{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,10]],"date-time":"2026-10-10T13:27:17Z","timestamp":1791638837597,"version":"4.3.4"},"reference-count":146,"publisher":"Elsevier BV","issue":"2","license":[{"start":{"date-parts":[[2019,5,1]],"date-time":"2019-05-01T00:00:00Z","timestamp":1556668800000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"}],"content-domain":{"domain":["clinicalkey.jp","clinicalkey.com","clinicalkey.es","theclinics.com","clinicalkey.com.au","clinicalkey.fr","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Neurologic Clinics"],"published-print":{"date-parts":[[2019,5]]},"DOI":"10.1016\/j.ncl.2019.01.004","type":"journal-article","created":{"date-parts":[[2019,4,2]],"date-time":"2019-04-02T23:10:04Z","timestamp":1554246604000},"page":"279-302","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":14,"title":["Stroke due to Vasculitis in Children and Adults"],"prefix":"10.1016","volume":"37","author":[{"given":"David S.","family":"Younger","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"key":"10.1016\/j.ncl.2019.01.004_bib1","doi-asserted-by":"crossref","first-page":"1","DOI":"10.1002\/art.37715","article-title":"2012 revised International Chapel Hill Consensus Conference Nomenclature of Vasculitides","volume":"65","author":"Jennette","year":"2013","journal-title":"Arthritis Rheum"},{"key":"10.1016\/j.ncl.2019.01.004_bib2","doi-asserted-by":"crossref","first-page":"1637","DOI":"10.1002\/art.39068","article-title":"Adult primary central nervous system vasculitis: treatment and course","volume":"67","author":"Salvarani","year":"2015","journal-title":"Arthritis Rheum"},{"key":"10.1016\/j.ncl.2019.01.004_bib3","doi-asserted-by":"crossref","first-page":"514","DOI":"10.1001\/archneur.1988.00520290042012","article-title":"Granulomatous angiitis of the brain. An inflammatory reaction of diverse etiology","volume":"45","author":"Younger","year":"1988","journal-title":"Arch Neurol"},{"key":"10.1016\/j.ncl.2019.01.004_bib4","doi-asserted-by":"crossref","first-page":"20","DOI":"10.1097\/00005792-198801000-00002","article-title":"Primary angiitis of the central nervous system: report of 8 new cases, review of the literature, and proposal for diagnostic criteria","volume":"67","author":"Calabrese","year":"1988","journal-title":"Medicine"},{"key":"10.1016\/j.ncl.2019.01.004_bib5","doi-asserted-by":"crossref","first-page":"936","DOI":"10.1136\/ard.2005.046300","article-title":"EULAR\/PReS endorsed consensus criteria for the classification of childhood vasculitides","volume":"65","author":"Ozen","year":"2006","journal-title":"Ann Rheum Dis"},{"key":"10.1016\/j.ncl.2019.01.004_bib6","doi-asserted-by":"crossref","first-page":"283","DOI":"10.1016\/B978-0-444-63432-0.00016-5","article-title":"Central nervous system vasculitis in adults and children","volume":"133","author":"Twilt","year":"2016","journal-title":"Handb Clin Neurol"},{"key":"10.1016\/j.ncl.2019.01.004_bib7","doi-asserted-by":"crossref","first-page":"35","DOI":"10.1161\/01.STR.24.1.35","article-title":"Classification of subtype of acute ischemic stroke. Definitions for use in a multicenter clinical trial. TOAST. Trial of Org 10172 in Acute Stroke Treatment","volume":"24","author":"Adams","year":"1993","journal-title":"Stroke"},{"key":"10.1016\/j.ncl.2019.01.004_bib8","doi-asserted-by":"crossref","first-page":"1195","DOI":"10.1161\/STROKEAHA.108.529883","article-title":"Analysis of 1008 consecutive patients aged 15 to 49 with first-ever ischemic stroke: the Helsinki young stroke registry","volume":"40","author":"Putaala","year":"2009","journal-title":"Stroke"},{"key":"10.1016\/j.ncl.2019.01.004_bib9","doi-asserted-by":"crossref","first-page":"371","DOI":"10.1161\/STROKEAHA.111.624585","article-title":"Towards a consensus-based classification of childhood arterial ischemic stroke","volume":"43","author":"Bernard","year":"2012","journal-title":"Stroke"},{"issue":"10","key":"10.1016\/j.ncl.2019.01.004_bib10","doi-asserted-by":"crossref","first-page":"2443","DOI":"10.1161\/STROKEAHA.116.013544","article-title":"Inter-rater reliability of the CASCADE criteria: challenges in classifying arteriopathies","volume":"47","author":"Bernard","year":"2016","journal-title":"Stroke"},{"key":"10.1016\/j.ncl.2019.01.004_bib11","doi-asserted-by":"crossref","first-page":"2172","DOI":"10.3174\/ajnr.A5376","article-title":"Clinical and imaging characteristics of arteriopathy subtypes in children with arterial ischemic stroke: results of the VIPS study","volume":"38","author":"Wintermark","year":"2017","journal-title":"AJNR Am J Neuroradiol"},{"key":"10.1016\/j.ncl.2019.01.004_bib12","doi-asserted-by":"crossref","first-page":"317","DOI":"10.1097\/00019052-200406000-00014","article-title":"Vasculitis of the nervous system","volume":"17","author":"Younger","year":"2004","journal-title":"Curr Opin Neurol"},{"key":"10.1016\/j.ncl.2019.01.004_bib13","doi-asserted-by":"crossref","first-page":"442","DOI":"10.1002\/ana.21226","article-title":"Primary central nervous system vasculitis of 101 patients","volume":"62","author":"Salvarani","year":"2007","journal-title":"Ann Neurol"},{"key":"10.1016\/j.ncl.2019.01.004_bib14","doi-asserted-by":"crossref","first-page":"704","DOI":"10.1001\/archneurol.2009.76","article-title":"Primary angiitis of the central nervous system","volume":"66","author":"Birnbaum","year":"2009","journal-title":"Arch Neurol"},{"key":"10.1016\/j.ncl.2019.01.004_bib15","doi-asserted-by":"crossref","first-page":"1946","DOI":"10.1161\/STROKEAHA.118.021878","article-title":"Treatment and long-term outcomes of primary central nervous system vasculitis","volume":"49","author":"De