003","journal-title":"J\u00a0Int Neuropsychol Soc"},{"issue":"Pt 9","key":"10.1016\/j.ncl.2017.01.008_bib110","doi-asserted-by":"crossref","first-page":"1996","DOI":"10.1093\/brain\/awh598","article-title":"The evolution and pathology of frontotemporal dementia","volume":"128","author":"Kertesz","year":"2005","journal-title":"Brain"},{"issue":"Suppl 3","key":"10.1016\/j.ncl.2017.01.008_bib111","doi-asserted-by":"crossref","first-page":"S336","DOI":"10.1016\/S1353-8020(08)70027-0","article-title":"The many faces of corticobasal degeneration","volume":"13","author":"Wadia","year":"2007","journal-title":"Parkinsonism Relat Disord"},{"issue":"3","key":"10.1016\/j.ncl.2017.01.008_bib112","doi-asserted-by":"crossref","first-page":"561","DOI":"10.1016\/j.nbd.2006.10.018","article-title":"The MAPT H1c risk haplotype is associated with increased expression of tau and especially of 4 repeat containing transcripts","volume":"25","author":"Myers","year":"2007","journal-title":"Neurobiol Dis"},{"issue":"23","key":"10.1016\/j.ncl.2017.01.008_bib113","doi-asserted-by":"crossref","first-page":"2034","DOI":"10.1212\/WNL.0b013e31823b9c5e","article-title":"Amyloid vs FDG-PET in the differential diagnosis of AD and FTLD","volume":"77","author":"Rabinovici","year":"2011","journal-title":"Neurology"},{"issue":"21","key":"10.1016\/j.ncl.2017.01.008_bib114","doi-asserted-by":"crossref","first-page":"1879","DOI":"10.1212\/WNL.0b013e3181feb2e8","article-title":"Imaging correlates of pathology in corticobasal syndrome","volume":"75","author":"Whitwell","year":"2010","journal-title":"Neurology"},{"issue":"1","key":"10.1016\/j.ncl.2017.01.008_bib115","doi-asserted-by":"crossref","first-page":"81","DOI":"10.1001\/archneur.63.1.81","article-title":"Patterns of brain atrophy that differentiate corticobasal degeneration syndrome from progressive supranuclear palsy","volume":"63","author":"Boxer","year":"2006","journal-title":"Arch Neurol"},{"issue":"3","key":"10.1016\/j.ncl.2017.01.008_bib116","doi-asserted-by":"crossref","first-page":"594","DOI":"10.1007\/s12031-011-9615-2","article-title":"Behavioral variant frontotemporal dementia with corticobasal degeneration pathology: phenotypic comparison to bvFTD with Pick's disease","volume":"45","author":"Rankin","year":"2011","journal-title":"J\u00a0Mol Neurosci"},{"issue":"April","key":"10.1016\/j.ncl.2017.01.008_bib117","doi-asserted-by":"crossref","first-page":"333","DOI":"10.1001\/archneur.1964.00460160003001","article-title":"Progressive supranuclear palsy","volume":"10","author":"Steele","year":"1964","journal-title":"Arch Neurol"},{"issue":"3","key":"10.1016\/j.ncl.2017.01.008_bib118","doi-asserted-by":"crossref","first-page":"325","DOI":"10.1002\/1531-8249(199909)46:3<325::AID-ANA8>3.0.CO;2-V","article-title":"Overexpression of four-repeat tau mRNA isoforms in progressive supranuclear palsy but not in Alzheimer's disease","volume":"46","author":"Chambers","year":"1999","journal-title":"Ann Neurol"},{"issue":"2","key":"10.1016\/j.ncl.2017.01.008_bib119","doi-asserted-by":"crossref","first-page":"181","DOI":"10.1002\/mds.10680","article-title":"Accuracy of clinical diagnosis of progressive supranuclear palsy","volume":"19","author":"Osaki","year":"2004","journal-title":"Mov Disord"},{"issue":"Pt\u00a04","key":"10.1016\/j.ncl.2017.01.008_bib120","doi-asserted-by":"crossref","first-page":"861","DOI":"10.1093\/brain\/awf080","article-title":"The accuracy of diagnosis of parkinsonian syndromes in a specialist movement disorder service","volume":"125","author":"Hughes","year":"2002","journal-title":"Brain"},{"issue":"1","key":"10.1016\/j.ncl.2017.01.008_bib121","doi-asserted-by":"crossref","first-page":"1","DOI":"10.1212\/WNL.47.1.1","article-title":"Clinical research criteria for the diagnosis of progressive supranuclear palsy (Steele-Richardson-Olszewski syndrome): report of the NINDS-SPSP international workshop","volume":"47","author":"Litvan","year":"1996","journal-title":"Neurology"},{"issue":"8","key":"10.1016\/j.ncl.2017.01.008_bib122","doi-asserted-by":"crossref","first-page":"723","DOI":"10.1212\/01.wnl.0000267643.24870.26","article-title":"Frontal presentation in progressive supranuclear palsy","volume":"69","author":"Donker Kaat","year":"2007","journal-title":"Neurology"},{"issue":"3","key":"10.1016\/j.ncl.2017.01.008_bib123","doi-asserted-by":"crossref","first-page":"270","DOI":"10.1016\/S1474-4422(09)70042-0","article-title":"Progressive supranuclear palsy: clinicopathological concepts and diagnostic challenges","volume":"8","author":"Williams","year":"2009","journal-title":"Lancet Neurol"},{"issue":"1\u20132","key":"10.1016\/j.ncl.2017.01.008_bib124","doi-asserted-by":"crossref","first-page":"138","DOI":"10.1016\/j.jns.2009.08.036","article-title":"Behavior and cognition in corticobasal degeneration and progressive supranuclear palsy","volume":"289","author":"Kertesz","year":"2010","journal-title":"J\u00a0Neurol Sci"},{"issue":"22","key":"10.1016\/j.ncl.2017.01.008_bib125","doi-asserted-by":"crossref","first-page":"2247","DOI":"10.1212\/WNL.0000000000001642","article-title":"Neurofilament light chain: a prognostic biomarker in amyotrophic lateral sclerosis","volume":"84","author":"Lu","year":"2015","journal-title":"Neurology"},{"issue":"8","key":"10.1016\/j.ncl.2017.01.008_bib126","doi-asserted-by":"crossref","first-page":"623","DOI":"10.1002\/acn3.325","article-title":"Neurofilament light chain: a biomarker for genetic frontotemporal dementia","volume":"3","author":"Meeter","year":"2016","journal-title":"Ann Clin Transl