{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,11,2]],"date-time":"2025-11-02T16:20:38Z","timestamp":1762100438481,"version":"build-2065373602"},"reference-count":15,"publisher":"Elsevier BV","issue":"12","license":[{"start":{"date-parts":[[2005,12,1]],"date-time":"2005-12-01T00:00:00Z","timestamp":1133395200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2005,12,1]],"date-time":"2005-12-01T00:00:00Z","timestamp":1133395200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/legal\/tdmrep-license"}],"content-domain":{"domain":["clinicalkey.com","clinicalkey.com.au","clinicalkey.es","clinicalkey.fr","clinicalkey.jp","nmd-journal.com","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Neuromuscular Disorders"],"published-print":{"date-parts":[[2005,12]]},"DOI":"10.1016\/j.nmd.2005.09.003","type":"journal-article","created":{"date-parts":[[2005,11,9]],"date-time":"2005-11-09T07:15:50Z","timestamp":1131520550000},"page":"844-846","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":10,"title":["The effect of dantrolene sodium in Very Long Chain Acyl-CoA Dehydrogenase Deficiency"],"prefix":"10.1016","volume":"15","author":[{"given":"N.C.","family":"Voermans","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"P.J.","family":"Poels","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"L.A.","family":"Kluijtmans","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"B.G.van","family":"Engelen","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"78","reference":[{"key":"10.1016\/j.nmd.2005.09.003_bib1","doi-asserted-by":"crossref","first-page":"59","DOI":"10.1016\/S0065-3101(24)00155-5","article-title":"New genetic defects in mitochondrial fatty acid oxidation and carnitine deficiency","volume":"34","author":"Stanley","year":"1987","journal-title":"Adv Pediatr"},{"key":"10.1016\/j.nmd.2005.09.003_bib2","doi-asserted-by":"crossref","first-page":"E19","DOI":"10.1542\/peds.108.1.e19","article-title":"Diagnosis of very long chain acyl-dehydrogenase deficiency from an infant's newborn screening card","volume":"108","author":"Wood","year":"2001","journal-title":"Pediatrics"},{"key":"10.1016\/j.nmd.2005.09.003_bib3","doi-asserted-by":"crossref","first-page":"479","DOI":"10.1086\/302261","article-title":"Clear correlation of genotype with disease phenotype in very-long-chain acyl-CoA dehydrogenase deficiency","volume":"64","author":"Andresen","year":"1999","journal-title":"Am J Hum Genet"},{"key":"10.1016\/j.nmd.2005.09.003_bib4","doi-asserted-by":"crossref","first-page":"1337","DOI":"10.1161\/01.CIR.99.10.1337","article-title":"Molecular heterogeneity in very-long-chain acyl-CoA dehydrogenase deficiency causing pediatric cardiomyopathy and sudden death","author":"Mathur","year":"1999","journal-title":"Circulation"},{"key":"10.1016\/j.nmd.2005.09.003_bib5","doi-asserted-by":"crossref","first-page":"467","DOI":"10.1212\/WNL.44.3_Part_1.467","article-title":"Very long-chain acyl coenzyme A dehydrogenase deficiency presenting with exercise-induced myoglobinuria","volume":"44","author":"Ogilvie","year":"1994","journal-title":"Neurology"},{"key":"10.1016\/j.nmd.2005.09.003_bib6","doi-asserted-by":"crossref","first-page":"540","DOI":"10.1002\/ana.410430422","article-title":"Very long chain acyl-coenzyme A dehydrogenase deficiency with adult onset","volume":"43","author":"Smelt","year":"1998","journal-title":"Ann Neurol"},{"key":"10.1016\/j.nmd.2005.09.003_bib7","doi-asserted-by":"crossref","first-page":"279","DOI":"10.1002\/ana.20168","article-title":"Fuel utilization in patients with very long-chain acyl-coa dehydrogenase deficiency","volume":"56","author":"Orngreen","year":"2004","journal-title":"Ann