Boysson","year":"2018","journal-title":"Stroke"},{"key":"10.1016\/j.ncl.2019.01.004_bib16","doi-asserted-by":"crossref","first-page":"1141","DOI":"10.1007\/s00381-012-1827-4","article-title":"Cerebral haemorrhage in the presence of primary childhood central nervous system vasculitis\u2013a review","volume":"28","author":"Pistracher","year":"2012","journal-title":"Childs Nerv Syst"},{"key":"10.1016\/j.ncl.2019.01.004_bib17","doi-asserted-by":"crossref","first-page":"2159","DOI":"10.1002\/art.21144","article-title":"Angiography-negative primary central nervous system vasculitis in children: a newly recognized inflammatory central nervous system disease","volume":"52","author":"Benseler","year":"2005","journal-title":"Arthritis Rheum"},{"key":"10.1016\/j.ncl.2019.01.004_bib18","doi-asserted-by":"crossref","first-page":"1359","DOI":"10.1093\/rheumatology\/ket398","article-title":"Childhood inflammatory brain diseases: pathogenesis, diagnosis and therapy","volume":"53","author":"Twilt","year":"2014","journal-title":"Rheumatology (Oxford)"},{"key":"10.1016\/j.ncl.2019.01.004_bib19","doi-asserted-by":"crossref","first-page":"1470","DOI":"10.1002\/art.40112","article-title":"Early outcomes in children with antineutrophil cytoplasmic antibody-associated vasculitis","volume":"69","author":"Morishita","year":"2017","journal-title":"Arthritis Rheum"},{"issue":"12","key":"10.1016\/j.ncl.2019.01.004_bib20","doi-asserted-by":"crossref","first-page":"1989","DOI":"10.1136\/annrheumdis-2012-202408","article-title":"Large-vessel involvement in giant cell arteritis: a population based cohort study of the incidence-trends and prognosis","volume":"72","author":"Kermani","year":"2012","journal-title":"Ann Rheum Dis"},{"key":"10.1016\/j.ncl.2019.01.004_bib21","doi-asserted-by":"crossref","first-page":"3522","DOI":"10.1002\/art.11353","article-title":"Incidence and predictors of large-artery complication (aortic aneurysm, aortic dissection, and\/or large artery stenosis) in patients with giant cell arteritis","volume":"48","author":"Nuenninghoff","year":"2003","journal-title":"Arthritis Rheum"},{"key":"10.1016\/j.ncl.2019.01.004_bib22","doi-asserted-by":"crossref","first-page":"261","DOI":"10.1056\/NEJMra011913","article-title":"Polymyalgia rheumatic and giant cell arteritis","volume":"347","author":"Salvarani","year":"2002","journal-title":"N\u00a0Engl J Med"},{"key":"10.1016\/j.ncl.2019.01.004_bib23","doi-asserted-by":"crossref","first-page":"19","DOI":"10.1097\/BOR.0b013e32831cec7b","article-title":"Imaging for large-vessel vasculitis","volume":"21","author":"Blockman","year":"2009","journal-title":"Curr Opin Rheumatol"},{"key":"10.1016\/j.ncl.2019.01.004_bib24","doi-asserted-by":"crossref","first-page":"490","DOI":"10.1212\/WNL.10.5.490","article-title":"Neurologic aspects of temporal arteritis","volume":"10","author":"Hollenhorst","year":"1960","journal-title":"Neurology"},{"key":"10.1016\/j.ncl.2019.01.004_bib25","doi-asserted-by":"crossref","first-page":"352","DOI":"10.1212\/WNL.38.3.352","article-title":"Neurologic disease in biopsy-proven giant cell (temporal) arteritis","volume":"38","author":"Caselli","year":"1988","journal-title":"Neurology"},{"key":"10.1016\/j.ncl.2019.01.004_bib26","doi-asserted-by":"crossref","first-page":"1497","DOI":"10.1002\/1529-0131(199808)41:8<1497::AID-ART22>3.0.CO;2-Z","article-title":"Permanent visual loss and cerebrovascular attacks in giant cell arteritis. Predictors and response to treatment","volume":"41","author":"Gonzalez-Gay","year":"1998","journal-title":"Arthritis Rheum"},{"issue":"Suppl 64","key":"10.1016\/j.ncl.2019.01.004_bib27","first-page":"S40","article-title":"A\u00a0population-based study of Takayasu\u2019s arteritis in eastern Denmark","volume":"29","author":"Dreyer","year":"2011","journal-title":"Clin Exp Rheumatol"},{"key":"10.1016\/j.ncl.2019.01.004_bib28","doi-asserted-by":"crossref","first-page":"1806","DOI":"10.1093\/rheumatology\/keq167","article-title":"Takayasu arteritis in children and adolescents","volume":"49","author":"Brunner","year":"2010","journal-title":"Rheumatology (Oxford)"},{"issue":"Suppl 1","key":"10.1016\/j.ncl.2019.01.004_bib29","doi-asserted-by":"crossref","first-page":"S153","DOI":"10.1016\/S0167-5273(00)00180-7","article-title":"Takayasu arteritis in children and young Indians","volume":"75","author":"Jain","year":"2000","journal-title":"Int J Cardiol"},{"key":"10.1016\/j.ncl.2019.01.004_bib30","doi-asserted-by":"crossref","first-page":"919","DOI":"10.7326\/0003-4819-120-11-199406010-00004","article-title":"Takayasu arteritis","volume":"120","author":"Kerr","year":"1994","journal-title":"Ann Intern Med"},{"key":"10.1016\/j.ncl.2019.01.004_bib31","doi-asserted-by":"crossref","first-page":"873","DOI":"10.1212\/WNL.13.10.873","article-title":"Idiopathic arteritis of Takayasu","volume":"13","author":"Riehl","year":"1963","journal-title":"Neurology"},{"key":"10.1016\/j.ncl.2019.01.004_bib32","first-page":"92","article-title":"Takayasu\u2019s arteritis","volume":"12","author":"Riehl","year":"1965","journal-title":"Arch Neurol"},{"key":"10.1016\/j.ncl.2019.01.004_bib33","doi-asserted-by":"crossref","first-page":"1329","DOI":"10.1136\/annrheumdis-2011-200795","article-title":"Distribution of arterial lesions in Takayasu\u2019s arteritis and giant cell arteritis","volume":"71","author":"Grayson","year":"2012","journal-title":"Ann Rheum Dis"},{"key":"10.1016\/j.ncl.2019.01.004_bib34","doi-asserted-by":"crossref","first-page":"27","DOI":"10.1161\/01.CIR.57.1.27","article-title":"Natural history and classification of occlusive thromboaortopathy (Takayasu\u2019s disease)","volume":"57","author":"Ishikawa","year":"1978","journal-title":"Circulation"},{"key":"10.1016\/j.ncl.2019.01.004_bib35","doi-asserted-by":"crossref","first-page":"1004","DOI":"10.1253\/circj.CJ-11-1108","article-title":"Improved