Neurol"},{"issue":"13","key":"10.1016\/j.ncl.2017.01.008_bib127","doi-asserted-by":"crossref","first-page":"1329","DOI":"10.1212\/WNL.0000000000003154","article-title":"Serum neurofilament light chain protein is a measure of disease intensity in frontotemporal dementia","volume":"87","author":"Rohrer","year":"2016","journal-title":"Neurology"},{"issue":"3","key":"10.1016\/j.ncl.2017.01.008_bib128","doi-asserted-by":"crossref","first-page":"216","DOI":"10.1002\/acn3.290","article-title":"Plasma neurofilament light chain predicts progression in progressive supranuclear palsy","volume":"3","author":"Rojas","year":"2016","journal-title":"Ann Clin Transl Neurol"},{"issue":"3","key":"10.1016\/j.ncl.2017.01.008_bib129","first-page":"605","article-title":"A\u00a0visual rating scale for the hummingbird sign with adjustable diagnostic validity","volume":"5","author":"Kim","year":"2015","journal-title":"J\u00a0Parkinsons Dis"},{"issue":"1","key":"10.1016\/j.ncl.2017.01.008_bib130","doi-asserted-by":"crossref","first-page":"15","DOI":"10.1007\/s00401-008-0460-5","article-title":"Nomenclature for neuropathologic subtypes of frontotemporal lobar degeneration: consensus recommendations","volume":"117","author":"Mackenzie","year":"2009","journal-title":"Acta Neuropathol"},{"issue":"1","key":"10.1016\/j.ncl.2017.01.008_bib131","doi-asserted-by":"crossref","first-page":"1","DOI":"10.1007\/s00401-009-0612-2","article-title":"Nomenclature and nosology for neuropathologic subtypes of frontotemporal lobar degeneration: an update","volume":"119","author":"Mackenzie","year":"2010","journal-title":"Acta Neuropathol"},{"issue":"5","key":"10.1016\/j.ncl.2017.01.008_bib132","doi-asserted-by":"crossref","first-page":"1858","DOI":"10.1073\/pnas.72.5.1858","article-title":"A\u00a0protein factor essential for microtubule assembly","volume":"72","author":"Weingarten","year":"1975","journal-title":"Proc Natl Acad Sci U\u00a0S\u00a0A"},{"issue":"7","key":"10.1016\/j.ncl.2017.01.008_bib133","doi-asserted-by":"crossref","first-page":"a006247","DOI":"10.1101\/cshperspect.a006247","article-title":"Biochemistry and cell biology of tau protein in neurofibrillary degeneration","volume":"2","author":"Mandelkow","year":"2012","journal-title":"Cold Spring Harb Perspect Med"},{"issue":"1","key":"10.1016\/j.ncl.2017.01.008_bib134","doi-asserted-by":"crossref","first-page":"67","DOI":"10.1097\/00001756-199801050-00014","article-title":"Tau complexes with phospholipase C-gamma in\u00a0situ","volume":"9","author":"Jenkins","year":"1998","journal-title":"Neuroreport"},{"issue":"25","key":"10.1016\/j.ncl.2017.01.008_bib135","doi-asserted-by":"crossref","first-page":"19125","DOI":"10.1074\/jbc.M110.105387","article-title":"Tau potentiates nerve growth factor-induced mitogen-activated protein kinase signaling and neurite initiation without a requirement for microtubule binding","volume":"285","author":"Leugers","year":"2010","journal-title":"J\u00a0Biol Chem"},{"issue":"3","key":"10.1016\/j.ncl.2017.01.008_bib136","doi-asserted-by":"crossref","first-page":"410","DOI":"10.1016\/j.neuron.2011.04.009","article-title":"The many faces of tau","volume":"70","author":"Morris","year":"2011","journal-title":"Neuron"},{"issue":"22","key":"10.1016\/j.ncl.2017.01.008_bib137","doi-asserted-by":"crossref","first-page":"13103","DOI":"10.1073\/pnas.95.22.13103","article-title":"Pathogenic implications of mutations in the tau gene in pallido-ponto-nigral degeneration and related neurodegenerative disorders linked to chromosome 17","volume":"95","author":"Clark","year":"1998","journal-title":"Proc Natl Acad Sci U\u00a0S\u00a0A"},{"issue":"6686","key":"10.1016\/j.ncl.2017.01.008_bib138","doi-asserted-by":"crossref","first-page":"702","DOI":"10.1038\/31508","article-title":"Association of missense and 5'-splice-site mutations in tau with the inherited dementia FTDP-17","volume":"393","author":"Hutton","year":"1998","journal-title":"Nature"},{"issue":"6","key":"10.1016\/j.ncl.2017.01.008_bib139","doi-asserted-by":"crossref","first-page":"815","DOI":"10.1002\/ana.410430617","article-title":"Tau is a candidate gene for chromosome 17 frontotemporal dementia","volume":"43","author":"Poorkaj","year":"1998","journal-title":"Ann Neurol"},{"issue":"13","key":"10.1016\/j.ncl.2017.01.008_bib140","doi-asserted-by":"crossref","first-page":"7737","DOI":"10.1073\/pnas.95.13.7737","article-title":"Mutation in the tau gene in familial multiple system tauopathy with presenile dementia","volume":"95","author":"Spillantini","year":"1998","journal-title":"Proc Natl Acad Sci U\u00a0S\u00a0A"},{"issue":"6","key":"10.1016\/j.ncl.2017.01.008_bib141","first-page":"1159","article-title":"Localization of disinhibition-dementia-parkinsonism-amyotrophy complex to 17q21-22","volume":"55","author":"Wilhelmsen","year":"1994","journal-title":"Am J Hum Genet"},{"issue":"1","key":"10.1016\/j.ncl.2017.01.008_bib142","doi-asserted-by":"crossref","first-page":"24","DOI":"10.1111\/nan.12213","article-title":"Invited review: frontotemporal dementia caused by microtubule-associated protein tau gene (MAPT) mutations: a chameleon for neuropathology and neuroimaging","volume":"41","author":"Ghetti","year":"2015","journal-title":"Neuropathol Appl Neurobiol"},{"issue":"6","key":"10.1016\/j.ncl.2017.01.008_bib143","doi-asserted-by":"crossref","first-page":"730","DOI":"10.1002\/ana.10222","article-title":"Sporadic Pick's disease: a tauopathy characterized by a spectrum of pathological tau isoforms in gray and white matter","volume":"51","author":"Zhukareva","year":"2002","journal-title":"Ann