Neurol"},{"key":"10.1016\/j.nmd.2005.09.003_bib8","doi-asserted-by":"crossref","first-page":"45","DOI":"10.1002\/mus.880100109","article-title":"Prevention of recurrent exertional rhabdomyolysis by dantrolene sodium","volume":"10","author":"Haverkort-Poels","year":"1987","journal-title":"Muscle Nerve"},{"key":"10.1016\/j.nmd.2005.09.003_bib9","doi-asserted-by":"crossref","first-page":"1369","DOI":"10.1006\/bbrc.1993.1368","article-title":"A novel disease with deficiency of mitochondrial very-long-chain acyl-CoA dehydrogenase","volume":"191","author":"Aoyama","year":"1993","journal-title":"Biochem Biophys Res Commun"},{"key":"10.1016\/j.nmd.2005.09.003_bib10","doi-asserted-by":"crossref","first-page":"327","DOI":"10.1016\/0925-4439(93)90058-9","article-title":"Very long chain acyl-CoA dehydrogenase deficiency: identification of a new inborn error of mitochondrial fatty acid oxidation in fibroblasts","volume":"1180","author":"Bertrand","year":"1993","journal-title":"Biochim Biophys Acta"},{"key":"10.1016\/j.nmd.2005.09.003_bib11","doi-asserted-by":"crossref","first-page":"616","DOI":"10.1016\/S0140-6736(82)91767-6","article-title":"Beneficial effects of dantrolene sodium in exercise-induced muscle pains: calcium mediated?","author":"Bertorini","year":"1982","journal-title":"Lancet"},{"key":"10.1016\/j.nmd.2005.09.003_bib12","doi-asserted-by":"crossref","first-page":"29","DOI":"10.1159\/000115533","article-title":"Effect of dantrolene sodium in myotonic dystrophy","volume":"22","author":"Mamoli","year":"1983","journal-title":"Eur Neurol"},{"key":"10.1016\/j.nmd.2005.09.003_bib13","doi-asserted-by":"crossref","first-page":"503","DOI":"10.1002\/mus.880140603","article-title":"Effect of dantrolene in Duchenne muscular dystrophy","volume":"14","author":"Bertorini","year":"1991","journal-title":"Muscle Nerve"},{"key":"10.1016\/j.nmd.2005.09.003_bib14","doi-asserted-by":"crossref","first-page":"175","DOI":"10.1016\/0303-8467(93)90122-W","article-title":"Rhabdomyolysis: a review of the literature","volume":"95","author":"Poels","year":"1993","journal-title":"Clin Neurol Neurosurg"},{"key":"10.1016\/j.nmd.2005.09.003_bib15","doi-asserted-by":"crossref","first-page":"26965","DOI":"10.1074\/jbc.272.43.26965","article-title":"Dantrolene inhibition of sarcoplasmic reticulum Ca2+ release by direct and specific action at skeletal muscle ryanodine receptors","volume":"272","author":"Fruen","year":"1997","journal-title":"J Biol Chem"}],"container-title":["Neuromuscular Disorders"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0960896605002622?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0960896605002622?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2025,10,18]],"date-time":"2025-10-18T07:54:01Z","timestamp":1760774041000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0960896605002622"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2005,12]]},"references-count":15,"journal-issue":{"issue":"12","published-print":{"date-parts":[[2005,12]]}},"alternative-id":["S0960896605002622"],"URL":"https:\/\/doi.org\/10.1016\/j.nmd.2005.09.003","relation":{},"ISSN":["0960-8966"],"issn-type":[{"type":"print","value":"0960-8966"}],"subject":[],"published":{"date-parts":[[2005,12]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"The effect of dantrolene sodium in Very Long Chain Acyl-CoA Dehydrogenase Deficiency","name":"articletitle","label":"Article Title"},{"value":"Neuromuscular Disorders","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1016\/j.nmd.2005.09.003","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"Copyright \u00a9 2005 Elsevier B.V. All rights reserved.","name":"copyright","label":"Copyright"}]}}