prognosis of Takayasu arteritis over the past decade","volume":"76","author":"Ohigashi","year":"2012","journal-title":"Circ J"},{"key":"10.1016\/j.ncl.2019.01.004_bib36","doi-asserted-by":"crossref","first-page":"170","DOI":"10.1136\/ard.60.2.170","article-title":"Geoepidemiology of systemic vasculitis: comparison of the incidence in two regions of Europe","volume":"60","author":"Watts","year":"2001","journal-title":"Ann Rheum Dis"},{"key":"10.1016\/j.ncl.2019.01.004_bib37","doi-asserted-by":"crossref","first-page":"1088","DOI":"10.1002\/art.1780330805","article-title":"The American College of Rheumatology 1990 criteria for the classification of polyarteritis nodosa","volume":"33","author":"Lightfoot","year":"1990","journal-title":"Arthritis Rheum"},{"key":"10.1016\/j.ncl.2019.01.004_bib38","first-page":"167","article-title":"Epidemiologic features of Kawasaki disease in Japan: results from the nationwide survey in 2005-2006","volume":"18","author":"Nakamura","year":"2008","journal-title":"J\u00a0Epidemiol"},{"key":"10.1016\/j.ncl.2019.01.004_bib39","doi-asserted-by":"crossref","first-page":"285","DOI":"10.1007\/s00431-004-1431-z","article-title":"Advances in Kawasaki disease","volume":"163","author":"Shulman","year":"2004","journal-title":"Eur J Pediatr"},{"key":"10.1016\/j.ncl.2019.01.004_bib40","doi-asserted-by":"crossref","first-page":"655","DOI":"10.1001\/archneurpsyc.1938.02270040011001","article-title":"Periarteritis nodosa: a clinicopathologic study with special reference to the nervous system","volume":"39","author":"Kernohan","year":"1938","journal-title":"Arch Neurol"},{"key":"10.1016\/j.ncl.2019.01.004_bib41","doi-asserted-by":"crossref","first-page":"865","DOI":"10.1016\/S0733-8619(05)70352-2","article-title":"Polyarteritis nodosa, microscopic polyangiitis and Churg-Strauss syndrome: clinical aspects, neurologic manifestations, and treatment","volume":"15","author":"Guillevin","year":"1997","journal-title":"Neurol Clin"},{"key":"10.1016\/j.ncl.2019.01.004_bib42","doi-asserted-by":"crossref","first-page":"616","DOI":"10.1002\/art.27240","article-title":"Clinical features and outcomes in 348 patients with polyarteritis nodosa","volume":"62","author":"Pagnoux","year":"2010","journal-title":"Arthritis Rheum"},{"key":"10.1016\/j.ncl.2019.01.004_bib43","doi-asserted-by":"crossref","first-page":"798","DOI":"10.1136\/ard.2009.116657","article-title":"EULAR\/PRINTO\/PReS criteria for Henoch-Sch\u00f6nlein purpura, childhood polyarteritis nodosa, childhood Wegener granulomatosis and childhood Takayasu arteritis. Ankara 2008. Part II: Final Classification","volume":"69","author":"Ozen","year":"2010","journal-title":"Ann Rheum Dis"},{"key":"10.1016\/j.ncl.2019.01.004_bib44","doi-asserted-by":"crossref","first-page":"177","DOI":"10.1111\/j.1651-2227.2000.tb01212.x","article-title":"Clinical, laboratory and molecular characteristics of children with familial Mediterranean fever-associated vasculitis","volume":"89","author":"Tekin","year":"2000","journal-title":"Acta Paediatr"},{"key":"10.1016\/j.ncl.2019.01.004_bib45","doi-asserted-by":"crossref","first-page":"817","DOI":"10.1111\/j.1365-4632.2007.02975.x","article-title":"Panarteritis cutanea benigna-an entity limited to the skin or cutaneous presentation of a systemic necrotizing vasculitis? Report of seven cases and review of the literature","volume":"46","author":"Rogalski","year":"2007","journal-title":"Int J Dermatol"},{"key":"10.1016\/j.ncl.2019.01.004_bib46","doi-asserted-by":"crossref","first-page":"517","DOI":"10.1016\/j.jpeds.2004.06.046","article-title":"Juvenile polyarteritis: results of a multicenter survey of 110 children","volume":"145","author":"Ozen","year":"2004","journal-title":"J\u00a0Pediatr"},{"key":"10.1016\/j.ncl.2019.01.004_bib47","doi-asserted-by":"crossref","first-page":"685","DOI":"10.1136\/adc.69.6.685","article-title":"Polyarteritis nodosa associated with streptococcus","volume":"69","author":"David","year":"1993","journal-title":"Arch Dis Child"},{"key":"10.1016\/j.ncl.2019.01.004_bib48","doi-asserted-by":"crossref","first-page":"1160","DOI":"10.1111\/dmcn.12002","article-title":"Cerebral vasculitis in severe Kawasaki disease: early detection by magnetic resonance imaging and good outcome after intensive treatment","volume":"54","author":"Gitiaux","year":"2012","journal-title":"Dev Med Child Neurol"},{"key":"10.1016\/j.ncl.2019.01.004_bib49","doi-asserted-by":"crossref","first-page":"483","DOI":"10.1002\/jcu.1870150711","article-title":"Kawasaki syndrome: cerebral and cardiovascular complications","volume":"15","author":"Templeton","year":"1987","journal-title":"J\u00a0Clin Ultrasound"},{"key":"10.1016\/j.ncl.2019.01.004_bib50","doi-asserted-by":"crossref","first-page":"814","DOI":"10.1111\/j.1469-8749.1984.tb08176.x","article-title":"Acute hemiplegia in Kawasaki disease and infantile polyarteritis nodosa","volume":"26","author":"Laxer","year":"1984","journal-title":"Dev Med Child Neurol"},{"key":"10.1016\/j.ncl.2019.01.004_bib51","doi-asserted-by":"crossref","first-page":"30","DOI":"10.1016\/j.braindev.2005.04.003","article-title":"Magnetic resonance studies of brain lesions in patients with Kawasaki disease","volume":"28","author":"Muneuchi","year":"2006","journal-title":"Brain Dev"},{"key":"10.1016\/j.ncl.2019.01.004_bib52","doi-asserted-by":"crossref","first-page":"383","DOI":"10.1007\/s11926-013-0383-6","article-title":"Classification of ANCA-associated vasculitis","volume":"15","author":"Khan","year":"2013","journal-title":"Curr Rheumatol Rep"},{"key":"10.1016\/j.ncl.2019.01.004_bib53","doi-asserted-by":"crossref","first-page":"1101","DOI":"10.1002\/art.1780330807","article-title":"The American College of Rheumatology 1990 criteria