Neurol"},{"issue":"11","key":"10.1016\/j.ncl.2017.01.008_bib144","doi-asserted-by":"crossref","first-page":"1042","DOI":"10.1097\/NEN.0000000000000248","article-title":"A\u00a0novel tau mutation in exon 12, p.Q336H, causes hereditary pick disease","volume":"74","author":"Tacik","year":"2015","journal-title":"J\u00a0Neuropathol Exp Neurol"},{"key":"10.1016\/j.ncl.2017.01.008_bib145","doi-asserted-by":"crossref","first-page":"620","DOI":"10.1212\/WNL.40.4.620","article-title":"Progressive aphasia in a patient with Pick's disease: a neuropsychological, radiologic, and anatomic study","volume":"40","author":"Graff-Radford","year":"1990","journal-title":"Neurology"},{"issue":"Suppl 1","key":"10.1016\/j.ncl.2017.01.008_bib146","doi-asserted-by":"crossref","first-page":"S29","DOI":"10.1016\/j.parkreldis.2015.09.020","article-title":"Tauopathies as clinicopathological entities","volume":"22","author":"Irwin","year":"2016","journal-title":"Parkinsonism Relat Disord"},{"issue":"2","key":"10.1016\/j.ncl.2017.01.008_bib147","doi-asserted-by":"crossref","first-page":"272","DOI":"10.1002\/ana.24559","article-title":"Deep clinical and neuropathological phenotyping of Pick disease","volume":"79","author":"Irwin","year":"2016","journal-title":"Ann Neurol"},{"issue":"11","key":"10.1016\/j.ncl.2017.01.008_bib148","doi-asserted-by":"crossref","first-page":"935","DOI":"10.1093\/jnen\/61.11.935","article-title":"Office of rare diseases neuropathologic criteria for corticobasal degeneration","volume":"61","author":"Dickson","year":"2002","journal-title":"J\u00a0Neuropathol Exp Neurol"},{"issue":"2","key":"10.1016\/j.ncl.2017.01.008_bib149","doi-asserted-by":"crossref","first-page":"137","DOI":"10.1007\/s00401-011-0839-6","article-title":"Neuropathological background of phenotypical variability in frontotemporal dementia","volume":"122","author":"Josephs","year":"2011","journal-title":"Acta Neuropathol"},{"issue":"1","key":"10.1016\/j.ncl.2017.01.008_bib150","doi-asserted-by":"crossref","first-page":"97","DOI":"10.1097\/00005072-199601000-00010","article-title":"Validity and reliability of the preliminary NINDS neuropathologic criteria for progressive supranuclear palsy and related disorders","volume":"55","author":"Litvan","year":"1996","journal-title":"J\u00a0Neuropathol Exp Neurol"},{"key":"10.1016\/j.ncl.2017.01.008_bib151","doi-asserted-by":"crossref","unstructured":"Dickson D. Neurodegeneration: the molecular pathology of dementia and movement disorders. 2nd edition. Chichester, West Sussex: Wiley-Blackwell; 2011. p. 1. online resource (xvii, 477 pages).","DOI":"10.1002\/9781444341256.ch1"},{"key":"10.1016\/j.ncl.2017.01.008_bib152","doi-asserted-by":"crossref","first-page":"1121","DOI":"10.1146\/annurev.neuro.24.1.1121","article-title":"Neurodegenerative tauopathies","volume":"24","author":"Lee","year":"2001","journal-title":"Annu Rev Neurosci"},{"issue":"4","key":"10.1016\/j.ncl.2017.01.008_bib153","doi-asserted-by":"crossref","first-page":"359","DOI":"10.1097\/00005072-199904000-00006","article-title":"Progressive supranuclear palsy with dementia: cortical pathology","volume":"58","author":"Bigio","year":"1999","journal-title":"J\u00a0Neuropathol Exp Neurol"},{"issue":"2","key":"10.1016\/j.ncl.2017.01.008_bib154","doi-asserted-by":"crossref","first-page":"139","DOI":"10.1002\/ana.410400204","article-title":"Neurodegenerative disorders with extensive tau pathology: a comparative study and review","volume":"40","author":"Feany","year":"1996","journal-title":"Ann Neurol"},{"issue":"4","key":"10.1016\/j.ncl.2017.01.008_bib155","doi-asserted-by":"crossref","first-page":"537","DOI":"10.1007\/s00401-013-1171-0","article-title":"Globular glial tauopathies (GGT): consensus recommendations","volume":"126","author":"Ahmed","year":"2013","journal-title":"Acta Neuropathol"},{"issue":"3","key":"10.1016\/j.ncl.2017.01.008_bib156","doi-asserted-by":"crossref","first-page":"209","DOI":"10.1093\/jnen\/64.3.209","article-title":"Increased frequency of argyrophilic grain disease in Alzheimer disease with 4R tau-specific immunohistochemistry","volume":"64","author":"Fujino","year":"2005","journal-title":"J\u00a0Neuropathol Exp Neurol"},{"issue":"3","key":"10.1016\/j.ncl.2017.01.008_bib157","doi-asserted-by":"crossref","first-page":"270","DOI":"10.1111\/j.1365-2990.2005.00635.x","article-title":"The impact of argyrophilic grain disease on the development of dementia and its relationship to concurrent Alzheimer's disease-related pathology","volume":"31","author":"Thal","year":"2005","journal-title":"Neuropathol Appl Neurobiol"},{"issue":"4","key":"10.1016\/j.ncl.2017.01.008_bib158","doi-asserted-by":"crossref","first-page":"581","DOI":"10.1007\/s00401-013-1080-2","article-title":"Argyrophilic grain disease differs from other tauopathies by lacking tau acetylation","volume":"125","author":"Grinberg","year":"2013","journal-title":"Acta Neuropathol"},{"issue":"2","key":"10.1016\/j.ncl.2017.01.008_bib159","doi-asserted-by":"crossref","first-page":"165","DOI":"10.1111\/j.1440-1789.2005.00598.x","article-title":"Argyrophilic grain disease presenting with frontotemporal dementia: a neuropsychological and pathological study of an autopsied case with presenile onset","volume":"25","author":"Ishihara","year":"2005","journal-title":"Neuropathology"},{"issue":"2","key":"10.1016\/j.ncl.2017.01.008_bib160","doi-asserted-by":"crossref","first-page":"195","DOI":"10.1007\/s004010100365","article-title":"Argyrophilic grain disease mimicking temporal Pick's disease: a clinical, radiological, and pathological study of an autopsy case with a clinical course of 15 years","volume":"102","author":"Tsuchiya","year":"2001","journal-title":"Acta Neuropathol"},{"issue":"6","key":"10.1016\/j.ncl.2017.01.008_bib161","doi-asserted-by":"crossref","first-page":"1536","DOI":"10.1042\/BST20130186","article-title":"The role of TDP-43 in the pathogenesis of ALS and FTLD","volume":"41","author":"Baralle","year":"2013","journal-title":"Biochem Soc Trans"},{"issue":"4","key":"10.1016\/j.ncl.2017.01.008_bib162","doi-asserted-by":"crossref","first-page":"459","DOI":"10.1038\/nn.2779","article-title":"Long pre-mRNA depletion and RNA missplicing contribute to neuronal vulnerability from loss of TDP-43","volume":"14","author":"Polymenidou","year":"2011","journal-title":"Nat Neurosci"},{"key":"10.1016\/j.ncl.2017.01.008_bib163","doi-asserted-by":"crossref","first-page":"1","DOI":"10.1016\/S0065-2660(09)66001-6","article-title":"The molecular links between TDP-43 dysfunction and neurodegeneration","volume":"66","author":"Buratti","year":"2009","journal-title":"Adv Genet"},{"issue":"1","key":"10.1016\/j.ncl.2017.01.008_bib164","doi-asserted-by":"crossref","first-page":"227","DOI":"10.2353\/ajpath.2007.070182","article-title":"TDP-43 in familial and sporadic frontotemporal lobar degeneration with ubiquitin inclusions","volume":"171","author":"Cairns","year":"2007","journal-title":"Am J Pathol"},{"issue":"4","key":"10.1016\/j.ncl.2017.01.008_bib165","doi-asserted-by":"crossref","first-page":"S44","DOI":"10.1097\/WAD.0b013e31815c3486","article-title":"The neuropathology of FTD associated With ALS","volume":"21","author":"Mackenzie","year":"2007","journal-title":"Alzheimer Dis Assoc Disord"},{"issue":"7\u20138","key":"10.1016\/j.ncl.2017.01.008_bib166","doi-asserted-by":"crossref","first-page":"497","DOI":"10.3109\/21678421.2015.1074700","article-title":"Distinct clinical and pathological phenotypes in frontotemporal dementia associated with MAPT, PGRN and C9orf72 mutations","volume":"16","author":"Snowden","year":"2015","journal-title":"Amyotroph Lateral Scler Frontotemporal Degener"},{"issue":"1","key":"10.1016\/j.ncl.2017.01.008_bib167","doi-asserted-by":"crossref","first-page":"5","DOI":"10.1007\/s00401-007-0237-2","article-title":"Neuropathologic diagnostic and nosologic criteria for frontotemporal lobar degeneration: consensus of the Consortium for Frontotemporal Lobar Degeneration","volume":"114","author":"Cairns","year":"2007","journal-title":"Acta Neuropathol (Berl)"},{"issue":"6","key":"10.1016\/j.ncl.2017.01.008_bib168","doi-asserted-by":"crossref","first-page":"701","DOI":"10.1097\/WCO.0b013e32835a269b","article-title":"How do the RNA-binding proteins TDP-43 and FUS relate to amyotrophic lateral sclerosis and frontotemporal degeneration, and to each other?","volume":"25","author":"Baloh","year":"2012","journal-title":"Curr Opin Neurol"},{"key":"10.1016\/j.ncl.2017.01.008_bib169","doi-asserted-by":"crossref","first-page":"40","DOI":"10.1016\/j.brainres.2011.12.010","article-title":"FET proteins in frontotemporal dementia and amyotrophic lateral sclerosis","volume":"1462","author":"Mackenzie","year":"2012","journal-title":"Brain Res"},{"issue":"5","key":"10.1016\/j.ncl.2017.01.008_bib170","doi-asserted-by":"crossref","first-page":"617","DOI":"10.1007\/s00401-009-0598-9","article-title":"FUS pathology in basophilic inclusion body disease","volume":"118","author":"Munoz","year":"2009","journal-title":"Acta Neuropathol"},{"issue":"2","key":"10.1016\/j.ncl.2017.01.008_bib171","doi-asserted-by":"crossref","first-page":"207","DOI":"10.1007\/s00401-010-0764-0","article-title":"Distinct pathological subtypes of FTLD-FUS","volume":"121","author":"Mackenzie","year":"2011","journal-title":"Acta Neuropathol"},{"issue":"5","key":"10.1016\/j.ncl.2017.01.008_bib172","doi-asserted-by":"crossref","first-page":"605","DOI":"10.1007\/s00401-009-0581-5","article-title":"Abundant FUS-immunoreactive pathology in neuronal intermediate filament inclusion disease","volume":"118","author":"Neumann","year":"2009","journal-title":"Acta Neuropathol"},{"issue":"9","key":"10.1016\/j.ncl.2017.01.008_bib173","first-page":"1","article-title":"Topography of FUS pathology distinguishes late-onset BIBD from aFTLD-U","volume":"1","author":"Lee","year":"2013","journal-title":"Acta Neuropathol Commun"},{"issue":"5","key":"10.1016\/j.ncl.2017.01.008_bib174","doi-asserted-by":"crossref","first-page":"719","DOI":"10.1007\/s00401-009-0593-1","article-title":"Absence of FUS-immunoreactive pathology in frontotemporal dementia linked to chromosome 3 (FTD-3) caused by mutation in the CHMP2B gene","volume":"118","author":"Holm","year":"2009","journal-title":"Acta Neuropathol"},{"issue":"8","key":"10.1016\/j.ncl.2017.01.008_bib175","doi-asserted-by":"crossref","first-page":"806","DOI":"10.1038\/ng1609","article-title":"Mutations in the endosomal ESCRTIII-complex subunit CHMP2B in frontotemporal dementia","volume":"37","author":"Skibinski","year":"2005","journal-title":"Nat Genet"},{"issue":"7","key":"10.1016\/j.ncl.2017.01.008_bib176","doi-asserted-by":"crossref","first-page":"817","DOI":"10.1001\/archneur.56.7.817","article-title":"Inheritance of frontotemporal dementia","volume":"56","author":"Chow","year":"1999","journal-title":"Arch Neurol"},{"issue":"3","key":"10.1016\/j.ncl.2017.01.008_bib177","doi-asserted-by":"crossref","first-page":"288","DOI":"10.1001\/archneurpsyc.1943.02290210066004","article-title":"Geneaologic and clinicopathologic study of Pick\u2019s disease","volume":"50","author":"Malamud","year":"1943","journal-title":"Arch Neur