for the classification of Wegener\u2019s granulomatosis","volume":"33","author":"Leavitt","year":"1990","journal-title":"Arthritis Rheum"},{"key":"10.1016\/j.ncl.2019.01.004_bib54","doi-asserted-by":"crossref","first-page":"1094","DOI":"10.1002\/art.1780330806","article-title":"The American College of Rheumatology 1990 criteria for the classification of Churg-Strauss syndrome (allergic granulomatosis and angiitis)","volume":"33","author":"Masi","year":"1990","journal-title":"Arthritis Rheum"},{"key":"10.1016\/j.ncl.2019.01.004_bib55","doi-asserted-by":"crossref","first-page":"222","DOI":"10.1136\/ard.2006.054593","article-title":"Development and validation of a consensus methodology for the classification of the ANCA-associated vasculitides and polyarteritis nodosa for epidemiological studies","volume":"66","author":"Watts","year":"2007","journal-title":"Ann Rheum Dis"},{"key":"10.1016\/j.ncl.2019.01.004_bib56","doi-asserted-by":"crossref","first-page":"92","DOI":"10.1002\/art.20077","article-title":"Prevalences of polyarteritis nodosa, microscopic polyangiitis, Wegener\u2019s granulomatosis, and Churg-Strauss syndrome in a French urban multiethnic population in 2000: a capture \u2013recapture estimate","volume":"51","author":"Mahr","year":"2004","journal-title":"Arthritis Rheum"},{"key":"10.1016\/j.ncl.2019.01.004_bib57","doi-asserted-by":"crossref","first-page":"1560","DOI":"10.1093\/rheumatology\/kep304","article-title":"Incidence and survival rates in Wegener\u2019s granulomatosis, microscopic polyangiitis, Churg-Strauss syndrome and polyarteritis nodosa","volume":"48","author":"Mohammad","year":"2009","journal-title":"Rheumatology"},{"key":"10.1016\/j.ncl.2019.01.004_bib58","doi-asserted-by":"crossref","first-page":"45","DOI":"10.1001\/archneur.1963.00460020045003","article-title":"Neurological complications of Wegener\u2019s granulomatosis","volume":"8","author":"Drachman","year":"1963","journal-title":"Arch Neurol"},{"key":"10.1016\/j.ncl.2019.01.004_bib59","doi-asserted-by":"crossref","first-page":"4","DOI":"10.1002\/ana.410330103","article-title":"Neurological involvement in Wegener\u2019s granulomatosis: an analysis of 324 consecutive patients at the Mayo Clinic","volume":"33","author":"Nishino","year":"1993","journal-title":"Ann Neurol"},{"key":"10.1016\/j.ncl.2019.01.004_bib60","doi-asserted-by":"crossref","first-page":"76","DOI":"10.7326\/0003-4819-98-1-76","article-title":"Wegener\u2019s granulomatosis: Prospective clinical and therapeutic experience with 85 patients over 21 years","volume":"98","author":"Fauci","year":"1983","journal-title":"Ann Intern Med"},{"key":"10.1016\/j.ncl.2019.01.004_bib61","doi-asserted-by":"crossref","first-page":"155","DOI":"10.1002\/ana.410140202","article-title":"Neurological complications of vasculitis","volume":"14","author":"Moore","year":"1983","journal-title":"Ann Neurol"},{"key":"10.1016\/j.ncl.2019.01.004_bib62","doi-asserted-by":"crossref","first-page":"488","DOI":"10.7326\/0003-4819-116-6-488","article-title":"Wegener granulomatosis: an analysis of 158 patients","volume":"116","author":"Hoffman","year":"1992","journal-title":"Ann Intern Med"},{"key":"10.1016\/j.ncl.2019.01.004_bib63","doi-asserted-by":"crossref","first-page":"1215","DOI":"10.1001\/archneur.58.8.1215","article-title":"Standardized neurologic evaluations of 128 patients with Wegener\u2019s granulomatosis","volume":"58","author":"de Groot","year":"2001","journal-title":"Arch Neurol"},{"key":"10.1016\/j.ncl.2019.01.004_bib64","doi-asserted-by":"crossref","first-page":"1517","DOI":"10.1007\/s00381-016-3080-8","article-title":"Pediatric granulomatosis with polyangiitis exhibiting prominent central nervous system symptoms","volume":"32","author":"Lu","year":"2016","journal-title":"Childs Nerv Syst"},{"key":"10.1016\/j.ncl.2019.01.004_bib65","first-page":"175","article-title":"The kidney in periarteritis nodosa","volume":"17","author":"Davson","year":"1948","journal-title":"QJM"},{"key":"10.1016\/j.ncl.2019.01.004_bib66","doi-asserted-by":"crossref","first-page":"189","DOI":"10.1002\/path.1700620206","article-title":"The renal appearance in the microscopic form of periarteritis nodosa","volume":"62","author":"Wainwright","year":"1950","journal-title":"J\u00a0Pathol Bacteriol"},{"key":"10.1016\/j.ncl.2019.01.004_bib67","first-page":"467","article-title":"Microscopic polyarteritis: presentation, pathology and prognosis","volume":"220","author":"Savage","year":"1985","journal-title":"QJM"},{"key":"10.1016\/j.ncl.2019.01.004_bib68","first-page":"181","article-title":"Vasculitis affecting the kidney: presentation, histopathology and long-term outcome","volume":"201","author":"Serra","year":"1984","journal-title":"QJM"},{"key":"10.1016\/j.ncl.2019.01.004_bib69","doi-asserted-by":"crossref","first-page":"421","DOI":"10.1002\/1529-0131(199904)42:3<421::AID-ANR5>3.0.CO;2-6","article-title":"Microscopic polyangiitis","volume":"42","author":"Guillevin","year":"1999","journal-title":"Arthritis Rheum"},{"key":"10.1016\/j.ncl.2019.01.004_bib70","doi-asserted-by":"crossref","first-page":"666","DOI":"10.1002\/1529-0131(200103)44:3<666::AID-ANR116>3.0.CO;2-A","article-title":"Long-term followup of polyarteritis nodosa, microscopic polyangiitis, and Churg-Strauss syndrome","volume":"44","author":"Gayraud","year":"2001","journal-title":"Arthritis Rheum"},{"key":"10.1016\/j.ncl.2019.01.004_bib71","doi-asserted-by":"crossref","first-page":"812","DOI":"10.1016\/j.autrev.2010.07.009","article-title":"Microscopic polyangiitis: clinical presentation","volume":"9","author":"Villiger","year":"2010","journal-title":"Autoimmun Rev"},{"key":"10.1016\/j.ncl.2019.01.004_bib72","doi-asserted-by":"crossref","first-page":"727","DOI":"10.1007\/s10072-011-0653-x","article-title":"Microscopic polyangiitis presenting with peripheral and central neurological manifestations","volume":"32","author":"Ben Sassi","year":"2011","journal-title":"Neurol Sci"},{"key":"10.1016\/j.ncl.2019.01.004_bib73","first-page":"1089","article-title":"A\u00a0case of MPO-ANCA related vasculitis with transient leukoencephalopathy and multiple cerebral haemorrhages","volume":"36","author":"Honda","year":"1996","journal-title":"Rinsho Shinkeigaku"},{"key":"10.1016\/j.ncl.2019.01.004_bib74","doi-asserted-by":"crossref","first-page":"1057","DOI":"10.1007\/s00296-006-0136-1","article-title":"Microscopic polyangiitis complicated by cerebral haemorrhage","volume":"26","author":"Han","year":"2006","journal-title":"Rheumatol Int"},{"key":"10.1016\/j.ncl.2019.01.004_bib75","doi-asserted-by":"crossref","first-page":"99","DOI":"10.1016\/j.jns.2005.07.003","article-title":"ANCA-associated vasculitis (AAV) causing bilateral cerebral infarction and subsequent intracerebral haemorrhage without renal and respiratory dysfunction","volume":"240","author":"Ito","year":"2006","journal-title":"J\u00a0Neurol Sci"},{"key":"10.1016\/j.ncl.2019.01.004_bib76","doi-asserted-by":"crossref","first-page":"2979","DOI":"10.1007\/s00296-011-2079-4","article-title":"Clinical features and outcome of microscopic polyangiitis under a new consensus algorithm of ANCA-associated vasculitides in Korea","volume":"32","author":"Ahn","year":"2012","journal-title":"Rheumatol Int"},{"key":"10.1016\/j.ncl.2019.01.004_bib77","doi-asserted-by":"crossref","first-page":"3413","DOI":"10.1002\/art.24876","article-title":"Classification, presentation, and initial treatment of Wegener\u2019s granulomatosis in childhood","volume":"60","author":"Cabral","year":"2009","journal-title":"Arthritis Rheum"},{"key":"10.1016\/j.ncl.2019.01.004_bib78","doi-asserted-by":"crossref","first-page":"17","DOI":"10.1097\/00005792-199601000-00003","article-title":"Prognostic factors in polyarteritis nodosa and Churg-Strauss syndrome: a prospective study of 342 patients","volume":"75","author":"Guillevin","year":"1996","journal-title":"Medicine"},{"key":"10.1016\/j.ncl.2019.01.004_bib79","first-page":"671","article-title":"Birmingham Vasculitis Activity Score (BVAS) in systemic necrotizing vasculitis","volume":"87","author":"Luqmani","year":"1994","journal-title":"QJM"},{"key":"10.1016\/j.ncl.2019.01.004_bib80","first-page":"277","article-title":"Allergic granulomatosis, allergic angiitis, and periarteritis nodosa","volume":"27","author":"Churg","year":"1951","journal-title":"Am J Pathol"},{"key":"10.1016\/j.ncl.2019.01.004_bib81","first-page":"477","article-title":"Allergic granulomatosis and angiitis (Churg-Strauss syndrome). Report and analysis of 30 cases","volume":"52","author":"Chumbley","year":"1977","journal-title":"Mayo Clin Proc"},{"key":"10.1016\/j.ncl.2019.01.004_bib82","doi-asserted-by":"crossref","first-page":"65","DOI":"10.1097\/00005792-198403000-00001","article-title":"Systemic vasculitis with asthma and eosinophilia: a clinical approach to the Churg-Strauss syndrome","volume":"63","author":"Lanham","year":"1984","journal-title":"Medicine"},{"key":"10.1016\/j.ncl.2019.01.004_bib83","doi-asserted-by":"crossref","first-page":"337","DOI":"10.4065\/70.4.337","article-title":"Neurologic manifestations of Churg-Strauss syndrome","volume":"70","author":"Sehgal","year":"1995","journal-title":"Mayo Clin Proc"},{"key":"10.1016\/j.ncl.2019.01.004_bib84","doi-asserted-by":"crossref","first-page":"26","DOI":"10.1097\/00005792-199901000-00003","article-title":"Churg-Strauss syndrome","volume":"78","author":"Guillevin","year":"1999","journal-title":"Medicine"},{"key":"10.1016\/j.ncl.2019.01.004_bib85","doi-asserted-by":"crossref","first-page":"27","DOI":"10.1097\/00005792-200201000-00002","article-title":"Polyarteritis nodosa and Churg-Strauss angiitis. Characteristics and outcome in 38 patients over 65 years","volume":"81","author":"Mouthon","year":"2002","journal-title":"Medicine"},{"key":"10.1016\/j.ncl.2019.01.004_bib86","doi-asserted-by":"crossref","first-page":"270","DOI":"10.1002\/art.37721","article-title":"Eosinophilic granulomatosis with polyangiitis (Churg-Strauss)","volume":"65","author":"Comarmond","year":"2013","journal-title":"Arthritis Rheum"},{"key":"10.1016\/j.ncl.2019.01.004_bib87","doi-asserted-by":"crossref","first-page":"416","DOI":"10.1097\/00000441-194710000-00010","article-title":"Studies of cryoglobulins. II. The spontaneous precipitation of protein from serum at 5\u00b0C in various disease states","volume":"214","author":"Lerner","year":"1947","journal-title":"Am J Med Sci"},{"key":"10.1016\/j.ncl.2019.01.004_bib88","doi-asserted-by":"crossref","first-page":"279","DOI":"10.1136\/bmj.2.4882.279","article-title":"Cryoglobulinemia with cerebral purpura","volume":"2","author":"Marshall","year":"1954","journal-title":"BMJ"},{"key":"10.1016\/j.ncl.2019.01.004_bib89","doi-asserted-by":"crossref","first-page":"245","DOI":"10.1212\/WNL.24.3.245","article-title":"Neurologic manifestations in patients with mixed cryoglobulinemia","volume":"24","author":"Abramsky","year":"1974","journal-title":"Neurology"},{"key":"10.1016\/j.ncl.2019.01.004_bib90","doi-asserted-by":"crossref","first-page":"287","DOI":"10.1016\/0002-9343(80)90390-3","article-title":"Mixed cryoglobulinemia: clinical aspects and long-term follow-up of 40 patients","volume":"69","author":"Gorevic","year":"1980","journal-title":"Am J Med"},{"key":"10.1016\/j.ncl.2019.01.004_bib91","doi-asserted-by":"crossref","first-page":"671","DOI":"10.1016\/S0025-6196(11)63005-X","article-title":"Cerebral ischemia in patients with hepatitis C virus infection and mixed cryogloblinemia","volume":"71","author":"Petty","year":"1996","journal-title":"Mayo