Psych"},{"issue":"74","key":"10.1016\/j.ncl.2017.01.008_bib178","first-page":"189","article-title":"Alzheimer's disease-Pick\u2019s disease; a clinical analysis of 72 cases. Acta psychiatrica et neurologica Scandinavica","author":"Sjogren","year":"1951","journal-title":"Supplementum"},{"key":"10.1016\/j.ncl.2017.01.008_bib179","first-page":"1159","article-title":"Localization of disinhibition-dementia-parkinsonism-amyotrophy complex to 17q21-22","volume":"55","author":"Wilhelmsen","year":"1994","journal-title":"Am J Hum Genet"},{"issue":"21","key":"10.1016\/j.ncl.2017.01.008_bib180","doi-asserted-by":"crossref","first-page":"15134","DOI":"10.1074\/jbc.274.21.15134","article-title":"5' splice site mutations in tau associated with the inherited dementia FTDP-17 affect a stem-loop structure that regulates alternative splicing of exon 10","volume":"274","author":"Grover","year":"1999","journal-title":"J\u00a0Biol Chem"},{"issue":"6","key":"10.1016\/j.ncl.2017.01.008_bib181","doi-asserted-by":"crossref","first-page":"542","DOI":"10.1097\/WCO.0b013e32834cd442","article-title":"Phenotypic signatures of genetic frontotemporal dementia","volume":"24","author":"Rohrer","year":"2011","journal-title":"Curr Opin Neurol"},{"issue":"6","key":"10.1016\/j.ncl.2017.01.008_bib182","doi-asserted-by":"crossref","first-page":"920","DOI":"10.1002\/ana.20668","article-title":"Phenotypic heterogeneity within a new family with the MAPT p301s mutation","volume":"58","author":"Yasuda","year":"2005","journal-title":"Ann Neurol"},{"issue":"9","key":"10.1016\/j.ncl.2017.01.008_bib183","doi-asserted-by":"crossref","first-page":"813","DOI":"10.1212\/01.wnl.0000343851.46573.67","article-title":"Voxel-based morphometry patterns of atrophy in FTLD with mutations in MAPT or PGRN","volume":"72","author":"Whitwell","year":"2009","journal-title":"Neurology"},{"issue":"2","key":"10.1016\/j.ncl.2017.01.008_bib184","doi-asserted-by":"crossref","first-page":"277","DOI":"10.1002\/ana.410410222","article-title":"Genetic evidence for the involvement of tau in progressive supranuclear palsy [see comments]","volume":"41","author":"Conrad","year":"1997","journal-title":"Ann Neurol"},{"issue":"15","key":"10.1016\/j.ncl.2017.01.008_bib185","doi-asserted-by":"crossref","first-page":"3500","DOI":"10.1093\/hmg\/dds161","article-title":"Evidence for a role of the rare p.A152T variant in MAPT in increasing the risk for FTD-spectrum and Alzheimer's diseases","volume":"21","author":"Coppola","year":"2012","journal-title":"Hum Mol Genet"},{"issue":"7105","key":"10.1016\/j.ncl.2017.01.008_bib186","doi-asserted-by":"crossref","first-page":"916","DOI":"10.1038\/nature05016","article-title":"Mutations in progranulin cause tau-negative frontotemporal dementia linked to chromosome 17","volume":"442","author":"Baker","year":"2006","journal-title":"Nature"},{"issue":"7105","key":"10.1016\/j.ncl.2017.01.008_bib187","doi-asserted-by":"crossref","first-page":"920","DOI":"10.1038\/nature05017","article-title":"Null mutations in progranulin cause ubiquitin-positive frontotemporal dementia linked to chromosome 17q21","volume":"442","author":"Cruts","year":"2006","journal-title":"Nature"},{"issue":"7","key":"10.1016\/j.ncl.2017.01.008_bib188","doi-asserted-by":"crossref","first-page":"388","DOI":"10.1016\/j.tins.2014.04.003","article-title":"Progranulin in neurodegenerative disease","volume":"37","author":"Petkau","year":"2014","journal-title":"Trends Neurosci"},{"issue":"3","key":"10.1016\/j.ncl.2017.01.008_bib189","doi-asserted-by":"crossref","first-page":"574","DOI":"10.1007\/s12031-011-9622-3","article-title":"Potential mechanisms of progranulin-deficient FTLD","volume":"45","author":"Ward","year":"2011","journal-title":"J\u00a0Mol Neurosci"},{"issue":"1","key":"10.1016\/j.ncl.2017.01.008_bib190","doi-asserted-by":"crossref","first-page":"92","DOI":"10.1002\/ana.21397","article-title":"Gene expression study on peripheral blood identifies progranulin mutations","volume":"64","author":"Coppola","year":"2008","journal-title":"Ann Neurol"},{"issue":"1","key":"10.1016\/j.ncl.2017.01.008_bib191","doi-asserted-by":"crossref","first-page":"37","DOI":"10.1083\/jcb.200712039","article-title":"Progranulin functions as a neurotrophic factor to regulate neurite outgrowth and enhance neuronal survival","volume":"181","author":"Van Damme","year":"2008","journal-title":"J\u00a0Cell Biol"},{"issue":"1","key":"10.1016\/j.ncl.2017.01.008_bib192","doi-asserted-by":"crossref","first-page":"49","DOI":"10.1007\/s00401-007-0223-8","article-title":"The neuropathology and clinical phenotype of FTD with progranulin mutations","volume":"114","author":"Mackenzie","year":"2007","journal-title":"Acta Neuropathol"},{"issue":"Pt 3","key":"10.1016\/j.ncl.2017.01.008_bib193","doi-asserted-by":"crossref","first-page":"732","DOI":"10.1093\/brain\/awn012","article-title":"Phenotype variability in progranulin mutation carriers: a clinical, neuropsychological, imaging and genetic study","volume":"131","author":"Le Ber","year":"2008","journal-title":"Brain"},{"issue":"10","key":"10.1016\/j.ncl.2017.01.008_bib194","doi-asserted-by":"crossref","first-page":"965","DOI":"10.1016\/S1474-4422(08)70194-7","article-title":"Mutations in progranulin (GRN) within the spectrum of clinical and pathological phenotypes of frontotemporal dementia","volume":"7","author":"van Swieten","year":"2008","journal-title":"Lancet Neurol"},{"issue":"6","key":"10.1016\/j.ncl.2017.01.008_bib195","doi-asserted-by":"crossref","first-page":"1102","DOI":"10.1016\/j.ajhg.2012.04.021","article-title":"Strikingly different