Clin Proc"},{"key":"10.1016\/j.ncl.2019.01.004_bib92","doi-asserted-by":"crossref","first-page":"1579","DOI":"10.1212\/WNL.55.10.1579","article-title":"Relapsing ischemic encephalopathy and cryoglobulinemia","volume":"55","author":"Ince","year":"2000","journal-title":"Neurology"},{"key":"10.1016\/j.ncl.2019.01.004_bib93","doi-asserted-by":"crossref","first-page":"29","DOI":"10.1097\/00002281-200201000-00006","article-title":"Cryoglobulinemia vasculitis","volume":"14","author":"Cacoub","year":"2002","journal-title":"Curr Opin Rheumatol"},{"key":"10.1016\/j.ncl.2019.01.004_bib94","first-page":"631","article-title":"Atteinte neurologique central et infection par le virus de l\u2019h\u00e8patite","volume":"22","author":"Cacoub","year":"1998","journal-title":"Gastroenterol Clin Biol"},{"key":"10.1016\/j.ncl.2019.01.004_bib95","doi-asserted-by":"crossref","first-page":"355","DOI":"10.1016\/j.semarthrit.2003.10.001","article-title":"Mixed cryoglobulinemia: demographic, clinical, and serologic features and survival in 231 patients","volume":"33","author":"Ferri","year":"2004","journal-title":"Semin Arthritis Rheum"},{"key":"10.1016\/j.ncl.2019.01.004_bib96","first-page":"150","article-title":"Central nervous system manifestations of HCV-related MC: review of the literature","volume":"54","author":"Filipini","year":"2002","journal-title":"Reumatismo"},{"key":"10.1016\/j.ncl.2019.01.004_bib97","first-page":"444","article-title":"Essential mixed cryoglobulinemia as the cause of ischemic cerebrovascular accident","volume":"30","author":"Fragoso","year":"2000","journal-title":"Rev Neurol"},{"key":"10.1016\/j.ncl.2019.01.004_bib98","first-page":"484","article-title":"Central nervous system involvement in hepatitis C virus cryoglobulinemia vasculitis: a multicentre case-control study using magnetic resonance imaging and neuropsychological tests","volume":"32","author":"Casato","year":"2005","journal-title":"J\u00a0Rheumatol"},{"key":"10.1016\/j.ncl.2019.01.004_bib99","doi-asserted-by":"crossref","first-page":"5996","DOI":"10.1182\/blood-2011-12-396028","article-title":"Management of non-infectious mixed cryoglobulinemia vasculitis: data from 242 cases included in the CryoVas survey","volume":"119","author":"Terrier","year":"2012","journal-title":"Blood"},{"key":"10.1016\/j.ncl.2019.01.004_bib100","doi-asserted-by":"crossref","first-page":"10","DOI":"10.1097\/BOR.0b013e32835b15f7","article-title":"Cryoglobulinemia vasculitis: an update","volume":"25","author":"Terrier","year":"2013","journal-title":"Curr Opin Rheumatol"},{"key":"10.1016\/j.ncl.2019.01.004_bib101","doi-asserted-by":"crossref","first-page":"59","DOI":"10.1016\/j.jmii.2011.12.027","article-title":"Comparison of cryoglobulinemia in children and adults","volume":"46","author":"Liou","year":"2013","journal-title":"J\u00a0Microbiol Immunol Infect"},{"issue":"2","key":"10.1016\/j.ncl.2019.01.004_bib102","doi-asserted-by":"crossref","first-page":"1","DOI":"10.1111\/dth.12430","article-title":"Pediatric cryoglobulinemic vasculitis successfully managed with rituximab","volume":"30","author":"Gim\u00e9nez-Roca","year":"2017","journal-title":"Dermatol Ther"},{"key":"10.1016\/j.ncl.2019.01.004_bib103","doi-asserted-by":"crossref","first-page":"410","DOI":"10.1007\/s11926-009-0060-y","article-title":"Hypocomplementemic urticarial vasculitis syndrome","volume":"11","author":"Jara","year":"2009","journal-title":"Curr Rheumatol Rev"},{"key":"10.1016\/j.ncl.2019.01.004_bib104","doi-asserted-by":"crossref","first-page":"24","DOI":"10.1097\/00005792-199501000-00003","article-title":"Hypocomplementemic urticarial vasculitis syndrome","volume":"74","author":"Wisnieski","year":"1995","journal-title":"Medicine"},{"key":"10.1016\/j.ncl.2019.01.004_bib105","first-page":"340","article-title":"Hypocomplementemia with cutaneous vasculitis and arthritis","volume":"48","author":"McDuffie","year":"1973","journal-title":"Mayo Clin Proc"},{"key":"10.1016\/j.ncl.2019.01.004_bib106","first-page":"36","article-title":"Hypocomplementemic urticarial vasculitis syndrome. A case report and literature review","volume":"5","author":"Buck","year":"2012","journal-title":"J\u00a0Clin Aesthet Dermatol"},{"key":"10.1016\/j.ncl.2019.01.004_bib107","first-page":"756","article-title":"Hypocomplementemic urticarial vasculitis syndrome","volume":"106","author":"Grotz","year":"2009","journal-title":"Dtsch Arztebl Int"},{"key":"10.1016\/j.ncl.2019.01.004_bib108","doi-asserted-by":"crossref","first-page":"183","DOI":"10.1016\/j.iac.2004.01.007","article-title":"Urticarial vasculitis and hypocomplementemic urticarial vasculitis syndrome","volume":"24","author":"Davies","year":"2004","journal-title":"Immunol Allergy Clin N Am"},{"key":"10.1016\/j.ncl.2019.01.004_bib109","doi-asserted-by":"crossref","first-page":"1024","DOI":"10.1002\/art.1780220912","article-title":"Hypocomplementemic urticarial vasculitis with glomerulonephritis and pseudotumor cerebri","volume":"22","author":"Ludivico","year":"1979","journal-title":"Arthritis Rheum"},{"key":"10.1016\/j.ncl.2019.01.004_bib110","doi-asserted-by":"crossref","first-page":"1409","DOI":"10.1093\/rheumatology\/keu023","article-title":"Renal involvement in hypocomplementemic urticarial vasculitis syndrome: a report of three paediatric cases","volume":"53","author":"Pasini","year":"2014","journal-title":"Rheumatology (Oxford)"},{"key":"10.1016\/j.ncl.2019.01.004_bib111","doi-asserted-by":"crossref","first-page":"57","DOI":"10.1080\/1744666X.2016.1205486","article-title":"Behcet's disease: epidemiology, clinical manifestations, and diagnosis","volume":"13","author":"Davatchi","year":"2017","journal-title":"Expert Rev Clin Immunol"},{"issue":"Suppl 60","key":"10.1016\/j.ncl.2019.01.004_bib112","first-page":"S2","article-title":"On relapsing, aphthous ulcers of the mouth, eye and genitalia caused by a virus. 