clinicopathological phenotypes determined by progranulin-mutation dosage","volume":"90","author":"Smith","year":"2012","journal-title":"Am J Hum Genet"},{"issue":"2","key":"10.1016\/j.ncl.2017.01.008_bib196","doi-asserted-by":"crossref","first-page":"1224","DOI":"10.1016\/j.neurobiolaging.2014.10.011","article-title":"Dipeptide repeat protein toxicity in frontotemporal lobar degeneration and in motor neurone disease associated with expansions in C9ORF72\u2014a cautionary note","volume":"36","author":"Mann","year":"2015","journal-title":"Neurobiol Aging"},{"issue":"6","key":"10.1016\/j.ncl.2017.01.008_bib197","doi-asserted-by":"crossref","first-page":"859","DOI":"10.1007\/s00401-013-1181-y","article-title":"Dipeptide repeat protein pathology in C9ORF72 mutation cases: clinico-pathological correlations","volume":"126","author":"Mackenzie","year":"2013","journal-title":"Acta Neuropathol"},{"issue":"Suppl 1","key":"10.1016\/j.ncl.2017.01.008_bib198","doi-asserted-by":"crossref","first-page":"54","DOI":"10.1111\/jnc.13588","article-title":"Molecular neuropathology of frontotemporal dementia: insights into disease mechanisms from postmortem studies","volume":"138","author":"Mackenzie","year":"2016","journal-title":"J\u00a0Neurochem"},{"issue":"Pt 12","key":"10.1016\/j.ncl.2017.01.008_bib199","doi-asserted-by":"crossref","first-page":"3202","DOI":"10.1093\/brain\/aww250","article-title":"Timing and significance of pathological features in C9orf72 expansion-associated frontotemporal dementia","volume":"139","author":"Vatsavayai","year":"2016","journal-title":"Brain"},{"issue":"5","key":"10.1016\/j.ncl.2017.01.008_bib200","doi-asserted-by":"crossref","first-page":"601","DOI":"10.1111\/nan.12178","article-title":"Accumulation of dipeptide repeat proteins predates that of TDP-43 in frontotemporal lobar degeneration associated with hexanucleotide repeat expansions in C9ORF72 gene","volume":"41","author":"Baborie","year":"2015","journal-title":"Neuropathol Appl Neurobiol"},{"issue":"3","key":"10.1016\/j.ncl.2017.01.008_bib201","doi-asserted-by":"crossref","first-page":"451","DOI":"10.1007\/s00401-014-1245-7","article-title":"Early dipeptide repeat pathology in a frontotemporal dementia kindred with C9ORF72 mutation and intellectual disability","volume":"127","author":"Proudfoot","year":"2014","journal-title":"Acta Neuropathol"},{"issue":"Pt 3","key":"10.1016\/j.ncl.2017.01.008_bib202","doi-asserted-by":"crossref","first-page":"765","DOI":"10.1093\/brain\/aws004","article-title":"Characterization of frontotemporal dementia and\/or amyotrophic lateral sclerosis associated with the GGGGCC repeat expansion in C9ORF72","volume":"135","author":"Boeve","year":"2012","journal-title":"Brain"},{"issue":"10","key":"10.1016\/j.ncl.2017.01.008_bib203","doi-asserted-by":"crossref","first-page":"1002","DOI":"10.1212\/WNL.0b013e318268452e","article-title":"Frontotemporal dementia due to C9ORF72 mutations: clinical and imaging features","volume":"79","author":"Sha","year":"2012","journal-title":"Neurology"},{"issue":"Pt 3","key":"10.1016\/j.ncl.2017.01.008_bib204","doi-asserted-by":"crossref","first-page":"794","DOI":"10.1093\/brain\/aws001","article-title":"Neuroimaging signatures of frontotemporal dementia genetics: C9ORF72, tau, progranulin and sporadics","volume":"135","author":"Whitwell","year":"2012","journal-title":"Brain"},{"issue":"Pt 11","key":"10.1016\/j.ncl.2017.01.008_bib205","doi-asserted-by":"crossref","first-page":"3047","DOI":"10.1093\/brain\/awu248","article-title":"Altered network connectivity in frontotemporal dementia with C9orf72 hexanucleotide repeat expansion","volume":"137","author":"Lee","year":"2014","journal-title":"Brain"},{"issue":"2","key":"10.1016\/j.ncl.2017.01.008_bib206","doi-asserted-by":"crossref","first-page":"152","DOI":"10.1097\/nen.0b013e31803020b9","article-title":"TDP-43 in the ubiquitin pathology of frontotemporal dementia with VCP gene mutations","volume":"66","author":"Neumann","year":"2007","journal-title":"J\u00a0Neuropathol Exp Neurol"},{"issue":"5","key":"10.1016\/j.ncl.2017.01.008_bib207","doi-asserted-by":"crossref","first-page":"420","DOI":"10.1111\/j.1399-0004.2007.00887.x","article-title":"Novel VCP mutations in inclusion body myopathy associated with Paget disease of bone and frontotemporal dementia","volume":"72","author":"Watts","year":"2007","journal-title":"Clin Genet"},{"issue":"5","key":"10.1016\/j.ncl.2017.01.008_bib208","doi-asserted-by":"crossref","first-page":"857","DOI":"10.1016\/j.neuron.2010.11.036","article-title":"Exome sequencing reveals VCP mutations as a cause of familial ALS","volume":"68","author":"Johnson","year":"2010","journal-title":"Neuron"},{"issue":"12","key":"10.1016\/j.ncl.2017.01.008_bib209","doi-asserted-by":"crossref","first-page":"2327.e1-e5","DOI":"10.1016\/j.neurobiolaging.2011.06.009","article-title":"A\u00a0patient carrying a homozygous p.A382T TARDBP missense mutation shows a syndrome including ALS, extrapyramidal symptoms, and FTD","volume":"32","author":"Borghero","year":"2011","journal-title":"Neurobiol Aging"},{"issue":"12","key":"10.1016\/j.ncl.2017.01.008_bib210","doi-asserted-by":"crossref","first-page":"1843","DOI":"10.1002\/mds.22697","article-title":"TARDBP variation associated with frontotemporal dementia, supranuclear gaze palsy, and chorea","volume":"24","author":"Kovacs","year":"2009","journal-title":"Mov Disord"},{"issue":"8","key":"10.1016\/j.ncl.2017.01.008_bib211","doi-asserted-by":"crossref","first-page":"1846.e1-e4","DOI":"10.1016\/j.neurobiolaging.2012.01.108","article-title":"Wide