1937","volume":"28","author":"Behcet","year":"2010","journal-title":"Clin Exp Rheumatol"},{"key":"10.1016\/j.ncl.2019.01.004_bib113","first-page":"1078","article-title":"Criteria for diagnosis of Beh\u00e7et's disease. International Study Group for Beh\u00e7et\u2019s Disease","volume":"335","year":"1990","journal-title":"Lancet"},{"key":"10.1016\/j.ncl.2019.01.004_bib114","doi-asserted-by":"crossref","first-page":"350","DOI":"10.1159\/000251993","article-title":"Cutaneous hyper-reactivity in Beh\u00e7et disease","volume":"146","author":"Sobel","year":"1973","journal-title":"Dermatologica"},{"key":"10.1016\/j.ncl.2019.01.004_bib115","doi-asserted-by":"crossref","first-page":"585","DOI":"10.1097\/BOR.0b013e32833cc9b7","article-title":"Pediatric onset Behcet disease","volume":"22","author":"\u00d6zen","year":"2010","journal-title":"Curr Opin Rheumatol"},{"key":"10.1016\/j.ncl.2019.01.004_bib116","doi-asserted-by":"crossref","first-page":"3951","DOI":"10.1002\/art.24149","article-title":"Population-based prevalence study of Beh\u00e7et disease. Differences by ethnic origin and low variation by age at immigration","volume":"58","author":"Mahr","year":"2008","journal-title":"Arthritis Rheum"},{"key":"10.1016\/j.ncl.2019.01.004_bib117","doi-asserted-by":"crossref","first-page":"600","DOI":"10.1002\/art.24423","article-title":"Epidemiology and clinical characteristics of Behcet\u2019s disease in the US: a population-based study","volume":"61","author":"Calamia","year":"2009","journal-title":"Arthritis Rheum"},{"key":"10.1016\/j.ncl.2019.01.004_bib118","doi-asserted-by":"crossref","first-page":"1900","DOI":"10.1212\/WNL.0b013e318238edeb","article-title":"Clinical characteristics of pediatric-onset neuro-Beh\u00e7et disease","volume":"77","author":"Uluduz","year":"2011","journal-title":"Neurology"},{"key":"10.1016\/j.ncl.2019.01.004_bib119","doi-asserted-by":"crossref","first-page":"424","DOI":"10.1111\/j.1526-4610.2007.01041.x","article-title":"The prevalence and characteristics of different types of headache in patients with Behcet\u2019s disease, a case-control study","volume":"48","author":"Haghighi","year":"2008","journal-title":"Headache"},{"key":"10.1016\/j.ncl.2019.01.004_bib120","doi-asserted-by":"crossref","first-page":"353","DOI":"10.1016\/S0140-6736(57)92590-4","article-title":"Encephalomyelopathy in Behcet\u2019s disease. Report of necropsy findings in two cases","volume":"2","author":"McMenemey","year":"1957","journal-title":"Lancet"},{"key":"10.1016\/j.ncl.2019.01.004_bib121","doi-asserted-by":"crossref","first-page":"151","DOI":"10.1093\/brain\/86.1.151","article-title":"Meningo-encephalitis of Beh\u00e7et\u2019s disease. Case report with pathological findings","volume":"86","author":"Rubinstein","year":"1963","journal-title":"Brain"},{"key":"10.1016\/j.ncl.2019.01.004_bib122","doi-asserted-by":"crossref","first-page":"417","DOI":"10.1016\/0022-510X(67)90083-4","article-title":"Neurological aspects of Beh\u00e7et\u2019s disease. A case report and clinico-pathological review of the literature in Japan","volume":"5","author":"Kawakita","year":"1967","journal-title":"J\u00a0Neurol Sci"},{"key":"10.1016\/j.ncl.2019.01.004_bib123","doi-asserted-by":"crossref","first-page":"579","DOI":"10.1111\/j.1440-1789.2006.00734.x","article-title":"Autopsy case of neuro-Behcet\u2019s disease with multifocal neutrophilic perivascular inflammation","volume":"26","author":"Arai","year":"2006","journal-title":"Neuropathology"},{"issue":"Suppl 67","key":"10.1016\/j.ncl.2019.01.004_bib124","first-page":"S32","article-title":"Is headache in Behcet\u2019s disease related to silent neurologic involvement?","volume":"29","author":"Koseoglu","year":"2011","journal-title":"Clin Exp Rheumatol"},{"key":"10.1016\/j.ncl.2019.01.004_bib125","doi-asserted-by":"crossref","first-page":"99","DOI":"10.1016\/j.jns.2004.02.021","article-title":"Cognitive impairment in Behcet\u2019s disease without overt neurological involvement","volume":"220","author":"Monastero","year":"2004","journal-title":"J\u00a0Neurol Sci"},{"key":"10.1016\/j.ncl.2019.01.004_bib126","first-page":"513","article-title":"The spectrum of nervous system involvement in Behcet\u2019s syndrome and its differential diagnosis","volume":"256","author":"Siva","year":"2009","journal-title":"J\u00a0Neurol"},{"key":"10.1016\/j.ncl.2019.01.004_bib127","doi-asserted-by":"crossref","first-page":"315","DOI":"10.1001\/archneur.1965.00460270091012","article-title":"Involvement of nervous system in Beh\u00e7et\u2019s syndrome","volume":"12","author":"Wolf","year":"1965","journal-title":"Arch Neurol"},{"key":"10.1016\/j.ncl.2019.01.004_bib128","first-page":"55","article-title":"Neuro-Beh\u00e7et\u2019s disease","volume":"16","author":"Hadfield","year":"1997","journal-title":"Clin Neuropathol"},{"key":"10.1016\/j.ncl.2019.01.004_bib129","doi-asserted-by":"crossref","first-page":"45","DOI":"10.1016\/0046-8177(91)90060-3","article-title":"Vasculo-Behcet\u2019s disease: a pathologic study of eight cases","volume":"22","author":"Matsumoto","year":"1991","journal-title":"Hum Pathol"},{"key":"10.1016\/j.ncl.2019.01.004_bib130","first-page":"1134","article-title":"Cerebral venous thrombosis in Behcet\u2019s disease compared to those associated with other etiologies","volume":"256","author":"Yesilot","year":"2009","journal-title":"J\u00a0Neurol"},{"key":"10.1016\/j.ncl.2019.01.004_bib131","doi-asserted-by":"crossref","first-page":"278","DOI":"10.1212\/WNL.28.3.278","article-title":"Neurologic manifestations of Cogan