phenotypic spectrum of the TARDBP gene: homozygosity of A382T mutation in a patient presenting with amyotrophic lateral sclerosis, Parkinson's disease, and frontotemporal lobar degeneration, and in neurologically healthy subject","volume":"33","author":"Mosca","year":"2012","journal-title":"Neurobiol Aging"},{"issue":"5","key":"10.1016\/j.ncl.2017.01.008_bib212","doi-asserted-by":"crossref","first-page":"631","DOI":"10.1038\/nn.4000","article-title":"Haploinsufficiency of TBK1 causes familial ALS and fronto-temporal dementia","volume":"18","author":"Freischmidt","year":"2015","journal-title":"Nat Neurosci"},{"issue":"1","key":"10.1016\/j.ncl.2017.01.008_bib213","doi-asserted-by":"crossref","first-page":"77","DOI":"10.1007\/s00401-015-1436-x","article-title":"Whole-genome sequencing reveals important role for TBK1 and OPTN mutations in frontotemporal lobar degeneration without motor neuron disease","volume":"130","author":"Pottier","year":"2015","journal-title":"Acta Neuropathol"},{"issue":"Suppl 1","key":"10.1016\/j.ncl.2017.01.008_bib214","doi-asserted-by":"crossref","first-page":"32","DOI":"10.1111\/jnc.13622","article-title":"Genetics of FTLD: overview and what else we can expect from genetic studies","volume":"138","author":"Pottier","year":"2016","journal-title":"J\u00a0Neurochem"},{"issue":"11","key":"10.1016\/j.ncl.2017.01.008_bib215","doi-asserted-by":"crossref","first-page":"1440","DOI":"10.1001\/archneurol.2011.250","article-title":"SQSTM1 mutations in familial and sporadic amyotrophic lateral sclerosis","volume":"68","author":"Fecto","year":"2011","journal-title":"Arch Neurol"},{"issue":"7363","key":"10.1016\/j.ncl.2017.01.008_bib216","doi-asserted-by":"crossref","first-page":"211","DOI":"10.1038\/nature10353","article-title":"Mutations in UBQLN2 cause dominant X-linked juvenile and adult-onset ALS and ALS\/dementia","volume":"477","author":"Deng","year":"2011","journal-title":"Nature"},{"issue":"3","key":"10.1016\/j.ncl.2017.01.008_bib217","doi-asserted-by":"crossref","first-page":"190","DOI":"10.1080\/13554790802632967","article-title":"Of brain and bone: the unusual case of Dr. A","volume":"15","author":"Narvid","year":"2009","journal-title":"Neurocase"},{"issue":"2","key":"10.1016\/j.ncl.2017.01.008_bib218","doi-asserted-by":"crossref","first-page":"506","DOI":"10.1111\/j.1447-0594.2012.00956.x","article-title":"Pilot study of pharmacological treatment for frontotemporal dementia: risk of donepezil treatment for behavioral and psychological symptoms","volume":"13","author":"Kimura","year":"2013","journal-title":"Geriatr Gerontol Int"},{"issue":"1","key":"10.1016\/j.ncl.2017.01.008_bib219","doi-asserted-by":"crossref","first-page":"84","DOI":"10.1097\/01.JGP.0000231744.69631.33","article-title":"Preliminary findings: behavioral worsening on donepezil in patients with frontotemporal dementia","volume":"15","author":"Mendez","year":"2007","journal-title":"Am J Geriatr Psychiatry"},{"issue":"2","key":"10.1016\/j.ncl.2017.01.008_bib220","doi-asserted-by":"crossref","first-page":"149","DOI":"10.1016\/S1474-4422(12)70320-4","article-title":"Memantine in patients with frontotemporal lobar degeneration: a multicentre, randomised, double-blind, placebo-controlled trial","volume":"12","author":"Boxer","year":"2013","journal-title":"Lancet Neurol"},{"issue":"4","key":"10.1016\/j.ncl.2017.01.008_bib221","doi-asserted-by":"crossref","first-page":"749","DOI":"10.3233\/JAD-2010-101632","article-title":"Memantine in behavioral variant frontotemporal dementia: negative results","volume":"23","author":"Vercelletto","year":"2011","journal-title":"J\u00a0Alzheimers Dis"},{"issue":"9","key":"10.1016\/j.ncl.2017.01.008_bib222","doi-asserted-by":"crossref","first-page":"789","DOI":"10.1097\/JGP.0b013e31823033f3","article-title":"Serotonergic function and treatment of behavioral and psychological symptoms of frontotemporal dementia","volume":"20","author":"Herrmann","year":"2012","journal-title":"Am J Geriatr Psychiatry"},{"issue":"3","key":"10.1016\/j.ncl.2017.01.008_bib223","doi-asserted-by":"crossref","first-page":"117","DOI":"10.1159\/000076343","article-title":"Efficacy of fluvoxamine as a treatment for behavioral symptoms in frontotemporal lobar degeneration patients","volume":"17","author":"Ikeda","year":"2004","journal-title":"Dement Geriatr Cogn Disord"},{"issue":"6","key":"10.1016\/j.ncl.2017.01.008_bib224","doi-asserted-by":"crossref","first-page":"742","DOI":"10.1002\/mds.20465","article-title":"Stereotypical movements and frontotemporal dementia","volume":"20","author":"Mendez","year":"2005","journal-title":"Mov Disord"},{"issue":"5","key":"10.1016\/j.ncl.2017.01.008_bib225","doi-asserted-by":"crossref","first-page":"212","DOI":"10.4088\/JCP.v58n0506","article-title":"Frontotemporal dementia: treatment response to serotonin selective reuptake inhibitors","volume":"58","author":"Swartz","year":"1997","journal-title":"J\u00a0Clin Psychiatry"},{"issue":"4","key":"10.1016\/j.ncl.2017.01.008_bib226","doi-asserted-by":"crossref","first-page":"355","DOI":"10.1159\/000077171","article-title":"Frontotemporal dementia: a randomised, controlled trial with trazodone","volume":"17","author":"Lebert","year":"2004","journal-title":"Dement Geriatr Cogn Disord"},{"issue":"1","key":"10.1016\/j.ncl.2017.01.008_bib227","doi-asserted-by":"crossref","first-page":"67","DOI":"10.1002\/gps.774","article-title":"Vulnerability to neuroleptic side effects in frontotemporal lobar degeneration","volume":"18","author":"Pijnenburg","year":"2003","journal-title":"Int J Geriatr