syndrome","volume":"28","author":"Bicknell","year":"1978","journal-title":"Neurology"},{"key":"10.1016\/j.ncl.2019.01.004_bib132","doi-asserted-by":"crossref","first-page":"483","DOI":"10.4065\/81.4.483","article-title":"Cogan syndrome: a retrospective review of 60 patients throughout a half century","volume":"81","author":"Gluth","year":"2006","journal-title":"Mayo Clin Proc"},{"key":"10.1016\/j.ncl.2019.01.004_bib133","first-page":"835","article-title":"Cogan\u2019s syndrome associated with polyarteritis nodosa. A report of three cases","volume":"60","author":"Crawford","year":"1957","journal-title":"Pa Med J"},{"key":"10.1016\/j.ncl.2019.01.004_bib134","doi-asserted-by":"crossref","first-page":"1074","DOI":"10.1056\/NEJM195805292582202","article-title":"Nonsyphilitic interstitial keratitis and bilateral deafness (Cogan\u2019s syndrome) associated with cardiovascular disease","volume":"258","author":"Eisenstein","year":"1958","journal-title":"N\u00a0Engl J Med"},{"key":"10.1016\/j.ncl.2019.01.004_bib135","doi-asserted-by":"crossref","first-page":"172","DOI":"10.1001\/archopht.1964.00970010188005","article-title":"Nonsyphilitic interstitial keratitis with vestibuloauditory symptoms. A case with fatal aortitis","volume":"71","author":"Cogan","year":"1964","journal-title":"Arch Ophthalmol"},{"key":"10.1016\/j.ncl.2019.01.004_bib136","first-page":"572","article-title":"Cogan\u2019s syndrome and systemic vascular disease. Analysis of pathological features with reference to its relationship to thromboangiitis obliterans (Buerger)","volume":"72","author":"Fisher","year":"1961","journal-title":"Arch Pathol"},{"key":"10.1016\/j.ncl.2019.01.004_bib137","doi-asserted-by":"crossref","first-page":"1001","DOI":"10.1056\/NEJM195306112482402","article-title":"Nonsyphilitic interstitial keratitis and bilateral deafness (Cogan\u2019s syndrome) associated with essential polyangiitis (periarteritis nodosa). A review of the syndrome with consideration of a possible pathogenic mechanism","volume":"248","author":"Oliner","year":"1953","journal-title":"N\u00a0Engl J Med"},{"key":"10.1016\/j.ncl.2019.01.004_bib138","first-page":"647","article-title":"Cogan\u2019s syndrome with cardiovascular involvement: aortic insufficiency","volume":"48","author":"Gelfand","year":"1972","journal-title":"Bull NY Acad Med"},{"key":"10.1016\/j.ncl.2019.01.004_bib139","doi-asserted-by":"crossref","first-page":"549","DOI":"10.1016\/0002-9343(76)90722-1","article-title":"Cogan\u2019s syndrome: a systemic vasculitis","volume":"60","author":"Cheson","year":"1976","journal-title":"Am J Med"},{"key":"10.1016\/j.ncl.2019.01.004_bib140","doi-asserted-by":"crossref","first-page":"1262","DOI":"10.1056\/NEJM197611252952223","article-title":"Cogan\u2019s syndrome in HLA Bw 17 [letter to the editor]","volume":"295","author":"Del Caprio","year":"1976","journal-title":"N\u00a0Engl J Med"},{"key":"10.1016\/j.ncl.2019.01.004_bib141","first-page":"294","article-title":"Cogan\u2019s syndrome with arthritis and aortic insufficiency","volume":"5","author":"Pinals","year":"1978","journal-title":"J\u00a0Rheumatol"},{"key":"10.1016\/j.ncl.2019.01.004_bib142","doi-asserted-by":"crossref","first-page":"344","DOI":"10.1016\/S0025-6196(12)61951-X","article-title":"Cogan\u2019s syndrome: 18 cases and a review of the literature","volume":"61","author":"Vollertsen","year":"1986","journal-title":"Mayo Clin Proc"},{"key":"10.1016\/j.ncl.2019.01.004_bib143","doi-asserted-by":"crossref","first-page":"709","DOI":"10.1136\/bjo.62.10.709","article-title":"Isolation of Chlamydia psittaci from a patient with interstitial keratitis and uveitis associated with otological and cardiovascular lesions","volume":"62","author":"Darougar","year":"1978","journal-title":"Br J Ophthalmol"},{"key":"10.1016\/j.ncl.2019.01.004_bib144","doi-asserted-by":"crossref","first-page":"915","DOI":"10.1016\/S0140-6736(02)11028-2","article-title":"Autoantibodies to inner ear and endothelial antigens in Cogan\u2019s syndrome","volume":"360","author":"Lunardi","year":"2002","journal-title":"Lancet"},{"key":"10.1016\/j.ncl.2019.01.004_bib145","doi-asserted-by":"crossref","first-page":"322","DOI":"10.1111\/j.1651-2227.2010.02050.x","article-title":"Reversible severe sensorineural hearing loss in a 7-year-old child","volume":"100","author":"Chaudhuri","year":"2011","journal-title":"Acta Paediatr"},{"key":"10.1016\/j.ncl.2019.01.004_bib146","doi-asserted-by":"crossref","first-page":"757","DOI":"10.1016\/S0002-9394(03)01122-X","article-title":"Cogan syndrome in children: early diagnosis and treatment is critical to prognosis","volume":"137","author":"Orsoni","year":"2004","journal-title":"Am J Ophthalmol"}],"container-title":["Neurologic Clinics"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0733861919300040?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0733861919300040?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2019,4,3]],"date-time":"2019-04-03T00:51:58Z","timestamp":1554252718000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0733861919300040"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2019,5]]},"references-count":146,"journal-issue":{"issue":"2","published-print":{"date-parts":[[2019,5]]}},"alternative-id":["S0733861919300040"],"URL":"https:\/\/doi.org\/10.1016\/j.ncl.2019.01.004","relation":{},"ISSN":["0733-8619"],"issn-type":[{"value":"0733-8619","type":"print"}],"subject":[],"published":{"date-parts":[[2019,5]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"Stroke due to Vasculitis in Children and Adults","name":"articletitle","label":"Article Title"},{"value":"Neurologic Clinics","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.ncl.2019.01.004","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"\u00a9 2019 Elsevier Inc. All rights reserved.","name":"copyright","label":"Copyright"}]}}