Psychiatry"},{"issue":"5","key":"10.1016\/j.ncl.2017.01.008_bib228","doi-asserted-by":"crossref","first-page":"267","DOI":"10.1177\/153331750201700504","article-title":"Goals in symptomatic pharmacologic management of frontotemporal lobar degeneration","volume":"17","author":"Chow","year":"2002","journal-title":"Am J Alzheimers Dis Other Demen"},{"issue":"2","key":"10.1016\/j.ncl.2017.01.008_bib229","doi-asserted-by":"crossref","first-page":"104","DOI":"10.1097\/WNN.0b013e31816bdf73","article-title":"Topiramate may modulate alcohol abuse but not other compulsive behaviors in frontotemporal dementia: case report","volume":"21","author":"Cruz","year":"2008","journal-title":"Cogn Behav Neurol"},{"issue":"3","key":"10.1016\/j.ncl.2017.01.008_bib230","doi-asserted-by":"crossref","first-page":"696","DOI":"10.1007\/s12031-011-9550-2","article-title":"New potential therapeutic approaches in frontotemporal dementia: oxytocin, vasopressin, and social cognition","volume":"45","author":"Finger","year":"2011","journal-title":"J\u00a0Mol Neurosci"},{"issue":"Pt 9","key":"10.1016\/j.ncl.2017.01.008_bib231","doi-asserted-by":"crossref","first-page":"2493","DOI":"10.1093\/brain\/awr171","article-title":"The effects of oxytocin on social cognition and behaviour in frontotemporal dementia","volume":"134","author":"Jesso","year":"2011","journal-title":"Brain"},{"issue":"4","key":"10.1016\/j.ncl.2017.01.008_bib232","doi-asserted-by":"crossref","first-page":"S64","DOI":"10.1097\/WAD.0b013e31815bf774","article-title":"A\u00a0model for management of behavioral symptoms in frontotemporal lobar degeneration","volume":"21","author":"Merrilees","year":"2007","journal-title":"Alzheimer Dis Assoc Disord"},{"issue":"1","key":"10.1016\/j.ncl.2017.01.008_bib233","doi-asserted-by":"crossref","first-page":"63","DOI":"10.1016\/j.jagp.2013.01.060","article-title":"Mental and physical activities delay cognitive decline in older persons with dementia","volume":"22","author":"Cheng","year":"2014","journal-title":"Am J Geriatr Psychiatry"},{"issue":"2","key":"10.1016\/j.ncl.2017.01.008_bib234","doi-asserted-by":"crossref","first-page":"237","DOI":"10.3109\/09540261.2012.751017","article-title":"Behavioural interventions for enhancing life participation in behavioural variant frontotemporal dementia and primary progressive aphasia","volume":"25","author":"Kortte","year":"2013","journal-title":"Int Rev Psychiatry"},{"issue":"2","key":"10.1016\/j.ncl.2017.01.008_bib235","doi-asserted-by":"crossref","first-page":"126","DOI":"10.1007\/s11940-012-0168-7","article-title":"Treatment options for tauopathies","volume":"14","author":"Karakaya","year":"2012","journal-title":"Curr Treat Options Neurol"},{"issue":"3","key":"10.1016\/j.ncl.2017.01.008_bib236","doi-asserted-by":"crossref","first-page":"443","DOI":"10.1016\/j.nurt.2008.05.006","article-title":"Tau-based treatment strategies in neurodegenerative diseases","volume":"5","author":"Schneider","year":"2008","journal-title":"Neurotherapeutics"},{"issue":"Suppl 1","key":"10.1016\/j.ncl.2017.01.008_bib237","doi-asserted-by":"crossref","first-page":"211","DOI":"10.1111\/jnc.13640","article-title":"Therapy and clinical trials in frontotemporal dementia: past, present, and future","volume":"138","author":"Tsai","year":"2016","journal-title":"J\u00a0Neurochem"},{"issue":"2","key":"10.1016\/j.ncl.2017.01.008_bib238","doi-asserted-by":"crossref","first-page":"176","DOI":"10.1016\/j.jalz.2012.03.002","article-title":"Frontotemporal degeneration, the next therapeutic frontier: molecules and animal models for frontotemporal degeneration drug development","volume":"9","author":"Boxer","year":"2013","journal-title":"Alzheimers Dement"},{"issue":"2","key":"10.1016\/j.ncl.2017.01.008_bib239","doi-asserted-by":"crossref","first-page":"189","DOI":"10.1016\/j.jalz.2012.03.003","article-title":"The advantages of frontotemporal degeneration drug development (part 2 of frontotemporal degeneration: the next therapeutic frontier)","volume":"9","author":"Boxer","year":"2013","journal-title":"Alzheimers Dement"},{"issue":"47","key":"10.1016\/j.ncl.2017.01.008_bib240","doi-asserted-by":"crossref","first-page":"E4530","DOI":"10.1073\/pnas.1318835110","article-title":"Targeted degradation of sense and antisense C9orf72 RNA foci as therapy for ALS and frontotemporal degeneration","volume":"110","author":"Lagier-Tourenne","year":"2013","journal-title":"Proc Natl Acad Sci U\u00a0S\u00a0A"}],"container-title":["Neurologic Clinics"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0733861917300087?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0733861917300087?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2023,8,22]],"date-time":"2023-08-22T22:57:51Z","timestamp":1692745071000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0733861917300087"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2017,5]]},"references-count":240,"journal-issue":{"issue":"2","published-print":{"date-parts":[[2017,5]]}},"alternative-id":["S0733861917300087"],"URL":"https:\/\/doi.org\/10.1016\/j.ncl.2017.01.008","relation":{},"ISSN":["0733-8619"],"issn-type":[{"value":"0733-8619","type":"print"}],"subject":[],"published":{"date-parts":[[2017,5]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"Frontotemporal Dementia","name":"articletitle","label":"Article Title"},{"value":"Neurologic Clinics","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.ncl.2017.01.008","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"\u00a9 2017 Elsevier Inc. All rights reserved.","name":"copyright","label":"Copyright"}]}}